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Otosclerosis
Description/Etiology
Otosclerosis (also called otospongiosis) refers to an abnormal bone growth in the middle ear that results in gradual hearing loss. The disorder is the most frequent cause of middle ear hearing loss in young adults. In otosclerosis, new, abnormal spongy bone forms around the oval window of the middle ear, resulting in fixation of the stapes (i.e., the small, stirrup-shaped bone in the middle ears). Bone growth prevents the stapes from vibrating in response to sound waves, which leads to progressive conductive hearing loss. Sensorineural hearing loss occurs when the bone growth extends to the cochlear endosteum (i.e., the lining of the cochlea, the auditory portion of the inner ear) and cochlear hair cells. Although otosclerosis can be inherited, its degree of expression and penetrance are variable, such that inheritance of the causative gene does not guarantee the development of otosclerosis. Diagnosis of otosclerosis is clinical, based on patient history, physical examination, and audiometric evaluation. Because hearing loss in otosclerosis is gradual, patients may not require treatment until they develop severe hearing impairment. Medications (e.g., oral fluoride and calcium) can help control hearing loss by reducing abnormal bone formation. Hearing aids are used for hearing loss, but do not prevent progression of the condition. Otosclerosis can be cured with stapedectomy (i.e., surgical removal of stapes and replacement with prosthesis). Surgery is performed on one ear at time with the more severely affected ear treated first; the two surgeries are generally separated by 312 months. If surgery is unsuccessful, total hearing loss may occur.
Risk Factors
Family history is the primary risk factor for otosclerosis, with 60% of patients with the condition reporting a positive family history. Some experts believe that pregnancy or oral contraception can trigger the onset of otosclerosis. Measles virus has been implicated as a possible cause of otosclerosis; measles virus RNA is found in the stapes footplate in most patients with otosclerosis, and vaccination against measles is associated with reduced rates of otosclerosis.
ICD-10
H80
Author
Tanja Schub, BS
Reviewers
Kathleen Walsh, RN, MSN, CCRN Cinahl Information Systems Glendale, California Darlene A. Strayer, RN, MBA Cinahl Information Systems Glendale, California Nursing Practice Council Glendale Adventist Medical Center Glendale, California
Assessment
44 Patient History
Ask about family history of hearing loss, onset and duration of hearing loss, associated manifestations,
subjective severity, and the social impact of the condition
Editor
Diane Pravikoff, RN, PhD, FAAN Cinahl Information Systems
Published by Cinahl Information Systems. Copyright2012, Cinahl Information Systems. All rights reserved. No part of this may be reproduced or utilized in any form or by any means, electronic or mechanical, including photocopying, recording, or by any information storage and retrieval system, without permission in writing from the publisher. Cinahl Information Systems accepts no liability for advice or information given herein or errors/omissions in the text. It is merely intended as a general informational overview of the subject for the healthcare professional. Cinahl Information Systems, 1509 Wilson Terrace, Glendale, CA 91206
Treatment Goals
Follow facility pre- and postsurgical protocols if patient becomes a candidate for surgery (e.g., stapedectomy) Reinforce pre- and postsurgical education and ensure completion of facility informed consent documents Monitor for postsurgical pain and complications (e.g., hearing loss, facial nerve injury, disequilibrium, vertigo with nausea and vomiting); administer
symptomatic relief, as ordered
Red Flags
44 Excretion of sodium fluoride is impaired in patients with renal failure; toxic levels may result in these patients, and careful monitoring is essential
Note
44 Recent review of the literature has found no updated research evidence on this topic since previous publication on August 12, 2011
References
Babighian, G. G., & Albu, S. (2009). Failures in stapedotomy for otosclerosis. OtolaryngologyHead and Neck Surgery, 141(3), 395-400. Cash, J. (2010). Assessment and management of patients with hearing and balance disorders. In S. C. Smeltzer, B. G. Bare, J. L. Hinkle, & K. H. Cheever (Eds.), Brunner & Suddarths textbook of medical-surgical nursing (12th ed., Vol. 2, p. 1817). Philadelphia: Wolters Kluwer Health/Lippincott Williams & Wilkins. Caylakli, F., Yavuz, H., Yilmazer, C., Yilmaz, I., & Ozluoglu, L. N. (2009). Effect of preoperative hearing level on success of stapes surgery. OtolaryngologyHead and Neck Surgery, 141(1), 12-15. Cruise, A. S., Singh, A., & Quiney, R. E. (2010). Sodium fluoride in otosclerosis treatment: review. Journal of Laryngology and Otology, 124(6), 583-586. Cureoglu, S., Baylan, M. Y., & Paparella, M. M. (2010). Cochlear otosclerosis. Current Opinion in Otolaryngology & Head and Neck Surgery, 18(5), 357-362. Ferri, F. F. (2012). Otosclerosis (otospongiosis). In F. F. Ferri, 2012 Ferris clinical advisor: 5 books in 1 (p. 731). Philadelphia: Mosby Elsevier. Niedermeyer, H. P., & Arnold, W. (2008). Otosclerosis and measles virus - association or causation? ORL, Journal for Oto-rhino-laryngology and its related specialties, 70(1), 63-70. Roland, P. S. (2011). Pediatric otosclerosis. Medscape Reference. Retrieved May 9, 2012, from http://emedicine.medscape.com/article/994891-overview Schrauwen, I., & Van Camp, G. (2010). The etiology of otosclerosis: a combination of genes and environment. Laryngoscope, 120(6), 1195-1202. Uppal, S., Bajaj, Y., & Coatesworth, A. P. (2010). Otosclerosis 2: The medical management of otosclerosis. International Journal of Clinical Practice, 64(2), 256-265. Uppal, S., Bajaj, Y., Rustom, I., & Coatesworth, A. P. (2009). Otosclerosis 1: The aetiopathogenesis of otosclerosis. International Journal of Clinical Practice, 63(10), 1526-1530. Wolfrey, J. D. (2012). Otosclerosis (otospongiosis). In F. J. Domino (Ed.), The 5-minute clinical consult 2012 (20th ed., pp. 934-935). Philadelphia: Wolters Kluwer Health/Lippincott Williams & Wilkins.