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19, Acanthosis nigricans L83.

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20, Acrodermatitis enteropatica E83.2A
21, Acrodermatitis papulosa infantilis (Gianotti-Crosti sygdom) L44.4
22, Acropustulosis infantilis L13.8C
23, Adenoma sebaceum (tuberøs sklerose) Q82.83
24, Adiponecrosis subcutanea neonatorum P15.6
25, Albinismus E70.3
26, Alopecia cicatricialis L66.9
27, Amyloidosis cutis L99.0
28, Angiooedema = Quincke's ødem T78.3
29, Antifosfolipidsyndrom = livedo reticularis R76.8B
30, Aplasia cutis congenita Q84.8A
149, Arveligt malign melanoma ZM87203
150, Bazex-Dupré-Christol syndrome / Bazex syndrom (atrophoderma) L90.8C
31, Behcet - morbus Behcet M35.2
151, Birt-Hogg-Dube syndrom DQ878K
32, Blandet udviklingsforstyrrelser af specifikke færdigheder F83.9
33, Bledermatitis L22.9
153, Blooms syndrom
152, Brooke-Spiegler syndrom
34, Café au lait-macula L81.3
35, Calciphylaxis L94.2B
36, Chronic bullous dermatosis of childhood (LIGA) L12.2
37, Collodion baby Q80.2
38, Condyloma acuminatum A63.0A
154, Costello syndrome
39, Cowden syndrome Q87.8D
40, CREST syndrome = sclerodermia M34.1
41, Cryofibrinogenaemia D89.1G
42, Cryoglobulinaemia D89.1
155, Cutis laxa hyperelastica Q82.8D
43, Cutis marmorata R23.8B
44, Darier = dyskeratosis follicularis Q82.8F
45, Degos sygdom = mb. Degos I77.8A
46, Dermatomyositis juvenilis M33.0
156, Digital fibromatose
157, Dyshidrosis Lamellosa Sicca (DLS)/keratolysis exfoliativum
47, Dysplasia ectodermalis anhidrotica = ektodermal dysplasi (anhidrotisk) Q82.4A
48, Dysplasia ectodermalis hidrotica = ektodermal dysplasi (hidrotisk) Q82.4B
49, Ehlers-Danlos syndrome Q79.6
158, Ekkrint naevus med ledsagende hyperhidrose R61.9
50, Eosinofil fasciitis (Shulman syndrome) M35.4
159, Epidermodysplasia verruciformis B07.9D
51, Epidermolysis bullosa dystrophica Q81.2
52, Epidermolysis bullosa junctional Q81.1
53, Epidermolysis bullosa non spec. Q81.9
54, Epidermolysis bullosa simplex Q81.0
55, Epidermolytisk hyperkeratose Q80.3
56, Erythema elevatum diutinum L95.1
57, Erythema multiforme bullosum L51.1
58, Erythema multiforme majus L51.8A
59, Erythema multiforme non bullosum L51.0
60, Erythema multiforme non spec. L51.9
61, Erythema nodosum = knuderosen L52.9
62, Erythema toxicum neonatorum P83.1
160, Erythrokeratolysis hiemalis
63, Erytropoietisk protoporfyri E80.0
64, Exanthema medicamenthale (+ATC-kode) L27.0A
65, Exanthema subitum B08.2
178, Fabry, mb. E75.2B
161, Familial atypical multiple mole melanoma (FAMMM)
66, Familieanamnese med andre specificerede tilstande Z84.8
67, Forstyrrelser i hudens pigmentering L81.9
162, Glomangiomer(arvelig)
68, Goltz syndrome Q87.8E
69, Gorlins syndrom = Naevoidt basalcellecarcinom syndrom Q82.8W
70, Graviditetsdermatoser O26.8J
71, Hailey-Hailey Q82.8X
72, Hand foot mouth disease B08.4
73, Harlekin foetus Q80.4
74, HAE D84.1A
163, HLRCC /Hereditær leiomyomatose-RCC-associeret renalcellekarcinom ZM83113
75, Hyperimmunoglobulin E syndrome = Job syndrome D82.4
76, Hyperpigmentatio uden specification L81.9
164, Hypertrichosis lanuginosa congenita L68.1
77, Hypomelanosis (leukoderma) L81.6C
78, Ichthyosis congenital non spec. Q80.9
79, Ichthyosis congenita alia (specificata) Q80.8
80, Ichthyosis hystrix Q80.8B
Ichthyosis, kønsbundet Q80.1
81, Ichthyosis lamellaris Q80.2
82, Ichthyosis linearis circumflexa = Netherton syndrom Q80.8C
83, Ichthyosis vulgaris Q80.0
165, ILVEN (inflammatorisk lineær verrukøst epidermalt naevus) L44.8D
176, Immundefekt
84, Incontinentia pigmenti Q82.3
85, Insufficientia nutritionis, zinkmangel E60.9
86, Jadassohn bledermatit L22.9B
87, Juvenilt xanthogranulom D76.3C
88, Kinky hair disease, Menke's sygdom E83.0A
89, Keratoderma plantare/palmare L85.8K
90, Keratosis follicularis spinolosa decalvans Q82.5
91, Kerion B35.0C
92, Kronisk granulomatøs sygdom L92.8G
93, Leiner syndrom L21.1A
94, LEOPARD syndrom Q87.8J
95, Letterer-Siewe sygdom = mb. Letterer-Siewe C96.0
166, Leukonychia congenita Q84.4
96, Lichen nitidus L44.1
97, Lineær IgA dermatose (Chronic bullous dermatosis of childhood) L12.2
98, Lichen sclerosus et atrophicus L90.0
99, Lupus erythematosus cutaneous subacutus L93.1
100, Lupus erythematosus discoides L93.0
101, Lupus erythematosus disseminatus/systematicus M32.1
102, Lupus erythematosus, lokaliseret, andre former L93.2
103, Lupus erythematosus profundus L93.2A
104, Lupus erythematosus tumidus L93.2C
105, Lupus panniculitis L93.2B
106, Mafucci syndrom Q78.4A
107, Malformatio congenita cutis non spec. Q82.9
108, Marfan syndrome Q87.4
109, Mastocytoma cutis D47.0A
110, Mastocytosis Q82.2
111, Medfødte misdannelser i huddækket Q84.8
112, Mental retardering F79.9
168, Milroy sygdom (lymfoedema hereditarium) Q82.0
113, Mixed connective tissue disease (MCTD) M35.1
114, Morbus Milroy = lymphoedema hereditarium) Q82.0
115, Morbus Osler (telangiectasia haemorrhagica hereditaria) I78.0
167, Multiple self healing squamous epithelioma of Ferguson-Smith, MSSE Commented [AB1]: Samme som tidl
116, Multipel symmetrisk lipomatose E88.2
117, Naevoidt basalcellecarcinom syndrome = Gorlins syndrom Q82.8W
118, Naevus epidermalis Q82.5D
119, Naevus flammeus Q82.5E
120, Naevus linearis (naevus verrucosis) Q82.5A
169, Naevus sebaceous Q82.5K
121, Naevus unius lateris Q82.5J
122, Neurofibromatosis-1 (Recklinghausen) Q85.0
123, Noonan syndrome Q87.1A
124, Oedema angioneuroticum hereditarium D84.1A
170, Pachyonychia congenita Q84.5D
125, Parasitophobia F40.2A
126, Pathomimia F68.1B
172, Peeling skin syndrome
127, Peutz-Jeghers syndrom Q85.8B
128, Pigmentmosaicisme L81.9
171, Piebaldisme E70.3F
129, Porphyria cutanea tarda E80.1
130, Porphyria erythropoietica congenita E80.0
131, Porphyria hepatoerythropoietica E80.2G
132, Porphyria intermittens E80.2B
133, Porphyria variegata E80.2E
134, Pseudopelade L66.0
135, Pseudoxanthoma elasticum Q82.8Z
136, Retarderet psykomotorisk udvikling R62.0
137, Sclerema neonatorum P83.0
138, Screening for medfødt misdannelse/kromosomal abnormitet Z13.7
139, Syndroma malformationis congenita med dværgvækst Q87.1
140, Syndroma malformationis congenita med skeletforandringer Q87.5
141, Syndroma malformationis congenita med tidlig længdevækst Q87.3
142, Syndroma malformationis congenita som overvejende afficerer ansigt Q87.0
143, Syndroma malformationis congenita som overvejende afficerer ekstremiteter Q87.2
144, Syndroma malformationis congenita systematis multiplicis uden spec. Q87.8
145, Tuberøs sklerose Q85.1
173, Uncombable hair syndrome (spunglass hair) L67.8D
146, Urticaria pigmentosa Q82.2A
174, Waardenburg syndrom DQ870M
147, Wiskott Aldrich syndrome D82.0
148, Xanthogranuloma D76.3B
175, Yellow Nail Syndrome L60.5
177, 18Q deletion

888, Andet

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