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Semiologie Neurologica (Popoviciu) - Bucuresti PDF
Semiologie Neurologica (Popoviciu) - Bucuresti PDF
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A n)
H 5>
gl lNvATAMiNrutul
MlNtsrERUtEDUcAIIEI
Prol' dr' doc' tlvlu POPOVICIU
Prof. dr. doc' CONSTANTIN ARSENI
sEtvllol"offi
LA BOALA)
(DE LA SIMPTOM
ci MFr''[
L,'
QTq
J"/
0u
^ A*Af'l
.rq.
qEP
lDllunADloACrlcA
fl rlo^ooolcA - lucuitlll
CUPNI,NB
l. lrlr|durnto
cioslonl
l, ln)lrlnmc di dloUnostlc topogrnllc tl etloPAtogonloh lezl[Dlle ncrvll'ol
I
.
lr.rtologld
:t,1.
Percchli
t.t, l,utologl{ Pclechil a II-a
"
'
"
' r "
l.ll, l:robl0nlo dc diagno6tic ln exottalmii
otorii
oculo
patologie
sistemelor
tn
dlagnostic
)
dc
'
' ' '
Itrottlor
l.l.
l.h, Prohlorno de dlagnostlc lr! patologia nelvului trigemen
Li lrroblGt o dc diag:nostic ld patologiA nervului laeial
(cochlear)
' ' '
L?. lintltlnnrc de diagnostic in patologia nervului scustic
g,l, t robklrno do diagnosttc tn patotogis slctomului vestibular
t,g, l1$ltonrc dc dlagnostic in patologia nervulul Slorofaringian ' ' ' ' '
l.ltl, I'robl no dc diagno8tic ln patologia nrvulul pneumogastric ' ' ' '
l,ll. lrobl' rtr de di{gnostic ln patologia nexvului spinal
Lll. t|rot,l(uc dc diagnostic tn patologia nervului hipoglos
paraliziilo! rnultiple ale nervlor
'J,lil, lrro}|lrnrc do diagnostic in patologia
r'flrrlr!rl bulbari
l, }ltrtlrtlr do dlo0trostlc In parallzti
ll,l, llrDlofltrcu scnlologic{ a delicitelor motolil
11,2,ltllnrh0roo t0lsclor pareze sau Paralizll
!l,il, I'rohl{ttlo do dlognostic etiologic ai topograllc ln divo$e pamli'ii ' ' '
721
183
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194
19t
168
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170
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246
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9 . l "o l, lonrn
dth x,^ti.
'tn
11.l. A gln)z ii l r l . r r c t i t o
l ).:1 . t J noz i i i c v i z u a l c
:r.;J . glloz ii L ! : r u ( i i t i \ c
I n r r 0 r ,o ztl
270
27(t
275
276
l )..1 .A t jnoz ii l e i n l a g i n i l o r . c o r p o r a lc
I0. l|rubll.|Do dc diagnostic in
tulburdlite d0 vorbiro gi lD afrzil
t().1. c t ls iiica r c a t u l b u r : i r i l o r
d e vo r b ir c
2'.19
2',7S
275
si rfxp}esici
siurbolurilor
:1,,,1",
lll]..i
:1.:J . Sirx
lro
l | r t , ( l 1 r i ! ( i e l e z i u r i ir 1 n u clcii b a za li
l i l .i l . s ; ndr. )u r r x , ( h t c c l r l L : ziu n i
co r ticu ic
I:1 ..1.SiI (lrrJ l l r c i h t f r t r j c z i rn j
d ilu zu
l :l .l ). l. iiudroa n r c ( t l t c ( l r l o z i ur i situ ste
D .\,.r r ia tc e tr jc
282
1.INTRODUCERE
295
;J02
J02
315
:\,17
3.19
:i51
352
' ,r rr i rl r,r' r l rtl l rIrv l Ii , i tr:ri l l0 r lf 1t r lt lc, isc vlt , 1: kt o t t t r t r xit r t t r , t t llit t i0
trl r i . trl r r,rrrr ci ti 0 i tr rrui srrt ir $ii, ( xi( 't t l. ( r zt .1xr 0lir r it . iir r rlr l gr |lt ir r t , r . sl, i',
t,rl rtl r' r | | III:| (,Ii | | i ru.t.l rrrr l tr' l rtrit . r r f r . r r lt I t lr . .
l ' l l l tr' l i trtri i n.l l n.nrl t t tii ( r t t r lcot r lr i vir t lit 't ', t t t t t i r t lt 't i glilt it lr ') , r : it t l
l " ,l I' rtrl rrr.r' rrrrvti l ,r' ol l rrc livo r t r , t t lr zit t t t i t ir t lt t cr , l: r I ilr '. llillt r t ir t , llt t o
l trl rl ,r , .| | |r| | | | | r(' i I 11i:rl l r, i tr[.r '( ii gct r ollt lo lt r r l, pt 'ot lt t r t 't ll ilr lt t t lt t t r il t t t r vtilr '
r,l l ,r, l rrr 11/rrrr ruorri rrgor,r r r r r 'l: r lilrSr
'. '1xr l, ir r lJlt r i t t t lt t it t gr t t 't t r r cf llilr ,( pt t t t t
l rrrl ,. l trl rr,r' rrrl rrrrsr' ,l rrtrl ilr ') , ( . 1( jr , f r r lif t \r , ir t t l'ict ', t t t ct t it t gilr r r r 1t ir I t r I I r icr '.
l l l ' l ' trtttl ttl i sntr: (l ( t!l, r r t . il, ir lii t : t : lu. l, iorr:,,t t r livlr so I r t 'r t lizilr 'i r yi k'
rtrrrr , l rr' l rrr rrr i rrl rrtrrl l rt r r :lrr ,illr t t t ir lci r ir zll( f , ( '( lt 't it ( tl, I lt t t r t r t lit u'illl zt r r r i
rl l ,r. l nr,, l l rrcl rrl i rrkr l l rtrr ci cit r t r t if ir r t , r lt noit lr t lui ( cu lt 'zilt r r t l f ikr t i'lr r l
rl l r,,i rl t\ | | l r. | |(,| | r'()| | i | ()r' l xrlilit |'ici I i, ov( t r l, lliLl,ou sl|plit inr 'f l, t , ii st , ct t t t t lit lc
osr niilo po$t - lr : t um a l ioo pl) 1, t '( ! ( it t lloit I lt
C' PROBLEME
DE DIAGNOSTIC
TOPOGRAFICrt rr \ rl r. ,rIl ;rr.Ii vr' ). l Jrrcoli r ur( x)
nt lr llovii, ur i, lr , bulllului t t lllt cl'iv r yi/ sr t , t t
r1lrr l .rrrrrrl l rrrrrurrri l ctLl i , I ) lir
4. $I ETIOPATOGENIC
iN LEZIUNILE
rr Irl rrrIr'Ir.Ir,Iololluclivrr. AllcoI'i ba,ndelotcle ol1'active pot' Ii lozrr,l'oplitt
NIiRVILORCRANIENI
l l r,,ru. pl rrl i ;ri Lr rni ci ul c slonojdului. Jlxist l sil, t t a{ii in t 'at t t r it t ot t t st t l
it|"r Irl'.rr''r1ii rroUr'ochiru] gio c, ridicarca lobuluj frrrulal pttillo ltftrt'l,a
I rrr t rrI r.Ir' I r.I r, rrllrrr,livtr, (iilro se atlal po l:a!a, inl:orioru'i, a, lobulni orbilrrr.
A l l ,.,,rt, l rrrrrrurl i srrrcl c, dat li leziunilo vasculluc lot ir nt l'olr r lupl, ur N'
Intlad,ucere, Fatoiogia nervilor cranieni este deosebit
n'||r ,r lrrrrir 1r|rIicrrIrrIrrivnscular provcnilj diu artur:l oerobralil ruti;trl'ittit
I l't.
Irogu,l;ri,
de
rl,rial5,,
atit
stb
proceselor
ryi
morbide xesponsa
.aspeetul
r,r,
(Dr*loix
r
1l)l-;$,
r.
rlr.
r';i
frilrtt'fla,
rr
vrrscrrlrrtizeazii
bulbul
olfactiv
$t[r aslrcct,rrlcontiguratiiloi ;i al contextelor patologice
fi
'.it, fi
I l l ' rl l rl {, l \l rl r16r.scu,
1l }?5) .
.\r:r.:r,:,t,ir,
.\cr.irtrir,ir
comploxitc,te patologrot,
oomplo-xrrc,re
patologict, d.e
de multe
multc ori luxuriantx
luxuiianti, si,
qi cler
' | ' rrrrrrrrrrIrrrrrrr'cl| cani o-cer ebr alo pot ploduco r nosm ii, hiposnr ii, t l: r l
(l(,1;{runrnatrr,
,.,r1,'\
pe dc o parte de pozilia strategic[ a nuolei]or de
i i ha luoina, lii olf aot ive.
rl
rr,u tlo 1;crminarein trunchiul cerebial ;i in iorma.tiunile
Ir| | | | f trrr, r.rrr:ostrriS
l,r,l lrrrrl,. lr:rzci craniului artreneazl tlcstul ilrl frecvent hipo- srttr
rulitoonto &cestora,
.l l l l rnl l rl l
porrl;o-ocrebelos,
in stlnca
rrtrrrorfiirnrgicalc.
2.1,PAT0L0GIA
PERECHII
t tNERVUir
0LFACTIV)
ll.l.l. tn prozonlaunor disosmiila indivizi la caroun eorocr6xam
rrorrrolol;lo
lrxt[ intogritatea neuronilor gi n ciilor ollaetivo, esto vorba
dlrosrrrii rlo nnturd
("Miloqescu,1925; Chusid, 19?0 ; Rir
_rinolog,ied
- Acestoa se caractorizoa,zd,
llll"r9.;l'opoyiciu.Fi Pascu,
1.980),
pril'anos
pozo
pozo
(r:ol rn&l
(oot
mir,i &desea
mir,i
&desea rdectato);
inJectate) : cl)
infectato);
d) deviarii
de;viatii do
de Bept
scrt: i e)
c't rinite
rinifa'c.iacuto
devialii
rlo
l,llzo (t:ol
orouitlrl do divorse naturi I f). ozen*.; g) reactii alergice uazalo; h) tum
""""ir
;j
if 'rii.'# fil,.rdsTH' .#.J,T,ii
i:
ii
ll'i;
iii;,
.t
.
"i'.]t-i"i#
j) sl;il,r'i.dupl,
intorvenfii
rvellrr o,orruJgrcato
po etajul supeiior iazal qi pe sin
ohirurgicalo po
nrrr.i;; l()
rr)
fiuli
diverso dorogld,ri
dorssH,ri respiratorii.
resDiratorii.
1,11111111111rr
11iN i ccol l i n i ( 1958, oit a, {, i dc }I iloqescu, 1975) a, u ar i, lt t l
i,ll | | ||| i , | | I rI I t .rr r.rrlcfalopatiilor posttraumat'ico oonsecut'ivo ltziunilot'r'olt
'
ItDl,,rllrl, 1rr,zrrrl:i in contextul clinic tulburlri scnzorialc, inclusiv aartsrnii
1rrr rrprti xi m at iv 10o/ o din t r aum at ism ele clllnio- cor ol) UlL'
Ittul l t,rl rrrl rt,
fl ' l r ' I
l l i ,rl ,)ntl ttt
r(l r:ul ur ( cer cbr a, Le
ant leneazi, r ar 'eor i t ulbr t lir li r ) llir r '
\rrrrrrl r.i rrrrl rrrl rti ol cI ochzia pediculului vasculal pr ovollil, ( liI l
l l tr,
rttl r' rrr r, l l rl rl rr l rrl r,ri ol rl i , calo vascular izazi, bulbul olf llel iv ( I ) r xlloir
tl l ,l l r, r, r, l l rl rH , (l i l rr{i rl e 1! liloqescu,1975) , poat e pr oduc{) r ln( , Blnjo.
lll Itrh
nrlo.t:iut.lii (cu atropirri,, cu rnodinX, cocainii, sulfutir, (l('
r,rrrfrrrrr,, r ) rir .!lri,.i/(rlostnarceXi,(e se pot flolda cu hipo- s:ru ltltostrtii
| | rl l l ,l l "r
il
:' | 'I' l)ivt:flttiu (unosmia, hiposm,iaFi eaenlualparosmia) cu,'inut lntt' ltrti rt prr4tnwit:d. ridicii ulrrlitoarr:lc problomo ct'io-po,togonioo:
lll 'l'trll'tt,trt ,l.f,rt'titt ola-ziw ,,fiaiologice", Sunescenla
po&tc 6it ror,llrr,rr, lrrlr" r'lllr( (i$, i'ot|8('(ntivirprocoselor'fllnolico alo neuronilol olfa,o"
lf vf ;l rrlr lrrrrlriurrilor rru,slom. Unele std'ri,Jiziologicelo femai (graoiili.Itlrt ttun,,ftu::tl / rrrrlleneirzii,uneo porturbtrr'i ln perccplia, milosurilor'.
Fh I lrrnrttri, rlr, l)il(li, hi;xrrosntiir din primul tlimostru de gravidittttrl
l,tllbull lrlpruurirrrlirr rr,lrloik,ir,1i al l,rcilll trimcstru, cu roverBibilita,totu
l{tlhr| ||ur(,1lr,r
ollitrrtivl dtrprinrrqtr.nr,
ff) l,nr,ll luli lynualt (r, (liab(ll,ul, ur'('mia,pa,ludiBInul,homopnl,iilo
lIlr,]llr, lr,l/r'r.rriiq,u,.)1xrl,af,r'ct{t,r)ouxmii c{,ilor olftrcl,ivo,pl'in (liYortt(,
r,rrrr.lltrt i Bllli(.icJlicl:rIil iclrl,(1,
lrr,r,r||rlxn||',
f i) '/'r,,rrrv, llnrralt tatt, lrx,c&r.'ntorlilru, $l[l,ulnifinlul, llr,bngilnrul,
*lIrrltlIr, i(x I Ir, lt|r,nl(]lul,r'Itrldn , ritr'l|1ul(1(]n.rginl,,0lonlrfl (lo zlhat,
rtrllurx ilr\ r.rflrrr, llrlirirr(,rr lor'irlil rlc solutii hi;roltonictr (clt.t'usr',1lir. t:11
|lllr,l|lrI r lllr ollirot ir'i).
ll
lll , I
l l l {i l )).
lll
l trl l ,rrtrrri Trsi l ti t:a nt vnlzt r , llsilt r r zt r ' Anosr ni: l isl'cIioli, t lr r . pilt lii,
'
,, i i ,,' 1,' ,r,, ,r' l rrrrri bi rt" c 4in4 bolir a'r t r lt r i sil r r t ir oa's. ilr nt t t t iit 't r As1'li'1,
'
",
kr
r|| r,r,l,r, ,l, r 1'r |z ir rl ri Rl lt,rltl nazo-lacrirnnl (pl'in stimultrtn' trigtrtntltlttltti.t
lkl
it
i
I
r
r
t
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liicr
it
t
t
t
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qi
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77)
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soni
co1ab.
,
r
rl
{
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ri
li
r
l .rl r'
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txtrlttrttt'l
cura intereseazd'ratlialiile ^olfud'i'tr(t.
l \l lttttt t'lr l)t t)11'!)o
.8tt'11'
nir
r t ot lr r 'l'r i
inso{'it
o
nu
oi;
t
l')
t
r
aur
nat
ism
e
r:rrcl
l
tl
i
l
e,
rrl l r| , i l trrrrr,rrr,
- sinl.
irr crtzurile de kviuni llill,t'cI illo, hlttttttrtrtt-trxplitrlt'ltil
tl tt rrl'' ,' ,,,,,, ,1,,
't
,,,, , ,,, ,, , jiilol intracu eblale (Alscni qi colil'b', l1)?7) Itt .rtstt
t lr t lt t ' t t t lit t t i,
i
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r,'
r'
r'
rl :rl ,' trtl sr r , lLbilat cr alo, st l llt t llt c t lt ) r ) 's1'l[ i'ir
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,,i ,,,r, ,, ' , rrrl r(rr ,,l l l roi i vtr qi, dc ur ul1, cr lr i, lcnom cnc do, t ll! {l}ozio il
t\r,, rrr .r l ol rl b., 1 977) '
"lllt
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l,l l. llll,'r'tl"rrri (or'o$tercil,clplcitir,{ii olll'ctivc) sc i'r.tl'illrclkr
it
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;' ,fr' r
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I' t i ,,,,,, ,,, , .,r 1,,l N rt| i l ri i ' in'cur sul l1r sS, t ur ilor gr avit lit xl, l'l t r ovt r 4}t '{i
llll
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ai t,, ,,,' ,, t,' l r\r1r ..rIrItrt| | :|I i. Alt ( 'u1i, ll ipet 'ostr tiit ' si' pr r r t l. llsr ) ci: t cll
l
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i ,' ,,i u,r' ,,1, ,r rr.rr.;rl r.1\i
l l l ?Ii ).
l l l Il t l t Il \| tt.,, rrcrr,
l r. trr,l Ii i rr lihr it r : qi ir r ur r elc cazur i do opil( , , psio,lt t t t lt olo
l l l rrl rU r
lullll) l i ( r 'l{'
| | || || | | , ,, | | ,,I , ,, , r:r| | ;,, , r,tl .l )t : r lr . ,ir r I ir zr . lt ' dt . t lt br Ll. : ll' llllt , r
it
in- m ig- ur t o r yi r un. lt r slit 'r i
i ,tntu, ,,, l rrl rr,rl r.,i rl i srrr,i rr piu, , lizi. gr r olalll,
,,,(
N,H
r(.i .i,u
lbu;x;i,
ti"t-iii^rifit li,ii?':ri:"if ff,.fT1,,T*1ilT%11
trilltcratil.S-aardtatastletlerseniqi
is?ej;;, degiant
in rireningiormer;.1;,rul;i
"biffi,
iitactiv,in
;:,i':1:]
liii:.1:il
.:"T-1-q'iolippr
z|'r(.rx|||lrlvu,)r'it,cerStii
dcville sesizabili,doar atunCi cind este bilatr
l)r:.rrrrrllc.ori,cin<Icstc recunoscuti,.1"
localenesemnificrti""'iri"itiil
"iii;
iirofla mucc
::l::l
ll:,:ci'l,rl,1.l,l
lli unei
9"qrg
rr;rzrl'
r,lt:.)rrkrcit;
leziuni cerebrale
ci, ;i it;.;,,';r;i se*acoroa
l:,rtir, uv!.ritrj. (Ars.ni 5i cohb., .19?J).'
;";;;i;
d]J"rlrnn,oe
'
poaleinsoliun sinaroi"F;;;l{";;;d;;';;;ii,fi
:i:,::l1ll1l,t..lll],'l,t:i:
ir(fr.r'rf
r pl t t,c cu
cu atrofia
corab.,isii,lsd)."-;;rmii
sibi.tatel
::,ll:il,:
lgE:,1i-rrtolie.(Arseni
p.l, irrlilrri
s.
in meningioamebffactivJ giganiq
ql d"
in
"ri6'r" ""ii"a
expansivZ!i in iiO_"oc"rariic"
I
l:::: lllll,-itt t umori hilofizare
jArsen.i
qi
iota'b,-1'erz).-iiu-u,i'i''au.i,
-""e
ur
:::i.T::lll:
iillill"Jl,lie:lii
I anosmiei
precoce
y:::ll.:1.,.':'
in cursulmeningioamelor
i":.i::-?lli
iltrlorior,
in vreme ce aceastae-st"
*ai u"ri" iffia1i
oe cetre
it
-u1t rruruilro"iif
l:liillj,,
.":emptu
.neorgmaliunte
"fr' ii nr"
r:rlus,.t'.r'aniofaringioimele,
-jt?.,1"jumoriie
g[oambte;;"r"r;i-;fi1"
"on
gtioamaeEentrale.r" rol"i"t "i"ontJi pragur t
::)-1;li,lil,?"9"_:,-11
,l"ll,Jg
t, ri"lmin:irionnalmultd,vreme,ir" ;;;;'.;;hJta
esturare
Inl,iluitri,
1,lnliv. .h rr,prorpco treime'din ;-;;l;gr";;;il
aripii
mici
rli.rroirhtlui,
r{o
pt'orlucc tnrUrl
so pl'o(Illeo
(, crc}l,oro
in-itria,lo
crcgtoro a prag"utul.
pragului. olfactiv,
olfacnv. resnec
res
r i [(r(]{rrl r'l |:I r1r ir,rrlrrsr.lii.llrrr.l.ivrr
Fi rl{.st:rlrlc I irziu sr,insbal,ltiiirrt
iJrsilnl'rrriuhL
r,urrrorii(ltisrrr, lr)fir).'Arsrni
r'i ,r,riiii. ir.9i]lj-rorl,r,rrl,z{,
lt
l"rt..
'
1$75; ll'isot''1{)52)'
iiir,ili" ,,\i,,r'rrrri ,,,trrir.,i1)7?;l\lilorycscu,
i , " , ,, , i i r 1
ri
ls
,,,,,,,!,:,1,,,0;o;,fl{tffi
?lffi&:"\':2i1.-peroeperea.unorcu.rodsubir
ji:"U/fr
jr":"_d,p';ffinn"T,il'H:ABffi
fIii-,:1fi
:j;iffii{{Z#:d.
:
.i$";"f;*r*"
"-;*t':#*::l[it:,"ffJ,",S"JT,,?il,*.f*j
ll.l.5. Ilalucinaliile
;i iluziile olfaetive paroxistiee
sintrorme
decrize
e1r'eprico
rr.r',',J;1;''.f iii';,?':gi.uJ,"'1,.y:ioz
, ti,,.,
r rtr.'r i:eu(a.t
i oe,tr*i"i
i,i,,r-r'r:"
:i'uiJr-.
.f"ii iiH,f r:;
"G'tdi "#rezulta[ui
j, ;i r.otab.,. t9Z6). Reprezinrd.
:..::ll:i"',.'
ior"a"",i"i
ir'||:rtr.
;rli;irt'ii:;rl#i:i,:ix:fri:ijir:::{b1.r$'",'.r'-;;:T,'3i,:
:rt( . r , ( , t l, . x ului r rn r.i n a t (c ri z e
u n c i n a te ),
,,:::!
,.. ...,:,.!:.!!:,!
. lriret,c.u,nainate
Wr!ir|. Crizeleepilepucecarede
unor mj
'itzil lrntt lx.l.(,(,p{,jin
srrrrrdrrr':,
rr/ir,,,rr'i{,r([
,i J"-"j:"'il'.j?tS^fl*:llfot slrt iare tz- rloTo
'}:::
i]ji,
:l$::fl
i:,r;l:
;:;,lili*riiiii:niis
rllTf;,],
{l{,!,'ff
{t'.'rl)$r,:
rrr{,r,,,'gimioi
r-i.".-a"p"[,"g;,Jfi.;i:;h#","r",ryHr
;*; ;ilffi 'sT, ;tl
:i,'i'
rura
li:Ii: (,lll;,
r "tc.1
:J':
i i :ll,'#i;
::,-f +
"ff:T,'*
Il:i'iil'
,11i;il;ti,i.'i;i''I:;.fff;
#.it;;'";il:';;'ffi"f,1,",iii'161i,[ii;)r
ru:
"iT
qil
fl',,i?.fl
i:l:lil,'lli:,,11:;l';:ii-':;ilil;,'i"'t#iT[ll1'"u0"",i11Y,;m:.yffil"il
llrji tl;itil* iti,s'#,
#,#
:1,i
tiliibili:rgiliid
14
I It
(NlillvUt,
ot,1,l0)
lr lr l i( 'ilr li'll
rrrvcl l tl rl c i trl l rrtl i r, vi rsrrhr tr r , lt t t it 't t r ,it t t t clt ', I it t ll, lit r 'I t ilt llt I t I l,
l rr.rrrl u ,i rrfi trrl ronrttl l xxl tl i olm r t r lr l, r olr t t llr ir t '( t t r r lilit o; t i'ilr i't 'r 'lr olr t t llt lt l'I ) .
dr po. Tt ilo
A J I\pi l i tu. (si ttrl totttrtl t r t lt r iu jr t , r t lohr t lharsuu sindr ont . r t l.
(r'ttt.lrinu.rtsulnrc'u,li) (llintrr, l115!; l\'llttrolcxrrtt, ll)fil{1
rliavrrostie
rdinic' lopogruricsi .tiopatogenic n, ttili ttl,t1||,i0/ousti,
,,,,',,i;;;l'rli;ll$;rlt'
1u,:rlrrfi t.ttrilitt,tuirl?iHilu l)illlrfr'lllt si rrrrilizcltzi't,tta,t"r lrtlbtrrtit"i, lltilr lrzitr
rrrl " i trl l urrtatori j < l e tu,vtill, in1t , r 's1, if ial1'it t xllr hullr lr r 'li, : r t ) Ar r t t ilit lt 'ir
uizuote
r r:rrrrrl sr:ade
in cil, cva zilt : , ut t ilai. t 'lr t l, slt t l lr illt
ii
totdoaruta l ap it l, lt llt al,
sepot exprimain urmatoarete
l.r;rl (cga,l sau jnegal), pini lr o drarnntici arntntrozil; ll) (lirrrprrl vizrrrrl
'11llll{ffiJi,Jcaititlii
lll .4nbliopio lepl.czjntdtlimjnuarer acuitrilii
, rir. rlrr ollicei ingustat concentric, dar uncori tloar sectolial 1sitrtt st ttlnltttt,'
vizurle.
ll\ Cecitalea silsiu amauroza reDrezintd, nicrrl,,roo rnnoti .,
l,lrirrt ccntlalc), vedelea macular'[ liind mai rcspectati,; o) ilitttItll rrtrr
rrr:rlic cste foarte a terat (cu moclificS,ri ale cir,rpulilor ct'ttmlftir,tr,lltt st,,r
lrilatoal[ (6i in accepliuneia,
l,,irrr{f pontru culori, cu discromatopsii qi chiar acronliltopsitr I'olrtli);
c*orectEiinli*iX,-piiiiizt;ne'
ce.nt.",u
,lr \rlrrptarea la intuneric este loarte deficitari I e) Adcscn lo1'oltsii '1i tltr
..io
D) Ilemerabpia reprezinti iliminualea acuitelii
, rr ll rrtilci,rile globilor cculari I f) Pronunlat edern pa,pila'r, prrpilrr,Iiittrl
*,
l.l spl:c Seara.
r,,.rr,,,
lrrlblre, tumefiat5, cu conturuli foarte qtelse, cu sll'ii (r1| I ' I I Ii t'I t l i | |r{'
"irort"
,,.rrrl,ii-rozate. Manifesti,rile edematoase peripapiltlle se itrt'itttl ltrr zott,
,r;rri rrLr cimpului oftalmoscopic, r'ealizind aspectul rlc ,,ntrlttorrrtirtilri,".
invizibilc ( llisr r t , l1) l': l;
' ,,rrr1i rrJl cpapi l ei deveni nd , in accst c sit ualii,
.,,.itri1i, {ininelseamaindeos?binc.rmai.oarete-;i.;l,iii,
g)
Yelele ; i t ,II I t i IIt tr ' It ' st t r l
\1.
n()l
('
s(i
u,
19?1)
D
uke
E
l
d
el
Sco1,
t
,
1958;
;
$i
r.rrulal fundului de ochi gi pi,strarear"tf"iofui p'r!i"ar iiJpiltir",i
inecat
e
in
t,r.rri
r.
rl
i
htate
qi
slnt
et lcm ul lt t r t sir '1 lt ) lt r
si
nuoase
,
ar
t
er
ele
la tuminri.
,
si ctstttlrtlt', r'l'r'tt
i
pedpapilale
hemoragii
l,,:rr'('l(i
papilare
se
obscrr''X
$i
... l') !):l!r"*,atoysja_peytyyalb negru fi tentru iulori reprezintri
zone
t
lc
t
't
lt r t t t llt 't t t t iI r r I lil t t t
tl
,,l
vast
e
i
rsl
l
ccte
trombozd
velt
la,
s:
i
cu
de
in-considerare,'inirucit
aceasiapoaresd,l
:l:,1l,,,1o'1'"]T3"jlrlt-,*:.ll?1
cr,rr,rlio scrio de lezinni ale chiasmei
l rrrrrl :rcr.storl ezi uni ; i ) C o af e, ct ar eavit r osult i se po: ll, o r ( r lr lizr lilr l) r r lt ilil, r '
$
lrr, lrlii (,\,[anolescu,1958) ; j) fn forma de ner-r'i1,Lopticil trtlt'tttrtlortsrirtlttl;r
i!.2.1.1. Amb_Iiop.iile
:!./,,.1.1.
"in "ail'*
Amblioniile
si,amaurozele
am.turncplo "pti"b
n.alra
<; a,,t,-..,]*^
acute si
sul.tacute
;i,
se iatilnesc in
rrl r:rl rrnrr.l i cul ari descri si i dc Rcnar d ( cit at t le Riscr ', . t 95! ) , ', ir r cllr r l nlr l ir r
rors(| ir1(:(i1i1tni,
de diverse etiotogii qi cu vdriate tocatizXri pe
clitc
;,ri rrrrl i o rnasi vi , tumcfi clc, cu ilspect t 1c , , nr Lcir t cii'" lN' it t lt 'r t t lr t ct r t lr r
:.4.2.l.l.1. AJecJiunile in lamatorii ale nerl)I.tlui,
r I rLri,rr'il canalului op1,ic.
wtic
:!.:4.l. /. l. l. Perinct:ritele,optice (nearitele
lrr lrr!r unui tablou dc papilit[ trebuio sii plecizitrrl .lut,lrttii r lio1ul,,
rr.lrlczirriiio irrIllLrnl.r,t,io
Drim:rri, a, tecilor nprl
//ri
r l )r' i n i nvesti ga.{ ,i isi si em at r iccqi r ninulioase: a. ) inlcc( ii kx, r t L' r r lt t l. r t r :
,,
rlrr olrir,ci,r,xtcrrsicirrlui pr.ocesinflamatrol Ae fa'r"eilinld"'Ja"
.i" fa
r rr,l ,ri ,i l l i te, coroi di t, pl i igi per f or at e inf cct at e alc glt t lr t t lt t i oct t i: r t ) ;
(
l') rrrrzii,o (anterioare, sfenoitialc qi ctmoitlale postcrirllurr) I tr) rrlirr'littrrr
r:ii]'ll:1,',;.1":i:,1^'j;'l:1.'.",':'si:l_::t11i.obi$nuilisinttacteitiepiugenc
lr r\ ul
r rru
tl l l,rl ,rro r, i, r lc it
rc l i n g i taa-SUpUrJlivi cprr.bro_spinalri i
ir illlii,
illl in nn|lrngrl
rrrII:rrrrrri ol i ial e urechi i me dii; t l) f ocar e dent ar e I c) ost oit t r I l) r r , lr r ii", r lr r
t,
-di fuzi uni
l(|i.|
o u; r Jr
rrl sr r l ((t,ut({r
l) r r k c ll)
s c nol-tt.
t. 19?1).
lrjl(lcr
ldcr sli
1 i l||l|st.
Sc
fir Scott,
l 9 7 l ). Este
E s l c vorba
v o rb a de ainzltfi in
trl, ; r1) inlrc!,ii generale (scarlatinl, variol[, folrrl'i,liloirlii, rlill'r'r ir', gli;rrr.
lrrl rr;rtir' :r|. rrrrr
rr'.rrcningite bazaie bacierie.ne1inc1u-sii
iaclarc S I
,,,Lrri rl i i -un, ti fos exantema t ic et c. ) ; h) papilit c lL, ll1( r $ilt l f it ll) ir ( llll( ,I t i, l
'rniiai,ato"ti
i'.1,):.,.'.',ii,'flll
lil)..1::ll::tsauale,altor p"occs"
rt' :rrr,rr,,5j i n scl eroz:l i n plici it llusr 'lu ocult t r ', it L lix: nillgo- cll( x llllil( :
l.l:1,',','f,':1,1
1
,il:]:l:rl:lij:_"1,"T:
sinuzjie
sfenoidar"
i,'alarc,se
r.r.
r1 rrrltrr{ii virotice ncurot'ropc (o{tralmonculoln itrlilrii, lrollrt lrti l)rrvirr;
;
::'l:
;:1,r,
I
ll
r'tinicc:
perinevrita
jl;:1,:1:
, r' , r' l rrl otni c-l i todemi el i ni za nt c; I t er pcs zost e: 'I cr r cr ialil, o; I t t t 't t iI t I '; iicr t r , t t lt '
l]l,i::,..1:llr,
, , 1rlr l ri p
rrr.rrllt t ll' 1, .
"pii.a"".iiaJii"#c;ilr;I
,i , ,l i v| ' i so nai uri ).
|)iIr11rrosl,icrrJ
trsto orientat de: contextul general
lil N c1)ritct,apticd, refrahulhard &clttii' :tan' stthur"utii (t;lndnntttrl 7r'slt
/,,r/
s{ , < uracteri zeaaX , i Ir plincipilr , sPt r l t lt r osclr it t r t lt l piLlt ikrt li, t 'r 'illt
-irn"eor,
/
pollrurli
r"rre cx_plic:iambliopia * $i cu la*traiua
.
*
a
ved
rl
rrrl
b:rri l , pri n l i ps:l sa r r r I isclef ia, m or lif icii, r ilol t t ] t ir xl, ivc r r llr t lt r t t r st r r t
l
rrri
,rcrrllrr,|r,).
r.rrtr':rL.)lrr r,rz,rl
cu,zlrlriirprr
ili"i qi
dispari,tiei
a vecleiii centiale se lnsiJeaza o
ti-;-;.d.;ii
|
rrr
i tchi mb pri n prczo nl'll ilr alilor l, t t lbut i i vizt t lt Lr lt t t it '{iot I I t hr .
l ' r(
a-eclematui
pupitr" ;"riuiloio" q,
;i consecin{d
!txtrioristici
:lllj,,.ll.',11:1,
f,ln
I
clinil : lt) l)cl)Ii, l)l'ujr(f, itt c,ilcvu, ziL' trrrlizitttitt tlr' ,,
('l' llr'{.
I it l)j' J o .
"
,l l r.r,r' r, rl l l rnati c:i a tcrti 1 t if ii vizr t lt lt r , pir r ii' l: l ct 't t ilr t 'lr t(rt t t t t r t t t t lt zii) t r ot t t
1,1l :i , cl ri l rl ctt rl i sprtri {,i ir ,pt r tcoplit r i I t lt nilt lt it . st '; lr ) ilt r it r lr r t 'r 'lrlt r r t t ilir {ir
, trt ir r sr l{, i1iit lir lt lgii or lr ilt lr t r slt lt lt r , t iot 'lt ilir , t r ',r 'sr t
r ri rr:rl ,rci i { ,r pt' ouxl tt,l i i si
..r'rr.1;rl. neyritc optice) iealizeaa:i.tabtorii
r ' lr 'r il
r,r' l rrl (' sl l ,l r tl t' t,l l rtql l l ri l o l t lr t i r iililo gk r ilol t t ( lt llllr i ; r i) iJ( r ai( l'll( 'rv1\
t1escciiuJ
afecrdrii
vu,ur"ti"i""-,iitrirJ"f"Si."
;t;;;'fr
up0rc: pc pl.rma
por
. i Ll rl i ,r,rIl .i { (i i l rfitrtrtti
t
""".*. *,:.:i."
l i col o t t t t t ct t lt 'i llt , t t r r t t i t lit r t t , t lsit t t li, t t t t lr lt i 31r ; 1lt t t l,
li:::f:.lll,f13"ll:
.rr|r
il.i,",
I
cl.recuprinde ptpila ".r-""l"i
.irrrl:llrrrllrarJ,
n(.r.1
ul opii(1lrirr;iI:r'zuuartc i
| | Jr' l ro,rl (f :rl ]ol rrrri i trl rr' { r , int llt t l vizt t lll ( lt 't t t t t t t t 't t t lc , , t t I l't ill'i t t lt r r llt r l
l vllsclor centratc atc t"ctrncrin lcrv "i(10_.LZ mln), realizindri-so
siud
l )l t| i r' | ,l LIll iLi i''r : oli, ll) 71) . llt r cr r l i t it r t I I ot t t t r I I '( 'I t ||ir |( r ll( \
l r rrrr :rri rr!r' i )'
Nrrl(,Jiol',i*xt,abuJbar, p4lilita sau sinrlrol.ul dri
_
,l r,:rr. l rr.rri rrl rrrtl l t,i ; rl ) 1' t r cr r zt t t ilr . Fiit r 'r 1, , ( t l : r I r , r 'I I t t r , : rit t lt l, gt t lt t i t t t , tt
lrilpil. rr.vrilr;.i,.domz
I.rrsii,ircrr1,l'l'
srrusrrlliriltrfii;il' (r)r:r lx)r{rrt,r', r.rr.olrrrlrr:'ii,irrl,itrsr,i
l \'lt t t r t t lt
st 't t , llt l'l"i) ,$( ' ilt lllt lllr zli ( ) illr lillll! ) zll lolll
rlrrI
l ,,l ( vl i l i i | | i rtIri | r,Ii .i i ' '
"i'#trXl:::iu^K:T:##,ffi:-ii"$:iilrTi,l":?Xr*,J
,,,'',,iJrv'ffi
tlllLLi,'#'ii?'ifdi""lffi
"'f"""11?Y1
i?:{?::;,;,i:!:,"'i##ii
#,l:'tiH"
i'_lTi,$"",i,",1
r:I l'lr!{,?i'[]i,'i1iii."1iL,slf
se
j:311",
se
Lci' oiieiene#iea
tap ae
]jlj,,lltu'l]:l;.,o:11 llry:fant
"':?n
"fiff,
,1.,,,ir1.,1i,!.1.,,fl"'l:.it'i,
J"i,*"
-l'iTl,:*gx,"ll,';ji,:l*$"1
l6
l't
l)l.lfl,,ll
r''I'l
,,,l.
r.rrl,r'l'rlllnritr
. |rl{'(x)lor.itr.
o
| {' { || | )| I r Dlpih'1.1,,
prr
li1,_(lr.
rtr. ,,fricci
obicei
t"mporatit,
f'enrpo.a
lrih
t,i. it,ii.,,,;;;i'
rt'i rr,llir,ro
,;;,,,,,.,,,
rrn riisnraf
nn
rliscrot
,j1lf,;'rt,'t,it,,.
(tt.s.'-ryi.Ashrvorrh,
rsos,'oit*U'd;"ijor.,"
iir,r""
gi Scott,
I n71).
;;i^1xrs.to|io.rl
c) ; .e) Oftalinoneu"rpj:llte ft;;i;'t"ib;;;;;
ty no".
virotic(.(ruieotd,
parolirtild
or.ioiil'ur,c"ira"e
:]ll,l Ii:l.l-,1
\':tlrorr.it,,
zonil zoster, variceld,l--bacteriene
"piau-i.;,
(diverse), riclettsiene qi
(in special mataria, 'irip,a,no^*]r;r- qi;;Aiiiiloza)
t,rr,l(.,,,{'irr(.
; s)
, l t r r l , ,, r t r rr t , . I r i . r r r .r'r';r
r ;:i i , r i .
l ) ( ) l ,.tt.l l r l i l .i .r r l l ,i i ( i r l r r r l i ;r g tr ,si ,i . r i i l i r 'r ,l r
'. t k r
r ' l ', r l 'r t r t . r , . i r l l l , t'i i i r r r r r l l , .r t .i l i tr l 'r r l r .l r
\,1 ,( i ( ,1 ,( r.H
i l t,r , l l ,'i tv
llBt '
; t , ; r , 'r l r
I t r l : r t'r l r i r ':t tl r l r l i tr g r r 0 sl l r ,, ( i r r i tr r l sr .r r r tl tr{l o t,ttl i ,l n ) l tr r ,L ,
l l l r t ', t r
pllt.lll
l 'r r l r r l : r r r r I r I r o Ir i r .i r .tl r r r r ;r i l l r ,tr s,l r r i i l .r r r l l ,z:r
vl ,'{\t {x,l 't,i tl t. :l
. 'l ,
r
t t r l r r . r r r , I r r r r | . r l , r l r l r . , r .|l r 'r ||u l r r fl i r i l l r l Isl o l i r a r ,l ,0 r ,r l ,i r r s, .l ,r ,r r r ,Lsi
lrl lrull
r.', lr,.rrr,,r'irAiil,,
ilini,.llll{lr,r)itsrr
pr, irril.g
;ri Iilrr,l,rrrixl,irrsrr
Sll. ll:, l,:,1,,
lllltl'rl r,lrrr,r,, lrrrir l:r 1x.r'rli,r'ir,,
rl. lrlrr'u.rrl v.tr.Lrr,(.rr.lrr,rrrrri t,, irrlri
l ||
Fl i tl ,
ltt
chirrinii(in scopteiap_eltic
sauabofiFj qi p"oauceamaul
|r'r| iiir, :r,rrblir4rii,
irrsolite;i de suiclitate,re_marcatd
OulA ieqireatiin
.trr,(';trrr'r,l,oirHli,
rlo citeva
Examenuloftalmologicarald,ciieva elo.
're, nouropatiitoxicu , asiecf
rrnrrtr.rliti,r'rrrrl,irr,lo.tu,ff
de alte
isclemic aI rer^r,r.l,rrr.o
paloarea F.O.; TACR^estemult crescut[.
cu
lllll''l
i'',
,Iiliforme,.
I'rrlril.hr sirrl,
!1.,l:::l9ll.l"Irn,!,yii,,cu.srrimtorareaconeertrici a cimpurilorvi]
llill,i,.,
z : rr, . , (.l t i rl r: llt lt a Unet m p o rta n te a l ro fi i O p ti C e .
por realiza nevrite-optice, inctusiv papilte.
jl) ,,r,i::1,::.i^i
,,:!!r!!ci
1 | r'n.?rscnutt
rascutarepot produce
I toDtl)tt3(lt' r(
oeSe S(.,1.0
Afterinle gO lrtS0l,r,S0rl0 irr rIll,ul.oz{},
'
t' rl rl r' )
ti o l t n l l
tl t
ttr r u l u i
o Jr ti r j l \r l ,
r u r l i zi r , ctl ctr r o ;r
ll|'
(jilzaro
;;'i,r,' n(i r j n{,ir,r
retrobulbar6r cu scotom initial centrL,l,
"Ireyrltra"
rrlrrrrrIri_rlrro rrl,rnfiooptic:fi
progresivi, cu intens?i,
a papileir
"*ouor"u
t$2;
Eiiazzoni,
i6[f :
'lii],,i,jl:.1.,,,:11,1.s11""^o-3joas';,^{sf,annon,
;l:,1,:l';
lil,rr{i.rlrr l)1lrq-l!|lcr fi Scott, 19?i).
. -. N tu.r.oltutitr.o1tt.icd,chininicd apare in urma ingerilii cle dozo mari
(ci
l.v;r grrrrrrc).rltr
t'
I tltnlttlttnttlt
,
l l l t ; O) .
rrr.lris.r'li. vitriui,ii,.
fllrih r r'rrrt'',, r.rrrrrIr'
J)ur,rirrur'rir1,ur
,,p,ur.i{i,,i
ni,li
,,,
rrl;rr.
r,lc
filllr,l,,r
JxrlIi gnrllr,tcin il crLtttolii:
,rn,,,i'l,li'i",l,i"i,r;,iiil;;liil;llililii;lfi1'lilll;iillL
l,'t,,r,r',r,,,r
l4llirt
r,rr:rrrr.rr{it.ziuirir,r'1r,rpil,
r-ri,tirit,
vr;;,,;,i;ii
,,, rl..r :rs1).rr
r cllr r
.,'t:'rrirr
:,r,s,rrrr,,,r,'r,i
:in','"i
lillil,,lill;J,';i:i":i,,lii,;ii,,]::ljij'lij;l'1rNcor,"'|r'ii,,
r,r'r,
1,,,,,
'ij,ll,,,Il,'i,,1"1i,j,ljlili,1
,d,,,,1'
,ill:ilill::,i'il
ilxlillilii;l,ii;ili:",'
rl t rl r.l t' .rt rl r. r.i rrrtr r t zr r : r l t lr .
l l Fri l | l | | l
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;i l i 'r 'r i r i r l ,i r r r r i l .'.r ;r i r r i ''
;;,.
Il
(
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r
r
sl l tzi i l r l l l t) l l l l i r
l i |'r r tr r 'r l r .
r t r l t , r t r r l i 'l c t
ir,,.'
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r r l cr xr r r t i tt:ti n r l t'tttn u l
' l : I l . l 'l l a t t t i t t i i t i l r'l tr r ttr d i tr i t:r tttl i l e si 'l b so l tr l
(
1
117?):
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i i l l l l 'tl o r '
l t , , l t t t l t t t o t t t d ) 'i r t , : t l i xl ' :r ttti tl l i ( i
I
l r r l tr!
t )I I t I | | I t t t I t 't | | r 'r l r t otr ':tzi i vl r l i l r ( i i l r ' 1 r l 'r 'si tttti i.i tr I't'Ito IIti L Ittr '' L t
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lli l:ourn,"vin.
1;urotiL,rofiri";;l;1 ;;; ihtfingh,,,,,
p"oces"
io"ito'iitorii
[cet,,ti
i,;li']l)ii,]lll;'i'.i,*j,iJffi:"?Hff;jiilr"groa'n"'
ale ochillui : d.iversctumori, facomatoze,glaucom,
,,,,,1i*1,,1,,1'ri,,r,i
jilirtr,iy?:1g!f-t$d*e{;"#^{#:#y:!;:*{i
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o-orbitare,
mctistize,sarcoame.
etc.); ny li"ffii""i.#irql,
trrrr:,)r'r(r(dr.rlo(xic
lrouto-orbitare
; c) I,eziuni'i"til,m"i"G paraorhi
, 1( . I r . , I I I | .I i t .| . . o.t
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II,l t);ntl.trntii
...,., .,
prin,
cranio-e.mefalici:
factori
a1
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bitc ate-sinu,s\rlui
liOit",
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ti),rurrrori
intro""n"i"nl,
i
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, t,,,,
t,rrrrr.r,i
tlc ariri, clesfenoial,
tumori-_;il;fTril;i"ii;i;;ilii
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::l',;11:l;1.,1:,1:!:1,:,'1.:1l_qit,i:
r'1 \r rlr,,r'rrr:rlii
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iii'sto"gu_w"r
Ir.:rt: trrr ti,',,titirt.Lirusen:ir Trr"il"i;;i;;;;;^i;Jrl
urnaiis'nr,.-.,;l,i;;;"#"'lo, hcm:rl.,l
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.u-.liiiii"iocrinr.
i l,j,,ij;:i".) Iroli,s,r,.EJuine
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rIrri rt,i) .,i
; ) | )isyri,zia,
Iiilu,ri',sii,, lui riichte;;re;iitii^'f
"noE"oit^l"'{oJfta,lmir,
i.s,c"rri"iicotat,.,r rrl
x".
c:to.f,luluzti
:
ful
a)
Co-nstitufionale
; b) Sindrorrrrrtrrr
,,,",,) 1..,,,,",i:.f:..:t
li,"r'rrir'rl
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;iit, ";,, ,, ., ; ,, , , 11
.,t lt,l,t,,t.irilr rtrt|,i,,|,,r1itr,.
rk, lirlrlottlclirrir i,i oIlltlrtrrrlogir',
irr Irrrrrr(ic
'l
ttt
Ftr'
iif
t'
1 1 1 1l r l r r r r t's p :r 1 o l 1 r g i r ' t t I I: t t I t I t I ri I
I r , , , l , r r z : r I t t r r r r r l l l 'i l r l o l r l r l r i l i l "l t'
sr ' l ttr tt
r r " r 'r r p ,
l I r I I i I i I l r 'l r ' .\r 'st'r r i 1 i l r r l r r l r ' ( tl l l i s r r ' l r 'r '' l !l "i i ) '
r r l l r r ti l r i l o l
, I i , t rI t rt r1t rt. l i i s i t t r l t l r' tl . o t l r i l r ', :r l t' l i tttl r 'l r r t i l r' l ' r i i r l rr l r' ;i
:r l l n l tt
Ii
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! r r r l i ( ) q l i l l i i r tl t' ;;l i tttr i l {'t l I ' t | | I |{ )! I I | | ' fi
r r l t : r r i i r ',
1,,,,
1 ' I t rI I t | ,tI t | | | i | ( t t \ttl t:;l ttttl tr r l r t'tttl tr ttl : ' rt I I i I r rtI t' I t 1i r' ' l l l Ir r II1 I:tItI'
t t t rro t.t t I r' 1: l l ' r
, r t l , r r , . r t l r 't l o r l l : r l t r ' , , t 1, ' l rt t : t , : r t l l t i o r 'l l tl i i l r r l r r l i r l i r 'tr r ', 1 'r L '
i . t r I r i ( I | | | 'l l I i I l l r '.
t,r r,,
I I ) l t t l r t , r t t l , t l r t l t t rI t r r'
r 'r 'o "r 'r r l i ' o tl r r l :r t'r r ' r l r r ''tt|r 'l r L l 'r i 'tl r l i r ., r r |.l tr l t
': l t r r i , r l r :
't I I l t l t 't t t t t
I r '.1i ,
| , r r r r , r ; , t rr I i I
il\
l l l l :l
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rt 7 : I I : I
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r.4. pfioBLEME
Dti DIAGNostrrc
INRPATOLOGIA
SISTEMHL0R
rrrttN tl t,i ttl itt P rrrl rl i zl rt (Hlu ll Hr , luilt ilr , r r r r llr illr l, o r r lr , ,I I 1t ir r r r iI r I lt
1 lt f cllilol.
trl i r' ,l rt{i l tr fi :rzrrIi l o rl c
lr r r lr r llzii rrrrI I I,i 1I Irr) . , \ t r csl, cir r r lr t lr r r nr r lilillr lr , xr ,
l)olllo Ail)lt(jiit, foarto oxaal, ftt rrJtrl()t'ril pt[.irrrot1'
r'rr,rrrii
rrltr i irri l,.iilst,r,r',
l rr:ttr.l a l i nri i r. ti i ne[ fi z iolr gi|r , : : r ) , {r r l, ( . r . ior
_ 45. ; [ r r t ( . t
I.i :
I
,
r
,
r
.
r
l
, r i rrl cr.i or- 50" ; d) inf i, r olr r zir l
: li- , {0": t , ) nr r zr t l _ 4. - , ".
Bl I.i.miloreo ctmpului d( not it0lp ;tt pt.;t)irea,bin<,t.t,la1i.:-p
.1i,.
, :r rrr ctzul in care ochiul sdnii,toseste fixator, del afecta,t va suicri lirrril,rrir,a,
rrri;cirilor in maniera indicatd, mai sus. |n cazr in care ot,liul lxrllrrv
cnI'c_fixator, o-chiul sind,tos ya prezenta o extind.ere a cimpulrri rlrr Iixrr(,io
;,r"*.rm,m
:ififf*liflri,ilffi
i;$tiFrl
fu",x[
i';ffi
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f
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;3Hl*T.1
jiril"lr',',","ff j$ti:p1r,ir"*:r
,riri;r
ilft{i,:}}}"{*;1$
jiilililtf
t:flr.rriffi'ft;ffi
ri
ld'*f
T-pfroq:*ffi
jiri'i,r1ir,J'llidnilltl[lFt*l::r;i"ilr3rp;;1:;i*:""*r::
,,,,,'"iljli:ilil,iIii;,n:Ttj"i,{'fiii1"fii.
T\;:ii,,ilx."lljy,,
;l ilil:lixl
iiiljinrl:ii;rril{}1l*#il}:ryfffi$il,r1if#*#r,lxrY
Uii:i,ii*i**i$*,ii,;'tr'{it'1fi;,'{#:ffi{f;;i;g$
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t
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,,v:"
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ll;iil;ill'lx;''
d1?"iih:,,,"',,,,,'
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:,,,:iii:,:i[,i,!!i:,:ii,i,,,,:i,,ii,|inri'i:i{;*|;;,-*,1,
l0
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s
IN IN
IN I
+a
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v l .q K
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b
Fi?. 7. lnvestigalia unei diplopii priD paraliziea nelvului aotor ocular (xlfr|l (lr('l)l'
ochilLl sting fiind normal:
pc'e relr'znkli
i' llnii 'ln
.StiLla r6ie s-! Dllsl in fdta o.hi. ui Prrc ?d lnagnra @lorait F tufL
l mJ 8 i ' e a ro ' i e s " d P p l r. e ? e rr a l l r'', n l D u l r' s
a " o d i i ' l P n h o mo ri n
c onti nr ,o.Se i .r s " r v a'c a eLo
'oi
u
d
Fl
rr!
i
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Li r bol nav Ll D r i v es l es D r e D ar t.a
P J r' 1 e d
a c @ . i t a z j t i F d i E r8 i n i l . r: i , , d ' * " t i d e n u s d r' . l . r. t l n 1 i , ' l
.tr r gar a" o i i ptopi e or i ani al A j ,n" i sre , . u
pLn
drPrfr3:
spre
lEvrJ'
rn l -l r. i h ' L r! :
$ f i r i . . n F a f rs rt d r" .
,Ac eea.ii nv es r i r a!i e,d" r ,r i ,l a ro : n ' . c a t l a i a . ' i r
" , . rri ' n i -l rI
l I t r Fi s P r' o 5 2 l
d FP l " /
aa t
n$
u w
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UH
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r,-" I tf,Vt,,
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ill
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tt('
t t ] r lt,ir
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ltttil) jlr ,t
( ll,r ,l,l t
l :rl .tl
l )i p l u lt it r
t't i.illilti
I I t I t ) t) tIit) | ;| .
r ,tilc
r .{ r illizilliL
(.rl r||r
Iri
ri rl i i ,
r l,,
s$'l
,li:"lli:",:';,:#:;'#;:;,,:::!,,t:;,,","_3;',?'"J't,Jj'lil;,"i"
iyJffiil
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dttl
EE
rut
-l::::iiii.qinH't,iiiilt*,:,*.#ii,:;:,?#;,rl*,ru;11;,1*"*1".ru;; #
d
I;sS
t,r;lril:1ilriiiii,ll,$l1x-"#:'oin{ff
,;t*m:"*|i",:,*;lTg"%f.?
paralizie
"r."
:ll,rliliii;;t:i',ii,Jillll.t""ir.:'*-##
ji,i":;:-..#,J,jljf
;I r
,,,ii,,ii,'i,
riiicr
t'i". aparli:re mqchildr
;?d;L1'JJJ
fr#ii:flf #friH
.l"r, u t,rrrr.i.rkfiicicnla^;,,#ilX
conoriioi,i, ia"-iaca distanta
.rlrr lrr,irr.lintu.taspre in sus, este-vorbacle. p"";rt;;di;;#il;
lnr rlorri irrrrr,gini,
prin inclinz
rrr,rrr{r,lr,s
sc ilnlunc ileterm,,inarea.
ochiuluipi a mu-;ctttului
aJectat.Astfat,
c vollrl rlr ochiul drcpt, daci, imagineaiann
lrosle)est",ma, jos sau
,, I --T-----l
b,
I
1
I
I
genrrJ Ld d. l ' rr rl j r i l
Fi g. ,?. D i pl opi c
.
muqc hi ul ui obl i " marc (s ru onl l r s "Ir' r r(' r '
de partea c l reaptd, c nre h nl oti rror' rtl rrl
j" '
depl :c eaz e gl obul oc ul ar In af' uJ s i l rr
i rl i l i fnl
S ti c l a c ol orati (l i ni i obl i c e) s ' i
inaintea oehinlui PamliTrrt '
f"?:,iff;"|;;H"Jil"f,,",1J"J;'"ffi,,f1
rerpecbi_v
oblicirl
m,,
m,, ',o1
-o1
o-.ptond
2.4.2.1. Paralizia tctald' a nenu'lui oculomotoraomtLmilmpliax'
a
ilo
a'o{iuno
dirocliilein
imobil
glob
ocular
oo*rrieta ;i un
jos fi ind tol'ttqi itttt triu
""f""fr"aie
(mi;ci'rile
inferior
arupi
i"i"t",
ati,
i'rr(.rirr""
-".ii*"i
bbuc-mar'')|i drc'prsulx'ri'r
rnuqcbiului
,:ii*]"p"!u't" "Tir";"
St:rabi.imulttivirsent csbe foarte'evidenb, irr rliplopia cste orizontllfi ;r
ptpita este midriabicl $i ,,fixa", nercacfiolrirnl lr lttmitrii
i'"i"-ii*i,.
Ir! flcomodare gi la converAoo!6.
osl'o ltlllll
a nerawlui ocuLomotot coT'?lzzr,
2.4.2.2. Itaralizirt' parliatrd,
'corirplel,ri.
tttltttrrrtxt
cil'
fllrl'lll
rolinut
l)iur trcbuio
,no,iireoventl ,fecit oca
lrl th'btrlt
ulcc Irtin nl,rlrlitrlincompleL (prr'rlirLll
i,,itriitil
.lir'
prrrIirrlort
p:Lrlrlizii
Ar:r'sl:r'
",,i"ttt,ltr:
I'ii
.,',,,u
i,i,,..r.i""ii. ii,:'i"-i',,i*ui
1x'.'t 1r:rr:r'lizici'
ll),nN
$lrb
srt'tt
rl'rtrttti,
;;;;;ili,t blli,i,, s,,h t'rtrtil llzitrtrii 'iinoi sing.r.
lrol'vr)lr'
rrllllltl'i
rnttll,,t
tttr!i
ttr
tl.rr
iiii rr ,,*,,i,,ii vrr,r,itbil.rlo nrlr*rr*
^f(nJli[,tr)
vrrrirllriLl'tl ltit'tozohttHrlll l'lrrll
irr,bl,rrrlitltl iltl'trtrttltt'ttr
il,i,',ilii'li','n,,
'',',,fizol,zr1,
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rr ,,lrlr,
1t
r, ,.,,i/
1t,tt.,ti;:iilc
a.fectaroa pfr,(iorrr lt
llce\loI[L
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n lir
s( . r ,\ir li( ,1
,t
n ti,trntttr
,,:! rl rtt6ptl l i
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lrlr ,,rrl r l ir r ir , r r l r r nr it .r i ri c v rj s rrti ,rrl t, e c c s tr,rr' -]a " . .-l U i gr" ti ,,c,ftai rni pl egi ci ,
r1'.,r'r.r|. ,lri.r'i irr rr.lriliilio sa,uadolesilcnli, (tiickerst:iff, 19{l+), lr, siiliiircti
, , r',.rrrrrrr l, r , r . r jt ' t r llr
t ilig ro tl o a s o ,l i e ta m i l i a l e , fi e p erson:rl e. I{ i gl en:r, oftal
r rr, ,| 'l I r, rr I I ) : r i( . s ii l11r ' t,l l (fz 0 s a sl i r n i ' m c rz erl u p i i O n i grel ti si rnpl i . Il nrerOa
, l, l ,,l ,l , r r , r ir 1r ' ir r r r r ls i rtrl rl ,,rrr.l !:.r r,;1 c u n i l a te ra i l , cu i ol l l i i z:i r.e or1;i i i l i
||r ;r,,rr0r I r i( I r I iiI , i r , i | l td j 0 ro N l ]l ' { rv c tte x , i l p :rrc c obi cet 1l r cri zrl . cU
il, , l,rt l ',1 . ( 1 r li t , r r t . r r |irtrl ,u .
l tu l s :ri i l , ,rrl e s r.tii u, s rl rL r tl cr gr..r1,tisi r-i i r' si i tul i ,
1, , "r,.
rr ' r
I
l J u l (...\l
r,-.1 , fr o ,.,.t, ,,,.,,,,,i ;1,,,.
.,.i rrt,rz"tl :1,r.
' r ( t , ir . , r t , - ,
, , l. l ,l ;'i r., , ( , r r ) t r r lilui( ,l i r:rrtrrrru ti rl s i r0 a l i z o a z l -r,
.te l mai fr,({ rr1:er}t
o ati gcre
, r rrrrl rl lr:r-: r I r , r ' r ' r , lt iilr t rl l .rt, rc s p trc ti ri d u n c o ri i n e l vl l i i ti i :r1.r,i nseci i .l
, { o,
,lf l, .:r l \ r r . i r r 1lr r , r i rrl i tL t| r.r:s ti l ,0
rn u l t n l i ri l l t,, ai l csi rt, i t.rl soci rti | cu
.rlr r;,,.r'i :r 1r lr . r ' r , lr iil I l1 ri . In rrn d c c a .z rrl i p o a i .c fi i n1,(,i (,fi l l ri
, rrci .rul
, 'Jl: rl rr( (\ \ ' ir lr lr r i ( ) r l) { ri r(' rl )., l 1 } (i l ); .[1 .l rr.< u 1
r,.. 96$).S -rrLrrl t,s,ri i s l i rl Lnr:.
r rrr r( '" r':r'i r ( ' 1r ' r ' r z r l.r lt |rr,i p ri rr rl i Il o p i i 1 r,t:c i ioi :r,trr , l .l i l i i rl rucl ' i , sl Lr [0r,i rr0
rrllrrtr: rrl r., r ll r r r ir lr r . r r iri
i rn g rJ i 6 i ri ri ;' i r.r,rri
o il l :rl rrroIl r,i ri ti (l l < l l L:z5i S ol l rarli r, l l l ti l, ) - , , \ li' r , i, r r ll l rrrr,r,r' i Irr ,IIrrr| o rIrl rIrrl rrr.
i I i r[r1ori l i i rrrrri l rl rrrr:l l i r
'
. u, r ,ri o l l {r r ' \ ' i, it r Llr r ic rl rrl l o l j rrl l l r< ri rv t,r' i ro sl l,c l ti i r.rr :rt.l cl r rl rrrrrl i tl l i
rrl, 'r'''r, ,,i ' r . lr ' r ' z r r r lr r lr r.r' r.ti irl i l :rl ' (i rri .rIr,rrrrrIi Irti(\\,:rl rl r rri (),l rrl ri rl r,,
ll) t ; l l t.
4t l
l i \ l l r t t t l r t ttttr r l r l r ' l tttr tt,r ,,r t'tt,ttt; \ttl ) t't i ( 'ttti t ( N tttt r l , l ,ttl r t :.1 |tt,,i i 'r l i )
rrt tl I t , rrt t t t r' , ( l l l l ) l l r r l l l r r l l l l l l l 'i l zl l ( l i r ,r ', t' l l t
t . ( , l l i / r 'i t z r i . r l r ' 1 r r 1 r 1 ,r r l u r r r l l r .
| o l r r l r . " l l ) ( i l l ; l i i r i ,l . l l l .,i l ) :
i\) fiirult'onl1ti. t:lu,si tlt l,rttltr. x.ltttrtidulii, rtl. lui lirrhtttt I)trtir1ttrurt| :it'
c a i t a {r t e r i z e a T . [ ]xi u 1 ,1 '( ] l ) l r l r l l i zi l ' l l ( l cl o l 1 ,1 |i l l ( l r vi o ( 'l l l 1 ]1 l Io i ( ni . i l l i r i L l l i r l ( '
Sc r e :i l i ztl r tzi i : l l l l Ji l l 'r i ( '\( ) l l i r l l l ) i ( '
a f e c t a r ( 'a f f ) n c o n r i te n ti r , ti o l l a h u i o u l u i '
( u q o l r e d u c l i b il i ) ,, p to zi , p a l p e b r a l i ,
o l ta l m o p l e g i r ' ( r 'tr vJo l r ( ,( 'IIIi II ( I) ||II) I( '|'
imobil lrin 1lalalizia le.rechilor III' lYSi YI), trxttliticitri 1)lrl)iLrl!' (lirilril:i
areactir.-i la luminii Si la acomodare), hipo - silit lnestozi(r itr 1r'r'ilo|irtl
4'I
l"i
$i llosor' l!)(ill; {lilrlr,lr',1
likx,,iwirr
'
rt,Iosl; tloslrl'istkr Ifisclrot'-llriiAgl
,r' t'littttsu,lrti
de ar(xutltL
t; Bi)mtrom'u'l'
tl..r'i,ltrr
<,ttttttttt
(x)t'l)r.('Hilrrii
.crvttlui
(Lgiiffili se da;torc'Uo
'cltltttttttl,,t'
t[. sltitl'itt (rxlrttr
,,i'castailivus'lui, ca urttt:iro , proccsclol hrloc,it'lr.
ittsl'alaro rt' 1ta'l'rtlizit'i
hematorir subdulat q.a.i. Succcsiunea
-de
"eiebral,
lrritf iazr'i' ;-i
unilaterali
miozi tranziiorie
,,ste
I I [-rt'
'r'in5,toa.rea:
a perccltii l' 'rrpili'
paralizie
ptozd
palpebrali'
completi
in
final,
fixd itt t"'ttt'
Fischer:Briigi iiolo; a izolat dou5, forms clinic-e: a) lorma aau't'd',
i
naralizia ocirloniotorrllui este urtratd, ime4iat de pierderea o111lofliilrfoi
i,' Surn,nprogresiad,,
in care paralizia perechii a [II-l sc.ast.rci:rziitr tttrNI
lreplar cu somnolenli qi apoi cu piertlerea cunostrntol'
' H1 Bindromul Iotoia-Eunt' Olialm'oplegiadureroasd"(sitrtltrrtn-ttllir.
tosa-gi*t) reprezintd, entitatea nosologic-5,.incatc se-asociazii o oft;n'ltnopf"ei"
o ndrratgie brigeminalSde aceeagiparte' Tolos:r (I9j41 a. tk'rctir+
"u
itriimunfeeia, dur-eroasi la ul caz cu le'iunj peria.rteriulc :rlo ritirrrrrlrri
llunt gi colab. (1961) la qaso cazuri cu inflamalii gri ttrlo"r"otioini.-iut
lente ale sinusului ealvernos' Smith qi Taxtlal (1966) alr folo$il'
-rJomu de ,,sind.rom Tolosa-Ilultt', Ia cazurile care au lespuns tavoltltil
iermenut
ta tra'tamentui cu corticosteroizi. ln acest fel se pare ci' se t'intlo sit' srr
fac6 o clistinclie clari, fa!d, de alte sintlroame asemdnii'toarc, diu'.citrtr
iini produse de'leziuni, in s1]ecialtumoralo sau inflamatolii, care tttt ctrtltrltzii
oromnt la tratamentul cu torticosteroizi (Other. 1967; '\tilslcitr ;i [lottr'.
iio, ibzi; nnllf,lt". 19?3)' Lapresle qi Desi (197?) considct'ricii It'r'rttrrttttl
('!,t{) llll n(!
tle'sindroin Toiosajllunt trebuie folo8it numai la caz*rile la
etiologia'
poate stabili cu certitudine
Mai recent, I[unt (19?6) a stabilit urms,toarele criierii pclrl'm tLingttttx
ticul tle sindrom fotosa-nunt : a) Criteriwl, anat'omic: deficitul tttrtttolttgitt
prin leziuni la nivelul sinusului cavernos anterior qi nl fisru,ii
"*i"-prio",
ornitiale sun,jri"are. Structurile care pot fi implicate incltd nervii rttrttlo
oftalmic, fibrele pupiloiilatatoari parasimlrilf ico tt l trrt'trt' l l i i
*.io"i,
""ii"t
a IIf-a, qi fibrele pupiloconstricloaresimpatice ale ple\u1Li lttlritlilttrl,irIirltt.
b) Cri,t'eriut etiolioi6 qi' terapeu'tic: atingerea forrna{'iunikrr ilmittlil'rt csl'r'
iiatizatA de un iirodes inflamator granuloma'tos oronicr 1i botrigtt, citto
reaclioneazd, favorabil 1a corticoterapie.
Cafuu,I'notologioolsindrom,nt'lui'Iolow'Huntloa[()1:irtstl'olsist'rrttt;t
tiza't {I[unt, I961; 19?6; Lapreslo qi I}'''i. ll}77) : ir) rrl'rrrl itr I'trrltrrt(it
'i* ambele spxe; b) debutul mL ci'" lcciLt do ryirsl.ir(rlitr .tr1,iI:'itit'
o) (l('l)lll'lrl
"nufl
rrlo; it A""ua" a VI-;), cu predominlr,rtl,llll virsLtdonrii6cii;
(lo-?l
lllloi
llllrglrl
tti;n1to
ilaie fi nroelesiv, in citcv:l zile sau in inni tntLlto
()sto
lllllll'1r
olro
rlc
nai
<xtnsl,rlrtt'
debut
ce1
ii,ota-itrii; ii) seninul
oontx)lllil'(rrll(111
oftalmoplogici,
'Lrre're&'
br-usc, de obicci ct clt(rvr zilo ina,ittl,oa'
I
oIl':rlttt'1llt'gi.i
tItt':i
itr:rlrlrtLtu'
oaar*iu, *uu, iu rarc cirzurirll l,niirr lilrtlr
gontrraL',
r:tr.Irrlrt'ii'
slirii
([t'buleazi
:tli,,ralr'a
air'ctiunea
;i-;;r"i
Filr
rnodeTAtd;f) dUrerea esLellnilAtol:llii, 'crlr.'i;itrrI rl{1t(gttlii 1r!rrlt)rl.lll
oital*ic, raroo'i prezonLin{f i*,rliri'. ilr horrrir:rarrju;g) rlrrorilo
pnroxitttioo. qi. u'0o U)il'""i,o,"li.i
sin't severe, cu caracl,cr contitnru ii urt oxu'c"arbrtrri
:r,ti.,"r,nzii,ou na,t ll1rI trrllrrrrilr'i
tn t'ori
do eurLsibilil;rr'i'.
iii^iu ao
'5icri'ivo ttltxiltr qi ortr.''r{illtttl
lrrl,vltlrri
iirririf n-ffii-i",1lrri, urrtrrri hr i,r,r,iI,r,irrI
ir, ,*t .,1 rrurvrrlrri'lrra,lrdibul,.r;h) olil,n,hnollogit,1xrrr10li tlo rttit,itttttll,o
iiprii;i I ,rxtornn cornplri;ll, (liit rtirr r,rrzrrti)I li,ti'g.r'. oxt,rl.n.cll, izulnl;ll,
:tr,r::i,:,1:;t,;,*,ii#x;!i:x*[ffi
ffir:;li#j:P"*:Trl;:3:;
l' tii,;;ll,l;
;t;t*:ll,*lt,ru
til;,"l;l;fu".,?ftritlts#Hl;{i
^t"'ito"iuriliiifri".\i.ii
Ff
i"
p""uri,ia
perechilor
I ;;..;i'ii ']'l1l'|fili*,1:"'n'*"
Eoger
qicorab.,
1e0e
qideArseni
qicorab.,
,,,r,i,;j,:iill,JllI:i,,gl?j"t:
tr) t|,in.d,rornulanNerior-e,ste identic
cu sindromul de
. fisurX orbitard,
ri lrr,r,r{|lrrii,
(cu coafeCtare&qi
nervu]ui opU"l.'^--*
-a
tt) N,intlromul med,,iancoafecte?zd,
to.,i icuiomotorii 6i primele rloud,
j,lilil!lT:f;it*.1i{1'jx'H',",r"1,Hffi
j?rtl#
J:l:l:l
1r;ll"t*;;":nf,I;i
atecteazd,:.
toateramurire
,,,,,,j;l ll;iilj;fif'l
"#:mi:
ri:;,r;ni;,**uili::,,J,ffi
#i'"'#m'Fl:,-k*#?#i
;iil;litil;'li",ll:,T,1#**,ff
r rrrp | 'r.l i l i rr(| ( , r rI iic t ' im are ),
;Hr,i"#fd
i'*1116*:f1ti*_T,%trf
p
:ry,,,rr,,r,1,riirrri,li;l,,1if
?*1i"-?H1fl*T*1":i'fli*i"",S1llf
fml*:
seadaugr'
d pQ'tro'
l)ariantii,:
,,,,,,,,',t'1,t,,"'i,l,i"'i;'i,"0!,rll.on')
sindromut'
gtaratrise-
,,,,,,,,1,1,,,'11i,11:,T,ill,;il,H11i,f,l"Jifig:'.ljx"l?,:i"tfdeosebi
"'anior,rin-
tigt!,",",Lq;
i;,llll,,ll)(;ili,'ii,1,,,,,,".,,'*i*l,'iff-:"'i;"if,fl:x;"^'ii*iiL
conmn
(curorlizal,oa,
a" r"r,f,l'r""i ori;,nroprosii
lil:jl,l,,;iililli:11;lrrlui
t8
{o
lr:rrlrrlir Iit
loltrltr : r lr r , r , r , r . lt t |: r lllt r
( l/ il r lr r r r r . . l l l r r
r | r , r . r . r , : tt i l i ) t 1 l i r i l
i" r,,r' lr rr lt \ | :r { l.'., r lt r r , . : r z r r r . r ) ; ! : |l. t : t ir , I r , ||r l|l|l i r l r r . r l , , , r r r I r , I , r I
rIr. .riirr,,r,r,rr
r' , . rr' t
tr,,t ||r.rtIr)r r ||LI I LI I I ) |. I i i) ] llil|lir . r ! . ir l| | 1 t , .
. I l I II(,I 1| r , i l . r \
l,l r]t
/
I
I
I
I
' ir ol| t ]:rltl.t l:l', {lil ( , ir z ||r i)
Lr t ; r |jlr lr ilir : r ir , l r , , l l r j t l t t l | . r i t l l l | l l r . t j r z r l
rr. : rr, lirr .liu t Jltlirr |, ( , I I r , i|\ . j. r , . l) t 1. , r l. t t f ir( [ c
lr . / , : l r . . r 1 , . , r . , , , r r ,1 , , r l i , , r r l r r i , , ,
t,rtirz: r rrrrlrt :r rlr, l|z:t t r , r r s ir r r lr : r , iii, , r t lr r i
nlr u r r illl l r l ] ( , t , , , ', , r , . 1 , r , , , 1 r | t ,
1,ortl,. ll
rl,, ,.lirir
r |r ,
'l,lr lrlollr r ur I ir . r . lr r .I
l, , t ll, ir , , , , l , l , , , l , , i i s {, l }r ) i r r {f r {, l l }l l i , t l
I ilrrr!r'lt. :r.,,r'r'\ lilllj olt l, ic ( 1,.' {I ) ( [ ilr ,I(,,r;rtlli.
Zt U, i) it , t g r l r r t , . r ] , , r , I t l l i i 0 ,
Ou InrN;i,ii;
1 r. : r . r l,itiiir.i
rro ([ili( jir . ilor . I r r nt lr r lr r i dn oc hi
; lr) \,.S.lI. cste rirxlr,r,rrl
,
,]:l.ll:.ll'].:lril_ll,,.lt,,,t,rrlt'rlfla
in unete
cazuri
ouilpr""et"coriiri,.,iii
],,,]i,l;1,,
'|| rr. t r , : r \ ' . . r . 1. o \.:r o o l ,.trrr.tj F a r.e n C io fl al rni ce
.i
l fl ,,r
l tui l S r,,i n
r',.lrrr,tlrl'l ; S,rrrllr.irrL.r.
si ltrrlpp, 19?3); n) sirr.pto_,ii"
pritil;;;i,,
-u
.,rr. .:i;rr:irrrirri p(rl p.ozcnl,,-rbmisiuni
spontan'e,- neori cu defit.it.
.f,i
rr.zrr rirrr.: (,) l:cnomcn.,lo
',: '.,,11',19,,,:
pol .reapFrolr jnterval, dr. lrrrrl
' ,.i'.,; ll urn:tglr, slulrlntn:tlologierispunde [rlorabil la ldmhistr:rrr.:r,
,,'l
or){Urilr(hr-seunoo4 o remisiune complerd, ilr
cil,ovrr,
i,llllli::, i'll:'!il},
,l::'.1:l:ljlll.rl
,,1
\riu'c:,I ezj: :^lapr.es
tesi Desi.reTi);r) rtinprrrrr.r
.,
::',,i::.1r,rl'Ntrlg,.lr. .r. disculi
,'. ,,,rl11,
Iie exislenla Lmui proces i:rfllm:rlol.
,|| rI rrII Ir,| |IiI |,'.t
I)fi 1rs.r.l.t,urno,l
1g73 ;' flult, iOfOl,
.(IIallpikc,
-Clanhyti" a ii,,,,i,
Jtr,r'r',,r'irrurrilrrrl| cil Ia clzrDile. Aeicrise Oe-Uathe*
0l.
{i
ri',rr,r,"rrr:rr,,r,rsi:r
criuici, a sindromllui rolosa-rrnirt poate-fiilSf
intilirir,ir
t I t (4 t ut ttt tt't r t ttt tn ) e care:,par prin afeCtarea
aceleagfzOnetopOUrl,li|r,
',, ilr. r':rr,{r
lrrrl'ri. sri,-ldiferenlie-m,,ieqi
a" di'iiiii,,f
. 'rritrlurlrl lrrrrl,r,isfcnoirl:ile( iloctton_Duvigueaud)
"""orie;t;-0.#Jit
b) Si"O"omut
;
lrrr ,r"Iri|,:rr,
(|IrII'rI,) ; c) Sindroamelesin.sului cavtrnos;
"1ru*ii,
cLl Sintlromrrl
rt,,
r:',,lrrrlrr.
(Jacoti) ; e) Sindromul pereielui extern al si,,r,
rrirr ,,ir,y(,rtr)s
lnrix) ; ii) S."l,lr.uryrt paratrig6minai al lui
'.i,rrrslirlr.irlalri
Raerl,,r,;
''ti'rrrIr''trrrrrrIrrri.(
rr) sinrtromirrtle dff'us aiiui-r,isoner-griilrg,,.
,l.olosir,-Hunt,
l) lrr ;rl;r,nr,sirrrlr.orrrrrltri
'rrrr.rrirxo;
a,cirui etiopatogenie a 1it$l
ri r rlrrl: rl:r rrlri srlri, o.ll alnoll( :
fi produsii,'tit d. crrrzr,
|to^te
..,.rl,.ril ll.,
r.rr ri rr. ,,^u"r,,r,rr!|]!o.t"t'eroasd
'i'ililli1,,":!:::,i!::,,i:,:,,{,i#[":,ii,,iil*fr,1i,\iJ,"?:rlif,fJJ,,,:flj;.'i;iililli
,,t,1,:,1
i'i :, i
r l r ttItr r r r 'l l l l r l /r l r |
Ir |,
l r ) ( 'r r r t z r 'l r . r 't l r 'tttr r t Ir 'r i 'Ir |,
''IIIr Itttr r 1 r Ir ';1 r |r
, r t t t t t l t l o t t t r t t u t r r t/r 1 1 r to r 'r 'rI r ' l r .r l r ;r r r ', tttItI|'It tttIt{i i t:t r |tr l l r tr " tttl t t'l
,, I|ir.:r|( ).
r 'r r tr r r ' l r xr l r l i zt'l tzi i l i t tl i vt'l tr l i tl r l r tl l tti
l 'r r x t 't r r l t r c t ;tl tttsi t,
'r tl r i l l r l '
'l 'l tr ttr r l t:l si \ 'r r r - r l l l l i ( l )
r l I r r l I t r o i t l i t l l . s l t i t l O.i i i r ,:r t,"r 'r r 0 r r r r ,tr 'l r r l r zi l ti 'i 'tl ttl i i i
, r t ' , , r l i t t l o l : t l t t l ( ' r l l l zt;i {) l l l tl l r l cl ct ttti tti t, l r l i tl l l r tr o l l r r g i i l l l l l cl o r tst" "r 't:t '''
( l !r l
. , , r , , l , r r l r i i . . i r r r t t l l t l ttl tr l l ti ,,\tr i i 'r r i ;i co l r l b . ( 1 f) ? ? ) . U l t 1 IItItIo II1 i t.i( l ( r l i i l ";,
ttr
tz't
ttr
xr
l
tl
r
tsl
r
t
l
tl
l
l
l
i
r
l
r
t
i
r
L
r
:ttl
i
l
tr
l
t'
(
(
)
l
l
sti
i
i
l
i
l
,
fi o
t , ', , , , r r l . l I i , x p l t t L , s ir - e csto
(
iII *
i ',
I i c r l c r i r tta sta zc cl r e p r o vi r l d e l i l n t',o l r l l sttl ' l l r i l i I I I I | ' | ' i i t I
'r r : i : r t r ,
ttIr
Ittr
rr
Itt[t
l
ttr
"
(
n
l
e
tti
n
g
i
o
l
t
p r i m i ti ve
I r r L r ': t z i t t t t n o l i l t r
i n tr a cl a n i o n i ,
( 'l ( 1 ) ' l ,t'{'r l 'tl
o
0
i
d
e
l
r
n
o
j
(
l
o
tu
m
o
r
i
I t , , r i i r r r r r r , , c n r t t i o l i u t i n g i o a m e , '(osteoame,
co r d o a m e J
mieloame, silrcoallti) rrh' ) ('\r'rrcrri
r t rrrrrolil<' ,,ru,t*,, 1,r'imitive
, ,i
Dintrnerviibciiornoturr,
0t,l rlri
, ' l l , 1..,', ::.,it r.' '.:ir,t i:lt s.lf',,1i..ir',,]..1e?{)).
, . lv l l l )(l l to (,i rs , tu ,rrta ,1 ,
t r l r , : r t l r , rr ,r |l r to i t( |,
l , , r l , r 'l | : r r 'r ' r : t r t r tl , :tti ,'tIi
,,,rrrl
r , , 't t I o t t t , , Ir !I ( i l r r tl r r l
,rr.rrr,.
'.;i
;;;,;,;:r
:rir;m;
l:llririliiixt,,liilii;ilril;iri::iiii:r,li,,l,,ij11liil,'i'rl]rr11
t r ( 'l l r l i r
l r r r l r r r o r j l r zi i , i tr r r r ,l r r r l ) r 'o ( l l l so r L o l r .zl l 'o tr ti I,t'ttr r |.ttl i Ir tt'r {,r \'r Jl r {r t
l l l \ '( r 't l l i l l l '.
r l l i tl i z{.:r zi 'i
t J i n r . l n t t u l l l u n i tl ,r
I,,r .l r r l ,tl l ( Vi cl o l q i r ,o l r r l t,, l l ) i l ) ,
'\ )r t n l t o l o g i r r
. i t t r l t {r
ti .i tt i r l r r zi l r ,,l r o l i o cttctr l .a l i td , l r cttl ,r i Itr tttu r t:r ti ''i r sr p ,ti t'lt'i"
(:iintlrontul
Gttllrl ll rtnitlit:).
Sernuele eiLrtlitrirlc it,lc :rcrrsl,ui riitt-
t;;::''ili:ii,,l;iilfixr;,,iiiil[*"jlti4!ij1l{i"i1l;rlJl:,|':l'';]-:'"r
I :l;r'r,i;i;lillj;
';il;i;ji:[ji],iil,1j;.",:ii{i:[]:l,ffiiJ1,J*1-i,,i'{#;i;
rlrorr sint : a) oftalmrplt,gic [rilrrl,elalti in glatkr (lifoli1,(r; lr) sorrrrrolcritri: c) ataxie; it) lis1,:i,grnus;e) delir in faza acul;li rii stalo arrrtrcslilo
r,oufabulatoriein fazele tardile. Pzrraliz:iileocukimol,olilor sinl rrrrclrrirlr,,
incomplete sau ctlmplete, cu prezenla la peste 50]i din cazuli r lrlozci
|:rlpr'lrrale fi cu oxistenla rrneoti a t'ulburirilor pupilalo. Acrsl sinrlrorrr
1,s11'rrodus printr-un defic,it de tiamind, (etilism, tuibuliiri rnol,ulxrlilr').
B) Bintlromu,l I{estenbaum ( Bindronlul periapetlttataL) rcr,lizoir,zii rrrr
rontp\l, clinic constituit tlintr'-un sindrom Parinr"ud, la, c:ne sc rrsLrcirrzri,
irisf:rqmusdisju:rctiv, mioclonii oculo-retractorii, tulburiiri pupilaro ryipnllzc
rLuclea,re
ale perechilor III ;i IY.In acest sintlrom este aiectal,ii srrlrslrur{rr,
cem;ie pei iapcrluctala, nucleii oculomotori si barLtleletlL,
longil,rrriirrrrlii,
posterioarS,. Leziiutile cele mai fr"ecvente sint da natut'il infcclioasr'i s:r,rr
ischernicii, (ocluzii rle arterelor plandui posterior al pediculului rotr.urnrlrniler, sari ale ilsusi pediculu.lui retromamilar (Aqgian ryi Vuil, I l)5$ ;
Pop.r.icir, 1965 ; Popoviciu $i Afgian, 196E ; Aqgian li cola,l)., I l)71-i).
Zona responsabili de aparilia sindromului I{estenbaum este replczcnl rrl,lr,
de un sistern morfo'fu:rclional periapeductal mezercefalo-diencciir,lic, crrrtr
rrrc conexiuni cu nucleii oculomotorului qi cu centrii oculogiri din tnrntlrirrl
cerebral, prin comisura albii, posterioari qi prin bandcleta krngil,rrrlirrrlli,
posterioarl (Bentler, 1965; Taube qi colab. 1965; Pasik, 1965 I Sh rzor,,
1965 - citaii cie Popoviciu qi A,;gian, 1968). Popoviciu $i ADgirn (l lxis)
nu plopus - pontru fenomenul de ,,nistagmus retractorius" * torrrrrrrrrl
de ,,mioclonie oculoretractorie", ari,tind ci aceasta are ca, substrnt rnollirlogic leziuni vasculare sau infectioase, reversibile sau irevcr.sibile, ils('til,o
de multe oii de hipersomnii qi de mutisms akinetice (Popoviciu qi collb.,
1980).
C) Sindromrr,l Lgle (o vaiantd a sindromului Kestenbaum) Bo (litrrl(iteuzeazd, fie prin palalizie bilaterali, ile new oculomotor connnr (1n
midriazS,,sonuolertri fi uneori paralizia miqcd,rilor riculare cle vcrticir,lil;rrttr,
{ie prin spasm de convor'gentd,qi mioz6,. I:eziunile rcsponsabilo dtr }rorl.rrrxrlea acestui sindrom sint de naturi, inflamatorie sau.prolifclai,ivi,.
D) Leeiuni,le ttu,cleureala ocxr,lonxoton
,ui comun, tnai illos ookt rlo
naturd sifilitici, duc, la teducerea tonusului in murschii oculnri, irr sprr,irr,l
al ridicitorului pleoapei superioare qi, in conseciniai,,la a,parilia urroi pl,ozo
lalpebrale bilaterale. fL unel) cazuri, diferenlicroa fu,lii rlo sinrlrornrrl
Olaude Bernard-Ilorner este thficilS,.
E) Sindlornwl arterei. nuclatr,lwi, oculornotorull,wicornu.n (ALlllolli 4i
cola,b., 1952) implic5, afectarea n ucleului oculomotomlui oonrun, nn{,loii
(,omisurii posterioare gi conexiunilc vestibulo-cortir:a,lo.Artoril rrrr0lorrlrti
perechii a Il.I-a pare s5,tic o ramurti a artoroi sulorrsrrluihtonll, rrrxlrrrrl,iv
tu a,nastomozii intro artcra cc,rebeloasi, supotionril, {i itrbolr! corrrlrrir,lrl,
ix.rsber io i n'ir,.
'Ir) $iw)romnl Lwl Aaenlald, Sohuranberggi llu,m'pol,tli(nil;rr,trlo
Alsorri
ilirglu,r'u
lirilr,totar[, oir,r'llc1;or.iznlii
plin uxisl,rrtrf,u
csio o n rir,tt
6i <xlllb., 1.1)67)
rlo oirltrli, (ru o (lutitii;i'i,
lrrrxlio tlo 90 Noo rr(Lr,lrt r:l,r'oir,ll,ur.tr
rr:tzr),
lllrillizirr,
il;rl,ou,axngorrr,l,rl,
cornplol,it,rr ;tolrxrhiirt,ll.l.l, cu ir,r:l,iv
lr, rrrrrirorrln,t,ur.ii
lrrcr.(fottrrtrrrttttl
v:tlrfl,tlo rrcrr:r,sl,il
lrti rronrrttr).Anllirl,
,,rriclic" :r,l ooulorrlll,or.u
f,',i,,1',ir*rili**p,;ti*;.t,;ifiixr*ilfiit1{{;ll*
'r*ii;iliiltifi;riiifii:;#xrrn!:,;"!i,:":i',iiru#*,
;r,;;1iil;1;iif#l*li,r*""""**-;ii#!{;i;x$*l,4,fr*#r
i;,ij,,
gtt'1,,ru
i:iI;rii,IiiI
Iri
I
hr*li*rtl
st.,.ffi
;.}l
I I;,t,:Il';r:'':t,
ii,lj-;.;,t
*
5 $;*g*iiffi ;gi,hT,ii,,i
,:-i[t'id**,f*iir***"1,*n*i*l**rui:?',","l[
:l,:i;il,,,il-;,ii
*i,'illJ:?j**ffi:ii."i?:*""
"..,"."",i1{iitfli*s:;
:uffi.r*?;
*",+,,grf:if
.ir,11;li,'lll{rii3i#i3{,,1fr{$Sl1"fu
*t+ffi$-**+*ffi
;lll,ir;i;.lirl;
iillllii;irj:lir,l",1",x'1"{lli*ii:i":"dl?:':il"J'"{"'rT;
li*':i*$*?i*ruTlfl
jffi,".it';;:;;Xg
otareamuscu.
l;:l:tjlliril;'{i,',ri,iffi
#j:ifiT!:i{{:{il1'.::.,rj'-,:f
i!4ffiiq1ll;giEil{iti
iili*i*
;*lffi
I,l::l:l::':l?l'1,:"il'l,il,,ii,,il,il,,',il,itli,"l';,ll,,l*ii,iS;jUruifii.,*f
rriiiil:in:ll
iiil*iff
i*ili
mrniil,-'lr'-*'i-ili
tlrft;t*'iti,liifi
t l r l"; t l )rrl ri l l, i 11ipr r r r r l- r trrr,rro rrr
5tl
It8
rrr'rr*'rrrrrri.
r'rrrJii
:r1r,,r'r,.rrii
lll'l\i'lll"lli',illii;l;'i:11i;;:;j1i1'1,,1::.'::lllrllll.'tLfi"
tl t'
l l l ttr r t'tr l ti i tt IIl r r
l r ) l 'l r l 'r t l i z i i t l l t'l '\'l l l l l l l r r r i r 'l i l l r r r r l i i tl i i r l tl r N 'l l
(
[(
'l
ti
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tti
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r
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ttl
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i
: L c t . o r t l i l t a r l 't l si ttt tl r ' l tttt'l l l t
( [( '( l l l sl l ti ( \i l to l 'r 'tl l ti i r t l V:l
ci
[l
l
zi
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)
i
l
r
Ittttto
tItIr
''
r
.
l
t
t
o
efl
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t't':;tttt
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t
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o
,
tuu"i
po sl ,cl 'l o i r t:r :t l ttl r sl 'l ttt!'t'i o o n r l fi i l ) ( 'l 'i i l p ( r l l ttr l 'l tl c' l o zi tttl Il t
itr portiunea
:liji;li,illrili;l-.ll$r
iiilriri,ll,ir;ii,,ri
;rillrf
imi:lii;iiUiU_i,
jitit
jn*lttllr,,l
tiiii*l'l;
t*xxl* ;t:
iIriIrillli:in,ii;i lii
ltw
binccontr',tr'r
rs,,-*"'ris*iiiii''re?4;\,oiculescu
li",'1,,li,i.]'"ili?l;'i*t'rLitr
iJ,4.it. lhrolizia ncrvului paletie (trohlear)
:!..1.;1./.N n(r
de semic,Iogi,e
fJSf
iff*"ur?#j":
ll,;ll;l;,-;li':till,:';itx",{if;i#ii#?;31[.i"_fi
('lriilr
.,
r prrr':r,rizic
d. gradmed.iua muqchiuruiobricmareeste
suficienti
vertislrd
a imaginilo"
liliill,iil,,'1,,1,1,',',,1,':Ji'i'ill#3fi
,!g-P.u"1':'
.*'"94di;
inciina'li
;j;
ol)rrsi.' I'^r'rr
i'tirl,' rrrrrrl.hiulriioblic rirrr<' tlo lrit't'lrtrt'
;;;"i";;;;td;";.1ii
Hi vrr
rr
nu(l(l'l'ti1'
leziuno
lizia bilaterald, izolalit rr ttt't'vrtlttipatt:tic inctici
1pp13pi
{i-ferenrirtd rL' .itrrItDtttttIfhgcodr|--ll"llwrI'
[x'rt'itrlr.ii
b\ Sindromut de ortcrd, cerebeloasdsuperioarri^(s.itrdronlll(I()IIj'Li1'IIiI'
*,,r]oi'in-" a tesmcBtului) este un sildrom inezclcefalic all'crrr'
lt.llt.
a#','t".tliii.
o""*"nii n-iv-u .oot"*latcralr' bemisindromcctt'lt"los olrrltlil
pil,r'trotl
d"
lrtn"Jf- *,i 1""iirin6rom senzitiv tle tip slringomk'Iic,
Ciaude Eernerd-Ilornor i It i ItI 1r'I'It I
leziunii. Se loate asocra ot *-d"o"l
Leziultile lntereseMi' lxxlttntrttlttl
*"*Oitni"'
*u.
hipoacuzie
si chiar o
"r,,oJ"io",-1"*"iscui
prrpil
r('
fibrelo
metliat, lemniscul latoral,
i;";;;;,
;i coliculii inferiori.
sirldromtr'l :ttt'h
c) Nucleul perechii a pa,tra mai poate fi implicat itt .
*n ii il*iii
opifiznnr'
1tild-1#l
:;ll;iili'l',1;,,11:;1i.,:l1;*gT{,i;;ff
:i'TT,:'^'f
ile lcziuni
tt":riipia"ctati sili,sizd'rimut tectl piotlus
2-4.4.7.Bum'at d'ed'atesemiologiae
il
;rliiri:l,tl;iir,;iiril:l.;lriu,*r,;'an'l*lxl*:i*#lii*#
r;;;q1,;1;riiiiiurriLi,rhn1ir,:{lir:lrr{,rf*ir#jirilnti
P erecheaaYl- ae$t eaf ect at 5, in30- 500/ u. t lint t lat t lt lt . l'zt lr ilt llllt t . l'
llXll)'
implicn paralizii ale mugchilor oculomotori (!hrad31- 5i Schlczingtrr''
rtl'rt'rJi
Dinl'opia este bornolaterali 5i orizont'alii" Firlszr'inrrgittt'.ttrt'iL
s.
irl)r'i.)'r.
jos,
u.gor
colror.lrL.
\r
se incieb1iteazi,orizontal itr privirca in
priJr
jllil,,,','l,,ii"ii]",liiilil,,,ili,/"lilnll"9""oas
i"i't"i
' (rcrrers;n)i'i"-'i"a"ui""r
,rj"{X1",'
si
,.,,,,,,rr
,r,,r.,,.,1,rrrrir,
,,,,,.,"o.,lXiulil""lt,ll,
roilcr;i
'u'.:n-
( t ( l lt lllgil r lr r r : r r ; l
par ezel, ' dc per cchc VJ do gr ad lr r cr llll ll
i"t".i' iiirrp"'ritri"n""
pctrlru
carurifd
""nirliouitut
initi;lo
dacfl teziunile
:lp"*1'
Jll
-::iitt.l
{tt'.lllli'l
slirl}rlrl'
prirnrl rlatil in :lccast'iililzi! osl'ttllr('u
au ?ost tlrcpLc satt stingi'
ti'tt1to'rnli;iilrt
pt t'oTtogra[i'a
2.4.4.2. Problemade dinllnostice'ti'o'pntogen'itt
neruultti oculotflotor artern.
A)Para|.iziilalron'tn,arc,sitttflelcventittl'ilrti|tl,r1ll1;rrril,i1|'rr;rltrlttirlit
ttcrltltitttttl'tttt
ou"n"fr6r-,r-iii-o'ai t, t,rrs"rrl o.l m,i lung dirrtr. 1,.fi norvii
vttlttrr'irltil
trut,i
rxil,.
nr{uri.
1)l
rliforif.
rt*
!"pii*t rn f,,i.',i,t
;i;;;;";"r.i-j
tnzonainca,rctrcotpur,,,,-*fitt""t'1'otnporl'ltlltriqiltil'trrrrrtlolttsittttxttl
cavetnos.
a)Pt'oaesauuS|lll'I'(t.(11t,'sittct'r'ulrtt:ttlttttlttl'ot"'rltttttn,portxlllott'tlVli"r'itii lirrttic :tIrrrlrirtli'rttt rtr ( sd lttittt:' Arlf..l' ittlol'tt'
til,
( I ' I I r :l 'r ( !t) ( \'
t
"-,riuiuu,i,
"ao.
t , , r z i l 't r , - l , L t ( '{r ,'l tt'i l l 1 l i .r i r kr i ttl .t'vi ttt'ttl o ttttl L tl r i t.r L t'l tti , t I t ' i I | ' I '
llitr rItr|.'Itt'||'tI
{ra,rul lrn1;r*o.iiilrr,i'r,pl 4i rr,r,hr'ulrt,biritrt,itlilil itttrrttt,irtrt't'I'
('iu'ot'l(l{!
rrfl{tr.i
tt
lrl6rrlll'
ir,lli"t
s.
l)(r
li:n'ti. Itt s!tlltslll 'llv('rlr's
tt lx)l llli(]l'll tlotvttl txtttlttltlttl'rtt'
',llt'l'(rll
itl,tirrtc, I li llr i,r'tttl,ttAiLtt'pro(t('x(ul ttl'ttudtrotlt
,lll'li,!:r:l;i;i;ii;'trltTi.t#'iT*fflti,rli!i:,r-1J*?:{'l,1'r'4
;fil"ill,,;lli;,,tt]:",:;#;;,:;y3ilii";;;i;
jii:,i['t,Hf
iii,tii'l
:i:;Kili;E:f:::i#,,Jffi,/,,:i1l
:n,liil
lL?"li
iiili,r'li,,if:i:;i!i':,,,{:i:'i
1l !\tratiziih:
)
nttderr,rr:rlp
IVa sinl gr'(trt(l(r(li[('r!'rrtiitl;
,trr il(\ r1(lt(\
lr,rr.rlir,rrr
;,,|i:j;li:Ji:'.rr
^,,,,
t
l5
l-l
l,lll'ililiifiilr;iritiJii,iiiii::rlliiilr;lil;l;l"ll';11,i:'il1'll1;t
l;li;"i;11,,:ilil,
r'rrrl'r't,''r(
:rtr'r't'rt'
Ni
rtrtzir:tttt
rt''r1i.''"'.'".''''
gi l o,
r.969).
h) Paralizia percclriirr V I ir :r,llilrerle :r,scnrorcrr
Si.irt sinilrttnu,l.,liutlti
^
pi 4n, celLal ,uirl\tlui or:bttar.
sJewidale
i).Tu.mori ale fosti 1tl,ru'ir1o-Ttalatine
ptotTLa ltilroestezio qi rrcvlrlgirr
.
jn
teritoriu-l ramu-r.ii 1r,.ll-1, l ncrvului trigcmcn, hiposecrc!,io lrr,r'irnali,
si pa.ralizia ner.vului oculomoror e:lern.
j) Paralizia cronici a neryului oculomotor exl,ern poate consl,itrri
prinrul semn aI unei lu,mori din regiunea tli nl,rt drful stincii yi sirt.r.r,tlrt
L
carernt (Sakalas qi colab., 19?5).
. B ) Paralizi,ile rad,iculare (intranearaniale ectranucleare) a1tlr. (rrl
mai fi'ecr-ent
ale porliunii ventrale a protuberan{,oi.
-in,,lezitni
,\ ind;rotnul
]Iitlard-Gublei esie lrodus iie leziuni ischemicc itr l,tl.il,o
riul arterclor medianeale alterei bazilare. Clinic se traduce prin tnrrirlizirr
facia,li si de ncrt, oculomotor extern ipsilateral, cu herniplcgic tli. 1rrr,r.L,'rr,
opusl'i_.Forma clasici a acestni sindrom are u:rele variantc, h funclic rto
extinderea leziunii: a) dac5, leziunea se intinde posterolatcrrr,l ryi iirfi,rrr.
seazi nucleul sru riid:icina principali, a trigemcnului, la tabloul cljrrio
amiirtil se-adaugi fcnomene senzitive de tip ilgic sau parestczic pc Lcrrri,
fala homohtelali ; b) dacri leziunea se intinde nurnai in diroclic 1xrsh,
rioa,r:i si afecteazd,pa[glica 1ui Reil, realizeazraqi un sindroru sctrziliv
alte-rn; c) dacl, leziuncase intinde in direcfie medi.rnir.qi cupr.ildr: trolvrrl
oculornotor ertern de partea opusi,, apmc o parelizie si a acr.stlri nrtv ;
cl) rnar::ileziunea se intinde in diledlia crlotci plotubeiantirL,, alirol,rrrz:i
qi n:untleleta longiturlinald, posteriod,ri,.
Q ) Pu,raliziile nuclearesint in gener,alrare ;i aprl rnri eltu irrprr,rrrril,
cu al.ctarea altor sttuoturi neryoase din \-ecinr:i,iit r.. .\stlr.l. Dlirillizirr
nuclenri, de ocu-lomotorexterrt apare aproape tot(lc:runa lsocilrti t'rr 1,rr
ralizie facialiL periferici..
Nucleul perechii a lrl-a sc :rfLi aproape elc rr:rrtrul porrtin l,onl,frt
plivir..l ipsilateralir,de la care o cale tlc asociatiecorxlticc,prirr intrrr.nrrrrl
irrl
bantlt'letei lotgitudinale postelioare, la nuclirul pcltlu nrn;clrirrl rlr.rpl,
oxtern de partea opusti,.Acst ccntru ponti estc Nd{rserllfccttt (lc lcziunee care inteleseazi,nucleul oculomotorului cxtcln, qa incit, po lirrgr"l
paratizia de nuqchi rircpt cxtelrr, :ll):ll.e;i o paralizic rr prilir.ii lir,1,i,r'rr,lo
rlo
ilc|p11r.i
prrt' qi tlerilfia coniugatir I globilor ocrrlitri rlc prrrtcrl,oprrsi.
O rfr.clltne limitet.i h norvul facial si alxtucerlsilc rrcrct;i lrarltr {i fiiri,
pararLlizja
miqci,ritorconjueatc r1r,latcrialil:rt,r,sugcr,c;rzio loziirrrulcni,r.;rll,
la m:rllinca infcrioat.ri
;r ltrrniii, lndo lctsiti rloi no'l-i lliliisr:sl lr,rrrrclrirrl
certl,r,rl foarle :lplr,4c lrtrul do r:itlirlrl1,.t)llnllizirr,rirrtleu,rii irilrrl,rrlrrli
de ootlornotol ertenr nu txtc rlr.ii, rlacr'ii:irrcurslrrrrlr rlo lattl rrl ri, cli rkri
('oncornilr.trl;
trucleise giscsc in apr',11itrr'.
s(rlLsoci:lzii
llrrlalizilrrrriscir.ilor
rle la-crilltate ;i plr';rlizir rrrrilrrtcllliisirrrlriluict'rrli Irrri:r,liipuiliilicri.
at Sinrlromttl lui (lus?tiui (sittrlln,ntl ilot;;o-[t lu.or:a
urLulftl lrqnt: .
tttlui pontin) s(' lrlllit(i1(nizl'llzi
(t.llIti(ji V,
rlt.fioil
lrl
tt('l\.il()r
1rIirri,t.rrIr
TI,YII qiYItrIrl, lrurl,r':r
llzirrrrii,lrrl)rrrlrilir|^ scrrsilriliiirlr'l,r'r.rnoll!:.r'zill,
de pi,rfor,ol)r tsii,(1('\'iil1
il illolrilol oirrrlltlisl)l\. 1)itt1r!ll
sililolrsli rii lirlrrgrnus {ilrc bfi1c tlr 1|rr,lr':r
lr,zitrrrii(l{r,rrlr.rrlriilrl1i \-lrsrrlgil,lllir?: ,l,rrrrr
r|()rrisi .Nlonl,rrrtN,l'i,
l!r(i0).
lt\ Sintl.tonrt,l.
Lu.[ ll,utturtntl(*irrltrnu.l urrrrltl tl lt,ilnht't'(nl(i) \rl
tliU'irrllt'fizu
,zii 1rt.itt
lt \'1.:r rlr' 1Ir1l1,1q
lr.zirrrrrisi Drrrr
llrr,rrlizirr1l(\n,('lrii
;l,i;i';'iiih.lill;lill,i,',J;illiij;l',1,;ii;*;l
,,,,,(,,:,,i{,,,,
,
rr:,;,,,,,,,
l,'l';,iliiil,j;l:;iiillill;jl,
stincii
te,n.
#:;';:::,:,i",!'i:w*.,t,f3,wi.
l,:,.,!,:.).!:':"r::i,'!::':i;j!:,li:",,#H::^
;i,,,i;-iir;:i*zui*$*"#ti+*i*$ffiiluts,i+rffi
i-isrr*,t*i*i+g***g'l'am':ln*}i;ffi
jl.ii,l,i;l'lil'i,:ii:,'i?*ffi
lr"*",:i:t":*;*lii;)*T""*,tT.ff
"i,:":#;
;,,:1i:iliimk#;il**i5xrl?*atr,':ur#fff
::
;l;;,ll;;ir-l,,lll#Tif i,:,ilTiiT,?fiii"*k*t"li:x
"l'":#i::tlfi
ri;i;itr1*llr*rl*l"l'ai*ffi
*"!*;l{6ryffi.,##i
rli'll-li,:*l',::*;,:,lh$.t"i"rli,*xJi""';ii#.#o"",."*,..,
'"'n"ii"i,
ll;;ii:l;:lll;:ll''ll'i'l;,iliih"3
,*t":1rgoame
'runo'"i
.i""ii"",fr"
,l.'',,';,il;lll'1,*f
'.,il;1,i{x'ffi
i1t"#:?",'"'":HtJf,[gilii*1',?l;,
r;:'lr;;r,
li:l:rljrrilnir#rl*i:",ffi
1;i:{"g:#qJ#$t?
i,
:,ii'Illi1,ji
;i,iii[,*31g
I';I
rl,.;l1ii'1illl::t,,tr:,*!#itr#::*#"*{,ffi
"k::rilr*11#x"ii;*t
.;x?d,Ti:Tif"::,ff;:H:
pu"ro'J,ili,io,."u.
r,ezi.nea
;ll,I ' ];l ; l";i';;;l'ii";:"r"..1;?;
fll,t"-l" ^u"."';i
1,'.,,;11:r,iilir;ii.,Uil{-$1$l=qitr#,*i':iI:}{1.+l
$
trigenicu':L
i'tii
l'.:'n**"
$"'JiT,'""!
i'i,liii:i I lil;ririlii?*ii,
ffi ,'[l jd'jff'I' i
j,tI
jlt',lltiliil;l
i'dtr{trf*lil,Hi
Lr,,,,il,il
iiliit
Ijii1,liiriili
i'ili*i
iil;r
ilnriliix#"*n*
iipl4*1n,htikirilH
r.Hrr* irrfr
)vlrriru
rrrr4ig,,rr,ri,
z.rirz.frr(\rr
irrli,r,{ii
rrxl'rrr,,;:ill,ll'l'lil'lJll,'r
[$
l l t r r t rr I i t t o z i l , d ( ' l ) i ttl l i r o l r r H i i .
rt
(ollllrtropklliik' ittlortttttlt'nro)
:1,4.!i.lhrnllziilrr ittlctrrur'k'rtrr'
rlill I(rza,r'oll
I )i I tII II' II' I t' i lotrgiltttli
t'r'zttll,ii,
o,ltnl.n11lt11iil.r 'iul(t't'ttt:l(xt.t't
( lltt'lr'1t't'olr,
siltt
rrrrlr.jroilIcliirrrlr'.
t'st'trfirt)r'
itlo palaliziik-rt'ittlt'lltttrrlt'itltr
( sr t.lrs('lrw(,grfr',ll)(i9) : a) rrt soltiul drept illtern este para,liz.Il,]rcntr'l]
(,rlrr.iugalri,
tle lRtclr'titatr:, insi, funclioneaz5,norrnal in timpul
|||rr1r'iri(.r|
r,,rrirllglrr{r'i ; ll) prozerrla nistagmusului tlisociai, singular sau_prepolgcl.rrl lrr,orrlriul oiro privefte in afarri; c) prezerlta paralolismului glo}lilor
,r'rrlrrli lrr plivilca, inainte, in ciuda parezei bilatelale a muqohiului drept
r ll l (.l l r.
'in
5u
t
ll
il
1
I
dc ,,o1lrrInto1tl,6ir'
rllllrtlrllrll'ii tL' :rlxlrlr'('il"'(1i trtt lxrslctiort'ti)
1r't'trr.ttii
t
t
t
t
tr,Ir':t t ri tltl rltltl.utrlitl"(1i lttt ltttllrirlltl'il)'
tlr
llt,irllrtoll
ltrgic
i
t
1
r
t
'
'
1i
,,o
lt)
l)iaqnostic etiologio: 'rr'/rto;-rl'in pliici eslr' (1:l'llzilti(rll'tttrti lt'trtrvtrtll'ri
l of lalmoplegiilor inicrttttclt,iur, ttlti- sau bilater:lltr; lr) lczitttriltrvirs(rllilt(t
se iau irLconsiderarein tjotttoxtul clinic (Ifa ingtorr si cttlab., l1)61i;\!rllHll
;i lloyt, 1969; Cogan, 19?0; tr'dtzsch, 19?1; Gonyoa' 11f74)
CJ Oltalmoplegiile internucleare pot si apari' de ambth piirli,.trsr.t
ciirtrlu-seqi o oaiecare asinergiea globilor oculari, precum ,1ipitt'rr'liziirtlrr
prir.irii veiticaie, 1l sus, ale globilor ocdari (prin extcnsia lozittttiltrl lrott.
iinc in paltct'| inferioarS, a rnezencefalului (Cogan gi colab., 11)5()-- r'iirt,l'i
r L'. iiotlechtel, lC6j).
2,/r.6. Paraliziile oculogire suprarruclearc
lr
l')11
t t'rtnt4 lttt
l)t
lt t ilt ) t . . x I lt , t lit /
ir r r J r li|l. r:
,, ,,,:;,1,,,,1'lll"-i1:';1"','i,"'j1i:.'i,ii,'iiill;lli,il,l,l,i;-;,,l,,i,"
llil,li,;i,i,,,1,,:iii,;,,'l,iil;
rl.rrrrrrrr'r':rzi
, r.zirrrr.r'rr':rrr'r'li.rrrolr,,iitl"",';,r"
r',,iil],,,,,,,",u
'riscririlo'
ll,ii,.;.iiir...i,rili"li
:i':li'i,';,',;:ill;);;:;i,l',;;l:]'ili.-:1il,i;:;,,r.ziunei,
",,ri,""" sintpii'r"1.te
,,,,1,,,,,,,,i,.
,i,,.;i.,,,;i,;;,;''il;';ili"Ji
T,;:i:i:".
;|?1iil11:#
tt ) t,tix:iir.itc
,,,.
r rr
da .u,tmd,riresint l,estatesofi"itilJ
laci"ntuhi
se tnis c t j, di;
si1 jireze
rita, la aproxirnativ
60 t,rl irr
r,,r,,,,,.r,ir,,,l.irl,,i;,;.,ilil|":;:ll:i^tu:!"i"
,r;riir,,.,,1,,i"i,,,-ioai.i'T1il::"ffi.'i:-Jii:tfiil?"1i?llff:lif;,yui*or'i
,
) 'l'rxttt!.ntet:u.n,is.mului,d.e
l.ixuJie: piLcierhul csio sol;i,;tat
pri\ i.:, r'rrrlr'('l)1i
rJl-fat. cramirxtoruiui, ilmp in care
.roA.airu;o,rrL uir",;.
,ii'iul
,,l,rr'.t;r l,(,rili,r'i',
.imltului vizual (#i;r:arit:a,"ii"ii, _"ii),'i_,s*
dc lLi,l*il)i).
tr rr,,rt rrl.trurl, st:
ltroduceo rniscare
r 11r'rr.r!'' rr.r'srr:irnisciiri s.gereazii -a privilii iplr stinlnlui r,e:jljr,!.Li\,.
o t,,ri*"
t"ri"""ur,i cr-iiLr.
;rrir_
r( rrr'|r
(''!*1r' rrc re'einrui
occipital oi ","u'li i,riir" i rre rir,,:*:.
'|",
t
\t,4t,
,
tt( t ttttt'p)
"i""riit
gen,rri..,
examinatolul cr'le
borr[r\'rLrui si_i rlr,rnr, .. . " .,'
('.rr. (e
ii, I
',,
,'i,;.;'rrr,
rni..:j5.
lerNir fatraochitorip,:" .,io,i,,;",,ia"iiiiii
) 'l'r-'xlurau
farei l.ente( tl"stctgnustrlttittptoltittetic.Utl ect:ul tiriutcat
,t
|' ,, t)t'/t
\l'rticaie de curo.i dileritc este
in Ilta pacrelt,rrlr, i.r.
.str soricil,atsii tiui,p'ir-irea u't 'riicat
r'i"
pe ceni,.lr er,-r11'r{rr
,, rlrri, ii'rt) irr salp ngeslj,
"ruJ'"u"..t,,ir'i
esti miscat-l;^il#;,i;;jtr.u
direci,ii.ln
,.,rrriitr l{)t.lrlll(j apari: nistagmu-"ul
-- '
optokinetic.
) ,. , ,, , ,.,, ttirttt0tnusul.ui,_;c11t!Uuia,r
rotator srLr\ tlistq(nt| ).tllui
t ..,.!
tttt , t t t . :.rt ',,
l .t .,
. t , ( l i r 1,( _ i r n l r ot,la l]t
^
r) r, irrr,,.lr,rraliziti
; ,"nu"u,-#iiii:,:?".,?,::t;,",i,",,x"::,r11:ij:;;;illi;
, sirrt,J)ri_..1rate,
-rii.,,iia-',1;;;;;,"
\,,,lrr,rtr'
leziu,rcltr.t
arc,tui r.eUr"i"
ur_nuclcut
' l1iI rl,tihrrtlr (ncrvulr,,estilul
_,.r t,,fr,l,ni iui Deitet,s
i"iilI
lltllli,li
;li,lLl];,Il;?:ii:;lJ,Jl;L';';,1'f,1i,'"_,ii;1;tl":l,";:lfll:
rrrr,rrrr.rl'rl, (J(,llsltllrl
'r._,i..,.'.,i
nucleilur nervilor,
.oculoin"t""i- aral
\, .1rl)rlr1 ( sI{l ilrlrft. ln_prezenfaparaUril".
iril21i"r"lJali'prs,irii llri,r:rale
, Ir r,r ,r| | iI I( . r| jl:rrt,rr ulechii protluce
'
numai rniqciili tenie. afe ochiuhii.
:'. t.( i.:.1. l, uihl tu e rIe di a
ElttostictoltograJia .,si etir.tpat
ogenic
,,,,,
,.,!,:,'i;,,i
,,1
,,,',;::'i',:i;li,{:i:,:,:,,;"x!;i:1,i.:,1:,^1i,,r"'1;,*;T:l:.fiH:T,,;"_,:
. l ' r.rlr' t ' lt, rlrrr lt <,r^ trlt.iloi O Lt t t lo
.,,,,ir,ri
;iliid;illli"ftlrliii'iTlift:J.,,*"TT;l'Ii
',,rrr,r'.1,;;
ii"i,.li,?i];
;iI;r;,
:
r1
l,
i,
lli:liilui#]rliixnsft,,;li
[mlri#"1*,uffi
I i 1;1,
i
r , r rrl ,rrl i riI r , or r t ir lir ljr r a; rtb tl c t,
c.iilar aculolttc:
I:i{/.
1 1 . L t . i u l ri i e
: Ne!rc!
.l : N.Eon
mezo.cialnr hcDicrrltrrnrr ;
.artnrl
:rdliocnl:rrat.r;
-B
l i . ri re rn i a . c l l o n '
C : \ . r{ o n n e T. . e l a l n i x l . . ! l o n r. l . r, ] ri i . o n r: n ; 7 -' I ' . h l i z i c
l.rt ll:i .\tdn : I - Pi.rli2ie n!(l.arr .onjlgali | ., - I-rerialic conjrrgai' lrnr leTirx'
_crnisJ'r('
itTnD'
tunjlgat:
Dc;irlie
)pNte'di.il
4
lrin
i n 1,i rrr1r
cc i ri l lclu1t elca' 1ot sr b t lccusalie cat r zet zlj,plr llizir i lr t it t il ii lr r llt . r l'
ci 1rr, rtct,ou5 ilt lr t '1r '.
Itr fttttcl ir r t lt , lr t tt t lizlt lt 'it lt , zit r t r ii 1i r lr r pt it t t kr t 't , r tlt' llot s] r 't t r rtlt t t t r ''t
r : 't lt 'r t '; 'it l lr t i lilt t t r i t l. t 'sir t r ! t 'olt t t t t I' r or illt ' ( lil. i l: i . i
vrri rsr.rl rrvt' r, iI r r 'i1lt I rst
l l g. I l ).
:r). , { ir r r l. r , r r it r llt ' t' ti l l t rttl r' t,i rt (tn ti l l Iri r $ i ? l .I t,nl at.)r,rrl r,
.
l rr..rl rtnrl 0
I' rrri l ' . r ' : iilul olr r lo ;i l r' rL .i rs u l rr,i r,l rrn l c j s j l l i i (tnl i l L,x l tr rri vr,l i rr,psul rr,r).
l i ,, rrr:r r r ili. r lii 1r r ir r l ,r' -ol rrrri r,l i z i r,
rl c l l rl c l l l i l a te a ])fi vi ri i , rj l l ([{ fvi oi (]r\gl ol ,rl ,'r ,, r ' ul: r . r ' i,r r r r r or.iq i i i r l l l )l l u i , s l )r' (,tr)a rte al ezi uni i (bol l raytrl i ;i pri vi tqte
Ii 'zrrr.:r ) , l: L r . : u' r . s (.rrs o c i l l z i -r,
() p a t,? l l i z i ofa c i a i 5 tl e ti p central
,i o hemi _
lrlcgir'.rtc l)itll,(fr ollnsir lczinnii. L,eziulile cauzale sint hemoragiile, infalrct r.l r. i .i lr r r r ur r ilr c m i s fc ri e e .
Nlrrriii'stiir.ilo inverse, ilitative, pleced aleviatii conjrgate alo globilor
.
,,, rrlrli (rrrruor,isi alc capului) sprc
lartea oprrsil (confotm legii lui pr6vost
I
'll
tl( ll )llZ\').
I l!1,
. Sl lltoulnele
Lui FoDiItre:
/.l .L 'r!l l l i rrh l rl i l ./r .Ir l&l!,ui\,r r lonlnor ii( oculosnc) jr .- r ilr r ec ol ti c odr dur e
lr ,) vr lt. por tjh( xr t*; Z _ Si r r tr dm r t l Lj i F ov i l ) c p.{nr nel l rd rn , l .!.h l )j i,- SLr ||,J"nl
rh L l i,t r Ir r yn{ ; ,t -' r :ir ' r ,t
t!i ltvil.
l) r nr l u.r nl i r t i nfc .i or ,
' ' Ir t
ot t
S xl .rotttu l f l( r gr t t nt t l-( lr Nltttt ( lillt llt ) llllll 'supct 'i( n't ll- lt 'glt t l't r lt t lt t i ltt rtlr'
ttrijlocill' lrt'
lrovillo
tttt
sirLrj'rotn
sorrtirrlirgir',
in
conljexl,ul
t,in) culrirrdtr,
gl'5rrli
;;;ililii';tti
l,;'i;;;;;it
leziunii.
parlea
olusl
de
-'
c,'i,'l,t,il's'ipsilatoral
f i hotrliliipo.sl'r'zi'
i"cdmpt"te ale privirii de latiralitateorizorlh, c"."i i-pn" cintl globii oculrri silrt itttlrtrlrlrrii
nistrE
"tii,r,ii
paraliziei.
ln diieclia
I'itt
I'iraliaiile migcdrilor conjugo'te tle tertic:ttlilate (sintlttittrttl
!)
jll'rlischtrwil s' h
"u'?Jrlunlt"
comisulii albe posterioare, alc nucllilor lui
Lllrtr'lrrrrr.i
.i Crial si ale iubstrn(ei cenuEiipcriapedu('lirl(din reglllll{'a r rttrrI rrl.'
litt
ucloa'r'
aoietlo"i p.ino tibrele ocirlomor'o'ii bupran
;;"r;l';t.;;;i
(ar\':r'
si'-'"
L;ltiur!i
vcrlicalp'
iiir:'riiliilTj.'i;l o pu'i-li,i"ryivirii
(:tx rr'l
r'r'l('
iar
i.n-'us,
pr-ivilii
paralizia
prorl'uc
inri-aor"rio' (craniait
mai posterioare (cautlal) realizeazi parallzla prwrr]r rn Jos'
rt'
fn cazul in care pa'ralizia migcirilol, conirgate de vertiur'lilrt'1't'
irr
lta'ttthrl.lrt
gdseqte
se
purlotizia miqcAritor orizontale, teziuiica
din regiuner 1ep12li 1J.5olli qi Srrlli' llrtil
"*o"irn'*
r"i'"ii'iur"i5cle veit icalitate nrr apar in leziunilc 'irt;:ttl:tt'
paializiil,'
Si;"i,bl;;i;i .i""tio"io"ii
in leziunile care a'fecteazi' zotlil l)r{'l"r
ntmai
ci
sup'eriori,
r-"
Bnderl1)(i1r)
i.rx"oli*fifo"
ibt}t;.rttltli. colabl,tooz; Pasikqi colab' 1966;
oxtrltrlrrrtt
imposibilitalcl
prin
Sindromul Parinaud se mani{e)t;
portlr'lr
ocuJari'
globilot'
a
-hlr
dr.
coborir('
rolr"Ariiol de titlicare;i1 sau
paralizio
itttrttttilrigcare de verticali{ate' lntr-o
,n"iiiA-.ti."'
i"ii
rr'.|rit
rtpui
in
sit'''
priririi
"";,Jf.ia"i'iiiriit"ri it:"cl,"nr,afcctarca
i,i"ti.
tat
l'ir'trk'trir
jos
foartc
"el
apare
in
numai
to ti.p ce
i; ilb;];; ;;;! ;i
lrr l1r
ilr_?irir,", il--ll.s L asociizi rdesea cu absenla rcaclici l)ulilxl.(i
(lollv('l'g('rr1rr
dtr
'
;i; miclriazS, relativ2i li tu menlinelea ree-c{ici
;;t-.
It''"
tlisprtt'i{'irl
jos,
plus
ln
rparc
in
privire
Daci,'*;';ierd; si iniqcareade
modirii qi a oonvergenlei.
llll(l{'irf rl
ReEiuncr precolic(llal'lnsle fl':.rl'lcaplorpr. do uumJrlo\lll
{{'
I rr
'rt(rt'iirzii
..indlomul
Pat inaur[
rn si, ca alal.-'
itl
lidicrilrx'
"",lotrrJi-Gi'ctm
l"
l)l(r()tr l
a rrilu', in special a llruscbitLlui
;;;;;;-;i;.
o;;"}ii
(x)ltvtf'gr'rrl.r
tr
'
rl.'omodal
a1e
Sr
i'ncrioare ii tleficite in )ol,ilitatcp.lupilei,
-ebt{i
il"
krzitrnilt'
i()tlir'Li
excepl
a
I\''-i
p""".hii
.In
A'r:oli;"ll-a' rr"t*lrl.i
;i;cdrile t1eurmirile pot ti pristri't^e,in tirtrli.l,t' trtiq|r'i.r'il'
;;;';;ljidt
i"t oinitt''" DiIlopia 1'o'rt''Ii 1r'oz't'tit irr ParrrliziilrL'v.r'1"
i.,i."i;"
tlirlitqttl't
satt vestibttlalr'tttu ittrlttr''
tiiri",- ,st,it,',rtareaopl orl 'irLeiic,-r
lerl,ical.
Sintctizincl4llpjgtlinlitr.r':l1Ltr.i,Il{'ILdcr'(]{)U|r)iLlillli(jiiil||,iu'll'llxIiI
.,t91,
lsi'ciit,ttttnlsntiIrrlti tttttllr,rlitttttltti'l'l'trittr'l''
lloi,4elqrl.iculitatosir
,,ris,,,i:
s:rtt ltit'ttlctt'itr'('gt,rrrlrtiltttpilltt'lrt
tliirrirrrtleit
:
a,)
t;ii;ii,,;";i,,t;irlorii
(1r)rr\'('r'gt'rr{'('i
; | ) ('
b) sp:tritrrsittt
i;;;;;i;i,;; i'i;; r'otr*trtgr:til,ir;
I
I
I
III I |)|||1
I
I
f1
l!rlrllrtl'
tlislrtAtttlls
i,'r', ittr,lttsit,'ir't'rtlizia
vitlirrllrlt,ir riqoirilol nisl,rrgrrr
r i: l
ctallli
It
01 c.) .
'''1 'i '. . 1 . 1 't '''i u tti l .I|!( l t],ttl ':|||Itt|',l r ( !( 1 i h r n t.,l ',t1 ti i r ,.'t'.r Itt'i r l r 'sl r ttr Ir .
u tTo l 'i r l i tw '
l r q t t c l t i r r r r l c l r r itl . i l t) tl n tn 'r i stttr '.'l \'' l r r i i o r '''!'i r r r r .tci t- u 'n r r :i "w e l t
r h ' D "z i I i r t
i
"
|'r
r
tr
r
{
i
tr
i
l
i
tr
tr
tl
'tl
o
g
i
r
''
o
si
ttr
l
tl
, ,t t t ,t , l i t r, , i rl i r u , t) to r l u ( '
'l(i il 'r
i 'l'ctr
l
l
r
t'l
; r l l s|.r r l
a \1 .( a ) l r r l r '1
t , r ' 1 , t , . l l i r '. i r t r , l l i j i x; ( i 'g r r l t 'i N l r r tttr l . t9 6 l l ;
, , ; ,'l;;:;ii iiffiil;il
pi l"*
(x'l'1rl)rllltl
,rrt ttltlltlizii multiplc l)a,l'ttil'lc (le oculomotoli' ln coli'ttzilt
r lili'r il")
gr
r
r
r
k
inlr
'11'\
11(
i.
(
ir
L
,.,, 1." ,,," i ,:rl ,, i'i, 1, : , l', , i; ; i'l ct r ob'll, pot I i
r
t
r
ijlo.
it
t
r
1c
et
:
r
'j
lt
t
t
lr
't t t t . t t
c*it
r
it
'n.
I
t
:
r
.
t
t
t
r
il.
," ,' ,,i 'r',;;;i;;1i,,";,;;';r.ir,t,:
.,,' u t , , i, , , , 'r , i' it r
u v I rr
pc.'(1hii
trururriirl('
iit oi vt, ,l-n'urteo..i
i.,; ; ' tl i i
erl('ltr
4l
hitlrr,'tlinarnico'
, 1 l,lli'rl ttrcll'al posttlrlumal.it. d-) nlecrnirtrru
vr
t
t
i:
t
lt '
lt
t
r
t
i
ic{'
ulnal
1t
'r
'll
lii
pcdl,
't
t
')
o{ulopi
lln(
a le.
r' ' .,' ,u,,,ai ;r," .i "
l'o"t t l'r
tt7
r l r tt tl t'
t'o tt,i tttIIr Ir I l l tl l t:r l l
:r p l i tr ':t l r r r r r r l r .r r r r l r 'l r ti vi ti i
l r ' . r . t r r t r t r , ; r ol
r , 1 , . l r l l ) u r ': i l i
l r tt;r i l :r r ', r 'r r n r i ,r ,:r t:r l t r r ti tl r i r r zl r i l r si l r tl cl r r l r r .
'l l ) \ r 'l r i l i) l l L r l
:t YI:r
r ,i
tr r tti ;l i r ' 1 r o :tl l r l tr p :tl l r l i zi i l tl l r l r l ttt,l ti i
, , , , , r r r , l r i t r r l l ( ' I )(' t I ' (, I I i I I rr' :r , l l l j t
si tl , l \' l t.
" 1 ) I I r 't r t rtIo r Ittr r 'Itl i ttl t':r l tr r t i t'ttr , str i ttsl tl t'stt l tl l t'scl t r l tr ttr i r l t i :r zl r l '
,,,,
r 1 r : r r l r " r r t l r .zi u l i t,i t.
'l ; l ) ( r , r r r l i l ( 'tl tt
l tttsi ttttc ( l tcl r L i i l r l ccl o b t l t) e ) l tl l r l r tl r ttl tr i i ttttp o tr r l I'r r l
; , r 'r l r r r r , i r t l l r t tn r ti ttcttl l t,t'tr tr r ttJl i 1 tl c, i a r ' <l csl 'tr l ttt: l - tt( t't'tt1 ttti tIIi It,",Ir l r r r r
I ' , l : r r r 'l i r l i r ( scr r r I r l i l o g n o l n o n i c) ;i p a r a Ji zi c i p si l r tl t'tr tl i i tl t o r IttIr ,ttr ''i ''I
scr l tttL tt Itti ,\l g r l l
l i tr l r ' tl 'r tt.
. , , r r r r r r r l l l r i ll r l i r l ) tr e si n tl r o tn Pa l 'h a u d ,
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, , ,, I.rl ol xrl i rrrt t il't illt ,lt t t t r , t it r lt 't r i,(|I I(' t' I II I i 1i I llo$1'\ 'ilc{'it Liii' \ 'ill l( lr l| ' zr r lr ir
li t t ( llr li lr
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r.,Lrl rzr o rrri rl t'ilt zi. p11, , "11,
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t lllt |, iilt , ( , lll'|ll|1|j||( t
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11' ,,Irootrrrr' | rt I o1r it ll(
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it t li't r {illr Hr r
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l'illt lI t lt llt
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7il
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i t Itr s(fl rLui l ti (| l tl
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1r' l.r'ir .M)lirlir
il r l( ' r ' r ll, r r r r r , r l, r r . lr . ; , r r 1r ir r r r I i r r o i r I i r ^ t r r(,rJl l f ( i
l ) L l r l ) t , ( x n r 1 1 ((!l
rrrrr ':rlizir' lzrlrrlii r r r ) ( ' lt f ( ' lr ir r r r r r r r r r l' is r r r r 1 . r | rl r l . r 'i r , r 1 , ! r o i l s e
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r
p:rrri 1, ., itrli\.ti, . ; ' r , , ' lulr . lr r r r . r r r r , r it l. r lc l , o i l e r i o l l c .
cl:rlliclre
'l'r',lllrrali$rni'[{]
o c:11'rz;rco'nun:.], a !fr,r'illiziirr)r'
'cr)rrzirt;
1,rilrili*i'. Slirh'iilza lloate fi con-(ecinla, lczririi dir.cte a tlunchiuhii
(1ercln.rl,
rrr rr .rrFirrrii,
re-qp{lctiv a cornplimirii
neryul r1i ocrlonrotor
cor lrr.
ti ) ') 'tt tt t ttt.i I t' ltr)d)t, l.r, rruri iiltrs (jcle srlratdrtOriaje, e\etcitii el:rtl,,
vrrr', ; r ) , i1.ir , r r l[ ir l]rrl )j l { ri ,tl rrc o ri fr" ul i n s o c i e l e a de rnodi fi ci ri a]e aaLi vi l ;i ,(,i l
r rr.rrrl, ;rrtr :rlr. r'cl'ltrrclol totornotorii. S-a flescris midriazi c6ntralat,rrl*iir
rrr trr r r r or , lr
i , { r r l: rl( ' $ i u r i o rn p o rrro c c i p i ta l e .A rs eni ryiJl otez (19?1) au d(,srt.i } r
,.r'.r, 1, , : r r { . 1.r r r . r l] l i i fi ri l rrrp i l a ,rc ; u ,) i n i ,rL rnol i l ei rontal c: mi ozri i psi l rrl ,r,
r rl r.. : r r o, r ' l; r lr t l ti l ttts l o n rl ,i o l U tri m trl :i ; b) i n tnmOr.i l e temporui ,, (i rr
r.', rlr . l. r , . ir r r r r ' : r 1 r' rrrr.h i rrl u ic c l rb ri rl s i tu de herl i o t1e l ob tcmprl nrl ) :
rrrrrl r r : r z rrr[ r r lr l. t r r l i ; c ) i tr t,u l i :l r)ri l {o] trc i p i t:r,l c: mj tl r.i azrirl
, c pl r.tei r rrprN i t.
trrrrr ! r r ' r ; r l) r t r ll tto fi l o i n fi l ti rl ,i rre d 0 ttu n chi cer{!brl l l : a[i z0rrrrIi r, r,rr
rr,,7 r ii t r r r ir ir il tz i i p s i l l l rtftl fi (i 1 r ? 5 o 1 , (1i n 0[z]n.i ); t,) i n hrrrnl i otrrrrl
,..tr.: r r lr r r : r l: lr r ,ir r r u rl rrrlrrL
, i rh ,i l i z irl, e p a rto :t, l czi rrni i , l l pi l i rLc pl rrl el r, rrl rr* 1,
(l rIrrr . r r r r r l r |' pI rrs i rrrrrl i rrrrp o ri )s i i n fl z | , l l i [al l -r,o rni d.rj rrzl iI r i I:rI ri r.rr|;t,
Ir'l r lll( \ r ' r r lr ilr r r IIrIri trItric r,trIrn l l ; t) t' l t l trr ml l toi ttncl c sul xl rn,l rl ot11,{ .l l i r,:
trrtrlt i: r z : riI s ilr ilr ' ; rl i I g ) i tt Itr^ tl rl o a tl c l c s r tl trl untl o rtr)tri ct. : rrri ,rai rr!.i r
l: r | , ) i l l : r .
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i rt I t rI r' t rr t t t rr t t rr ( I t I | | |r i I I : | , l r i r l l l tl i l l l r 'r r ,
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\r |r ;l' l l r sr tr i l r to r l ttr r t tr r r r i r r l l r r r r
' t'
t ', r r r l r ' I r . r r I o l i r r Ir ' :r l r . q i l r n r r l tr i Ir i 1 r o l l r r tr 1 r ttItti ( ;\r ';r 'l r i 1 1 i ( \r r r sl :r tr l i tr r "t r r .
l ! r / r l r rrr, r 'r I r . s i i t rrr { i i , tr r i t l l i l r zl i 1 r rirl r rItl r tIr i 5 1 r |o r r l tr i l r r o i i si r l r '|l r tci l
, 1 , 1 , r ', r . l r i l o l l l l ,
I\', \'l si IIl .
l 1 l r t r r i .t. tTti l r l tl i |i r l r , 1 i p g tr ttr tl I I ri I I , I ) I t I i | (' I (I Ii ttl tr ti r ,i r l r r tr ':r r 'l r r
'
1 ' r r . ': r i i , l i {, i r . i r r si r L r vi tr r r r i r |r 'i l L i r r r . r tr Il zl r l L r l ti r ,l 'i .
\ f r r l l i r r z r r i r r r i r i r 'Ii i r l i l r i l i i
i r tc[a u tTtti t, M '( ti ( r 4 .ttt) r tttti !. tts.l i r ;t, ttl
| , , l . r l \ r l r r : r l ( ' :.tk' i ttl r t,ti ( tt!i i l o r u l t:o tl i a t, ( \1 b ( t]L i l tt) 'i t t ti l l l ( 'l l r r l l ( ' fl /r '\
r , r , , ( ) r r r i r l l i l r zi i r r r u r i tr u tl i i tl r l r r t i tt xl o 1 ttt,la r .n l i u tt ( ,l r tr l l i ttt,r t '.i l i ttl r t r r ,
l '1 1 , ,) l f l i i D r l rttl tr ',r 2 i r r r /i fi ( l h ( !l n tSto L r N ,l r ttl l i l i t'
l l ttl tl e l ) 1 1 'zl ,r r l r r( ) r r r r r si r ':r
, , , r i l r : r z r i i t r l l ,zl r r l c i r tsl r i t'r r l i c a tl i ttci i .
. '. l . l i . i .
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ll
i n .l e r i .o a r a
o ,l .t ct n l t i l o t' 1 i ci i l o t
r tl c ( i {r l r tl l l l l l i co ttsl l i o l ,o r r r i
l l i o . u s,p r r sii cr i p l i tt Iczi u tti i ti l r tl i vt
't )
, l , r : r r k r r s l r l c o 1 i 'r r r l l i l so l ) l ) r 1 ( ' i ttl i l l l i i r I: h e r n tl t'l g i i sa u l ,l l tM r ti l ) o l l l ,l l l r '.
i r r , r l r r l i l l i r 'p i r k,tr ti r l i , r tr r r i n g i l t . i ttl i 'c1 i i :tl c si r tttsu h ti ( r i tvt'1 'tl o s. l ( 'zr r l l r l
r r l r : r r r l r i l l r r r r , l cl l tto N , l ti l ) r ) \i ( ' r ,r 'tr r l r l l l '1 scvt't'i l t'1 c. ( ,Jr tttl :ttto v q i l i ttl r l r r ,
t,r,, ,
l r : i t r . r ti
('lursi(I,I ()70).
stl r tl r r r l i r ',,
p l i tr l czi tttr i r l c ( {'l l 1 r 'r i l l ti ;i ci i kr t
l ' ) i l l i o : u . ? a l tl i l i ti i
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l l , 't t t r t : t | i o r , ^, r 'r r g ttsl i r t{'r t Ii ttr l l 'i 1 ti tI1 tt'Ir l r tIr isi l l l o l l r i i {.tto l l l l tl tr r i r '. A( ,|, r i ,r l
, r r r r r r ' l i s c p ro l r r sr i ci l r : r 'tr ,sl t'tt'r t rr r l r 1rI i i t I r I i I r i i ( tt l l r x) l l tr ) ( l l l l '( ', \'l r sr ) tl i l :IIr r i r l
r r r L l r l r r l i l l r l i r l i tr ci , r ,o r r .i r r i r t,li r t'i si r t r l tsr 'l o l l i tr r i l tl t', sti i tl o r t'r l r tttzi l o l r ,
, 1 r , r r r r r i i i t rl t'r r o cr r l l r tr ', <.r 'r 'sl r ,r 'r 'r Ir
r 'ttt1 r ctr t1 tL ti i |j i st,l i t[l 'tcr t l t i l l rfi l r rr : r I rl r
l r , r r r r l ', l l i ( l c i l r ,( '( '1 t[j l r r t'l r . l tt;l i l l tl tl t
tl .c t'ti i 'r ti tti i tr ti tl tr i ctr tti tti t l tti r l tr r r T:r
,l
r r r r l r r . S i tttl tr r tr r n l ( 'l r r ttt[r ' Ii ct tu i l tl l l o ttl 'r ' t'si c r l l ct'l t' ttl l tr l l r l l l l , .r l
, 'r I l i r l r '| 1 r i .
l t \ 1 i ) t ) u : h i tl
:i t'l r \tl r \ti o /,i \ ;r i ttt1 l r tIi cl ] i l l {) i .1 tl {'N tl i i r i i r r s( 'l ( tr }7 ,:r l r r l r l
r ; 1 . , . r . r r r 1 . l r rIi L i i , si l i l i s, I,r r r tttl to zr t r tt'l "t't'i r ct l tl r Itr l {'r ;tl l
r r r r l l t'l ( 'r {xl {l ) r '
l j :l l ) tl r i l ,l
I'
r i r r l t'o tttttl
i . l ) r i s l ( 'r 'o i r r l i ,r 'i o i i r r ' ( si tttl l r r r r r ttl \\'r L l l cttl r o q ,
, i 'l i r ') .
r i l r ttl l r r r t( . r i ( ' j r l r r r ) l r 'r r
l \ lr l l i \ tl i tt r i i tttl tti l i tttr 'l t'l ) l t) 1 l l l ) ( 'l i l l l l ,i i r l ( f
, 1 , r r o r ': r I r r r I r tIi I,i o i i ,r l c l tr u 'r ':t;i l ,l ) l r ' r r t Ir ( r '\'i i ( '!r l l i i r 'l r i l ( 'zr l l i . ( ) l ( zi l l l r t r r l
si tl r ,r .'ttr l i :tt 1 ttti ,,ttr r , ,i ( r l 1 o :L l { l l r r r l l l r l r ' r r r r
' " , i t r t , r t r t t i ttr l i i i .tt.l tti o u r tr
{'l r r r tr l r " l l l t r l r tr l Il o l ttr t'. I}( ' I ri lr ,r l rr' I l {' i r , :'i r '\l ) r i l l ( l tr tr t r l r tr 'r ' tr
', r r , 'r r r
1 . r t , t t l , r i t r l i ti tti l r tt n r l ti r l i l ttr 'l to sl t ti r tr tt r tIr ' * r tl tttr ttl tl t]t t( tr i t4 l t
i n i ttt,',tt,
r l i l o z;i . l r r r l r l r r i r l i r r r I
( 1 r :r r 'Ir i tr r ctr i tIr Ii L i l r r ,'l i , r r , l I
, , , 't : , , r l r . \ u l ) tti t) i tt
r l l r I I i I I I I I 'r ); r | ! LI
l.
r i l r l r r l r . , l xr r r l r r l l r l l .
l t( 'l tti tto :tl l l {') . l } l l l l i
ti l r r tti l l
l t t r t h i u l , tr tr tr r l r i r .r i ttl t'r l r tttl t':tr Ii r r ttIl r I l r r l r l ,.i l l l i tr l i l i l r Il l r l i ( i r 'r r r
,r,,ultti
l r ,l ,r ( i r r ' r 'i r tr ' l }r ttr r l
I
r r r l r l , r ') r ; { ' r r r i o {( vl ( l c Jr i o zr rri t r t I rrt i i t ' rr . l ,.i ttti l r
r r r l r r l 1, I rLr rr i t r t t I I t i l j i r l o u r tl l ;r l l r tr t I ( i ';i tttIr o tr r III l 'r l I tr .:t$ i 'l l r l l i r r l ) 1 ',r 1 r, r !r 'r 'l r r
r r l l r r r r r l r i r r r ;r r l i c r ,',t vi t'r r l r i .i r r r t r ttl r l r r l r t ( l tr ttto t i l r l ctr r r I | | I I | | | | )| | i | | ( ,
'
| | I l ( ' \ ' I Irl I I I t ^ l l r '
l | | l r - r , | l l r ) z r , L tl tr r l }|i r tt|tIi r tr 1 i Ir r Il r ' tl ti l l l r ', l l tt( l tr r l d l o |i t\t
tr
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ttr tp tr l i i l r
IIi r ttr l t IIi tttIr l r r r tl o :ttttr ', l r o ttl :r l l ,r r l l 'l 'l tr )
r l , r . : r r l r , f l r r l r r ) n r ( 'l l r r r i l r 'l tl ttr r tttl
I I r l r.r, l : l l r. i I r t r r t t I I rt t t l i i r rI i I r r I Ji I i rr' I I I I I I Ir r l tr 'r t r l ,r t ,r , r tIr r r ttrr Io t i l r r r :tl t r l r r r tr ':r
,,r l 'tl ,r l ,
t|I) |) It,||) t
I ' i r r t t t , I ( i .tl r ':i l tl tJtl tl tl t ttl t l i tttti
'r
.) tl) t t i t)tu.t.
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l r r.r,l l i l rfrt ul tl i tl trtl tl .
rl, rllir i o ! r t l r ) ( l l l ( f l l ( . S i l i ( . Il l | | l t \, r .,.1 :tlr \, r l r,
,. ..
l ||l
l ri kl i i (l t i I I i ( I I I r I i I ti ,l l l tS
rtrl rilr r l. r ' rri i rr.rIrr I i(i :l ;{ ,1 )r' i rr (' rrrrl r | { ()rrrr .i .i ot rl i rr i r
'
r,.r,;rl :.,r,s. r' r' i rl
:r(', I I r|_(' (IrrI | rlil r) ii -l l i ' rf\l )l i r' i r rrrrz r (l i l Iro l tl l r, l ,l uki trsotr, i !l n' r1,fi ri u\rl )zi r,
.
|r"r'r' J r r ' : r I rlr
i, il) ( ' r ll l l l s i rL (j r i rrr r': rr,r'rrrrr:rrrri
fi l urol (j fnrr,1rri ,i 1i rrrri rrrrrr,rl r,si
rr(l r'r ir r ir lr r lNlil, ic i e s tt tl tr s (,tl l l n l l t tn : ri obi $l l ui 1.
'.'.'l .,\ "/). lI rd,,iJic ti r i,le d,i,nanticii,p tt il.jr c
tr)
ll 'l'ttlht.cdrile relleaului ;folomotor apar ca lezultat al leziilii oljcir.ci
1,,rr'(irrrrirlirr comlticata sa cale, fie peTea uJercliii, fic pe ccrr, c/r,ilir.lri,
lr rrilrlul un etiurLilot mezeuccfalice. Existii" dozd eucnlital,i[iiti:
.1.)
.l'ural.i.tii 'pztpilure &sacial.ecu trulburdri de uerlere, L.l ulrriu.(, :r,
rrtt)r' l(.zirrri carc afecteaz5, atit fibrele pupilare, cit qi fi].licle opti$f,
l)(!
I|:||(|r.L.rrIlor comun (intre retini,, rii zona d.inaintc:I coryibr g;nicril;t,i
, \l,r'ri, lrr)do fibrele pupiiat:e se alespart cle cele optice) i
:t\ I'u'rulilia pu?ile,rd, amaurotici, rezulti, dintr-o leziune tlistraetivii,
,r'rrl)lcl,i rr lctinci sau a nervului optic. Se pierdo rcr,ctia tlirect:-r,si
corr
'.rr,. : , 1: r . l: r lr Lm ir ri , l n ri m p u l s l i m u l i i ri i p a i t i i ochi ' ]ri i
i rrsrr s,.
' fer.l al ,
lrr iir.irzii, r'.110(ilr'corLsensua,lila stinrulare; luminoasti a ochiului'si,ni'rl,r)$.
I rr llz i.rrrrilo. r.rniLrtorale, rlc obice:i prrpila F"stedilatati (midriaza arn:ruloticii
),
rrrl l r . llc r r r l r lr : lt c o n to d a l e e s te n o rm a l .
lr) I'rrroza, pupilarl ambliopic:i apare in cazurile i]t care leziunilr
rr.l irrr,i srrrr ,kr'.r'.lui
optic slnt irrcompletc. Rc:r,ctia lulilar:i la I'ntirrl
..i. l..l:'i 5i p.rrlurigit.i, a'tit cea dircctri. cit
6i cea coirsensriald.ln lczirurilrr
unrl;ril rrl(', (x)lll,rincfiia,consensuali oblinuti, prin si;imu1::r,reaochirrlrri
rirrrrl,s .irl. rr'r,i nrla.c rlocit r.ir,spunsuldircct la lurninii. pareza pupil .ii,
i r| | | | )| i(| | ' ;r' i i rr iirs1,d.solisii iu nc-r'ritelerctrobulbarc, leuropatiile dlabd;ir*,
r r rrrr r lr lir r lr ilrI lr lr r r g i r,l ' r_
llit.ir l('zil'r.rt .iiikrr a,lirro.tc se g!'tseftc Ia nivelul chiasrnoi uptirr.
I r : r r r r IIi' I . I ' r ' r)rrrr(' r' ,r' r.l l tr-ro l cp u p i l a re sl nt pi crdnte nunl ai Ii ! sl i r)l I
.:rrr
Irrr 'r I r . r r r ir , ' I ir r r ' |' r r' ,' rr' I' ' . i , i l c o s l ,oc d rru ti i , lY cm o heni :l nopsi e i rs{)oi l rti i
rtr ,'r ltttli
ii ltttpiltrl h urt..iurt
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,,, .rrlrrirrlrlrr
l\r'rrrolorlir.)'
(l'{)l)r)vii,ill$i t,Nsru, l1i,$0).
l) )
l 'l )
, l;r ri c rr l
lttttl rtl o t
811
'l t.\l(t.t1!.tnli.tvrliri.,
' l' t x t , lt t ' lr r l rtt.l i :,i rl u rl i a:r: rr) r:x rrrrri rr i .i l r. rk, r,l .rrl ,r,,rrl i i ' drr.r
l i tr
lI . I t r , { iiI , r t r ll rl r,l c rrl rrrc r' tr{ i , 1 l r) r.rrrr rrrrl rrrII,)l \l (i ; r,) rrr]i .Irrr,I1,r,Ir,
r lr , llr lr ' t r { lr tr r' 0 ItrIIrr,r'rtt l t!fl .t,o l l ,.]r,.
l 't t ) a t :t
t|tl
l:r.r;rl:riz,lrlr'i- I'rrr.rrlizir,
firci,l.i, ,r,i.,n,:rL
l,;"f",,11i
l,," ,, ti'pr,,,,,,,,,,,,,,,,,..
r,:| |1 :r
i
' 1i111 -q l i l " :i r l ,Ol j l trl i , l On ,.t.r,i l (,.t ) ,u ; r., r. t ,r, rI I rrrr r,.,,, .,rr.rr
r rl.i, 1"
r,' .l rlr,lr
l ilt ( lr . r,.s , l l | | i r d e fry rfU l r.i i n l ezj U rri l r. l rol ,\ul i l t(.;i tl l
I r.r,rtt.ttr'lt I Iil tl I c lrlril uhcranl i si stinca temporaluJu i, l:l semnole
di:
iI
l :r.rrl rr r l r r loc ir r z li tl e o l ti c r.i s i s e n l l to d e .' l e zi une a al tot ncl l r 1l,lrtltiz
trl rrr,,trr
(\, \'1, \ I I I ) ,
ln( , ({ rn t s i n ro d i fj c r' l r.ja_l e L .C .R ., i ar i n cazul l )roc{,s(,l ol
| | | I(|(. | | r1( |I r.I {. tio spal:iu - scnne. dt hilx,t,telsilne jntlacr.:utjatil;
(j) l)i
rri ' I i ()rrI i{' I rI (l('vilr(' irrsi rrrrri dil icil irr lari'lc sitnaifii tte ,pe:ratirii
ltit,l
Juciut(i
It rrrtt , t,rr' 1xr1:si :tIr,.i itr trnrle
Jornt de distroJie nlus;ularai,,di,prli.ntio:,iti
::t rl t , r ir t s lt , nit , ( lllt , l ,t (,_ \l )l n (,' :l tc n t s rtrp ],i ri de contextul
cl i ri i c al l xrl i i
rl t l rtt. : t .
ll l, it t 1, , l. .trtl ri .l u ri rrt .x i ttu -tcp n ,.,i mnt
,yl 4,,1i
Jol i dt qol gti o
, .l
' u t'tl ( " t lt t , t t ; u, t ' , t : ,t1 t1 rtrr1 ,i t,rl n l fi ). S r.n rrr,.l r.r.l j ni r.o.j rrti urrl l l rsC rnl i rr:r
l ,:rrr,rr r . r ' 1. lr lc u,tri s i rrrl ro rrt d . tn .j g h i p o n t o_ce.ebcl os. ptl Il ftl i zi a :l l i * ,
l ,:rz,
r r lr r i( ' l rri l ul ' l i i n c l y a l i i d e i ' a c i a l , ra cl re sc asoci azi i tul
, brrri n
r gil
Ii r(' r' Il I r'r
rI rr(''r)' r.1rr'".rrr,
si ilfccla.ca $rstului in ceb doud tleimi alteriollrr.
rrl ,' l i rrrlr ii. lI llt lr ll{ ' !i i z l i s c a s ri c j a z i i s i h i p o a cuzi o.
l,lr rrrl i rrr'il i lo lrr[io]ogigt' alc lir z,,i (,1,J1iuluj alt.porliunji pietroe,sl lr
.
fi
,, trl Ii lr , r r r |, r ' lr l 1r .l r.r' i rL ,rrl i rrL i ,l ttrrc { l c r.t.. zi l tnr., di e fl ectrtri
sau ri l l ,r,
f rrrll(' rlrrIri-r('r,rrr.rr,1r'r'isI ir. .,rtrt pror:csesitttGtela {tce*tn.il:el: tnetringio:rrrr.,
l r rr"l rl, ) r r , ilr , . lr : r ll l trl i .l .l r.. ()s 1 (,i 1 (,
te ml o ra l c, C .:l tl j nOl ntC rtU mi l i cl l i
r
i ,rr , , lt | | |l., I '( I I( | | I III I I I (' , r e ti ts l ,a z c
dt h car' ci troarrrI
'
l lol cni te
r r r,l l r ' llr , : r liz ; u i { ,| ' Irt.r,r' rrl r.,l l )(i l )).
l l I ) I t it r t ilI s i l trrrl r' ,i ttl tt: l l o l t0 l i o n u l g e ni r: Iri pi ori qi nea rutrt.tttrr
r1.. arLi setancl c cri ri rr.
'',rl t, t r r t t lt . ir l : t r t rrttrl i tr"(i' , 1 )o tri u n . L x u .1 )1 ' ..lr)edi
' rl C ,S C rj se
.rl , :r, r ' r lr r l llz lt r i s i n l l i l rt' 1 r' l rs g rri n i tq l rtt C rr r.gl c ).
rt1' r.i qr,.
l ':,r:l ri ,r ir l: r . r l: r . s 1 r. rrs ' r,i l ri i i r,rr l l l .r,:rte a e r stul ui
l )o r,cl o tl oui . trci rrri
:,rrl , ri ):r . , li' I ir r r lr ii,
(' r ri f(.fl rrre :l s l l l i v i l l l c i , c n hi pcl aauzi c si r,.r al tcrrr.r,rr
lr,tr.i
l: u. r r l: r lr , r , rrrtl q .rrn g l j o n ri lg c n j c n l fl t e s te deosebi i , (l o tfect:t1. N l l
'. ,, l L t r lr lr ipo : irU l l l l i rr Z j f. l .e $ D c c ti rri n l l ,. l i carc:l :ri t()],tLct.\i ri | rr]]i Irri ,
, r i 'i .l ) ir
lr r r lr r r rilr rl t. c rr l tr,:' 1 rezso s tc r..T \.0 c t,scl epal ol og,i cc | cs1ttrrrs:rl ri l .
r'1 , || lI r r , r r l^ r . t .l (' trrr,r,l i o l l i r1 ,t,
i t]Ite t,i o t,)]rt c:ut sc i dl tri ei .t l )i rrl ri i :ti :r
l :r.r:,1 ;rlr r r ' : rr t iololic r.l i ti .i l Iu j l l c l 1 . D i tg -n ()s ti cl l l ani l i ()nl i c sri l l rrztl
rzri 1x,
i i rrl rl r l{ . r r l r l I I r cl j rrIIri .i t,il,l g rrs l ,rrl u i ,a l s a l i vl _l i ti si l t.l l l zl l l l ti .
l l ) l, : ir t t t i/ r : : t ti trrrl r d .i ttrt[.,l u l i itl c rto " t:trl
f]pn1nt. tl ut(i hi 1tlrl, .t!l r,l i ttr,
,1 ,'t I't,, ' nt t t l . lr , ! t i t lt ,L l tl l tl c u t)d u .l i n tl )l tl u l ri i
i rn pol l i rrrrr.i ri nl i ,l rsi ;r1r,rl i
rJr l l r r r r lr ir . r iit lr l i i , l l i ti tl i z i t, l :rl i ;rl :-rr, :l r{ j ti tzi -l i l t rl i trri rrrl u.r,lrl
t rrr rrl ,rr
l,r.r',;r
rrr r : r l, ulr rri. i r r r r r l i v rri i " i ,.l i p s t' s r l rd l I,' ,i i l i k , il r l i i r,r,i nl rrr' 4i l ri l x' r' rr.rrzrrr..
I 'i rI r l rz r r lr r lir r lii iiilii l l i o l o c i (,rl c l i rri l i s i ,i o l a z r)sl { ' r.ri rr I ccl c rrr:rii rl ri srrrri l r,,
rl rrt l tr' lr t r c r ii t r l r l i rrrl i l r s i l rt l tl l r'
N l (, rrrr,t,l ri i rrr,,rl i i ,
l ,l o (j c s { r: i l ti l ti i
r, Ir'rl Ir,I r I oI Lr I r Ir 'I,I I II I | |I I I i s I rI{, IrI rri I[r,rr1l It
0 s l l t I )l t t.t,i ti 0i i i (,l .i l \,r,f]t(,t..Mi i I ;
ll rl ro r i lir t r , r i l' il. ( ' 1, l l l ti (t).
l ') l, r ' ' it t nilt : , il trtl t d i tl rrl .l tl i tl t ' i rtrttl r ,or:t.tl tr
I i ttt 1tt rtt tt | /I / (l t l rrr
Jrtrtrl l r i | | | t':r(,I || r| :r| :i ) i rr l t,o rl r' l r' z i rttrr r o trr I,l l ti rr rrrl l rl :t l l ul l i ztr, l tL,ri rl r,
I t{;
r:|{;t. | 1)?:l).
l l ) l t:i tr nilr ' : : ilt r t r l, r li: : ir r l lt t t t i. t l( 4qt t r slilonu; loir ! i'r nd. ilr ! , r lu( r l
t,rrl rrl i zi c Irrrillii, izol; r lr i, r lr r l r u lolt lr lr , t t t ut ( 'sl( ' ill( "( r lill it r 1. r 'r glclt lot r t t l
,,r rr.r' rl i rf l tl lr ( 'r niI ( '1r 'i,r . r r it r lczit t t r ic silr t t Llo ] ] I lLi l) r t ) r iilI |ll. I lr l I 'i ir r I r 'it r r r
rr rl , : rr) l rl rrclir r ni ir r lilir r l, r 1olii,lr ur ur nilc I i t r allnlr 1icc
r ilir r {l( 'i lr r r lolr r lr 'I
I l ri l ol i rl {. r lla\ ilaluhr i inlllior si ah loiii pLlot ir lir lr'ilc
( ' iii r cir 'or ulL\ r l: r 'r ,;
, r rrl\ r'iic tlo ilir.crsc neiur'l (f irol,isc sau ilrir) altc inf{x1ii' lr)r1.'lrri1:rurt,lr(l
rl) (iornplesi ri d(f alte niiiLrri (de pildri, ?lr'.rlizil, lirxrialll pritr rr;rlr
'.l, ):
,.,r1.ir (l(, ior'*.ps sar,r chi?f ln'in uaitelc spont:util 1:[ r{) llli$cIt).
:!.(i.2..1. Probl eme de d,iagnorli,c etiologi(; i.n pqr'trliziil.e tu.cialt, p, ri..[t
\) 1'araliziile,faci.ale in.feclioure sint rrr t, mti frccvenlo t|'til
rrr'
, r|rl|r lLltritlltiL, dor.i:dinrlu -.rt-'in ultimii ani cii, IOlj oxi til! tlrlrn{'rorr{,
rrl c,,1i i rcspo[ sabilc de pr ot iLr cer eirpar alizii] or laciulc ( ( lr alr t r i'( , , lll7l;
i orrl ,' r' , 11)7 4i 'I ': r in( lel $i colab. , 19, i?; Popovit iu qi [ ?t r , st , r r191J0,
l1l8l)
,
\:rili'1, l)oi; ji)1n'r'1'orri
diverse infectii b*ctcrieno acutc sN,n(,ri)lLi(x',\'i rirrIt
,,rl i orrri trl i tiil, , yir \ r sur i gliilalt ', t r unlef olse elit er ovilusuli ( lr ) ( h0, 1l, r
.rr,l i i c s.a,), r l'bor . if r uu'i, nixor innt ui,
\ - ilu- qr d m onor ill: lr . ozr i ir r f i'r '1r
Ill,irlrr lxri lt
';rrr'. r'ilttsttl lrt'r'yrt,it,, \'irlrsul herlles zostor $.[. l)rllizii
rr i rl rri t,c ;i i rr pr ililldicukr t ieyf it olr G uillain- I lln'r i, plcct t t n I i ir \ ': uir r lr 'll
rr, rri rrrl ol rtrl, lllit o. llLr llc t lir Lt r r , pr llaliziile f acillc l) {) r ill( ni, . '. ; r sr rzi', r ' , , r r
tr,Ii rr" ' si rrl ir i r . 'lr lihit ir ] 11'( lt ior t se,
iit l f elor nt , t iul ( lo il( f vr o( l{r (ili't r r l lr l
l r( rrt[ 1' si (,,r L'jia1i1, cel ur ir i ar lcse: t ,o r I elr yit ii,f nciaLi, insolil, li r l( . ( nli. r ur l
i i ,r' r.1 (' rvull: i it r lpet l[ ot [ 1 1r l1 Jlr r llopo. Tnl t o cu, zur i, l) r I lr liziir I ir ( f r r lr l
, ri l rl l rrttl l ur i ot iit lor ' $j, r 'csllcr , lit ', Lnm l ir lt st oi( Li1o.
inclusiv unr : lc l) t r llizii I r cr r l, '
Il ) l ,tnr lt plllilizii {. t ollcr \ - i {ilillli( t r i
l rrl ri l i ol oglt zisr , , ,it lir ipt l ic<, ) ' r t lo lt r i lleil - - it t r <t lt lt ) t t r ni( t r lt lt ) int t t t t l
\1, (l r)\' (' r'r i si I ') s1r 'r 'cz,1l) 71) .
l ' ,) l ' orl! i: iilr . lir r : ir t . l. r : lr uot t r t licr sint ( 1c( 'lulr sr l( ', 'll lllt ( , 1t lli r r ll I r t r zcr
r' .rrri rl r' i , Nlc osllui lt r t t poliil r ii illt ' ll) ir , \ lr ) i( [ cii ( '] ( ' lx) i ili) iir '{'iri, {llr lli ( 'r t
r' : ri rri i i srrr ir l si ; iit r l t lcllir r iiir . t ,i I ) r lr liziil( , llciit lt t 'r ' ll) ilr ' ( lll, il ll l, zil.
l c l ;r l l i rurrriist r r sit t i t la1r , t I t 'lt t r t t r t t lir liilr '( li] I ( r lliillt ll llt r ir r l gi t t vit r r lr 1r . r ,
'
:i lLllri.
1l't
'l'11l'l,,
lrr'i r'r . ir l { l, r r r , . r r r , . r . l. t r , |1, . : r ; r r r r r , l i z i r r l t l , i t r l : r r r I i o 1 r I r I r r , i I r
,11i, l)
Ittr li.ll r,rl. l(.1)t1r(. ' 1, ; t llr r l, , , r
1r . r r r lr . i, lr . r ir li r : l ( r 'l , l i , I I | | | | : I I {, |,: I I a|,,
r| lr' rr' :lr ]r, (1l.rr || r'r l( f it |ir r lr t r r l, r r r . r r r r r r r ll r r . r r r r t
t r c r t t o l . r , i r r s r r t t , l , l r t'r, li l.,.t l
lrlril' ll:ri ll'trigrr:i, lr lt
I |r |ijt ' |) i||Lr iJ , 1, . r r r r r j , , . , r 1 r , , . , , , , , 1 , t , , i . , , l l l l ) r , i r f r l l t l r .
l(l:rtri. :,iurn iir'{ll r[c l r r ] r r ir ij l: t r t r lc r r . r r r r llr r lc t r z iid t r t o t i l l r r l r , t : r r t , o l r s c r , r r l . i r : r
,,1i,'r , irr,.'rrr 1,r lr . lr r. - . i r r r , 1, .; . , . , l r . , r.r.rr r L. .1 , , , . , , ,
i,r,.i,,1-ir:,)(,rirt) r,r,,,)tr.
: 1.;
I \ \t:,.
.
t..r lr r r t l ulL r |. , ir r r , r : , t r t |' tl i u l t , n 6 6 1 , 1 , , y , , l ; r r l r , l r r r l s r
' , ir./rir ,
rrtLl:rl.rrzr'i
ryirlr't'ri i' colduct.l audil.iv e,\tern si in zona,r,eiroarrr.io'Jrrr.r.i,
,'r'(. l'(!,({L riri citora zile insialarea par.aliziei,
cnre ap:rre de
iri
trrrrlr rlr ltt 4li dc ore. riebutul fiind la nivelul
orbiiuiarului 'eg'lli,
buzr,lor..
'l'ir\ ( r'rr(.r'(1t)tit)):r. rjtat cd 60
boid.rf ,, ilintre
doal urr
",ufe,rii,
,.1,1,',
"."qii
" r'r'vrrr,sibil
rle co'd'ccre ,Jiziologicir,,',
A".i ,i"i ,rli.""p.tibili tlr .
r rr rlr.r.rir.rr'rirplctii,in citova sijptrrmini.I-iestulde 40f
s,teri 6 d,_.gencr.sr'r,rl: r:rL ri,,rlrilrrri irlt slr completi, cu denervaldo
"consecutivii, flr:.rr|l| ti r:rlr'$t.tlor.i.r.u impnsibjlit:rrrdc rcfrr.n|i.comnlr,1i. a tnlrslr lt,csl,itr,
r rrrl irrilrrl:r-:'Ir'orlo rolrlcrur,l. g:,rde \c,,iJbilo O".n1,r"ijr.iri
ii'ii,.
-uneori
,irrrI.rrcIrrr.l'i,,
.u dtlo''.a,re:i f(,t_eiqi
cu terrome.'ul ,,to"ri_lto. .i,,
r rrrrrrlilr'. Itolnrvii cu ul simplu
ibloc,'tle conducere,nervoasi prezintii,
tr.r,rrrrri
siirrrl.o rlisbzrlIati1,dt jrrurciul de origine zJ
coartla tirn_
p:rrrrrlri .ri lrr,rr1.51i,,prgul cle,sl,irnulare
""l"J"i a trmbii ri,minr
anodic;,gatr,:urici^
(i(. :lrnllelcpitrli (l.av_elner.,
1969). itr schimb, bolnavii care
ll,'1.,y;.'
.l' ,,.*,'r
r\,,
ir,r (tr.n,.l\l||or,ulnplelJ.d,,Oh;cni
plcziotri rrn prziqdc sLimt arr.
',r'llr
,li, : , u
l, i'11
ch[ ir r J ip, i ds l. t - , . puI q la s l i r n r r l l r . , . a g . r l \ i l n i . r . r a n o d i c l ,
., rrttr,tt., -r.||1..-i||l
trr. ] |i.-lnr-ne: t , ccstia ecuzi hiperacuzie prin aboliret
rcflexului
,lr
nr r.., | | r
ilillri,rtrUi ( J ilv er j, ol, ,
1969. / .
,. :r,r,r.
ir , r lr . r , r . r ; . 1r alo r lu; , p dup, . .
lircirll crLrllLd
lrr
i ,,r' ' | .,il,r.r 2 ,.,,.t,r'. r t r , , r |uz r il( pt . r . z c n1. r r ^|u i , ; l i z. l:. r I '
nro,r. (1069)
dr,
il trl
. 1rr
.r,.r,, rr'ti{.L ii,.r l.
heqr . s z os i, er . Sindr om u l
lacrinilol
r l e c r c {i o d i l
, t : r \ ilr , , t ' ,
.,t.,,, { , , / t ) . r
l 9 6 l l ) (l c r,x d rp i , rl c :re n ar.e cornpi cti i a musci rj l ol
', r.rtr , r r r t t r r r r l r lir i l ,r-i r] l ,,o c o s c a ' e i rn p l i .i gl ,ngl i i ' .ul i .l cni ci i rl , si
t,l ,',rl 'rl J r l' r ' r ' i( .r r r . r ' v r[rril ,[{ ,i r] s i i , r" to p ro ri ' ' u l fati . de l resl ; san.,l l i ri ,,.
\,, I iirl',),r {'ril. 0(.}
l lsitriilrta rlonurvti,rii, in utma tirt.i:., s. pr.othtc' ,
il ,l rr 1 r { , ir ; l( ' r t t r x r l rri l o l c l ,r t,' g e u e ra rei i r
tc c i al e l ui S cl rri ,al ri ,rsl .t,i i ,i l rrj ),,
,r i
rl (,rr irr Lirrr;rrilt.rgonotiirii riupii, plr:rlizie f:rciali,
,.\otij nrOtoli srr
I' r,i l .r r i ir l t . ii,iu t i t i i r,c l ol l o l r,-p i c i ,t,o ss u p e t,Ii ci al ,
ai utrgi .rrrlt[i l g:rrrq]j u rrrrl
. , rrr,rrl . I ir r
I lr r r r lli' r rrrl s l i .' ,p l l l :r L i ' (O l trl r.b s lri , l i )i l .; ' f' v{ l r,i 1{,It,11)(i l t).
\:ri l r l " r r r ( r r ' " 1 i r rirr rr' 1rl ,ll r r'rri , s a p ro d i L c arL rIfrrN ;' n,si ' r r(j ri r(x,i rrri
rrarri i ,i ri
i ,
:rlr,i Irrr' rr| | I )rI Iri I II .i rrr,r.\,oltsltl)(fr.tul1(],olu,c cij,liiljolcsc .1to
cii,i tlist Iir.rrr(,iorlt l,rr
r r 'i i i rrrrr lr ' : r r r iLilr r r r l: r Irtrr.i rrrl l | i i .
tri
-,\' a s i ; l l i n d * l rt rr,ti 1r,rt1. l i i
t l ttl 'rr l l z it lt i r . iilililic rrtrl rrg l rrrq l i o rrrrl rrirl rrri ru l rr,l ,rl rrpi
' l ltis.tr.;rr,
i rrl (i rrrri cl
r.rrl gi crrl rr
: tl I tD:r' r . lt t ir r , r ' v lr i|l, r { )r1
s rrl rl ' r' l i c i rr,l
((l o l rl i rri g $ o o rl , l l t{ ;j i , rj i l l l l rl l t,i ,| \r,r,l tr,f,
ll ,(;l l ), i , llr ' llt 1i r r r l rr,r' p t.s rtlz (,s l rfr ti { ,1 i tj 1 l l tl l r i j l rr l i tr(l tt,1t1l l rri
l i l rrrl trt
l llll
8ll
i),
r. i I I I I , I i r , I I I I I r it , ii. Ull l
I , I r . , r , \ , , 1 . l l r , r , ri t l
Illl
l l r t 1 'rt ,) r l t t t tt. l ) ttt4 l i :: tt .l r r t:i tl r i si ,i tttl tl 't'tt,' r r tr r l i l i tl r t'p r e ttr tl tr
, r . L , , , i t r 1 r . ||t:I l r Il i l l t.r ) || l i t, l r I Ii I | ( , I I ( , r rI I i r,r' i ,r .r 'r r r r sl r r i r r si r r r o rl t Itr ':tt r
tl r ' 1 Il o |,I i Ir r ') i '|'Ir r l tttt t''
( | r Ir.r , ( , I I r | / i I r r ctl Ir r r :r l o tr ( i r tttIttItIi
rrr l,l
li
l r r l " r . l , l r l r :r tr r l r r t:r l tr It:tl l r r r l l t l .r 'tIl t:r l l r 'l Il 'l l r :l i l ' i l r r r ) (l i l zi l i i I||IIIIL ||II'
, , , , l r l , , ) v t " r i l l l r r l l .r r , ( i r tr r r l tt , ? ,i ||l r o l r ' :ttr ti r 'Ir I:r Ir ', r r i r ,r ' tr 't l i i l tl tr r l t l r ' ,r r
lrl,.r
r I I i r ')
{'l ': \i r l r |r
l fl l i i l )
. luliul
lL,
r,rrlilr.i(i (,lltrr(,(f(LI)(Ia,(,I)|(,I,
i ( , i {l f i I , i l s ( , 1 . l t , , S l ) .
py t i. . lt t . it : ( s p r s l r r u l
Lenril.rrcirl)
st, rlrrlo
r,lrr",',,ii,",,,,,','i';1,,"iit
-'i)i),;li;,],,;;Tj;tt;)l#illi,o;:,::i,!/,,,;"i,,i,:,,::,:,
I.
(r).rlltr(irlrcli.a't'rr1li 5i sulrlt,iit'a'r,
,plo," irr itei,iilacl,r,.Ir:r.alrrr,ir.
:r rrrrrll,r.l.rar.rrlizii
"a""it""i" i;i ii'"i""it,1
faciale.Spasr:nut
facial
g"il,J t,,,,,
1r:rlrrliz,ir.lrrr,illri, sc car.acterizeazI prlrtr.o
coitiractLU,i pel, rii]ji,.l1ii l
l,j',",la,ciirti,
'llll'1l
.cirreptrisisti 6i iq afal:i _cr;i;ii rnrlnife.stzrre
lr,ir,
r''.rf(.l]irl::.
r)r'Lls1(l
tolieo-clonico alc musculatur'ii hernifetti.
ll,l ll, ttix!'n:tn,Ltfu.t.i.,l
,rin til) ,,ru i'it rrr.,-iiiiii' r.lier'r, ,ir,rLuririt.l
. l
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l.r,,i.:r, rr i \ul,
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i s
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.,,,
i.;,,.1 .lrj,,t.
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.r . r,rlrrrl irr rurLiL:ut'ririlol,re si la ;tlli rnusc,hiiri 1,,1..r,
Ilod,.,.,ir,l ,,
r,-rrr.rr,,
:,rl,ili .jr.rtr.irr slror,ialcu ociuia cinofiilor.
Iloirisj*innl nu cslr.
,,,, o,i,r.r ttlIr,r'usrLsr,,rgt,iL\.(,
Zi t'oarfelcnt, ltlttgresir_"
;li<ler:lls do ltrri,
apar'irir,;arJ;rl::r.,r
,, ]]rrir,r,,
rtirr
l] . .],.ll,.:lli].l.: llli'til]" ruuscutare
''r r i ,
;.1 ).
l j , , l r r ( 'r 'l fi Si i ;h r ( 1 9 ? ? ) l ttt tvi r i cttfi r L f i tt sl r r r sr ttttl fr tl i :r l o * r ^ r tt' tl tt
, , , , ', l L l , ': i l i l , ) .i I.( i - , ( '{) l l sfi r l tl i r r r l .e sl i i t'r 'l i r i sl ) o l r tr l tl ( f, 5 j 1 1 1 '1 1 ;1 1 r1r',Ir tr tt'r r '
q l l l l ) r It( ', i tr l o l i tr tr l l tth i i ttr i l n i ci i tl .r ' 1 t;ttl i r l r r r l i r t'l r tl i i , tr l ti r t't i tr
'r r i i i ; r L r
, , ' , t , . r l r r r r i i i i i r l i r r ','r ,Ii tti c s1 - ,l l sm l tlsr ' PIr xItr tl u :t r ttr i tt ;r t' r l r l l f( l l Ii l l l r tr l r i tr ttl r r 't
Itttt1 ti Io t r Ir I t r tl ttl l l r :t ttr
i ', r : L i r r t t l o i i i l l t {'( }l i i J1 2 Il i l to l t'tr t,tr l r t']ti l r i q l l i r l r 't.l r
Ii r t'i r l l , i tr so {,i l l i .
r , ' r r t ) r r " r i 1 t I i t tttr r 'l ti ttr i l tl l l tr '\'l l l u i
l ) o s1 'l l l fs( 1 'l r cl \r l r ( 'p {'
[( i
( r i l zti r i l l , sl tttl-i L
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l l ti n cl tx'1 Ir l ttr i ttg t
l 'i r r r r l i ti t'i r r r Itr r ')
( l i i r r l r ti
, , t l , , i L . r r l l r r r r r sr .l ti r r i tL i,,i [r i u r r l l l r .a l
.]rIri rirl l ul ]li u 'l c cl l zttr i , i ttttttl i i ( i l 'i t{i r r tr ti stts
, , , , rr LI rl t ,r l t I i rr r l 1 I) i l r l n 'i l sa l i i t o i l ,si'r'[.
'l 'r r .o tr r r ,
, r , , r r s l i t l r r l ;i Ir u xi i i i {.r i l i ( r l c{ tl 1 ) l l i si i N g l r i o g ta l l i 0 r ' r l l r l ) i r 1 1 ( 'r l l r o l r r i 'v) i ' ( 1 r r
, , , r r ' I i l r l l i czi u tr ,' l l tr l i l cl i tr l 'i v( r si r i b l l l l l l 'i i ,' fi tr tl t' l tttttcl ti l cr t^ l r ta l
I '1,,1,
lil:'t,.:1i,,';::';;1";,I,iilJi,Jii1",Jir:;:ili,1t,tiill;;lllil:
'll,l"lil;;,Xi
-tiii
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t; cil,o-ao"o;.l, p""ii,o,i,i
lr.axtm,.irt,.rr,,t
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ii,lillxl;,
-
i l , , l ; l l 'i i i :,i l l
r tr It.ttrr'lrtli'lit.crtttt si setrz a l, ii
' r' r' lr' g irr, ' rs{ 1
r'. } rrr. r' 1, i
tttl l i r r tttl i t
fo r r r r c
I
I Ir . I r l rr | | ( | I / i ( : t l : [ ' ( ' f r i 0 t.
i: irr lr! )l | | t r f l t l l r ' r ' l | l .
illi\
(,
lr
r lr
It | l | lr .ltr
( , (,|,(,I,t:II,
(.u
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(l I
::.1; . 1i"S ilr lr ' { r r n u l l u i } l t' l l i c rs s o rr-l l o s s rrl l rrl ronsti i rl i rrtl o ptrr.;rl i zr,,
l r.i rl i i ir lliliu( jlc lr li' , a ,d e s c l Iri Il I.r' i rIr' i , c a rc s c r)or)tcrt' l rcl rr rtrornri rti rl l r
,rr i l rr ir r l( ' r ' r - ul(d0
| lu n i s a u a n i (S n l r| r' rD :rn;i l l e nte, 1gtj 6; ti r\-orn(,rJ l J)(i t| 1.
IiIrirrrrrrrL'Irr
l)ilrll,li1]iccse pot insoti do urt simplu ,,bloc de r:onrlucci,t'., r,u
r rrrrlclrrlo loilrlii, dllr cu ocaztia repetiil.ilor se pot ilrstir]a yali$ile
grllrrlr.
{li. rli rr.r'\.r1r J)o lnUsctlatura faCia,li,,Cu pareze reziclUirl. si cu Coltsl,(ruli\(,
,1 r:rrrr r rlr
' r c ilr lc . A pt r e d e p re fe ri l tl l a fe me i Si ]a. Ti rsl o tl ai 1i ner,t,tl ,r,rl
;rrrr':rl iz irlrr r i llell. Ro s e l th a l (1 9 3 1 , c i ta i j d e i l l a verner, 1969) a l el atat crrzrrl i
r || irr,irlonlir l'utniliale. Acest sindrom se insoteste dc cele mrri nLullo rtri si
,l ,,.,l cr r r r ' n, . r llr , , lu; r s o i l (.i c t' ,i ,.i .rl r.h rrz e l o r' ,c ar.l rof l i bi l ar..r.:I,..r.r, ,tr.tl ,tl
rrrrr|r'rr Ir'1oi, rftial drc:i ptlr:ilizia fuci:r1[ este Inilaterr]ri.
[-rr rl lr.rril0rr
rru p l o r r r , ( iille es t e i n s ti i n c o n s ta n t, e s 1 ,ere l rezertat ri ,,o i rl j cnl i i i rrl c rr
l i rrrl ri i ( lit r lt t r l) lic at u ). H a l e o ri tu m c fi e re a fe te i poa:te sr' Ll i tei " url i L
l rrrrrl i zr:r
l rr, r:rl rrt r r llt r r i s it u l n i 1 1 ez i l e , p e rn ri ti n r.l u n d i agnosl i r. rctl ospccti r l ' l ,l
\, r l i r' , 11, ( i1) ) .
l.li.7. Sirrlronul lui Xloobius este o rar5, afectiutrt, {.(rlgenit{ iiii 1l(,
,l rrrl o rlic ir r r , : i r r c ple c i z a ti l , c a re a s o c i t.,z i o
i , !a l . l l l ' zi p l tLrxl a i tni - sau l )i l :r
l .r'rrl :r. c r r llr laiiz ii o c u l o :n o to ri i (i n d c o s e b i d e abi l ucens).
:l.li.l|. Sindromul lui l{eerlord leprezintii, o cor}rllicalie treulokrgir,:r
:r rrrtrrirhrzci, irr cnrsrrl cr[eia poate apirea o p:],]alizic faciali peli{r,r,icrr
:r rrx i rrlr i r r r y r r r lot irl i tr' is i c u u v c i ti i ,
i l .7.i !. S crrr ir t kr llia. t r t t t r lt lt 'lt r ir( lr t . r r s{ir r i) r 't r lr r ir r t l{r : . . . . . l rrrl rtc i rrrr( i i l
lt ilt ct r t r t t zilt '
'
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,rrl
' ' i l i vc qi rl (' llii) lx) lc, ol) i{) ( 11ivc"'
sir r r lr l( t r r r lllr rr' L
i | i ' cul i " i ,, f e ( t innii'us) pt ii r qr ir 'r 'r 'l. r r iil . it t ot t r t t t 'r lr ll
lll'lii"illlll
l :;liii*iii1j*tililr:li**t*:illi;',)l,iilii,i;"i;,:lil'1
r zi( i. i r r r t ; t t t lt t t l
,,,i ,,,,r
t" " ' i ntl- o cluzi lpar cm il, t t ll( 't t i lr r selr iubr t . l- r ': '; "
i
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( t r . r 't il. r t . r t r r ir ''r "
: b) i. ie: ii', r t ae n?r t t illt i. t 101t st i(
i ' , ,.i i ' i :,;r;;" ,;i , , ; c. j
l l oxi ce. r r culiloam e il( llslit 'r ', lur llor i si : r llt ' lr l'r r ( 't r \ r "( ) I ||I I f |sI \I
r| ,.| | r0D l rl i i
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t tt t).t
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parult:ii
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sf irIir( r' :
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t
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ai
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(l'ilrltli(
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crizclorniQrr'nout7;rl) in cursul unor' tt'(
"i,r'rui
1li?S; (iastaut', l9?3)' .19?3'
, r.olirb.,
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tlo strl('r'irrl :l
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, i;;;i;;;'1-ii :'i-: qi, ile obicrri,so acompiir i:'t'zii;i
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urehro',t srttt tl. /ir/rrir r'rrt't
,,,,.,:;L,i;'ail,"htl,rlllii'ii,rtt-''ito.i <lt i'rLllittatttt:
1|ltt t't['t\tr')toQtic.
1.7-1. lrrrr.sli(lirti:rsrrtnirllo.r;ic:i
11lrer\.ului acrstic lu'miI'cste:
| ) I'.'.t
rttttittrr
t'ut rrlnrlii rt,rrrastoirltlot, N utecllii txto.nc,:r conrlrrl
i l r r l r ' o ( l i r l L i l l l l l l l r t:t
I t rt I I i rt I t t r^1t r ' '\l 1 t'tl tt'tr r t r t r tzttl tl i ttr r Ir ' l tt '
, ', ', ', f , : t i , 'i , , ', i i i i tr r z,o l r r tl r r i ;i }r i tr
l t'r r l
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oolrlpl(]x,
r)r'tr { 1' , lr r (f ( ' r iir r ' ( ' l5r i rr'l rri ,,r' rrr rrr' .r
rrrr ,rrrr rtL ghi ur i rtrtrtLrr,r' r' cr* ,rrx,
rr' i .r,l
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a sitrdititii,
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1916; Als(,ni
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rnonn.L
,,ii tenrl,or.ir_tului
pot :r,riita,1""; o ;i;l;'L1"su,e rr merirulur
.l]: :1
.,,,,,r,,.
'l;; l:ll r)r,,r.l|.
l I (,iu,ln(,mulacusti(r,
sernu clinic, care aparo irr
rr , .zrrli. r...r,,rrlrrlri \r..roni;i,otiU..
-plimul
io;i".'iiii1 ,ii,,,,,,,,"r,.*nur,,
..r,,,rl
\i\.i rdo uhi,.eir:irrr hrlriclr,
rr':rr{ lr l,11".r11
"'] ,:
l,rjn dp,,Lrmp,.,rJ;lr(.
lrrrllr{,llii,
pr.in hernorlgie intratumolal[ sau prin's}as}n
al iutcrci
.rrrlrrrrr'. Iir 1r'irrririazr'rse constati ta
e-arn",*i'odi"cti.ril surditate rarri
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l,,loncru.otogicri)
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dollasarca tlrurchitlui ccrebrali prirr
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rk, auz a1iri, destul (lr,
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I)'l'ulhuritril.u
l) il\t,lburrfu
ih naurot)ollnl
l,lM olinntolar,iocpo0 irrrlrlir:t ln ooutontt{
rrlitrif 1i rrultrilosl,r'1,r.i
vtrr'ligirrorr,xr,r,
lrrsrr(il,rr
t.[orrrullo ori r[rr
rLt zgurrurl,o
zgornol,rlrr,rrriou.
rrrrti1111.
Lrr.c 5i rkl i,ul[rulrit'i do ocltililrrrr, (11,llnnitro iL ltrror Iti pot'c.soitrtbilitil
fl
lirlri li t t lictr (ovitlcn!itt bile l:l prrrlrir,ur lolioii,).
vcrl,i.iulonlcl)1,i:rl,
vertiiul ino
inotitor.ilor.Ultimele slni, in roalitui
ol,c,),
rrl,c,),vcrl,i.iul
onlcl)t,i:rl,vertijul
rlitrrlo,
o.
l',rlru.r,rrrl,i.ic.
lil. ,,1,'ttlsol,o
wrtija't sint amefeli in infelesul cei mai trannl gl
l u yi ttl ,t t lt t i :
rr,) fir,lttr:lo_voltije de. origine c:i,rdio-vasculari,(boala Arla,ln-Stokotr,
I rn tl i u tt ' t liilo sinuzale, aritmiile, tahicardiile, stenozcloaortict, eic.):
b) l'llst*r vr*tije din unele sti,ri prodrornalcale anumitor crizo d0
rrpiloltsio
I
o) llrlsolo vcrtijo ds origine psihici, (indeosebi din std,rile fobice):
r[)..1)r.r,l,solo
vertij_e do carzd, oculnrl din tllburii,rile do rofraofie, in unolo
grulrrJiziiu,lo rnuqchilor'oculari, la, indivizii cale poartl lontilo ncC0l0l.
prrrrzrl
l,orlruviciului ds rcfrlc{,ie q,a.);
c) I'u,lstrkrvortijo dupii hiperventilalie ;
f) tu,lsrrlevorti;ic prin tulburriri de statici, (a,st,ilzo-a,bnz
ice - ln tftboa,
ttr l,ulbtrrll,rilctlo <:oordonarode natur5, cersboloa,sii):
(rl'(i.),ll'(r1
tti, citrltlritrtr
t[o vtlcittilhrlo: t,ttttt
lrtrirurrur'l(ltlitt 1u'oot'lio
lrtrrgitl
tlo ,,sitttlttllrtrol,rol:tltit'ittlitrt'.
tirr(\il,
Jl('t'vlrlui
vcx(,ibt.tlar
liorrll,riryitlotittrtrit'ca,
I 'ur liaul ar il,d!,i stmiologice:
Vtti jul aestibulatr( denumit Si.rel'rolaltirinti.c
J oste tnai lttl{itt ittlltts,
rrrri puliri zgomotos fi rnai putin calactclistio drxrit crrl laltirittfic. I'ort1r'
ifolmr oll (!\lc('t'Jrilrilrl
rrrsii,si, aib5 un caracter pa,roxistic,de 1;iprndni<)l
r,rilcririlccapului. I)urata accstui vcltij vestibultlr (qi a sitrpl,otttclotrrsrr
,rirrlc) cste variabilX, in functiet de natula fa'cl,orulrtiet'ittlttglic,crtt tlrr
sau chittr o irtcxciiabililltlrr vcsli
'rlricci antrcneazi, o hipoexcitabilil,ato
par
tle
lqzali.
il
lor
',r.lrrt
J! osibili.t d,!i 7tal,ol ogiee :
A ) N etritelaaestibularcinfaJioctse(luessecundar$i ttrl,iar, IrrtloI,irIiLii
, lridcmicii,, herpes zostcr, febr5. tifoidri, tifos cx:urtomal,ic, In(rtilrgili
lolt#rospinali microbian[, meuingiljc virotice, mcniugitc tultt'tcttiortsr',
ripii, difterie, malarie, rujeoli, brucelozli etc.), I)etalicm rloltr cil'r,r'rr;
Neurita ustibulard si.filiticd' (satt neurolabirinl,itu l'uetiad'), I'tl, nni
,rli ^)in ultimii ani, cste produs:i prin mecanismcdc rrre jugo-virsoulll'ilfi
rrr stadiile secundare$i tor'liruc ale bolii Si oste car:lctorizattipritr vt,r'l,iil
,1,,lrlare Yiolen{5,,crr eri&ccrblri la miEci'r'ileoapului, olr hipo:l( uzic f i
',ll
q,rrriluriin urechi. Pe lingil lista-gmus qi rlcvialia bralclor, se ovi(l(,lrl ir z.ri
,' ltipoe:citabilit al c vcslib lari.
I:) Meningoneurifut oestibulard,u,rliditd' sc pro{luce llr ll)roxil}nli\
l, -10 zile cle la a,par:itiapa.rot,itliteicpidcmictt, asociinrltt'sr'rn,\rli ri (l
tcziune concomitenl,i, a facialului, e\'cntual si :r' itltor' lrcr.vi cll|rri{rtli.
uncori bruta.le,sin1,doclinn$al,e
lrirt lczirtttirrrrvli
' trr,nifestirilsvestibuJaa'e,
l, co, rneningeale,precum Di plin r:dtlm consccut,ivtlot'cgliirilol cirrrrrlrrlolii
lrrriferice intraiabilintice. Se realizcazzi astifel utl sintlronr tlirl coclrlco
prin acufeno, hipoa'cuzic gi rna ifost,ili \,('sli' r'sl,ibular,care debuteazil
lrrrlnre,Ilipoacuzia poate li uni- sau bilateralii, de tip percelllie,cu ovolu{,i,.
lrrlrirlii,,uneori pini la sulditate (uneori definitivl, all;oorit'oversibili,orlrrli
(.r vindecarea infecliei urliene). Scmnele vesl,ibulare se tr:ltluc pritt ulizc
r rutiginoase (uneori foarte violente), nistag lxs, tulburri,ri rlo cchilibru 6i
hipoexcitabiliiate vestibulard.
c) N earita cockleo-aestibul0ii zonatoasd, (hcrpes zostcr) csto [oir,r1,('
r':r,rii ln forma acutii, veltijuJ apa,re brusc, ltr crize, oda,1,[cu il,1)l,t'it,ir,
rrr[ptiei, in contextul scmiologic al unui Findrom vestibular aru)()]rioH,
rrrr duratii de 3*8 zile. Se poate asocia o hipoacuzie do pcrccpl,io, rldrli{cir,
,,r'olutiv5,rpinii la suralitate totali, $i definitivS. Unoori, instr, sinrlronrrrl
vrlstibular estefoalttl discret, cu ame.felimoderate,pc prinl plan sil,utudrr-sc
rllt]o simptomc ale herpcsului zost'er cefalic'
dJ Sdndromul l,ui, V ogt-I{oy unagi, vorosimil dc originr: virol,icri, tsrrr,ilr,z6,I ncvritl'i, oochlco-vostibularli, (cu sualitate qi crizc verl,igiJlol,so),
uvoit[ l)ilatoreltr, vitiligo' rrloleoio 5i polioztr.
a\ Sind,romuLl,u,t Il arada, fourtc ril,r, tot tle la,tuni virol;icl, ol[.rr
t,Bomlun[totcu I)t'$ft{loltl,ul,rntxliittd ilt plus qi dt)t{lillirr:(lo r(11,i}rI.
.lr'ritlll (l(! l'rt't:vtrttl.oirr rrnck' f[ri, sn
I\ Ilteninllo-net.nt-hrtrcnlrnalt,
llltr, ct'l ttttt'itttlt'uoll,ttxttcirtlou lczhrrri
tr.rrrltr0TLin Slnthom ooohloo-vrtt'l,il)l
rlrlltinlo do rrorvi ofttolortl El ou Sotnllotlc polirmlicttlotrcvlil[ 1,tloroa,
orr
sinrlrrirrr liolridiuu do lln Oullll,ln'ltu'r'r{.
107
,r{.
ri,,,r,,,.i,,,2:,
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i,i.* ,;,i,,illill,,,l,,,i;il:il;il,il'l,i;,]]li;ll,,ll,l);.j,,;i1ii,,,,;
li ) ,\ t,u t.t\)(liilr
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tilf,"li''j.
,n,,,r,.r:,,
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, t', ;,.,,;;;,;,i,,.:',iq,:ilil:],,]:lil.,Ill,^u;;.;1,'
.,,.,,,,:,
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din unhrtoiditrtrttr unohi n.,,,t,(tt,i),t,,\
,t,tl
, ,,,,1,,i,,,"1i,1",,0''r':t',:,'ii,:i:
z,:rri,,
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,) 11, ji(rlifolicc.
, , ,1ll,l:.iil,l,lii,::,;i'j;i:,:li;iJlli,i;i,;;i,,i,lli,'i,;ii,l,iiiillil,li,,i,,T;;t,j,i:;1,,,1
1i;i;;i;'.;i;;ii;
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ill l;11';ll;;,'r,:'",,1;lt;ilil,ilifl,r,iv,,srir,rri,rr1.
,,,iiil..'l;-iiil;l;i,:':lJi,,i:,il;il;lillll:;,;l;j;llll;
i j ,,1: ,,..{,\..,iroii,i,
,lt;;;t:r
ii;;,:il,,iii,,llil,l,l,llil:li:,i,lilil,,lil,:t;i:,'lll;,:;i;,,tl,l,il;i,,tijlii'l;"1i;iil,il
,,,,,r11),,1i,,'ljli;;,'l;l;1';;ll,,lllllt',1'l',;j,ll;iiiljlili;,ilt;,,ii;ll,",Jt,lll;;1,;';ill,,i;;,liij
: l l frl l
tt
r ' r r r r llr lr r l rrrrrri s i 4 rl trrr,i t,t.,tl i b ttl (t,t.i r.,,r,,,,r,i ;,i .'
i rr l i rrrl .,rrr' l
t{)11
,,1&,1
lr.lr'..l'r,ziLur..
(l''1r' vi.irr r,,i..lrrtr., llt;lt, ll)??, Jl)l{0; }1r1xrvi.irrri l,ir,s.rr,
'8tl:i) )t sir'inltltbulbia )llil,l|il!,81,!iIij(r
\ or,l,ig,irorsosc plitrsoirrzi!
trrllrn.!
"
1rrirri,r' sirrrpl,'rncloinitialc, pulirr<l ,,pii,rtlt,Jic'in crize foail,o vi'l*nlr, iri.
rr r,i,lL(,ulrllur ufoalc, aproapc ioldcartrra accentuate la schirlbiirilrr
dt
t,dr rr' :[I, (.1]pllrur$r asoclat(.cu julbuliri de ec]ilibrr.
I ) I )t lt ttconertarfte tulbu{rile
vestibu,lare apar in pesi;e 90}i, rlirr
,rrzrrri, rrrilnilrlstindu-sesub forrua unor crize vertiginoasg
cu ahuri'rnttrrillilirlrrril, i!.speciai in cursul.py.seulilorevojhtive -ale sclerozeiruultiplc,
,.1:"r',rrrrr.l,ri
,.Liar ca sjmplo.nle.inilialo.
Crizejcviolenic. br.u1rt,.,sj;,i rrLrr,.
\ | ,rr,,trl l IISII |
DUitlora[,de ojJjcei olizottal;i schimbilrr1'rlo.oUs,
'.Stc.
rIi|| |rIrr.r)||si1(,.t1(.,1
stu |otalor. inso{i1dc l ulburiri dc ocbiljbrrr.Ur:cot,j,
rlrrl.r,itr'irruci par.ezecie ooulomotor citern, putern constata un
rljrior.iit,lt rtoltriculat,
'istagrirni
,..ltgc. oetu|lelc sp_itao-eerebeloase
pierra_Xlarte, L]t, boale lxti,
,,
,f.)
,l
I t u\t! t, rh .:t
di.', rstlcJut'nede altoJii cerebeloctsr
puD apjrca accc,.^Teiti_
,1.n
.
|.clorl-tntc.
clt duraLc dc la {.itora minutc
''r):r,\{'t
Iini la citcr i.i,zilt.,
ir,rioqlriLlo
olt ttaxie ccrebeloasii,D-icu nistagmus, cao", -,1" obicei, eiito oril
,,trl:-1,l,ib.{r.r',ri
ii lcnt, pctbisijnd si inrie g,izelc icrtisiuoo-i. p,ot
, i|l',r'r{
{ .,.1
Ioirtu] li sitrl rornl{l,le,.darde mu_licot.i ilrala J hilrer|xcifabili_
"t,,
lrLl(1,l)ll,ild fi:u.nizaohiar unple indicat. cle diagnostic prec6aela
adtli,ii
lrr('r i r ir'('sirn],tiomai,ici
din familia rerfiectivi (Fh cox'si L"i*tl -igil;i.
ti
.4l
cr:tiurtite
aentriculului
at ly_tca qglio'arne'qi .[i"t*i
)
.
*ri.l.*ii
r.r rlc vcrl,r'icul IV, glioame de trunchi cerebral,,alte tumorl buibo-pontiitcj
iilr rrrri()(i'iiri tr,pt'oapetotdea.unade tulburi,ri cleechilibru, nirtagmu s
d'izont,o:
: rt;r,lot \
divcrsei*Lnnc de tlirr_rrLi
',rli(,irl,\'i.tsiiLuli,semneCn!.pbcloase,
,<i,.(r(.||]
,' rr.,)rrlr,
f'ol,rlar, ]si n]alifegtet,i vertiginoaSe il] c,lize, tle obicei
rL (,|ii,r|,lI|L{)
si acccnl,uatede sclimbiriJe de p6zilie ale capului. Se
I;rritt
r'\ i(l('rtiii,hir,u- st:,' i'excitabiritatevestibulird t'" p""t
rrl u rrcoli JriJxtacrtzie.
"r.'i".i"""i"ilt,ir",
I'rrr.rrritrlr ax1;ansive vel.Tiene qi rle ventric'l al lv-lea p'ezi'tii
cel
rruri lqflr;r,1,irr contcxtul clinic
6i iindrom,ut lui Bruns, arr"
,tin
i. y,l1
dc crifatcc
qi""osti
vir.Jtult,
'1.'1]ll::l::l.i;.1
,L'('li!l('{,,
ir,i\ir(,11i(:,
Bljxlcsltl}lilluil:i,rii, tlo cokr rnlli rtttl{;tlttf i, sotrttttrdo lltt'cllttrr
ru rlclvilor octtlomotori, ott rliplolritr.
tti i,ri,.lorn. (aI .lui .!'iytlty ), tlr'ii td'ittlttgitr
c) B'inrlromut Ttseutlontti
r,r..tz*tii. se c*ractdrizc:lzrr,t,r'irr inanitcit;rri ver"liginoascirrst*lrl'r' rru'irl,
il,r,, :m,i nrrtin brul,al decib-in boala Mdn.idre.
S1 VeitlSul paroai'sti'cepiteptia,. tr'orna cea mxi pctent:r' do vtrrli.i
psihoselttoritt'l.ii
lraroxlsiic epil'epnii este repr6zedtat:a de criaa tampo,ali'
.er :aiie lle ineleal,i 3i-rostogolire(Arseni ii colab" 1978; Grsl':uttl'
",t,
r:r;r r -vd"iijo1
F6Joviciu ri colab., 1976i Stoica' 1978; Popoviciu \siPascu' l(lii{)'
ii,,'r
.sponran(in cazulcxisl'r'tr1r'i
{ie
'.
urrrt j octr cll eploEetrtreoseuitde adtivl, fie in mod rellex, sub itrllttctt(rt
'o.siibulrtu, care realizeaza cxacerbrrea paroxislicl :r
.i,'nr
"""it*iii
l'ocaru-lui.
lrestibutogatud'
V erri.iwl'enitepl,r'c(epiteBsi'a
) poate fi cliferen{'iat tlo rrllo
'de 'vertij - cu ' aluri paroxistici, (Sloica 1969' 1978; S:t'gt't'
torruc , lilicc
.
,i . uirb., f'glO; Gastaut, I973; fopoviciu ii colab" 1976.;.PrinciPrulcl'r
de diattiostic diterpn!itl, sint : a) alterarca cunotIin{er i o) 1l'Fr'r'rlrrr'
'i:tite;ir (Iie-independent,fie altermndcu alte siulptomc cliticc (lo ('l'r
rcrLiiului
i,';"'";;d;rH,-tie
ci si buli, in cadrul unei crize epileptice convulsiv.
i
g'*o.triizat"l
: it couslabareaanolraliilor EEG pr'rorist ilr',r'pi
.,
''ul*
lclrtice
cu* loealizars ieinporalS,. Traseele EIQ po! prezent'a' dt':Lll'lr'l'
iol'rue iritative cu sediu temporal qi in perioaclele intercritice'
9. Exi.std, insX gi oerlije tenporale ne.eltileptice(in tumori, .altct'tit"
l.r'rLum*iiJme de lob ternpor6,I), caie apar in crize cu durati mai ltlttgii'
rlrr rliteori sint aproape lerminente qi-au ulele-caractere clinioc pit'rl'itrtt'
t,r,rle.
Astfel, bolnaivii idcedrci, senzalii .le ghalie, alorid.ica,resau dc loltot il'r''
(L(! irrrllr
rlu rle proiectie in diferitele pianuri ale spaliu1ui' inso.lite sau nu
r,,nolCiostaut, 19?3; Popoviciu qi colab., 19?6; Popoviciu $i Pascu' l1)$o;
| 9E1).
-!r,t..,,posrurat",.r-iolcLrtfinsorir
I rr :L l 'i r . r ' r lr ,t.ir , j( . hlm
l )j i r' l c d o p o z i i i c A l e c a p uIU i . B ol na.i ,,ul
i ;i
mt.nti rrrl
,:r.1,rrl
rrrr,,trit
1i I rrrisc{oda{I cri coipul 1in.,,-60""*
i"i.,,lt"i_
r r,r,lr, ).
".,lil"ii-..ii"i
7) Nut,rnnitatestibulard(Dr1 Hallpi,le, 1962 Cawthorne colftb.,
$i
llrt;1,;l\I i I' |.,r'ri(.I| , ISZg)cuprindeB $formetlinice : ;
uas,t[bulurd
p^ro1triu.-.zi.sd
esteo afecl,iunobenignl, cri inoi"
, ..,::!,.\'::::,,,:!ta
,
(30-5qde_ani), careinterescaidneuronifvestibular.i,
lji. ".t I Ll iii!l]9 i$ulte
Debureazi,brusc prin crize vertiginoasocri
::l:
:l.ilill'
1ll;lll.! $r i.cr-qenr4,.
rr('||s||
t"lr,rr.
in citcva ore sauzile,ciup' carcdisparc.-Nuluting0
Irrogrcslvir
rri. irxIrr,I r'i,irl,onsitatea crizelor Mdniire, dar qr6bek
(ir..i;;T;
l'l,N( l) .virltrnli*zii,
".*tii;6;; de
sindrom veslribur'arcu-rripoexcitibitiitate
lar1,*r
rtli rrrllr,l,tl.
'n
IN PATOINGIANIIRVULUI
DE DIAGNOSTIC
2.f)..PROBLtsMI]
GLOSOFARINGIAN
turingirvte.
ll I
t'ttrtvrttt
r'i.rrrrtlir
rl,.s,.hirtr.r,r.,r
srr'ir.r'i..carr':r,il,ll."i,,;,.!;,''i1.,i:ill,";,i;1.],';.'.""'
pr^ r'rissIrthilc,,sl,o
lli:rgllrsi'icrrl
!.lf.i!. Novrrrllliuglosolttritrl;irrrrri.
.st
itt ltttr,lir' (l(' {'clc /rrl Jt']'ttt(cLlture:
1(,lrf1[
ullot' l)rlr'l,iotllllritlilir
attii lt t'i.ttl,i,tirii satr, Ttrint.ard (est'rl'ilr'lii ilt
l) Nnrrutgia glosoJu'in11i
I r,r'rnirr.rlogia riecbi teime,n care f'olluie abandonat) afecteazd ill go]ll'rtr,l
lrrrlrrrvii peste 40 tte ani. putind insi Bli apar5' ;i la tineri.
t)('l)nlnl bolii cste de cele mai mdte ori brutal, iu llini, siililtal'o
rrllrrrrrlir. lntre prima crizd' durcroas5, si -urmi,to-al:ea pot trece cittvll
r:itrlirrritrisau cifcva 1uni, perioacli,va'riintl mult de la caz la caz. Criztilrr
rnnilorr(f rlevin din ce in ce mai flecvente.
l)llr'rror debuterzd brusc, violent, la baza limbii sau intr-o zonii' ditt
l,,irr rrnristhlia tii. Locnl durerii maximale se afli' in regiu:reafarirgiarl iii
"inelr-ati, rle nervnl glosofaringian' I)nrexea qi zonele
tlo
lrrigrrrrli
"s:ie
ilrrrli.r'o sint sl,rict localiza;teuDilatelal (Arsenl fi Oprescu.1979; Dcptui$
| 1l{;8).I,l'i{rl(son(1963,citat de Arseni $i Oprescu'1979).astahilit klcalizalerr
rlrrr,'iii irr lrd. ,o1u?,in funclie de {or:ma clinici: a) in forma tlctsir:d':lir'
lrrzrr lirrrbii, in regiunea arnigda,liani, cu iraclieri^spre.timpan' ruri"ljlll
rrrrrrrrlilrrrlrt6i lggiunca submarilar5:t:J ln.forma fat'.i,ngianii:in regiuncit'
rrliirl(l,rliirnrj,'" r) \tt fonnu ti.mpanicii satt' oti.cd: in rcgiunc'a awicrrlari' prolurr(lil, s:ru nr condlictul lutlitiv exte.rn; d) in marile ytatotisme il''trcreu'
ir';rrlinsj .in zotre m:ri iltinsc, respectiY rlai inferioaro fa'tlii't1e ccltl
rr,,rrl,r'
i,.lrrlrrlc ttrai ils (Arseni li Oprescr, 19?9)' Bolnavii '"1i(hel'eaz5'dlrroreil
,.rr j'iiirl tk'oseLtitile violeirtS,'5i de ahoce, lscmuilrl-o cu o ,,lolitlr:ii clo
devtlic" etc. In rare sit a;lii, durerea estc apreciatii ca o
|rrlil,". .^rtrrsoc
'rlist'onfot
t (BoJrm qi Strang, 1962 ; -Bues, 196ts,,cit'a;li dtr
,, riz,,ii,. ,[,,
()l)r{rsctl,
l9?9).
Durata unei orize csie la debttul bolii de 20*il0
ili
'\r'rr,rii
cltrerli cst'tr
lncetarca
bolii.
rlrlr-se nrilol1,t odat5, cu cvolntia
',',,,rrr,i,l,
fiilcl asitriintelpl}loxist-ice
intel']'aleJe
ci,
d
ebul,ul
si
lrrl,rrlrl.ilrr l:t'tLft,iiort
de la uI boln:w
r-al'iez5,
du]eloasc
intru
crizele
ioliktle
libcrtl
I't'l
1rIrrrrrirIitur.
zilc. Roala!o:Il()
irr rrll,rrl,rhr lrr,cil,oi,rtItrirutte 1tini,1acitevil orc s:l* Lliteva,
(ca;t llttl'
dur:ite
qi
variabile
oa
remisiuni
rlttltroastl
,,i,rlrri itr l,ttscttt'i
:I|l||,1r, t)r,r;r lrr' I -i atLi). Clizclo apaT tlc cele m:ri multe ori ziull. cltt
jn fazole alvinsa,te2llobolii De asentenea,clizt'ltt
,1,'t,,'i,,'itirrs:isi tton,Dtc:t
se relct,i la intervale de tjmp valinbil'
iit
slh't,,
care
;r, lr.,i,r1r'ul)r
"d.eneTralgie glosofaringianri presrlpinl0
corect
filrthi.liIrtr ilittrtttotl'i,r:t,t.ltti'
rrrrrLrlir',':r
lrolrLrir.tjltLiin timpul unei crizor anlliza facl,orilorcaxedetermjllil'
(,,trigger zones") (Arrrlrrrli{irrrlizci qi locatrizareizonelor declartqatoa,r'e
qi
1981)'
Pascu.r
r,:rri si {}lrlcsctt,19?9;Popoviciu
Illrriirirol), pacieirtului in timpul crizelor-permite ollscrvarea crisptirii
Ir,tr,i. rr,rrtrr'l:iti i iuloluntarc a miinii ta nivelul zonei inferioare t[ ltilei fi
,rllr. l:r,r'illr.,, sa,u sDre urcche, intrerupexea masticaliei etc' Fenomcrl:lo
r I ,,, ,rr,, ,t , ,ri i i :.i.rrtl'lr r' ."i se pot manift'stnpt in inroSirr':rhomifotr'i fi pritr
'
grrt'ii tlc partca- dulolii. In tirnpul crizci- tlurerorlsc bohrnvji
rrscirciuncrr
F,l,irr.(l(! rrbicei, olisltrti, cu fncit:s imobil ,si a'plccfl1iinainl;or pclltl'u ll
lrr,ililrr srrrrlg,r'crsnlivei. ln alte (iazrlrirbolnavul iqi montinc callul a'llooatt
sn,rtili aptrtd,01 mina' urochon
nrtts.ttlllttra h 1;r'r'txrcrvicalli,
rrr :r rrrlii.r:r,
rrr,rri
r'\1'\rl)'
r':rttltlttl
llll(li1:iv
lurlitllrgtr,illl
1i/slrtt
it.r',,grrntrl,
rcfirozinlir'o (lllpilr
ttprtt'i{'irr
cliz|lot
frtol,ot'ilot'tln,trr
Atrtlizit,
Irr'cipil,i!
tgiitnt'[.
trLcnl srrlorrtrrtitttiliitttttli lrrrlnltv(ilt llr'vtillgi{rglonolilt't'it
it rxrt'l,tt,rr(i
ltt
tl
HJrt'tri:t'l
tlt'iztrlot',
tl|!rllllnqltttrn'
t"",, tttlottlrltlitt
l)r,,rrlrrlilirr
iorrlil tttt
'',,,
:rl{i
Irrolot'i
ttrfii,.;'i,ttrtlrtlrr,rLrglttlifirri,r'risl'ii'rii
r:ttl
ii,rti i,l,'1,1"
Dr',',tr,rl,l,
1tt"'rri
lt:rsrtltti,
ltlsrrrt'rrttIlrtl'ttl
criz,'l,rl: rriitrrr:ti'ttli,Hl'riitlttl,ttl,
, trr,,Ir',',ipil,t rtprrtr(irr
,16
I I:t
' '"f"l"."ir',llrJ",i]:i:$ri*:"t:i*l,,iiii;li:;li':
;l:rll#i::*'l#::;l#y#til'itli;*r"*l!tri:,i
lflf,
:o*:i
jtr
ulr,irri'r :tiriril;i,
,t ilrrt::;rx;li
liri:
lil
i*lxmil'
;i;i;;;i;;
rcsiuncrmtt-'r
ral r"nduclrrl:'ldit;i'ctt'r'r' -'i
l''I
i:;'
lo::'jl'I|
'III:Ii
'
ti o' or"nolrt'ingologicc
-"' s-,,n
"tn;oi
*'t;n#: r:i",.#*r:":il,i:!i:il
caz*i
rles'is
liii$ *i:iilli::
,,ili L.
j[i:i]]
ji,d{
:ili,:t',tlii*1"'!i?Fi:Li
;iltrui
t"*yil".:ji,."""',f
1.}i;r
lii.,irri
1e?8
r rrrrrrrr
p"p"'i.".;i e;o]]1"
l?il"].i*tT;-ti*[:ii".:i!H1':rgil';
'S:ll*:ii);*,""r1,-q,e:Ld,";';?,,:?;.i
ll;1i,T;"#!'::ffij'l;,.'""""
"1,irl,cr
motrorii salr gusia Ye'
];lj
;*tlti'{,,j;{,;:i;,^r,.|,0;'il,i,ll;,i,',!l:;i,!:I
rrs :'
dc'l
*T*{ft'"'?l#::tii';tll*'.i:ilr:!"i:l{'rinl;i"'
jlr; I ill;l
l;;;
;
lll
lll'jil:
;
ill
:.'
ll';:::';
:il"
rl;ji::l;l
-:
l',,
tr r r r tr r i i r 'r rrl"i r"rr''' '
;,;!:'
.1,
,,r
u',1,."
;i
;i
.;'
.i
ur
pc
r
,i
..
,, r r ,bii
^l l :i l l ,'
;*:*l**i'lr-i*rli
1r
iiri,i
i1
(?"
i*;lii;i,
iil'In*?im
J-$Sr:;l
xlT*i$:1;'":"'"""1';;liti:iliii'li;
:,*iT
\s
lff:{ii?fr'{h-itffTfr
l,lq:";lrihi{",,$ff
iihi#hiili'"H::*;:*$#,*u!'*;
-'nii'fifiTJ,:iij'lyli:'iil,',*':*,:'';,'',1"{fiiJ'i';
ltiLi':iil;tii,:lit"i
jgi ;g iliq*iTl::d
ii
i,,iri
;iiin;i
1r.#:i
iilliilil,;,
"irf
"i
",
l,
::r',,lnl,l
l'flllil'ii
tlll,
illll,.)/'li,{t,ill,i],:fi*il,,
,t:frin
iifr
rt
il
II
/
";;illl;ll'll],':iii
",'ri',flllJ
lll:l;',;;1
lniil"
llil;i:lll,;
;i::[tl,llil"'
,i,."itt,'
l :r '- l ttfr l i r r ;i l r l l l F( 1 - r
tfr,v*r.X
I \,,l t't, r
fl i
r''' I ri ''
rr,,
,,ii|ItIJlii,'r
l)tll,r,ltoilir!v:tltilll,r,. Hltt(lt.rIrIluI
I,sl,(!(1()ItI t)I(,I,it,l, rLt u l,tri_irr
cltitr1(':t,Nir'
.lr s:u(ii|nl.o
vior(f r,r',rsrrr,rirrrirrri,
(lu tl$urintiro novr'tlrgiL\gl(]solr!t:rrigirr,
\i, IoNllt'oIiv,tr rrlir:{irrrrr,
li. bo s,:rnudc tliagnost,io
cst0
1,,.itfll,lli
rlr|| ,'r'(..
r,..l)r'r.,vor.iitr-r,
in_punclul lllrirrgrrlrrisuperior, adicd,intre ci}nu] car1,ir:tjr rr' Lrn( 1.[ fr osul l]roi.l. lloba rlccisivd este alcoolizarea
nrvului, cr,r,o
l'l||rl|rr rltllerca,. Uneori se constal,ti asocierea
sindromului laringritri
rrpcliur' ou sindromul cle ganglion sfenopalatin.
I I ) Neuralgia glosofuringianii secund,ard(simptomatici)
g]os.ofaringir,ni,s^eoundari,se d.eosebegte
ctini,c d,e aea,primari,
. ..t ):.1.1..:l*l
rin :rL(,al'cte
t'r'
elemnnte:&) fond drrreroscontinuu,pe cale se supropull
pr,ro\isbice: Lr) tlurolqa, nrr at idqi - intcnsitateb, dctci
' Ii.i,r:r,rlr.r.[rrrcroasc,||||.r,'\ l:llglll pnm rf lr : c) dulerca so .localizeazii
aproaDctorclpaunaitr
,:.,,
al. g-ibul i. crr iradieri r,uricutare si frr:r,ndibul*r.e;rt.1
1'11
lj^,pro.,ly-dc,,' ,.',lr\t:Lt,i
ltipo- calr tnrstozi:l lojii.amigdaliencsi a rngiunii farlngie'n,.:
r') r'ris1;i 5i semne de afectare lsociatd ii trunchi.tui dotor ar neryuru i
rllosofrrliirgian; f) se a,sociazaqi semne din partea altor nervi
cranicni
rr\ ( r,rrrlr; g) sc constati, extindelea ariei durcrolse peste limitele
anato, ,. j,;1l
glooof*ringiao ; h ) evoturia cs[e progrfsivi,
cu agrav:]r(,rr,
"
,ll:.1I"]!i
. | ' \.rrl,t.r.r''":li
r':lpld:i r simplomat ologioi, fdri rcmisiuni.
l |l ,.rrrrtiL
unor lorrnp ll.ipice.si incompletclj, dcb t, sirnptoma{ologirr,
t,, t r:rlri' i glosOlalingipnC
recundar.r'eSLedc cele mai *r,Lt" OIj SuJiCir.llii
rr| , ir'l:rcl('1lst,lCu.l\lUIfe tot me rlp nevralgie glOSOfa
r.ingiani1S{.Cundrui.
prri irrsi rlcbuta cu tablou cJinic rle ncvraigie
i;i" aceste motiv(!
1l;im;r;.
11rrrl)11'r.i
tz.'t cii orice ,er'ralgic glosofaria-ngidnJ,irebuic consirlerati, rlo
ll rr,,''(
n,rmzridrrpi efectuCreain\.obIjo:]I.iilorparaclinit,,.
1.'rll .r
1 lnlynrlar;,ri
r '||) |,t' r'r.:t
Ulnr l(.zUll.bc rteqafi\ o o vom cOnSidr.r*pr.jmit,iv;,
('ttu,xclc acle mai ft ccvenJe aie rrcwalgiei
gloso{aririgiene secun{larlr
ilP t./r bazei.ctortiulai liuai alei ,;1";" -pi';"; .i,'
..',::.1
.:.."\
.t"".':t:!j':"^:lJ
!7lilt
tll..(.'il,lr'
b) tr&umdlismelecranienei c\ arahnoid,itelecen:r)ttrt: (),{,Un..r'rnolrflngc);
t(,tt,crce
7unrcti: meningioame, neurinoanie : e\ anel)tisme ulr\
|rr,r'rrIirIr,i
(jl,lrunc i t) i,nfec,tiilocaie, indeosebi amigda,iie;e
etc.
I II ) N eualgiu glosofaringiand,
,,Junc!,ionald,, (simpatalgia)
,\r,r':r,stii,llormd, d.e ne\Tc,lgie glosofaringiani, se caracterizeazd,
mirr
rI rr!.r r cr rritt,totjercle arsur:i, 1.1b:r,zalimbii si in
regiulea trUgq"ii*ei'
ai,
r,ir,rlr{.r,{'rll}ro trompa lui Eustachio, spre ur-echeafoedie,
oar Dl spre alto
(
zrrr.r ir'o depii,qescteritoriul nervuluiglosofaringian. Std,rea
dd dii;;i;;i;
-tilidi;
:t,lr.ltrLvilrl r[r.viuomai prosnant:Lin-1ifrp-u]clegtilt,iliei-..
in Soi;'.
l'lrr:r.rii :urrirrrprcsinunui"corp sir{in.'Din ,1;;;;;;;
c,cesl,i
n:}ci{!nt.i
r,U LUSC.
Ir|'r'rrrrrirsl,lLsnlt'trltr-oglenc
rn ineerCxrilelor de a Climila l.co"nrit
rri,r'riirr)'..fi.,za!ia
do arsur.X
se-.asociazi
O"-rii"ti" *i
;;;ilriili""1i
nu
po_f
fi.obiectivate
raun er"-ui""
al gusi";;i:
l'1.'1,'j:.l,,i.ll,lli._u-tii,,care
|,r! | r,irtr! ctzrrlrtc se noteinzl ,li rut conte_xtnewotic, care
"du"t
Joac6 un rol
irtrl)orlrltul;
in intrerincrm clur.erlor.
i,l.9.ll.-Puraliziarrorvului glosoftringian
I,,l,l'rrtizi|,
nurvului uk,*"1:11_iilti,l.r=
so
l)rir: disfagioponNru
itlitrtc[1,o ilo]irlo ; tr:lftlliziru rnr
-m.r,nifesti1
.l ) ' l ' utt,tt , , , t il" d, f ullulit i, 1t t t lit : 'lit l' r "'t r : 'li l rt ir' . \ r' rrrrrrrl t |l r r r 'r r
rrrrIr,,tl i tttl . l ' :r't : uljzi:ri,nr r . 'tiiir r lr r i lt it t r 'l t ir 'l'r t '111"t ir r lr r l |; r 't it t I ''I t I i lr llr 't liL'': l
l,'t',lrtl5ar'lra;ri dcsfiiquralicl"'plimrLirti f itrrli rtl-tlrrelrrii{ici 1rt'ttlltt rrolirli' llt'
'
,,f',iiiii, a"id,,t.toasi poato'antr'"n1, lllil,iurr(l{ r('rt ruli.trtlttlrlttl' itr Lt'tittc'r"
r,, ,l*r"t iezi'nilor b-ilaterale at nt'n t,hri glostrlu.i n gi lrr, l,ttllrtrtri''ilrr rl.
t t lt t r
,1..:.l rrl i ti . si nl qr lr e. S- a sr 'm nal: ll. {Ll' asf ll! {'nc1, u lnot [ ili' it 't r ': t ' lit r t l't
t
lc
culio
t
t
'zot
t
:
ut
r lr r \ '
,,i o - . liii"r t n* aspeclului l: r 'tinqolui 1r 'r 'i
' ,i i i i ' i i ' i "
B )P aruti ziat t i. uselt 'iuluicot lslt t r : t or super ior alJar it t gt t ht 'i'ilol; r 'r 't t t in: r
,r,.r' ri J' c, i al .r t l, - " a i: r , r ing't ui ] r Lt lt liz&1, si'r ' 1'alior L sJnill. r r r 'r r f i l'r llir r
A. nn\ 1. ( lnllI il) |l, l. c|\ {. I I J: '{''. |||||{'iI Z'I
' r .' us (sci l i nl ] coI t jU, i l, i ] ui \ / c] 'r clJ) .
or t it elea hr in3' lr : i . r I lr lr : l ilr '1'
Ja
{onom
clor
.
'o"
sl]
ll
5i
rr, r,r,tounti a
, r a''
patoltttit,q NliRVlll',tll
2.10.PR0BL,EI|uDu IIIAGN0STICiN
PNI'UilOGAS1'RIC
0i,,,,,",;*,,1';;ii,;h,,1:ii',,;iiiiiiliiiilllli';Iill,iil'ilJ'lfffi;,yilliiilll,fl!,lfiii$flllli
t lil rbil,
;ltt.l
I I li'
tf
I ') .t ( | I I t i I t I I
lt
i,lr
l,r
j1
t,i t1l
lll
1ol 1r.l ,i i
l,lr r r r L tl
i j i tfl l t.l r,l ,l l l tl
,t ,
. t ' i tt4 tltti
tl )r,l l .; r i,
r r ll||r |lr |ilr u ri ,s l ri t,;ri { | t.rr,.r rr r,, l r.rrtl r ri ([o l ,l l s(,. l \,
1fu Jr| r,r,i zrr| r,:r
L rri rru i rr,rrrr.r, i : ,,,rti c i i r r.rl n o,\i urron l l ,r.i l gi rt,rri ,,.
iir
,: ']:l l l: ] : : i, l:lr: r ilr
] , r.ir
i' tr ,, )r rrr..l t(,)ti ' .i { 1 , ,r,rl .l r()i (l
i irol .i tert.i d, l 1ur,r,nuri 1i l .i r,r.r.i
;i
l i l ,:,1
'z
ir
,
r
i'
'i ,. | 'rr: r lr ( . : r i' , . , . r i g u ti tr..u l rrri l rrl ;r r,:r1 ,i ,i ;;1 l ] ti m!,uj r6rbi ri i ,
l ri r.r.rL.r.r.:r
|,'.,r,||I I, , |. . r t li. llr . . , , , n s fa l | l !rl u _ s e s i trrj l , rr.::r.i
de respi rrrti ,,. l ,;rr:rl i zj i l r. ,l r.
iIrirIIr(|L()|i pr.oduc modifici,t i accir.tlrte
Oe tona,tic'lpiirl, ln ldorrir,), r.rr
I rrir| | |r'rl r r(r lrln lralii. Palariziile dt'rbd.ctc'i
realizcazi,' r:r.ir{
cont},i1,,dise,,i.t{l
,,1:
i r i n s p i ra fi c .
).ll,,n1,1,,ryt f.trnc!-iei 'se*zitite sornatice ce.ceteazti
sensibilitat t,:r,
., .l|
', :| |.rr , r . lr r r , ( . t lL l r I m u (,o !.F ;u ,. a c | c s i L ri lo erpto:.l r.i . cl i ni ,.,,: z,,n;r
,,1,.,,::i
'',.1,""',lt',lil,..lii:l;l:|,':
l';",1;'l;ll'','
"...;;,,,'
;:"i,:1,:,;,,
ill,
jriroii1,r.i'uncuri
r,\ii(,r.n,
do
r,,iii,ii,.,i"i
sertltoliir.i
"n"i,
i 'rl|
1Ilrlr(\
,' 'r,
' ,,.'
.' | ' i\|.tt.t'1t|t1
itt,ll|'
ll|i,
1l, |lit lr , |l , i{ ; it r r r r r 0 r ,
r'l||:1, i-i(f
r.ii|'|'ltl'rl|'
r l0r
' iz|||,
r , ;t r' 'Zii
(lt ,iflltSt)
t , i] |
(tt rrl; rr1lr'r'lrrl;1rrr,rL rr l, lr ir , : r liz llr . iir . 1t
r . r , t lir t r r r . lr ' llr I ir r g i , , , i i il I r r o r i S r r r r r
,,,r i,,i|,|li,,l,(,fil,t,r!
t *' r, t 11, iir,/rl.. illrt.r,
lr , r . l i' r r . ir |) r , , l r r r r r lr i lli ir r l. r . r , i i i r r r , i il t"'i ; l i l r l r t r .
l ) r r 'r , r i h ^
,
r t trl, i I i r ' I I rr rir; r I r, rrL,r r r l, r . r r l. r lr . , lr r liliir
, , ir i, , r , 1' , 1 , , , , , , I i r , . I i , , , , l i r r r l r r , r . r l r ,
l lrl
1t'l
!,rr, 1,.[0lJt,ilMtt
t)tdl]ll(;N(]s1,t(i
lN t,A,tut,o(ilA
Nt,RVUt.,Ul
sPlNAt,
(A00liSl)ll;l'l,jlfl,ljllllA A XI-l)
't,;,,t.1,"j:"^T"lFl1inserniotogicina rrrrr,ttui
spi,ralimpti,.,i
impr
.j"_iiglgsr:r, nermruispirrat
icri:
I Jl'l;,1"\'::,::l^"*:,
I'i|amctlut clnuc
''|
nentmLrannna internd, i nurvrtrii-il)i,,at
est,t,
trt cu cel
practicat
practicat
cel
p&tru compolenta
p&tru
compolenta
motorie
motorie
;;""Jrir,iiilll"Sli
a nervului r)leumol;li:liil
I ilri(]. ""
ill
tro(x1$il,il,
ll'rrlro(rsl,outittlo urgolrt'it,.ltr etlzttt'ilo an dabltl lonl,-ptogrettt',
.rlrrrc strirkrr', dispnoe qi tlisfonii pinir, ltl a'fottit'. Iltllllcxttl (lo l;uso osl 0
, iiur irrurit suu chiar abolit.
D ) f'aralizia neraultti sphtal et'tern'so lllrt,llifcsLilprin ssnlno (lrll
grrrtr*' mr6ohiului sternocleldomastoidian ryi tlrpez do llcocil,lsipil,ll,o.
I'ara,lizia unilaterald, a muschiului, sternoaleidomastoidtal,so ruanilirulf[
irr primul rind prin qtergerea retiefului musculat a'tit in repaus, cit.qi lrt
"tirnpul miqcd,rilor de inclinare qi flectare a capului do parten lozitttrii.
l)e asemenea, muqchiul prezintii o hipotonie marcatl qi atunci clnd lx:l
llllvul intoarce capul de partea sinitoas5, qi examinatorul se oputut ,l,cottt(i
rrriqcd,ri.
Uaeori sd poatelvidenlia Di o ahofie de gtadc diforitc a' nrttqchirtii.,
lLri"Ilin cauza actriunii sternocteidomastoiclianului de partea.oprrsir,l"ozitrn
partea
Paralizia
unilntclrr,lii,
sinS,toasf,'
poate
fie'ugor
inclinat
ci,tre
si
oapul
lu,inuiciriului sternbcleidomastoiilian nu impieteazd, prea mltlt miqrrfililn
,,apului din ca.uza intelvenliei celorlalli mugchi ai gitului. In clzttl lt:rrtr'
liziei bilaterale, capul se afii, in u$o&r[ extensie, iar bolnavul oxtrcttl,tl,t:t.t
groutate flexia capului.
Parali.aia muqchiului trupez re,alizeaziaurmS,torul tnblou cliltir: : rr,)
rrrrrlrul rle partoa lezati estecoborit qi proiectat inainte I b) mugincir ir,trh'
Iiuaril a portiunii superioarea trapezului este qtearsd,; c) spD0iulsuJrrltohlvicrrlar.eite hdincit, iar r:laviculaapare mai bine reliofatd,$i paro proi{joltlliri
tllai te; tl) coborirea scapulei; e) cleviereain afarir,a marginii- spittrllo ir,
on,uplaiului; f) diticultatea efectud,riimiqcirii de abduclio 6i .tlo t'itlicl,r'r'
a briilulni; g) imposibilitatea de ridicare ,,in coa,te" dirl. pozil,irlllllllnl,;
h) rlificultatea efcctuirii miqci,rilor din articulalia nm:iruluil i) 1l,r't'gctlrt,
r:,lieiului qi hipotonia muqchiuln) trapez; i) a,trofia,tnu;ohittltti l,rrtlcz
llurulizia sittgulatd'a neraului spiual este raril. lJfl, :lllrtto rlo ttlrltrrri
i. rrlrrerLnd,
cu paralizia ultimilor nervi bulbui (in spccial ctt port'rltilo tt,
tn i n nli al,t
I X-a ii a X-a) (vezi in continuare), 'loluli, procesecaresegd'sesc
ttlrof)iere a foram,enu,Ltrimagnuln ;if sau' u, regiuttii, cetuicule $tt,lcriottrr
(lr)carcosteomielibice,pahimeningita specific5,qi nespocificft)pttt prtttlttco
Adesorl, oparul'iilo tn
lrrlalizii nnilaterzlle sa'it ltilaterale de nerv spinal,
itqiunea cerui,aaldlnaltd (ca, tle pildi', sec{iunea spinalului in tortiut'1i*)
silrt rosponsabiletle proclucereaparaliziilor nervultli sltittttl' Ane,tritmttl
rcrlebraLecalo se dezvolii) il canalul slritltll superior pott,e t:otttlrrimtl
^rterei
10(|6)'
norvtrl spinal qi poate si plovoace o paraliz,ietrrrilatoral.i'(ljor'loohl;ttl'
ii';"':i:l'';'?'i;ll*,i,,5x*TiffiJJ':i
iil:i::ilI
;;:lllili#;
li'iriii:i;l'1
:1.11.3.lraralizia nervului spinal
ir;,i,i*ii,:q-$*ll#":$|liii,:,yli::,*imiti;$::t{^*Ti*:
jni
,,iil,i*i+*!#_*ii#_',E,5,1,:*ri:;t'*r{jrft,:ffi
tij!:j:i'
rtrv;w::;v;r:;i
ir I lrl,or nii). C drcirLoltlul liroidi
!.i,il;:'Jt
;i:r
ii:,
trtr'",::*
"i,###,:fll{f
'ffi
*'f::'u1":*$,,i:il,#:::fi ):;*'J'1T:Ha
;i';li,:',\"Yf
"'#,fi
utrvului.""*"nt
i.iir,rr
rrcrroui\,
nri
-oi'co*ilJi'ir'rfiL),',"o!!,lJ1f?t1,fl.1
illl,l-llHl-""lHlglinn:Ysx$itni"';''i;;i";;;;ilifr:'J#il.i|#i:
i r.zr,ipsirarc*ri ;;;;i;-;.f.il-ii #, i;:i: ?:#,,Ir#; *:,Ttli
1
r. 'orur.rrl;pr[tluCe "
YoCestlirlet
*"
1i"""?,
iii,*l"ll;i,li:r".i,",1;,,f,1,J#lH":T;iil,f,H,,,:$it
lll,ll;iylii,-',l,,.
I'a.ralitia
bi.IateraLiide nt
ri:,iliii11fii,n,lilii!:y;;,*f
i"#t{{i,TEH"{,#l1,;b*nuiindeeir
,ri,',,,,ii,ii'"i,i,n,i"i:;;;';^;:;ii:,:'tr::^;i",iltfgT"fi
,:lyitd:'-l",Pml:
Ftg, 77a,
"Astr'{te lch,rnatice ale examenulu.d
lalrjngoscopic:
tr\,
@
I lj8
NDRVUI/UIHIPOOLOS
IN PATOIOGIA
9.12. PROBLI]MD
DF]DIAGNOSTIC
n norvrrlrrihipolllos(XtI) lmXrllod:
somiolofliolt
9.1L1. lnvostigutria
I ) ( )hsurva,t,irr
1,ozi1;ici
."i a nn;rootuluilimbii in sboretls rolf&ultrrln
gitutt.
I) Inrplorarso mol,illtillli Umbll, solloitlndu.ssbolnavdul rl1,oroouto
,routo mtgodrllo podblle on t Imbn.
'lr0
t
l, ' , l,l\'
ti|llr|r'll ir r |, li( . I I i|( || I r r r r lr r r . 1r . r r lI r r s t t | . l , r , i l l ( l ( . r t , l l l r l l 'l i i l r , t .
Hi| lr l)ilill0 titlr'.
OIrsllr"lr,{ilr ; r r . t ' z t ' r r l, r , ir lr , lt r < r t llr r lij
.//,/
r l| ! . )I I llI lt(,-
il i c . \ 'e n i u l l
rrrri.
, l r l l {}r . u l t i r . r r , l
| :t0
:.1;i.l,Itt)IJLEltuD|ll]IAGNUS,II0iN|,4'trtt,rlrit,tl,^li^1,IZll|,()|tMtl|,1.1|'|.|,:
AI.,ENIIRVIL0R 0ltANll'lNI lllll'ltAlil
crt itloctirri mllltii]lc tlc
3.i3.1. Atoeliuai extranelraxialo
0r:rnie i bulbari.
ttorvilor
:li
;i1'*:1i4i*?,'rf
ilTi'lli#,{l,",,;ir;#*ht,ilHiTffi
;iir1;'
uul'l
::::uiir'lr
{iif'.'i'l::'r;l
"-.iili,Hiitimixa
rl:;:";i,"q.;,,;,;r;#:;;l,l;*;*f
{li$ffi iti',illl*,il,,i;,lilll,,
#*:',lillfl**;i,l'll-"*4i!tiT"i$i$:ltil,*t^
l;":il:r
o1,T,,.",
'u,.'',,'
"i,,,r
illi:,:j;jtiti:tiJ11lJtfi1":ii'iii1H!!:HTi::,:,,:.,j
,
$Hil$jiti#fi'iffi
jli?'#ll;rmiril
iii*#;!,*{,*"i[i$1i
',1,*:ril"s:ru;;r!**ii
ffi';:l,t?;;);,H..**,ffi
.,.t
. i c 'i
" 1 i n 'r c,
:,"'w|*,::iil:!,;;i]t'.#ltlil".:,:1:1.i;,ttlla!::,i
:*$i'.ii;Hffi
*#{i":*l+
lr*.
tr*,'*iffi
;,iT$";',J'ff
$iJ,:f
:*ifjl!:::#;t"#;il:,i#{iln+u:r
:,i'i
{,"i|:;:#LTi{1*#'ffi
;l'i;u:
',1:'
::1:
;' ;:,'H
l;,,;
tll,:*#j*jy
r'
rll :l.nliTl"til,1"lr,'"",1';:',;tll,;,ll;j,_l;;
,,,,,,",,
l;l;ll;
'*'',l:";!E;,!,"ii;;,J,"i,,i","i,iiii;i;ril6l;i1li
il;,,;l,J;;
'-"#llii#;,d#l;i,
1ii1i{tl1i,'"*ff
itii:{:'
ffi.fl"*iihti
i,,il,l,,
;
tii,i"'.lit|),,T,','l,l,i:;":t::::i:,,,i
r"rr '' 1,,i,,.,l,rl,
i"i,rl,')','r
'',".,,i
,',:,'ij':.:1lij''
t'#;lil,;,,,Li,l,tl,;,,!,|'li,,l,i,i.)lii'ijili,;,,":,"1,,;",
lniti;i
nn#i;i:lfii
lirjj'i'i',{riilllii'
.;fy'f,i:i
,,,,,
Wiil
.,''
lllllllllI ;l;li;li,
'"' p,i/i,i'tr
ii;;:ll:iilll'l:
'l:l,,ljf
l':il.;l.lil,
'lliill1:'ii,';:irllli'l:"
llllllllllllll,,lll;,li,llllllllll'
ltlil,,:l'';l:,,;11,,'1,
I , , , : i I 1 , 1 , , ', t , i t,g ,ttIr tIt.ttIi Ii ''
r i r r l r r l tr l r l r ')
:l)
r . r t r , lr r , r r lr r r r lc J ( . z j t l t i
llljl,
illo
l,jlr rt,il
s ilr lr , olr ll
lur , \ \ ( llis s oils o c i l t z i o l t l r i r l i z i o
tt:iil;Llr,
l :l . l il llr ,{.trrt,rt ,lr,t U( , lr : jr l, , t : ls lr , i( lt : l i r r lp e z .
tl 0Or;attti :r :r ..Jrti.
t,,,r,' ,:.,.' ,:,.t.,;.-.1-,.t,tli: it t , r c op. t t ut lt t i, , 11i, , , t , , : '
l, iit u , r ; i
, t ; o ) 'a g ; r : i c i r , i . , , , : r ; :
,
,I rir : l||Il r,mUl nlonellc LL.
I ) f iudrtntttl l.ii,Iackson
produs cie obieei cle o icziunc r-rqirrrlrorrrrlrriillcr,ior, (llcrifolrn) al-este
vagului $i a nervului JripogJos(Llotri:r:si
,',Lrlr., ll)(il); Pr.rpoviciusi Fascu, iOSfy. in, simptcrniatotSgia
sindrornrJui
I r, r',rl.rrr,rrrrui scr,nitlt'seadaugS
,i p"*iiri"-d-ii-rrfil,-ii'actorii
it;utoiril
t2\
ri ttrl Irttto r1i tr: r lt t l r ii lr lx) lllr , r r l r Ir'rI i ' r trI ri t t I ' i ;i | | !i I i()I I I I I I I i 1, 1r ilir I r r r ( l I 'll, l,
l 1).1| i ; l i i sl t, 1l) iiLl; llr por icit t r . t l': t , ; r r t t . , lt ) ijl) [ i s{' r r r r r llt r llt izt 'r t zii1t t 'it t
si i tit ot ilt I tr,I rt i I i t rrI rri , pr nt ) izic il) $ilr li; ( f r it liiil, ( r r lt '7ii vit . illr t ( ( 'll
l rtt' rl l i ,,,i rt,
i l rl ri ,rrri t, vi i l ul u i palz[ t ului qi r r I r r I ir r gcllt i) li ( , \ - cr ] t . uilll) i'ir l l] r r lr r ljzi( 'r r s( , ( r i: r lr l
I rtttt;chi l or st er nocloit lolir ir s r it lian si t r ; lpt : 2. Ut t oor i I u1 li r r lil, llt , {i r t
itcrvii simpatici celvicali, o1t sindrom Cltrtdc liol'nrlr(l lkrl'tti't (liory I I,t
rol al t., 1.969).
tr' actoti i et icloyli. crsint
i : : '. ) I r aum alici, in speci: t 'l, Ll r Lir r , lr t l qil, t t lr t r ;
h) Fat:tori, ttt.tno"ralipi c,tinpresi,ti (turnori ale glaridttor ptLlrrlitlr', 1f i'ilrrtlozr',
lrctastaze l,:.,cele,adencpatii, llmfosarcorrno s.a.) ; c) l:'utlori iilllrtutrrl0tr
(par{}ii(lite) :iircese, celirlite q.a.).
3) ,\i xtl rr; m r l, de hem ibazt i ( sit t dNt nLul [ t t i G alr : in, sit ulnt nt ul lr r i( it r t ]
'Lain
;i {ioci.n sau sindromul lui Bertololti'G arain ).
'1'ablott'l'semiolagic este constitutt tlin po'ral,illi l:rt11i;rlr: tlt' trlt i I
{'ra}iicni, in {olmele lipicc qi completc fiintl aiccl,:rte tttrtttr c|li' Il1 l'r'r'' r'lrt
tLc nenri cr:lnleni <le o p:trte, da.t cu clemsili-c s(xnioloiliot) ll.o tLrirrtl, I rr|i:r
1;i l e, i n funcl i c cle sediLr tinil;
ial el leziunii. il f olt nt 'lo int 'ot r t lt lt 'lr rr lt 'r t t r
r
rlrotn t1o iii:nihazri. tttlii ncrvi cr:iiricni 'q1ni,cruli:i1,i (f1'{'ill rrrrlil.rtit'rt l. r
inti ftecyentil), i:lr nltlrior afect*rorl l]ervilol ci'lnicl]i sc {rtrro lil'tlitt rrlr'
rintcro-postfl';or, fie riin srns }ostoio-alltotjoi', oll plirxlet'i'rl iirilirll,i lir' '
rrcrviit)l; c1':1ni{,nirlin fosa oerebralai mijlocic, fie I ultilttlol
ijlllrl(l lrltl, lrl
(1r r:ri ' Ti crarL ioni ( I Jlom or r t i si cr ) 1: t b. ,195i, cit a1 ide. I logcr f ii i'olr r J, . ,llll; 1r r '
iri lite situt,irii, ito llot :lio!:ita li unul sa'.1lillri:illilllli n(llvi rtitlli{flIi {i,' i)irllr ir,
;,ontloittterali, (Arsol]i 1i col:r.b." 19?3; Iloiler iri c(trlJ-), 11){i1i)
Gr;lcirt tL'-t srr sl)rrr,rl('rr'
liultir ;remc, itr tvolttfiil sildrotttt'lol
romni: dc ltitcltonsiun{r intracrtlltiat}li , cero iw|1rc ndosea1,xl'(!iv'{ r, \IItrl,r]'
tllncit) 1r'rtl rltr lt.rrtr
r'{lcruihri pi1:iht', r::u'o aIliie m:i t.lci;rtrnc. ll s i11{1ro
i"lr::rirm sc ilcrrla'azii, llelltle tls ltziiute lt, triittlrilot' senzitri|rr sr'rrzrrIiirl{ r
rr rotorii iltr':riier-r"ilxialr.
i'u:lo: ti et,olttgtt-:itti s iiztltoa ,tictor Cor{:i.11de h(ntib,L.ii.
::.) ' 1' t.mor ile: t t r t nor i oll] 'N sil {lt }z\ - o1t alir r ir r sii; i lr , lzr i , 't r it t it r lt t l I
r i inai , j{r ss; lLlr ll{'^t lr , r t lr iI r 'i lir r , '
Lri )Irorici i l l l rI ] ct di] gr lccl|i't lin: iil'llct
vol b:l de tum oli linola, r it r giclr : clt o it l lt lo: t zf i, bll: r ll t r lr lt r it t lt ii. ( lr 'lc t r r : r L
l l tccventc $i i rb t r r lt lof il0 a, t t r ic: ulllt ', lli'lzit lc.r illLlr : r l( rsi r t lt ' lr t t it r lr 'lr r i ( ir t r l' "
t r r ',r t t ir o: rt r r ''
.r,bi cpi l cl i o:rmc alc : j1) af jiloi'bazalo poslt 'r ior t lc it i r llc r iilLt ut t ilt
i i ml l sartl rl l trl o : llo l inolar ingt llli, llit r '( i ir t vllil( r lLzi'ot r lit it t l lt t ilr r liv. t r l'
:ofrrfl l l ne), 1r s cut it 1i t um or ile 1; tit nililt : lllir t t lsclot lllL, zci; i lt lr ' l I I I I iI iI : , t 'Ir r
{ l i l rrosarcoatlc, sllcoim c qi osl, cosllco: t t t xr) ' }I r lir ilr csint Llilt t oliit r lt t t t r t l' '
lni Iitr.\taclri(), ir,lr:}nlalului s:t,l alo glandclol sllivltlt, ({lrtr;1'rriilttrr
;i rrolrrl, ,
1l )l i 5; ,\r' sttr i ; i r lollt 'b. l9?4) , llli"r t Lr r l ; i t t t r r t ot ilt t r r it r I lt slilt 'itI ' r r kr lr r r zr '
rl l l tri l ri , r,i t lt it ui. l r lir lllr : r , alc r lit r ciu ( r it t t xtt no llliil) ) llli' sllt l 1t t tI rt t t I rtit t r' .
i i i tr ti tl l l rrotr,t coil'illo, I , i'( '( r t t lt tli. r lin lr lt o l, Lt t t xlr i lll0llllolllllt t t t t t t lt t t ', : r lr r
rl )i r,Ii l l ,ul ttil 5tr ir id r , i r t igest iv ( , \ l; cni 1i cohlb. , l1) 74; jir - r gcr '1it , olr r lt . , lllt ; lt ;
;{i r,)i n1i [.rrrtt lnir 'r ',ll] 51 ; {llalll ; ii r olr lb. ' 10{iL) .
\1l ;s l rtn t gt i lllt c llt t l, t lt t l, ct 't r t it t t tsir t t lt t lillt t t l t 1o lt t r r t t ilt llzlt : lllt t t t 't 'l
,1' 1,i rl ittl
' r ri rl t' , t r t t 't Lit t git t lt t t t r , ,t ' t I t r I t III 't t ttI ill{r .j ()r I{1l,i II I I j i slir t lt I ot 'lr ipil'lr lr ',
r rrrrrIIoIl l rrr.l r r zr r lr , , i, t t t r t ot i t llot t t it r t , , lr llt slt t r xr ilo: t t t t lr ,t t t ii'I oI I r r r I 't t t t lllilr lr ',
lt or lt ll. ir r {. ir . ( liog( 'l 1i cr r lr t lr ', llllill; \ r r il'! r l I
' Il Ir,r' rrri trr' i ,rit'ir lr , r : r l: t lr r i
, ol ,rl r., l l l i j i
ll) i 1) .
l t)'l 'ttul
1t!l i :1t tl .
l rr:ti ri \!
t:t;r
, 11)u'lt
rylrrlittrri t 'rr: :t t t .| , rt r : lt r nt t r lt , t nu l lr . lr i rx r l i ( I I I I I i r| | | I i ( ( I t r i I I ; r r r r u . ,
l l l ,' 1, , r' llll rlI Ii,og r't ;i r . olr r lr . , llt i; ir l; . r r . t t ir t ur ' i t t f . t " r t r ,t t: r 'r t n t \ t t ( , 1 ( 4 i l t t 't , i
, ' . t tlitlt illt t n t (l(is''r'. 1lJ 5: l; . \ t . f ir ' li , r lr r ilb. r 11. ) 7 , 1 ) ,
rlt (lixlitt tro :rlt tinliLjplr , ( , r L lo( . lliz lt ( , baz ali l , \ r s c l r i s j f ( t l l i ) . , l 1 , i , l ;
lj,,,r
| {,rl
l).. t||ri9 . / .
ct
r rirr,
rr
t . rlI l i l l { ' -
t[{'cttunl
inlranelraxialtr
cu loziu}i
lr}ultiF}c dc nerri
eratrirni.
l l o t ttr r t, ttr i ' i :i ( r l l l t) ( r l ( f l |zi tttto l t ttttt'l l ,ttl tti l tttl l r i l l tttt'
r r l r t ;r r , tr tt l i r r r l to ttt r t'r i i l r tL l r tt l i ) l l l l r r i || I ( 'III||i II
l ,l r r tr ;i l tr
r
l
r t t t t l l l ttt l l ;r l r tttr I'i N r r "r 'r 'l l '' ( 'fl i r " l l l ;r ( 'r 'r 'l l
i
i
r
r
r
l
r
r ,l t
T
rl t' l l z i l l tr(' i l , l l ,l ' l ,(tt' ('l iitst' l ,r' iIl ttt' ttl l l r l r, l l ttl { i l 1 r'r, tr I ( |r I ( r I I r ii,( , it l l ,i i ,v i t,rl rt,l rl .r
irrrl rri , rir r , r '. t t 1l' t r t k rttti trrr' tr1rirri ttti ,Irrrl -i i ' Iii ,u l Jcl nl l (fl ol ' (l o.$fl l ori tl l i i l l rl Li
lrr,i r.* i l ii,r r , lr r r ilr r ilr r i (tri g r,rrrri rtrrlIi rl rri rri r (l c o b i cui i udoml l l ] vl l go-i i pi nl l l tl l
r.:rl o Io l lI l, o l) u1; in& 1 ,i n s ; c o r' D ttlt,l i rl o trrL s i n l Lcl ei i vesti bul l ,ri si nt l :o{l ,r1]{\
rrrir.r'r,srr,l,i,
r[c irndc rezdltii rin ;rt:t,tr';.ittdt om vestihulo-cclebelos, ctl m&r(!
l czi utri i l
m i a trn i o !i l &l c ro pul ni c de l artca
r
r
r
r r r i- i, s inorg
, chhctPl
r,.r I.i i .
" B oidc e
,
l 9 6 i ) ; (e ; l i n droamol e bul bare nucl c:t' tt'
r L i rz!)rI lr ( , i, ll) 07 ;
iz,,llrk' (Avcllis, Schinidt si Jackson), care in mod exceptional lezrlltir'
},iind pe prirn
o"itnlirau ; (r) sin{l,roame
1960);
rl., scncibililal" (SaradiiSvili' i SIr,!- ,\t-cvclidze.
r'l:r,rrI.rrlbrrr':rri
lrr lr,.rrri:r,rr,,.lr.zi(.alLerni
pc fali Ii pc hornicolpul opus;
l'rmo rlgnzi('ir,
r.rr lrlrrriri,ttt'slczic termo-:]lgezlca! contrulaieral:i, ; cu tulburriri dc sensibilgczicS,hilatel'ale pc faJi, iar pe cxti'cmititi doar tle pa'rtctt'
lrirr,lr { r'r'tmr-it
,,trrrrii'lozitrniii 1g1Sinoro:r,me\Tallenberg ii,ri, tull:urili^ dil pa'rtea cor'(I1liJu, 196i, ciir-r,tcle Popoviiiu qi Pascu, 19$0); (h) Cazut'i
,.rkrl r,,rr,rt,lc
, rr Irrll,itlllriilt' s, nsibilitrr,t,bilarerah llc foir'i,pre"uul 'i ''aztiri cu tulbllr':ui sr,trzil,il'cbilate-ra1c,dar lucitlizate tloar perioral, inciusiv pe 1imb5, ctt
:r.:rrlz ir.tSr lr,lt ii cul{r,b.'i9G;,.
'
cu interesa'refi
de sindrom lTattenbtt'gmai' entiinser.
t,,,riit srnttolc,ltice
qi suferintrl
gi
ast
ciazS,.
(l${'l})
care.
1965),
19i?; Scholjt cohb.,
t),rrlirri,
i,rr,l,.ilor''r'r'llnicniVI li VII $i chiar alectarea fasciculuiui piramidal (clt
1r'rrilrr,rozi'1,
controlal,cr:t'lii), sau forme in care coexisti' qi trulburdri vasor,r,rl,oi
ii (ctr orractci' :tltein) fi llgii hcmif:lciale'-&sociate-tneori cu algii
lr,,rrrir,rrr';rrl'it1c
corti,ralatrale(lsch, 19;7). S-t relat-atsinlrcm'tt'lsub-bulbal
,l t t i ();alrlii (crLllpocstezie faciaii, siadrom cerebolosqi ClaudeBernard --palte, hemi:lnestezio clisociati qi eveltuaL hemipa-rezri
ll.r'rr.rl rl. rr,r,r:r:a'i
dar ldri atingerea ncrrilor , I-XI)'
r
r
rr
r
i
r
ir
I
iii
rtlrtrrilaieralS,,
lchol'lt
1 lrr
.i r',rlrr,lr.(l1ili5) qi l?0poriiciu 1i colab. (1980) au -rclatat,. qi sindroamr!
{le paralizia perechilt-rt'
irrslilil;c si de sintL'om Pa,rinatd' 52111
\\ rr'llr.rrlx,rlu
supe'rioar(')
)iittts{r.i, Icl'in l"zi:Lne;iaarl.rci |crcl'ol.Jtl'{c
Ill r .rr,'il\
rizualc de rip uc'"ipita).crt hAm!anopsir',
s,',i ,i,..,,,i.,.-iirlllrrrtrrriasocjr'1e
r .r'ilrlr coli irLlii satLalcxic (Ilcyer si col*b., 1956; tr'irchor-$icolab'' 1961)'
hemibulbttlu'i
li ) flitrl.roirtu,LLui lJabinstii_Jageoltc sau' sindnmll
'rut,t,,,t. \iu,lr,t,,ul clqsi" ,l I'L; B';hinRt:i-\-ageattc sr 'aract el i zeazit,.lli,'f,',,i' ruir, tt"rniftnr.'r:is",ll bcmiplegic nohtralatctali' plin ll('llri
'rrr...l,.zrr'
p,' benricoti:ulronlralale[a1\sipe.llelrulafa ]l)nl'
Icl r,r,r-iulg"zicli
somlrir
(ipsilaterx]c),
lllteropu-lsie
Lhr,rrl,r, IrIi|I tlisrncltir',Il,sjnergie.
-prl'n
ocglurllrt'
de
l'elopalaLuft.
(,r'j
plin Lerrriparllizie
t'lt'il:u'' ti ulr(
.tulbur';rr
iphll*1''Iali,o corzlr vocalc'
.r rl. r,tt Iritc ii Jlriu l':lliLlizil-l,
7 | sittrlrotntr'l lui C estan- Chenatls este asemd'n5'tor cu sindrorlltll
t,', ti,,r,it,*i.i N,ignnrt,', irr labloul clinic asociind totdPauna (pe ,lin'{itr
,'i,,rrr,.rrilkrr,cestui sindrom) qi semne datorite tnei - leziuni * nuc.toullll
r rt|l)i*I , l0rlpoctrY cu o par:]i;ie. ipsilatera15,a I'[]ului palatului \i 8' corzii
ltt'i Dei'tart se caractelizeazil' prin crizo vcrlri'
,\ ) Uirul,totnt+I,lLutJleLtIL[i
nislt'[inrus orizottl*[
r,ii"r"'iri,i
*ii
si",,'i"1..
1,t,'',ir,i"nitlc 1arl,c:rlcziunii),
braiTelor sPro
plin
devielea
i,iii',ii'i',5i ",'iti?,tlt $i/iau rotatjor)' liur:um 5i
lt t l, (' ll
l(fzlllllll.
l e Potttitrc
l\) il in tht ru nt,tt
lizt,ilzri,, solrriologic, o lxurtlizltt
I ) fiitxlrtn ,ttl ht,; "ill.it.t(t)d,-(il.bld.r.r'rr
(10 l )n' l ' czi l l' l {l l l pl !l ' l !l l zl l r
rrl i rr,Ir i, ' I r ir t if lt ilii,ilrs i L u l r' r' rl l i ,i n s o { ' i l ,i i ' ,rk r o l l i cci ,
l !(l
, \r'rrl l l r , r ilaI i/ , r ir r r r r l r l l r/rr' l rr.l rrrrr,rl rl rrr' n l i u l t{ r, si utl nntu.l \l thtt' l)t t)t
trnrlitntlttl
itr. lt'11tnrttlu.lI )| tI | | |t t ' t| | t t t . r'tt prttlllizit: 1,o1;itliiit l)cr(r(:hii lIr ,
rl rrl l l rl i i r lr , lic il nr { r i, o li l l rrtc trrIrl r' Io r' IIi ' l ,i rftrtior p l rs?i .
l{)(iliI
rolnnii Ii/sr,u rrrrrlisrro1rl(irrot,ico
(Aqgin,tr
,,siVrriu,,11)l-rl3;
l.)01xrvioiu,
l'rtyrviciu f i -^Dgiil,r, 19ii8; Aflgilur li cola,b., 1975 I l'opovi0itt i1i
coltlt., 1980).
II) Afecliun,ile inJec,lioases'i imunoalergice d,etntnah,i cercbral (polfur\tcirfitlitels de tip inferior sau superior, rombcncefalitele, sclorozr rnull,iyrli"l,qi afecliunile demielinizante inmdito) produc variate tablouri srrniologice, cu configuraiii variabile, complexe, de lcziune a norvilol orlrriolri,
rle cele mai mult ori nesistcmatizate.
III) Bolikt eredoilegeneratinte
.:i d,egenerativeimplioS, do ascnrcll{ll,
k'ziuni ale nen'ilor cra,nieni.
A) S-a conturat incleosebi entitatea clinici denumitS, paral,izie lt .
lr.r,rd,
Ttrogresirti (P. B. P) a adultului, care realweazd,r'tn contexi Bemiologio
crr:ifectarea ilegernerativi, a neuronilor motori din trunchiul cerobl'l|,l, lrl
|Jpecialai ultilnii{)r neryi emnieni (do Ia perechea a Y-a la perechea a XfI-rr,).
.,\celsii, P.B.I' I'eprezintd, doar un $inahom in cadrul unor variato lxrli
r)curologice. In tonrte raro cazuri, P.B.P apare in mod singular, oil oonsfituind cle cele rnai multe ori o modalitate cle debut a acestei sufcrinlo
rroulologice. ln cadrul P.B.P: unii autori inclual qi aspectele serniologioo
din scleroza lateral5. amiotroficd, (Norris gi Kurland, 1969).
Contexl settrioluoie
Cele mai multc ;azuri tlebuteazd, cu tulbuldri de vorbirc (clificu ll')l,t,i
de fohalie, in special cu rinolalie), Apoi se asociazS,dificultd,l,i in doglui,i{ia lichiclelor lsi a solidelor, atrofii faciomasticatorii, faseiculalii po linrbil,
;i pe muqchii rnaseteri qi tulburi,ri ile masticalie. Iieflexul faringin,n rlisp:lr'e la multe cazuri in plimele faze ale bolii (Bonduelle, 1965 ; (iirho
qi Kovarik, 1970). In alte cazuri, imediat clupi elebut, s-au inst;aluh 1,ul
buriri de respiratie, uneori gr&yo (Black gi llyatt, 19?1 ; Castaigrx) {i
colab., 1971). Completa paralizie a mu$culaturii masticaliei duce la dl,rlorr rrr,
rnandibulei, iar afectarea orbiculaluldi buzelor pelmito scurgereasalivei rlirr
gura intredeschisai,'Asocierea aproape constant5, a tulburlrilor dc doglutilie duee la acumularea salivei, alind impresia unei hipersalivalii.
Palatul noale devine imobil qi aton, pemitincl regurgitarea fluirlokrr:
pe nas. TulburXrile de deglutilie sint frecvente, ceeace face necesartrirrl,rorlucerea unei sonde nazogastrice. Bolul alimentar sau lichiilele Du pot fi
l'c!,inute de citre buze, iar gura nu poate fi suficient de bine inchisX,. ltolrravul este, de asemenea,in imposibilitatea de a impinge cu limba alinlontcle in fariDge, motiv pentru care t^z^ reflcxS, a rleglutiliei nu poato {i
rleclanFatd. Bolaavii se ineaci uqor cu alimentele.
I)iza,rtria este frecyenti, $i evolueazi, rapid pinii lzu anar[rie. Ao|ul
soapir,prin nas in timpul fonaliei, iar corziie vocalo sint in pozilie &nol'rnali,. Dificultii,!,ile iniliale in vorbire sint proclusede hipomobilitatoa limbii,
Ll ca,r'ese atiaugii, paralizia pa,latului moalo. Bolnavii n[ pot pro]rur|,lr,
rolect lingualelc, tirnblul vocii captrt5,o tona,litatc nazalX t;i dispa,rornorhth,tiu, vocii. l,ipsrr,clo inchiiloro contpletl zr,glolci, palalizia, mrrsorrlai,rr
rii
t'iit'iLralo tosl)irr11,io
buzclor', cit;i i,ulbLr
cornplotanzii tftbloul serrriuloilio
rr,ltulbrrrtrrilot'tlo vot'lritr:in I.r,l!.11.
Atrofiilo ttluscrrlrrlotirrl' plozrrnto rJi vizibitc. lrirrrb;r,osl,o Iltrsorl,,
rlin prirnolo[rr,zo
irrrobilil,
irrcrl,
lrlo lrolii, $irrtrnrrrrrltr
ryill,rof icit,.llo irrrrrrrrrrrrrr,
tn:t,url,r,,ti,
lrlclil'ot t'r,lirrl'r
rrlrolilt,tttrtryoltilrtt
Ll oxrlrttotrttl
sl,rr,l.io
4i lu *l,rlngo-
l :l tl
l: ! t )
|
11
T
l ,rt rl i tt f ilor ' , r . s il r lc rrrrrl i c o ri r,l l l r . f.l l o l rro rrl ci tl orl l rsl oi rl j l l l rrl ;i l ,r' l rl l rrzrrl
l ;r.rtl l o lilz li, t t t ir iiir z i rr i rr r,rrr' ' rrrlr.trrl l { i c i l ro l ii . [.]rrtroti l ]al l tl i zi i l , qi l l 1,roIi rr,
:tcr,sl , ot ' t t r r r f c lr ilr u p o n rL i l l ro l rl rv i l o l s i ;i l i rli co cl rpul tl tci t cu aj ul ,ol l l l
rrriirrilor'..llrrscit-rulirliilcrrpa,t
prr Iirrrbi, }r tulseteri $i urr0or.iii pe musculatu| rI
llu I l ( 1 1 t .
iladrc nozologiee
1) Paralizia bu,lbard,progresiril crotui.cdla adolescenli qi la adul{i
;xrirl,orp[rea fie ca,Jorntd sptoratlicdrlie ca Jormd,eredo-familiald. (Colmant,
ll)?it ; Malkland qi DaIy, 1972). Diagnosticul cle P.B.l' puld poate f i
st.rrlrilil;numai pdn examenul anatomopatologic, care va erolude leziunil{,
pilir,rnidale, P.B.P apflrut5, in ailolescenld,a {ost consider.ttii ite Marklanr I
li I ralv (19?2) ca o form5, particuiar5, a bolii Kugelberg-Welander.
:!) Grw)ul sclermelor lateral.e amiotrofiod (S.I'.A.) cuprindo 3 tipuri
lrt itrrripalo,in ca.rcP.B.P apale fie la debut, fie in cursul eyolutioi (Hirano
ri rurlub.,1967; Brotly f i cota;b.,1971).
.r,\ !l'i1tul sporudic al B.L,A. cuprinale cortextul clinic de P.IJ.P in cel
o/odin cazuri (Nishigaki, 1970 L972; }Iiiller-Jensen Be1'nhardt,
1ru{,irrlii
;
Fi
ll)7;t). I,'r(.{,vrr1,a
P.B.P in eadrul acstor forrne sporadice de S.L.A. es1;o
rrrri rrrarrrla biirbatj decit la lemei (Girke qi Kovarik, 1970; Rai qi Jolly,
l1)?1; .Nishigakir1972). S-a raportat o creqterein ultimii ani a, frecvn1ei
irnnoi bulbare fa!d, de forma spinal-d,a S.L.A., indeosebi in jurul qi pestc
vhslolc rlc 50 ile ani (Dazzi gi colal:. 1969; Campbell, 1965; Sahar lllrr t r , 19 69 ).
lr) f ipul ,rd,eGuamt' reprezint;, o asociere intro S.I-,.A,, parkinsorrisrrr1i rlcrncnfi,. Tipul ,,de Guam"'prezinti mai frecvent sernne bulbaro
11iriyrrrsl
irrilirle<lrcit forna sporadicfide S.L.A. Tipul ,,de Guamrt are o evohr(irr rrrri k'n1t1decit celela]teformc (Ilirano qi colab., 196?).
l,'ol'rn(r
dt) S.L.A. asemdn[toarecu cele ,,de.Guam"seintilnesc, se pare,
r1iirr l,)rrropl.Nu s-a putut insi preciza nici un factor ereditar, nici subIr':rIrrl irrfcclios plintr-un virus lent (Gibbs qi Gajctusek,1972), deqi so
prrrrrcii uilt, multe ozuli cu sindromde S.L,.A.realmentevirotice (Popoviciu
:r I'rrrr:u, 1.980).
It,rlalil tliltre complexul parkinsotrism-demenli, si S.fl.A. s-a velilitrrl lrr l5-2io,( din cazuri (Brady ;i eo1ab.,1971), f:r,pl.ronfirmat 5i do
:rllii ((lrrlrl;r;si col a,b.,1966; Bonduellc si mlalr., 196E; llla,it 6i cohb.,
lt?lt).
c,) 'l'iytrl tril,ilar tle iS.7,...|
., r.lesttl rlrr lar', plczirrlii u l rarrsrnisjrrrro
:r,ulosorrllldourinlmtl, ia,r scrnnolebulbalo sint tnai frecvenl,()((1as1;lr,igrrrr
ri colirlr.,l1)70I .llilrr,tro;i r:oltrb.,J067; Ilrrglrtrs[i Jol]r]m{!,11170).
il) I\tuli: itr, hnllttrni,lttolyninti, tlitt, uytr,-tisrkt ,,t |.nt,l.i
i rttu.xr,ttlurt
l: l{ l
.d
l:tl
a per:eohilol
IX, T, XI qtXtI gi rii1,
Si
ilcrimind,rntnsu;i
]:fllpTlglo
lr:tlrl uorros 4riforico
(rospctiy
lniduva cor-vioaH qi bulbul), ocle tloud, cauzo mdi
I|('ovonro Illnd Bclerozalaterah a,miotrofici (inclusiv sindroamele de SIA)
qi niringobulbia. In. aceste-situalii se nai impune G*; sd; fa,cd,un aUgl
p-iimetor segrnenrccewicale-9i
j:i':lig $il.or9r1ial gi fald de com-prosiunile
{uo.r)ulDurur,cal.eartrg-neaz6adeseatulburxri paretjee Ei atrofiee Elos<iruur)gol|,rlngee(boala I:9tt inalta, .tumori ale giurii oceipitale, iumori
llrl ltmedu laro tnalte, glioze mie)o-bulbare,pachimeningiti hip'ertrofied
cetljcalcinalte E.a.).
, -, t') lnyJqlo1ati.a.lui-fVprnickr,afecliuredesrulde l,ar.i,cauzald"de o
tloliciant[,_
de thiamina,(de obicei ]a alcoolicii eronici), asociazA,
o oftalfii{i.
I
otalS
o
ala.:i
ic
si
progrcsi.r.d
demenfi,
(Vicl,or
qi colab.,
),
.(ldeyai
JI,.lr:qio
071; Iilank
gi colab.,1975).
O.
PNOBLEME
DE DIAGNOSTIC
IwpaRauzu
3,1 EXPLORAREA
SEMIOLOGICA
A DEFICITNLOR
MOTONII
'tJ
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rl
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T
!) J.'uxt,1tl,r'uitt
lritlittri lroitlrrli plrrtlttsiipt'irrstlltti.tt{rrvIti'rtIttIittt'(ot'Itt
llt'olol
rtL' sislltttttlttivtrtttlrlrl-ltltzilitt),
zir at'iololorplllattttttlillttc
i)tr)(1('s(r
lr' ;. rt.
mativo care comprimL pittirit'ttlporttin, boli tlernit,linizrtn
' 3l Purapleeia paraunl'rald este reznlt.r,l,ullc'ziutiilot' I ti I It'I Irt It Ir' :'ll
lobuftui paiacintrdl (meningioameparasagita'le,tromlrolkrhilri tlt' sittrtr
lonEituclinal, sindroame bilaterale ale suferinlii a altelelot (j('l!fl)I'iIl(| itI| | ('r'i
oar'6etc.). Este important de relinut faptul cd' dcficitul trtolrtt' lrtrt lr' l'i
precetlat sau inso-tit de crize jaksonielle loca izate Ia nrt'rrtlt('l| ittiirtiorltr',
de tulburf,,ri sfincteriene.
'lrecum $i
4l Parapteqto-prin leatuni nt'ultiple.In atelo- $i al'ttli{)s('li'r!tzrrtxrt('brali,,'multiflel"e hlune de clezintegrare ischemicS,pot a,fecta,t'tt ltrtrciirltrtrr
fibrele corticoslinale ale membrelor inferioare la nivelul cmisli'rrrltl cllrr
brale (centrii dvaii, capsuia interrri,) sau in trunchiul. ccrobtrl, Irrlt'lizlttrl
t istt ttr
paraplegii sau tetraplegii (cu predominenll pl raplegiei). Pfi n t ttrrtrrt'r
iimil-arJse realizeazfi p:r,raplegi1leprin ]eziuni multiple din sclororll llr plii('i'
din unele encefalo-mielite, din boala lui Little q. a.
lin sindnnnr lo
3.3.1.3.Problemed,ediagnostictopogralicSi eliop&Iogenia
paraplegice,
In diagnosticlt'l sind,romuhti parapleg'ic este necesar sL so I),rtrrrrlgr'i
in mod logic $i succesiYurlf,5.toareleetape (Riser' 1952 ; -$ollcirrrr ll){i?;
'
Bodechtel;1965) : a) diagnosticul tlifercn.tialintre o paraplegi(' rii {r.,11rr1,'rl
doparaplegie"; b) diagnosticul de tip al paraplegiei (piramidalil ; tlrr ttltt
ron motoi peiiferic; pedcadon:lla' poliradiculoncvriticd, . polittrrv.t'ili|l ;
rnusculilri) ;-c) tliagnoslicul dc nivel irr crzul paraplegiei pillrttirlrrlrr (rpi
rtald qi topografia acesteia; cerebralal); d) tliagnosticul etiopttl rtgclt it"
Yor fi eliminato in plima et:tpii it tlirrgttoslilrt
1l Pseu,il.oparaplegiile
lui :
r | | i r Z r) . : tl ) a Z ta .
l,rrl
+r'rrziiir(scrrrlrr'lr.
r':rrlir,rr
r.,ilr 1rloIorrr.rrlrrrrrrIrri
i, lr,rtllrrrrluitrtill,otlgrr,lilirr.ic
I r r t t l r , r 'i | , i c r r ) l tti n ttr l tz{
Ir r {fr r l l
l l l t'
t 31l
t: l
A
c) l\l itrrl,irtt.[ntt
t t,tiltlr l' rl tr.rrlrrrrttri(irrllritrrplcgii,lrl)oi ilr r'\{'llll'i(rt
lol,r'r
t lr\rzrlrlir rtrol,otii,ttrllico 1i vt,iJrrl,itlivtt,
r,Ilrrgiir(1ll rrit,r'i LttIIrrrtrr,t
rrrlr,lrnr
rrr cvoltLtica,st:otttlrrnlri
lji r,trrrlr.riir,r'cli1i
iInclvil()r'clltlli('i.iJ{)llLll(t1f
,lrr lrrzirrnotrcylaxiu,Li (irrrltrosolri
pilarnidale) Iipscsc..\Ioclilii iirilo
irr,rrrrLclc
rrr 1,.(l.li. sirrl, cl,r'actcrisi,ico.
tl) l'olk nieli,ta,&cut{i e ltri. II ei.ne-Metlin intli, totdeauna in cliscu{io
lrr rtlr copil s:l,rtIa nn indilid ti[5r, mai ales dacai,s-an conse]l]11:r,t
sclnno,
1rllrrrorri1,olii infec{ioase (febr5, manifest5,ri digesljiye $i/sau respiratot'ii
'rll,clrrrlrr,str:i,r'iigoneralc), algii poriferice, ce{alee,ytlsi,turi, radiculalgii,
.rlgii rrrrcl,h:, fa lialgii, semne meningeale (subiective gi/sau obiective).
| 'rrlrrlrlr{iir, loate ti dintr-odati' masivd,, hipoton:i (,,paraliz izr,de dimileairr') rlcsclisi de West), cu reflexe abolite, sau sepoate instala doar o monolrl,'{ic, cventual paralizii parcelare. De ^obiceifenomenele generale qi meninu( rl(i l)r'ecod partrliziile cu 3-5 zile. In unele situalii, pierdelea blutali,,
rllrrrrrrl,icii,,
a fortei musculareeste impoftanti, qi ertins5,, atingind mu;chii
rr.rlurilor', i:r,itrunchiului, ai membtelot, cu extensie chiar la nivelul mugchilol irrrrlvrll,i de pericarionii bulbopontini. Atlofia rnuscularS, este precoco
si irrrrortantd,.
q N euromielitn optiad, ( oftalmoneuromielita, boala l,u,i Deuic) debaji,rlo obicei brutal, de multe ori paraplegia precedind semnelede nevriti
I rrrr,z
opl,irii,(Dri,ginescu qi colab., 1962, 1963).
l') Ilxistd gi cazuri ile scleroad,in pliici acutrit, care realizenzd paraplegii
(rrrrr hrtrrlplegii) dramatice, flasce sau spasmoalice, cu senrne plramidalo
irnl)r)rl'lntc. Sint frecvente puseele de paraplegie acnti, in cursul evoluliei
rrrrci scloloze in p15ci. Puseele evolutive de mielit5 in cursul unei gclerozo
rrrrrll,iple pot sd, se declanqeze cu o ,,tragici brutalitate" (R5-":.fgP",
g) A.lte encefalornielitepot realiza in contextul clinic malifest5,ri para;rlrgicobrutale, I& care se asociazdqi semne suplaspiuale.
\) Spond,ilita tuberculoasd (boala lui Pott) trebuie suspicionatii totrLrr,rrur,in liulrr unei paraplegii acute la un adolescent (indeosebi) sau Ia un
rrrlull,. l)itgrrosticul este u$urat prin prezenla conira,ctudi dureroase ;i it,
rlru'olii colornci, dar mai ales pdn evidenlierea ghibozitS,lii qi a altor semno
rlrr plri,lrrrryilo
vertebrald,.
i) llr,nrtnu,I primi,tits rah,id,ian al ltti Ewing poate realiza o pa'raplegio
lrrrl,rr,lj1,Lr, copii qi Lr, atlolescenli. Djagnosticul se verificS, prin imaginilo
lrrrl ioglrr,[icr: plulifocale, in geocle, pludver"tebrale qi costale.
tumori primiti,De se,usecurl.darei,ntrarahid'iane,intra- sau extrn.
.iI JLl,l,c
rlrrlrr,lopot plorluce paraplegii acute gau cu ingtalare rapicl5,, precedato
rrrlrnrrirrlo o sourtl periorLdfl tle rahialgie qi ciaudicalie spinal5,.
lil l[t,n.in,go-mteli.tasifiliti,aii a,euttiintfi, astS,ziprea puiit in discufio.
l) Il telom,ataciile (rumolismen'tul, total, transaars li ranxolisrnentul
ttpintl rnl,rtrior) pot realiza fie paraplegii, lie tetraplegii dramatice (Lazot'
Ilrrlr. l l)?2).
rll lrli,cl,it,lc;r,
rlil,i,lrrs1tit rr,lr.,
llrr olrirr,i, ittnii, rrltttttt'ltt
r.l,it.jrrlol
srrlrcr,iotrro
ttcvlrrriltlrrlr,tr.lrirlilttziutttlr'ttr 'itriLllitnc.lr
r,rr
n,,irrrrr,
ri ri rrrri rIIr Irr
1
-l.zirrrrii,
cltt'ltt'lrrrtso,
llr,trlltl,rr
rrtr'rrrltrr,lc,
r,u sr,tnttorrsooiiti'tr
vcslibrtlrtlos.ir,.,r,rr.uri\nr,
S..\I.Itr1otrttrr{'iilrrrrrltrsctlo irrvi,sl,igrr,{,ii1,
crtnlial potrlt tr i.liuglnosticu1
r,l.r,
trrrlir}e1,ice
qi imunoelectrofoletico scljce, I[il| rlr ,i lill|s rljrr 1,.(j.1,].rrrlrr0
rrlqrrrnerltein plus pentru diagnostictl ,l, S.II., ilsr, cltlrr cr{o ru't.rriil:r,
;lstii,zisocotiti, ca o JJoaU,autoimuni rle aut9ag1gsi11l0
(l'clrrlro li ,lolvirr,
ll):14; Ila.bat, 1957 ; Liirventhll li colah , 1960 ilrlrlsrlen 1i c'lu ir., I 15tt;
I )nmii,qi cotab., 190-1,1965 ; Schapira qi Palki 1961 ; Vari Surrrlr,,'I llri? ;
l3r*usqi colab.,19i2, 19?9; Cojocaruli c,",Ja\,19?8;'Pop6viciuryi t,rrr.rr,
l$80; Kright, 197?; Colby qi colab.' 1977).
b) Neuromiellta opticd'( oJtftlmontielila, boala lui, Dpuic) poir,t;o
, y()r f i
o evolulie subacut-cronicii, x11..tlebut ?xlilllrrletic - paraplirgic, rl.5i iir
rn:ljoritatea situaliiior debuteazd,acu'l saLrsr-ibacut(Driig-nncscrr
1i coi:rlr.,
1962. 1963).
p.oru1'1eginspas t,-ttlicd,r:rt:d,oti.lili.
cJ Mielita .cro,icii,.lueticd
-(Er.b),
tui GuiLlain ti Thion {asociotorlc s,.irrrr,,
licd"u, lui XIarJun gi sin(lronr,ul
de encefaliti, cil tabes qi.cu mieiitil Erb), frqiysnls altddatir, sirl .r lr.rrr
r.te rar intil.nite astizi in practic,r,.neurologici,. Nu tr.ebuio i,Ohrqi rri lrr
rLiti.m, iar prezenta sgmlului hii ArgyU-fi6bsrtson, a hipclcil,oz.i, rr
lripefrlbuminozei qi po^zitiviratea-reactiilorB.W. si 5 benzoi r',r1rirlrr.l
rr,,
diagnoslicut.Tn plus. in pataplegia rpasmodici c1orl.-sitilit.i.r,
'.lrrilici
rr.lui Marian apar gi : keratiti,, tulburd,ri psihise importante (ca11,c1;r'r'irr,1r
qi
,1,' tip demenfiall ;i, adeser. convulsii.
J) Compresiunilemedwlarede diver:e naturi (tumoralo sa,u ilrflrr.nr!r.colii, primiiive sau metastatice, subdurale, extracluraLe sau intramoriu lllr.o)
|eailiz.eaad,,
in funclie,.de livelul acestora,_plraplegii sau tetrrrpkrgii. l,)rirr'
1,,rnj'i mulle pobibilitili de reaLizlrea dellsi[11[16e6o,' - O compresiune realizatS, brusc sau tapid se poate manitosl,rr,rrr.irr
{r'-o paraplegie flascfi, ulterior, in decurs dd citevi s[pt5,mini, 0voiirlrrrl
$pro o paraplegie spasticS,senzitivomotorie. Se intelege c5,tle obic.i
I'rrzr1,
' (rrri
ou dureri railiculo-funiculare intr-nn^terit'olil limitat, bine prociz^,1,
stu bilateral) precedd,instalmea aleficitului motor cu citeia sil,,l,i,ririrri,
Irrni, sau chiar ani, fenomen cu male valoar'e diagnostici.
- Alteori paraplegia esto lent-progreSiva, de la incerrut sDrrrticil.
,lrr de mu lte ori precedald,cu mult timp inahte de fenumenetlo clnurlicrrllri
$pinal5, oel mai adesea fir5, clureri.
- Alteori evolutia lent-progresivl nu esls precedati, de fonorncrtrr rlo
rrl:urdicaliespinali, in scbimb pot apxrea 1y15iop11i
sfinctoriene plnooor..
- Dvolulia cea mai tipicS, este unndtoaroa: mai intii faztr, rodlc'.
LrrL ilureroas5,, apoj perioadi, de clauclica,lie,apoi sindrom Brown-sdqnrrlrl
r..i,iLr shriit, paraplegie spa8tici,, inso!itd 5i rle tulburiri tlc scusibiiit.lt.o
(r'rrrctle mulLe ori Pot liPsi).
Compresi,uni,Ierneilulara ceruicala superioare prorluc rnono- s^,ll h.rrrl.
plegie, urma,to r1e tetraplegie spasticS,, cu tulburd,ri de se.sibilit;,6 ,rr
lIlvet.
l{tl
140
,fl
||irlorl |)| | ()| |ri | |i! |(. (rrrr t,irkrrrtrr l' rIol{r'||ltirii, l0trlt'rrsr,rlirrll|zirrtrii).Axl lrrl,tlt'
piklll, itr lrolrlrtoililrttik)
Ll ttivrrlrrll)tr, lrrz, trllcxolo crr1lt,tlt,l,o
lrlxlotrrittttLl
rrrrprrtiolrtc
i ncr:r,
rliu
rni,ilooii
r'ai,lnhl
rlll(l\(ll(i
outanato
lrbd{)rninlllc
1trozonl,o,
rii itrlirliorrro sint abolite. fu stititrtlr, irt compresiunile sub Du, r'cflt-rdo
:r,|rrIlrrrirrIrlrr
so mcnlin pii,strate.In cazul unei compresiuni sub l), r1itlearirrl, r'1,HoglrrorrtuluiDro sepoate evidenlia semnul lui Beevor (itr1, de Arsoni
,,i lolrrlr., l1)?7): la ritlicarea capului $1a trunchiului, ombiJicul se deplarrorrzir,
irr sLuirdatoritd, laptului cd,porliunea superioard,a muqchiului ilrept
rrlrrlorrrinalprimeqte impulsuri motorii, in vreme ce porliunea inferiotr,r':i
r. i rlc lrirllllizitl,i,.
l.l:i
' l A l l l .l .
l Ii gl .i ri l { r
lligeirile
l, l \ l ( r s i l
Iill)lrlIl
I ||flillrrrcu
l r l . { ' rr l l i
Dlepli antcrioli
Sternocleidornosloidieni
cr;.C,
Per. XI. crao+
c , -c t
Splenius
(lomplexul nrare
Drcpti posteriori
Micii oblici
Cr-C"
Ct-C'
S c alcn i
'I'rtlpcz
C,- Co
Pcr. XI -l-
q-c"
cr-c,
cr-c,
n.
spinalI- ramura n
ccrv;cali
C" Co
Coborirea
umi r hri
Itomboi d
IL'tghiular
Pectoral ,nic
,1
J)orsahrl mitre
Subscapularrl
ca
cn
clcl
ca
Supraspinos
Subspinos
Rotund rnic
Cr cu
0r Cu
-Cdrtuclia
brafului
Dorsollil mare
l l otund mare
Peotolaiul ma].e
SLrbscapularnl
N eN ul dorsa
all rl
r lru i r r r r ,,
N etv rl l rotLrndul
n d u l r r i r r f.
\Iai Inul l i nc r\',ll t)r,,\,.rl l l
c l i ]r pl c )' rrl i ))rrl ri :rl
Abduclia
bralului
D el l oi d
Sup!aspinos
c, cu
ca-cs
cl-cs
C,-Cu
cs-ce
C" Cu
Fl exi a
4nlebratrului
Biceps
Brahiai anlerior
Ltrng supjnator
ce-cr
ce cr
c6-c?
ExteDsia
antebratului
rygrl
Tl.iceps
Co
Ii adi rl
to
l '1e\i a nri i ri i
Pahrafii
(mare qi rnic)
Cubital arrLerior
C t* C e
tt
Ilxtensia
r:liinii
Prinrul ;i al doilea
radial extcrn
Extensoflrl
degetcl or
C ubi f{ pos tc ri or
Cu-' Ce
i l adi al
co- 0u
n adi:rl
fi
(lolr:l
Marelc rLcrv
t44
Per, XI -F
t:t
Fl 0xi a p oi i c el ui
(pri ma f i a
(loua falangd)
ri t
l l cxi a i n dex tl ui
Itl ter{ )l n,s ipal mx ri
$i a mcdi us ul [i
fi doIS.rli
(D ri ma fal angA )
l rl cxi r { l tl angc l or Fl c x or c omun
(s l |perl , fi pr0f.)
cr"-c"
or--c,
l \l rrcl o nt'r!
cr , (:x
or -- 0N
{.i Ii Lrl
Irrii rri
r r iii (1(' i r, r \ |
S pj nnl
(c I.\ i |rl i
(lilll:Ll
i
N c N ul
{ (l
.rrl l r{
C i rc unrfl (\i
Ileltoid
.!,!. t
1l
"--*
C, I3r*
C..
capdui
S p le n iu s
It0lolijr
crtl)1rhri
(sr'fc
drr:rl,trt)
'1'raprz
Il i di carca
rrmi ml ui
Dintat mare
rr olrn{rtlJ.
TABEL NT. I
l l i di carea
bratuhri
f0lfclt.
t,
I
N r. i l
Scurt il cxor'
Lung
i l (),i a d c gc tc l ol
Ll Lc ros l ,ti p:tl rrrri
'l [i 5
fi dors r' l i
(pri rnr ftl nnl i i )
(rL (l ouu tNl tl
' rl .{ i )
r,|l t,rrl r( i rl
(r' Ir'i rl
l r l r tV ri )
cs
c"
cs
cu
ot
Cn- Ct
C"
N erv ul l 0l l rho
hoi rl r l ri
Nen'lll llDi.jhiLr
ri Lrl N nrl li|
N erv ul pe{ Lorl
Nervrtl rnxr(hri
Ner.JulsuIs.:tll
N erv ul s l rpf)si pi nos ul r I
N erl ul s rl s pi tl (
CircuDrflc\
CircumUex
Ncrlrl sul scl
Mcdian
crbi!1l
,9L9,
o? 1)1
C' D'
cr
l)1
Itac l i al
C ubi Lrl
tr{cdiaIl
ilubit:rl
c?-, T)1
l l c di arr
l -(?
' r)r
i
(tr1)i tj ]l
j,',,,,
N { c (ti x rl
],',,,,
( l rrl rl l :rl
l4ir
(:o|l,llllalo trnbol
CorllnuarccqbcllI
o
tl
I lxl orBl[r
l){ lccrlui
llxlcrrsld
lrlU rrrlo r 4
rl{:grd.c
(primn
hlu rgll)
(r (loro $i a
lrchr ftrlanEtr)
llJ
Extcnsor comun
Plopriu al indexului qi a1 auricularului
Intcrosogi
Lombuicali
o o -o !
Cu-C"
Ct
Dt
liadial
I
/
Radial
Cubital
Cubital
Interosofi
Palmari
c"- Dr
C"-Dt
Cubital
Cubital
dductia
pollcelui
Opozant
ce D.
Median
Adduclorul
policclui
cr-Dr
Cubital
Interosoti dorsali
cr- Dt
Cubital
Abductotul
degetului 5
cr- Dr
Cubital
Scuftul abduclor
al policelui
ce- Dt
Cubital + Median
Abdrctta
(lcgctclor
Alrductia
pollcelui
10
L"- Ln
Fesierul mic ii
mijlociu
Lo-L
fesier superior
Abductori
Fesiexi miilocii
L, - S
Ln- St
fesier superio!
fesier superior
c o[ pid
Obturator
Pdtlatul crural
Croitor
L^_L.
L s- L 4
Lo-L"
Obtumtox
Obturator
Nervul musculo-cutandt extern
l, f lorlll (li)rpsci
Psoas iliac
Lr-Ln
A l, (luc llu
c o l l p Hcl
totofla
IitlrnLru a
(roIptcr
llo[n
(f r th {
(flrll
lr 'In
'jxl
(!n$ln
0xlu
g0r bol
r40
:urator,
musculo-cutanat
interll, Bciatic mare.
Adductorii
Drept iltern
Ilicep$ cluxal
Somlte$dlrros
somllllenrbrtnos
Poplltcu
0rollor
Flexia
pioiorqlui
L4-r"6
Gambier antelio?
(Si rotalia
ineuntlu)
Peronier anterior
Lu- st
($i rotatia ln afardl
Extensor al
Lu- S.
degetelor (tn mod
Extensia
piciorului
Rotatia
piciorului
induntru
Irlexia
halrlcehi
Prima
lalangd
- Celelalte
falange
IJ
Extensia
halrcelui
t5
Fl exia
celorlalte
degete
- Pdma
falange
- A doua
falange
scia!ici
Marele fesier
L^-Lo
Lo- Sn
I-o- sr
I'o- Sr
Lr- sr
Lr- L*
t0
sciatic mare
Sciatic mqre
Sclatlc male
Sclallc poplibou intd
Muiculo-cutaDot cltorn
QnAdJicep$ul
crulal
I _.1 R o t a l i a ,
liJ
iixtcn\iA
piciorului
in alar{
(l(llrclln
I
'
A{l(lrr(LinFi
|,Pr)rllla
rhgcl.olor
l tl
2l
Lung fi scurt
oxtensot
'/
llxtensia
celorlnlte
dcgcte
L'n-l't
c fl rrIl
popl i l eu
'fibianul antcrior
Sciatic poplitcu cxtcrD fll
anrenol
Gemeni si solea!
Gambier postedor
(qi rotatia
iniunttu)
Ltng peronier
latelal
(9i rotatta
in alard)
Ln- s,
Ln* S"
Tibial posterior
Lu- S'
Ganbier anterior
Extensor propri[
al detului mare
Lr*Lu.
Iixtensor comun
al degetelor
J-ung peronier
later4
Peronier anlerior
L._ S.
Ls- Sr
Musculo-cutanat
Ls- Q
La- Sr
Iibial
Lungul flexor
propriu
Lornbricali ti
interoso9i
Lrngul fle)ror
proprm
Scurt llexor
proplrlr
Adductor propriu
I-ombricali qi
interoso$i (pt.
ultihele doid
falange)
Extensor propriu
Pedios
Loinbricalt $i
intr06oqi
Flexor comun
Scurt flexor
plahtar
Flexot comun
Extensor comun
Pedios (ln afala
degetulul 5)
I"omhlcall ti
lnterosoil (pcntr
ul[hnd( doul
fslun{c)
anterlor
Tibial posterior
Ln- S.
Ll- Sr
vl
Ln- St
L"_ S.
Lu- Sr
n. plantar intern
n.. plantar htorn
Sciatic popllLcLr
exlcrn
plant{r inlorn il
Ln- Sr
Ll- St
Planl inlcln
plantar int(r:t
Lr* fr
plant0r lntcfn
Lo-'- Sr
Dlautmilntqr:1
ll cxl0ID
t4r
-Ttiaeps
corPr
- Exlensor
rodidlis lonqus
B{qrhlcte diaI is
,flexar,'.carpi
ra0talts
,Pqlflchs lcnilus
pallitis.
Apponens
pallicis
Abdua.f.or
brevts
flexat pollicis
Drevls
,Abduclor
Po icis
Exlensorcoai
'tudiolis
brcvis
'fxlensorcffpi ulnoris
Exiensot
digikrun
Abductarpotliais
lon1u5
Abdwlot Pollicis
brcvts
sibiifiis
Flexarccryi
Abdrc.btdigili
.flixor djgilj
quintibretlts
SFt
ciis*
Atubusntdits
&
Gluleusnoxinug
.8
Gtoailis
Senilendinosus
Eiceps fenoris
Voslusblerolis
Seninenhronosu,s
Percueus
tonquS
fibiql,is
2a
Exlensor
digilorun
longus
Anloiot
Fastetilr
riottrt,l(tttt iitttrltotrtrlt' , , I )()| i(t III i{|I i I I'i1' ItttItrtioItIii t lottit'it),r'iI i1iI'toltrtllrrt'
prrtilirtir,, lrrrrluttt ;i sottttttltltl tjot'tItIit'tttI
l)osl(ni{rllltf. lirllllt lt,ltt ('ill'lllrll'f
Ilr,rrriIilr,I,
itl c0pilli,litl sttll lit, \'il'sl{r.1,itl0l(',
tjr'urlo.
rlr:LrttLc:t'zir
l,ritl rl'i,tolii
rlis[alclocalizi,to1:lrnomblclt inlerioare, cuplinzir([ ittl,ii ttttlst'tllrtltt|rt'
1rr'rrr
la illccpul ou (lolioil lrr()lt)r lrrr
rrior'[, apoi pe cea gambier'; post,erioarr",!,
plc:r,irnporta,rlt, menlinind mu1t5,vreme sta,liunca fi rnol'sul (c,,trr ilttrii rlrr lrr
jlrcep[t poate lua un aspect stepat). Apoir 1en1j
]l iil rrr
-progrosivr ll,Ilriolr'(
Iolllizirr(l
o\tinde in mod simetric qi la treimea inferioarii a co[],J)s()lor'
frl,rofia caracteri,sticd, ,,in picior ale coco,i' (sau ,,in cizmii iltaJl,il,") li
lrozi{ie de mrus-equir a picioarelor, cu consecutiYletulbut'iit i rlo tttoli
lilnte, insolile li do tulblrrd,ri ile sensibilitate ectromelice (strbi()(liivofii
obiectivo). Xlernbrele superioare si]]t afectate mai tirziu, do l'egtllii ilri(,ilrl
{n atlofie tle tip Aran-Duchenne, extinsi, ulterior pini in lr'eimca ttti.ilotrirt
?r antebratelor (atrofie ,,tn rnan$eie"). Existi qi form de tl'ecclo irrlr'(r
boala Chaicot-Marie $i eredo-ataxia cerebeloas;, (boa1a lui Fritxh'tr irrlt),
situatii in caro se asociazd si tulburiri de sensibilitate profundX, cu irl,l \jl'
{prin"leziur ea fibrelor radicuiare lungi din coraloaneleposterioare) li, ov(rlr'
t,ual cifo-scolioz5,,picior scobit cu dgete in ciocan, precum !i mioi fi lirr
dive semne cerebeloaso.
4) Itt siringr.tmiel'iase constat5, lrecvent semne motorii poricariorl:rl(t,
cu sindrom Aran-l)uchenne. Amiotrofia, cel mai adesea simet'ricii, int{no'
{ea,zd,membrolo suporioare cu fasciculalii' excoptional de rar apil,r'irrrl lrr,
lrlembrele inferioare. Prezenta tulburd,rilor de sensibilitato di$o(lirLt(1
:iirigomielic, suspondate, a imporbantolor tulburbri trofice, a sindrolrrlrllri
(li:rglxtH
}iramirlal asociat, procum $i Yolulia foarte lentd, ne sugereazri
liicul.
5\ Iurnori,le intramed'ulare ti traumutismele aortebro-mcdulu,rtt(:tr'
pot genera siDdroame motorii pericarionaler asociirl,c(1ll rt,ll(\
hnnal,omi,eli,e)
$ernne comisurale, indeosebi cu tulbur5,ri de sensibilitato de tilt si|ittgrt
rnielic, de obicei inil,ial suspondaterapoi sublezionale(cu niYol (l{,5(!rr$i
bilitate).
ll\ Leziunila rdd,ic'LLlare
.mteriodre prezintr, o serie de particllllll if i,li.
I)istribulia topografici' segmentarS,a deficitului motor $i a celol'LrlirosorrrrriI
colelate a1esindr'omuhi do neuron motor periteric este identici' ctt |trit' tlitt
Icziunile perica,riorului, dar fasciculaliile musculare sini exceplirtLrtl rlrr
fur intilnite.
Pe de alti, pafte, vocinltatsa ridS,cinilor posterioare facilil,oltzil' rlso
riorea frecventi tL unui silfdron do protoneuron de tip radicnl'l't,'
1) Comprosiunile raaliculare (tumori, arahnoidile, hornii (lisrlrrl{r li
rli,o &fectimi vertebrale compresive, tumori vertebrale primitiYo s2l,tls(xlllrr
rfirrt, boala lui Fott .s.a.)teallzetuz['cele mai Yaliate sindroamotolx)gtrrli(1r
(rorvicale, dorsale, lombare, sacrate) mai mult sau mai pulin o\l,irrsr!.
llrrrliticilrils de reflexe (osteotendi:roasor
cutanater a,rticull,re'pilolrrol(,lii,
rrvsntual m[coase) $i aprecirea tulbu.rAriior de sensibilitate i],so(,iirl,(tl,r\
rlclrnatomerele respectivo tranqea,zl localizarea $i extonsia, loziunil(]I'.
2) RadicxLli,tela(respect'ia ma'rlingo-rdd'i,culi,re1c
) virc1,ieo' ltotitrtt sttlr
rlo llto ctiologii pot fi unilalrorlllo (n&i mult sritt ]nfti l)ulin oKliins(r)$rr'rl
l)ilr,l,(nil,lo.
Jl) I'olirtdia.tl.on,(,,1n
ild( lt\tl t'ollizl irttblortrii;r{,ttltlcgitltr (trtiti tiw tlorrt
.i-,i.1!.)!.
l'roltlrutr dr l.itr1tt,*lrtlrt1t,tt1rulir
pritr
li tliol.oqiritt ltrr.t,r.l,i:iilr
I, irttti rr.lt|tI t|t|)|1.t||tt,i
tttrlrtt1ntilr trl
l\ l., itttil" p rirrtt'iunulr:
l) I'olirnn.irlilr a,nlui.ourd,&u,u,l,(i,
(lM,l,(, l,ut IIein,c-llh:tliri). l)rliciltrl
rroiol sc irrsiirLulziibl'utal in decut'sdc citeva oro sau zilc, rle obicei dupii o
iorrrliilirlrlili, (lo nrulte ori inso{,iti,cle fenornenedigesl,ive,I'espilatolii
1r,,r
i.r rlr. rr,rrrrrrnrorringe&le),
dar uncori Ei in plini, sfnS,tate (,,pam1iziilede
rI rrrrrrrr.rr,{i r' I ). Sc lcalizeazd, tablouri I'ariallile, cu paralizii limitate, parccl:n(1, riur, rIirrLllotlir-Lfoalte oxtinse, tuteoli cu caractexeascendento(sin'lr,rrr l,rrt(ly). 'I'otdeaunareflexele osteo-tendinoasesht abolite in zonele
ll)il,r'rapi{l attlfii musculancDihipotonii remarcabile.
1r:rlrrIiiicrr,
l,ipslsc 1,rrl
brrliililc de sensjbilitatt-,.
')) I'rtl irtm,itl,i.tn,
o,nteri,oud,cronicd se caracterizeazS,plin deficite motorii
lrr rrllolii lnuscrrla,r'c
(rle rnulte ori rii cr fascicldalii), cu instalare fi evolutie
l{'rrl plrrgrrrgivi,,orr loc ,lizare bilaterali, !i simetricd sau cvasisimetric[.
l\l:rjr)r'ii lrljol,lrcos1iol
,r sint degeneraLive(rareori cu caractero erdo-familiale),
c,rk, rrrri rrnrltc iiinrl dc fapt forme atipice de S.L.A. (Ratlu, 1978; Trillet
rli |olrrlr., I070), iar unele cazuri putind reprezenta forne subacut-croDice
rlrr prrlirruriolilevilotiice (Drd,gi,nescuqi colab., 1962) sau sechelelounei
a,nterioat'eacute (Ileine-Modirr), in care atrofiile musculale
1roIiorrrir,IiIu
rrrrlrlir.iirlc rlotolii, dupi mai muui ani de la stinger.eaprocesului acu[,
rtrlcp ;li, so extirrclil {i si se accentucze ptogresiv. Drpi, Radu (1978)
{l \ rirlrlrrlrr,cir,ontil itli distincte a atrofiei nusculare progresiyo Aran-Duchetrrrr., r.rr,rlc lal)ir fi {l pa,raliziej bulbare proglesive Duchenne este indoielr r(ir,, rt'l,i.ii1oilleplezentind mai probabil forme atipice ale altor afecliuni
rr'lr,rrrrrIr'orrrrIrli
lnoitor (S.Ir.A., sindroame r1e S.L,.A. el,c.). Crdem, deci,
r':r lrrlnurLrrlrlc ,,lrolionrieliLiilanter.ioar.i,
cronici],devine incorect in etapa,
:rIlrrr,lii rr,orrrLo;Lin{elo|
noastre, pentt.u cazut'ilec1l otio)ogieneprecizati"
Iritrrl lrlrlirlir,bil si $e nlilizeze telmenii dc ,,sindron tle S.L.A. atipictt
rrr,rrrlrr ,,sirullo])r I )(r'icalion:t
l anterior oronic de etiologie nepleciza;bii,'r.
'l'ilrrrl lrl rilr,i IrccvorLtintilnit este siuchomul amiott.oficAran-Dlchenne,
rrr crr,r'r,
rloiir,ilrrl rroi,or qi atrofia rnuscular5,incepe la triye.lul rniinilor,
rr.:rlizrrrrl,Ir'irr rr,i,r'olil,
oi)ritentolor tenari, |i hipotenarii [i :r, interoso,rl,,r',,,rrririt,sirrrirr,tiii')
;i ,,rrrila in ghear5", dupi cale progresiuneaatrofiei
l:r rrrrclrrl rr,rLi
oll|ir,l,t1or,
tg lrzaa,z\,,m ta t1elredicator.,, $i ,,mina Si antolrrrr,lrrl rrr'Irrrlrrl,icJ'.
-,\tl'{rfia ss poate exti de qi Ia nivelul nusculatur ii bra,I rrlrri |i r'lriitI lrl rIl so[]inturalizomelici a memltrelor Supelioare.
ii:ur (lrF(,r'ir.i
rji cazut'i de ,,poliomlelitrdcronich" in ctre atrolia debu1,.rrz,:lrr nilrrlrrl utl$ct atut'ii proximaie armembrelor superioare,realizind
:r,r1,i.,lc prorrrlolrriopa,tice
(Yulpian). tr'ormole de ,,poliomielitl donicS',
r r rlr.lrrrt,lir rrrcrrrlrleleitlforjoat'e (pe glupele tnuscxlare peroniene) sint
l l l r ll
l t r r'.
( ]l l i to l l l l l {l
1 r l r , r 'l l p l 0 g i c o) , |) o l 'i ci l ,o l o r r l o l ( t i i i t,JIl ,t'i tt l l tttl ,cr i 'ttl l tl l o l ' l l Il ) 1 1 ) l tl i
(
o
tt
tl
sl
r
o
ttl
,o
tl
tl
i
tl
ti
t,si
i
,
tl tt l ti ;tr t
l t,ttr l l tr xi o
. . l : r , r '1 r l 9 t L {! l tt( ,l r r r i l l o t' ;r r r ti l i r r i t
1 1 i Ir r i r ,lt0 l i i ) t1 i ( l o [t1 ) 1 o l tr \l l tl ttt sttttzi l ,i t' r r tt
l o u i r ! i {i l , l t l r , i,o tr i r r tr tl tsf[|tti i
ll, l
l i i r t l t 1 i l r r r t t t ii r l i stl l l r
tl;tt i1irrtt
r,itrtl irtr boltrr,v rr,rrouzrr,L
lrit0vit sri,lltit,tninisoi ,hr,lgiilu brrsottlii,,
r', itt
illrrliari l,osliaulrIr'o
i]i 1xrrinoi[lo,]rooulrl Ii t-lttittllrttliili slittrlIrt'icrt
tlrolrlenl,ulilt cirr.eau sui'vcnit Ei lorlo ]onololilteliotr ;i l,tLlbttt iili ltt tl0 srrtrli
rlirigrtosticul tlo lotttlttr
lrili[a1,cin ;a, trebuie categoric sii inbi],ndorti'lm
scilticri ban:rH,,,siilii xe gindirn la o compresiuno in cozii (10 (,i '
rrogittrlittt
sau cron.icalan't-progrtsiuo
b) In cattr,L
rtrvi euolulii suba,oute
irr prirrtul rind la o campresiunaa cozii de cal, in spocialprin tutrroli srtlxltt
l e primitive (neurinoame indeosebi; limfosarcoame ;.rr.) sittt ttlol,rr'"
si:ltice (subdurale sau extradutale), alte tumori extrrldttlrrlc,borula,IIotl'
elcirr, alahnoidite chistice pseudotumorale, sau la comptositttti rlrr rrli'r'1,
rrrinrir. inclusiv rertebrale (boala Pott, metastaze !s.tr.)
lll) Lezi'unileplemLrale te^lizeaz\ silldroame de neutott tttrtlttt ;rt'r'i'
li)r'ic cu topoglafie palticulari', uqor de recunoscutr pri]1 ertenBla, (x)lrl'rlr
l,ului semiololic in teritoriul plexului respectiv (cervical, brahia,l, lortrh;rr,
siloritt,).la caie in rnorl obliga-turiu se asociaz; tulburi,ri dc seusibilil;alrr iri
ta'ofice in respectir[l teritoriu tle inervalie plexurali.
sanxiologicd'9'i problem'ele{k dr(llttorlio
Arnintim pe icuri colt.stela,ti0,
r:liologic Ln sindladmela pleaulare :
1.) Sind,rotnuld'eplen cemiu'l impiici : alteratea mi$clrilor tic IL'xirr,
roirrlie qi inclinalie lateral5 a capului qi a gitului' la cate sc pol, asttt:i:r'
i,ulburi,r:i reSpiratorii prin paralizia diafragrnului, prtcum $i trtll.trrtrlri tlr',
n'nsibilitato in teritoriile ratliculare Cs-Cn.
E*te reahzat de multiple afecliutti I tr'aumatice (rlt colonnli tltvi
ra,Lr.inalte), tumorale, inficlior-r,se,malformrtive {r-r'zi Arseli ,si rrolllr.,
ll)iiti.
" "'1;1'
g i nd.ronutdaltlel,iru.bdpoate fi reatizat lie tle leziuni t'rr,rlicrr
l,r', 1i'u-[r,), lic,le'tr"z.iuni-alet-mnehiuri]orltrim1 re (sllln'lioI',trti.jlrxtrt
.;r i,Ui..r:iur),Iie rlr' leziuiri rte trinchillitor sccundult -(suporiorrirrf(rri(rr
q,iptxt|r'ior), fie '.rleptexului insuqi.Ca ataie, se pot rlistitrgepatnt, I)trrittttlt'
I'rrt'jtuul.
i
I
i
t 0il
r0r'ror
rrrui1r'ir,iDitill
ryi..rrI uu,uriri
''i,1";;;lil;l,;'l ,;r,,litt'r,
ili',,'li,lliiil:,jil
l';rLa,liz,irr
do lrhrx llrlrLiill r.nla.2r.r,r/usri
rlc tliatrtrr:,tlit,!,inni:
,
tl 'laniu,ni l,r& ryjeliq?Irr,rrivr.lil colorrngi/cerricrr,t,, inierioartr
,
li,diorr{ir,l(,Nl lxrljr)rrre, sa,u la nivclufclu,viculei, a/riL,xilei si l-[ zonelor
sujpia_ si
(.tuIi,a
irulrllrrr.ilrrllrr;
,1 frlcturi
tertr
ale
claviculei,
viculei,.luxa.l.ii
ldxaiii scapu
scapulo_humerale.
lu.humcl1l
lc. cl,irrga
clotrEai.ii
rii
1,,,.1,,:]i
l,l,l'..],,; lrir
Sl qlf plerului
ctriar..r.u
snrulsprea
I'iitticinitorl;
l,f.
,(ureori
,|,,rrrl)rr'sl|rlrL,l|f
r , rrlill',fl.llll,,li
)rl sl |l l l|t il,\rla,
il\ lt a. ca
p tl d A ia
p u rl d to ri i de
nl (} rvent,i i chimr,c a d e pil.ld,
l a purthtorii
Ii c. jintewenfii
d e (,i
cirje,
chi nri ,
_de
Icgluurdo mai SUS;traumalismeobstclricaje,cu L.zirrne:r
l:r,.r(,,1)r.:rr'r't,''ts-l
rImpllt
.nrllerii (consecutivexnui bazin sirimt, rrnei
!f::),'],1'.'.,,'::nlrr,rn
l)r'r'?r'hrirlrrrtel{'ctuo-irNc,
unei eompresiuniexercitate tle manevrele obiitetri_
, :rrr.,l)r'lr,\ll ptcxului intre claviculd, prima coast5,
elongafiei sau smul_
Di
llr rii I'julir.irrilor')
elc.
I,'\'.yil,tsa.* r(:Iiculitr ftslp?t;, rudiaut,,pntii)t'intec!i()1sr...."4oxi.c
,b\. r.t:tprr,(.,
,(
purl\ ac.tntln.
l,r':rsr.t1r1
Su.feriu,!e
tlc ditsersenaturi : hpondilite (indeosebi morbul
,r.rr. 1)
-uertebrale
,tumori Yertebr.ale,
r.(rr r.('r'vrcar)
;
i.tr_ara,hidiene ;i extrarahidiene;
lrrrr.lrrli;i rlisiocllii vertelrr'ah.;/herrrii
de tlisc cervicule._
coslt)nertpbrolc deJileu.tu
i sralarir rr6oastricen.icalii,
...,'.rt .l':'rr!!:i
.alc
:.||Inrrr|lr{,
Ni.rtcnlce,rcalizalo ^si
indeosebiprin tribcnrofja nru^chirrlrriscrj
rr.r :r.rrl('llot,crre lxgrslcaz{ ,.defiieul scalenic',(saptiul rliltre cei
doi
Ei pnnra coa-slii)rqicare iD acesl mod r.omprimi,ple.rul br.;r_
if
l,li,
ll'
il,,l
:',,
rrrr sr irr'1(,lltsuDctaviculard,
(Arseni qi Oprescu,196?; Ionescu,*popovicin
rri culalr.. .1.921
; Riser, 19b2).
,.1 rl'lrmori ale, virtulyi p.1r$g-n?T. Sinilromul paneoast_Tobias,
in
i
.
cru,.
Insii p,aralizia plexuliri biafiial, inti]ninr dureri qi un siDaliorn
,lr.
I t i || t{ r.
, { t , l il {} {,t u t.Nl.
Nervul circumflex
Muschiul
dellaid
,qomufl culanate
Muschiui biceps
br cnhial
lr' l l |r.
Circumflex
Ramuri cu.onle
ale antebralului
/rr.
.r. \"f\i i
c i i c url rU c \ \i
lrli rr cnbitalul :rnterior, lungul supinator qi fasciculele cubitale ale flox rtrtrlt I i
i,ornrrrrplofund). Iilexia falangelor distale a,le{legetolor_?r[-4.{t'orli.ttt.ijkr
r,irr r,sl.oimposibiki. ll\carea de opozilie u,policelrri trLt st.poal,c trlt,oltttt'
Sl lealizclzl l
Iiirrrl inlocdilS, prirrtr'-o rniScalc rG n[duZlli.ai fi,]iclri.
d, policohli po ltnlali llan r:u oolela'lto<lttgcir',t
1r,rzi(it: in a,bduclio
(r,mlna,riitttia4ri"),rtIt olit,t,ttttsolx)11('(fx I illllir
r:rrlr'lt olie rl eririnon
qi prr rnrrs<rrr
il: 'i a) . l, r r lr , xlt t lr lc it t r lt ir lt , t r ': t pt t t t t
llrl;rrt'rrrrt rI r,I rt i r,{ rrI rr i ( , 1i11.
rrrrl ui (rr,ll rt i I 'illor
| fi[
rtt
l rrxi co (ti rtl ' , r t i izo|r lc lr nt vt 'lul t t t t r li: r t t t t lr r i; ; r l) l'zi- t t r r r ': r . t t t t 't lj: r t t t t lt t i
r
lit
lir
'lt
lot
lot
r
t
it
r
it
rrl
ir
r
t
ablot
t
l
* i " .i " " -ti f .fn r , ""Jcar Dia8cslccr r lclet ist it ir ,
(n
rrli qi rl,rlr.rrrrrlio
irrbu{it{'
*l*ii iuoe.eio".o in t6i,iioriulncr.ruluilnudj:r,D,
(sulrr::rtlrirrtrl:'l
.i,:l;"it;-;;i", ii .i dc atlolii muscularcin terilotiultlislal
rt('
totali a nervului cubitl,l so(11rt
:
gllfA
cu'biLrId"
de
minh
icuhru
ltrittt'r
,,in
in exlensie,iar |eiilrltr' rlotti IrLlattgcitr
Ialangi a degetelor se
atitudide fiind mai exprimatn h ultimele rlouri, r1.g.lr' ;
iiu"i"l-r""".ie
jnicro$o'so ,.ritrl
frl U"e"iJ mi" se menfine in --qbd,i;ie, iar slaLiile.
qqu"a'
(''a
t,+bachc'ii
xllirt(r
primul
iii
inierosos
spal
inift'ebi
,i""ri,i".
*i.a,t- l"i S-i.rrd).'b" asnninneacrrrirent& hipofcnari cste i4rlrlizitiir I
il. ot.ti'alc, iorso 1leniveluT!or:1iuilii inforioarcrt :r'tl1r'ltrrrtttltri
.i'io f "
';.iinii), 'd'.r,torit5,cru!5,rii fleror'lui c.o1u1 prof.ntl ;i .ttlri
"rir"
;l;;;ii;J;i
la o pozi{ie a nriinij cu ullimele d('ui ilogcl( rrl
,-nt".ioif
^liiltn
'rf.lri
Ji P;i" piralizia intelosoiilor se compromil tnilciitilc rl'' ubrlrrr'lir'
t[\;;
ite degetclor; e) beficilul Ino-torinrcres"r'zi 1i tlcx irr' rtll i
"i-0" ",Oi*i*
aore i"g.ie, ddeosebi a degPtuluimic' precunL.)iudduc!irrp'rli"
t"fot
par[ial aceasti tulburaruptitr miqc:lrt':ttlt' rtlt't
lui (bolnavulc6mpenseazd,
ctthiLrrlrrnl .t i' rr
t) ParaliziamuqchiulLri
medianl;
nemrl
riii". .*ilt.i;.p"iir
;;;i';;;,;;.[ un tlcficit rl adduc!iei!i d llexici rniiLriiigr Testul ltti [rr'rtrr.trl
ailtluctoniiui policelui, in sensul,c5' bolna'vul tttt izlrtt
;;i;;ifi;t
!;irtiria
mina
un ziar siu o hirt'ie intre policele intitrs .6i irttl.r
cu
i;-t";6;i;;
doar prin flectxlea ultimei fala'ng-ea polictrhr i- rti
rla
face
i;l';i;;i;;;;
i; policelui, rcalizeia prin ucrvul median) l-h';,Test'ul tlt: ,,r'ii*
;rl;-;;;;ll
iir',r,"'i, deEetelofi atunci cind r-niinilesint aplicale una pcstc it'lli) l'r'rrr
e:trem6' de par,lli
ti,tele lor pa*Imaro.qicu degetele_
_i.nabduel.ic
P:";:':i
iri{ir'
intre tlegol'tr
Fig'
i,
lr,l
r -
Pa.alizjr
x'i#A#il
ii ;';t;
Iti"*g*xil],*:'*g*r**gttl'*tm*'"'11"'#
23'i
vul'urlriltl'-t'ut'tt'
i,
i;,.;:;; se
a.'.^"; cu-caiacter
i,,'r'qraat,ercauzalgic;
carrzalpic:m)-Tr-rlb-u
m) Tulburirilo
riU,,eo,i
asociazdXi
Ii dur'cri
"^."^-;"";
;rr,.rrorii
si t rofice se intilncsc atlobeain lelitoriul nerfulul (delonntlll irlr'
o*c,i"ioi."a pielii, cianozd, pielo lucioasS' qi subliatfi, txlt'tttr.'
;;";hiii";;
ovdntual chiar ulceralii a,Iedegetulqi mic).
I'rincipotii faalori elinlogiri: a) Leziuni IrcunaIl( la.nivclnl coi ttlrrr
r,,,,r,o""ttirihuninrusrtni 1-di raI,;'plngi ale ncrvului l& nirelul itlrlcl'ril
rniiuii (adesea o.1io41'so-;iliziunea :lrLeleicubit'al'';1contlrtr'
i,ii,,ti
"i
"
"f
inaIe pc osul pisilolm (par'rliziir ir'liiiiiiii ,1" 1t'nutito. nervo:l,sc-tr'rm
',(trotti
'.{.sto,]:it'tciia1"
g;'dle d'eJileutuisoalenicrco:tstii'
ntii
ljlor"'l: b iU
'?bm
(,:rlli; lri])( 'Jlrofiarnuschjului snllcn an[eriol, cu ingu"l:rt'ea-,,deJilottltt-i
pot ap,lclr irr/lrl(s,/lcltil'/li'lrri'
rir.rr,Ir.rrii . i ) 1 ,'; r)aolile rultilale ittTec!ioase
(livct'se
a.
tnalurie
viroze,
lii('i'lii
9.
neruth,i tatl'ial se carrlcterizcaail'1tt'inlr-rtsct'itrtlo strttttt"
:,:,),1?araLizia
tlt' ('rl,l'os{! lr'l'
i' lirrC1io rltr srrTi*l lt:tiutti,i, itt l\1111,{itr
lrrrlrrgirirrrr,,ni.r,,
:
rlis{irrgo1;t,1tuva't'irtiil,i
tnyttt
hldii u ttt"trttltrixt in[ (purali:irr',,,ltnhirtlir"
l\,))ln ptrrn,l.izi.rr
rrltirt"
ru)';\trir
lr'rt{'ttl
l9l:')
Ilirt'r,
drrxit'i
itru ,r,tiilurd,r'tnhtil.t
,ur.tir,"
"
ilu,rll,il'ir
ii";l;;,ll;fijlir,.il*:tf,',.:}"!!!iliiri'Jll'''::'ill.i5'Jll"L"'r;#:tl'Ll,i'ji1::l*ill;
,,,,, ,.,,.,,.,;"','i,ii.;,Jf;-J'.ii"ll
tin.\, t.\t..!,
r . r",,ri,i.,,,k
1"il :i.::.:',"jJ'"',
;:"J^fr,Ill"f..l;
^
" n r.I..|,.d ,-;g' dtA' r .j.' t) p' tr a:,?.\1r l) j?*t"ir o.r :_,an":Jl
m ei i i anul uj .
lrrllrr llrxici rrltimci falange a rlegetului ariltitor', astfel ineit, atutci cind
r'|rrir ,.rl(! rrrjozirlai.
cu fala pa]marii pe masd,,boLnlr-ulgg pq_?!9_-lg-ZCil!g
rr:rr,rrrjll urrghfu degetului aeitnlotl Unelo mis(.iiri coEi.h,
srtrcrur,ji{.,,
.rlr, polir,r.lrri1i rr,lecelorlalte degete sint imposibile sa,uincoinplete
"
(indeo_
ri'.1)rItriri(jlIiI(r rlo prehensiune qi t1eprindcre ir,obieclelor). Nir trebuie sri
Iil,ir||r |ii rle rnulto ori apal dureri cauzalgice,r]rbotite t1s tulbur,:iri vaso_
rrrrrlolii ;i l rrrliicc,limitate ldhlvehil inAe.iiitui,.i aimerl jusului, in special
rl I l ).r
l| il
I
sc consl,ati dolr l)c ur.l i,-,ritoriu par{ial
. 'l'u trut i}'i}:. tlp- S-eg51bili.tpl-c
rrl z,rrrr'irlr.itrllvrrlic lr,Iu'rrrrlrri mrtlir.r (.[i,t.:'.j ,^i.
I'rin.ciptlii.lurhti ttidouit,i t a,\ lczilunilrautta.ltceh rrivolrrl br,:r[,ului
,
(Dlrtiirl)r'it)rttrtr,irllrrrslrrrrlrrlirr.,I,,t[l,l!rHilllri,L,ziurriprirr solu{,iiirr,jr,,rIIIrL|
l,jrt;r\r,ni)r lrr rrirr.lrrl lrlilii lolrrlrrr); l') rrr,vlilr,itrl(,r,li,r.rA(,;
r.i r)r,rii1p11,ii
Ih0
1t,?
cutanat a!
cubitql
Gheora
cubitald
FlexoruLprofund
'ol degetelor
Abductcr
po{icelui
(logcltrlor'"(a,lluilr'Iottlolll)
rolol'(fxl'(,rIr.l1)lil()l'(logoi('lr)l
i n)'I(rst,lll,,r'ilslil'iXl'ii
ll cfcctuarrrl tniqoil,riidc cxl,ensicqi indeplrtarc (r'iisl'iraro)a-tltrgtrkrlrr,
rlc nrrter Dirralizati' nu sr: observi tcndoanelo olil,tlnsorilor' (Ji11 25 b);
,,1 destul ,,itringerii miinii (al lui tr'roment) de asemonea alatir, cL (l(r l)rrl
li.a lc ralizi tir,nu se evid"nliazd nici tendoanelecxlonrorilor, niri I)r'(tt'trrl
nent-a radialului extern #ig. 25 c) ; p) Testul prehensiunii uttot ttlritrt'll
mici plasate pe un plan orizontal (a1 lui Pitres). Bolnavul nu pttitl'tr sir'
a,pucdobiecte-,intrucit pe de o parte este imposibilS ridicalon, miinii si rr'
(l(g''it'l(,r' {"
nijmelor falange ale dcgetelor, pe dc altb parlc IIe-\iunoir"
r'i rlrtlolit:,
paraliziei
llcxorilot,
ilce ttificil si cu for(i rcrlusd,nu ilatoriti
rnirtit sr,'
pot
decit
dacii
de
flexie
funclia
exereita
nu-qi
ci,
ace$tia
irpl'ului
:r,fii in cxtensie. In schiir.rb,flcxorii vor funcliona foarte bine tlaczi so t itlit'r'r
rnina de ciltre examinator, sau daci, se plaseazi mina in ii,titutlittcir '.rlc
se rer:narc5,po 1r'r'il'l
lusirciune" (Pitres) ; r) fulburd,rdej.e.-.sen-s,ib,-.ilitate
liu-I cutanat al nervului, dal mai ales la nivelul pr!4ulUi. gpaliu inlrtrrrtsttx
tlorsalsi ruaialcs la nivelul ta bt cherei anal orAiceff;g' 2d d). Este rf irlizrtli
ttild (piin luxalii ale umirului. ftactttl i ittir'llr':rl'
tlr lezi.initJaumgticeti.n.
ef.'.), sau olte prcrcsParilo'e (tutnotil.
brrrrierrrsuiuj
Abductor
Opozant
|^,,,*,*
',': lt )
Interasosidorsali
Interosast palmari
Lambticali iIl, IV
/ i./. 3./, NrNul cubitnl: ramuri nervoqse, distdbulia Dusculali
fi crtanoti.
cubitald.
Crila
ferloriul
cutand
Edial
:
-Fig. 2r. Nelvul
r - r!ri. ,,itr Eit de lebede"; ! - Sequl ,,rasfitnni dertrelot" lF/otuettJ t , - Senntrl ,,std!8erii mlt,il" (l".ott.i,)
.ulirrr
rrrl.a nJrili;tl
ntr se obsenl tenddN'F eteDsonlor it m.i proeminmla tadialtrhi crternj d-T.ilornrl
lr
"
I li! |
lclt;i,.1rrr1r1r{,iorlrl
rlc trr,vr,ilcioricc lrrrrtitrliro{iorrso)
so t,rrcrtrrolt,qillr
lrlirr:
r') l) inlirrLriLlrirfor'{,cirlo tbttrrr:liu .r,cr.riLltsei
cvirlerr(,ilr,Lii,
rulr,itr,lt,sirr l;iirrIrrl
,.ltl.iltrii 1i :rl trr,.r'.,rrJrri
p'irr i rr,.I i rrIrr',,,r lxzin rrlrririr: p;rr.lr.:r,
r{}'r:i., :rtl.,.i
, ttul bulrruvrrl.1.spfiji'i pe mcmlr.rrlinf.tir.,rtllcctrrl; I'l.rlizlu
[rilrrt.rrr.;rl.r
ro llil(luce priu meriiul legi,nat
,,de ra!:i':.
ttt l'orali;'itt t.ei,,ul'rij,sity inleriu'(prio. fueloL.ieti,rlugili irlr.ltir,i ,.rr
,r'r. r.Xl) lt tir pi,ttitltZl:t
pl,,r.(,!Lcnli)
prin LU,nLiit0ll.t,(.lc
S(,rocUnOtstu
Ji.||ll r
;r.rir.rirte,rlc_paralizj nrufchiului Jesier rnare: i,) Iicttrrc{,i1, j.krxolilol
,
'.)rpsAi:b) Dimil-uurr'l furlei de a\-tr'nsica corpseipc Lttzinjq ILirIir,;rr.,.:r
,lrtr.pozilir'lczindi,
ostedilicilf,; d) ln ortosbarisiruoiorn:rprczirrlir,, lri1rr.r.
LIr,lrrzi,.lo-rnhrrrri
(?entm,r, componsa,$i a egaliza contrailil l,rri,u,goriislir,
I,r1;\ourorcoaps-el); c) ijcolioz.i cu concavitatea spre pat.to|, siirriil,o;r,rii
,1,
;
l) Lu{.r'sul-$i
mti s,lesrucatr . scirilor se face cu dificlultaie; g) Itr rkrcrrbil,
i crrl;r'al, dacl se lixeazL baziul bolnavutui, acesta nu-rsi
r.irlirrrr,
]oatc
q|rnb:l de pe planrt1patului; h) la contraclia fesei,so remircii
o itsirn(!1,ri0
1lO COtlUl.aCUe,
s.ctatice
in funclie d.etopograJin
_prezintii,,
ltziurrii, rrrri
. ,]0!PgratjZltlg
rrLllt+j
I'artant(' semioloEice :
tu$1o1 myryh1t91_
garrrb--ei
ai +iciorutrii, realizincl un ;ii,ri,,,.
"qr..
',']:llt]iri"
corrplct rmobil; b ) rUersd,eEte,.Etepatn
f,_
ridicareapc vi|l. tlrir.irr
:,..,,,-,]],,1.
,,:.lrli'1.'bla!.1-yoe?.p:
vjduri
ciiciic
este
imposib[JI r.)tr,rtir:rvl
tipc
.,.,.',']l
,)u
l)r):rr' rgr: ft) r'rrrrizian.rrotici
a
posterioaro
lL uD,llr0j
_ .muqculalurii
rrrr. l.', i*rposibilitateafrexiei gambei
(testsemiologiic
' ' ,rrr1
aetararizi .,rl,,i'iiri) ;
,.r r\ lrofiile muscdare interesor;z;
ri
]r_q-Eq4gt
_"lSlrscriatuxfi"-_postoriol,rd,
i ,.i Inrisclrlalur',gjmbei : tt firlB'ufir-ife
' ',r,t'r.x
de scnBibilirat,.s(, r.\t.rl
tl, rrrl-elnlrntreguluipicior_(cugxceptiapirlii interrrcrt,
l.l,',,,11'll
|lrrrlr'i
| .,, nri,le.'ler fir,lertle),,precum si pe fala laterald, a gamboi
I t) J)c ci,lrr rrrr,r
sciaIicesi,,'tpnnrolc
si-sosilrri-.rzjr
l,llll,: :ll'l-"lE111"
.simpJome
t,,. I,r.irlrl
l , r : r r l l l | l . ] t r t,l ZtU I]l l e IJd ,cu l a f( .
C i t, si i n ce l ,. tt"o n t1 u h r o .
g)
Sr : l r |'l :r .u r ci :
r lrllrtri,ri vasornotoriiFi
_(crleme
g,rnhieroqi atc piiorulii, tript,r,
"rnbritticXii
-Uaf]gs
('r,rLlozir,.
l,
plnntare,
ale pl:lii';i
pi,r,,
l i r r r l s . d , .) .
^f" "iigLiifuii".rlce'.,1ii
iu; fuiltt:ittc
] sint rnuit mai fi,eaveirtc,lrt(,11ri{rrl
,,|oni ttttit.C_7og.re
, r'\ rr ,rcrr-L1jrc
t'ru in trcimer
mijlocie a coapsei fie sub ni]Iehtl tle crrrorgt,lltii
r lrrtirurilor dcstiniite la muschii regiulii
]ostcriouc lr,crrq)sri. 0rr,rr,j,rrri,,
rlr'ri.trtrlrlsrrrnhl-ipo co..psr estein pi,rte cdnservat:i,
i,r,rplriilizil o$tc(liH(l
r"rr')' rir sr riirL rili irL u'.tt:xfrrl cli'ic predomini fie semnelepa.r1lil,i*r
rrr,
iie ccle de sciaiiopopliteuint(.rn.rlrrroiitril:rptrrtrrr
. ]'.,,;.1:llllliJlll,
l*,l,cru.
' ,rrurtn(' nl ri tl lt ir lilr t r nor vs{, i: r t iciilr i: oJr . t r ct . t oi_lst . , icst i||: t lol, r . r : r , lur l', r l]
Irl l l l tl i l nl l ,l l t i ill( r sir |t r loiir ,L0r Lni1rin
, il; r scicl] ledisl; ilr clt .
lt).,\ l)t,r.u,licitt aointiaiWTwfiitc.Ii-iitam)
1s,i ,, ,..t,t.,,1,i tiltirtl, ttost,,ior
Itt trtt' , t,t l t) t t , ) t . r . , llt J t 1, : r lizr llzii, : t r ) I r a, r , lr lizia, '1, 1. \ {) t ilt }r
1i lr ddit ct . t , ll'r
, \ r r l{. |ll, i lI ||lI ir .
| ' r(:| | r| I| | III,(
|| t {( , lt il{) t .I t odl. r , l. iri rjtt r i ga. f r . r r . i ( llr . r ( }r . r
.
u
.tt;rr.tl i ei ;' l i .. r pr 1'lr , r / , i. ; ! . r r r r . r i. , , , r 1, . : r r g,
. . , , r i|, i, . , , 1, , , , , f , r i, , if , Li ir t r r lr r r i, l
rrr| |.rr' | | || r || ,,r |r lt ir . |lirI i" : r r
1,
llUt
,
cr c( r p{, ill [ r , r lir r st t lt t i ( I r t I iI t t r r I O t , ii
l) t r . i0
.r u, \(| l l t rIr.; 1r 'IIi r . llr , r , r r r r , ; r lr r lr r riolij) i lr ) it 'r ( 'r r r r r |r . inI r l, I rrr'I rt rr r,, rrI r r r r
1
l{r I
poil,i,(!
1i plrlsat nici hr addlc,licr-nici"
starp.cvh'firl ?ioiorrlti, (,irtor)ll ?o?t.t(r
rrr lol,rr,{,irr
iltu ni, qi nu poatc sd-fii fle,ctezedegetele: e) },iolta plantard esl;tr
lrtllrrrsilii; d1.1\lcrsrrlcsle dilicil, de alurd tal'$3ld ; ,') Atrofia.i+telesea,za
l''girrrrr.rr.
pl:lnla}i, rnargieiJepiciorului $i moletul gainbier; f1 'Tcndoqgl
'frint abolite
l,.,lrilirln .,s1,odepresibil ; g) Eellexelc achilian fi medioplantar
;
lr) { l1q117xlgigi dureritre de, tip-rne-v.riiicf ' sint destul ile frecvente; i) Une,rli xr, rtrriir.r'ci $i $tergerea lgheibulul retromaleolar ;i picior ,,in gheeri,",
cu tlegote,,in ciocan": j) Tesiul lui Fromunt:
in staliunea intr-un picior, tendonul lui Achile
ri.mine flasc, depresibil, iar gemenii nu se contractfl tle parted paralizatd';- k) Testui ,,piciorului balant') : bolnavtl, plasat in decubit ventral, este solicitat s5, llecteze energic gamba pe
coapsi- Ie partea bolnavS, piciorul rimine balant: l1)l TulburSrile de sensibilitate obiectivS,
sin1, rjecelate pe ta1, plaiitard, * piciomlui
({iq. 26); m} Sopot eviden!idii [ulbur;ri vaso'
ni ricrii qi trofici (edem aI piciorului, ,rlter.alii
ale pielii !i ale unghiilor. ulcere l,rofice nalca-
,i;i='--\',',)\
--'-\:iv
ttervut.
dknhr
' tatirat
lrl;l
zr (lll,o I)trrliolsolxrrrirlllslrr,lrilirrrrr
rlirrgrrosticului
de krziunetroncularil,
lr.rpr.cliv polillotroulari, (polinortrrrpllicii).
Nr lilcbuio sL uiti,m ci, polincvritcle qi polineuropatiile realizaazh
r lulrrrr)Nill:forme semiologice (mixte, motorii, senzitive, pseuilomiopatice,
psrrurlot,ulretioe,acrodinice, hiperalgice, parestezice, predominant trofice,
prtrrlornitralt vasomotorii q.a.), care ne pot sugera posibilitS,tile etiopator1r'rrilo(Iiiscr, 1952; IIareq si Nisipeanu, 1976; Mareq $i Stamatoinr
llttis; l'('rrLlofunda,I976 : fo{letea, 1067;.
l) l. prezcnld unui sindram poline,ari.tric(polineuropalic) cu ilrstalare
rt trli. .ti. str.bacutiine gintlim ln primul rinal la urmetoatele posi,bi.li.td,lieti,ol)trl.t)u(tn(e:
r\ Polinetu'o1tatii, toni.ce {profesionale, med,iaatnentoase,crilninale,
stt i r i il u,yv, eti.lice).
- l?olincuropatia etilicd, est de obicei mixt5,, dar cu predominanla
Lrrllrrrliililor senziti'r'e (sublective si obiective), apare la un ei;ilic inveteratr
rrrrrurli fiind pledorninant parestezic[ qi dureroash. De obicci este leltlrrrrglrisivti. Para iziile mari sint exceplionale, 'Iulburiirile trofice ryi
vosrl rri,ir-esint precoce. Se poate insoli de fenomene de nevritS, opticil $i
rlrr rnrrllrr ori, do tulbuli,ri psihice care realize zh forrn psihotici subacut[
rr,lrri ](ursakov (contuzie mintald,, a,mnezie,confabulalie). Se poate realiza
r1i lorrna pseurlotabeticri) cn algii fulgurante, tulbur5,ri de sensibilitate
rrnd:i [i ataxie.
1rrrrl
* Polineuropatia d,iabetic:d,
cu instalare subacut5, este rarii. De obicei
rc rr:n,lizcir,ziiforma cronici,.
. Polinatroltatio, arsenicalii eeutd,-sub&cutd,
este cle obicei profcsiorrrrli, rlstlizi mult mai rar medicameltoasi'. Apare la murLcitorii care lucroazir
rrr lrriricle arsenifere, in industria pieliriei, in industria unol vopsele, a
ol,r'iivulilol raticide 6i a unor insecticitle, in industria chimicd, (hidrogen
rrlsorrilt, acid arsenios, axseniali). Totdeauna apar iiemne gastmintestirrillu grave, precum qi ali;e simptome neurologice (convulsii, sinthom holelilirlrrr rr,rseuical),tulburi,ri cutanate qi ale fanerelor (stria transversa,ld
r, lrri .Nloesla nivelul unghiilor). TabIouI polineuropatic este mixt, dar cu
lrrrrrlon rinrln!'a tulburi,rilor senzitive ;i trofice.
. PoLineuroytul,iasutrurnind,aautd-subdc'utiieste tle asemenea deoseglrvrii, predomininrl in tabloal clinlc tulbudrile psihice (confuzie
rlr
lril,
rrrirri,r,lit rgii;atd, sau torpoare), tulburiri cardiace) hepatice qi renale,
plrrcrrrr 6i tulburd,ri tligestive (clureri, virs5,turi, constipalie) ,1i hematolrrgirr (crr seinne de podirie). Se poatc realiza,Di un tablou de encefalopatie
psilrolricir,de tip Korsakov. Polineuxopatia poate debnta asimetric (pe
rrolvrl ndial, in dreapta) qi este predominant motorie, cu atrol:ii muscttlrrrrr lilpido.
' .\'oLineuropatiamercuiiald, acutii-sttbacutd'este tle obicei acciclcntalai.
rrrr,rrvolrrrlbar-suicidard,,la cei care lucreazS, in przenta toxicului: distilirlcrr, rnorcnrului, fabricarea lSmpilor de incanalescenli, qi a ampulelor'
lrr,rliokrgicocu trompe cle metcur, industria termometrelorr a barometrelol
ri rr rnilnornotlelot cu metclr, fabricarea sirulilor de metcut, azotat de
rrrurr',ur',olorulX, qi cianurd' de mercurt intlustria farmaceuticd,(calomel,
lblirlrrrrrlu,t;ill, os1,o
J)r'orloninr[rt rrotori, Dutin(l (lobullt t)l'in lritltlotr
tl,itttit'1
irr (nrrlirrl, rttttncttlo-trl
rurrriolrgi<l
tlo trntll,ittottroltlf
, lt'iltlil lroplil'trtt
l0{
r'\l(,t'lt)fi rtri){il)(ltt.Nr.rrrlrisl,lr
ri rlo srrrrurctlo ottcrrllt,lr
4lt 1,irt,llrr(xtt.illl
((.rrstllrtl(!rlr.r'rllrrrl0lts0
llri Jrt,irrr
;rlllrr),
lotr:it'o aat,l,r:-su,lta.at,l,c
(11'itt iuriliri, lrli,lol,
.
. Alty.1nl,,inr;u,ro1xr,lii
lrr.trz'rl,srrlIr';i rlc rarJr'n, trioltoclozilfostat, tclanclorel;nn) s,, 'r.,,<,Irr,, ,1,,,
t.r
rlc
ou loxi(,.1. rrrsp.r,l,ivr,)
','/rf('n1,ul aparif_ir,(la rmrlcitori oale lucreaz:'1,
ri plin asoeierea de paralizii do nervj cranieni (oculrrnolor,ii oplir.i,
.fi
rrtolrleo-vestibulari), tulbur.iri psihicc gi sau semne henurl,ologiiur.
/
tulicd.fste rard. P.ealizeazho for.nii rlixl,ri (r,rr 1rr,r,
.- P.olineuropat.i_a
,
,l''rrLirrllni,.r
tulburririlol senzitive)qiseasociazricusimDtonrcr,rr':rol,rrr,isl,ir
:rlopccie,
o\ l,t,rI
.altera{h uxghiiior (cu striile lui Mees),convulsii, Bi}rrl)l,ornc
;ii'rri.irhle (tremuriluri, miscX'i coreice),sirnptome psihicc (rlirrlrrzi'.rrl
l,r Illl0s1;]ce).
100
1n schiml,
ili,;i ;,i;;,r'i;rrt"J; aft"osti""i ae 'eticulozaparaproteinemicii'
,,tl,it'r1;a,cepricioasd',6t instalr,rea sau agra,valentrbloului clinic (cu
ttlrrz,r,tr.r'I lIrrrrIr';ri/srrrrr,r'r'r'IrlIiIr,,
I rrir,IrrIrrIrr,, irrli)lllr{ii |r,rIrrtrrrilr,,,
lxrrr,lir
Ilulgkltt ;,rt.), l'olilrrrrrrrrl)itliiltl)iLliut{,('l)llLzictr
so t({l los(1r'r'lrrtiv l$or',
lttitt lthlrrrl lrr trrirl; (rlrrl crr trotti,lrtrlor n irlrrrl,i't,scrtzitir,i),irrll rlr lorr
lr,rl rlo ,,irrrplt'gnalo" ttcttcrtrli treoplazicl, cu cvolu!,io prtrgrr.sivir.
lt) I',litturuyuliilr tlcgru.cruti,rc.
Aoi so inculrt'azir ir5rr,-zisir
,,1r,/ilr,
tt it,i" hip, r(n,.1;,.,itamitiali ,.r c,./piliti?; (buofu ly; D(jlrin, sutt,tx\ .t
rrlulttr(ti (t;ptil, lt;dpsi tourjttrr). SiLr b4li dcgr.rr|r':rtiv|ril
l' rl
',\',trrlir.
1rIrrgtcsi-i'r'i
, in care atrofiile musculare cLrdebut distal itiiing ilr rrlo(l In)A11,.
sir', in tlectls de ciliva ani, toate cele patlu rncrnbre (rlul x,slxrclii r.orr;r
stk', bra,lcle,ct'nl,urile qi fa!a). Se inso(escde mari tulbulriri rlr scrrsilrilr
lrt,lc do tip ectlomelic, cu caracl,ererlisociate (cu nlaforilii hiporrslr.zir',
ltini )r anestezieprofuntl[) si eu mar'e atarie. Cel rnai iiilescrilrr,rli'lrrrl,rrl
lr'rlii, b,rlnrrvii acuz; si clureri fulgurante. Un simptonr pirlrierr0l 0rrir,
({'.rt'.l)crlnitu rli:lgnosticulfftti r}e ,,tabesularniotroJic',)il corrs1,i1,uir,
lrrgr,,r
liitile foarte ugor palpabile, strlr folni, de ,,mitrinii, r]]r, 1r'ul0hilllill
r(.r'\-orse,crlc) itr intregime pot fi hipcrtrofiate. Sint prtztnlr'lrrlr.sr,rr 1i
l.rs.ir'uhlii musculare, c-ares6 qtie cd,"sint,cu tolul excepiionrrlr.ir rr.lr,,i
1rat,iile pe.rifericeD) Poliracliculortr:rri,tele realizeazi sindroa;me senzitir,o-rrro1rir,ii lrilrr
lrtale . Di.sirnetriee, cu diBtributie atit pluriradiculall,, cit si (rl,rr)tl('licir,
rlo obicei foarte extinse, putintl gelera tablouri paraplegice sur rrriri rll
ut abi1 .tetraplegice, cu axeflexie osteo-tendinoasi,,cu nrlrt:lti Iripolorrirr
trrtsctrlari,qi cu atrofii precoce gi lapide. Sindromll ile profouelrrrrr sr,rr
z,iliv (cu tulbur[ri globale de sensibilita;be)
ptezintii aLeasclnclr{,1ilt,tt ,r
rlistt'ibulie poliractricula,ri, clt qi ectr,omclicl. Cel m:ri iulesea sc li:(lclr,lzil
;i trlvii cranjeni (perechiie III, Itrr, VI, Y motor, VII, fX, X, -\t ;i I I I ).
ill,rrlilir.r'i,rile
lichitliene, cel rr..u
i ailesea cu disociatie albumin*r.ilol rgir.ii,
r ir r'i palafeze diagnosticul tle poliratliculoncvr,itir t.irrillain-Ila ll'r.
iUU;ilg;ilt*11l
i;lr)litiri
*l*iiii,--:[-l,li'*
I
+.
PROBLEME
DE DIACNOSTTC
Itr TULSURARILE
TONUSULUI
MUSCULAR
*+*#*t*ms[t*f
r{]niilil
i
*fi#jt!!i?:,T""{$*,il:'lf"{'t*:"tkl'k
j'ml*:*+
i*{i-T*l,l-'*:*"*}T*l$i.*"-t
B'lrH":it'il:l:$
;tE?C";g:yj*ti1d;Jd#1,fi
4.1. HIPOTONIILO
MUSCULARI'
t',",!llr{ff'::"t:t'tilt:?{f ;'!'!t"-'ie
l[ e) :
* rrttr,r'rrlizrtlri. r t lt olit r r t t
t o1|lr r t ' k t t
r t t loo l l t t r l i l t o i t s r ',
r t l r o l i t t . 'l l
t r 'l 'l t r -
ii":Hi-""3il*
*:.ql#fr
iil,:i,fi.:*:b::
lli3;*r"'ffi
il
iiill,
:ii*xli**l##ir,r,,",n'lii]*iiiii.!3?i3d':i"il#i3
t','"inrui,s
lif"f*lff "###f*j:":,fiif **,'-ffiiiffi
i:tiffi,"",H#Ti*"T*,H[r..{"3-;1"+$ti
jl,fl],
lf,'(t:ii""-,'::ff;l'l;
i;l*F1;?''1i'hiJt',:3'ff
;Aj"ilf*T,lil,l
,:;ilil
3;
*1
:::fi.li:!i6,:#:;t#f,:!
f::;::
i'*tf
;,;,1/;:,;'"Ti,f
"!i
";fl
i?;j:f##i"+
ltrrffi
d,$gl;ftt*l{r,i.
li;;i;
1[,.*firt1;;[****L:riliiiJ::i:l.i:T,1,,.J
B) Boata Lai, lJnrerrillrt
ll'tl*'#'r;ilt*#illG:!:i'i"":iK:?i'1"1'":TJ:3J
l,""lr;}ir;;
llllni,l.f,i:{'1j.ffi
T1,iii:'{Jpjjt_*i,';#,:lx''
,:,:,.:;,:,iiyi;fiiil!;,f,l:jiii,':,!ij,
liitlrii{iiit'fi',1-:l'itl11ll,;;lx,l,iJ,fi:iL,:":l
iiilfril;li:t
i,r,ir[
iliiillilililifriil;i:
il,llin;f
l*-irui
l(|0
lil',
o x l l ri ttrl i i ,, tl i t' lt t,tf,tl t' i sl ,i tl igrttrrrrrl
lrr,r'rrDii.r r lolr ir r ,t r t il|t ,,ttl :rl l 1I' i i tttl [l tl t,rl ,tr
I ? {l
r.;rlri,1rllrrriIirirIrriisr{i,r,i
llrrriv, rlr',rrr.lrilrlr.;rrrrp)o(sin1;rrrsir,-rrrlrrilii
,,r,oprr
rlc lrrrrcirtci' liiset. 1952).
:!).
l:t.lt'r i nlcl.c aerebeloasenta;ine ( atrofi,i,le cerebelo(s(:
;i. Iltt(.|c tl.is{rofii musculat e progresire.
4..'l's,besitL(forma amiotonicd,).
B,l J{ipotoni.ilenzo,imulNsall mdi gtulitr,locali,zate(tle 1,iplrrtrri;rl,gir,,
lrrla,piegie,l,etraplegicsau doar la citeva se,gmenteale corpulrri) rrlrrrr.irr
,rrrrrilr:,r,'lt.s;lual;; pulologice
:
1. ,ln- najoxii;atea cazurilor, hipotonia se instaleaai, brasc 6i esl,c llrr
liziil,ri tle Le.zittttiale aroalui refler toni.gen, respectiv ile leziutii ntrtlultn.
,.,i pti,Jerice. Aceste tulburili tonice prin atingerea arcului rcfltir lorric
'Ir.rnentar sint totdezruna iinnitate si segmentare, dispuse dup5 o topoglrrtrr.
L rrliculaRi sau tlonculari,. Se constati, qi coexistenla trrlburdrilor srinzilit'r,,
t otice qi paralitice iar leflexele osteo-tendinoase sint abolite (semtr li rirli l
:rrportant). Ilipotonia este cu atit mai importanti,, cu cit lcziun(fl, rr,lojrl
rirri bnrscl. De pildi, sectiunile miiduvei tealizeaz:acea mai masivij lllr
, i(nte rausculalri, ct topografie paraplegici sau tetraplegicd,,
a. [,eaiunile merlulare antrerreazl simultan hipotonie pin[ ll lllon il
tttusoulari qi paralizii (de tip paraplegic, tetraplegic sau mai rar mouoll(lfli().
:l\t'&,rlrnatism?.[e
medt are (cu secliuni complete sau incomplctq t,vcrr
I rriiI prin comolii medulare ) qi lrcnzatamieliarealizeazd,paralizii hipoi,orrir,,,
rrrr atonice imccli:rte, de tip para sau tetraplogic. Adesea debuteiuii ;rr.irr
il o fazii de +oc, insolitil rle un raasiv deficit motor ni atonie crr rr,i'|,.,,,.
' rslco-fendinoase !i critanate abolite, cu incoltinen{.I sfincl,cr,iurrii ri r rr
rrrrrt'i tulbur'dri de sensibilitate. Aceast[ atonie musculari in ]eziurrikr r rir.rI rr
lrr'c masiye persistf pini, cind se instaleazd,ienomencle de aul,orlrr,i,isr
rr
rrrrlulirL, cu respcctivele simptome de elibera,re,cu sincinezii globrrlr.. lrr
, rrlsrrl compresiunilol medulalc br.utale de diverso origini, sa,u irr lrrzrrl
riror'frpctiuni spinalc incornplete,se observS,adeseoriacelagidcfirril,rrrolrrr,,
rlrr trr hipotonie mai pulin marcat[, qi mai pulin clurabili,.
Lc;iunile medulara a.arle nelraxnn(rttce tealtzezzd acelaiii sirrrllorrr
I'rllllitic cu lripotonie. Itste vorba de m,ieliteteaar,tetransoerff $i rlrr 2,,/r,,
ttitlikt acndd,,in care palalizia hipotonici, qi aretlexicriltlotniiri 1:ilrlorrl
' iirric:! 0u topografie tetra- sau paraplegici,.
ln ytoliam,it:lilele
subasutesau tw instalareprr.rgresi,t:ii,
pc prirrrrrl |lrrrr
r r srl,ueazi,paralizia atroficii, hipotonia {iind ins[ nolipsil,il.
!, In compresiuttiientetlulareprogresioe(prin i,umoli tle rlivei'sorr:rirrli,
rltcrxe, pachimeningitii,,arahnoitlitn q.a.) hipolonia^cstc rilrtxl'i irrl,ilnil,ir,
rlrr obicei constatindu-se contrlcturi musculari. ln scliimb irr tir,irrro
trtirrlieqi in tumorile intramedulare, leziunea,pericrliona,lrlpoatr: llrirr,rrr
rrrci, de la inceput hipotonie muscularl.
3. I'eziunile progresil)e spinala posterioarepri,n leziun i ale atnlaqntlrn.
lt,tsllrioare(ale fasciculelorlui (ioll qi Burdach) sa.upr'in leBiuni r(r(li(ut(rt
loxtarioarerealizcazd,de tsorn(lnoa,lripol,onii plin inl,elfln:treilu,tt'ttlrrirrrlh'r
lr)nl{r Olementiu.
a. ilipnl tt,<)ostorrodidllo 'm i(lite poltlffiaor,r.restc rr,prtzlrrl,rr,l rlrr
lrrbrl,nlti nkrsi rr ril,rrt{;iilo cu irnpoltrrrrtrrtull;ulr1l:ir[o stqrsi]ril il,i!1,{r
lrrol lrlriri,.
b, H i.rul;uq,nt
d,t' r t Jihrr lu,rrgi (dt. .nr(loun( Ttuslrtiourt,)?v:u.lththr
,r'r'{r
intnlll('iio lul (x)ut,(fxl,
rr.rrriologirirr t:lrrcpc 1rt'irrrrrl
pllrn sotr,l['i,lrrllrrr
lililo rlrrptol)ti()nr{{rl)(
i{r,rrr ;rrr,llr.lil oslr'ol,rtrrlilo:l,.ll
i,ricrrlriprrlorrir.
rrrrrrr
lrrfrr.rii.Adctr,lr,r.sl,r,vollr:r tlt'ni itou. tt'd( ttrlu t)tii tttuhintlli, ltr lrrrr. irr
(,orir,\lul clirric:r1lrr'4ir, rrrrrr,1rilIrrrrir|Irlrr.
f.{r'girrrlitrr,irr :rr.r.nlr.
rrrlrrlrlir,
t7l
llrt,rL ill,
o: r c r aL) .
l. Alealiunile rlasculttre, ca c1opi1t15in distro{ii1eilusculare plogte; ir,. (rrLri.rzulilu in c.ne se irxtaleazi atlofii importante, degi :rrcul retlex
r.ilc
rllra,t,t),
0. It;:tutlilc
ftttmaliuttllor cu acliune Jaci'Li.latoareosupta dtaxt'lui'
(
prin
intemediul sistemului rei;iculat facilitator tlescentlent),
t t llt ,t)Lt)tLioen
siirr,r(ii iricLr,rJhipotoniamusculard se datoreqte preva,Ienlei acliunii for:
rrr:rtirrrrilot inhibirorii etescendente
(infec-tioase,traumatice, degenerative, atrofit\ I'eziunile aerebeloo'se
ilr coictreloase cu tliversele lol forrne clinice) se pot insoli de hipotonie
o
rrrrrscrrlat'd(uni1aterald, sau bilaterali, erentual crr predominantd'
'le a
p: lu), care se poaLe evidcnlia, pe linga-ptobele clasice de e:.plorare
i 'r,,ritiiziliipasive, qi prin allc probe senriolcgice:proba pasivitdtii a' lui
A rrrlr'6Tioriias (dd rS,sucirepasivS,a tmnchiuiui bolnavului, remarcindu-se
rrrisciililo rnai ample ale bia-tului de paltea hemisindromului cerebelos) ;
prolrrr, ,,r'ezistenlei" a tui llolrnes-Ste,ivar"t; proba reflexelor pateiare
qi
"'o"ttlll^rl;r*,*or, neostriate (coreile tle diverse tipuri qi etiologii, acute
qi
caracteristicS,
hiperkinezia
asooiazS,
crrrnicol sindroa,rnele atetozice)
variabile.
rle
iltensitS,li
lrip,rl,uttia
c) Llnale sind,roatnaaesti'bulavese pot insoli de o discret5 hipotonie
rrrrr*r,rrlrrlli
insilater ali leziunii'
d\ It l&lunite neuron'ilor tnotori'centrali, hipotonia muscularS, poato
Hriti(' irrl,ihritii,numai in situafiile in care sindromul piramidal s-a insbalat
lrlrrsc.dlr si il accsle cazrrri hipotonia dureazi doar timp de citeva sdptrirrririi.in cale asist[m la o hemiplegio flascS,(sindromul piramidal deficii:r,r:rl iui Barr6), dupd, care se instaleazS,hipertonia piramiilald, c&racteris'
l,irrr'i.Nlonfioni'ni ru:rele parali.ai'i fl'a,ececentrale pseud'opariJwical
-inso"litg
si rlrr u,1,xrliimuscula,re, adesea cu distribulie pseuclora,tliculari (dar fd'ri
(meninfronto'parietale
d.e
tumori
unele
rea,lizate
ii. | ). ,r,,,tlo*usculard),
giorr,rno,glioame) sau de suferinle vasculare.
4.2, HIPERTONIILEMUSOULARE
4,2,1. Iliporl.orriilo plroxistioo sint roprezentata la diversa crize de
Iitr orrt'pul ln int.regilne, Iio auumito scgmonto
(ont,'tu,hffd,cliro inturosor.tzii,
u,
oor.Dori0 ii:ola,toti oi"!l'ol'durlll,iirlrr Iunofio i]o rnocllnigmulcontnlcburii'
t{ll,ll (l(l i)l(1.
rtxl,0 <1()tl00Lttttlr.}-tttittttl,o,
l't !,
4.1!,1.1
. I l ipul,otti,il.upu.rotittl,itl rtutt,r'ttul,izttl,t:
|) lr'onnt:ltLort,i,rd,r:qtik4tsic q(n,arlizal,ii (glarl rn:r,l}r,irntr,r.grrrrrrr,ll'li
zirlritl,u $ootrtr(lirlgonot',liza,1;)
sint rcl ,tiy nryorrlo rxtnrroscrrt,prilr lrrrslr,,n.
rlrrrt* bruscil rr,corr;Liorrl,ei,
prirr carrlr,toruloonvulsioi i,oni(x),l)rilt {lut,t[l,n
sorrrtii (minuto), prin tulburf,lilo respiratorii, vit sor]ro1;ol'iirlo a,rxrrrrprrrri
rrrnonl;,plin ernisia dc urin.i in crizi,, prirr mulscaroalirnbii, prin prrrzrrtl(,rr,
rlo ottioei a miclrirlzei qi prin surprinderoa moclificririlor lrllr)(l (Ar.sorri [i
,
1978; Popoviciu .,qicolab., 1970).
"lrb.,
lr\ Marca crizd piliatici poate sd, realizeze o corLtrrrcitrr,il,
grrrrrrr.rr,li
zt,bii,da,r, spre deosebire de criza tonicd, epilepticS,, ar.eo dulttii tnli lrrrrgrr,
rru se insoleqte de apnee, nici tle emisie de urinI qi do mursclrrlr,lirrrlrri,
rtioi de sernneEEG, apare intr-un context psihic revehtor., illr.sirrr;rl,rr
rlr,l,ologia critic5, este ,,neulomimetic5' t, adicil, are o topogr:r,tir: cN,r.orrrlrr.
sj{)ir{ru colespunde structulilor anatomice reale, ci ,,itleii,, 1o otlr lrolrrr,
vul o are dcspre ,,organizarea" Ba corporald,, creintlu-se zr,sblirlo Irr,lsrr,
.,schem5,corporald,'J (Enitescu gi Popoviciu, 19?8).
c) Tetani (si sind,roamelespasmoJil.ice) pot s5, realizezo (x)trl r.rrrlu ll
spasmoclice ale extremitd,lilor (cu spasm carpo-pedal, minil rlo rrurrrro4
ii cu planti, excavati,, cu inclestarea pumnului), a1o trunchiului (orr rrl,trrr.
ciri ale torsului), ale muqchilor felei (cu,,ris sartlonic,)), spnsrrLtrorrrrkr
rrrotolii, ale limbii, a1elaringelui qi chiar crizc tonice gcnei.r,liia,0orkr lrll r.t,
pscudoepileptici,(Riser, 1952; Figi,rd,qan qi Popoviciu, 19?8). I'rr,zr,rr(,rr
srrrrrnclor
lui Chwostek,Trousseaugi Erb, lipsa pierder.iicunosl,iuf(\i,:lrl,(,
,.rl{lontele,modi{lcd,rileEEG qi EI}IG (1a proba g:lroului), motliliici'lr'ilrr
c:rl
lcrrrici qi/sau als magneziemiei, clarificd, dlagnosticul (f ir,glriiqrr,n;i l.,opo
virirr, 1978).
) CrizeletronicedeJosiiposterioariiau fost ilescrisc inilial rlc .lrrr'lisorr
(ll{?1, oitnt de Arseni qi colab., 1978) sub termenii cle ,,cercbollilr.lilrr",
seizurest'$au ,,crize postedoare,t.Apar mai:llos Lr,r'rrpir
,,l,rlrrrnrs _like
rr rr l:r adulli tineri, in special in tumorile mecliane cle fosri,lrosloliorilrr
(1rrl,po un
pulrti,.r,i
Taterial de 1040 caauri de tumori cle fos[ posteriorr,i.i,
rlr, Arscni gi co1ab.,1974). Aceqti bolnavi prezintii de obicci ;i |i'rrorrrr,rr,"
rlo Iripcrl,ensiune intracraniani,, insolit5, adesea si de o r.cclo:lrol i1(\l'(,ilr
:r lrrhisului, precum qi d.e pozitsia ,,ceremonioasi," a tnpultri.
. ln mod brusc, de reguld,in urma unei migciri bru;tu a ca4trrlli, col
prrl se plaseazd intr-o contractqd, tonic5, in extonsie, in opistotorrris, irr,r.
rllpul este.aruncat_inaloi,eu ochii deplasali in sus, mcmbrclo liinrl Jrlrisrr,tr,
irr lilexieqi pronalie. Uneori se asociaz^$i trismus qi incontinorrl,rlsf irrll
trrrir,nir,.
devin-e foarte neregulatH, qi supcr.ficialtr, stnt (lr! i,ill
^R,espiralia
t llrovne-Stokes,
apare bratlicardie, pulsul este filiform, bolnrr,lI I'jirrrlrlorri.
rrrroori obnubilat . Criza dtreazra do obicei clteva minute, putind I'i nro r,l,rr,lil,.
t)rr!ir, .crizd,cefaleea $i vd,rsS,turilese intensificS,. S-au deicris qi lonnrr pn.r
l|ak) da $tza tonioe, caracterizato doar printr-o contracturfl ;la,rrrxinl,irrrl,
l rxrfci, sau a membrelor qi a oefei, dar nu lipsesc aproa,po nioiodrt,l,it,i'trllrrr
|itrile r'<lspiratorii,
paloarea qi cefaleea.S-nu descrisii crizo tolrim 0rr prrrrlrr
nrirrrrn(;ir,
unilatcrali, cu asloct rlo torsiuno a,xirll5,(Va,n Boglorl;;i Mur'l,irr,
lll'..11"t,
oilrrti d.o Arseni 6i oolrr,b.,19711).
Mrr,ioritatolr,ir,cosliororlzo l,lrrirr.
rirtI rryola,torlropontr,u.trrmorilo rlo frrstlpostoriotli'i,(inrloosolrivollrlt,lr\)
rii ;rorrl,r'u
nngt.jfi,rilol;errrpor.llc,
t5i r.lrtrrlol,sl,lilldo rlrizo in ctr,toso H1ill1,1rlr.i
trrrrr||;iot rl,rt
tr.rt1;r'rrlluio
rIIrrrlrIrrrIr11;o
0u 0r'iz0kr
rrpilopiirrrr
it)llir{r(li,iHr,r',
l0ltll ,
Atlotri qi rlrlrr,lr,,lll?lt1 Al'Horri1i l'opnvilirr, l{)Bt)),tl {!lrrt,{!,rto
II il(,I rIr\I| |\I|,
jf po;rl,olrrliltti o fi{uttoltrfn,
r.o ltrr,tll,ri, I,rrtrit,il,
itrxlrtil,iL
rltr rrillrrozii,
1i rlr'
t i/ ]
.* trlsl,e ceroa,sX"nla,sticir.
- Ditrimrt'r,rzii iir cnrsrrl .\otnuului"
* Ocderzl in s (.;r,rltrr
loa,lizirrrlscrrrtirrll i Neglo (rr,ltrr(ii rlirr{rr,lr.).
g1;1111,1r11{,111rivir,,
Ii\(ll r()rr)(' rrrrI rrr(,iirlitr{lt,lrr
ovirlor I'ii rrrlrt s0 t)rir,il,rrlfi
ii uur)r'lriulovr'(!tlc trtiriuili nllivr, t'-,trrltt,l,hr
rnrrt jrr <tttltrrlr.iircl,rrit
t:trirllir
rI rr ttrt'rttlrtr,(lr,rrrtrtrlItti Noicl).
Irr'I,rrrrrIrLt
r virlirrt{iltzlrrcrrrtrlrltrllr,
|IIlri't rr ltri l,'r'otttlttL
I'rtrl)1,,,(|(||||rl|
lrrlrr,t
cirrrllrrrlrrlvul
iortiri ln lrrrrDrrltrr,IritrrItlrtii
rr.r,l lrlllrrr, r.rrrlr'Iilrlii rrl,ttttr,i
t't't
r{r rnolllino l)n |lt] }ioior', cin([ $e lirlicii, $uu oilrLltn{.rge,respcctiv atruDci
r rrrl i{i i r.lir)i'r,
irr:-riote.
'."r'Dul
- Jl,ellloxcle <le posturd, sint exagerate.
' Uitracterele contracturii imprimd, bolnavilor o serie de aspecte
prr,r'l;icularecle posturS, qi de migcare : atiiudine statuificatd, qi,,in sein de
irrl,robure", mers rigial $i_cu alur5, tle ,,fug5, dupi centrul rle groutate,,,
- Diminueazl la aclministrarea de scopolamini qi de substanle do
Lip r[tropillic.
-- Llipeltonia parkinsoniani, antreneazX disparilia unor sincinezii
ronlule gi se insoleqte de o serig de sincinezii paradoxale, ca cte pild5,:
lioxiunca precoce, anticipath a lungului supinator la inilierea flexiunii
rrrrt;obla,{ului.
:. l)up5, teLanizarea"faradicii, decontraclia musculari, se prorluce mai
.
lctri; rkrcit ln mugchiul normal, iar cronaxiile tind sii, se egalizeze.
- In cursul ,,kineziilor paradoxale', hipertonia dimlnui| in mod net.
-. I{ipertonia pa,tkinsoniand se insofeqte qi de diminuare& auiomalisnrrrlol rnotorii, plecum gi de bradikinezie.
1r) Sii nn gitnm combinaliile tariabile de h,ipertonie ectrapi,ramiilald,
ti p irn,rn[d,ald.dtn sind,romul pseud,obulbar,combinalii1e d"e conlrq,ctul.d,si
,lr'.:tltusrnedill d,egeneresaenlele
lt epato-Ienfiar,lare(boala, Iui Wilson gi pseurlo;rrllrrrzn lui Westpha;I-Striimpell) qi tlin d,istonia lenticulard,progresi,oii a
I u,i,%inhen-Oppenliedz
(spasmul ale torsiutre qi variani;ele acesttia),' rlistorz,iila
dt, u|ittttline ilin sindroamele extr.lpiramiclale cornplexc, din sindroamele
din disronia musculolum deformausq.a.
'lcrrl'r.r'ubrir"e.
tl) Rigitlitutea ile deaerebrare, prin leziuni ale sistemelor reticulate
rJlsrrcrxlontedin ca]ota mezencefalici este caracteristici,. Este vorba ds o
r,orrlrlacturi, foarte puternic;, a membrelor, a, capului qi a ceiei, care este
rrrir.jola1,ii,
sau diminuati, prin schirnb)i,rilede pozilie ale capului (fenomerrrrl Lui l\Iagnus qi De Klejn). Crizele de rigiditate prin decerebrare realizi,l,zi, t> hiperextensie a capului $i a coloanei, extensia membrelor infeliol,r'e, in vLeme ce pozilia membrelor superioare este variabil5, (in flexie,
rlir,r'rnti ales in extensie). Se insoleqte de reflexe tonice cervicale si labirinlicc. Il,igiditi.tite prin decerebrare pot fi reatizate cle procese rliferile (tumo|rrlrr, irrfocilioase,vasculare, tra;Lrmatice)care iDtereseazd,incleosebi calota
rrrczcrrccfirlicii, sau structudle vecine (epifiza, tuberculii quadrigemeni).
rr) Arseni (1950) :i, d.escris crise untriculare au a,spectde rigidi,tate
dwtLrelnald,in tumori cerebrale cu variate localizS,ri:
-- '{umori rio fosi, posterioa,ri, (50/6,respectiv ulterior 90/6).
- 'I'umori ventriculare (23%, respectiy r;Jtarior 271):
turnori de
glllrlir, pineali, turnori d.o yentricul al Ilf-lea, tumori de ventricul latoral
orr rlivorse localiz[ri.
- Tumori supratentoriale asociate cu angejd,ri do Iob temporal.
ln gloamele frontale profulrde, care prind peretele ventricular,
ln tumori sau hemoragii extinse pe scoarla cerebra15,, situato bilah,,r'rr,l(henatoame cronice subtirrale bilaterale, tumori parieto-occipitale
lrilrri,rrlc).
I)rrpir,Arseni (1950) $i Arseni qi colab. (1978) cxizele ventriculare nu
rrn r!$poottipic de rigiditate decerebratd,,intrucit membrele superioare sint
rlo colo rnl,i rnrrlto oli in hipedlcxie qi nu in hiperextensie. Pe de alt5, pa,rte,
rlcrsl,oclizc vor)l;r'i0u
liu'oitpitl bnlsc, la sohimbnfc:r,
d.epozi!ie, petrtrn ctr,sri
ltrlczrr irrurlirilco lrolrrrr,vttl
se crrlcii.l)in obsctvn{,iilcptczcnl,rr,te
rlo Arsorri
(llllt(l) iii Alsr,rri1i colrIl].(ll]?lt) rr,iirsrr
cii,i,orr1,tr
rrrizolri
rlo hiprrrl,rrrrirr
prrxllss
lTrl
rl r, i ,trrtotrl r. rr rl rrrri r ' l x li{ lr r l( f l" vr '||||iI I ||r t I r it t l ir lr 't r ii|r ', ilr llil, t r 't t I r lt ' vr tt r
r' l ;rl l i r l ol )r,i " r 'it lr r irr r ; r u'r l, ot r t , r 'lr I iit r r l pt r r r lt iscr ll it 'ilr r ( ir r llt 't t '1( 'llt tlclr it L
,rrl rrt, rl i tt crr t r zr rpt t lt t t lr it liiI r t lt it llr xlir lt r r r ir l t lit t lit r t lr t t i st r lt it t t lr iit ii lt ozt
)
l r, i l rtl tttl t.ti . Aocslc r , t izc sit r l, t lr r lir , [ r {'r r lizr r r '1t ilr '; ri(i 'r l . . t] ' I i (I | | I i r I I r ' ( \ r 'il( 'r r t
i l oLrb., l {}7ii) .
l )rrpi i , A rs t ui ; i ur lr r ll. ( t {) Tl: i) r liagr r osiicit l t lt r lt t t t t r t t r 'i\ t ' t t I t i l t t I rrt rI
l rrrrrl rrrl .l l l i l i pc hlzl pr t : zen! oi llt t t xf it r cr jzo ( lo l] ilnr t l, r , lt ic, it t r r li l, , r 'r r li r r r ', ,
Itrtttot'[:rse taoe rlupit cclehlte sitrrptotntt tlrrtlltt'rt;ttlc(l(r iol](tglliIiir l)l!rIr'ill
l r,i I rU rro| rrl, t lr r llr t , ur n ur m ( , r ! zi :
(lrizclc prot'luse t1e tumolile tltr liosi, posLt:r'iolrii ltttplir,rr r1i gtrrr,'
irrllrrrrili caldio-r'espiratorii (brattior,rtlic, puls net'cgultlt ctr vrttirt{ii trrpirl,
,rri l rrr,crrsualeclela60 120/ m in. r espiur , l, ienet eguht r i( let ip( 'lr Yr r ( 'Slr r lilr .
l nl i ,l r' o sau cianozi) , pr ecur n qi it npor t lnt c m at r ilir st lil i ( lf lr il) ( 'r lr 'lliilr lr "
rrl lurrranianfi ;i fenonene cerebeloase.
- f izele plotluse de l'urlolilc fiuntale ca,rc ilfc(icrizii pt'rr'lrrlt' t t'ttltt
, Lrlrr sint deseori asociate cu;rierderi alo cunostilrtci 1i ctt lttllrttliiti prrr
lrilc do l.ip frontal.
Crizele de vtnl,r'ioul al III'Ie:t, se insolcse de li'tttittrcrrt ltiJxrlrt,lrttrtr.r'
rl rlc crize convr sive cu pierderea cunoittintei.
C ri ze le clc yent r icul lal, er al ss inso{csc de ir llspir ': r ( ii, t t t ir lt ir t r : r
i pirrost'ezii in rflcmble.
'i) Contr&ctur'ile psihogene :
;'lindromul, catalitic (al lui, Kaltlbaun, lt K'rappdin ) Htr t'rtlrtt'lt'r'tzt:tzr
lrlirrl,r.o imobilitate prelungiti, cu durate do ore sau tlc zilo rt l rrrl t rrr t t t l t t t .
(':uc pirstreazd, o atitudinc catapleai,icX ,.qitegativistii. l't't irtrlit', :r,r'rrirlrr
r1:rro orltatonici poate fi inlocLritl de sl,ili de agillt{io, trtt it t t I t t rlsi rt t rt ,t
:r;1r'r'sivitete.i,ipsa sennelor neluologice obicctivo, pt(x,tlrtr \'i t rtIrtlIctttI
trrrrr,i.ionalqi pasager elirnilS ul gindron extra,Iit iulli(lll I siur rtllrt irttl,
rrlii olg:rnicd, a, sistemului nervcs.
'
(lontTactx$a (hiperlonia) piliat'icd, se iirrpurie oi} tlll (r])i[r'lr(]frl,tt ttrlt tttL
, r'rrt crt semiologjc crrncieristic cu ccloraturS, nevroticil.
,1.2.2.3. Contt&atur'il.ere.fLere,locale pot sit apari' itr alltilr', rt,tlttrirr'.
,lirllsu adec.tiuli viscerale, precrim ;i in unelo sittt:lrtttrxr t,rt'ttzlt,lgic,'
tji il
(lrttl{.rlttl
,rfir ziBul sindrom extenso-progresiv a,l lui Sic:r,rrl ;i llrurr!.
,'lirri(1 r.ste I eYela,t0r'.
fl
ir.J. l'liolr!,l,li\ll,i
l,l'l'll}l'A'l'l)(il'lNl(i
lrl,l lrlA{iN{)s'l'l(l
sl 'l\)l'{)(illAIl(l
i r l t r lllr r ill
i rr pl rr,,l , ir llrt t t t t t ologicii t llr t gt r oslilr t ll t t t t t r i lt l, it r ii slr lt lt zr r : t zr lr
trr
p"
r
'i
li
t
r
r
r
ot
t
lot
t
lt
t
t
',
rr"r' .rtrrc| ,r' It tlti t o1t r it t lt l lcslr lclivli ir r I I r t t ll'ili t lt r
r, l c rl rr l Irrott t I llt I r ir r t r t t t t 1;
si I t ' r r t t t t t 'r lt t l t r lit lic.
6.
pnosr,Eurg
D0DIAGT,{osrrc
IN ATAXIi
SEMIOL0L}I0I
I r I rI I I i i (rri i,I r ) ,
i i .!.1. A l, r t {i plir r lullr r r r iir i dr , sot r sihilillt r r plopr ir N'r 'plivii ir l\ r 'l ir l
,.ri rrrri1l 1l i l i , r 'icr rsr t t t t xr t t l; t r t lt cr t t r it t t t 't t 'r 't t : t zi,lilikr st r r lsilr ililii{ii 1I t I r I t t t r t I r '
,)rrri l i rfIl l o,[i it ( 1 00t '0llt t r t l it c{'sli( ) ]lt llblllili pr r t plilxllr pf iVr r . r \ t r t 'r t si: ir r i r r ''
i ur,Il i trl l ri i r,l rlor t t egr r idclt : pr t ; liir ilt '; ir r , r lt u|ogllt i'it 'r 'lt t 'ir t lr ilii ( ut 't t llr t lt zr r lr r .
l irlrl;r'rt;rrisl rti t tt t r. r
I r , lr, 1)lli{ri,ilrt rlllrtnilind la mctn}lnrl,: inferioltlc)
'!o
r,' r' rrrl ,l 0fi vililiikr lnot or ii. [ n 0lr t t lilc t lisr , r 'el( ] , pr ohclr lni if r t t t lil't {'r r I r lr r
,,i l rl totl rxtl i ti t: ust 'l; ili. l! st cir npr ) t t lr n1, ( lr t r ol, ; in t r 'i, t nilt r llt t l cslt 't " r 'r 'r "1"
i r r r r ir l' l I
,rl .r i i rci i tl e lir incl'put nl i) cost eiil:dir coljI ge i] r llliiiiir i{l r r ll, 'r '; r lr ir
r 'r' l
,J!l rl rl U l rl ri )ttar vllrti't spct c'r , ir .ou
e, im pr ) 1iil] 11or lcvil{, ii ir r r iit 'ot r t 'lr rsr , r r r r t r r 'r
iI
I
I
I
t
,
)
I
I
I
I I ||
lit
t
t
'lr
't
t
r
t
'r
t
l,
in
sil
lL
:
11f
il]
.
i i l rrl i i :r-rk: ir cll
llr [ t , ] , Lo int r - t ul sot ls
,.rrrilrlirgic{ri,t,.'laplu1 ci ve{1ereii,corcstelrzintlLlbrrllii'ilo tle crxr|riottrttrr Drirr
l]| 1rr',
rp; ior':cepf is fi cir, ocluzia, oohilall' le agr|lvl::t'zii l)itt rtct'rl' ltrolir,
(rriil'rrr
rr',rlrr lrti Hornberg cste pozitivil irl il toalo plrtbole rlo rr.l,rt''rirr
,' r.rrrrrchi ,pl i lnl- ) ar eiicilloiir ilui pc cr ellst l! t iLlici, ?r ol) il, cor cillui, l) t ol, I i! lr lr r
l i ri r,.i r,)oi l uzi. l ochiir , r rr nlir elt e cvjdent ( r t r lt : oli chiat t r ot t sir lt , t r t lr il)I r t llr r r
rl0 c,-{rt,:i0u&tit.
,,!(
i i c rn:l j it sociazi' cle obicei li bilot onic m lr soulr r iu si, r lt r t t t t r ll"'t i,
sitiii (lc i]sotll{)rt(iircttttsrrttittl(.rrl,'
rr iL.lier clsi;eotefr[iiuoe,si,, fenourene ci-!.r'c
pt'oftrntle.
, jri i t irii ciiilot selsibilitirtii
ilsto important tle relinut c[ lipsesc amr)tolilo 1i ttisl'rtgrttttstri. trrl
, o, iliit':r, e$te Iloln][1i.
:j.2.!.j" ;\t.t+tLitr,ilLsolitti d,e drelleaie osteotend'inortld litiioij t I t rt r;r I , ' ,, r, I ,
rrrr lrlcme cli;rgnosfice ;
t. Poli.rir r"iti,le {. 1.talineurol.tatiifu.Si: insolcsc 1i rltr irrirrrsl,r'zii,rll i'rrl
,rrr':ilt titr stn$ibilittte oblcctive cu disl,ril)rti.io p1li{lorllil}ililii t rt I1t rtt rtr' I it ' I t
r lc r llli
rri i i ' ).up(r' l ioiit lc,ci1,li piot ulll1o) , t le iilcf ler ie oslic( )1, ol] ( lilr r ) r r $il,
,,iir. rrrotorii (i[l iicterist'ioe, ova'l]tua] isi de aiil{}1ii. []tttrlrt'i tilltsivilrtl'rrrr I'rtl
l,Iriirilol i'ie scnsibiliti],to profund:i ;i il itLlr,xici Irr:rlizr,rtzri,
,,pscrt{lo I'irl}rlrrrl
pr,lilrlic". .Durerile la presiunea fira$elol ltlllscullu() iii lil lrrcsitlt tolt,1,lltrrrllrI rl
,il,,r' rrervoase sin1, consttllto. .A1bc somnc (li[ ctt)l,()\t'lll s(rrl)iologir' $rlri
e1;ioktgio.
r l i l(' li';rftru. stabiliroa diagnosticultli
!: Po!,i,rtil'icutonet)ri,tale lrrtruncso irr trrl)lolll sotttirtlogitr, 1rl ltttl;:r
trr,rtirrrli r,r'rr
,.Ir.rrr, .I i i;{i I t I gxI.lIse atr]l,oriol,pozitjivital,e& scmne]rl rlti ckrrrgrr,{,io
jt it r dr {) m lr l ( }llillir ir ] - ll: r 'r 'r 'r ')
polL{t
r
t
pl
;
ognot
uonic
r
r
licir
idi,
r
,
rri
nrl
|
otnrr
l
;i
l i l t,rl tl .
il. ;Jin,thonuJ meduLu'rtlt Jibtt luugi (d, d)nl t,tt: po:tlcrio4l'1r)srr trrrt:trr
I I'it (rrl
Itt tr,t::tzi\,rxtrlttsiv pI'ilt l,uIbulilri tic sttrsriLilitrrtc pt'trluttrlii (()lI$1,i1I
it
r
lir
t
'ir
r lr' , t rt')r r
t
r
t
t
t
t
r
br
l'llr
{)
x(
t
ur
jil
ii
lit
,
(
pr
r
r
llr
lt
r
t
inllt
t
l,
l'i,
st lu
rrrrl rott1trl i l , ii, l, 1xic
t r t t t t ir 't t
l, .iI $of , ( , r lr t t r r I il0 llt I ) r c$it lil( f r ,t t t lt t ^ioI ot
.l rr rrtr' l ' l trxiiroslr 00- kr lt t lir ur asii,
l rr| r. ;i :r, L| t t t t oI t it t tiI ot lr ( : lvi) it sr '' lr l'( '( t llllli1i l: t , Lr l0t r gll{iltt 'iir I I 'ir I it r iLt t
i ) ' l \t,lnt r . l,r ) : lliz( lir zii'col t t t : t 'i lt r r lct t l' i, r r lt lt t t rt lr r r ir r lir t ilr ( ii,llr r lr I t r I r r I t t t r '
( j l l tr r .r l l : l l tl t\i r i r ( i l l :t,ttl l l t'r i tt ti i r :tt :r l l r r 'i tl tttl tl r tl t' l tti 'r t tr l t t"tt
116llr1;i9lt,trr,
t' r r r '{t|t
p l |zt'ttl l r
i l r . r r r r r r r l l u i i \l g r r l l ti ,o |r r r |Ii r o tI) r l l l r f( r l l l tl l i l i !r 'l l l 'l l i l l t tt
l
t'ttl
r
i
l
I,'Ittt':Il
t:t
i
l
l
i
l
i
i
r
l
(
r
r
zr
i
l
r
l
o
l
r
i
l
l
i
i
l
l
r r r , r r i r r 1 1 r . r ,lp r '( 'r l r ( r '.
l r tr '1 i tr ';ti l ,
tI
:!. llcrsuL cstc ebriosr ezita,nt qi titubant. lJolltr vji lul Pr)l l)iisl rrr lt'rrii
, rrrrl{ri, in trinlul rnelsului, ci deviazti ii a,ubinza do s ustol lljill,i{r llrirtrlrr'
I r, r' rl r :rnl ,t t lit elo
s'lu r et r opulsia. I r oba r net sulr t i it t slt r a. r it t r it r ir l r
1r ,i rrl l oi ' u1 vt r st ibular , I oat s ?la r elalii p: lt o1, gicc, bolr t r t vt t l t l. t 'iit t r l r r '
r, ri rottstanl de partea leziunii cerebeloase'
ii. lr eftijlrl ,,:i nlStugmusuL L.r,un cerebelOS intliCii lcziLLttcrt,t urt I t . r i I t t r rI 0 I
, r'r*lrrlo-vcstibuliile.
4. Proba tlet:ieri'ibra,telor. Br*lele tlevia,zil dc- partcil ltrzitttrii rrrrlr'lr'
l,)irri', sl,u i1e partca emislerului cerc,belosccl mai lczlt.
4t.. 't'ulbu,itiri care se ea:plicd, ?rin alter&red a,JerenleLoryropt"irtLttplirt :
l .H i potoni*'m 't Lscul&/ ii. Secar act er izeaziipr inllascidii'r t 'l; t 'r t t t t r t s|t t
,lru ii. llicLtm ;i prirr aroplitudincr exirgerat[ a miqci'rilol pllsivr" lio ' '
,l',r{"'2,-i,prin uir,ii, tr,erele plol:c: ',t').I'a mobiLizuTectpasbii u tttttt l't'ttlttt
:.,t
rttllo-.rltlrirrtrri I lrt
1,,'riot',"!e atilge cu uqurinli, umii'rul cu articulaf ia
t,ru ltra.xiurLileprriiTe a10 membr'lui inlerior, se polltc atingc f.srt .tt .itl.r
rl. i,rl flexiLLi*it coapsei pe bazln se facc c* mtlt:-"t'rrqllri1riil'!'1i tlt' rttrr'lr
,lirr* oxagcrl,ii i t ) itintei,sia mtittii Sc lacc,ostc lilnit. lizi,l,r1i.ii (1rt ,l,'
,' i ,, ,l tl Trbo p, . . t "iL: ildt ,uii lui l3ar a, ng. I m plir nar ca ut r ct t t t ilt r illi : r lilr r r ''
r' , l t,ri srrrir t . , 1t L, r r t hjt r lui la un colebillos in sll! iir r it r lt r r 'f it r r t l: t r l'l'r
rrr,ri rl
, tr pi Lr : 1. t itlr ohar ': i excur sii r r ui am ple it lo t r r cr ut lx't t 1uist t lt t li, t r lr r r
ii rrl:r!,ii iiril irr Il o -hrtlnerillia ; e) Probu rcziutuqei' ,tt Iui lloltnts '\lt tr"rtt
ll,;lrri";iil cstr: iolicil'at sil frrci-lflexjunea :mtebrallrrlui pc btrr(. lrt . L r"
l'rLlttttt '
.tit
1,,',1,'r,t.lu itron ienl Ltl in c:r,re dtitn dl'utlul r":utebtLi'1titlLlir
ii I l lr t l'i picpt t Ll or Lm ir lr l ( r lli't I it 'i r r t lt i lt r llit r lr r l"
i ,r(l i ,r' 1,rr
tl { r liir iuir
,, i , ;. tl ri ::1ii: ! i [ r 11]t:ll11or
it ii liliei- int r iir ii 1a t inr p in 1'ut t r '! ior t ' r r r r lr r r lr t r ! r
,
uux clt t 1e t liscr onom cl; r ') c)( '\ t t t lt r 'r 'l'lt ot t t r r ) r '
l r. rLl bLt t : r . r c'er L{- '. I }oiil1iii
\ !' trrl t(t' t' e . f l?, r / 'lrpit
, r t t Tt t Lar r . 1) ccllt t qit iilt t cllt r t t lt t i ir r lt t lir t t t lit t t t t ir olt r : r t
,, :rl i 1turi r ir siL,1r t ;git lt lbole at i. 'i'11, t l*Lt : r r r r iiii r r t t n'llt "- r t , l, t r li: t t t 1r ,t , , lr r
l L.r
i i ' i o si't it , t il lnilciili iuei ln4llo 1i it t r t u'lr t li lit ir lt t t r r t i t t r I t ||i I r I t L'I r r
1 ,r Ll,' 1;:',:'i:ciri.:,,rlttr-iiI !) Praba tisl,n,t't,ricit'onift ( l)]itlltitttsrrtr ri lr"rr
i; i ir il lt r r t 1) t lr r t sl'rlrtt t t r ' r l'
ii f it lio( j r lil ) cl( i bt 'r t 11lr
,' ,,;. j c i rci't lr ir lt r . r , r 't t iL.'si
'
,,,1,1,, ,,r, * li ; r , jr it is ir r lir izi{ir r ) l. iz( ) t lir r li. l) t r plr t i, t : ir lt 'zit t t t ii r r . t r 'I r r '|. 'r r, ,
,rti rl l ' orrrsllt t ir : lii, r f s{r l'it li( jit liaislist lt x'ilt r t 'l t lt t Lt it it L'\ t r r r it llr rllt llr r t t t r t lt I
rl l ri pr,i trr ir l, r 'iasi t lisclr t lt ot r lt l, r 'iir ,pt it t . iI t 1r 'lilt 'I t 1'ar t li"i ill I li r r r r L
,, .r' ,,i ti ;i , ilor , ( , iI iji liiln) t oniiI t ir t isou] illi.
\ |l | ||('li g,at]'tbet.
',
, , . ' , !':'.:!':
' r,| ': r:, r ir i ( . c t c t eos i u ti tp U x e to a l x i t(.ti i .i i , i n Scn.u I C ri i l l p | i rnu l I.i mn face
rrr .rrrr. rr'r { ar ir l|5c r p e l l rz l rl c u n rc ml j ru l i n f| r.i o r
t,xti ni qi i bi e i n rl ci oj l er"
i I i ) r : l( , i r ' \ r unc a g i rm h c i p e c o tT ]J i ' i .
rl1. I\.olxr, ind,ice-nas. Li a_ceasid,miD&r,re so observi,
cri ce'ebelosul
dii;;;;
::.' 1.' u,l, lr u; r r it i, inu'pr u. t it t cr t lt r t , zil'iilt t t r r ) l'l{) lllilvt llt r t r 't t {ir t t r lr r I t t t lr t 'l'
I iir lj<: it r r r lt r lr r r 'lLr lr / ll
tl r(.r.r/i tt,. i rr 1r t , t r r . , i, 1ir t r r c, , , , 11i- ioI cit
I ll'rot
, 1lr ii t t r t , lt i, si.
lt
r
Nit
't
r
r
lr
t t t l lr it lt t : t v t t t t t , i r t r ,
1,
r
,
.
I
i*lr : r 'li
.,1r,,rs.l i .i l, ii; r r lr 'it 'l't r l sli lj
,,r,i l r poziiir ir t i( ir r lr i, ci r , iir r Lr r rl;, r r r r i r r iyr , l r t t r t ir ir I illr I ; lr 1 ll, r lt t r r t t t l lr t r r '
,,,,,,,1,,,, r 'ir iir r r i,lr r r r t izr r t r llt llt , i{r lir illit r t l ro l t t: t t ' t t l t t i r lr t : 'i I r lt llr r . r l"
'
,
i ,.l ;rl ;ri f,Irr.r r r , Lr t li lt r lillit t t r '. lir '1'lt t lllL l"'lt t r r vlt t t r 't t llr t t t l t t ir lilr r r r r : r r t r
lit r r r ''
( Lt 't t t t llr r )
,i l ' r,,t t t r st , li, 't lt t i) . lt r t t r lit r 't t it t r r r li4r ur ilit
, s i t n; r i lr r r r lr li l J r i l l ( , o i n f C r c B t _ u
ou,lUClCilOr
,1
t.l
lll
c lini c , p e l t n . q r i s e m n e l C r , e r f l b e _
depeltlr.bd,rilepe care.te.tletermiin.
r,a c6piine gtndim
l.:,1]l:.ii]1119.li
ru
Iixrl ]-l
lt urr mcduloblastom,
Ir,rrrl r| [rH ,i tttllf ot t t t ll. t t t lr 't r rI t it I Ir rt Ir' I i rI,i r' ; li t t t t l'oli ; lit t r lt r r t t tt l0 llllglli ll( llllll
r l trrl rt' l os' (,\t'r ir ^t t1i
i r r olr t lt , I 1) ?'1) ( lt 't r r rt r t r t 'xl't rt lllt lht lt l l'( 'lllt ll t liit gr lr t $lr (
r ir, r ! r r , r r lizr r , r rt r, r , t r 'lr t loir siit t t t r lr r lot t t t it t i r lr '
.rl . l ' i rIt,ri l cir , i r r lr cr lulor r , r ir r r k,
,rl ri r:ri i rrtr tl r ! . {r , t r t t lillo,
l, il, ll gt jllt r l( lilziit lr r lt t ' liit t t pklllLt t t list lt r 'l'( )( sl'll|t r st t lt
,' r,rrl ;r, rrsl l trir i . . i sr 'iiilcr t it t gt r 't t llr ir ', r : ellr lt 'r ') .
l ' ..l Jol i teclem 'ial'inizunLa( i, t t t lr t ost t 'st t l, at eu'm nl'LiSt li) t r r lt r t r zit t ir ir r I t r t r
rirrrrihr(,lro lczeazir,ccl rrui tt'o0yorlLcetcbclul. Irrt intlivizii l,ilL(\fj' lll(12('lrt'ir
rrrrri siutltorrt ccrebolos ()u oYolutie lentir, qi ml,i Dls$ ou pu$r)uli i1i totttisi
ri,ti,ii, l;otrle:r,unasuspiciunoa unci leuconovruiitcr lIIiLi rrltts tlrt.rt' rt''
'iiii
si simptomele ,,iiramidale Si vesljibula'rc" I!xistii ittsri,'litltrtt'
'rxx,iu'z,ii,
i,,,,,t,,jiorr'"".1c'scleroz,i inultipH, in cnre sernnolc coriireloa,so l){tL (r,ll$l,i
I u i rrruliril yl'ttno singllrele manifnstd,ri ciinice .
\1. Afeclittttile rasctdare a[e cerebelul,ui
('lr'zlll'
l. llenmagio cerebeloasd'nu este chial asa de r:*r'ir, clllrl slt
irrltir
ptirlrrtr'(!
din totalul hemomgiilor
, ir rt.urizentin{i: de fapt 10-13%
(iorn'villo)
l{l]';ll;
1960;
colab.,
(McKissock,;i
,,.n biale tltpl, uneJe slltistici
|rrrl
tlrl
ccrc'}{''lorlsc
hcmoragii
multe
mai
1942).
Ce]e
\lil,diell 1i,i.ngrist,
olrsorvttte ttc P"opoviciu qi collb. (1980) in zona de vasculaliztl{ irI tt' lrl't't'r't
., r' r.lrl ol se t nLer o- supelt olr ( .
debutul brusc, cu grcluri fi viirsil'tttt'i lrr
Sr Do&t.r recunoaste tlulft
(
azur
i,
l caic se lsocilzS, o t r iadi' cat act cr isf iclr : : t t nr t t '
r,,.sl c 90V din
i ,.' ..t ci oas" ri*"t n, pr "r lir i, pr iYir ii ipsiht er alc ; i p: r r alizic f acilr l{ . 1x't 'if r '
I rl7
(lrrrri
(irLlirrlrr.r.irrtrtrNsil* rrupi,oitevazile (in formeresubacut.e)
. ir*^('ci(l.lr1'
lrr,lrrrzr'i,
r, sindrornneo- sa! paleo-cerebelos,'infi;;1ri; ;;"I"'*ilj
rirr'|ir Ir(rIri rr'| rrrrrI rri (Arseni5i corub.. r g;4r. s'. po, t.'^*-cra
sLazaoaD ar:i-ir,rrllorrrul
do' irilal,ie meningeali,.prr.cumsi ;-";
pir"*;;;i;ili--:;1;
.'
|., | |ir r.( r ,I rrI f r s o. r nD'd. e tn t| rc l ti c e rc b ra l (Ars c ni
1i col uh., i 9Z4). E xj sti
ci
e\irut run.in'erapi.t.indnoseiri-;;iJ
l:ll,'i:l;
.'l,.llr::'n,^"_r',:,:,11
"rf" gaJ? OcCipitali,.
:r|||liirirr(,rul'
cercbeloase
";;'rJ;"',
Alteori
bolnavul igi"revine
] _
,tllr :l ')r' r r.Urn:rloasii
inili:rlr. frri a pfezetrLl,
Scmscpret m,rri
cercbeloase.
(., (l,rpii r.ircvazile .A aparii iemne de nip".i"nJi,rne'in;;;;;^";;.i
'"r,r'r
jt",*]f;
T":rrt,il",f
H:",1,f,i",":;ff
:i*:F:lt-,""""Xi:?li"
rrltlii:iffi
r',r\'(tir'.rru.ui hemal,omcerebelos.ri" ;;l; ;;i;;lti-"Jrr
insl e'olufia
('iri r.rr- p.og'r'si'ii,.aspectul
crinic fiind asemi,ndtorcu cer al unei neo| (,r' lll l I I (,cl'('r'e luJia ( . . lO f
in: t llSCU. lut Um , J r al; ! r r ) .
ponto-meze.ncefa,lice
(popoviciu
J.9l"tt"ooit
il,J:,i,fil]:.Ji,l:y"I"t
r:'nrJ.rfdure sanu_urtamt:,ptur ci, reziuniburbarecu simne si cod,t.j
cei,ebeloase
,rrrri,rr'\r,
(.tl mar Rdeseanumero&Sesinalroameischemice
ale trunchiului
(sildromul
arterei cerebe_loase
postero-inferioare c* r,',iantele s:rlez
'i'r'r1'll.NI
lrlir'e'ran-|-b,'nais,
sind|.orrrul
tui srbin.tri'.r'rg,nrtc, -rndl'onrIt
,.i,',"lll'.':'l']
djudromut trri pi,.rrr, Ilarie.Foir hrr ..h<,miprr.,.z,r
].ii
l:,1).]"':"u
l..s1rn.
. - \'ezi cJp. l), intftr-ir Inlrelgd jligJli.
,, r"-r,,.lo;,{,1
i, ..rcl.;o!ulrii e"t,.
.,\rrrr-,Ulr{r, l,rtm u e cot.cbelo.rs|
l'jscuic Ltio lt"uo(biltJbazil:r,. sc nLri
' rrrr's. r'irn.rismentere cerebel0ase bilaterale trin trombozcre vertebrcr,
l,rrzilirr(.(l)oloyiciu, -pende{untlasi l?ascu., fOSO;
Scotif fO6T a,, b).
ll.,:LtroJii.le cerebeloase
/. \r' sirrdim la o otro.fieaercbploosd
seaundord,s[n$)lomalicd.t] nr(.
/' rrl.r. llrll lurrc.iLnrlrumcclebelos,carc s_ajnsl :tlal la un-bolnar
ti care nLt
rIr' 1risI ii rrr,.rrl1.iiictul. et,iologic, dari la,care eviilenlieia
in antecerlente un
r:r'l|t|-t. tocTlos.roxl c. lraumatic. r,lScular,ctc ., po.ibit gencfttor
cI corr_
c.r.ouotos
si, l:r i.i_Lrc.
prin jnvpstigdliiJor.for.turfo1lncn.
::,)
:il]
I
illll]"1?i-L(.
r.rr'.( { rirl(rgtallc,tomogralie arial{ computexizati,l s_a
eviilenliat ;-trofi:}
l llr' lrll
ul ui.
:!.'ltroJiile
cerebeloose
pritniLile :
ered.ofamitiate ne sint sugerate ite intervenlia,
.. ,,,.,::.).,,1,!.,f
.!il:
-!t!:!il*yt
nnot
l?clori. gtnefici. As el. se surprin.le caraclrrul crerio.
' \ rr{,.rrr,ir
,ir.
ri||r||ri||,(lr,Dt
.ut i]r'cloc j0 cnpildrioSau In-adolescenti.cvolutia bolii erfe
|l'trl Ploglcsir'5,,iar in conteitul semirrlogieo,pal n*irf,rl.t
si alte elernente,
respTtil-e:-. pcta^la
tui. frri,ed.rei,ck
tmphcli'qi l;zi""i
:.:l:.:ll
f:::l-1,1:".,lglli
,jl:,111
tulbur5,ritrofice._ Hredn_ataoi.a
.&pinacirebeloa,aA
$i
1.,]'-1'l
l?)r"froarc
t t l l t.t
.{ C rn n r,
rttr t ' e J A 41L.itds o ei rz i L f i
p i U n ti d a l e Ji , cv{.nLur.l ,i l emeul (. l rnri ,,_
lr,l r((. ( t nl r ) ( r ilf iLlur ( h u | r,r,l . . I)i s i n e rg i a o e rebel oasi mi
i , oel oni ad u, l rti
l.knnwy Hu,nt rk'.ltrttrlzii clt tlizc rlo r:$ik,psio ia,l .sindromul
cerobclor,
rlt,irrrt,,s,, :riirxriirzi,
qi oi rriiocloniit,"liizlt,, la urulrhii
ill:,'::,'1:i,
l":,1r
r.r.r fr .r.,1".
lr{
rrr)rr'k)r'
rr-rr1x'r'irrir'r.,
int.r'rrrrr.ir:rri
Ir','r'rrrrr
1i .u (lr.ir.r'ir,rir.rrr
l|l1,]{r-f.rlvif.
r8 0
.tf.rolta
otrl,od(Vtltt ltnxd,
ltti
eoft]on_tItlittr,$
rlrirttlr.rrz,i
l.
n to l tr l i t'
180
alolosuDrerrolor.
ttinjurul_trasusu.rui
si
l"i',i,;lliJ,ijii,.u':tili,oo"_T$'f;,lt
-famiiial(cu tiansmisi
rn(. .rrt(,sorulu
olo"-*;*ti"11?rlter
'cr.csiv*]*t
'"^iffi
t;:"#3"T'fi
li{.i:#-Hffi*
:::tl:l'lt:ffil#xtrall,#ffi
t"*itix'3;Hyt3:l#ff;
:"3lidl3i#5#ft
iijijiHilF::::;,,"i,!"
a lui Dennv'nrowq;
dnexaeae
iii:.ilillii;i; Affi'#-1"Xt'#ignetizare"
i:',"i.}}"x'ffiry**ili|I';
r{iti'qT#{f
;J[Iiugsl$',1ffi1"a,i'fl
ei Botezi
r1);)t
i srsorqi cora).r.,,
r;r;, F.ff"'fi
F
O.
lt'tspl'ttot,,otitlt
DEDIAONOsrlc
PROBLEME
INVoLUNTARE
MIscARILoR
"ul,Ti;lh,t?3t;,.Fradis
6.1. HIPERKINEZIILE
Sint migcx;riinvolunta,re,rrariabils ca aopect sorniologic'
r,rr,topogufie qi- ca eti6patogenie' Majoritatea aoestora sint tle orlgittt'
oxtrapira,rnitlalS,.
xtllt
6,1.1. Hi.nerkineziibruqte ;i clonioo, fir[ dcplasdri sesmenl'ar'('.'
limilatc'
r.u deplasiriiegmonlaredd obieci
(li)r colllli(lllr'
l. Mioctoni'ilasint eontra,cliirrusculareinvolu-ntat'e,
sittcrottr'
alteo'i
rsincrone,
1i nlttr.
uneori
r,.u*ia,J" iil clonie,arirmicc5i
(c.vt'ttl
ttttl
un
rnurochi
la
numai
sru
:nuscula.
lr
un'lascicul
rria"."ii-iiri"
0{)n1trt(tlllr'
cu
mai mulLc grupe muscutare).Sint asemlni'toare
i,fri*t
fntctt*itnlt'tr
"" ptoOrie di e^xcitegiite
electticc galva .no-tarariice'
ino..ri-u
tlo .lrt'
intlivitl
1a
individ
tle
foarte'variatril;
este
iii"ii"" mt"'J""ii
_la
fr,l
'i
iiir'^iai" rr"ri;. u"ele sint discrete, cle micii, amplit.dine, f[r]l 'ir'i,rrrr
r'tt
pntinclu'sc
oottiittttlrt
lespeativcl
corpolale
il,, ,lellasarea segmenielor
:trn1tlt"
tttlgertrtoarc,
sint
dimpotiivi,
Altele;
*ui-cutu"e.
i;,-;i;;i;tiii;
s'egmcniet'corpornlerespectivo $trtr('lrirrl
;i;;"r,;;r.i-;;r;lor"
-eiirix
ritmiec, sfereolipc, conrinut'(ttrirr'll"
rnin6to#
-o,lu.nt)
iiifii:*,ii
i
t'lottit'r'
"J"p.
carepot produco (lorctl'?o!:'j
mai
a,tnple,
mioctoiii
ii'ril"te;;
9i
mai intense.
musculare
"
au remalcat Ga$ttuutfi colab (l97J)'
il;d
cum ne fune dreptrr,te
'reprezentatmultd, vreme o. sut's[
dtt"t'rt:rl'ttzit'
,*,naaoiii d'J,ffiucro"i"" a
ltt st'ttvttl
fie
utilizat
s{
ii ,i"'!ir"tt*iirli.
"*tii.l""ii-"ioei.,i"t*.oot ad ,,*ioelonio" trobuie
involtttt'
musoularf
contraclic
orice
iniptice
s[,
udi"n
nf.
I ot"tilit lictr, Muskens (1928' cit{tt <lo Gastnut 4i
i'iiiii,"r'."i"ti,'"J-;o*
r:olab.,19?4; qi do Popoviciu 5i oolab.' 19?0).
Contraotia'sourtdiivoluntai{, poato afecta,unul sartmni mulli rnu6chit
ri,, no'ptoauclna-nicio mlgcoro(ttoflnsare),otunci olntl ttcli()neftz[!(r lnn'l'
mlioi,lleproducindo rnirlcaro.
i,hi
'
ln luuctio ritt tliatribulia lor splJio-tetnpwald,pot' Il dlsiinro doutl
nlunel
t n)-mipolittiiJragnrenlafe,
u,"roi'orfiiirioiu{a iiiitoiti W"orotir'ote
coqro'
irtttroulntu'li
nlo
vrriat'o'p&r!!
;il{
ll nrjinotrlo
6n.f0
nl0olloutn
rlltlFttl(lo,
rrlnerono
blla,tor|l.1o,
nrnr
il
nncluo
at{oolond{
rnlg i "ft,ift;ti;Jnoron
b)
ill
,11-{i,
r"or.r
;.popovicru
;i colatr.,Jgz2,
ii r.otub...
.(ll:
_.i.il].1!o,:,.Gr.h,lt,
,:lo'lltcP
,,, ;l^
(ttt.ufne
t
potologiae.
l! .hipnict) bJ
carpoI fi, la rlnrlul
:...,r.,),
,l
t.t.'!,.
i -. ttttn?rotlt'
org.unt?e.ncppilepltcc,
care pol, fi dc divcrsi etiopatogenii:
*_
rl|r.r,rr,rirsrj(encr.Illitc), to)iice, degenerative,metabolice
etc. 1
m-ioc1orrr olganicc epileptice.
L) ,l[ iocloniile orllani@lnepileptricepotfi intilnite in nlmeroase afecliuni
:
di,,t enaeJtlikr epiLlem;ct,(fort,o tt,iortonicdsau, atgo, !. .I!?r,y,ij,e. ultp tt,ptyo
,,,,,'.,,,..,.,,,u,,ru
V[t? eunlrope Srnr l,irpidc. rifmice, Unebri
) lt lttL
'r, irL||.rtormpte (nu-d{'plaserisegrnentare).
Apur rle obicei in coDl.cstul
tchra. radicrrtatgii.pare-liziiouula!.c.bip(,rsomnie(srrr
..' :l.l:,.iir: ll-rl: i!,
menirgeale. sliiiIi-c.ontu:zive.
chiar cu evolugie slre
1.,,.1::l],"',
,,rrrrr'.
. ],i::lor,n.!9
rt.rrLn{ttf t cri alte mc.nilesliririertra piramidal,.
lparkinsonieno
...l|r *lri)snrdo IoliitrLo) ,si cernbeJoasc,
(.lorcaaelectriad,a tu,i Dubiu i cste o formii, pari,ic'iari,
de nevraxitii,
' ri'rl,trrnici.crr rrrlocloniiampJc.brusle si rlpitl"e.
(1lltol)ol,lttrlttiicl,tlivt,tHluslttrclc,tltrltii ittl,ottsilrrlrrrt,
ltctrsltttrt
t1it.tilitttlrrtt':t
((lir,s{;rrrrl,,
I}Irtttgltiott,ll)71JII'rtpovirritt6i ooltlr.,
llllilJ, llll;ll; (lrtrl,a,trl,,,si
nitt
ll)?(i; illt$sir).rti,,sicolrb., J {Xit}): lt) MiockrtriittrLtlivosit,tlgtrltot'rrl.izrtlt',
clrxrt,,[lilafirt'rrk',rlo obicoi silttol,rioo,ltlttxrli itrsii, itsittttrl'rico5i itt lrltsrtttlii
(rrli,errrindd.olao crizri la alttr,,tle o p:irto srtu rtltl lttrrnioot'1xrt'lli1).
Artslcrr,
it rl;clcsoilzii,cu plcczfiderorllusculat ra axo-tizornolicil lii lnu;clrii llrrrioli'
yrlrxlrrcindo bruscii flexie a capuhli qi o proicc{ic irulint,ttit,lr,(,llbt',,l,rtit't1r'
liorr:c, mult mai rar fiind intercsate $i membl'ele itdcrioilrtl (r.rttciitlctr').
lr) llioolonii parcelare, localizate la rnici srrgnrcntooor?orfrlorsitll clt irtr t tttt tr ri
lrr, r.numitc fascicule musculare (fil,ri tleplasi,ri segneDtir,ro).
:lrrrlrr'k'
Aceste rnioclonii insolesc o pierdere de cunoiitinl,il,(ltbsoltl,ii,),
iilri)rnene (rniocloniilc qi a'bsenla) filntl cxtrem de scultc ca rltltrt,lit (ilrr lrr'
ril,cv:l zecirni dc seculdi, pini, la citeva secunde) $i pot sil, sur'\rirrir,firr Blxrll
lrrtt, fie dnp5, unele stimuliri senzcriale insolite (,rrcacljtr s(tllzo"ololtirii"
rr,hri llusirens). Un alt element semiologicimpoll,ant, csto trplcz(rrlLrrl,(l(l
rIcscii,rcarea electroencefa;1ogra{icd,generalizati,, bilil,t{rrN,lir, Hi,)cr()111,
fi
pE f tf
MA L
l \4IA C LON tC
sub,:Utp1r,eSS7qi;n tpucoenaclat.ite.
, i / tl::
t:\tt"^.
nt ps1r,,,,:,*J1!i.tc,te-25!ygzonte
t t t nr , , / .1 L l _ J s /rl e L tp v a n Bo g a e r.t,rni or,l oni i l esi nl mrai tcri __
,r,{.. I j, r r ^nr i. . unoo l rrto i rL u ri b rl i s ti e l
)i m- l l rrrai orl i nre (r" bi r,r hemi g,,n,._
insoiir.r,
rruoori;i de urrciipcriinozii lipisnrt.
I I'll]j .,,',,
,-' r :r ugil!l,,ili.rnl",,
n .t utur .r ale nrembi
elo-r..
spa s me, le ru rs iu u , .b, c ru if rlio n r,
]rl' |r.n
. 1 1.r, r r ( t r r l l|c ) . A p rt L r (.Op i i
s l d ri i
c5 -r5
pI,'plir.e.l1y,r1x_1;.
esrcs,ibacurr.rnorl:rti.rlupit.
l,'.,.,:i.:.ll',.',
i,-,,I l,:i::
. I }ljricrrueckpr(1974r
I iirir,.'!rrLr |o{:1,.
ltlrll).
si_['opotir.;Lr ,.,,1Jb.(tgi6]
-,i
i,rri,rrriili.
ttin pESS prr.zrnrao .:,,.initn,.rr,in,,,r"
ttit,,r,.nr,iat^
,,
1t1i1,t-!51,:l
r. I.r {r,. ir11r'.rrr1r,(lonll
ree.pileptice;i epilepl,ice: a) tarea reactivitate ia
r||r,Ur.:i\|lztI.\o-lc-0zoftalr
; b) durilta ln:l'ilung,r)aJ,."el SecirSelC
ntiOclo_
r" r' r r |lt U'rrj,t.
u cont.ra,.l,i(.
lonicJ rez;durLili tl" hjperkin,,ziivrr|jrr_
'tc
lri|, (rczi riilii sus -, inrlecscbi cnreice)1c) lcpetiqil
peiotlic:i a rnioclo_
rrilrl t,u itrt;crr:llt'rLesi,ulcle regul.,lte(intre 1_'1b ,""ioAa;
d) plezenla
1,,,rrt,h'\(,Lor'lttr(+
ale hri R:lrleimecker,c:l'e de cel.emai *.iii" Jrii"so,t"sc
'I ,r'|',trii]r'..
.'.,ir,l .c3 ;i nriocl6niilc o rernrrc:Liti pelioclicir.,r,..
.,. , . \ t , t ! t t t ! t tpt
. L, t l tt)t ,( re p r' o z l o i a ,n l ' o rmJ .ol i go,j i rnpl oni uti ci
de errccfa_
r,l) t l. t ll' l. a s : | t ({ ,, :l rJ . n ttL U i t. i n c tr re ml ,cl oni i l e di rfragl n* i i c{,
' '.I|r.r i. , l: - L; r t lr , , , 1. . s rrg l l ;t c l t d rrr2 l g 4 a z i l . S N u caD i .:tni l i .
L I'ottl)Diu([ottusul tt,ulti,plen (al
aparo la adu11;i si
.lui tlri,etlreiclr,
'(1,12
, crrlrrrl,clizr,lrz,i pril nioclonii sinctxice,
frccvente
pe s), lotali_
r.,l ' l. t r l . , . lt . i Uir p ' -2 , d c l tu i rl , h j 4 o !5
;i c v ldri ceps. S e rcc,,Jl tl i ci l zr l i r
'r ,)l | 1 lLtr llr |: ll( 1., L l .rj j Su l u ]rri , S i rrt d e ,r bi C t.i l Or i nt,r.fi obS ,. (ni ,\ i .rr_
'rr c), I ' l, l( ' r ) r , ir r , ir ii t.i rtril i L p s i l u rp a ti .
W)
clilt1tt,itu ltoi Ii in{,ilrrilc itt ntnna,r.tasl
,.
,)li,trlrtniiIc
Jot tttt: tl,r:L:lrr.,.
, | |,r
1 l I ll l(t'
(l tl
l )l )l l t
)tJt)t :
l.,'llut
tt1,:1 "
( . t . ' 1t . irpt
t iir . r ' r r , il ,f f u r t , i t t r , r , ritrnt ') r * t rr r, , i r, r r :r,,i
r
'
,rti r x : lr t t t it t t r
1, r' ilr; i[(llll l]lIrr'1 rlr,
t r . r lir |r r r , lit r ir . lr r it r S, r t , t t r i| rr I rI I I . rr Ii rrr r r l t l l , i 1 r r r r i 0 1 I t o t t r r : .
lrirr:hroutn,c'l;trrirl,lco:
Jtollvltfrrrllo4l polivllt-tttrtlrrlo(/ig' l4'l/. lll'rruvltr['rt
tlrr lrr,ltrrlll'll lrr,ltrrlivirl1i rlrr Ll ctlzil
ttntlrrrrll,rrvrr,r'irtJtllrl,
rrlrrsl,ot'ltolivit'I
| 9:l
l(lN
trt cttz r i ( r lr . , i3
rl t, It,,/n r,i ,.,rl rr { i (,,/rj (,( 1.,
srl l rl rr l 0 r.i scc.) (l \rl rovi r,i u
' ir .li,.,
rrr l o l, r lr . , l1)^r
?li)
l l t r r . lr . t r i. ui s r .ru i rrl o g rli tr)j )o rta n t c B te l cptezenl rat 11o(l escei rci r,t,ct
de
,
l )ri rrr r r : r h. ||I I r i\ r . I iIII| ' ;rl rrp l u !o .U l IG, p o te l l i l l l e oare tra(i l .tc si tcus.i e mi ' _
I l,,l',,', rrlr'u(it litr.:rlc lrrrlri I'ecrutan1,1i,I'eslectiy,
fiecale ,,vlrf', t1c pt,
l,ll,l{,1iir
pr,intr.o d.,soaircarentuscnlrii lrioclonic5'iTassilu,i';i
,rlrr)if('stti
t rl rrrr . , I ll( i1|) .
'.. ('ti,:, l" cpileTt.ire tiotlonice qenerrlizate biktter(Il.entttsire (1|mgoclonic
, '
/./i,\
lrl.l,'frnilirrlogilr, rrrrlu'ilor anglo-saxoni) pot sil apa,*.i itt tty.,t[rtc*rele
/,
r ttltlrr!i clin iut tltile.plicr::
) in l,ncl,. t'r'lri rlp ,!.ilepsie.ltetit zral (rclatate antcrio].) in o:,.r,e
,;r
:r', rri'
s r n l 9 ,,,r* r' rrJ i z :rtol l,tp t C a l e j U S ti fi C l i r.l etrrni i l c:.r,
tl e,,mi o_
' , , s( .jtt {' c' t)u) .
r'l rrtri i t' llr
ir) irr :rrullc tlin cazurilc lc tpil.c:psii t:atrLtlsi,tL
11rrLnd,-ntu[.
1tr-iuvtt,
!,l t,'t,r! ; |t . |, 1, , t , i. t . , .,.| o t,.iJ,,
It, r1,.[1;1
1;yfi i z, i , i r,;ri ul ,l
rOt s i .j rl )..| r. i rr s p r,,.' 1,1
r:r/1r t ( , r r , ( . , r r u, r r ' l ,rti tru s i .e , d e .o b i c e i i n fl e,ri r:, A stfel , ti upi
[i l rsdaut,si
l rrl rl r. ( llt 7' 1) o t t ' ei rrrcrl i rr b o h ra ri i r.r1c ti z r. tL,j l i uLrcl uni ce pl tzi nti l
si nri i i _
' l .tri r t r r ' r s ir r . I ' il; , t o r.,l , i tr ,.rrrt,.rl u l , r,i z r.l ' r. r.,!rl \' l \i \r. f,,,,,." ' .],ri ,i ," .
( 1 9 :,7 r.(,i l a ti ,l . C r.ti r.u tS i c ol ul r.. l !]71 j ,tr ,nsi .l :,t r, ,,1]t.l
'1 .,,r/, , i r ll|i. t iil
IIIi | \' | , ) I I I I I . || hll: r l, t . t1 ,. trs t\ts
: rt trl i l i z :rt l o n| l Ii l l d{. ..i trl l ,| tl ,i \.., p;l i t
-c i
r||,rl') l)., 1nl trriocloniili] care apftr
fi. c] uni. fc1lotllrn rpilcptiic (109, din
. rz.rr'il, f io p'ecotiri
din c:rzuri), fie
(3?f/o), I-ie siit (i;lco_
.(50.0/o
rrl {,l t1 o olt 0r iz ele to n i c o -c l o n rc e .
'rmeazi,
,.) Ii.,i;.iii, qi clzuri de cpilepsii manifesl,:lte prin cri:e et:clusi.u
ntio,'/,,rrr,1. ;1;.,,;1,,1"..irr
sleciLl in adolescen_ti
untori si in mica copilir.ie),
_(dar.
l r , ri rrrir,(l,rnii1cm.rsire se produc rle obicei 1a treziic
.si tiot t,i licilit-lte
',
l r. ,l ',lr li. i' lr . t 1' .oc
. r l rj l u i .. Ii c tl n d e p r i v rl o r d . o:rml . t, r rrni i Lr,,1nrvi , mi o.
,lorriiT,. (".jr.r'lis") p,rt fi pr ur.oc:l,tc de stirnularerr, lurninoa,sl intirrmitcnt.),
i l i rr'1 f,
, r r r l, s i c qlf . il,
G,rs ta u t ;i c o ta b ., 1 9?4; A rseni ;i col rrb., 1O?8),
: -1 9 i 2 ;
r'rr Ir rIl,,,i lrtt, lent:r,l
,lC rlzele S-o1arc,de lumina de tCleYizOr, rle
,,Urmriril
r1 ,",\ izI rl.'L(J.'rerr iirg epilelsy,') s1u do stimuli irten,tionaii
lpiiml.r:rrea
r.rprrl i..:r rrriiriii in firf:r, u,.hilur, stimula,rea luminoesti sl,r6boscopiii,i.
Foi,oir, rrrilriliilt,ieir ir,ccsl,Ordesc:i'ciri este bine cuiLoscttri (Gastaui si'colab.,
t:);t.; \ r r . ' . r , i. r . j c uh J r.. 1 0 ;b ; N a q u e t s i W e k l rui n, 19?2). A ceste mi ocl o_
, r.rt
,t'rt,rl.r':rle'i sirlctr.jce, uneorl lilritate cloar ]a rtru.cchii periol,bitui
" prrlpr.lr,;rli,
da. rte'bicei sint difrue, debutintl pe rnrrschii axr,r_r:izome]ici
,rr
r1rrrlrrri crl,inzinrlu se qi pe tnu;chii periterici. lliocloniile masirre pot lveil
l11!,\'('rl4r r'-iililbiio (rle obicci 1-n/s1 si aprr rn ,,elisu.tde mioclonice)'
l rr rl ri r' , r llr( lo 2- I 0
s , d a r u n ,rJ ri s i rn ,,s frti is mi orl bni c,.cu C nl rr,ti t1e
trrirrr1r. .. Ul |hi:rt rl'- o|e, putinit cuirnina.intr-o crizii
Ee]reriiliz?1ti tonic<t_
,1 ,'r,r'.r . lr r r r iz r ' ' , nti u .l On i ,' ^ , U ,l l l :rl i r/r,i I.rLgr. pol .,i i 1l ,ri .r.i
r:,," ,,.i ;i
:r1,, rlrilii.ilc vigilcnfi, insolrite fi rle tulbncr-r,ri r-lgetrtir.v. l)iJgnosticul
i. i 11r'r'{,r'iz. epil.ptice cit mioclDnii masive este con{irmat
,*i p.iri it*,eslirlrrliilr, lrltl(i, cu,ro c\-i{1efri;iazl pclir.irf u;:i-Inde (s:r,u ungo'i r,!rf-ur[le si
trrlrrrli, llcsoilr'liri (1o undo lentr, eelelalizetc, itil,,tr-rrall., si.rrtrrrn. ;i
l ri trrl l til. c .
l l li, t l, Uit r : t c r . s lo t'i rt,j z ,"rI )i i )(II ()I I j (j(| rl i ,i rn l tl i zrt.tl j i tasi \' (r eS 1r,r.l tr.i trl ri l i ,
l rrrl i rrrl s ii, r r llni ir r tn c q fu l .i tr, t,n r' q l l t.l o tc
t,t,., l i rndogutr: si 4n utcr]i l ttl tttli i
ttti rxl tu i. t t r ' t t . t r lt t ! i. .r' .rry ' r,ri(rrri .r.l rrrrx ' D i 1l ri si rr, l l rrgrr' si vi Irrrrri l i rrl i il l ,rr
l r,rrl rr lr r i llr r v r ili< ' l rl I rI I I II I I )r)t 1 l ; rl i s i tri ,rg i rr c . I.Irr,I,IrIIl i trri .r,I' rri .i i :r l tti
l i r trrr.r r l llur r l) .
t!),1
titl
tl
lt
Lr
r'(,rlrlrH(.
rrrrrrychii
rJlului p:rl:rlului(,.nisti)Srr
5i p'efi'r'crr(i:rk,:
rur,.' ,l \iillr_
Irri).,liI;rlingt'lui, h.ring(.lui,aiplan;cului 6ucal, ai timUii 1cumisliri irllctr
rrrrl,r'rlrt pr.ricclic - retractie), ai gl.oiriloroculari (cu
,,nistagmus',ocular
l)r.rrtltrLr, girstor sau retractor)r_ ridicdtorii pleoapelor, rliafragrnul (cu
srrglri0,rrru..r.hii
inrercosbali,
muicbii gitului si;usctiii diilati ri rncmbrclor
j.l|l]r.r'irnrrc
(cu-miiciri ale degelelorqi cu
_migelrialtemante rio lrronalierrrpirrir,{ie). Cele rnai frecvente
miocloniilo (mioritmiile) or'ofa,rin!1o-sint_
lrlingi()nc, precun fi cele oculo-relo-faringo-laringo-cliafragmatice,
care
Firl l)ilaterale,.cu un I'tm de 12,0-180/minut pi care "sint revel"atoarepeltru
a.[u,;!,i,wni
ale_triunghiului oliao-dentorubria(&uillaln si Mollaret, 19Bb; Bon_
(luollo, 1968i Gastau-t,1968;
popoviciu qi
4lajouanine qi colab., 19b6;
colt,b., 1973) prin leziuni yasculare, ercefatitice, tumorale siu tiaumatici.
Ill.
..
.Miokinlile. s.au Jascicu,l.aliile musculare sint contraclii musculare
l,rii(i(:lilirre. dc,mici arnplitudine. eare nu produc deplasiri SegmeotaJe,
rrrur.se-obserni, Bub-pieLe,
_sub forma ulor contraclii-clonice, ieritmicej
lrrlritte, fulgerltoars ale fibrelor musculare izolato li caro so succed la inter.i
vrllo
qi neregulate. Aceste fasciculatii' apar uneori pe teritorii
^lirccvente
rrruffi11s1,
alteori pe grupo musculare intinse, chiai gc nelrallzaie. Sint net
rrurrrntuatede frig, de_ohoseal5,,_cle
percutia muqchiior,-de excita{ia electriei
ryi do arlministrarea de ad.renalin5. Nu sint irifluenlite nici do' somn, niei
rlo srupolaminl.
Vulo-araa semiologicd,a miokimii,Im (fasciculaliilor muscalare) este
.
rluoscllitS,,reprozentintl un sernn precoce, revolator- pentru o sensibilitate
rluorma S,a fibrei musculare la mediatorul chimic (aclienalini,), consecutivi,
rrrxri rlc_rervii,ri (feromenul lui plnngnl prin.leziuni, subacut-cronieegteri oru.ionala (sclerozd, lateral* a,miotroficf ; poliomielite subacuts qi croiice;
r.nr.cllopoliomiclito lirotice subacute 9i cronico - Dr[Elnoscu si Otteanu.
M56 ; gi1ing66i6lie)..So igpune multd atenlie in sindioamelo de pseuclonr.lcrozl lateralS,amiotroficd (Barrd gi Roger, cila!i do Eiser, 1952) prin
Irrsirrni corticale (tumori parieto-fron-tale, a,rahnoidito etc.), ln care so poate
r1)illiza o. monoplegio sau o paraplegio corticald, phamidald,, inso!^iffi qi
.
rlo ltrofii musculare cu fasciculalir, dar. prez-enfa in coltextui semiologi"e
rr,r.r'iz,'lorjacktoniene odenteazi de obicei diagnosticul.
_ Astfcl cls faaciculaiii muscul.are se mai pot intitni qi itj c(ffeea jibtitorf
l, lu,i Moroan, care esljo o newaxiti, acuti Ei caro &soeiazi b 6ntoxtul
norrriologio; f2,g6io1l2,!ii,mioc_l.onii,tuiburiri neurovegetative rlo tipul aerorlirrioi, t,rrlburd,ritrofice qi sudoralo qi eveutual tulburari do somn,
. .fr'usc.iculalii_musculare. izoJate la nivelul mugchilcr felei pot fi observ rr,l;cin sptasmulfacial peri.feri.cpaslp6ral,iti.c.
INncep!,ional,d,a
ra,r.pot ti intilnito Jasciculafiilo musculare ln potira".
rliut.l.on.earitre
qi in unele p olin etri,te inJeclioase fi tasi.cs.
uneori-fasciculalrii izolate_la basedowieni, la i:rdivizii surmena_ti
, J,l..ri,std,
5i rrntxrri dupd, o obosealS,musculard,intensfl la indivizii normali {miokimiile
lrri {'rrrt'ho1).
{i,1.!. ll{igctrri involuntare alternatile, regulate, rilmiec ;i
stereotipo
Irt1tlIIotrirrolrilxrJrirrr,l,ic
(;llrrliirrsorrilr,lr)
rlrrrlivcrsrrrrl,ioplrlogrrrii
(poslorrcr,
lrrlilic, rrirI'urrrIIrl',
posl,lntrrrrurlic,
strrrilrrl,c.).Alrir,r'oltr rrrI' rr( i rIr,r'r,Il, llror
rlo Irrrr1rIiLtrtIitrrr
rttorI(,trLl,i'h,
lrrrzi(ii(ittrtlttsivirrlrozi{ilttir:ttrltitus),cslc t il trritrirr
rll Itr'rl.r,rr(ii,
rrrir:ii,
(J l{) oscilr,{ii/sr,c.),
r'oi,r'ornt'lit:i
(irrrilil,
;i llrt,rlrlogr.sl,rrrrli,
rrrrrrrrrilc:rtr(,itttri
; dc lrutniirar,c
n ltarrilot.,
tlo,,flr,r,rrr,,ir,
lrilrr|.lor',rlrr llr,lrrrrr
:r lolrci crr rlogel,clc
ci.c.),dilritrrroluti,slnrclisplrcirrcrrlstrl
.rrriqr,l'i,r.ilrrt.
lrqlivr,,
l irrlrursiliciila cmof,ii qi tlisparc in somrr. l)c rnllli,o ori irrlrrrrrsclzi,rri
, rlrcrrrilir,t;o:r,
ccfalici (rniscIli ,,tlc afinna,r'cr)sau ,,rlo rrcgrr,{irr,)).
:!. 'l'ten.ulr\I,ulaintenlionalii,(d,ea<:!tn,nt) ap:rrc il sirxlrorrlrl rrr,rr,lx,krrr
irr lirrrpnl nisclit.ilor acl,irjer,
:r,oceritnirllu-sc'progrusiv
otlairi rrrrrlczlollrrr,r,l
rrrir.r'iilii(ovcrrtualtlori,rlrr,slh.qitulrniqcirii). Ilstu rnai arnlli'l dtcil, lrr,rltrr.rr
lrlr Jlrr')r
insonitr,n[,rrereg'ulatd,,
rlisparc complet in reparrsqi Irr rrrt,rr{irrorr.ir
rrrrr.i1rostuli. Se insr:festede alto sernnecorebclolse.
:i.. Tr.enlurdlura optoz,l]ion
alii este tot o trcmn.rii,turir ilc rr,o[irrrrc,rupi
lrrrl lu sfirqitul uriqcririlor activc, da.r'esbeconstiluitl r)in osciLl(ii lirrrr.lrr
rrIrl,lr, (iirniste,,biit{i,, dea,rip:i,ca?etind sii indeplidrczorrrflu[)nll lr,nprxrtiv
lrlrr obicci supcrior) dc lintii (de unde tennenul tlc ,,oyrozi
{iortali'i,"nrru rlt
,,irc1iu1roantagonistL"). Este ca,racteristiczipentm sintlroa,lrokrrlcrrt,o
rrrlr.t'itro
dc, diverse etiopatogenii qi pentru degenerescctll
elo hellll,o 0o|rr
lrlrrl' (lioala lui \lrilson qi pseutlosclroza lui Wcstphal-stliimpt,ll), rrsor,i
Irr I u sc a,f)roapel,otdeauna si do miqciri de tip coreic qi de spasrirc v iololr1,r,.
,1..il'r.emurd,ttuile
permanlnte 86 obscrri,;tit in rdpaus,-cil,6i ll (irtrprrt
rrrl rr{i rcrii r:nor postuii qi constau ln oscil{ii neregulatd ale ilegrt'ck.rr( ulrooli
ir.r (tle iltosr,:rl,i11irl,,
',r :rlr. lruzelot) de mici rmplituclinc. Pot fi : .fi:-iolcrg
lt4t), (moli1)e (simultnil boal* lui B:r,sedow),"lt i pcrii r,itliene, \rt tt,ilittrtrtt.
rlrrrric,ln intor'icaliile en mereur, cu nicotin[, cu coteinti. Nu so lrrsol,onc
(lf, $('funo extrapiramidale, eu exeeplia ccTor senile.
;,. Trcntoru,l isltric ,si al sirnulan!,ilor trebuie diferonliat do vtrirurl,okr
Irrt.r\trlnte do 1,remu$,tufti. Acost tremor nu are car.actelo rituri<,o qi rlu.rvr
lilx', eri dimpotriv{,: apare intemitsnt,
apare in prezenla epr:otu,trxllor',
lrrl o 1l1yq1la,
neregrrlat, heterotipie, Iiinit variabil tlela un morncnt; lrr, oll,ul\lrirlc_fio ln, repaus, fie in miqoare, are caracter net circurnstau I,ilr,l, l'iilrl
rlr.pcrrrlentde_sil,ualiile emotionale qi/sau levenrlicativo (Soflo1,(rt,,
J1r0?)
qi de ticrrr;i,tlc spasmt:;i rkr curilorsiulri'llizrr.rr.'.
.r .lr.rrrtltc ori sc.insofesto
p;rlrrrloxulc,clownieno(Riser, 1952).
{i.l.i}. Iliperkinezii bru;te, iliseonl,irmc,rapide, dc ounrolrr rdorrir, tlozor
.
rkrrrrlrr (ncrilmicel
1. . Ii;cd,rila coreice sint rniqciiri involunta,re gencmlizrd,r: (dc ohicr,i).
,,rr prrrrrlominanld,la,fa,t5 ryila rnrrnrblcle supcrioarc, bruql,tr,dworrlr.rlllo,
rIrfir,(,, il,$irne1;r'tioo
do lir, llrr gl'ltp
$i asincr,ono,schirubintlu-se noirrccl;:r,1,
rrrrrslullll ll altul. Sinl; va,r'iabilcdc la un monrcnt lir,altul, so inl,rrrsilicir,
lrrr.rrro( ii, lir,eforl,uri 6i ln cfcclirilrtu,rrnor acNiuni rnrr$cul:llcicllmcl,or,ncrrri
rrl(,nfional) 1rlra,zi1,ind
rniqcir,r.ilo
vohrntalr', ca,rtrdcvin asl,lrrlilra,tlrxrvll,r,.
iir. rrluLrrcl,z
ii, pinr'i,lrr rlispari{,ioirr loptus doplin lr pl,i, ill lrr routn rlilprr,t'.
I rrr.olisirr! linritrr,l,o
Ia,rrn ltt:rnirrorlt(lrcrnitnroi),irlr,do }iklir, ltr r.rirrrliorr,
rrrr'lr.llrllr.rttir.rr
qi .jttxttrllt.l:trrtitr'.
Nfitt,ririfrrr,orlioo ,vr, inlthuso )n:
q) (lol'rrrrtrt.tu,lii( tl'utl.t,thtr,ttt),
tr:[ttrrtpltr lit rtrlrii,rlrr ollirrci in1,rofi lfl
rrtri,l'iitrrlrlrril oli nrrr,llrocvrrtrlll,
ltr,1irl,ilo.lCrcr,pl,iorrrrl
ro lnlllturnl,o11vl r,lr|'t
rrrlrrllil. \lrrrrri ilr rrrrrlrul,rrlrlrrri lloli rlrrrrrtl,ixrr
lr,lo.
'|t0
I0?
':"..":
,,...,,'i1...".'.':
I I | | | | I | |IIItiI
rtLrOiji,lrt.r.r.r.trrrlir.t,-
.em
n Di l l r n i r i l l O _ r . l t r a _
o l r l l tr 'l '
l tti I't1 1 :t) l r 'l r l l zi l r l i r
( ti r ttl r u n ttl
: '. l l r n t i l nl i sttttl
''r tl ttr l tti
l r r r r ', 'r , l | | r | l . r 'r i , Ir Ii r l :t, t l i sru t t t l i r t t l ri , IIItt II|' tIII||1 | I t t rt 1t I i I t t t I i t t r' , l l l ( l tr i i l l l
, , r , r r r r r r c r r r Ir r r 'Ir 'r Ir ,o ;l ti l r .si tti
r l i r r l o cr tl r ' l r ti tt tl r '1 tl i tsl tti l r l tt,i l r '1 i r r l l l t'l
l tr o l tr t'
t r l r '. r r t ( r t r l l l ttr ,:r zr i si i ,r 1 t,'tttl ttl tttr r l ttttl t,i t l t I I t I t t t ' I r i t I I t I i . St'l to l tl t
, r r t r r r r r . r i ti ( ( ) t!,i r '( ' tl ttr l l l ( '.
l ) i l u l i : t n t ul ,
r i Il r 'Ii tttI,' r 'tcti o l r tr r r i l i r L l i i ( tr r r i i ) r t' t r tt'r ttr l l t i zr ':r z:t l r tttt
r , , , , r r r i I rr, t r ri I rri I i i ' ( ( 'i r l ) l ttl \ i tt j tt ttttxl si ttto tt i r r tl l l ttr tl tr r l r l l l r i t ( 'i l tt tr r i l r r t'
1 , , ' r 1 , . , l r l r , i r tr t r l i l i r i r tl l o cvo l tt{i o l ci ti p to l l ttr si vi ,.
{i . t . i i .
l r .r tl r ', Ii ti t
t'r r l i l t'l ct
cl o tti t'
r t l tJl r 't l i i ttczi c tl i 'r ti ttt'r 'i r ttl ti l ctr l i r l l r ,i l ttti ',i r l i 'i t
1 . . l l t l , t : r l r 'l r l czi ttl i
t t t t t I t t I I t t t I t r, l t|r 'r l ,r tr tt
, , , r , r , : i , r , r r t lr l ,i |t'i zi tttl r r sr r i r ) 'j l l In i fci i fi
i l IV{}l l t]l l r l l l '
l r t tti t'r l ttl i r r i tttn i l i i l Ji l tl r r l l r sl tctr i r tl Ir t tl cg r 'l r 'l l r r r i i
r r . r r r l . r i : r r r c l ll r r si t'r '
Si l tt' r n i l tl i ti
i ,t'l l l 'i ttr ttl r l tr ', \'( 'l 'rl r l r 'l r l i l r l ',
| | l ! , r , ( l ( ' rr t r r 1rI i I rrr I i t rr r tn o tl ct'l ti L
|,r'
l l l l ( 's{'r ]' l r j zr l tt', r 'tt r l t'tti tr 'l r ttl .r r
| l | | l r I i l | r i ( l ( 'g ( ,1 |l o l si r n i i n i i :tl i l tr tl i l l i
u r l cg t'i cl o t', ti tL tl ttttttl i ttl l tr r ,i c' t'i ti r l r tl l l tl i tt t'r l r r ttsi r ', 1 1 1 "1 r 'l r 'l r '
r,' rrrr(lllrj
''r l L r L r l r r i r . i t r tr to tl i r ttl r 'p ctttl e ttl , i ttt'i l ci l c, tl e r ti vtl ttl t' tttr r tl Ii r ( l 'i r l c l r 'l l r l l r l l ,
, r r r r r r r l l . r l t rl l i s( 'r i r i vi r t'i i ) l ) i l 1 r l to ttl r 'tt fi cr ,tl l c tl i n l r tr cL ', tl t' l ti 1 tItIr l .'tr r l i r '
ttti ti si l 'l tr r tl i l tt'' tl r tl tzttr
r r r r l . l l t 'r i r r l i r l {i r l i .
l ,i r Ii ti l r t r n i r l l 'i r l l r r si tr l 'l l tt{i l l
, l r r ; r i . r r r i s c r i li r l e i r r ti cl r r i tl l r tc l tl cg r i t,l o i l i r l c tl i l 'i .i r ti t l r vi l l l l l tti l ti l i o tttl tr t
, r , l r l r r r . i r r i u ttl n r ,
r 'i r r tl sl tl r j tt a 1 r ti i , $ l ttr l ttl r i i fcl r :i ;i r i l i tt ttto tl ( ( ,r r ,l :r r r l ,
l t ) l l o a l u. l 'u i l l r l l l r l r i l u t
fl tl I: * i b tu l t. l tr i l 'o tl r i r tl r r l i 'r '( i tttr i I'tl r l l
r l , ; . r r r r . t 'r r l i r c i a tn i l i r r l c ( cr r i r tst'ci r t{r t'r tl tt'i l tl r td i i }r i Ir I1 r 'tr tIo I) r l l i ( l r r l r r $ i :r ( 'r ) t
( l i r tttti t Vtr g i ) r r r r t ttr
l , r r l r r i l r r i l , l l l 's) . ,\l ) l r tl n p r i r ttt;i tr t't' i l ttt l It l tr i ti tttl r ttt
r 'o l l l r '\l
,,l,,lr rtlli
i tl l l 'l l t
N ( 'l r l i r ,l n l 't.
( ) r o l r l r r l r r i Jl r tl l t,tvo tr l ctt- Sl ) l l l 7 ) ,
t'o t|o tl r i 0 zr t
q r r tr ctr tl i zn l i i
, r t r . r r ; r o | i l t zi :
t'\1 l tl l ) i l i l l l l i ( l l l l i l ,
l ti l x'ti r ttti 0
l , l . r 1 r , r 'r r l i i , ( i tr r ,l r r r i r 'l i r tn tr r r cl ti i i i '( r ,i ) , l i r l l l tr l i i l i tl t' t'ttl l r i tr '( tl i r l r r g i r '
"l ti r tl i ) '
r r l t( |i i r r o l tf i t'i , l !'l i l ) i 1 i i l ) i u l l l ( 'l l l r l r r r . tl i
i ttti tsl i t,i tl ttl i i ,
l ' | l r , ' o ( 'u L|l l ] r .r
r r r , r r {r r ; r r u g r tr i vl 'i r 1 i t.r i l r r s ( i r r ci l l vr t l tr tti i l l i r tttti r i l tl r r r r l i l i l i r l tti \ o ;1 1
i i l ) l tl z) .
, rrr liiilrr
i rr r i i tt Io tttl t,.i u vctti l i i , r t, l tti l l r tl k'tr o ttl ( 'l I
, 1 , l t t L t ,l i r r p o l i r l r , l u l l ti tn i i
IIt|) ti n 'u i t'i i tr . l tr i tr r tt Iktl r tr tl csl c o r r l to l tl
, 1 , 1 , r r , 't r r l i r , i Il l i r i l i i r l i i
( tr tti i ) , r 'r r tt ttso l i i tzi i : Iti 1 tctIr ttti tr r 'r i tr tl ti t'r tttti tl r tl :r
r , , r r l r 'l r r r l l r r Ittr "tttIr It Il , i ttl i 'ti o r tl '( ' si l ttttr l t!r 'r i ttttl ' tl s( x'l l ( l ( 'l l {i i ) , l l i |( 'l l \ l l r |z r l
, r r r r l r i l l ', ( , r ) l ttIl r '\r , ( ;tl r 'l o tr i , l r i l r r ( r 'r r r l i , s;l ttttttl ' tl 0 i tttsi ttttr ', I t r ' t t t i I r: r I i ,t r t )
l tttt
rl) liult
/ti ( ttr
tl ;l r l r l ,l r l i r tl ( l tr ,l i r tn tt'.l i r l r tl tr tl .i l l ttr ttr ti l ti n ttl tttl ttl tt
r r r r .l
, Ita l;tlrl)(lil'
i tl r tttt' l r t I ,{i I l ''r ), I I | , ' tl r ' vi tn i i r
tl t.l tttl i .l i tt ttti i ttl xr ,ttl i )
l r r , 'r r , , I r r t r r l {Ir '|{ ||tIi Il l r Ii tl r , o t ttl r 'l :tIr 1 r :r Ii l l i tr r Ir i l tt cvo l r tl i r , l ctr l l i ( ( l r t I
, l r r r . l r i l r r l r r l r., |!) r 'i I, r 'i i r r ( i ( |( , l ) tl i i ,l r r tl i i i tl 1 i l 'r r .j r r l , l l ) i l ) tttt'tr r l ti r i l tt l r r r tr l r t
l r r r \ l z l r r . i t r , r . :\r i r r r r r r z;i ttt l r tl r l r r ttl r tl tttr r r !r ;1 i r r : l i tl l r ttl 'i i t'r {l r ' \'r '( l ( ^ r l , ( tr l l
. Tiaurtle
,lrl ,1,.,,-r,,lrlorrr1rN,
,/
.silt ;nisc,rli inyoluni;are intelmitenie (discontinte), c,Lescorrtplere,.brn;tc, repet:.te, rapide ,,litle clr:rcicr clonic,
Ir.r.rr Lpc.-\cestc acio sillt inoportrlne gl absurdc, ailerea :.ealizind
,,ges_
lrti incomplt:tre'r,tloar schifate. Sint loarte cliferite ca morlalil,ate tle"ex_
jucrnntlrr,
Jttitrt rtr. (clipit,
blelerospasm, grirn:rse,tuse, rtisucirea gitului
sr,r,r ,' LPului,rniccili :rlp_membrelor).Acela;i tic po:r,tgsi'r,
fie lepetat timp
,lr..lrrrri_r'lu_
rr,ni,ri,minind absolut sterectip, pinii'cind pozrtc sti tlisp:llii,
.r'rlirrrl locul altuin. Ticurile ccrleaziiin sorirl
!i, la incep'ut,pot fi influonl
1r,l,{irl(l critro voin.fri. Sc exagereaziiIa emobii.
llorr,l,rr.
tk.tttri,ktr(a l,ui Gtlles d,elu Ilourette) so polNe l'esunoi]lbcplill
lt1.z''rrlir{lr. ii(uIi rnLrliiII,',gorreritliza1'0,
la, nivclul 1c{,0i
cn pt'orlornilrrur!ri
.1r,;-lrlrllut,ir,N(,('ii|,t,'.
s i Ulr [,rilbtrli-r,r'i
psilricesi 1,uIbLLlr'i,r'i
{10 vol.l)ir'{)((]ol)r{,lrt'lic.i ciroIrr,IiIr).
l)obrrtr:rr,zii
in copil,;iriil,tlc rrlriccicrr ticLu.iir,r,riirlo,
iritri,sir
r,rlittrl lrlourtsit', po rnir,sur.rt,
lutorrnl,rti,r'ii
psi!to1lri,irr,.
Nrr
;ii rr Lrt)IIttr.riliIor,
tio {,otrIrI,IrIr'i,
trici rrrrll\rntrrlr, srtt0ritri,illrrr.v0l r,si,
olgrl,lli(:ii.
' ll
r r r r r r r r t i , r 't . l r l i zj r r tl r tr n i i r r i t,i i tl i vt:tsr fxp t'( .si vi r o u g ti tti i tst,l t'( x'l ( 'ttl i l i |.i l l ( l i r l r '
i tt r t{i l ttr l tl tr
r i str l r i l i
Irrri
r {. 1 ) r '('vi r z ttr , i l n ' ttttti i th i i Si tu l i r i l e a l i zo l l zi
, , , , 1 , . p l r r i r , . i tr t'r n str l r i r i ;i r i i r i l o r ,
h i p ti l l i i r tl z i l t' r tl r r l o zi t'i i
l ) i l l i r r r l , i r zr l
r r r . L r I i I l r I l 'l r l r c1 i vl j : r ,i ttt tl ct'i tte i r n ti ccvl tl i ,.
\i"lf)zl
l ) {l r i ( ' l i ttn .i l u .l r ttl .i stt;r t l ti l r t.l e r ttIr i , l u 'r tIi ::u .l r i . si \tt tl tl tttttl t t!l tt
r t t t r | r r t i i tr r r t'i l tl i i tr tt i tl ttr ttt:l tti l tr sti Ii
st'tr ti r I l o g i 0 l ', i tttl l ',r st'l r i tl i tt r r |ttr r
, I rrr;rilirrrrirlrilii.
rr) ltdo::rt, dubtii' (st.:,tu.s )u Q,tttto'a,lll* al hti lt o!ll.) t'r'lt'vi rlc rrlrtlli 'r
, 1 , , ( i r n r ' ( 'o ng ( fl i tr l ,i ,, sr tl r e ste co l l str o i n l a , n tl tl l tr r ttr tr fl l l i l tr i tl tr l r tttttt'i r ',r ;r t
I r r r r i u r r l l n o l se ch cl o ( l o e 1 I( i e f:ll o p l l l 'i c i n fl ttr l i l i i ' ( i l r tl r ,l l stl r i l ) l i l l l l r l ) .\r l
l l l r co l i c.q i c i tso ci l r l r 'i l tt o r l i l t!'i 1 i r , I ri I'I t t t t i r I I r |: r tl r '
'r r : r l l i I r r c l r i ti r r e o u tl a l i ) .
t r l r r r l l r o l i i l u i l ,i ti .l c, r 'u l u l l ) r ':ir i l l si l l i ( '( r fi 1 l ( l ( r s{'i t {1 l r 1 'r 'i z( ' ( x,tl \ l l l r i v{'.
l t)
rrriuctouii,
atirriir.,
J,r.()Ar'csivii,
tlizrrlLUo
qi rtr.rrrrrr,
l]l1i::.i:lill;,1'i:,1llu]1,1,1t,',
, ir.totozrccfi 0r'izo
corr\,1r
lsiyo.llvolulia osrerrpidii( | _ 4 rrrri)spr.ir
lll',,]ll,llt','
. t') Ilncr,lalqtotid corsccutiDd,pritrobtastozei.fetate (i.terut ntralear)
dc Joet0/r_Ehintrutre:te de fo:lrtc multe ori in tabloul
tUut. tnt,t.ntp((ttntt,tqk
i(\rrU,)iglc col.co.atel,ozi,bilateraLi,. geoer.alizabJ,,
,sociatd cu spasm de
- ar,axiecnier"ioaJ?
."".]lapiramidalni
Llt::':ll.
(,rvt s r r ol,
{].::lll:lll,:l
r t ( . pt lc o ft d e ti C i b i n i c l p C tu a l .
l,erraparezi,
,:lli:i11
iJ"i/#'f#
;#i'fi,1
ifi ll$T5lll,lil:l*,Ll"",^fi
i;Hf$,.1"",*f
l,li;
lii;l'':ft]'$' iitti3i,T"Lo"""'
accidenbelor
vasculare
cerebrale
ryiexceplio-
(',!. I)IS?ONIILE(SINDEOAMELE
DISTONICE
SAU DISTONIII,,E
KINETICE
_ RISER.1952)
SPASMODICE
,'lirrt mirycxriinvoluntare cu caiacter tonic c:!re teurizcazia
o atitudine
pllti':Il;tr]i,
cnrc semrn!ine un timp rrariabi] (citeva *""aro,l" *uo mlnutet.
l,r'rrrilrpcl r,irnramal mult sAumai pulin durabild,pe care o induc. SpaSmrii
in frod_srereotip,
f1;arielrlcvent qi -adesea
lll"j:,.::--!]lli
lll,.!ll,
!o Tgp:t1
||(.
o Uri llutit
suOrotrirott
in tol cursril st,lrii de l,ogl(,(llnpol.i in sontn).
.\r'r.,-trr
rl.isronii,kiuciiccpot sj lie.rnaj mult s,u-urri'pr:.i; "i
;r';",:;i;;;i;
i\ir,ll/ix?/,3nt.. lJe obrcerse insolesc,1ide hipe.r.bonii
e.rl,rapiramidilc,precum
rii rfrr-liipolliinezii, Aceste distoaii hirletice tealizeazl o'a"phr*"u'*'"g;""_
{lnruritii unei contrrcLii spasmodit,e
lorens" a $nrp,,lo. .,,iuscul.:']i.ll:,Ii.
rjUl'rlr.(!r'r-fi;11(r,conl.rtctie-crrrccstcprogresivi.re[r,ri1.dur;l).f-.(,aractcrul
r(!l)r.r,rr,lr/
itt mlfcar rnroluntars realizate so datorreryleunor varialii nein_
rotnlr: rlc tonrrs mrsclhr', bmsc_diminuat
_siapoi din nor i:msc exagerftt.
n {x,stc rtcplasi,ti tr)nioe a,normale sint ritmate qi oarecurn stereotipe
Ia
rtrxrlrr,ri
bolnav, putind ant.rena cu yreme& deformalii scoliotice qi aiiicu_
Lrtrr. Nu slnt $on,sibilela preparatrele cle tip atropinic.
(i.2.1. Distoniile kineticc localizatc
L Torticolisul spasmod,icprozinti urmitoarele c&ractelo semiologice :
..
llu Bptsm musoular tonic antrencazii, o lonti, rotalie qi laclina{ie vicioasd,
1r,ol,pului, ou o contraciio a muqchilor stemocleidomastoitiian qi ttapez
(ovonl;ua,l.qi. o_piolosrrlui gitr ui do acooaqi parte, .rareori qi r murichilol
itrvocinrlri ,i glbulrri).uuor:r'i rxruLrac{ia,
tonicrna color doi n.rry.hi ino'rrrr,t,i
{lo (pinull oiri,obilltorluki,, il,r: cu,prl to flccto',zil 1,oni(rspro u.u.fI (rol.rrrcolini.
20{t
\r'rrrrll'ri,
rrorrl,rlclir lotrft,iiltrlrrlzi'l,lll,rrnlrlrtprl o trcrrr'1il,
yrtu'irrirrlll,
(notrrnrlr,),
, rr!ttl litrir,irrrl
xrt rr'virrrlirr lxrzil,irr,
rrorrrlrli\,rltr. irrrcrlirr,l,
lo lrt.orlttr,rr
ttn rrli,
,lrrrltt],(filrr"l lr.prrrir.ct.r,lrzii,
lrr lxrzi(,irr,
vi0iolr,s:i,
*i I11lltrt'llirlrrprrrhr,
rltr rrtrrli,
rlr,r'rrii,
o solirrrlc osci[ir,{ii
Iotrkr,irrcglllc,cilrc ]lol, l'i rnirilc rlrrr,fr1111,1
1u,1tt,,
r rrlrri,cllt, r,on;(ir.rr{,
si!lr lut, s(} ollutlt llr,rltrltLlsalclt,
olrprrltri,ltlilr goHl,rrl
rrrrlrrgorrirl
rlrr cortl\ic, rnili rlcgrtllii,sjrrrJxrlic
rlocil,olic:tco(l.i,iBrr,ll)f!:
llrllrllt, lf)iri),ci1,tr,t.tlt
$oflrrlirt[,1$(i7).J3olr,llilpllrt rlo obir,r'illu lrlll(i li
rrr.r'|Iltoh)r lrrrrgltrsiv.lr:i, trn it(lolosoorrttto Vorn gi di irt f itnLrlrltrrl llr,,r
, rrr','f;rlilrioltidcrrrioi,sitn l[ o seclttrlii,
postcrrccfa,li{,i.ii,rnlt,iilkrs rllroii,gixirrr
I irlllr $culno rlin selirr,exl rrlpirl,rrridllii qi dacr'lplr:zini;ii,gi r:r.izcrrcrrlogirr,
r
r,vrrrtur'r,l- pareza c,onvcrgenfci globilol ocula,ri.
f,)st,rrrlu o dcosebil,ii,irnptntln!ii, practicr-l tlil en!i?r'm
,i :llitului
,ltrrtttttotlit(tlc ori.gi.nce ra,piramlduld,) d.t: aLte
dc
turl,ir;olix,
r.lnpfi
J'orma
, rrrrr lrrrrrti:r,z:i:a,\ l.lorlicoli,sttlcon.geni,t&l
csto perrnnncnt, irrstl{il rrtr0rlr,i
r rlr. rrsimctlii trl.nnio-fa,ciale.
Acest torticolis congcriital loltro I'i i:ol,vrrlrlil
ttn',t nmllatrnatii crutt,icne,ocr:ipitale,ratebrnle sau, nru,trcu,fuxt
(rlrr olriru,i
,,r irfcrr{iabileratliologic); b) I'orticol,isnlsimptomatic cste rnnstxrrrl,ivrrrror,
,'r izr. loc,ir'le: tnimitd, localli (roumaticit, virol,icd, atc.\, red,i(rtLilii uroi.aqll
rultniot'it,s1ton.d,i,l,itd,,
arahnoirli,td,
ceroi.t:aki,
ln acesto situ:t,l.,ii,
tol.t,iooliHul
r,rrlr,irrsolit tlc durcli in muqchii contractati, dlrreri cilre dc ,.rbir.cisinl, r.r,rr
, , r'b, I rrslu dcclanqatc tle tuse, de stri,nut qi de migcilrile oapul ui
ryi:llcgi t,rrlr I i I
rl I'rri!,ii.le aici.oaseale atpztlui tleterminate tle l,umoli ale losci postoliorr,rri
'.r rl'. L.ziuui vetfehrc,lo(dc^pildii, un morb Pott cervic:r,I,o ftaciurii, ru,rvi
, rrl:i,ry]11'111ip
rLscaliietc.). jn acestesitunlii, de obicei tottiicoli$ulcrl.oIirrrlr
tllr.r ic.irnintc, cu inclinarea,.laterali,a capulli), tlacl nu drrfilitiv, ccl prr(irr
lrrrrp rlc. srlpt5.mini,firl exaccrbilri tonico, filr'L manilit'stririlespu,strrixlilo
I rrrlr,rriiil icc ;i rapid intcrmite;nte, o& in cazul vcriljabilullti torticolis slrrrn
rrr,xlir...Si!u, elrerrtual,:ttitudinea vicioasii a capului (.'s1cpar.oxisl,irr'l,'rlrrl
,lrrlr';rzii,citcva, orc, so ilsoleqte rle ce{aleebrrifall;i tlc vir,r,srituri(ciizr,hr
Irrgxjiirr') ; rl) It'alsul torticolis spasmodiaad,reinsole,ltc, 3u11,
axtr(J
s(u .
'li' ,.r
tl.tr l .t i net:ralgii a
nera occiptital al lui, Arnold,, se rccunorulo rr4rrr,,
_m.arelu.i
,lr('ir I,incrtrsea,made ]ocalizareadurerii qi de scmnelodc a<rornpir,rrirr,rr
ri,rrl,
l,lituur 1i ntliologice) de lezirrne rrtliculrr,r'ii('r-('o (rr11r'rrze,
rlirtrt,lcif
irLl,r,i
lrr|rr.lizrr1c,
]riperostoze, deform:r,]ii ale lNrlui olos ctc.) ; ri) ,I,ttt,l,itnliyLtl
,,rrrric(r'echiul torl,icoiis mental al ]ui Rrissaurl qi }krigr', ci1;rL,{,i
dc liirrrr',
llrl,2) $o_
r ccunoaqteuqor, plin car.acterulatipic (pozifionu,l),lllin irrkrrrsi"
lrrlr.,rr,
ltrllluri,rii (majoratii r1eenrclii), pr.in callcl,enrl inttrlrrril,trrrl,
(iru'{ill
anxioasi,) qi prin depista,r'cafaoliot'ilol psilrogtrnictruzu,li.
,r (l(! rjt,luo{1,
!. Spas,nulntonoplagi,c
(Jiiscr, J 952) ('Iorrnt'n incorcct,,ll.ll. ,l\.rnr(\nul
rrrri oorcet ar fi ,,Spasm rle 1;orsiurrclrr,aobil,lt,).Actstn ilt.r",irr 1yrrrr,r,rl,
| , ti r(1lirlosimilir,r"c
cu tor.tiurlisul spasrnorlic,
da,r'otrloonlizilr.olll urr rrrrrrrrltrrr
rrrr1r.r'irIr'.
Dsto vor,ba,do 0 nriqcnrc de lorsiunc ircestui rntirnlrrrritr .irrlrrl
rrrrrlrri sIu, dc pronrl,tic ;i ilo supinl,tio {orltl,:'r,llt,rrrnativitr,r:u,urr Icl rlrr
,,rrluliu(r') illttnrrrr,tivii.Oorrira,o(,irr,
spirsmfiljci[ esle lehljiv lcntil, qi plogrr,.
rrvir, r,!t'(toricOvtr,rnili r:tpidii (d1Ir niciodnl,li,0u r:illilctc|ul d0 brusr;hoh,
lotr,icil), llstfrl incil pozi!,ia lnorrnlllir, estc nlrrrtinul.il oitcvt, sturtrndo
Jrlru'l
lrr.r'itovl, rtrinrrlr,,plinl,r-o ,,hipcr.1,onio
rlo lroiti,ult),,'
(ltiscr, l{}I?), Allrin
rrlrrrlrntl srrllrrr,iolr.r,sprcLivrtvinrr Ll loc, llr.irr trlitrxll t(yr rrrrstrrrlrrl,trril.
'rrll'lr,Ht,i,
rlooorrtlrur{io
liirrrl tlo rrsrrrncrrt,rr,
ltrnl,[ (in !.- Ii nlcrrrrrlrr),
rlru r1tr,6ri,
rrrrrorr
rlltrl,t'[,it t1r'ttcillr rh.ol,intp xrl v irrr,ll rrlrou Hplll{|l],t,l,lr r1\l)iJl,li
r,()l11,fl,(]t,illu.
(1ruIi ltt trttzttll,(]rli(rolimtluittltrr.xtrrrxlh,,
;ttttrt'tltttthr.
,{t,lrril)ul ttrrrrrllortrt,lo.
201
(io(]roili\',iruril rri<,iv0irrlrr,r
ltr(r lttr (] rt'il,r11.r'
ilupir|it,l,iv,
litrviziili ; $l).lrittttrl
ri{,i l,r,st,lltir,
trioi rni4clililrrirrlctL{,iorr*le
s:ru aut,ornatc,trici rnlnovrr:loilo
olrlirr^ll spllsrrrului(irrclusiv r.[on3a1,ii]
ltclivi r.,:inp rsirir'r,
rr,nrcrnbrului re$1rofiliv)rru llot suprirna spastnr:lt,.T)oll sornnul le abol,5te.
. r\ccst slastn brahial ap:r,rein sti,ri postencefalitice (de obicei), in sufelil{o \/tl,sculare,tra[maiice eti],
{i.il.2. 1}istoniile kilotice gencrnlizatc sau cxlinse
.. 1.. lJpasmul de [,rrt;une. (tlisbutia, lord,otit:tia, l.u.i.Ziehen *i Opytt:nhcim;
tl,i:tlotrirt l.entit:ulard,progresird,) prezinl,il douii elt'melte somioloEice: disr,'0i;.ri luriiun(,1 (lla..li.r. 19..3._citrtde Soil,.ler.lC6ir. .\.r fpl. ii,
lrnz;iir.
ri{. ropll,us.iI1 decrLbil,,:rceqti bolnar i lrrr aplorrp., n(,rlDali (cu er-c,,p{ia
corriil,atrilii :\lNor eyentmle semne-t1e encefalopir,tic: herniparezri, nins-ciri
r,rrlcu'ltr,loziceq.a.).,1nmomentul in o:l,re $o lidirii, !lin pet, t-rLrnttriirliniepe
Lii sr,irrilbozo in lordozii, crpul se re-rroflectcazit,,iar eOoi, ollatil cn o:recirlrr\,| primilDl'pa;i, ap*re (sll] se er.rcelbei-Lzi)u I lrurrrro r:le i,onusposirrr'rl, o:u'c intereseaz5,
atit trunchiul, cit si rnemblcti:. llolnavul se riiicd,
lxr villirl pioioarelorprintr-o e\t,,nsit' a mombrrlor iD{criotre,a,poitrunchiul
lslt inr:ulbnt in rnod ploglesiv intr-o ptternicfi lordozil qi rot:1i,. lxtr:nlr,
lirrrlr in ou,r'ecapul sc plaseaz:iir]tr,o pozil,ieda tolticolis.sau dc rctrocolis,
irrl rncLnbrelc janpcrioarc se r'risuctrscirr pr.onalio sau in supilai:ic. Acest6
riprrsrrrccetleazii,tot I'cla1,ir;lent- si apoi din troLl l'caplr, in mod alternativ,
rrrrliziiul o lernarc.rbild, variabilitlte postuf.lliir cu rtltudini bizar.e, contorsiorrrrtorincit :icest ilspeot grotcsc a,l bolnavului :l fort fo:lrlc llastic
rorrl)lrirl (Lccitre liiser (1.959).-u ,jIraocooninlirnt ui li,,,j,turL. (.ritrc\\iurmer
(r'ilrr1rlc_liiser)cu-rn ,,clorvn mrcirbr.u').Dil lrricinr lrcestor sla$mer mis-iar
r,iililc voluntare silt inadccyat: si, apllrent, rrecc{)r{1on!,te,
rnelsul
cslrr r.rtlem do.cliticil. l)e f:lpi, se prodtic i.':tlialii toni{ro(in scns de hipers rrr ilt, hilxrlolie) la un grup muscular fa$ii tle alt Lrl iji dintf-un monrent
irr rr,llll (lie siruultan, lie alterultir.; inert s-l qi sug?r,rt(,.i lt accastjl []oa1{,
lrl rr yrn'ba rlc o ,,dismetric a r',plr turilol f i :i !rju.tifilor tonice,' (Riser,
l1r'l).
r lr, iji in caznl boh:Ivilor pr,rkins;rieni st p:)t rir jtfol, ;i l:r, aoe91,i
lrrrlrrr,r'i,kinezii pr,ra.lox:lle.De obicli rn,rschiifetei si :r,i lirnbii nu sfnt
irrlolr,riii, 11.lrs-::r,u
rlescL.is
cazuri eil ccintefe3,lret aceJNorl,roxlizinLlu-se:
r'rL\lliirrrrlir,. l,tl'lu"ari de vor'l|lr'e.i lio rn yr1i..,11.,
l)in,.puttct.d,e"leilre eti,op{rtog6??,ic,
sepot rlistinge mai nrulte tormedo
(lo t{)rsluno:
irl)itrslrt
r) I)istonia cle l,ortiltne agu-zisd,,,id,ictpr.tlicd",ialentificati do unii cu
it.r,,masr:u,lorum.
,,rl,isl.rtrt
, ,elte in realitate o boali, clegenerativii,,
-tleforrnans))
lllosirrril rne'labolicd,
(Wooten
qi co1ab.,19?3),de obicei cu c,.t
t'a-ctereredol rrrrilirl, c'r,r'c
ap.tre ir copiH,ries.r,uin adolescentil(Eldridge, 19?0; Marsrlen
rri llrr,r'r'ison
1974)si cirro poate fi recunoscutti,pr.in evolutir sa ptogresiyuctttt'.r,lizrt
tit .
il l)isknin de tol"r.iule sitnptomaticri est{l mult n-rai frecvent5 qi aparo
.
rfrrlri, srrrrin crrrsul svoluliei rl.nor {LJc.a!,i,toLi
a.la stru,cf,urilorentrapiramiilalarl.(!(livolslr tntt,uti: Ancc.falitrit:p,irl,enicti
(cel
mai arlesea); - Alte enctfn,
.
lil,rrl - Il nrrrfrr,Io
p tr,l,
ii, toni.oa(crr oxirl d0 cl,rbotr de pikli) i - I)e11c.netrcs)nb lutltolo hnl i.r:t.r,l.rt
rc (hou,lu,Lu,i lYil,son;i boa,ktIu,i, lVet I,p htr,l,Striint,pr .)
In rt,ttr rt,1tl,l'rii
r,li,l )sotnitutrslt.r,llit.r,ttrirIrllc
(iuolrrsiu sl)it$lno{j.l,ri[ol(]l.istitlo
(lo li;l ;l.r,r'liitisrrlir,rr),
lrlo irr(,rri,rr.iili,r'i ur)r'(fo
.Il;01,r)zi()t\,
r{Lrtrilr\
|,rrI I I rrr.il,
r.
ii.ft CONVULSIiLE
(i.il.l. Aspcetesc.rniologiot'.
S1r'erltrisdbilt'rlcaltc rniir,irlj irnolrrrrlrrlr,,
,,rrrvrrlsiiklso pl\izitrtii s lt formi-t,tlc acatBe.lllo llol 1li y(uutrlt:;rrlt,,tl\t
corliotalii fi insolindu-suct:l rirrrilrrlr.rr.
;.rrrrlir lotalilatc rnust:ul;ll,urn,
r rl.
,' picrrlcre tutali srrr rcl:tf,ivti:r, siiuii de constiitltti, sirrr,rIirrr1roIrirri,
7,,rr'lirll:,silul!ii in caro intercseazilun gmp rn iir:rtln,r.
ttrtri irrtrll itrrI rrrlrr
lr1rlin 0xirilts.
l. (lon,mtts
i ilc tonir:osittl re,prczenl.iltc
tie conlrrrc{,iirrrrrst,lltrr,prt.lrrrr
o stiu\) p[,ro)iisl.ioii])0 t)lln(, 1i'i,,tllrI r'lrIirl lr.ri,r.ri
i,rlr', (r1lr'oatrtron(l:lzat,
l,rlri,rlr: iigirlital,e,crrt0antLent':rz,:i
urr scgrnt'rrl(.,,r'l){rlill,
srrrr,ilirrrlrolriIrr,
rrrlrt,lrgtr,
lnuscul ,ttilii t0tpol:rlli, JJrcrnplulr.r'lrrr:rirl rrorrsl,r'rr,liv
cilr, l;rzri
,l'' r'oltla(1uri, lotricl gonu'aliznliurr,tliilepsiciglllnrl rnrrlturrrvrtlsir,
lrrrir,rr
, lorricr',itr (iu(', luzilulrll st'c11s;olol
(x)rrvlllsirrlprrir,ir
si hipt'r1,rxriLr,
rt't,lizcilzir,
rrr llrrric sl,r] irr cx1t,r'rsiu,
irrso1it:ir1irlc o piclrleltrlolaLi,rr sliit,ii(l(f .rl!l r
i tr(,i .
!. (l utt: ul. siilt clot ir l sinl r ni6r r ir i it r voluni, llu r list , or r r r r r r r r ,$lr
, , l{\ l
l r.l ,r' , i l rrpl ('r r o1t , li1ir . r . , r r lr , l, ltr. 'r
r 11
'izt t(.)l l) lit r ilp, t i( iit lr r *t r . r r r i; . iil, i lr r , r r qlr , ,
.' 1..i {' r,} i rkr . r nilr i g. u p. nr r r s<r r r lr rr','Lr . r lur ill, rscr
i nl. ii ( zt x, i r l. sr r . r r ir r lr r, r r ir r r r i, , l,
{ rl i N l )l l ri ( , iirr,'r r pit ir i1i r , or r r lllclli, ir t lt , soltt r l l) r , ol) illf illo ( chir r l . r r g. r r . r , r r li
z:.| r' ) l i (l c ( , r 'lr rr r I r i r r r r r llo r r I i oI | sr r sllor r r llt r 'r sliiI
'lr ii t lr , t 'igilI r r {, i, , li, r , , r r r r , , r r
[[l !)t l i l l l l lr olilt r t ir lt 't r lif icit f ( , i1,[ i i) t ol( ) gir I t I t , cl! r r ilr t r ilr , sllr t , ct lr r 0lr ic|t
r' 1ri k' pl ,i ci i .
r\r' ci i i r I r r t r r l'r lir r r nr r r ji,( lr r r r ir , irqi
, ( r llli{r ii) I n) 1.$i ir r r lr r , ir r rrrr r , r r r illolr , r r r L,
Irrhl :tu.ri ..tt r : ut it loqilr ';lt ) ( lr . lr . t lor r ii lir lr r r r , r lo t ur r r vr I I iiil sr , l, ( , r r ll( , 1, r . t lnf
r.rrl i zi nrl folr r r ' l'r r i. o . lr r r i. i
. ir , r , lr ilr '1r si. igr , r ( 'r r r lizr ilr , ,llzlr , lor r ilii, ( r r r r r i
| ' ' rr' l i i ) l )r!'( . 'lir r r l |or r Vr r I r r ii|r.r'l0li( 'r '; [ r ) ( 1r r r r t r r l. . iiL,l( ] , , ir ', rr . lr r r i( , r t
lr il f ii1
:10J
,{{rg'(r'.rul , i. lr,t.irr,I'l,r.rlitrl,(ft,vulliln'.,
lrrlrlizitrrl sl,ur.cd,
dtt ril,tt rpi.lrnl,i,
1{)rior}
ohr)i(:;.) (r.rurkr'i, rirrrn.p'r'gr.aii
Jil
cxistti
ir.irtii,
i.*iir[,,r''i,,irii,
t'rri.ir nr,' t'r.r.* .[oni.L,,,t,pit,,,siol i il;i; ;iC;il dou[,fon'o pot
ut' roc'r,'ioci
ri sa,'Ibcrr,i: r,J
rmi,
;:',fl
i:llii'i i.i l&"'"t#,#?ljlli".",ln,1"b
(i,iJ.2.l,roblcme de diagnostic
etiopatogeniegi topografir:
.I. ln fal;a-rlnei crize conrrrlsive.sepune in primul rind importanta
Jrroblcmla sl,abilirii dacXeste
g" d".ir;
sau, dimpotrivE,
'carepoate
{frc{, este rrorba de o cridd,conaalsiud,
"o+?
"pii.pli";
neepiLelttiid,,
s, survind,
(pgloyier3
rriio.'rsrsr: 11 crizd,
ni ",irnr,.,'
:,1")11."-i]"3::rj,.:j::]l:!1"t"
r,pllr,pHil
lir,tr l'lrntl tttic llclor prtllrgr,tril.
rlr,uztLrotgrr,trir:r
Vottt I'oztttrtil
t:rrl6
rrlr Ilr\lv(!ll, (\rtln otiztrlot'opilopl,icrr
lil ttttgrr,t'i:
I ) lll tnt,nqo.trn,ar'.lulo1xtl,iu,
l,m,ut ,l,ittd,(pt'irr frr,ctori itrlrtIlrrrrl;rr,li
olrnl,o.
Itrlrrli) r'gl,oc:urzlr ooir rnlli 1t'rrrvontitllr rrcolsh'1,
virnt'fi,,I'txlto sl'[fio orlrrr,
rlr, rr *irrr.;rlii,tr,4fi.r,ir( hi,lnnit) n,aonotu,Lil sittt tlo h,nnontgi,i ottrclru,lt utu,
I l t'(,hn.oidick0,Ittovocirtullritr:oircullln"utlooortlottttrt,ttitnotrulliirloculrl
orrrIriIir111|,
lt'l,vr.r,liuprolurrgit, munopot'o lllutalo do tlcga,ju,r'o
foIirL'[, rr,lrli
,,rt,, rlr forctrps, vitlext,t'it,c{,io,
cxpulzii lrtltorioilso (prczotrlt,l,ii virrirrlrHr.,
rltrrlrxrii,iror'{,ioutcrint'r,),opora,{iicrzilricne (prin soltimbtilo ltlrrscil rlo pro
,rtrrr,), ltjliziIr'o tlo ocitocicc, b]oo:llcit,cr'tilol rcsplriltot'ii uJo frlt,ulrri lrlirr
q.a.
rrrpilir(iu tlo lichid arnniotio, rlpl,urii, tlc pla,ccnt':i1,
)! ) .Mani,nllitre,s,iencefa,lita.lcDrile: mtningito acutu ba,ctrrt'iotronrrpl,L.r,,
r.rrllI rr,Ii1,on,cnto bactcricne, viroticc, richettsiono, lucticc ntc.
ii ) I I em,u,toama
subd,urale(fotrtc frccvente lil sugar, pinr),lt 60'/, rlrrlrr'i,
\rir('ui [i colrb.), angioame (28o/sdupl Arseni 6i colab., 1071).
.l ) Putapitoza(cisticercoztl,,
hidatidozd), do ascrncnul l'oir,r'l,o
l'rrrcvcrrl,o
lrr rtrrglr'(Arsoni .1icola,b.,19?4).
t),Llleence,faloptali,iTtri,nJactoriprenatrali(careaunoliouirtitrprrr.iorr,tll
{l|z\ ()fiii.r'iiombrionarc 5i fctale) : a) Anomalii congerlital.a
(iuolrrsivil,lroDtllii
.,rl'rrr()zonLiu,lo),
carc produc disembliophziilc {ct:r,Io:mlrlfOl'lllll{,iir: r':r,rrir,rrrr
(rrr'r,('rfitlic, oxiccfdie, turicefalie, scafocefillie,piatiblrzir., irrrplr,rirrrr,,
lrrnil:rlii). b) Malfortna!,ii cerebrale(microgirie, polenco{alic, tnlllirlrrlr,(ir,.
\r'rrrrlrf( lltirrli). c) Anoma,lii occi,Tttto-ceraicale,
<1) Mu,Ifor,nru]iirtutturtltn'
(i,llAi()rriLliozir,
cerebro-trigeminali,,
boir,la,
lui
Lind.a,u
d,0.). ti) AJit,l,iu.tt
i
_
i ntJiilt,
1i tel&urfumoza(prin factoli gcntrtici): la.*txtd
'ltrnrtlrLhol,.ice.feXale
,{rrIr')tirIfonilpirul'icii, sinrlromul lui ILutnup din por.Itirr,lrclll,liot'l,sol,rrrzir,
l:rrrrilirrlii
diiuzii ctc.) ; lipotlistrofiilcsauslingolipitiozdo (irlio(iir,IrrrniIirrIIr,
,rrrlrrrlrrlic;i
a lui Tu,y-Sacrhs;
boala lui Niernlln-PiokI gir,r,goilirrrrrrrl;
lrrrrrlrr
llrl (liurolrol el,c,). f) Atte, aJeeliuni,metubolicaeraLlil&re: ftrlilrrriotrrrr,irr.,
lr,rrrrrrr.isiilrnliir,,
zlciderniahiperfolicii, piridoxin-tlepcrulcn{,ilnou-rriiscul,rrlrri,
r,l Niutlto&megcnetiaeau tulburd,ri ale formulei, cromozomi,o,Le.'
rirljrrrrrrrrl
lrri lt linoftltcr, silrrlromul lui Patau (trizomiu l) s:tu ttizolni:! li, lb),
rt|||(||{|rIruIlui Erlwards ('l,rizorniaE sa tlizorni:r,f 6-l.fJ), itli0{,irr,rrrorr60f,,l(lir(ilizorni:r,27),h) Infec!,ii materne(lat.srltoli or,rrptivolr,lt.rrrrrrrrri,rrrrilrr,
rlr,, rr,ltirboli infocfiol,so).i) Afec!,i.uni.
paratitara uLl rnunari( rxoplrr,xrrrozrr)
II IIr.lrIrI rj rrrI IIr
,11I,)rtrr,[tlopta,l,iip,rin aplenlitizi,ci asu,pra norzci.' tr,trunrr,t,isrrur
rl{\ lrlluurli gosl,ilntc,iradioli cu rulit{ii Iioontgt:n. k) '1'ttlltu,rdri.
nu:hr,hl,irt
ttlt lunttr(\ oa;'o pot prod[co oncelirllopll,iiirrla,nl,ilo(tlilr,hoi,,lirtrrl,oxir,ozi),
t'lt.). L) It)ttctfu,lopuli.iprin aJenl,iu'ni
ambrionare6i,fttuk ltrit irloorn1rrr,LiIrif rlrri,rrrlrr f,rct,rrr'-Zfli,
n) ALli faaktr,iu,ntennktll(vllirrirr rltrr
ou ic1,<t'rruckrilr.
lrr li lrilrrxrfioo otc.). rr) l'rcrnd,tur,;l,atp..
f/ir lrol.llil,scul;vrr, lrtrhrti sii Icctrtrolrilorn oonruls,i
otr.,trt
ilt
tr tr *in,L rtt i tr..t,b.iI ep i.Lep lioe , drlr orlrolutooli pol, lilsrr,o plorp,
'lr rzi(irrtrliklrl,irri :
l-,\pttt lu,l,ltoltttl,u,Lrti
(,,sp/rsl}r,c
de pl,ti.n,s
tht sLnolol,lt:r,llrri Itrrlrr,tlrii
l,r'rvr';,l'r,rr rHil lio tlt oligino llfircl;iv-orrrofionlli,
oit,o t.oirc(io
rlrrlllrrrril xtrit
rlr, rrrrrri,,.ll|rrsc srrrl(xilrt,n,!tiilzil
s1trsrrrrilrlr, lrlitrs,itr H|r,r,lrrlrr
llt.ri ittlli, rtpol
ttt ltolrol,tr1rI'rrftttuIr,,
ott irgii;l(ic, gtr lril,jri rlirr piliglrrrt rii s1 1vi,ril,rrliilil,
rlrau rlrrlriprl ltrrlt',_lrt rrxpilt(ii rlitt crr itt co rtrrti1tt'olrtngilo,
cI irlo(lxrJ,t,tl
Itrtrrlr',r'rrrtr.itt l'itttr,l,
xli|lr,lrLolt ltI Nl)itsttt
rrl gLllrri,rl0 tttlrlrrrlrrr,ivll,tr
rlr,t'|.
Ittlttlrtrt'lttt|t,irHlisi(,iclt ('lrrlrrzii,l)i(\r'rl(rrrr
rlrr,,lIrrr\rl
llt[r1rylrrorrvrrltii.ltttltr'1,
r,tlr,yrr,
rrrirr lr,, lrrllll rt'irrlr,riln ltr,t tll, litl,rlytrttt,r[
r'tizr,hr|r,rlr. V l,i.rltlh..
;::::l:,ii3-X,:fi'Jifilj".'*lffffHi3,.f,,J.,F,;:,A{:l{;.'\f"n,:J:;Xf:;,,;
tt(iriLc
urenl'ica.
s).c on,)itsiiteah cnceJo.ropiii
h$itlt-plitita.
6) centoutsiile
i i n. k,r en ;o, gra uitli ad. T Cott aul s iile, rti n' i nt
)
or tta! i o ;t tian ; n icd. Z1 Coo ii t
xiilt din tu.tbur,iiIp pnrloarin"
lr,ctrnie. pi*uJbniiop,,,f i.iOi**
;.u.j.
ll\ Unele conrulsi,i febrile.
.. .l)itgnosticul se orienteazi. uneori relativ ulor itt contextul semnelor
.liri.. ;i de h,borator, alteori imlrlicind i"""stigalii
Aeoi.",lit dc aminun(il,o 6i.,atente.Astfet, Gastaut.(19?3)._$i
eop""t"i" "1i
ffSZ6i;" pl"_
lrrrsd illercnllie.eaclintre ,,atac.l ckr.epilbpsie.''lresp"ctiv"rtrU.
A"?""r,ulsie
tonico_
,,'"uri"l,i,ra',lll,ll'lll[)
propriu-zisi,,
ads
i'ouiir"
u",_"o
puor,"o
!i
t,gpilupsia
f|rzr'tlr ctre sc repoti! dc o aiurd, mai mult sau
mai pulh cronici {i care
rr'zrrlti-r,rlin..dcsci,rcarahiporsincrcni, a unci populr,'tii';urotrrle.
O crizi
,,rrPilo|tic:i" ,Iic[', precum l-r crizele convu]sive accidentale ("o a" priJe
rrrrckr conyulsii febrile, crizele de.ecl;rmpsie p"o"pui"lif
tolice,
rrrcl,tbolico $_.a.)nu constituie o veritabili'epil"pri.,.';;p;
"r,i"tu
cum
nu
constijo
1rr o voritabilii epilepsie nici rcpetalea mai-muit
s;u ;;i pugin frecveni.d,
ir lnror crizo conyulsiye in crtrsul.unci afecliuni acute (eniefilopatia
urerrri.i, rlin boola lui tsright, encefalitele acuti). CrirJ"
.irii.pt,"e veritabile
:rrr, tlrxri, un c&racter iterativ, crnnic, ele repetinclu_selat
anumite intervale
(r)rrr,ii!(jllrte sau mai lungi).
I flngem atjenlia indeosebi asupra oo,nawlsi,iloy
kiltoglicemtca din hiperin..
strlin.i:tnt.uL
t u_ncftonalgi clin kiptirinsulinismul orginl, (i"oo
sru ca,r(r|r,)nt irJtcelulelol belrapancreatice),
Caro tle obicei se confuncli cu epileprrirr,.l,)xist[ insii, citeva elemento care ne pot orienta
asupra ulei conmlsii
li;xrqli..rnice: a) precesiunea crizei piin unele simptime
revel&toare:
1rrIn,r'c, tchicardie, tremurd,turl,
hidriazb,,
patiitalii,
anxietateI
l)).ifr ist,(ilL!,a
unor simptome interorilice,_ca : so-noterrali,,"concentrareilificili,,
itrrilrlrr'rru,
ir,1;entiei,a mernoriei qi a inlelegerii unor nogiuni abstracte,
st[ri
qi de dezoricntare,
aprtie,brirtipsihie,irclerenfi, sti,ri de ag!
il:li:,1,.1,,1.:
I i l I , li\ ( ll il { l ( ' S l V r t a t e .
ll. ,\tumar de d,ataetiopl,togenice4n,uieele conaulsirseepileptice
A .. ()r.i.zele
epilepN,ice
conuu,l,s.ira
la sugari.llajorita,tcLlcrizelor convulsiyo
...
itrlrrrrlilrr
'sirrl;i.r'(itrr r.r.pi*r'r1e.ort' cunoqtinfir,itr,u cro obnubir.,rc.Nu tre.
rrIr'1srLlil'irr]rrr}iu|ir{,rr,rreos.llir,iicu oalo copilul mio pr.zitrLit
0 cr,izit,r.lo
204
:10$
irrI't'rr'.olclrrirlii
tu.rtllitii(<:trrrprr,r'i(irLr,(i lrrrri,
I i) I')pilr'1r:ttlt,:r t rttrttt,.r,i.tti.
| :, Nni rlrrlii' irrrrrrrrr,lisnr)
r,rrrr.r'r'rrlizrr,li"r,
rkr cica,1,r.iccu,
irgrinuo-sr,rllrra{ii,
rltr ll.Lrrrrzlr,rlilrrzrl, li
rriu r':r. il,r rrr.lo conLplicl{ii taltlivc (rbr.str
, r r',.1,r':rh..
r.lrislUli.l.l, |ir ,\l.r,.rrrsi {,,,1irt,.
([t17,{),m jorii.atela,.cslor(,rizu
,|itr i.rzl i/, dupi l.ure ur.meazd
r.rrrlrlr. I.i1rllitlr'l t irl (.1!t,,/.
crizclul,ocaJe,
i,u (1v('tr1,uli,l?i
generalizarc (lfio/o rlin botnavi) qi alte tipuri de crize.
2.^.(lr'izale.
c,pitep,liaa
An meningite g^iencefalite,foarte frecvente l$ copii,
'.'. -irrlilrrr.;r..i .h aduUi. eLiologil infccfjors riplasinduse prinrrc orim-elc
rri.i r':ruz(.irupL,rtanloale rnanifcsllirilor:
cpil cplico (Gudrn-urLrlsson.
tC6Cr rt:rt.rlr.,{r'rnni1i cotab.,1C78;.
?n cazul crizeloier,ileDlice
sur\.cnitprLlr-un
lorrlcxt irifeclios acut sau subacut, v:l trebui sA ni ginaim h: a) Meningite
srrpural,ol b) Meningite virotice (vezi anterior) ; c) Encefalite'de divErst:
rrrrl,nri (viloticc plimitivc sau secuudare) at) Meningitd, triberculoasi,l
I
r,) .Abces ccrebral.
lrr oadrul rnanifestii,rilor epileptiec postmeningoencefalitice clomin[,
tlizclc con-vllsive generalizate, :liit iu pelioada acutl u, bo1ii, cit mai ales
irr cr^rr,1,a,r'divf.Trebuie sd,nu uitlrn faptul cL ulele accesepot si, survini,
rlrrpiL,luni sau ani de la sting_ereaprocesului infeclios (Arieni;i
cotab.,
l1)73; I'opoyiciu ryi colab., 1076).
. ij. Orizele epileptice ca simptome de ilehut sau I,n cursul et:oluliei procesr'.lrr,r,t:pamsire intracraniene.
,sinl deosebit .de frecventc, putintt ijungo
a,dult(Arsenisi r.ulrtb..l97S). Arti;|,
lirrl .l:r50o/udin rolalul cour-ulsiilur-lr
,.rizr.lr.r1J)eptir.ed.in pelioarJade tlebut a proceselorerplnsire intrlcraj
rrir,lr (22o/o)reprezinti un prelios gimltornde alarmii,, cu-tleosebiti, valoarc
l,r,rrljzrrto:rre.
de focar,putind udpseaintlicl qi natrrraprocesuluie\ptnsiv.
rr |ursnl rjyolutlcr proceselor oxpansive intracraniene (360/o) reprezinti
(l{r lrrulto ori coirsccinla fenomenelor de hipeitensiune intracraniand,,
pirt'zirulLr-si rraloalea precisS,localizatorie (Arseni qi colab., 19?8). Cei(r mai
r'pilcptogene tumori cerebrale sint cele situatc in vecinitatea zonelor moiolii .si scnzitive ale cor"terului, in specia,l astrocitoamele, oligodeldroglir'irr)r{rl{', rncningioamele si glioblastoamele,
l. lrizele epileptice prorlase d,euJecli,unile aasculure neurochintrqicala
lrrr lrlrxlu{l irl ungioarnelecerebrale suprateutoriale, in aneurisntele:.rterei
|rrtrrl itltt irtternc si alc rarnurilor acesteia, \n boalo Bturge-Weber .si tfuai,rar
I tt.ltt ttttr,[otn,
ul prinr,&r i.ntraparellckintdtos (netmuma,l,ic).
5. (irixtle e.pilepticenn pt"oceselainflatnatorii, tt eurochirurgicale se in.tilrrcscirr : l) Tuberculoamocerebru,le(fcrarte frecvent - 850/odn cazuri dupd
,\r'rcrii rli rrolab., 19?8); lt) AbcesecerebraleI c) Ifai rar in araltnctid,ilawiorhir*utt,l,icd,qi in go'melesifil,itice.
(i. (lri.zele e,pilepticein
Tsarazitozelecerebrale: a) Cisticercozacerebrald,
il
l1l')1, tl, sirnptome de debtit, fie focale, {ie generalizate, dupd, Arseni ryi
;i
lr rfrrIr., t.f)78) 1 ls) H iilatid,ozacerebrald.
ii
7. Ortzele epilaptricet:ascalure ss intilnesc indeosebi la adultii mai ln
vilsli qi la biitrini, fiind realizato de: a) Ramolistnentala
Tsseuotuntorale1
It\ INnlr.fal.upa,ti.a
hiputcnsid ; c) Unele hemoragii cet'ebrale.Debutul ictilirr.r)r si oonlioxtul clinic sint rcvolttoale pentru accste manifestiri
r.1ri
lcpl,icc.
,\. Ori::i.r api.l.e;plito in, bolikt rlrttontnlite $h1t m.ult miri lrur:
tJ I)itinuqit, t:r'rrhttkn,virtt,ior:ltntirii
n,Iu,i
i b) It)pik'psinmior:l,onicd,proTTt*irnl,
,ii
ilil
il:
,il
{l
it0tJ
ry
PfiOI]LEN,IE
DE DIAGNOSTIC
{ . tmruLBunARiLE
Dltsnnsuitltt*tCu
vti Ir'.
?. I,lristii sittttlii in ctre ,lntpt,le si sa prr,'t,slt:irle Dneei| alte seny.e
trrrrtrlrtli.ae.si, clcci, au t.:r,ior,.r't,
,[,, si, ptonl s, mnQl : .,t1 rLrtlerilo mu:;culare
rii ru 1icrrlrr'..ir pe|ioada i.le inr.-ir,zieprcp],ratitic:i a poiiol.riclitci ir,iriLrrio:lre
rrrrrir_;
.lr) -llgiile premonitorii cclvicale s.lu dorsrie il hern r,tornielii;
r).l L rluiilr r inr
r olioi. , ti .l d e c l c b u tl u n e i p a rl l i z i i fa ci al o;ri )
el gi a i rr' rugural d,a
rrlri lrrllx's zostcr I e) drlrei.ili. clhiJicle c.r pr.edoninr ntil noctirrnd, in
irililis l rrr'(l1ilu; f) duierile lJ Lirlrl-rre di,r r,,jrnpl|simrilu medulare.
;j. lf rirli,. siltutlii in cwe urrrtlr c;t ea, prii inpari(1jqt:L lor,, tarita_
.
hilt .lltturc rl.in.icenle u,nor afer:liuni I i,1 forrn r, ,le.ici, a crmplesiunilor rneilu_
I rlr. ;, lr ). l"r'n r tlgiui. a
qi polineurop:ttii ; c) forrn,l algo_
.mrof
Il Ir|| {| ( ||||( . : | ; l nr . v r J \tr-l c p t:l_poliner-rito
r.tn tp p ,
L 'L.'ul.bn
rd,tile de sensibilitete subiectiud, pot sd, aibti o ,rnure uLlo&re
.neurologice(Guiblrt
t tltx'.n
lt)4..rtu, nnor
;i Guibert, 1g?4) ; :i) Terino_
-a.fec!,itm,i
rrrrrlqczi:t,srlmnalati
poinihe eyoc:lrea unci ,siringctnielii
de ci',tre
-boin.,w
rrrrrrrr rrLti sindrorn siritgornielic;
b) ll,el.ltarei1 rlc ciitre boln:,lv-* unei
irrcrr;r,rrilil,i rlc lecunolstere a ohiccteltrl cu liuturul pipiitului, rre face sri
rrr. qrrrrlirn 1i 1:r,o agnozie t:}ctil:i, plr)Irie luui sinr1r'ornp rriet:li; c) Rela_
liu(.:r ulr,'r'rltreti (cuntlnut-, dar cu execcrbliii in p.r.rorisrne ittloce hemi
| ')r'|),,IiLIr.,L.\ir{cl.rtu rlc prl}utii, precurn qi cu 0 coior:lturii afectiyl clezil,
grt,'lrilii) srrsctci.uziidonri p0siitiiitrili : - l) rlur.ilr.e tzl:lrnicii oLt c..lractor
Ir.i;xrr'1rr
Iic I - o IcziLLucr, firsciriLlluluisliir't.'hrlic
(ltunci cintl sc colstrr,tii
8i o l,0u1l{)rr,lrrrlit0zi(r.
5 . ( lq. r t t , l. u' d: 'l tl rrtl .r:i i l o t (rl i s t,s l t,z i i i rri )t rtrj rrri r,si i l i o l ri rru
r,i ,o,
j tccsi ( ' [ I iit t r l t t lr r l rr,i r,ri rr l i i l rr l rri l rl i v i s rr!l ri i l i ' ;,i l ;r rrs;)r' rl r: 1l ,t,ci z
,,rni (c,r,l i ,,
Irtl tri r r iiI r r li, s r , r r z t r!i irl o l trl rl s trtr rl c l o ru ' r,1 r.,,\rl r" strrr rJr-rl rr,r,r,< i l r,ri trrti rc
:i II)
llll
( ) rrrrrrr(,i rrrrIr
rrrrrt,ililrlrr'r',ilir lrrlgrn.rlrrkr
tlbotico: ?toestoaap,rt sul)
.nprvriu,lfi
lirrrrrri,rlrr .r.izo rlo silg.lllrrri s:r,rrIrrlgr,r'Lltrr.i
tl. int.usitate foarte-miro.
int,tliitttl Jtf tt'rt,itxll;0kr
stirr,lri0rrlrri,
rLr obicoi lu :,mbele membre inferioa,ic.
uli nlrrsin.f impul uoplii-ryi nrxxrlinrl la tratl,mentele antinevralgiceobiql
rrrriirr. Asrrsto rlureri au lu, bilzr-r,mouingoradiculita postorioarf iudtic'd.
(l)lnlt,esiuneh rldiculari dir, doui tipuri distincte de durori: durere
rlc tip novrulgic qi durere de tip mialgic (Alexaniler qi peritz).
| )urcloa de tip ner.ralgic e o durere vic, ascutit*, pltrunzdtoare. manili.l:tlit |rt o tln,rn|1sx1'seleclric5,$i este asociaLi-cUlarestezii. tunnicd,turi
^la
nrr,rliirrrl
.rapid pe inLrclgl dislribu{ie a rddi,einii (tle umir in jos, in tot
rruuulx'ul superior, pini la tlegete). Ea este maximi la periferie, bine 1ocali
zrrl;ir,rlistal, iar proximal e r1ifuz5,.Durerea do tip ner,T:rlgicctilrintle de la
irrcrlut lotrnembrul sau se poate manifesta nrimai in reglunea-proximalX,
collorirLrlulterior.
[)ttrerel clp tip ncvralgic are doud aspectoprincipale.
-slrpel{iciali de inlepi,tur5, cir acul in zona perifericd,
.r'rrrr so ^o.senzatie
intinde proxim-al. Atlesea ea este precedat* de amorleal5 -qi furni
(,r'il,uli ; ca este produsi, de compresiunea iibrelor rddd,ciirii rloisale crl
rl isi libu{,ie superficiall ;
- o t.lurere situati, profund, constrictiv5 si limitatd,, c&re so accenLrrtu,z:'i,
ln mlqcd,ri. Este asociatX,lrecvent cu o redoare lroiurdi
localizatd,
rlc r ricci 1a,git, umi,r, bra! I rnreori durerea se intincle pe o regiunc mai
rrl,ro i ol estc provocatii, de compresiulea fibrelor rldi,cinii dorsallece inervcrr,zir,lolmaliunile profunCe: muEchi, fascie, pcrigst, capsule articulare.
'l\rritoriul durerii radicutare esto mult mni intins decit distribrrlia
rkrlrrlri,otnului, deoarece clurerea iradiazd, qi in muqchii inervali de r[cl],cinil lr,ftrcta,t:i.
irr extremitatea supcrioari a membrrrlui dispozi{ia fibrelor nervoaso
csi,o mLrlt schimbat5,, ilatolitii aranjamentului comllicat al muqchitor,
rlirL ou,rrr,
c-alzii,nu e.xistd,o suprapu:rere topografici, exicti, intre distiibulia
sltp(nlioia]ti gi profund5 a fibrelor rddS,cinii dorsale.
.ltrxlrindereadurerii in arii ce depi,qescdermatonmele clasice ar fi tlato_
.r'ilri,qi intcresii,rii fibrelor simpatice din rddicind,, yom putea observa astli.l rlurrrli tle tip sterno-cerwico-faeiaL(datorite compresiutii la nivelul C").
fi liipul costo axilo-brahial (datorite, compresiu:rii la nivelul Cr).
(hi(x) compresiute pe o rXili,cini cerwicalii,inferioarA, poate ila dureri
il rcgiunoa_pectoraiS, fl_vom av_easimptome dc pseudo,angind,pectorali,,
il rirz ('i durcrea este Iocalizaldin stLnga.
precordial5, poate fi dat5, de hernia cliscului Cu-C,
.. l)urcrca
I acest
rlisrt cornprim5, ridi,cina care formeazi, nerwul toracic anterior' 'medial
(t l, 1i 'l\) sl],uner-yultoracic antero-l:,teral (Cuqi C") ; Ice$tiJ, inet"vei],2i,
marelo
4i rrricLrlpeetoral gi astfel bolnr,vul poate rvca o clurete localizati Drellrt,lirtr:.
'r 0i
l)rt'rrrort,
rll l,i1trrritlgio rrsl,orllr,l;rrlil,L
rrrrcisli,t'i rlo lrilrrrloxrril,irlrililrr,lrr
lr,ut'ornllxcttllr,tii,
itr rutt;clri, nlrtr,ro
r.Irllrrirrii
[rlorlrriti,prin cortrprrrsirtrtoir,
vr,trlfrrlo.l)il llr, tnrrlrrlri,irrrprrlsrtrilo
sirri;oorrrlrrsrr
rlrlrlrilxrl;pr.irrni,rlLr.irrrr,
,lrrlrrllir,crtro$llrrnzir,torr,r'o,
I)rrrcftlr,trsl,osl,riot,Ioolr,lizlt,l'l,
irr rrtrrgoltiiirrrrr.vr,(,irlr,
rirlrioilrilo vorrbrtln oxcil,rrl(fqi uir osl,0abolil,ii ciIrl. r.tlrlir,r:irrrr,
tlors:llrI rrorrlr
sllu sgotioniltii,.
; rrrrrziiI.orr,loosl,o aucgl;oziir,l,ii,
liidii,oinile vontr':r,klsinl cornpusndin {llltr groa,sooo l,rausrnil,irrrlrrrl.
,rlilo r[ot]oilrc Lr,muschi i1i din fibro rnl,i subtiri oaro pol pftrrlrlco o nl,rr,r'rr
rrrlrrlir.i in fasoiculelclnuscuLtr(r,I)urr:rilo obscty:tttr rtnoori lrr crrrltrrr^ni
rrrrr,rr
ri,tltrcinii ventrale uu $lnt inso!its do corrtrrrc!ii nrusnrrlirrrr,
,1,'rirr,.,,'
,l(' iirnt, provoc[tc de exr:itareafi]rrolor radiouhro vontrilkr lino.
lrr regiuncr ccrvicalL, o hernie rle disc intru,fora,rninn,lil
Doll,lorrrrrrrri
irrrr,
trr'orlrrooo comprosiune selectivi, a r5d:li,ciniirrontrtllo, tri,siirl lrl,rlr1,
,1,'r':rli mai rnu[t s,lu mri pu{in intaotii. Acclstii, ovontlrl.t,]ilill,(\
Irr{xlu.r\
'' rlrr'{.r'cdo tip nrielgic. ln astfel de cazuri nr'. cxisl;ii sullnrprrrroirrirrl,r'r,
,',rrr (lo distribuire a durerii ;i dermatom. Daci, ]rct'niu,rlo rlisc rrorrl1r
r,irrrII
rrrrlxrlorridi,cini, cxistd,o combinatio ale durcre dc tip millgio iii rrovr.rr,tgic.
llrrtrrnrt intereseaziio arie mai ma,rs decit cea I unui rlorurrrl;ont; rlorrr'lrr,
rlr,;lrrlardistribulia durcrii corespunde dennatomului.
Nllncvrele pentru proclucereadurcrilor snu acccntnrlrcrlkrl sirrl lrrlkr
lrrrzi{iille capului, glttlui qi bralclor, cum ar fi: intoarcorot or,yrrrlrrisprrr
rleafectatdqintoarccroa capnlui spre pr,rten afecta,l,iirii pli0rr,rr.l,
I'r,r'l,r'it,
pr,sirrrrii pe veltex; hiperextensia coloanei ccrvic:r,loI floxirl coloirirrrir.r,r'
r rlrrloI cornpresiuneaexercil;a,t5,
asupra gitului I prx'cuilirr,rr,lro
l'izrrlor. Hpi
rrr'rsosiru percu,tiaparavcrtebralS la nivclul leziunii ilpliur,rrrr,prrrsilrrii
I
,lri,,ilrlr pe trunchiurile plerului brahial (durclo;t s,rLr'prrrrsl,cziikrrirrl
.r
in aril tlerm;tom ui rospect,ivsl,u pc itlilorl,gtt,tr,r'io)
1rr.r'roptrlo
I Ir,I rIi rrrr,r .rI
t,r!'siruriipo mu;chinl scalcn, Atit in leziunilo rrulicrrliLu!roil ;i irr crlr, rr,lrr
l,lr'\ului,-sint ilurcri pe trunc.hiurile plexuhri su,rrprr rnrrriclrirrlscrrlr,rr
,rrrlctior'.In leziunileplexului cif&ctelistic esto llptul oii sirnlrl,orr
rrrlrrllrrl,
rrrlrrrrsilicate
de miqciirileqi poziliile umd,rnluili brtlului. l)rr,r'qiirr llzirrrriL,
rr rli{rLllilremi$cii,tilemembrnlui afectat ryiin speciilltr,l.o
bltl rrlui (rlrr rrrr,rrr1rlrr
,rrrrl so imbracii sau se pia,ptF,n5,)
decia,lqenzi,rlur.olil purrtr.rrl,orsl rrr,ri,iv
ili limiteazii,accstetipuri de ni;ctrri, frr,pbci,rir so rlirl,or'rr;rlirr
I'rr.iotL1,Lt1
rrrrrri
,prsr.rr muqchilor scapulo-umerali,qi nu trrlc{iunii po t,r'rr
rrclrirri.ilrr 1rk,
_al
,.ttltri.Mi;clrilo urnlrului nu au nici o influcufil, ruuplrllrrrzi(,irriliirli,rirrilor.
\r'r,rrsl:r,
cxplici, tle ce unii pncienli pot sri nri;to tl.ourbl,rrlilltxrl,rr,l,,
crr lolrl,rr
,lrr''.r'ilr'rni,ri po curo )e atr. t|pIiclt,rclrtr',.r"uLiurrii
po blrulrrl:rli,cl..rt.,
rr.r.r.rrl.r
trtrrrliu a,bducfioryisupinaJ,io
cu capul intors corrtr:r,lit*r'Dl
(s.nrurrllui i,rlxfgrro
l:r gil,) (icclan;o,tzriclureri itr nemllrul suporiol. rcsprxil;ir.
I rrtensificare:ldurerii so oblino prin tuso qi striinut, tkxrilurco lrr ptrr.
I r{i(|o clostorobrrrsc},a pr,csiuniiintr.*ab{lomina,loqi intriltoltc i.o. .Atr.ir,rl,rr,
'
ru' pont,r:.oxplicaplin f,r,p[ulor),s0 pfoduco o sl,r,zii,
vonoiwtr furvlsolo opi.
rlrlll(! Di, r.tsttol,$0 comprilnij, $itoul tlural qi rir,d.tioirr
ikr ; oorlplruirr rroir,
:r.t,rrr,sl,l!
so polfo rtlor yr:_rillis
I I'il,ejn,lu-sornioluscopio qi so vir, vtdol cttr
rrrlrr.t Iniclo#r,trrt.risO irtlj.rsl,o:r,zri.
l\plioa,roaplr)$ilrnii po prtrrlolo ntilllgioo rlor:la,ni1cazil,
tlllorj Irrrnr|r^
(.1()nll)r'()silllol,
riuli0lrliirii provoitlriXhipor.rr,lgrrz
ia rnrrgultilor',frr,pl,orr,rrrlrto.
ttrirllgltxrttt'ulll)1,zonolr)(l0oLrlIBlr,ltllr,rrr
ll,Lrrlrrrtriij..l'tttr<il,ol|l
, tltlooltttttttttll(,
trrilllgir:o
rIulotrlr,Ho
r,l,olit, rr.iyolrrlrlrilo rlr,rrrrrlilrr
nitrl,loo.r,liz
lrruvoilnorrrrri.
,111,r*
lirt'ir"1
B ,ll ltntlitf(u,zii,
i'rr,l.luir[.
l)tttrrttlur+r1,rrrrrl'loolrt,l,r1,
Hi (fN1i1x:1,'lllt,g
ltt rtrirt H(tgtltoll
l,lr,
t i1,ittl,rrrrrnll,l,;
rlu 1,t'iroo
rlrr1li1,
i rrl'i I i ,r,rr.(,I i lor,rill crt rrov,rrrri"
'fiimrii^,; ,;i,f[
irrr'r,
liirlir(rrilol tlotsrrLr.Vitttltx'lr(,lr(lttlrtlii l)l'itt itrljl
lr rrr plirt src(,iottirrr.lr
r'ii ltttttriolirrlttlrrllrr(iik' lrx,rr,kr
r.u Ir ot,ociritrir
rrr prrtlr.lr'tltttt'trllxtrtltrtlrtlii'
r,iriirli'iill sLttst,lo
Ititttittt,rrlc r.rlilrt{ir,i. tltrii rtuioti(ltllirn) rrrrlrrii.r,1r'i
sur$l dllr'otji,!jii rcdoitt'eilrtll$orspirs rrclorrrrrscLrlulc
lorlrlizlrlt,r'r..1)r'r'zillii
ilttrolrur,, rlorlurr{urc\irJtiiio des(fii1('it
tc t,rtutintuitle poterrl,iilldin princlt'1e,
Ir)rsr' rulriOlLllll'(r,
t.) I)urqile r:rnlatLalesinl (.trrter]nirat'ede leztrta cordortllclor laierale
ilJ l l)os1('1ioa,r'ot],lcm:iduvei spiri,rii, in special ale f:rsciculelot' spino-talarrrilr,. Sin1,duleli surde, neplecise,lepal'tjzate pe un teritioriu r1ale fi sint
rlr.olritci irrso{ite de tulburlri do sensibilit:rtcobiectiv:i cn l'el.}artizal'e
}e
ltir ll|lni(orp srlu cu nive-l la un anumit segment.
rl) f)ut:orca n,eni,n,gi,alii$e rraractclizeazii plin dureri oel:alice difuze
r rr rrrrloiilc tle ceafi, qi oste deti, in turnorile cerehelo:lrie ;i hemor:lgiile'
suiralrllrnoid jt:ne I durerea mr:ningittlL sil,uati, spinal trstedatoritS, tunorilor
rrrrrlulillo 1i hclniilor de disc ;i se calarterizea,zin priti coiltrootar'ea pilrir
asoc:iatl"lcu dureri pe ma,i multe segmente.
vcr{;Lrbrtrlir,
L:) D,urerile Lalamice apar in leziunile cturc adecteazf grupele nucleare
lirlr,r'alcale 1,alamnsului.I)ulerile se localize*zl pe hcrnicorpul opus talarrrrrsrrlrri
lt:zat,,rrai ales pe fat-i, li pe rnernbml superior, au o accentuata
lrrrrtliltto aiecl,ivS,nepH,cutd,qi se insolesc de lulburi'ri tle sensibilitate
oIirrrlivil,, rnti a]esproprioceptivi,. Aceste dtrcri apar indcosebi irr ll:zinnile
anurne in afecliunile din teritoliul alterei
virroulare ale talamusulli;i
lr,rrliculo-optice I leziunile vascularc tlin tcritoriul artet elor talamo-gt*1iculrrir'i,si talamo-pedol'tltii dau aSterela tulbul'5ri de sensibilil;ate obieciiYl'
cu l.opografie caracteristici, da,r nu genereaz:i durerei'l talamicl propriuzisii, slu goneleazi1doar dureri tle mai mici, intensitate.
.l)urelel t:llamici poate fi conl,inuX cu exacerbiri, sau po:r,te surveni
tliscorrl,inuu. Soarte acleseoriap:Lri!ia durerii sau exacerbarca ci est'erleterrrrirl ii, de survenirea unor excitalii liziologice, liminale sau unoori chiar
srrlrliminal.e.Astlel, drircrile pot si aprrl ll rlpliczr,relupei reci pe o1lraz,
irr lirnpul picptinatului, a survenirii ultui culent tle acr reoe I lrlteori
r t)rrritirr dril'erii cste determinrtd' de excitan!,i senzoriali (mirosuri deza'
gitrllrile, zgomote sau lumini putelnice) sau chiar a unol factori t'rrolioirlrli. -,\cca,sti, integlare in durere a excitaliilor senzitiYo senzoriale sau
ovel'reaction (stprarcacfie). ln
i,*il,i,r', ,r I'ost denluurili, tle citre lead
ilgi I ruli cu tlurerile talamice, mli trehuic emitrtite noi-iunile de hiperalgizitr 1i .lriporla,tie. Il/teral.gezin, se traduce printlo sensibilitate dureroasi,
r.r r,rsivi, plintr-o scidere a pragului durerii, astfei, incit uir stimul ile intensir,poduce^tlui'ere. Hiperpatia este tot o hiperalgezie, in
sillt(, rr({l-rrreroa
tlurerea
are o tonalitate afectiYd' nepli.'cutd fi, palalel, e\ist6,
r.rrrrrilsir,
I,rrllrrrliirj. da sensibilitate obiectivi, in sensul unei hipoestezii mai rrult
;.rr,rrrrrni pu(in accentuate. Iliperpatia apare foarte adeseori in cadml sin,lrrrrrrrrluilalcnrio, al;turi tle duret'easpontrni'
11 I)urerile [isceralc. in eazurile de lezare a dilerselor organe intcrne
lrohraruiiecuzi, rloui, categolii de senzalii nepli,cute : pe de o parte dluerile
l:uu,|rr ilc sufclinla nt'rnijlc citi, a forrna{iilor recept'oare de Ia nivelui orgarrrrlni rtsDectjv, iar p.' dc alti, parte, d'ureri,proiect te (re.ferite)la riivelul
As1{e[ bolnavii cn anginI pectomlS,acnzi' dureli in rogiunea
lcgurrrcrrt^r,lor'.
ll r'ocor'diir,lir,qii pe fr,tl intorYrd,tu brllnlu.i sting, srferinzii de ficai; acuzztr
dtlef i ploicctato in
ilrrr','r'iirr rrrrriltiLl rlrcl'l, bolnavii cu ol'jzc tenalc 2louzil,
pon'rt:1
Yrulncl(f ,zonel0
t'oritorii
A&\$1.(}
oljc.
itrghitro"sctirtn,L'l,
rogi {)a,
'lo
Irri I latult'.
1I4
Irr pt' rr r , llnr , t t r . tr t 'olr t glt r il,cl, lit t t t t t ', llt , t lt t t t r r i r 'ir it r ct lt llrsil) li illlilnit l\
t t r lt t t 't r t i vir r lr , t t l'lrit t t 't 't ll
r| l 1rrrrrrrri i l r, f rt\lit r ( l( ul. t i] ( tlr t lt dir t ', t '. t t r t( r t t t t lr l: t t it
ilr
r
r
t
'st
'r lt lt r viit 'sl'llt t 'i lt ot sisl'r 'tlrr ',
it
t
so{
lt
t
l
tti rcrtrl ri gi t, slt icii, it r sf ir lr llr rlr r lt lo 1i
rl rrr' ,.rrl ,ti go t ir ,1t ) r il'lllr t . t lg It I i tt t t rI t I It I i rr. A. t r slt r lt it lt r t lt t t t 'it zii t r il t '\ 'it , r r t t '
.rl r ! rl (' i :r zik: , cpuizir t t l 1t c lt olt t it , v. Nt t t 't r lcilzr 'i,llt , lt 't 'it lt iil olr iqt t t t ilr i' r t
,rrl i Ii rr1r,l o: gr r . slliir '. I t t lt i, , t , , ( 't 'izI l'r l' gilllli( r ' lit lr t li|'r ' i| t t t lt i t 't lt t 'r st '- 'lt
,rl tr ,.tt.:e t: iicar al. e: ( t 'ila . l( t r inlli e; i cso. f ur ingilnt ' ( r lt asnt t ' t llt t t 't t t it sl. lt t
l rrl i tr{ r si csoit lg, ct t icnil la dcglut ili( \ ) ' oil( t l^t iat kur '( st r t t z, t t ( ii- t lr ' lt r r r '
(i rrrrr;rl rLrtrr or $iin t est iculului) , t t r iza r : lit or iilior p ( st : r r zllii it t i{ir ll Vr I I t t ; I I oI r I r r ',
,,:rrl ri r l trn r if onnii, l r ept at in t lur cr i violcnt o) , ar ize ur inut t ( r lt t t lt 'i t t t
r '.zir'.i i1i rLletril), crizc hringiene (foalte pertculottso prilt lrpl,rtl lri prrl
,l rrr' ,' l rL:r,siixit ') .ln t oat c lcest o cr izc, nt ss ale1list azi'llr t ziuni lr lolt t iit r t '; 1r t
rrrrlrri ll trivolLrl c[ruia se resirnte durerca
7,1.2. Analiz:r tulbur{r"ilor obitotivc ale tliversolor slrrrifuililirli. l)rrr
rrri rri r,rcn
acest ot ' cat egor ii t le scnsibilit at o poat o scof t t ( tiu ovit llt t {r i t lillt ill
rrl)('(,fo piltologico Di anurno : in unclo irnpftrjrtriiri sti pl'o{lll(1rr(, r\\lrl.lr'r'lrl'r\
,, norrsilriliti,!,ii, sbilro nurnitii hiperestazial altoori ill)itr(f tr t l i t t t i t rt t rt t , ' : r' ' rrl':r
lil;ii ii rcco1ttivo, care sc nutle$1c hi,podtniet c:ll(l l)orllr(r lllltl'Alf ltllril lrL
rirrt
IrirrlrIr,r'oilCap:r,citi{,ii recoptivc' sta,re numilii. ansra3iP. IIil)r)(f$11',ilr,
t1 ttor't'ttptt)1:ttlt4!tt|
rrrrcslr,zia pot intclesa 7;e itr)tli aroncttlu,re,raditttt,lu.rar,',t
tt)tt)tt(utna nt e m ad, ula, r e.t r jLelot int oi'csit i; o: t t c r nollt t t 'ilo t lr r sr r t t sjlr ilillt lr l'
,,rrrl rrri'birn rle hiTtoesteziesau' anest'eziegl.oha,ld,s',t'ttlrttt ittlt't't'srt' rttttttrtr
rrrrrrrrri toca t eg0Lii ile sensihilit ; , 1ii,celel: r 1t 0f iinr l iir lir o{r r , <, ir r r lI oI lr ir r r r l, .
h i l tor' :rt,.zie
sau allet t e! ie t l'isoaiold'Exist r i t louli f t r lt t t 'i t lc il's{'lr l( 't r {'rtrlr r r l
,rrr(i i :
1.. D i s ociaJia sir it tgomielicd. , in cilt 'c br t lt r lvt t l lt ict r lr r r r r t t silt ililr t it 'r t
i ,,rrrrl ,rLl gozicii,scnsibilit lr t e: rt,act ilii ; i st nsibililr r icr r lr t ol'r r lr t liiI iit r ti it r lr r , r '1r , .
\ 1rrr
tt iri s lrizgo iit.ielir: 1i \rLsintlronm,elc sirtrtJlontirtlirrtr.ri st'tlrtlot|i1lr. ['zti t tt
itl, llt, ttiyt,lttl tttctttli
lrlrlr'loL tormo:r,lgezice :llc fascioulului spitto-l,tlltt,ttt
r:i l i i tl i n co m isiir a ocnt llie : int er io: r iil, sa, u 1a' nivolt t l I r lst r it 't t lt llt t i r lr ilt o
I rrl rrrrri c post er ior .
\lL care bolnavul lriet'rltr strrtsibilititltrit' IttttltttttItt
:!. I;isocit1,lia l,abel,icd,,
ri s.r^ibilitatci, tacl,ild, opicriticli, sensibilitltcrt l,otttto-lrlgrrzi.il, ,1i t'rrrt,lit.
lrll r rtLrl'r,paticit fiin,.1 irLtirctc. Apare in. trabr:ssit'tt it sindrottttt'lt' 1t:st'trlrlt
t,r'lir',;si eite dctermirutri tlc iezirc'.r, colllolln0l()l [)()sit'rioirrl'.
lrNl(j.
T0P0(ittArl0 lil I,l1'11)l,AT(xl
?.2. pltoBlljMl,l DU DIAGNOSTI0
SIINZITtVIIlI0PO(iRAII(JII
SINDIiOAMIJ
l,;ii,:t;1l;.
#lllilil
!iii,#{"rr"ffi
i{#irt"3:l
rii#il'
#*"il*g
rrrurirIcttIrr
rlirt lrollllr,lui Ilr,srrirrr'.Ilocli
t1(lrt)l(ltlrl)ic(,,
Srrltllrrrrrit.trrrr
rlitr lr';rlli,
rlirr polfirii 1i rlirr rrrrrrltr
irrhrxiclr,l,ii
cu srtli'trnrirlrrr
oxirl rlc clr,r'lrorr
qi llrr.
Iriltn icl.
lr, t\in;lxtltttl rarl,iottl,arsi7tol,i,tnilitttlrtt'
irrrrtiirtrrrrcltoit,zr't,
tIrrloli cu rl il
l,r'rlrtr(ii
t l,tlicuhlro,pit,fo$tozii
si tuLbrrlrilirl.osursillilil,ir
t,oobirrcl,ir.i,,
l)t.c(rlrrt
rr lrrllrrrliilialorcllexclolin ttr:'il,oliulrtrlir,cirrikx'
irrtori:srto.l,)slo crr,r'ir,rlr,
r ul icli,t Ii sl;r:ib
n1,iilnet tndioulilril, dot'rnltornoricii,lr,1;ulbur.ii,r'ilo
l rlrr su rrilr i
lrlr lr', r.lrc t,sl;otlo obiceigklltlli,. l)cbutrL[rlurcrilor si ll1 srrrrlnrloltr.ior.jrrlr.
rrr,olir,trl,u:lzri
tlingnosCicrrl.
l,isrrr
o, irr r rlr,rrr
^{ccslrr cstc blrrt,ir,liit 1,r:rLurnlr
qi proglcsiv in tumoli. Adcseorilcziuncrtint cttrscitziirrtrr,i rr l ll l
rrll il itriiccl;ii
rrrrlr'icirii,
oinrl voi'bim de polir:ldiculite, sau irrbcroscl,zii,
lr,lil, r'iirliirrirrilr,
rrlrirli{flc, cil, 1i norvii periferici, cind vorLrirrrde pol,irnilit:u,lorrrt,tilt.ln
rrlr.sl,rsitrurl!ii,semnolemotorii sirrt irrrporbd,nto,cu pu'illiz ii llrxro pr,r.r
l'r'r'ir'1
poliratliculonevrite sint dc obioci irrliccfiorlsu vilrrlirr|
. ,l.ccs1,c
.rr prr1,luil un clt'a,ctcl asccndent.Alteori se lealizclzii ruortirrgorrrir,lo
po li
r';rr
I ir.rrlolcyrito.
5. S'i,ndrom,ul,
d,e,,ganglionitii" so caliloterizoluir,plin srrrrurrrrlrr lr,zi
rtrr: rrrclusivii a ganglionului spinal ;i a lii,t1.[oirriiposl,olioir,r'o
(srurzilivo;
plitr ltectarea ,,pri.r'ilegiatd,)'
de c5,trc virusul hcrpcsului zos1,trr,crr rr,l'irri
lirlr l rcuroectoderrnicil,.
In localizarea clasicri, sintlrornul sorrziliy :rrrr rr
l.rll)ogr'r.t'fie
radicular5, manitestintlu-so printr'-o nevralgio rlo t,ip ,,irrl,r,r'
rrr,ii.rrl"unilatelald,, violenti, continuX, da,r cu exircclltiiri pilrrrrisliru', rrrr
lrrt:url,ereale constticlie, de impuns5,tulir,1i rlo arsurii, lil cu,r.o$o ilr1r,(1irzl,
:rlrtoupcobligiltoriu o enLplie critema,to-veziculaL':i
r-rrrirrxrrl;i hrlrrrglrrl'ir..
lrr practicii, asist:in la varilte loca,liziili: culvicir,lo,colvico Irlir,r'lrr
;rlr,,l rrrilcn,le
(,,intercosta1e"),lornbo-inghintlc, krmbollornrLlir,Lr,
ri:1,(,1'{)
ii{r1lri
,rlicr'. .Sr-r,
mr uitLrn tormele craniene,cu lcziurtoilnctvilor. rrlitrIicrri, V, Vll
\ | I lris, YIII, IX, qi X.
li. S intlrom,u.Itle Ju,niur,litd,tt,l,hti Bicartl.1i l,'ot'trsl,in'(,slorxrrrlr{'itrlrr,
lr,zittttii li,tlitcinii in por!iunea sa erittr-Incnilgcu,lii, Lr,livclul l,r'ir,rrtliiit
ll
,lrirnii t1e conjugare (JtU. 29)
rr) )n sinilrom.u,L
de iritulie funiculafi, Lulburiirikrsinl, ;rrrl lr.rrzilivr,
r1iri. 1utrlucprin dureli vii, a,soci:rtcFilrrlu cLto blLlrt{i,rlc lr ilrocsllz io, rIrrrr'
r ilc liitll cxacetbatetle mi;cririle oolounei1i tlri irn,sirrrrr,l,
prrlll cr'li'lrlrrlir.
;'i, irsoci.rz:"r,
ilor' 1lr,r'lrvc
ll r.lrlir lr .
;i trtitutlil i antllgico ou conl ra,clrrt'lt,trrrrirolr
rroio
1t) ln sbtdromttl tla aompruiutta,fvniattlut'ri,s(tunrkf rlr lrl,itrrlr.tt.
lir^sittt pc prirnul plan, iat cclo tlc altrcl;rr,nr
sirtrzilivi so lliulrrc plitr ;rlgii
,;i lrlirr hipoestezii in benzi (uulicLrln,rc).
ffiiili*tr#t;:l1'-.;iilH$H;xr*;:#i
,,r,lp,m"pirlT*ffi
,."#HTi"",H11"*ir[*W,e"":;
ifl
*]*:ff
it,rli[$ip;i*:Tf
f,i,:K::#::;#::ri3,,1!1i,J&-#"1'1i"",t:Y1X'S1T3.ir
,,,,,,,.1;*1*l"liilill
ti'r,i.i.,.t,)'te clr,racterizatprin diminui,re-agi"rr"i;L--iri"i"r
modurilor cle
3*s,,;tl"":#**;r"x*wii
::iilliiitii:q3":,::lJ#J:'rtxif
*.ii;,,I,{
}!tiii"ft,+*r$:*r$irwf#.1j;#fffi
titl#1ff
i;#:"'tri
i:l1"il"i,"fd'
;i,','+3il:
rrrllio 6i sc instaleazi, atrof
iilii'*ls*;#I;
*,::lffi
senai'tit:e
sintin runclie6i d'ectnna
,,*,,!,':,1!,i;!Tlt,,u'.';:ff;:ty*yvdritor
i'"fir'y';"1;$i"l;;#gi33r
iiiii'Jl'Jfi
J#xi{-$;%Tiltf"",iff
,',,""lfi
:;ilrl;i[T#
;ii,
ii!{:Xi:t#h
!:)",;ii"},
l;:t",.,,';t,xjr"d,
{,'
apatii)' sini senzitito-llxot
ori'i, dar cu
l,I*t-fftu'Jii.;#l;,{tli!n"'"'
,,',,,,
j#fr+"*
t*:"
iil:1lplr_[T:nx*lhn#iii1*f"?".#i*ffi
ii':ll,lfr
*fltT****il;,,*#t+*",+t*t,
,.,,,,,1;1.l111;,#,lJlfr',3'y,:Xril:!:iJiffi",tlifrl1"$itgli,iK:tr;r,li*:
plli'i"i'.ii"Gpostseroreraaitt'elic;.
lliil';|U;,,llti.JJ1trl3i.**?1?o".ui
'i;i
;,!;;;:i;.;il#i#,?#;*flJf*l'?J,1f""#TlHf,"#?'i:
i1fi?Ti:l:
tlJ ,\1te lul;.neuropalti realizetzi"
fot.me spn?ittt)epurc
;lnt;1lxl",ni***i"ffi
".i#Js,trHtil
d,"j;Jr'i{#'fti:,:jxd,Tfu
prrrplirx:tpl,ive.
.nulu.Inra
1. llin,tlrtnmole sanli,l,i1)e
L Sinilrornt,Ll
( com.plcte)u nddlu,no
sacli,u,n'ii.l,otala
i rhl,cnuinri,rrJlr,r'ifirr,
rrtrciitnrstozii glollnlo subiocl;ivoqi oLricctil.crlorlcsulrtullczirrtrii (l;rrllrrr.
trrto tlrr scttsibilitrr,{;o
ir',
srr,rrkrl,t'rrllk,g
,,otr nivol"), ittsotitri (lo l)ir,r'itl}lcgio
gi l,ttl'ico.N ivrrlrr
ItrllrtLtiLt
l lu lhu t r],tikrt'
i irlrttr.llrrr.r'Lrt,
l,rrlllurrit
i v(Hot,iIt,ivo
rlrrsr,nsiltililrr,l,r,
rl opirrlo rlo rrivoluI lrrzirrrr
ii urtxlu lu,ru,ryi rlokrrrrrirru,r'ou
I r'rri,lrui,
:r trivlltrlrti l,rrllrrrlr\,rilor
rlrr sotrsilrilil,rr.l,r,,
u,r'odr,oxolriirii,
villonrr itr nl,rr,bjll
tr,rr,rli:rgrrorlilrrlrtilollir. rl ft,zirrtrii.
i!. Sindronn,lrlt hlntirrliun.rtu,rrriulrrlr'igrr,rr
rildrlrrrrrl llnnon Nrtquuxl,
lrilrrr,lrrxotnilrilil,rLlii
fiitrtI rlilr,r:1,r'
6i 11,11.
1ql1r
lorrnilrllilrl,l.ll
lr,t'tro.
;rtol'rrruIrr
iff"+'"onc'1a'le
if#','tr'fi
iril'll;l##iry##Jiff
{{id':,,!fr
"f.',Hf
,r,,ri"iiuriouio..r,rtr*r;*lf
h,S,t'#xil*"?iJ#"fffjffi
l
'-Jft
,xill,',6ldiffi
;rt;
ilifi1;$i;;,,1l;ti;f
;i;lji{{ryi"J.i",1ff
i.,r,iiili,".rri,'iiii;;,l,ilivil;l,ll),ffl'i,"fili,iiJ,1:iii;fff?sfifi.l]
llllll*j;
fl0
qtt
1 rl [(zi (, f l' iir ) ( l it r ( r ' u rri [rri c , ]rt,rrri s o c l i L rc rr rrri rl rrvtri vi t gencra - pe i i l gi i
l rrrrrl i zi; r ,r r r c r r r I r lr r I r rij rrl i ,r' i o l s l i u l r,rn t,n rb L e l o lde accea,fipal te cu l czi ui ter,
i rl rrri rrrii rI rr v c i . o rlisuci:l!itr fa,bcticri horloLll,ct,alii leziutii qri o disotinlie
r irirrlorrrir,lior"ltoll,r'tlatelali leziutrii. Astfelr o lcziune in legiuner ri.ir.ali
(irr|rrr.rrlii) [ Irorniuriir]ur'.ei stilrgi r.* g;cnela i (] tnonoplcgie crula]ii Jting?:?
sctrsjbilii.i,l,ii plofulde conDtiente in membrul infcricr sting si
trr('r'rl('rt.ir,
pir.rrlorr.rrslrrsibiiil,rii,ii tenrro-algtzice in partea ch.eapt5, cu nivel pi*i Ia,
Rdddcinll
posferbad
Rdddcin& posl
Rdddc;rd dnt.
ven!raid
it Cdu vd
Radecihd
| 'o s i I r i I i I r r {i r ,l i r r l r g i t'r ': si ti tr ;l r r r ti r 'l i l t, Itctttr t{ttttti tr Ii r t, It'zi tttti l t' tl ttl to
ttr tl ttti , l ti r l tt
r r r r , r l L r l r r r , L l l io tr r r r l r r l r r ., l r r l to l i
i tr Iti r ttr l r Ir r |r r tr . tl r , tl i tct'sc
Il l l (
l r '_
,.1 \i nrl tonr t t I t ( n) ut ll. i loxl. ( , t 'iott r . r t lizr , ir zi o 1( , lnlr r llit lg( 'zit ' t t t lopr r
1i r:rl r,, trtl i r,lt l, r t i, it r sr , gnl, t t ( 'r 'kt cr t llr olit lr t col'r , slt t t t t llilt llt t t ' lI li{f loll: {r f (lr 'l'
,l r i r,r ,' , r' tr piir l ut , r l"r s|ir
t silr ililiiii pt of t nr t lr r ; i l, r r oiilr ' ( r lcf i t lc ii; r r t it it t ; 1'
rrrrr' l i ,j , rl rrl rlc r r cccit yili '1c lll lczir t lt cr t . St r ir t t ilt t 'slr , ir t r lt 'olr 'lt i I ll lnt llll
1,rrrri ,l i ,' .
IL Si arIntunu'lt srn.-iIi'ta o,lt' I,tttrtrrhitt,lrti ((n'bn|1.
t, i rtt ' l r: l ) lb t t 't ii, pr r t ubr nr , n! it le in. , f ar iour tit t t ct t st azii t . r iiilt r r r t t r 'r ) r t lilr r {r r
trrrr r.l ri Ll rri r. r jnr r , r lllt 'olol r f t 12r iir cr ucir lt r t c: r l{) r '. ia, r ciiilc st r r silr iliiii{ii li'{r 'r
rr,:i ,rl , rl r' i tr I r 'r t t , i1lnt r .l) {) il( ic( r LL,
it t . {t slolcZiilni l. ol g{'il( f l'il Nit t t ll't it t lt t st t t
t I t 'it t t 't 'I I r jilr r t tll r t t
tl i t,rtl ti ttr;l ir lllt t llilit lciicnsil) ilillr loglollir , lii, alt lt 'ici
l r,,r,Ll !r' l r )i bcilt ilr r t t st czic r ror t t lt l nt ellr li , ( t t ilo ixlos( '( ) li illl' I r lt ; r i ll l'
, r ,,,,i rl si t i t t glor ni( '1i0.
Aceir st ir ,t ullr r lt t 'e alt t , r 'r l"t ; i r lir ocir r li t lt ' r lt t r ilr ilt
.rl r' yrri c i n r : ir , ost t hiin sint L'om ullui \ Yallr t nlr ct g, lllt t i llr r lr it t r lii Nr r ; : 'r 'r r ll, '
r ri l rri ( l cst r r n- ( lh{llliir ( \ 'czi ci) p, 1) .
: t c 1'Lpcr lt r t t . t ular t t lr t t t lt t llr lt t r lli r lt t
t.,:i rrtti lc'pr r iubct ut t ! it t le su, 1t tioat
.,1r\ (' (,oi lh ii. l.
i c. r '|, lealo f r , {ci, lt r r t r c}r i. t ilt t i ; i r nt 'r nlr f t r loi.
ll lc;ittrtiIt bu, tu,re intrt'oli t:nrr:,riel,ot'rrtiI Lrrtc llrrolrilci ltlitl rrI r I i I r' t I t t r' ;I
,rri , r' r' isl i i nl le lt t t t cl ioiu'erpt lin1; r ilcz: lr : ol.f tlscr ict t I Lr ht i1t it 't t t tiIrI iI I iii : t t t lt t r t
l rrr l r,| ogl os ( r : ille genot 'oaz: i o hom iple! {ic cr ) lt i. it
f lii t our l; - 1,
; , i lr lr t r r lizir r lr t
l r' ' rti r l rout ilinr ir ii ipsillt t t a, lo) sc lczliizit ; i pr lt r glir r r tlr, r i llt r il ir r r ! ir r r lr ; r ,
, r.i i r Ii . t(l n r f ( r t l, zt i 0 lt t r nti[ ncs1r ] 2i0 oolll. lilliLt ( , 1'r Llii
l] l't lllli st 'r t ; r ilr ililr t i|'r r
r lc i: ip lnlr olit : ) r 't L lt 's; r t r i'ir t r t r t 'sr 'l| . il , i I i i : rt i I
l ,r,rl i rrrri ri (t1m i o r lisr . r cir l! 'iir
I t ( r ', .
l' ? .
:r .
lll.
S i n i r o tL tl ttl t l u ki n i cr : i tt l tttl o l o g tu , 'tr tr tr ti tti .' si ttl IIIIII|{'Ii ) i Ii .t,l l l i l l l l
, l l l r i t t t i c s t li st l i cl l l t( ]su i i L c i n r i l ti n :e l l d e ccl ti i ,.l tl i l tl i 'o
l tttt i .i l i r tr r l l tttr r
r ,l l ) r 'l r r i o r r \
I r z l i L . r l t t . I '1 tl e i l o i l i l h l n i ci
i
t
co
n
0
!i
u
l
l
i
l
{}r
'l
l
(
r
csto
r
r
l
,I)
l
(
r
Il
l
l
l
l
li
tl r ' l r r tl r r l r r '1 r ,'
', , r r r r , , , t r l l r t cl o l r tl o r 'Io ftr n cti o l l .t ] o , a ct- 'l o t ( '\l ) ( r l i l l l ( 'tr l i r l ( 'si
1 .9 6 7 I L l r tr r r r r i l {1 r , l l ) .) i , l l l Ji l i I |,Ir ctttr i IIr '
r r r r . t r i ( S i t g tr ', 1 9 6 0 ; f,i i zo tl h cs,
A,i u r i .r g r L tr r tl , L 1 ) l i {i ' ci l l <l tr l l ]r g |l ', l l l ( ;0 ; |'r tIto Ii Ii tt,
. r 'l r r '1 k r s , 1 9 l i t;
l 1 l , i t i l ) o l ) ( i t.i !i i r r ,i i 0 r r L l r b ., 1 l i i "i 0 ) . l 'o l l l tl t i tl l e Jl 'g t'r ,t.l r i' tt'tr sl r tl i t tr 'l r tr r r l ttr 0 ttr
, , r , 'l l t r r i i i r lr o l $ tl i ,
( l 'o p o vi r i tt,
l {) 7 {) ) ( 1 ,'i q . i tl ) ) .
g
l
.o
l
,u
l
cl
n si t' l q o n , tl t'scr i s tl r r l ) ( i ,i ( i l 'i tr ( ' si l i ,tt r r t '
I . s i i u l ro n n l
l r .r l tr ,tr ti tt
tr l ) t!r tl
f r f l l s l r ( {t i t l ttl l l l i i .l {ti l t( l l ( ) sj l l l l ) l o l tt( l :
i \) I]( t i a ttfttl ( '!i ( tl r l ) ( l l ttt
r l l so t'i i r l c ( r r u l i tt<l ctr tl l t.tl tl l Ir i 'l l l l l l l r ( 'l l i i l r l
l , i r t t t i i . t , t t o l ti ( \o l u l i r i tl i tfttl ( i
l r l r r t , : r p t o l u tttl i i ) . l ,) r i sl i i , si l r r r r {i i i r L tr i l r t i 'ttl ) t ttl i t'i l ' tl t s( 'ttsi l r i l i l r r l r ' r r l r i Ir
t r r l r 1 , o l i t r t l tl i i cl t i r sl tco l t' tl tr l l cttzi p s( 'l l {l o l i l ( l i ( l l l l l l l '( ! i 'l r l l l i tl i ( 'l l l l i tl l l r l l ( 'l l
( 1 r [i r r l ) ( 'l r i i i r l !{'tl ( 'zi i l r ^ 1 r r r r ( i r r l l r l r '
I r r , i . r r r l i s l ti l r r t{i r r i :r xl i r r |i i sr ttr l tr l r i l r i l i ) ,
] l r r r l . | | r , ( x ) i l i( i i l i i , i tt i tst'ttto ttti t $ i l l l r l l i i , ( l j i l g l l o sl i t'r r l l l i l i 'r ? tr ( i l l i tti tr 'l t|.tr r i
qi
l tctr ti l tttt'sl t'zi :t t'o t1 i t'ttl l i tl tr vi ttr ' l i l ttl r r r l i l i l i l I
, r r r 'r t ( , z i i l
i r r l l tl ti t'r 'i
l l r 'l l l l r l l '
I t 1 t l t t t t i l r r r tr :i i t,r ,yi r l r r l l r ...|i r i i ( si tttl tl ttttl ( 'i l l ( ' l l l i l r { l l l l Ir l l i l l tIl t'
l l tl i tl ttttsttl tr i , r 'i r r tr ';l i tttti r
, r r 1 r r r , r 'i r r zi il r r tttt ( i ttr , l ,l r l r ti l t l a i s ( l l l l zi l l l l fi t
t'tl t ' tt |'i t t ' I r' t I '
rr r r r,, , i t trr i rr r r , t r r ;r ,l l r .i i n l ( 'tl tr ') ; c) l l t'tti r r l ,tr ',r i t u r ttl .ttl tl r ttl ti
l \//tl xr
r r i r l r . ( r 'r , t t . l r r ,l l r r n ( ,,i l i r 'tt,r i i tl r r l Iti ttl tl l l ti ttr 'r r
l r to l ) t'i ( tl t'( 'l 'l r 1 i t'i ) tl l )
( | l \I ' I t i
t I | | I I I ( i | , t || | I Ii ) i
i
(
I
I
I
r
Ittttr
tttr
i
1
ttt'i
i
tl t
r
,/r
tl
;i
r
.
I
t r t t l t r 'l , , r x t
i
'
l ttl r t
r 'l l l r t t , t i {//r ,r '. r i I r 'i |,t'r ||i {'|( ' l p |r 'i r tl r ' ( t |zi l l tl l i ,j o l ) tl t' ;tl ttl t'i t o l tttl tti ;
l l 'l ', t l t t n I n r , : i r ' ( I rl rrrI r. t r I t t I tttt l tr r l r ' l r x'ttl i l r ,l t zr r l ttt c r tr i l l r l i i , ;tr ' l tt'l r ti ctttp ttl
:l l
Irrrlrrirr')1
g) Asr.*otnu:it (1r.ilr rullrrr'ii.ilr.r'lt'sr:rrsibilit.le,
rr,dcoscbirrrrr"
lrrtrrlrr);lr) J.lipr.'rputirIuLunic.i(silu,,slptrTcaclir.lalamicri,',cn"esprirrio.
lrr' l,.rrrr,rLrrlui o ,,ovcr-rcactiou,' ll tufllcrd), carc constd,in fendmenul
.rr'irrs .ii .r'icr. c-,ir:i1rnt, chiar. sublirninat, ,Lph;at de partea bolnavi sarr
(lr\ p.r,r'l(,a
$rruir,ljoasii
nneori, plecum $i alli excitanti (de ordin senzorial,
fractul mahi la -ta lalnic
5c. cer- | frontatd )
sc.cer 11,6) \
t,..
/i\
f..:.
R:".:..
i' . . i' :
...j ;
-/,/ii,t.--
i' ,
:'.
.ia'
"-ttll:i
:::
:::iii:i!l
i,i i:iR
-.
\:.:1.;rj
I
I DM I
i= /
: ro i j..ji \
' .,.,..ji
rf
IPVP\
lvcv',
.^ - (
I ' .'
Wn:
\!Y:/
,ii i:vl-l
-.'.'!
:..:'..:
P.Reit
E spino-tdlah;c Y
sc.rrr.13,1,2.s,7
',
)
:\,^:.
rL
lPt
e Reil lat
Sc. cer (11,12)
LECENDA
6r nucleilor
Gr nrcleilor
OM:N.l)f,Rp-
6r hucleilor
t6a nucleilor
psihlu)sc,,irrt(.grcazi"
ir.rdurcr,..-A,.1ft.t.
rt,,pililii, o c\(.ittli(.
i:ll'.iJli,il
Iir(.lilii,
dllr(.rl)tfiqrrrlcr'rnir.i1instx.cillirigrrl
srruatt'ulri.r:e),'(,lrirr
simDLl.
ItI ittgr.t'rrniclii, l)ill)i{,l.itnl,
ctc.. rl"r,larrs,.rr.zir
il* Xa,r,,,,liiri
lrir:1r1rirrrl1l
.ru
nr.\'l t {) ( |ut ' f lr r
(l o
t r ) lt H (,.v tr,.c
i l r' \l D,i "di
i r: l tl r t,okl ri l trl i t,l j r_
l l .i l c t{ ,t
r,\l r(,l l l ( lr ! ( l( , Z ir f it 1. r)l )l l ..i i 1t l -(.i
l i i .{ l Irr.l t)1 ,i is i rrl . r r.si rrrl i l i trrrr[1.
tl rrri l )U l (.t, i r.
rtr.(.1 t. l nl( r ( l no
.
it l (l l ,| rl rrl g r,z i r.).
I tr. s l rl r. r ,i l . l rtrrri rr:t.
I rrr I r.I I r i rI.i , rrrrr.l t.
3r0
(ttltir't'ttttlIr'
(itullorolri rlozugrr,rrJrikr),
tt'rttttLici
rrrirrrHrrli
cttto!iiL',rrvlriLllr{,ii
rlrrlrr,tt
tlttttli
tIo ;ttttI't'rt,
rrrllrxlii) 11irrsti(,ir,t,iikr
t,
lirit,r'l,tr
vii
viHorrt:r,Lr
Jrol,
tlrr Sr!g('t! .l{l{i(l)r'r'il
lroltrrt,vr'1,.
Ani,fol,ttltul dirr lrolna,viilui Iltrrrrl(<ritrrt'1,
tt'ili
rlr.orrrlrii
rlo aflxrNilt
rlc rnt:zilii,,lttci{,,,tttrlltrtort,sI rt'zislrt It, ittttttui t lrt1,r
t't'l
sll bolnilvii,", iill rtlt lrtoirrnl, rrl ltri Ilrrrt,tlit,l'it'ttttt,
rrr,ttzrllilkrrdo par'1;ort,
gt'oiLzttirlit
vtrrtltt'tlirt lltt't'trtt,
IloIrtltt'i'1'',
r:intl oinl,itcotul, o srrrtzlt{ir:
,,lrl'rttroi
iOtllt oxoosiv ltt 0ticu 0x0itit(io s0ttei
leritlinl,ir,tlo t t'tr:t,c!
'l'r'o|llil,ii],ceastii,
lirl, srinzoritrllsa,upsilricr'iIr'1rl,zin1ii,
fenoructtulrlo supt'rrrcrtc{ir'lrtltr
rrrirr'i,(,,ovct-teaction"-IJe:r,d
) sa,ud o ltiylpatirt" A ccstolonotttttttost' t'r ltlit ii
lrlirr lrlptul (Sager, 1960) cil, in nuclcii latorali convttg c-roil,lll'iirrfi1,tlitt
rrrr.rlirrlitrtern (prin intermediul nuclcului dolso-mtx.lian),rril,iii tlitt tttr'tlittl
r.rl'r,r'rr,a,tit prin nucleii tjalanici de releu pc cit'iledivcrsclol ilf('r'olrlr\H|tl
zil'ivrr,cit 6iprin nucleii talnmici nespecifici,in lela{'iecu fotttta,tiit,t'trlitrtt
lrrlri, rcspectiv chiar stalii pe sisternul reticulat asccntlcnt (v(lzi lig. iil)).
I lqr,rl1i f161p"* (citat'i de Sager,1960), incercind sL explicc tlut'ot't'trhilx't'
talamicX. au ar5tat cd,lezarea fibrelor cortico-tlllatnicu rt,t t'IiItt'trt
rrrrl,it.,li,
,'r'lrtlelosenzitive talamice de snb in{luenla colt'ical5 inltibitolitr 6i rlo tttrrrrrrt'
rr('r,g1,i
nouloni senzitiYi ar prezenta o ,,supraleact,icr'ln olitto r'rcilrt,ttl,
llrirr,r subliminal. Dup5, alli auttli (citali do Sagor, 1960), rlivcrsohr 2rolr"v
(tasoalare, tumorala, i,nflamatorii, cticatricialeelc',) an cxcil,rt,txrlttlt'lt'
Ir'. ion,a,le
rrr,rrzibivc
talamice qiar producedurelea. Incerclrile cloinl,olrotrrrtt rt tllttt'
lilol talamice au dus Ia ilispute incd' incomplet elucidato. S-rltr rr'lt'iltttil
tlrr rt
rui,fol talamugului, in afard de rolul si,u ds re]eur qi unelo prtnibilit'rl,{,i
r'nlrjbui Ia elaborarea senzaliilor tlate tle stimulii nociccpt,ivi tlo l ip pt'tr
'
lolxr,tic (Mori.n, 1955; Ilead, Ilolmes, 1912r cita!,i do Sagor, I9(il))' lrltot'
rt'li't'
rrrill,e (1936) a ard,tat c5,alterarca nucleilor laterali exalttl, lronalil.rr'l,r,rt,
livil, & senzatiilor, intruclt aceastS altelnre ,,Buprimil, un l[n:]ljj. trl,or, lrll
lill,nr selectiv aI sonsibilitd,lii gsnsrale", a cd,rui func!'ie csto tlo tt,ttllri trtttt
||rrrrcnteledureroagogi protopatice ale acestei sensibilit[]'i. l)uror('r\'lihltl
$onzatie, esto fd,r6 indoialS rezultal,ul uneri funclii coltionlo, lnl,ntt'il,
"
rlorlr
la nivelul scoarfei excitatia se transform5, in senza'l,io.
Desigur, dnrorile rlin sindromul talamic ritlioit, plolllornrl rtivtrlttltti
lrrlrnlior al integririi senzaliei dureroase, iar o ,,soluJic irtrprrr;abill' qi rltrttl
rr problemei nu existd qi mdte tlin concepliilo mai vochi 6i mtli trtotlottttr
pe interpretd,ri $i fapte totuqi obiective, difur\' tlo lit lrutol ltl n,ttl,ot"'
lrrr,zrr,to
(Alnoni qi Operscu, 196?). Scoarta cerelrralii, rcprozint;ii lt,pll.rlll,ulsttporiot
rlc porceplie a clurerii, Dar qi talamusului Ii levirrc, dcsigul rttt rrtl lttlltlt'
<:il,qi llrr
itrrportant, atit do releu pe cd,ilesenzitive (inclusiv dunt'o?r,H{i)'
lt
lill,ru seloctiv,precnm gi de a ,,moclttla" qi do n contribui ln,ttlttlxrrlut'trtt
rrivolul scoar'fei a unor senzc,triiparl,icularc * tlupil, cttttt trlllillt(llllll
rrttotior'- prin convcrgonla,ln nucklii latera,li n' unei lnulti[utlitti tltr ttLr'
tttttrloi t'tt
tr,tr!o extcto -,proprio-gi visooroocptivo ;i prin I'oltrl,iik)ittrtrst,rtr
liltnal,ia, rel,icnlarit'qi cu sc.oa,rfa
ccrclbrt i*l(Sllgcr,l.$60 1,\rscrti qti()l)r('H('lt'
(,or(o'at(totit:t',\'1\t't\Itl
f lf(i?; IloDovioiu, 19?9); i) Mrri pot apiirtr:l rnirscrirti
la nivrdu) rniinii (prin ltrzitrnrrllI'ilrrtrlot'
tlr.norlrlsitrf tliscrcl,ttiii lot:a'liz11,e
lrrlit,ttto'8trirto,r'os1:txrtiv
t trucltttlrti trotti,trl-ttttttlilttt l,l Itri Lu,r-s);j) ,,J\llrrrr,
drrgrdcltrsin1,tltrrli volrll,trtltt trtllt o
lir,liunir{r,"rrsLccu't'it
tttol'int,irfi
, ltt sttttsttlt,i't,
rrri6oil,r'iloltotozi<xt(utStt"zisr,lotfit,utlittitlo,,tlt'gcl,trittglttrlrtlot'prinnri4r
ntnlotittkt Hitlt rtl)roz(flltnlrr lltr: lt'trttltittrt'oltttitt
rt,l,ol,rrzitrr)
i k) ll'rt,l,hurllriIrt
cor]1tt
I tti gcttic ttlrt'ltrxlr'rttuttt l)l ill I'r{rtlll)l,rlr
(ll'itt lrrzlttttr,;r
hk'ntlilltont,oni'ntd
rr,lttt'cll,t,i,
prxlrrriqtrrr,
li rrrt|,zirrrtr,lrr Irrilolirtl rrrrt'li<'nl
rrn1;cin,ltl
tt r1t.r,lrt.rtlcI
zrl
l)o: l| {'t i( | I i .
ill
:l l :t
tr
IrrLrLrrlrrIii,
rlrr olriooi ir cvltlrrrttl, ilrli',r'irrr')
; lt) A'ir{hr)rrrtllui 'ltrl,ttt t1i
rrrir
rrl
ir,,
ll,rl,inxl,:i
(ltrrtr
rirrsotttrtlogttozirttrtzollttttzir',
I i) A'irrrlt
5i itttozrrtlilLlirt'irr)
tli\ lr,
tltr ll, I(tcllllorl!Jl'rr'
lrt lit t'til,uL
\n,' ltgtl(rziotligil,ltlil'(itrcttltrtoilrt'k'it,
tltt llltclrrIl,ttl
rl,,rrrrrrri
qi tltr lt,tlilittttr{,il ctrlocittci tlsgtritr,ttttr'ltritt tllltrrt'1,
lltr tilrttl ,,r,ltrsi1tg
Irr:rllr (lc orit.ttl,rllotlroaltt'lr-sl,ilga
I ltcalcttliel rtgtiu{itr
rrr'rr, lrri Illlyor'-(iross(irr spocirr'l
lltltrtltt cxtxlttliit,lltitti tltt$tlttttrtll:t lllrr\i
llzittttilor"
,,,rr.llrrefii);-j) Altc sernncl,oqtogxlJ
icc corticnle, ptilt osl,ttrl*irt,
l,r Ior'rniri,iurlilevocine.
t, I t tin
:)) lir cailrnl sinih'ornului pu,riotal sa pot itlanti'.li.caur nt,iil,tut
rlr',rrrtttr topograJica
:
r1 iliidront'ul senzitiaparietal global, clasic, lvl lrti, ).)(i6rint xi. l/lyt
tr'lrt
r,. r'r,o[noaqteprin tulburxrilc de sonsibilitatesuhiocl,ilL rii obitrol,ivr'i'
trlo ttterior, Exceplion
asoci;r,zi\: antiotrofic, hctnitlllollsio qi rtlrtzirt
lrrr Ir,ziunilestingi).
ll Sintlromul, de girus puietal su'peric'r (a'riile \tu, 5b) t'tl.r'lizo'tnti,rt
.rll.r'.rrcrnai pulin marcatS,a tuturor sensibiliti,iilort 1o ltt:trticorltttlrrott
lrrrlrloral, cu test&urarearapirli, a sensibititii,filorttlcl,ilo,toltlticii;i tlttt'r'.
li Lii'l,i
krr 1It'rIIttIItII'
r,r.rri, tllr cu rnenlinerea indelungatd'a abolirii solrsil,ri
c) Bindromu,llui Anton' 1i Bn'binski (vezi :ltrtcriot) cslo Ittrt,lizt,l,ltritt
lr',riritrimri ertinse, cate implicii,: puietala, anteriolt'ii, ltt'itttrt uri ri, rlottrr,
r rr, rrrnvoluliepr,rietali,, girusul suprarnillgirralqi u p.r,tlc r[itr pliort,trttrltrlirtl(\r('i{(firzii,
tl) Sind.romul,
lui, Gerstmannestc produs priu luzirtni (1il,l'lr
i cit'ctttrtvoltt
lrrrr.!i'tle trecere.lintre circumvolulia parietalii inlloliollir, ,,s
\', ," \'il,it'lla mijlocie clin pirtea sfingi.
t) Sindromul parietol p08terior al lui. An'drd Th,ottt'tt'tt${) l1!olllrt)rl,'1l'(\
irr
1rr ; henianestezie predominanti, pentru tact 1i portt,r'ttilrttsiltil il,rrlrrrr'
1rrrrl rLrrili'i,
I br':rdihinezieqi disrnatrie, apraxie idoltolicI orxril,rt'lttvrrtltrtlii.
l) Eittdromul'
Ttarietalp ro.fwfl' al' lui tr'oir (prin lozitrncslirrgii)itttlttttt,rrrzrtr
rrrrrrit,otul conteit semiotogic: tulburS,ri souzitit'o billl,rll'rrlo, illirttlntirrrl
trtrri lles simlul pozifiilor, apraxio ideomotorie bililtotrtlit Illtilzitt tttrrrlrrritl,il
(,1,,tip mixt); hemiplegie rl ro-r,ptri.
iii,,iiiii,i;;1,,ril;Li'll,iiili-#l**[qt*[,#;#i'fl"'ii]
;.i;r;;"';i:Iii;itijlil'i'li#,:lii",
rrc.seusib'itateselocalizeaza
pomini,sau
'"1.
jr:
t ul]:uririte
Aus""silriiitat",i-oiaor,ht"
d" tot111;*,lll..
lbi:u_r
(,i,,,, ,',ru,rrr,
,,,'',,..,
ri.lL(lrr(r Icz.lroa conccrnitenti, a fi,ontalei
assendeate in
rr,rlir,ccrrto
;i rrcl,l,rofiioror"oraro-*"*itn.iJiJ.i^o"."rlre
de-Sii"
il;iiiiliili.
gg,lii$11;!li',1$lll;itt,*
;x"Jilill?1,"#"*'jtl:,'"'i",ij""'*'.*t'11:
aproa.
ltii:i?:1TrJ.........,fi";:ilr1,'1,';*i*",'S"iliflili,":"i;*rroduto
lillilli'Ji;J
;IItn,li'l":;;,;lt*lui
il,1,lj:
,t,1*riil"*,y*::[;9l;:ll_itffi:ff
f
iiiiriliffi
!jri,"*lf
#i*:i?rdffi
,rrurmnay,*,i:i:s"*1
)r,rT',trnr rile subiectiw de
din sinalromulparietal con,r,^,,.,,,
'ensiiitita4
a,morferi,
carcpotprera
ra
.,,,,,,il,,0'Ji'''Jifil',i*.."13"'*1ff**n'J".ll;;H:
j?Htli,"i*Hi'"r,"jT;;c?},^pi"si'ci
r,,,,il,i{!i.':,i'if#tll#?ll;,'i
care
,,,,,^,,?,.,1liii,iil#':f::ifj'iij?,1,fi.*1,"*
llj*,llgf;y,i:robiccte,
jfl
l3'fiit"il:;I?f
,*li;l[tx,T"llJH3.:*;l:
:r;r:,rl,i
i:::ii,;T'fiiLi;,tf
'(;il',l:"jlili',J",;;Bli:
i.:,fi'J;i;"1.#ll"T?;"jji"il,lJ,:*.i*:
l:ititlii:;
'ii:ii";11"-iliilililli'hllli"'Tl?#ii.,i?i,,fffil_X"-1m;;sticui,rircrin.lJ [)c
sau itfefior,
a miinii,
DIIIOI,,()(iI0
?.3. PROBLEMII]
D!] DIAGNOSTIC
IN DIVF]RSESINDROAMII
AI,GIOiI
7.3.1. Cefalalgiilc (Colnlcilr)
ijt:ililil.tiili::;
i,T,:l:;r.,1;';#i;;j;."H"ilffif'J."JilJ,.HX?"",1""'Js,;i;
,,r!
{} r1r'rzl't,
nlororlc dc 1jp R rav&is-Jackson.
\\ Cefalalgiilc acule trc srrgcrcazri,,evitlcnt, o co,ttzdnrt,lli,,
.
!)
lxr or,r'o rl
Inrrrrrin considolarc qi o invostigilrrrin Iunc{,ic de lootlizl,r'ol cofllt'oi 6i rlo
r orrllri,r.LIclinic in c;u'o apu,to(Arsturi qi Oproscrr,1007; llrrrris ryi Wrrlll',
I lrl'1, (rit,trfidc Arsoni 6i Oprosorr; I]otrovi0iu rii .l.,rrscu,
.19?0):
I ) hr t:t'fo,lalgi,it(t la t,l,ir(,l(: it) 7n regiu,nao.fronto-l,arttpora,[ii
.' sirruz i h]
lrrrrLirlir,
sil,uotrnoidrr,lrl,
lcrrii,l gllrrrurrrrlilill'i su,uilirlociclil,ii;lrrrr';x'slli
(Irrrk,o8rrItI
itir,sir,rr
rlo rlivrrrsotrl,1;rrIi
irr'lclioprriio(t,crrr1xn't1I)
1J,,rrirrir,l
I rr,r'tot
l,r orr,rrrltrii
irr yitirli)1 irrxrrlicirrtrlri,
rirttrllr1,rrtirr
crrrol,irlirrtril,
Lt'rr,uttrrr,linttt
I
r l.frlirlli lrl In rtllitttttrttu'ui1t
il,t.tl./r,,'
trrvlllgirr ocoipil,l,lii,
-AlttoltlI ltrzitttti
li't\ icir,lostr;xrt'iol,lt( | r'rrrrt rrir,I i rrrr, trrltrrir,l,icr,,r
lrot'rriorlircrrlir,,trtrrur.tlilctt,t'"
Ilrrzir)1llrrfrrrrrltr lriprrtlr,rrNirrrrrr
(rtr vn {itrrr
rr,r'l,rrrillil
l,u[lr'i,rrrt,rrirrgit,il,
; (!\'(!n
oruri1riIrrIi1
tr,,rrttir11itlr, rrotrli,tlttl rrlirrirr)
r,iolInll rltr rl r,l rttl , tt,t ttttt i
; |ll,,Xirr
ffi'i'l,',v!,##l?f
ff,i,{ti#t"l1.HT,Lr,i:*;n"x*{4*-xi
lli!li,!i:d;f;
l:l:l't.:Yf::,i:.3- Temb,rurBurorior,indeosebila muDchiimici ai miinii, raleolr r(,illzuld un srndrum um6r_mind,),insoliti do tulbur{,ri vasornotorii
Il,fflil;JilfrlT,::li,;,"i:;i,i;'):z!"n,ii:;,yii,.l*:ll',li*rlli*,yl
ii
n(.nzrlry
propriocoptiv);
d) Tu ru.rdtioest
ibutire.1r.arr,,
suir
flll::.iti.l',,:'.rl
fi'i'l-ir'iil,iil
r,lli)|;,!)tiiillffi'iflffiK'ff,(#d:fiiHil,iilli'f
i,,ll;l,i;i;il;
tth
l !-rLl l
lr'rtr'rllgii,-slrl)rr irl:rt.irlit,lrc
(llr, bolrrlvii hip.r'tcnsivi, rrt,teliosckllrri
ici qi
l:r, irrrlivizii ln t,il,Nl,ii,\l/ lrr u.lekrl.yiil(1gtnuali::a.le : a) Protc.sc i.nlt,ucranieneacute (ltenn "
,
I rr rr(! ; ll{rmo}'ugii iltr,:rcerebtrlc - in c*re cefaleea,se instaleaai, deosebit
rlr, lrlrrl;tlr plcccrlind coma - srru extracer.el:rale turnori cerebrale cu evo.
I
lrr{ir, rr,rirrrpi,omilticiBau cu alte sin4rtome pini in moment}l declalqJ,ril
rrrl:rkrr:i, plin creqtere bruscit a tensiunii iniracraniene; procese infla'ma.
l.'lrii, ll)ccsc celcblllc. nreningite, rneningoencefalite
; irdrnboze ale sinu, rllrl lrr'r'on(,rse.-i rle \'onclor cerebralc) l->)In.fertii qenpralesud t.,crtll
;
(sc vrr,ctiutil contextul clilic infecfi_os.1c) Altc inJbatii; ineningite, arterito,
i
'craniene
'n6n
f lrrlritq, 1,..r'rarUebitecerebraleI
Ai
1 71
.d.1
.Traunotismc
lt i.lr(t lt.ttsiunp afieri^ali.I f)
(cu
oaica!,ii,
monoxid de ci,rbon, ititri{i,
.Int
rrilr':r{iq.r.): g) S'rf/.iirlf riscrraleacutcsou aculizate(caretrt,brrje,;rrtrio
l,rlrlliilrnr r.ind nr1 ge poatc clucida utr met,anisrncerebral).
ll)
.C^efalalgiileperioilice (Amcli qi Opreecu, t|)6?; Botez qi gerbi,.
rtcsr:rr,,.1965
I Br"uetman,19{4 ; Kudrow, 19?4; popoviciu Di pascil, 19?9);
,l.l,l!ig11l.o(in.situal.iilcinmr.ealgiilepre2iuliuncaractcrhernicrrnic,
lrrrlsrrtil,inso{it $i de alte simptome, indeosebioculare). Vom reveni rnai
li|z irr iulr-un subcrpitol seDarat.
.l[
cerbrolc (angioamc. anevlisme,; se pot
, a(ormo! iit.e
-ir"oli,2)dc
-r-asculore
crize cefalalgice
pscudomigroroase(dar aproape totdeauna'rlo
:rcr.r'rrsrpat'te) sau nemigrenoase, putindu-se insoli in ulele accese algioo
i.r rle rrllc simptome (crize epileptiee, hemipa,reze, tulburXri vizlale, fdno.
rrrr.rrc:rt:tzice, eventual de paralizii periotticc de nervi oculomotori_ca do
llrl'lir, in rlnevl ismcle de aateri, comunicanti, posterioard si in cele de a.rteri[
Ir'r'|'hrrLi posteIioari).
.. .3) le,Jal.algia p.arocisticd, peliod,icd, tn tam,wile cerebrale este rar{,,
tipul ct'l mai obi;ntit fiind de ceialee progresivii, cu orar. matinal, sa.udo
',.l:ll(.e c()ntinuii cu exacerbi.ri paroxistice (Arseni qi Opreseu, 196?). ABth'1, cefrllccfl,prroxisticl pcriodicri este car&eteristic5,pcntru fazele rie detrirt
;rk, lurrrolilor dc vcntrictli laterali qi de ventricul al treilea, tiind declanr;r.rliirlc _rnoditici,rile de pozilie ale capului, de trecerea in ortostatism, do
,'fotl ;idc slrinul (ArsenisiOprescu,l967) si oste in,lol.iti$i do al[c ,onrrro
r,.tttol,'gict.(obnubil_5,ri
paSagere:rle vedcrii, tulburiri din pa,rle:LLtn r
rrr.r'v
l cl'i|,nt(.nlsI endoerrno),
! ) Aefalceu Ttaronisticd,d,in, hipertensiunea urteri.ald,poate fi tlifuzll,
*rrr locirlizrtL (fronto-tcmpora,15 sau in rertex de obicei), api,rincl brusc,
rl{, rjr'loruil,i multc ori sple rliminea,ti. Se poate realiza qi o formi psettlorrrigrrirou,sf. Examenul funduiui de ochi arati modificd,ri nete vnsc:rlaro
lrprrslrrc ilrteriale, edem sau clia,r hemoragii).
5) ( ofaleaaparonisticd, d,i.n hipatensiunile arteriale tecuntlu,re oltor
u.ltrlir.tti.(fcocrornocitom, aterosclerozS,sistemici, qi cerebrali,, ecla:npsit,
irloricu,lii profcsionale , suferinle renale) trebuie corect gi la timp identifi:
cul,ir,irr contextul clinic qi prin investigalii corespunzitoare.
6) Cefaleea parorisli.cii, di,n encefaloputi& hi?a.tensh)d, se inso[r:qto
,si rlc all,c rnanitcstd,ri cerebralc consecutive etlemului cerobral acu1, rlirr
ircoa,sl;i'i,
oncefa,lopatio.
7) Uttul.eaa parotisl,icri din hi,ytoNensiuneu
o,rteriald, (t:sen{il.1ir,snu
rrrcrrrrrlirlil,
tlivorgilor frlotori) rto csto sugclalll prin survenilca accstt.iir,Iio
lrt ltururlolr,
irr dinosllt,t;innt(,,cclilr,klr
rlo potnil" - I )iirtrrcsctr,1)rxIotllIu,
l1];8),
Iir', rlitrtpoh'it,rl,lrt, l,trr11'11',1
itt ot l6ntll,istrr (ltilxrlt'ltsitrtrrtrr,
6t'i1s1:rlir,:i),
it"\(l
l nl t:tl l )i u1)l c :
Ir'
| ,t , r' ( \ | ) | I I I ( | .
x27
ir+r., rtl,tirtrnt'
rltfctrtt{it,l)r,tlilicili alc slilii rle cLttts{:iin1,ri
6i pr'rbcltt
1i/srrtt
rlr. I:rlrotlrlot t'c\'clatoi-tr(,.
l')) (lt'[ulutqii co'ntinue curstante sau cM sicotrst{r?rr,(eYentual cu \{r.r'r'lriiri px,r'irxlice)apar in foarte numetoaseafeclliurriI L) Leti/ulli oso(ise
,,trr. tttrtirttlt'tn aie cotoonei.ceraicale su?erioare (fn acestia cefaleea cstc
,rr'r'ilriio-rrrrcrrli,
so cxacerbcaz;lla schimbirile de pozitie ale capulti $i se
irrro(cslo i,,iilc :lrnedeli.)Ilste vorba de: unco-iliscartroze cen'icale, rrrt-rlforrrrir{ii rrlo .iorrc{iuniioccipito-cervjcale,rniozite etc. 2) Insuficienle circuIr lari i rart:ltrale (earotidione qi/sau vertebro-bazilare), 3) Arah'noidit e corc'
/rla1r:(lxrsi,frilumatice, postmeningoencefalitice). 4\ Ce.Jalalflii de tensittnet'
(lrsilrogrrrc). Aci se irrcirrlreazi, gi unele cefalei prin coirtnctura Dlrsculalru ii r:ryLLlui;i a gitului (,,mtscle tension headache"). 5) Diverse o.f(]i1ttli
sislrntirtt (ancmii, le,ucemii, afecliuni a1e sistemului rticuloendotelial).
ri) (lt.lirlcur,bolnarilor cardiaci fi di'n alte stiiri' hiponice (insu{icicnlc catdio'
lr,spirrtolii cronice). 7) Cefaleea posttrarmatici, (postcontuzionali post'
'
a
t , |||' ,( i()i rrrIi ). 8t Ctfqlpeo,boltat'ilor hiperlensir. 9) CaJaleenaroniri
'
,ti,thriiril,tr. '10; ln'direrse suferinlo hipatice., dttohenibiliare fi t'ettale,
Il) i4prstuf i,l,iiladed.iaerseorigitti, (endocrine, neurogenc, in diverse sufet'inlc
rli;1r'slivr:,s.a,.)pot prezenta in contextul clinic cefalei persistente, zdesea,
|rr rrrirr:cl'bii,riparoxistice, asocia;te cu parestezii peliorale qi iir membret
(rr sDirHr[ cmpo-pedal [i uneori cu manifest5,ri conrulsive. ].2) II i;pogli'
(r'rii(r se manifestd, prin cefalei cronice) de obicei cu exacerbS,ririnsolite qi
rl(f sr)rnrrolcntii,, sti,ri de obnubilare, transpiratii $i uneori cdze conY lsiv.
lii)
nu uititrm cefalalgiile din aJealiunile octtlarc (ghucom' tulburiri.ito
'\i,
lcllirc{'io, iridociclite, cheratitc Di alte boli inflamatodi ocularc), din gfec.-.
lirrtti. na:ale, rnastoidtene si. sinttaqle (tralrmal,ice, tumnu e prin infeclii
rlrr frrcrr,r'kroale 5s.a.)qi dit:rir'fecliunilemauilo-dentare(infeclii de focar, perios'
i ittr, l,umori q.t.). f +) Cefti,lalgii.lehot'monale(1* femei cu disfurclii oYat i"
r,rrc, cu mcl,ritc eronice, in proclimaxr in climax etc').
lt) Ceful,algii,lec\nl,inue regr$i1i), (Arsni $i Oprescu' 1967)-sint t'epro"
zr,rri'rrio ile: lj Cefaleile din encefalopatiaposttrm.malicd'' 2) Cefale;iie ltl
h iprrltn.si.ttii tralali . 3) CeJaleeaStsihogenti(hr lemisie). 4) Alte a.;feeliuni{venl
rr:ri sus) in curs de vindecare.
7.11.3.nl igrcnele
Nligrtrrt l,r'ebuie diferen{iati, de restul cefalalgiilor 7}ritL utrs.at$el'.e
xrlt: xrtirtiologtcopaz"ticu.lare,in sensul unei cefalalgii periodicer predonti"
rr:nrl; srrrr o)iclusiv unilaterall, pulsatilXr insolit5, tle obicei de tcttomcrttt
,rrrrlu rr (l'otopsii, hemianopsii, oltalmoplegii), de tulburiri velietiltivo
(itrr'(rfi, vr'irsil,tui'i). De multe ori migrena are o incidenfi, familirtiri. Litt
rrll i.k.rr'rlrrlilyoai)o decisiy de tliagnostic cste reprezcntal,{le r!.ll'i1irl
,rlriirrrrili irr lilolestenli (pind,la virsta dc 1A-25 tlc ani), astfcl incil ull
riirrrlrrirrrrrriglenosapd,rut tlup5, tirsta t1e 2,5-30 de ani sugcreazirllltLi
rlr.glrrbiu o lcziunc organic:i intracllniani,, cri de pikli, un tune\-r'ism' rtll
:rrrgiorrr,o turuolil ctc. (Arselli qi Oplcscu, 1967; I)iamond, 1974; Iilboln
r;i I)r. Iiirrc Olivrrrius,t07l).
trirr
I'tohk.rrtc tk' r.tioprtlolle
l,
lllilltutrt' dttitlt
uilrtnu
)
,,(l| izrr i t t I i i t r{ t t i I rr' , , , f lt t Hlt ' t . lt t r it , t lt t , t r lt r r ' ) ) ir it r l, t r 'l i t i i v
,.'',,,,||
r t ; r , t ( l ( r l ( \ r l l r) r , 1 r1 l l l ,
l , r r r r ; r t r ; r l t r ( : r , r 'r 'l o t l .tr ,i sl ,:tr l i i ( p l l r 'r .[r l r r l g i r ', r , r' I rr I rr I i i i rr r l i p o r i l cr 'l r r Ir l ;i t,')
, r r r r r r r l r | r r ir r g r .r tr 'r ';r l r r l l c l r to l r l |tr r r r r ,Ii o |tl r Io t|,tr i |r . r l o l r .zi tr tr r '
'r ti j r r r i ,,r
,,r,lrt,rl.r.
l l r i i r l ; r , i t r *i Il r .i i i l r r r ti r l r
tr r i g tr .l t;i , tr ttt i tttl ttr tt, r l ttp r 'i tttr i i r r tr l r r ti ( At.tl tr i
| | ) l 't l 'r , , | | , l tl {i i ;
l l l i 'I ;
l ) i Il |l ''||{1 , l 1 }? .1; l ,]l i l ) o r r !i l ) " l i 'i n r , ( ) l i vr r |i tr s,
I l l r r , ', r r , l l , i) f;) , l r u l ( ( l 1 Itl l r r ttl .i i i tt si ,r tl r i l i l cl r , r l i r r g tto si i r ttl r r i , r r r ,r r o H i i i r u l ,
'
,
r l , r r r ', i r r v csl ,i g r r {i i i l l '.r r l '' ( i r ( ,l r r si v l u l r ,ti o g r r l i cr ',
| )t I r"t rI r | ( )(' r | ( | I i | |, ,| 1r'rI
'
I r 'l r , ( , i l r x'r ( fcl l r l r i g l l r l 'i l r ') , i tr l tl l i l
ll,,
i tt sp r tl r .l l l r tl r l o u l r r i tr r i g l r .r r o i i tr r . l r ,r r l r r
'
, l l r ,,l f
f,
l '\t
'ulu
ti4tt
lttt
t , r, l t t t i , , i
' ,11
i qrr'nr r ( t . st 'nu i) t t t t u'r t lor lit r tdt iu: [ iu ( t t Jr t lr r t t l( l. il) t t t i|t t t|t 't || r t l
1,,,tl ' 1,4t(, tl lr : it , lt r nit nolt t it t *i t r lt sit t t lt lt lt t obI r t : l, it rt r lt nt loqir r ') t ir lr r '; r
rrrr IIui rrr.l (' r'vcllt t t liiili
:
tl l l i rttt, uii t uilabild, it r silr r r r liilir it t r . : ur r sit r r I l, or r r 'lr r r r r . r r r r lr r gir , l
rl rl rl l :rl r, 1r.r! , r r il, r xlillt 'r ,cr r cr izli, lr lgicir ,sl, r r ir r r or liI r Ir,|r r pl'iclizii, r r r r r r ir . r l, ul
rl rr, .rl )i u( r,r t t r cclr t iiicon( ir ir t t ( lo iicr ir l'( )t lr t il'1,ir r t ilvr , sl igr r f iilc cot r r plr . lr r
rr,, l r r! rrrrgio; llr lir r r r r , t r bur li) t r r r ovit ler t ! ir r zr 'it r it t t ir r ot gr r r ir . ,
It1 l ' :i rttrlant i. r lr t ntt liu r tn. giot t , nt , eLc
t : er eLr u, ltir, ) r 'lr t \ r st 'lr lt r 'lr r u{lr t 'r ) l! r iliir .
rl , ,rr,rrrrIrrrrr iir r r r r 't1x'r
r t , sislr i, ; i r lupii r t ispar i( i r r cllr la, luici,sr 1l) lr 1,ir $( r 'r . r : Ji
rr , r' 1rrIr.1rI ilrir',r t lr r ,it r vcsligr t l, iilc I it t liologit 'c si t t t t giogt r lir r r scr l''pixlt "r r zi,
'
rrr rl i , ,r r r.r i ti t, r , I t Sot t lll
t 'ii.
| | l':r ttl.otJtiqt'()tq,tlitt, rt,tt,ttrti.sttttlr<:crtbrall: totrpot lr'i o iu,t'irrrl,' r.lr.
rr rl , r.rni (,lr ) gir ut t lif ct elr ( illc 1l! it t lt : I uigt t 't r l pt r r pt ir r 'zisI ( \ t 'r r r 't r i i1t
l t,r, ,( n, l l ){i 7i / \ r 's( ini ; i colr . lh. , 1974) : - Vilslr r , r r lr i i rrI ri rr|,Ir I ji, it r r . : zr r r l
,,nr \ | .| | rl ,l or' psr ru.
r lorIrigr t : r rot rsc ( 30- . 10 r lu r r r r i) .
l) Ur ': r lr r pr , r r islr , r r {r 'r
0ir t c nU r ot t r lot xleir zii,iDLr r lilll;r lt r lt ; i I r 'izlr ,r u'lt r lr r l, ii|'i,
' r r' | | r.1,' f rrr.r r t r r kr gicc,
, I rrr rrrrrrll (.r l f i/ sllr ilicot r ) plot .
I no(
, lilioiit iI r l slllii r lr r lor r lli
Pt 'r ^zt 'ti,r; r 'r
i ,rrl .r , rr l rrl rlit t
icl, t l iu ilr r evlislnr r ll) r t r pl, o.
l) r r 'zct r {, ir r, r r or I ilir '. r li|ot '
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t ungir r gr ': r liir , nlr rpr t lr ilr l
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2:t{l
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, rrI,r;i trtIi r' ,rr l, ilizit r t l r lr , l ri{(,t r| (,| |(|l r , it t cit I r r t t ( r , I r t iur liologir r r spr
r r r : ir r l. pr , t r lt 't t
l rr, r ; rosl ,oti o lt ,ii,
t l lt t 'lct iogt t r f ir r vr ', r lr r ) llr li'i, ;sr : it r l, igt r r lirl , lonr ogt r r lir , : r r ir r l1L
, r,rrr;rrrh' r' i z11li, r , |t 'cl, t t x,r tcr . litlr glir f ic q. 1, . ) .
tlJ ll t,l,lutntt!ii. uIt .losti t:urln'u.lr ltttsltt ittrtrt yi tlt ;ionlirntii. rrrtnio
,,/i rr!rr' (i nr I r ( . $ir t t r o br r zilir t i, plr r libuziir , sir r r l|or r r I ilippl'l lt \ , il q. r r . ) .
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l l l rl ;l ), i n(l c osel) i aplr r if , iir st r lr vilsllt r lc ll5 r lo ir r r i r ; i nr vt r lsilr ilil, : r , lr , lolr
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1,rr" l i cl l rl t . r ligr ', r r i b: r zil; r lr i.
lrr slir'qilr, rtiri tleJruic avut irr vtrlclr ftrplu). cii \i u,n.rltaritr ltipruli
,,tttttr 1xt1sit
, nulr r o m igleni, llazilit t ii ( slu ot icu r r lii, f ot r ni r r lir r ir . ii r lr ,
trrrl l r' rri i ).O ar t at t r , s- asipr opus ( l'opcscu qikr ln, . t 9?7) ploht , r lir r gr r r r lir l
,rf l rrr;xrtrti cii,cu solulio t lg glucozii 20- 30% ( 20 - 00 nr l) , r r r nr ir r xilr r ir ( iiL'
rrr ,,:rrrr ptorhce disprlrilia manifcstridlor nenlopsihiur, rrl pul(fl, oli.r'i rrrr
i,rLl (li' ('onfiunLrc a originii hipogliccrLicc l urror clizl rrrigrlrro:r rr'.
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Alyiilo
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orcipito-ccrvicalc
.oeoipilo-eervieale
n ) 'I\ruumo,lismeaertebraletau ,rterlel)ro-marlrr,lrrrr.
'l'rr,llrrio rrrrtl itr
(Arscni qi Oprescu, 196?; Alslnli qi oolrrb., l1)?:t) r'iL rlrr
r rrl,.r'r.Irr,llt,rrl
ll,r',.r Iltuuratismele vettebro-rnglullnu eotvicukr irrcutrrlri,
o rlrvrsr,lrrlir,
lrr,rrrl:rlc 1i cii trebrie ciiuiate cu glijri, irnirlia[ rlrrpil llrrlrrlrlirrrr, rr,rrr
ri,'ll rlc k'zirnreu,tit ver"tebmld,,
cit si mtiduleril,.Silrl sil,rrrrt,ii
irr oilro grr[r,r'rrr(rr,
rrrlrIrrIrrliiesto oligosimptomaticit snu inexisl;ontri,in schirrrlrrrrrxlil'ilnlrlrr
r ltlr.lrt;rlohaumatlce sint importlntr:, sniclinl,alirlicrrllrr1l,trulrrrlrrrltt
Ntr
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l,,lrrrrlrrllrcnzi),llgii puternice in ceafii,,cu ilirdioli sltrtr rtgirrttolrrr,cipi,
lrrl.r ri sprr um5,r, insolite de contr'..rctlu
a rnlscrrlrr,t,rrrii
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4i rlrr lirrrilr'r'.r uifjr-riiIilorcoloarreiver"tebralecor.vioalc.lr)sto irrlxrr'1,rrl, xl, srr ptr,r,i.
rllzr.rlrrrii,sirrt sau nrL;i sittptone asocial.o(lo lrrfr,rirr(ii,
rrrrlltrlrrll'1.
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lt ) Ilisaryatiile Lefi&)ral.ecerait.:ala
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,
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,,
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t;r r tr :'r ttt|t''ttl tI
d r '.l i l ttttr ti sr tr l ttti r , t:i ttd tt,tn r r l * r tl 'tL i r
.
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iuvi si rritlri, f,,pii,i ,,,i lrr',jiut int,clscat"r,i,,
r-;rri:,.r.r,.
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,'r l rtr', rrsliirl irroit:olitx: coltrlclic muscul:lr.ri
olercite o iriiaiie de plex, rlrr,r
r* rit.'.' p. lr.lr'i, pr.rrlucind r.cacliir.:rso,sp:rstice.
Trebuid lu:r,tiin clrrrri
dora,r'e lt stabilirea diagnosi r
cului qi nnii factoli profesiorrrrrr,
c.n de pildii : 1a h:"n:Lalipiil c,,
Sccl cn i
borireu nincrilor prin greuti (, ;
lr z.ugrrli :i h tlli nrcsr.tirii,
.,,r,. llclpilzi crr braJr.lein hi
l rp | r,l ,,l ti ,1i i ' ;i cu gi trrl i n hi l ,.r
r r1crr" i t,i I r urri i sporl i vi t' tt i rr
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li' irf,r'irrziirpri,lrpo tottleauna
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o set.iede'ttrlburijr.iy:l,scullrr,r,:
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,rrli,'r'lrirrlr',
ntiinii si sllt1l,1 i1lr1,glll1l
rr.rrrlrlrr. rirr'1xrIior)
si {'rrrlico ort,itlsc (1,('glrurctrtrurtr,
trrrtsotrlar(irri rlr\
l:rttrrlr'lot).
ir lr(,r tnlriiLscrn(ruolll,ablou olinic trebuie si, ne Eindim cri silr,lllrrrrrl
l rrrz;rl;ii"lrollrf li gerr(rlit.rlc lirrrrle ntll.i
ctiopa,logetli
(;\rsoli 1i
( )t)',.r(,, l1t{i7 ,lohns(m._iiSp.r,lding,t9?4;Jnctctri -tg6-?)
i.
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$o el,ea,
Ir'rrrrrrrrrii<
rr (rrLri rrlcs),il{1a,rn:rtoriisau toxice alc nenlilur periferir,l si rr|.,
Ir)..l)r.oct'so
r:on4rlesiv-e
rcgjonalesau locale cu readlii conjulciir o
lrlr'...rrlui1
i.i.rl'ir:.
iilrr..s. crr,r..inglobeazi,nervd Si vasele; c) Iractnri c'rl.
.Irr ir.llrrlc;. {l). l(lcfi)?:r1ii (boaln,I[odgkin, tuberculozii) e)
I
-4feullrrrri
:rl{ rlr)r}IllIi l)l(,ttl'i[l.
l)rrpi.A.r'serrirli
(1962) cauzalgi,r,
Otr)r.rscu
pfczitti, trei grade : gri,,{l,tlI
rrrr r.r zirlsirr Lrcrrli; g|ldul tl_Il-le:t, uru ca;rzalgiaregion'ab (ciirl {tri,,
rrrrrrr.l...p.irul i,1r,cg rncmbrul .respcctiv); gradul al Ilf_lea sa.ucsatz,rl
,iirr,rlil rrzii(.i,rl l.',r'cnele sl: extindpeo jurni,tatc
rle corp qipot chiar.srr
lrl r('. ri rl. 1,'hil opusi,, cu tendinfii de gencralizar't). cr6tleri cii aci.srrr
r.lrrrili.rrrr'_rliu.ti
pr.cfioaseindicl{ii de diagnosl,icin cazu.ile cu srirpror..,l
t.Lrr',ir,p.li'L'rfir,, ,,ba,slard[,), cu topogiafie nesislienatizati
;i lierrrrir,,
rrr |{ I,iIr'IiIr'(|Ilrrrror tclrrrerripcrima],ic:r,,,siurlr'orn
f izioprtic" (al lui ]Je,-hir,rlr
i
l r,,r'|,rrl]
(.\t(.r)sop|ogr,rriv',
(rrl lui t,r116;.
-.i ..-irrrlr','rrr
7.i|.{}. rll11iiloloraco-:rbdomilale
|. h'rn\t,l0i.o.fNnicu}ui (f renalgia) esterealizati, r1oleziuni ilitatir.t r 1,,
rr,r'vrrlrri
irr lrrngul sii'traicct din regiurea cervicalii ((rr-Lu) pirrir
,l'r'rri.
I:r,rrir.lrrl rlirrh,griLului.In prezenla unei frenalgii trebuie si,
girir,lilrrt,,
rrrrr,r'r'isrrrr
rrlo lrlolelor invecinatc (ale arterei subclavicularri
'c
sal rrL,
1rlrIirrrrI.LIIrrJ.
}Lrlrnonur'),h tumori sau.infl?malij rlediasl,inale,l*, pkurilrr
rrrrrrIi rrr.I i rrrr,Irr s[rr rliilli'rrgmatico,lil pcricartlite sau ]t un abces'subliirl|rg
.
t | ll I t ( 1.
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c,,,,{,,,,,,,,
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ilillii);i,,lilll;'H,,,lllli'1i,1,,1;lllr,il"i3lllli,,l,li1l;liil'
lrcntm altii, rfcctiune netrologrca'
p'u'aaii"'
l'('v('lrtloitr{'
lll;'i,iiii;$iii.t"'i
(ecrrinococozil)
I ;;;i;;:i;,1,i''";:fi:i,l:i"illil,Nl
se ridiciaumitoarere snspiciurii:
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lit['ti[i:q1.nt*iltfli*h';,'t*:ffi
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7.3.9. Sinitroanele algiee alc mcrnltrului
Lttr rrotir,lir,).
l'rlr:"ii'
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zostcr A0
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rrtrr .. tr trrz:i ltrlr rcelrri,
lu hcrui:rdiserrl,i.l.s_S,.6ipucstczi.r
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r,|| ||,,.,,IIIIIIrrl,r.ecln ji po ultirneL,rieg,.lc.
1) Pn:r ntt )nalif icir ol' d,e re.flene.Reflcxul ahili*n este diminurrl
r.rr ,rtrrrtrtirr Jrfrilil rle aliscli*Sr_. Uleori refloxul cutanat, pla,ntar po?],h\
Ir rr.lrrlil, sirrr..ilp:ircchiar semnul 1ui ]3abinski, ca manifeiljaie
supn;iozio.
r rl:i (rlrr,lolilii tulbirrririkrr vesouhre l,scji te comprcsiunii raii^icul&r,.).
h ). I'r(;:(n,t{t tu,lb*riirilot de btet itata po:tie avs:i certe yalori looa,lizit,.
',,r rr. \:ii;[ol, <le.pild[, p:rrezx ilerorilor :tp-r,reiri ]relni:l discului Lr._S,,
-&_,u,
mu:"hilor ld_0Jd\DLltrslrr
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tl h,r,lue.:lui.
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il scll o{tcn{oI Jt ,t,,j.Lelornc p ).[to rugur,rlrer,ni,lrIis;ulrrr
L, |,,,.
frr lr,.r'rriilu
,li.:-r,lop.iu coinprciiunr piurir.rdiculir'i,se pcato rec,lizr,
, i' .r.Ir , r l) r.t..rllnLl , cu p-r,fJ
llzie.dL.nerv scit[ic popliteu ericrn, dc nor.r
,i, r.,lr,i l)r)plitouintern s:)u cl:i,' oinrL.'m (henidifah;m) cte
coadii,do orr,l,
i) I'tt'.:(,njdtulbu,rd.rilorsl i,ttcteriene ne poalc intlica hernii media,rr.
,1rr tr rr':r,ur(NIi:rirre,
c&rc comprimi $i I'ii,laiciniles:lcrute infet,ioare.
I' n I t l,t,me tlc d,itr,g
nostic etiopd0 genia 6n. Iotnbosciatalgi,i :
,r) li,olruirrtim cir, mrre:l rn ljoritatc rt rombalgiilor, a lornboscirllrrr,l
.
l,rr)1,.)cr'trr'rrl.,iiiL,,r.tlr.,t,,.s0it,lirr
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,L)j,r'i si.()pr*{ju, l1)iiTlAlstni si.Nirniott:su
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ir\tscni ryicollh.,
llif:ll
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li ilir,,f,,
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/, ) ;I
i tl r l r r r tr r l l l tt:,ti Io Ir Ir ,r tttttl t, ;j i :ttr ,ttt ttt tr vl l tt'
, r , r r a . r l c rl i r t r I tt rrr rrrr. l r l g i r r o ( sr x:i r r l ,r rr l c r r |l f tr t:tt tttttl l r r r r tr l t r r tt :r l l i '
( 'ttIII||t|i ]||IIII l :r l l l |l l
i l l l l , r l r ( 'r , r l r .\l r r l Il i tIi f) 1 t0 l ' si i i r i l r l i , ,;:ia l l t tl i o l r ttl i i .
p ti tt : t I rt I rt t r , tr I rI r' ,
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,
tl r r tl i vctn c ttr tl r ttt l l r '
l r , r i t l r tl i cttl r ttr ', sl i r l r tr l i L r l i si czi s, n l l i tttl i l r r
', , ,
I t , , r l r i l oi , i r tsi , sr i r tl 'i cl r , tr tr Ii ctt|l t'tr 'i ;tto r l ttsi l tt i r r i r si 'l r l ( l to r r r r ttl zt cr tl tr
l , l l , r . r l r r i r l tr l r u l l o r i l i l l czi r r i i i
6 i tu t si tttl tr tr tt tl c tu r tr l i i r l r r r ':rI r r r ''i r r r ,tr |:r I,
,
rrrlr.rlrrtrlt
l ,r r l l l r ti r ti
stttzi l ,i vr t- r r l r i o ti i .
. ) , \ r i t r l il r t, 1 tIr tttl tr i i csl 't't'r 'r tl i zttl r 'i ( l t ( l i v( r 'so J]t( xx's( ' sl l tl :r l ( r L r r r r r , r l l
| , I L (Lnr\i(c,
l u tr to t'i i r l c sl i ctttl tti , r tl tl t'sr r l l tt'sr ttl tl tt'( 'j I'l r l r r ) ti l ,r r ,,l .r l r r ',
, , , , l . r r r r r c r r l l l i r r c si r n txi i r l r ;.r .) .
I) o r tr ttl l c o t'i r tl L i i l r ', r 'i o l ctr l r ', r r r r r l l r r l r
, , , 1 , r r I r I o 1 .i r r r Irscsj
r
i l c si n r l l o :r u to i r l g i co r n l i cr l i ttst, i tt l r .r i l o l i r r l 1 r l ,,r r l ttr
l'
, l ) , \ t i t ! !i t1 L l r o ttL ti tr d ,
cl t';i t'r L t'i , 1 t'tb tti r r l o i r tl i r tvr r l r i i r r vcr l l r r '. l l r
, l r t t l v ti l .i o i i , ( i tr tl o scl l .i vi ttr l i ci ) ,
stl ,t.ll x) l l i ( f Ii l to r l tr r i r r l c r r l tr tr r r r 'r
' r i r r l r i s cj tl i o ( ti o r tl i n o n t) , tl c ti {:ttttr r ti tl tt vct,i r r j i l l r l r r ( o r r l co tr r . o r l l ,r
, , 'r r r 1 , r l t tn i cl tl u s o so s vi ci o s^ o l tl o (I()I I I I ) t i I I Ii i l tcl Y r l l ) ( 1 !( 'l r {r r r l ( l r ' \:r r l
, , \ i | | ( . l r ) r ' r r c|r 'r tl r r i sci r i ti c. Ir l r "co l tst,i ,r tl l .i ttr i si l ,tr t{i r r ( r :tti i ) , r l r r r l 'tr l ,'
t ' 1 , r r r r c l i ri o sl ,:tl i sr r l l i l cr p :r ,r i II o r '&) sl i r 1i str t, ci tttl st't'ttttr l r tl :t r ;i 1 r r ',r r , r r {:r
,, ,
tl ttt.t,r r : ,'
ci t 1 i su l l Ii r tttu l tl ttr 'i l ttttr l l i l tt
', . r l r r l i l ot l l ti b su l ) cu tl l m l c,
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,
l r , r r i i r l i scr tl o Ii i , L 1 - L 2 , sc p t( xl ttt1 , ( l o o l r i tci tl tl r :r , tttr r 'l o tl , r l r r t, r r
', ,
r l , , r r l r : r , r r r r i t'a tl i e l i i n l cg i u n cr r :l l tl ,cl i o l tl i i r si sttl l tt'i ,r r r tr r r t r u l tl r :r l r . l r r , r r r tl
, , r l r , r 'r r i i i r ( l i scu l u i l sI- r u , r l u l e r i l tt i ti l tl i l i l ,r r i tt 1 1 '9 - i l l ttt'i r:l r tl l r \) r r r ttr r r 'l
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' ' , , rrr ' I r i rr I rr i . Sr : co n str ,ti i , ;i o h i p o r r :sto zi c i l t l ,cr i r ti ttl ttt ttl r L l ttl r tr . l i ,'l r r 'r
, , 1 r i r , . r r l i r ) {1l l tl o se l l o o a p si t d l l r cl o i r si 'r , fl txr tr tl ,i r 1 l r l r r ,zi tt.
lr
r r ) n t ( f\tu 1 scm i o l o g i c se n l a i l o i r tsr xr i :t : t I i t t I i t t t t : t I (' i I l i r r l l i r l l r ) l L r r ',r
l
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r i t o l u l i :l tr , n n cl e d e fi ci to tl u tto l i i ( I i t t t i I 'rt t t rrt cr l l ttr r i l i i l i r r r r l r ' r l r ,,
'
, 'r 1 , . r 1 i l r Il cxi e i co r r p sci p e N ,b ( l {) l l l r {l ) , l tl tr l ttttt ;i IIi Ir ( |Itl 'l i It tr r r r i .l {'l r r r l
t , , ', r . r l r i r r l t s , S i r td r o r n u l tl e cr u r i l l r tl g i i r l ) {) l tl ( 'l i
l l r r 'o l i l r i l r tl ctr tl , i r r l r r :r {l l
, , ' , r 1 1 1 r g i lr d i r n l i o l * o r n tsi vi l h o r tti r l tl i scl u l i i tr ttr r l i r ttr i i , l i r ' l r t o r r l l .r r tl ,,
r rrr, r.thrhlllLi
( sp o n tl i l i ti ,
tttm tl ti i , vctl r r l tr .l l ,i ) sr r r t i r ti r r r r :r l ti r l i r r tr :r ( tr , tt
, , , ', 'r r r , r 'r r l l s tcttl ;o m , r r i r h n o i d i ti i
{i ( r .) .
l, ] ;\ t:ontl.Qitt tittl.t(Ild prin al,to t;rt,tt':t: (tu,ntori., ultrttsr: ttt 4llr l,t ', t t:t
n t t t l . l t tti n )
tsl ,c tl o o l l i l o i t I t t i I l t i r: r'rr I ri', q i tl o tttttl l .r r o ti l r r Jr :r l ;,:r t, r ,
l , I r i l r | l i r l i i l ttr r i tttttl i t, str ]tt) i tt0 l ) o tl xl l ) l ) ( ) tt'q i tttttt tttr l l l l l l ( r l l r :ti {r r i i l l ttr r |,
t
r N i . r , r : r l q i r r s{) l l ) o l tl i z0 l r ,zi 't,p r l f,l l .r , tr ,r r l ,0 r 'r r - i tr l ,Otttrtti , c{) l l t:r r .i r r tr ? ,,l r |l
. r r r , I r i r r l t t i , i tr u l i i tu l si ttc fr r l .,l rl t,ttl l r tr t- i ttl r r l tr i :r ' i i l r i r r i . Al ttu r tl tc Io Ir |, Ir ItIr :r ,
r l ) :i l tl r l i .
, r ', , r r , z , i l r i p r r i 'l l L r r i l t.r l r l i r r r 'i , 1 i l r i p r l t r l i t, cvIl l i r
t,
''1 , \ t t t il q i (
r l tl tttr r l o l s( ' Il ( tl tr ( r l l l l ( ' tt;' t ;r r i tl tl ttt'r 't i l , , 'tr
ttr r |u l u i
i
r l ' l r ' l : r {:r , i l l l l t) i
r r r tl r l r l i r i i l t 1: r' t t t t t t r I r i t I I t t i , l l r r ,l r l r r r ' ;r 'r r ' | ,,
:t
'r
1 ,,
Il zttttti r l i r r l r l , ( 1 ,
I r , . . r : r , t t t r t1 r r Ir i Io I :tItr Ir tr r Io l t. l l ) r tl o t( 'r r l i zr Il r i i r r 'Iti l t
L l ,
1 , . , ) , li r l r l i l r l r tt l ,r ti l r tr r tl r r i l tt:ttt i tr ttr r l ttl l r :r zi tr ( tl zr , tttr r t tt , l tt
r , r r : r l l . r . r r ' l r tr ';rl tr ) ,,1 L
i . \ ' r t r , r llt ir r I t' u trrto ttrl rrtrrl tr (ttrr' r,tl tti rt l ttttt tl t i i t I l ui l i rl h ) u\
r', rrrr,r : r r i, r r lot pt itt l o t,rl i z rtttrt i l tttl t i i p tr l :t,l :t :tttl ctoctl trl r)l t, rt (' (ri tprl l l ,
,r o l rrru, irrrri Irr I r' t rrIli , i trs o !i l l i , l r1 tIrl rtP rr
IrtItIl rtttItIt,l l t: rt Iti 1tl r' 1rrtIi ol t(r1rl i i rl tl rl
r rrl r l r r r r r : r r r r r li s lttz rtl i i rtl g rl )i tl i ' :i l i (' z i (x )tl c tl rrl ti ,i trl l itl r t' xci l ,l l ttl i l trl t' ttl tr.
i , t rt;tl E i t)Il l tr(fsl ozi (i i so l xrl rl r,
.,rrrri rr r li) . S r i r r r r r ri l i i tl t' i , rttti u rti l tr,t:rL s l itn
l i tl o pfovi l l o di rl l [oectl l i Ii i rl :l
,r,r,,rrr : iI r r n r r qlqir r,tt t) t)t.t.li ul l i :i t i L o (r'
' IL l ' & (o
, rrr:r I:, r i r uc r r r r {trri o o l , Io l t.i l t' i rp ro p i l l L c tt fotnr ro oul turi l tul i tt tl ri l ttl
,.rzrrr; r i r r r r r l. r ( , lr iu l l )s r)i [s ),s i fu i [fi (] i n c l rc s o :rsoci r.tzi lo, dul ' cre po 1r1rl
rrrl cl i rr r r ir : 1,c ot |s r ,i , i ttrttl i rl , s u l l l tfc l l tl t l c ntut i l l i i .
t,' r t t l' , r i t liol, t ! lic i : l ) $ p o n (l i L )z c l o u rb i i tt-' , cl i scop* ti i ; b) S potttl i l i l r,;
.) 'l 'rrrr r r ir ir , ' r ' lr , bt . lt l f s i l rLi rl l t i i rri h i tl i c n o (o a rc trrebui e ci i utate tottl ci tttrri r
rrr l Lz rlo 1xr',risii'rrlii,li ilgt'lyiuli i tlulerilor) ; t1) ArLhnoidite sphtrl(!; i,)
I i rrrI i r. rrI i I rr, fr lr rrri)nono|li['i', r'i|oticil I f) Procese inlhntntorii siiu tunl{)] irlr!
,l rrr rrr ir r r l lr r r z ir r: i1 ) I' ;o i i i ' .; h ) C o mp re s i L rn ea,Irel rLrh.Lide cX ,tre rtl ' rrl rrl
,.r' r \ trl .
:"- Nindrorn,rLL;ohJ-piciorreplczintii' corespontlartul slnclromului utttri't
:rrirLrrrlr lrr, trrirnLrrttl supolior', fiind gencrat (foflctea, 1967) tlc faol')r'i
! rr! ir{ t.ior(,iririr,r,snpri\ liutulni ganglionar prevei'tebral s:lu asullra pl(,
rIil,)r' \'(l,folir1,iv()trl)(lomino-peh'iene (afec{iuni alc por!:iunilor telmittrrlr,
.'i.. lrrlirrlrri rligcslrir', rtocl;iuni uter'o-anexitle qi .t,-ezicale,procese inflilltrrr
i,rrii ,i rrrli'r'trrl,ilrlollcrito|elle Di rctropcritolrealc, psoi'lo .,q.4.),precul)l til
rir. lczirrrri lrr,riiculrut (sponililutloze, spinclilite ry.a.). Se poate recunorrtlr'
l,r irlr o rlrrrolc lsooiirti, cu. rn:rni{est;d l.egetatiYe de tip simpatllgic t1t
(rrl l rrrl iili v . r s r r ' r t r r to l i i .D u re re a s c l o c a l i z c a z i , i n arfi cul nl i a qol dul ui , r' rrr
r, r'lrrrrlr sr, lir rui;cir,rile mai ampl ale acestei articnit[liir iar episodic ilrr
,lrrr,l rrltc zortcli: i.nt'ecinate (r'egiuDet inghinald,, lontbilrd,, fesierii,, Irr'lrr
rrrl.r'o irrlolni ir, coirpsoi), Irecrlm li dista] (in regiunile tibio-ta,rsialtii, r1t
actiYil, Si pasiYri a membrului inforiol
lrr.r't" rrrr(rrhlr';irL,nii,).
llobiliztre:i
,. , 'r i! r lr (.irzii {ir! r(.r'{)ir')
illl rcplusu1 o am0lioreazit) de;i de rnul0e ori se irsinlri.
| ! r'.i rr r { r r l) r ili lr t r t r i i l .i l cn o c tu rn e .
,\lrlorr,pr' l,oi,rhrrnurts9 cr.itlerrliazir,m{liologic motlificiri osljeoco]lrlf.
rii r.irl(, (.(,loirriri vilrli{rbrale {orso-lonlblre, mcciitici,ri ale arl,iculalici t'r'r,,
tl rrrrrl r r lr 1ii r r r r t ut i ()s i c o l o ro z e tl l s o -rn e ta ta rsi ene ($ofl etetr l -96?).
li. Sitrl,rr,nrul ctnaltr,hri tursiutt, iKeck, 1969, citrr,t ds Dofletea' 11)li?)
. rlr., olrrrrrrrr, r)tnologul sinalromului cnrpian tle la membrul supu'jot '
l,l rlr'.rl'rrolrrl, rlrr iritrtria nervului tibial posterior in canalul lLri ll,iclrrrl'
rr:rrr rlrrl I,ibio ir$ir-ilgirl.o-cirlcelrcan).Se $tie cii, in acest canal osteo-fil)rrl
Ir;,,'r,,.',,,,' r|(r|r.Lrltibial posterior qi r-aselc cilitoresc intr-o teaci fibrorrHrl,
Ileror proprirt rtl
rrr r.r,irrr irrl,crr,i;ocii sinovirle a tendon',rlui m[lchidui
lr rlrrr.r.lrri.irr l,iicsl, cilnrl, ncrrul tibial poiterior sc bifurci, inceidoi rxrt'r'r
1,1,rrl.rlr, r'rr rlr,stinillio notorie In lnulchii pia,trtari qi senzitiYl la plttti'ii
iirrrrIlorrrrrI rr,l;1iocsLe fiivorizat de traum:}trisme locale (lractnri lnitlrr,r
lir rl, rrrl r.i'r1) (l )rrlrr:,jii, ontorsc, di',-ofse intcn'erilii chirurgicale) ;sido picio
prin furtlicrituri, infcpS'trLli, a'mof$eli 1i dttltrr i
rrrl 1rlrl, rii rir, c,rr'.iol,ctizc:trzii
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l u L o .Itt.tl L L l i rit:ttsi i tl , i n }l l )nl i i i l i i n dcgol r,,
,
,.,r' r r , li, ,
r r ! s u l i ' r,
'r ,,,:'r c r r ilr , lilli
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q rrl rri r i, r lr , r r t t t llc r t ti , ttrttl ri l i . Ii ttl ri i l i L l l tIIr rl i ItII:il,ri l torrrl l rrl rili)l rl ' l l l i l ' t(rl i l
rl r ' r', .I ,. r| , . I i rri | .\ r r | )r' i i i ttl ,' r' ,rri i t l l l ' r t l i i s i rtl rLl ttci ' t i i r l r" 1r1r' l or' . l )i r11
rn rj t, ll r , t lr r l, r ; llii rl ' i l ' t 1 r' i i r I i ( r tl tl ' i { tt rrl l rtt i i r rl l 1!' r,r| 1' rrr 11frrl
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, , , i r , l l i l c r i,r r l o l sr r l r r [o r 'l :r l r i , r r 1r i <ri r t t t t I t t i .
'
7 . i l 'L t t t a !4 i tt Tl ttn ta ti ( h o ( ,l l u i 'l l o r l r tu ) si ^ cl l t:tr r i l 'ti zcr tv,r l l ) l r l r r l l l r 'r 'tl
1".lizrrli,
l t i L i vcl u l tr r l i cL i l r l i ;i i l o f l tti r ti tl r r ttso l i tl i tl ttfi r ,l to ( tl r r r l r cti :r l l l ' l l l
| | \ i i i i i t t s i )i t1 i i l o d i !{i l .tr l o i ttl ctr tr ttr tl r L l si tl ttt', tr tt i l i tr l i tr l i r p tr ' r ttl ttl r l r ';1 '
I l , 'r s i ( r i i l f s.p ]'c ci \,l o i i l i Fl ) l {r l 'r l 1 '1 r1 ) {) stcl i o i i l l 'i l l u r l r r r l r ( 'r , { tl i r l r r r r r l r :r r r l
'r i , , l , . r fi s t n s i i r r ti n p r r l r ttt- r tsttl tti , l t'ttl o l i o l 'i t,ttr i tt to l l l t;tts r r i l r r .,i r l r r :r l ct'r r
, r r r i r l i l o t i ' ( $ ';Il e t:e l , 1 9 {i 7 ; L i d vl o ;i Il u ca , l !]i i O, 0 i l r r ti t l o [r r l h l tr r , l l tl i r l
l , r l : r i | ) I o s f o u n * i n e r r o r t si tu fl t p o r n u l d i tt r l ci i l o i l I( :l Yi
l ) l i r l l l ':r Ii . l ,r r 'r r r ( l
, , r '1 . r , i t c l v i l 1 r | ti i g i ta l i p l .r n tl |i .
t'$ l I l :r tr r tr zr r l ;r
l ) o zvo l tl l t'cr ] l l ( l vl r ) l i l l l l l l i
1 , r r . r r i r i . i ii n l l al r r r to r i i
l o cl tl e ( o so i r so l i n e t.l ( ,i l ti ti ) , ( l i r ( ' I t I I I I )I (' r 'ii I I I I i r l r tr l r :i l
ttr :r i r r l r ':r l r r '
r , . , j r r c i 'r , l f i 'r , m i :L tl i ,r 1 e o ste o fi te , d c r o i l cfi i }{) fi o sl 'i l l l 'tl i vr r l sr r ,
t , r r r ' i . 'l \ : e l . r L ti e 1 1 i {cr cn !i a ti i d e l l te a l e o i ,i r r r L i ttr l o l tr l l i o r ' : tr ttr l :tl r r tr r r l l 1 r r r l ,'
, l r r , r 's o o r 'i g i l i ,
4 .1 ( lo D p o tcl o l l l l l r l i ,i l l i j i ( 'l r ( f, ttI( |:||III i i ||Ii L r '
o sl o o co n d r i tc
B.
PROBLEME
DE DIAGNOSTIC
iN TULI}URANIUI
TftOFICEDE ORIGINENBRVOASA
strtnqomteltce.
'?. Pielea_rece,
nAkdd,.sub!.ia-ld,
uneori pitald,, lividd, cle aspect I,amolil, rr. prrrrlcobservl i n,poliomielite, mielite;i altc atecfiuni medulare, daL
rI|rr.or't
sr rn ncl]lrpl0grljevasculrre {Arseni,i .8o1ez.19Zl).
''1.I'rr.zcnla tle Jlirtens, de eruplii butoase1i d,6 aspcite sclerodermioo
In,rLl,cI t -r'cvelatoare pentru siringomielie $i alte atectiuni medulare.
.l\'lot'maled,^,:I
Irfl!]ilit.otpd.unghiilor,precum ;i eJilarca degetelorss
. ,4.
rrlrlrr'.jc
lrccvcnf iu rlivr.rsclcalec{,iuniale nervilor'pei.itelici,piecurn gl
Irr ${ilu'ozrrin pltici.
5.^,lIipcrtroJia. i,inilor,. mergind pini, la aspectul d.e ckeirotnegati,o
.n
rl\ ^
l,ll l lll{.:rllo ln SlTrngOmteltel;. ltcq me lple reci, cianozalese intihese in compresiuniie med ularo.
rl:rr' ,.i irr hcrrriplcgiile vasculare, in'polinevritr,, pol ir:adiculonevritc gi iri
ull,rr nouropatii.
7. Arpootul do membru rogu, dureros, se intllne$ts in sindromul eriIlorrroliulgio,i:r,rd ogetul alb, ischemic este u$ol de recunoscut in faza agazilri ,,Hiltooplltrlocal[t, din sindromul Raynaud.
'\'. 'l'rofalemul crozio (sinouime: boala lui Meige i distrotia edcmaloau:'lI rrrirrrltrrurrl.localVat; edemul ,,reumatismal,- cionic al lui Desrnos
.rlrnr'l H.gr'cntar aI lui Debove; pseudo-elefantiaza neuro_artritici, a luiI
l\,lrrl,hirrrr
I lr{)rrlu,luiMilroy) repre,.lintg,o v&rietate de e.demcrorlie aib, Aur,
rr{lr)l(,r',-ou
lclxurtilio segmentari, avind _cel mai adesea_ sediul la ineml
l, i {,to rl lct ior,l o, uni- sau bilateral. Nu are * se pare _ nici o specificitato,
Ilrrr,t,ulli congcnital, ererlitar gi 16afl.jal1 dar ddmulto ori inso^,teqtebolilo
r\rorlo-{logonot&tivo,unelo boli do colagen, apd,rind chiar in rcuinatismnl
clorrio crr poliartrit5.
0; lldcmul
.rozat^aI ,fclcir..ulobrajilor, al gitrrlrri. al spnt(.lui ,"i al iolol
, ,r'HI|.rr.
il, |lInl(rr.lillii{rLiL
lrnoori fi rlo pigrn.rrl.rr{.ii
tri tlc l()lr git,ctlzii)
ho Irl.ilr(,!1.(,
irr pDikiLx k,r'rnlll
DrnirrziLll(lrirlrlt lui I'olrgorr-,1:r
rrolri.1,24t
t4'l
I:T.,.TULBURARI
TR(T.IOE
OST}'OABTICULABE
1, 1.,'nr,cl,ut.il,c
spontaneindolora srttyit fie insidios si fd,rri o ctuzii irlr.r.
r',rrlri,
Iirr rlrrpr'i,.urr
tr':urrnrliismrninim. Indolcnla aoestorfriacturi gcncrlr,,
. r utr'|' nnlsuinla ; a,)iliind igncratc de bolnav qi rlo medic, cintl anilr,,r, rzrr,rr I,rrllrull,rofunolriolta,Li
moderatd,,riscd,sii nu fie ti'atate. b) Anl;r,o
n, rzr, l'rrr!o (,ltl)ul.iri osoiirtc,cu deforrnS,rischeletice,dezxyi.ri, incrlr.h'i,r,r
,,jr',ri", IIirrL)riiiIi,i'ounlro (lc pgcudo:utroze do cr,lLlsuli viciol.tsr,
$i
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lric", compiu:ubil cu col nl.tlbosului'
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1r rrrr
i,i," ?"-iirli"t" ir"torie, a c5ror<lurataqi lnrplitrrrlirr.sirrl,
rtti asDccl, polifazic cu componenie scultt I rldlorrlt'lrt'{lt'{trrfot'lltttltllr'lot'
tr.tt
(cx transmisieautosomalL_recesivA),
tegateSi ale
l.]l,l,,l,l.l,rr,rlrir,
,l.llllll
polfe r(,cunoir:Lc
"J|'irlrXlllrlt.:rtr...SS
prin crr.r,ctentleretliiar, prin apari,:, II|,r,,II)I|:||L. rrr arlolcsccnti.prin amiotrolia
rizomclicd,inso1,iU,
ii d,r
r-|||r.U,Irl:rlr.\r{t(..cn|npo.p|in aprrilia de
sidri episorliccde conbracturi
dc clorturi pi urrnrtc de.miogtobinrrric
ffanziroric(revoll,'i::.,:.1:,'j]:..,j:."1
rllrguo\t rn), prin cs?mcnul ncurologic ncg-r,tiv (in afara
: |lrl,ll.olt(.i
t,rr'.',.||l(.r
discrelcrizouelicetl-tJ0% dincrzuri,)jiprinoramenul
,
p'obcide ischemic
r', ii"',ii;;;;;e-p'ind
la sitcnliu
I :rotr.yrlrtlii-bioelect|ice,
l ' :llr:.,11
irrl
'.;l].1:,I
ttrr',.ir
paralel cu instalare:l coftracturii cluic_
,"Lr{L(riir , ,/s' tiorvlanrl
$i gglg!., 1965, citali de Radu, 197g; Sr,ior
,1rSli.lrrri,1.0?5,r:il,Lli de Raa1d,19?g).'
.i. .l!tit'tt,,li;tr de origine eu.rlouind pot
se
inriini io:
tltittlt'ttfia,hipertiroid,ianiiare-o pred.lominanld,
proximali, (ce1m:r,i
.t
.rt
.l
.rir'.,,r l)r\r\.r
,1l t,.rtir,rn:rlrar sc.rpulohumcrali;, sc asoci.r,zii
adcscltcu fas.
, r,'ur.'l||1,.t,.rr,.t Sr .m
iologjc
nl ). dar cxrmenul clinic neurologio
i lr r' ri.{r,r I v, lrr. ox&msnul llMG
-der.uh
evidentiazi, semne minore d.e tip neurog6n.
t,prIn hip,ercortic-lsrru.
(indeosebiilin sinch.omutti,i Cusn'i"gt
l,:.::.,,,r::!
,.. ,..,.,),
r, ,r't l|rirr
lrtcs,.irrn3SCJlii,
dC obCZitate.
luir t'f ii pdltnr
sc itsetmilrd cu miop-rtia 11rogresivii
,r.,ltrr\,,
;t ir tlr \r.vItr..\prr| op&uz;cili,_
L, femciintroi0si G0dc ani, pieclominnIa rhdiir rr:r rr,.rllrllot. (irxloosebila rne-mbreleilferioare) gi
id asociazi,cu hipo"
l,rrrrr. rrrrr.rrLrr.i-r,.
I)i.lr nu existi frlscicula,lii,r,eilexele osteo_tenilinoi,so
rrrl .r)rr,r'virl(!, rru sc evidenliazii,alte serin6 neurologice, iar
examenul
ll\l (i rrr rtllvi, rrrrxlifiq"lr.iirirportanl,e.
ii;;i;l"r"i
'l
il'ft n,rlparc;m) lipsesc irampt'le trrllsclllrrll';tt)
ictrttt..ttt ttti'
-"""tr"c
spoirtan" stu pnrvocul''; l'i1,s's" rtllc
rrlt'li rtrllrrrr'''
':,i.1i""rorii-riar't"t,'to"itelot foarte dvoluatc, utLtl* srt
iU;;'i;;^
l'(l
o)
";;;pilsi apar retraclii musculotctxlinortstr)
; ',1' lf rr$l(\rrr'rtrrl
,rieotentliloirsd
IriIr.r|,'r,I,rz.r
r.irr.:rrtr.r'ist.i..r.:
parlicrrl:rrt
;iJi"al ;;; Eilta ii'ronr" alil,udini
(itr i.ttrt:t llrtr'lr'
r
ir'-pr"'
tali:r
o*onului'ri
oIfr,f
i,,rinLl'
'.rlr'
,:'i oiili'i1f
""
cu mindci' lijrrt:i, ctt rl.schirlct'':r rrrrrilirlailrr lir rrlr'
,;,i ,1;;i;"i;iopai:ic
itt "lrttrtl rlc H 'ttr:r'
i,,,:itifo"f,r."ia,.:u'buza,le .,tlpir'''. ciL rrslrIr'1l:ttrsv('r's"
rin t..ltnin l:tciuscal'rtl'rlrrLrLt't:tlirt lrtr lr'rtrrl'rrrr\
,,;','';;";;;i;rlIl:;
l)6j6r'ine) ,,q.4.
('niotttttiile )' S-tr'11'iocir' :rlil lrrirll'rrrrrrr
E.3.2.2.2
-i,';I)istrtfiite ntiolott'ice
sc pL's'',zi ;i.iiprrl .l'. r..'ftntliY lrrr'rl'tltrt
,,,, u;;;;;l;
.'itrluL
"irci,t
;ili,,;',,*"ii^"f,i*i"lj,''iiistroti
(srrrrb,'iLr,,lui.Sl.itr.r'l), tlirtlt'lt:r
r,
(J)r'irlil
'ijo!r'icL
rx)rrA('rrilr[
cit fi 1'rtl'rr'rtriulrrlriir'.
,,,i,i,ini,lii intaniilr'i,(congolitalrr,),
tt
t'lttttt
rrrrlil:i{i
t'r.'t.zittl:i
liii V'rr liul.*lrr:r'g),prtxtiirtr1i rr,,irrr'rrri,il,,iriile,
tl r r r t tttl tl tl t t t
l)istr:4iit, trnrsculorepyognsiac
(llNt.l,1rlt, obicci nu ct'e0il,zii
t , r l- {r } , rlc
l r .. l )l .i l l Il | 1 rri rto i ,{ .l u c ; ,:tCl ,(,t.(j
{
:
:r) l ' . r lir . l( ' r ' A , ! r . l ,i t r.rr{ l o ,ti trrri l i l l (rrl ro o ri l i i nrl spotarl i ce)
,lirl
; lt) Dol ,r,!. oi r ' , lr , v ir s l ,r.l o rn i r:i ;i rrv o l tri i o l rtn i , L, rl trl i l r.oxol l l bj i progtorrrl r; r,) . , \ l, r ' oii. rs, i t lr rl i c i l rrl rrr,rl ,o l s i rri ;, i rr rrrti rul rnl .j ol i l tr,i ,rr (rirzu'
l[
' .l l ' l l
lllr4
.Jl
*)'i.'ri,1ll1,lll],il,["i,ll.il;]11,,:i;,;;;lil''i;i,,i
(r!.*kr,r,
rri,,
|iil#{;j;4i#:"1{H"i"*:1,;irtv:{rli*i
li",illii*i,
itr*,#,F,"?H',:g::'*".Te;:"x"*;;t"lr'***:.i1
iilll*#*$nllt*s+:t$u""ttll{y#'i{i*ilr
trapartal t*nr",]Tl'j.".1{'_!1['"ti,.f;"'.ltlii,il,l,,
r,',r'mer1ul
;,
,rirrr,.rri,.r
rtrrirrgr'.t:r{:r.
co'sLr,r'
rlupii,
in deglutilie,
illlili"rixffnJ:"T,:?;,u,n",ii,ila
"#
#'tgdllt*"t'
I
j*j*;,iitill,
T+?,l3""i'ii,gT:?Tg#
lllj#ii #*""qf
l,illlitiirl;
#t;;
.rl', aroplitudinii potenf ialelor
i'i;o;"'ni"t""-ql iinioii"tt" 1972, cilati dc Ilrdrr, 1178)
.ttltt irrrl
s-au itleniiticat qi conl''rat i' .lf i.rii ir'tri1i
4. N eurorniatoniilla
i,rei entiti,li cliliee :
"'T"'lll;l';:"1'
;ll; ii'i
:#3Y'Hi:#i11:'i:'1y?i1t,i"'f
;f i;*;:'"*J,'"
lll#,*ihttn*:xl*x;'*,:xx"l"*:lig;#T'r*il'Il;
llr"i.mi$*;i":,:ru1"**L*"'l*lm:i1,i[i:t;
;'l,'l,l'
Tt':$tH
tll'iiiliiilil''llil'
;ri:ii#:tT&f;***tUx,,*gt,
iili'',1'i;l"i:llll:"1
.'"li-X"'gnl,#x,?".'ii,:,"1"i".:i:3-S"'#;;'f
.rrloalte etiopatogenn.
*LiJo*..l8l?r)'1,?
(inilamatorie
i,j.nai"cta.e
,',i:ilii;:,1;1,
f.,lfli;,illllJ,illiltlll
.rlr.';'ir'';i('ir'
l,ii:ll..1;:lt-r?ffi:J136;3#;ru;;ilil;;i;;;i,r,i,rr.ii ' :r
iil*:.*u:l*',";t**l*i3;r"l*:;*:r':lrifl'l"liili:lililti
jli,llrlrt/.uri
-,fi
iil-]j*fl%Tr"*fi
,tlt!t"';;"ff
inl"+i*,r':#l$
{ Ii{)hmer qi colab., 19?1).!'er
;x,l**mii,lmnl'"t;"*'*"*:"t'8"J;1".h?'li:
,,riitffi"""
atlf"hlor
lrittlrtritrltttrtlt'
ti'ipletelor tli' tetanic llx^ir'rn(rrrrrl
$i
ob,n,'i"-"*".o""l'ol"ifiljl
,:'i,i""ii,rr"
ii,;liil;ll:;
i-iri,i,,]lll:ilil;
^-w"in
de lihre alro
ll'? l), tir plrrje
tirl;''Lll;;n,*+:""i*iii"lili
;;"'"liliiil+iffiii'hii;:l'i'lli
! ('grnl:t'ir,re(Pctttlolutltll, I t)?5' I $79)
(Isruurstl{xil' ll)li,i)
)nt13('l([rii t:rttt'Litt'ui't.1
ulr'uZdc ,,rul,i,t:ita,l'tt
r')
:tl ttr t
^girr.tlt
, 'l l t r l i t i t 't l , t : i l , il ( fl l l i l l l l ,l ,o l 'r l tt tl o |' tl r r tti i r 'l i 'r 'l i r r r r i l 'tl {l r n l r n l i ( r ' Str ttti ttl o g i l r
i,,i,'
l l l l l $ r l l l l ,r ti i r l i i tr r l 'i ,
Ti.'lii:il,lll;1,'l::;,0i,;lirlilll:"lll;1,'if"illi'
l'l:,,ii,',"1
:lli'/
('tzri' , ir r r I i' iI r r , | ,rrru rrrl i rrrri rr l i l r' r' l .l rr' ,rs .rIrr,r.,rr .i ' i rr,i r.rrrrzrr
i i l r r.i .,A r,rl rr,
r Ii o iUI llUt h\ l r l rl i i Ii i rrrrrrr,o trru s (i trl l l r,(,.
, \ . , 1. t 1. ?. . i.I ' r l i n i tri l r,l r, r.j rl i c i l rl t, c rrl trrrl ri l rrrl l o ol i rl i l i ci kr prol tl currr
tl c tlir r gt r os ic
l , ! ir r i rl l s rra n l r rl c l l r,I)l ttl(j i c l ( 1gl .l tl )cl ,zi lr,
, g. nl -L(l o rt,tcci i urri
trttt. r ' t l: ' r i. ir l. lr lr ; l l r.' l :i
,1,, (,1,i ,.,.iputi ,n,,rfl i ,,:i i
l rti rrri l i r,.. r.rr,r s r.rrri ,,l ,rgi r,
lopog":riitr ot'l rrriLi trtlcsol, r'izorrrclicti, pscutlorirJopal,icti,
tlc ruturri infla,,
rlr.s,.rrcr':rl
iv:i ;i/s:tu
lll.]1:ll.il;1
.autoirnurili,nesupuihl,c,ctL er.olugie:rcutr'i,
l|'':rr.rrir'irU r'11lrr(':r
{r tl. rnull.'
t,licu ilrlcrl.sirr.c:r
ti]'larir[(!
--iir t(,-r,rur.ilor
rr |i rl:rr.irri l,rt si ir, lrrrochirrril,rt,
,.r ||ln rrl.:'|rjrl,..
nprruaso.i clrii,r.: iLltol
\Irr'{11(I}||I|rirri c hb., I,Jti3,1965' PopeSouqi R:i,tlu,19ig; Iropor-iciuqi
lolrrlr., l1)Ti]. .1.1)?5)-
I,'!iyi,',:.it'l_1,lJtiut;_tite
_(g:rnpul.I illpti \,lralton-Ac1ams,grupul
| I Ir||rI t,' ,rI('I ;I {i Ir Nlontli{lii tle Neulologie
L,(.,..1.._
($rFN) (\-ezi popescrl ,"i "naiu,
. '
Il,7,s) Nirli
trxohrsi' viLotice, ar<a.-curir
s_a crezut (priir virus Coxsn,l
'*rrl.i I3), de obicei fiind r,-orlba
r'liir, rlirr glrrpnl.
rle rnecanismeiirtoimune puse in
(l{r di\'{,tscinfeclii Yirale-(Ohouqi colab., 19?0, citali
.1rrr,.rrn|o|i
tlc liopesoLl
ri l.i.rrlu,.19?8;J)un12 colab., 1963, 1965) rlar ile mfite
;i
t i.i rtc piceso
lrcii rrtrr,llr,r'if
ictrttr.
rL) l)olin.iozilele acuf,es.i subrrctLtcse pot reclnoaqtc prin debutul
lolllti\ brucr').,.u
rnti,Wzti,". i"Urr.,."iai,.,,,
.sc np y rpit?
]:,1.1.
ll| r' f n l - i:llll
vrrt'jirllttt\.
t ttsr ttt.u ' p
tt t.u tL tlr u lp .
lI iu,l.oi.i.k:
sinlj acuzate la nivclul brale1or qi gambelor, inso!,ite do
.
i,tntt (rattlpr
Lr.t.iltr'llil ,1i
,mt6(ulc,ra, apoi.5i de parize'interesirrifs"g;e"t"ii,
l)r1,\||r,rirri.,:llr._t[rnrl)reJor,
ial uneoli qi rnusculat0ra faringelui sia rrd,hrr|| l),rrrUtrul, uuscnllrtur't cste.sensiltilii,la presiune
;i fermi, (indura,tl)
lr l)rll) ur. I,ioilexeleosteo,tendinoasesint insd, de obicei
no"mri",
e*J
r, 1r{ir li'r'r r.lLr. rl'' pulir':rrlic
"o
uloneuroiliozite, ill care se constat[ si'moiiifi' |l'r {,. L.Lt1.\{,,p]e(,nrr}.sitrLlbnriri de sensibilitate dc tip pclincvritic
;r:r.r.r
ryicolab.,1963,196b; popoviciu qi colab.,
.l)('1||rrlr{.ltoll',rtiLir'(l)rur],,
l.riiif. llr;.;,).,\itrt1,l,,tt,.rlulsqitr
,,tt04,tti t.steprezenli lu i1r|orirnalir 40o1,
rrrr rirz |r (t,'. r.{(' .i ( |tie. 1974.cif rli dp pup{-sr.u Ri,lu, t9;g,,
iiiriri
;i
L l 'l r ' 1, . lr llr l. r { l! . : { .i tl t{ r' . r.i o l j i c \(.l n l l o a "e. po.ki j udIl rni i ,, otl cmt
.ul r_
l ttl :r t r : , 1r .ll' , ( . : r lir .rt,.rrr:ri :rl ,,sp 4 , h r1 i . p c ri o l b i trri p,,gi l , pe
utnr.ri , p,,tur,:l
, '.
,t
t : , r I : | ( I | | I |( .
l'.
sl l,r'l
sittrplonteuiscepule
de cardiopatie(tahica,rdie,subticui_
,
,:t.','tt.'i:t_
\,.l.rri.r
rr.rli.i.1f,
blu,,rtlior-entricrlar.),. adenopatii,splenontegaiie,
ulcera_
ut
tt,t*{)"
tt.-tItdt.
..a ..
p t( ,cu n l
\L o !lti( t
lt,t
;;l of[;.
llitl
?illl
fr,nr('loHl)illlloHul)t(1lllo
sirrl;rlrrostfiittlo strgrrsl,ivtr
fi crolli(xf.lllrsciorrllr,tiilo
(ll ' ltl)srlt(,tn
lot. ntt cxclurlocllrlotLrfulnoull,rrlltt rtt ;tlocls rlo tlctrot'\'l,ttrr
lr41r'rrrrriclollllic :rl nrniotrotici, nta,il,lcs cil (lo pot {i rnascatodc fcsul,urilo
rrIr|)| :rI rrIii(r) irrrlcostdli cind ili rlu origin{t& In fasciculclo lnusculare profuntlo
(lirrrlrr, lll?lt). 'I'rchuic sii mai;tim ci fasciculaliilc,de rcguld,,ploced amio.
lloliir. c) Iltrlkrx idio-rmrsculalconservat; rI) lieflexe osteo-tendinoasecol
nrri irrloiJcl,dinjnuato sa,u abolite; e) Tulburili vasomotodi $i sudolrrlo rlcstrrl rlo frccventc I f) Existii, in unele cazuri semne neurologiceaso.
riiri(', rjil,r'cpulmit diagnosticul topografic: tulburi,ri de reflexe qi/sau do
si'rsilrilil,lto, cventual alte semne spinale.
4. INl.tatrodiagnotticulclerutind, incumb5, o sedede aspectereyelatoaro :
t) I)t:n.cn:urcacompletd,.' irexcitabilitate galvanici, qi faradici a nervrrlrri I incxcitabilital,o a mu$chiului la curen_tii ile excitalie scurt;,; lenlrrr,r'ca,,si miiriren pragului contmcliilor la curentul galvanic i scidercil
plrrgrrlrri rcobazic a1 muqchiului; galvanotonus muscular pa.tologicI creql0l'(rlr cron:l'xlllor,
trr" i rl i ' i ,x i lr {ii l, . r '''r {r : t it lg, . r j|r f r lr . lil sir , ir r g0t r r ir , li(
r ,1sllr r1,\ (.Ii I I i )i | |I , l, . . , . lt , r l
I' trrrA ol rllr 'lr r 'r
. I I lt t r r t I r r t I t ir 'I itNr
l t t tt t t t sit r r lt r r r r rlor r isr r llr l r lr , r r lll'i r 'lir ilr r r lir , :
i ,r,r,r' r r' l r, - {; ) lr gr 'r r ( . t . jll,r r sir r l, iI r r 1r o|I , I r r r I ri.r llr r r liili
slir r |lcr , i|r r r , .
I l. .,1ttiol.xtliilt tttit,lapulict rl, t,r,ol,r.tlir:
rnlidi,
1.. ,,1ttt.
id rolti.tr,tli.tt, bau[u, Lui, .lI t:irrt+f,It:rlirt, (paliotttitlilrt. rnttt.it)tu,tl
' , rl ,t! )..n. r , : 'r t . lr . r iz. lr zi p. ir r : it , ) Jr Lsl, , hr r : r alr it li, j b) _Al, ir r g. r r ,rr it iir \ ir ir
r, rr' | r' rror' r r r I s', r lillr r alir r , 1 l, 0 1r ) . 1. : 0ca, lizlrriLr lt igr r llr , lo,
t r r , l r r r r i : r r lr . r r r ! r ,
I
r 'rtrtolIir0, irr grriru':ll lrt'ixln'.rir ritnt0 lil rn.|rbrtlir
irrlirriorr,rrr ( i rrrI r,rrrlr, I rr
1,, !' r' ttl xrl ( ] r Tr u, alc, ; i, pclonict 'c) , ilr l la r not t r lir u'kr sI l) ct , i{r i , ( l
; ir r ; 1r , f l1, , , 1, ,
r,ttr,,U l i r/rr Lr r r r r Trlrr llhilr , lr , l 11) ; \ r niol, l, of iit , sc llsociizij,
t,rr;
pr r r |lr li, , ir
.,
,: ,., i , sljr , lj'c lir r r r 'lc r r r pir Li. Lr , t r r lit
11'r 'r r . lizir r. ,. r lr , rI i rrri rrr.:I 1i r r r lr r r
l\L
l, I l'
- llll) r '1r ) llr . loit . r l( . illpor . l: t niJ ;
lr lxr lir , , , lr , t , ( . ll{. \ r . lr t , r , t , lr . r ,
i , rr.rl rrr.l l ,No
i r nzilivc olr ir . r . t irr , ,
i. c) Nu Be const at i f asciculalii, t ulLr ur r i, r , sr
IrrIl .,rrr' Ii liil lir n, icli( r r c ( t l: ar 1n, , ot t , 1; r ecI inir c)
r r ici 1, r r lbr n, ii, rpr
, i r ilr ilr r i
;
i
r rr, (r' tr.l ll: t Ull, . , , r i. Si 1 pr czcnlc; i : _] t ipr . r t r . r r r r ir . . r , , . l. : r h: r : , sr . t
r I . ir r l, r . r .
' rr.r ,. rj ,.| |. r 'ir lr '.
ixlgji. r caci.ie I n( : njlr gr . r "li l: r , r ir . lr 111,, 1, 1111, , ,
^r t hit lXii, . r
trIr.r' Itl rI.l , i. n LCR
{pli. i, ) cit ozi. apoi_ r si hipr r , *llr ur r r ir r ozi r r r oilr . r r r t l; ;
1'r lir.rr,.{,irr,
dc <legcnerescenfzipc mlschii cor;spunziil,ol,i l.zirrrrii .,r,rrrrliri
.r,1,ri or' .r: iir slr il'. r zi lr pid. ; h; pot , i 1px1, . -si
|, r lt , . lr r llr r r |ir . i llr , t i{, r . r , . i
' ,l :r.l i rr:: i) I iind vor ba r lc u r f cr . qjunelir olici, , r . lr c t ) n, ilt r rr . ( 1, .r r r lt ; ,
,'rr l,,j/.il*i rnai extinsc (poliocncefalomielitri) po{
sil ,,ira.i, 5i si,rIl.rrr.
, | | r '(
| I| | I( | ( ) -
'.). A nt,ioNroJin
miel.opaticdd,in hentatomielic..l) So rttnl,il,rrirr r,lrpirl,
t,r,r r'()rril,riorealeziunilor cIeate prin hemolagiil,iriI.ir,rrrrrrIrIIIrr.ii
; lr,) li)*tri
l,;'.rl:i. rlr.,,un.{lctor
generator
dc
}ior.nir,.l,orrrirrlio
(1nurirrrriIilrr;
.etioiogic
I r l,rr,rrrl"(,
c1roFi,,T"t,
sau la_chesonieriI a,rxrnrirlio
vlrscrrlu.iir,lr,.)i
"q;
I J t.i*ir.iL tiipcctul ate
liip Alan-Duchenno Unililtot..l ga,. Iri Ii r|,rIr.tr,I lrltrrr
lr' ! rr ( irzal leziunilor cervi-calecu cea mai bogal,r.i,
vir,srrrrlrr,r,izrrl,ir,,
r'r,
l,'rrl'osl,(, r'iltii,
in cazul leziunilor segmeDtclor1,":S,; (l) $o:r,so|iriziirrrr:
r,lir.i..f lit,sc5,,
cu abolirea_mpid5,
1,rr,rr
a i.eflexclorosico-ti,irrlii r,rr,x.,{1rrl,*1r.r(.rl
rrll)r.iiri.s()nzitivecle tip tlisociat siringornicli.,crr rlislr,zil,irr
irrrrrrirrr.rir.ri,
rri,Ir,rrrliLl,t-r,
I .o) ln cazul unci hematoini.lii rrrrilrrl,.r.ir,
h,, $. lr,s,rriilzii,rl.
lr:rrlcrrlozirrnii,un sindromRrorvn-SCclunrrl
l.irrrrlrrlo lrr,rrrrr,l,o.
; f) lrr rrrrr.hr
rrrr,rlirr
Nc insta,lcaz[sublezionalun sindrtirr ;lr,r,lr1llrgic,
lrrrrrriplogiir
Hrr,rr
rl,rrrph'si( , h inceput.fJasc,a,poispl,stic g) $r srrlprirrrlrrroriiI'ii,iir,i
rr,l,,
I
| | ri :,,s;ulgltlloletrtr
ta tnccput, a!oi xantoolr)rnic,ctt pttl,orrrir,l
lri;x,rtrllru
r.rrrrr.,:r,
,.ji rnoderc,ti:i,crcrsterea clcrlcntclor c.lnlirt: (u,1,illirrrlir.ii,zii, r,il."
r rrolirrrrcltxrzil,).
l',.
..lu.iutt,tlii.le-littormctajoasr olo ncuru.;ittitpidruit nIr lln,tt tttr,,
t, ,t'trlt,r.,
rlitt rny'rlnl','nti,lilirVtin ullr uirusLttirinL, ilrr olrilr.i,r.rrIo,.:rIi.,
rrr,,,
rr ,rrrrr.lili.(rrr:rir'.rrilr.
liP,\r'lr,n-l)uclLrrrrrr.).rrtirrs{luilrt.rrlrrIirli.,irslr,iirrrlr
r,r
l,r rrrrrlrl'irril;rnrrLOtflascrrccl rrrli lrrlr.stlr,
ru 1r)|l.,i_trrLIi;r
Irgir,ii, Hi,
Irr,i,rr,;l
rrl.'rrrt1.rsr1
r.r:llrllr,irr,rkrsirr,
;i ptiu contrrxhrlitrli'r.],irrs,
Iulr|il, prcfrrrrr1l Ir. r
rrr'rIil'i.iili|rrrkr 1ip inllilrrrir,l,or
rlirr 1,.(1.11,.
or'l rrlri rfilr.s.rrrixislii,ni rrr,irrrr,r
rlr. |r.zirrr
ro I'rrctlillir.ir,.
I I I " rl tttiolroliilt ntitlolurlIttr t:u.r rrol.tr!i1
[r:rtUl,
l'\trtrt.tll:.
,,1tttt'tl'd. ttttiolro,lii.rtt,irloptlir,ru uolttlirrlr,lrlit({ iIilrr,l.tr
. .,\,.
.r l irrilrr'tl, ll)i'l):
ilrr lrlplr\ r(f(.11q1H16
, ,ltrlrlt,rrJrrIrll
,1. ,.lnt illt"li,r_rl.in lntliluidilt tulttilurll, r.r.r1i1rl.
rl,
ll (irr|,rrr
rt,tr,rrrit,
tlr,l:rlrlrrl|ii,tirttt,r.rrIirtrr,r,lirrr,ttrrl
Irrrtriliir,l.
{ il,i{ulvilo l)t.ofol'(
i l (,ilI lu,arlul{,ii rrlr,scrrlirri
(irr1,r,,g5 ,li ,lI rlrt n,ni),o arrtio_
1t'rtfitt, (r:tt tlofirriI n1t;1,e1)
Ar.o lir, rlgbrr.l,1 t opog4tio' [ista lir,la inclnbrglg
lrrlx.r'irr:rrrr
(:r,nriolrulictip Atan-Duohonuo) qi iiii,ovotuoazii,
lent,_progresiv,
|lr ll,lrnr\I)rally Ur.tntl,uitrciLsucccsiune ]ezionalii,: rnu;chii erninen(oi
Irrrrr,rrriii. hipotrrnir,rc.(nina sirniani) mu;chii interusoli qi iombricali
;
{r||ill:r.$(.lt(:li.lir' i);flcxorii drgtclor. tmina de prcdioalol.); esDensorii
rlrrgr.lr.lor'
(r.a,rotlansformi, mina de predicator in r-niniiale ,,marionetX,D)
I
rrrrrsllrii brt{,ului (,,brrr,f,ulineft
$i btlnnt',); muqchii limbii (mai tirziri).
l\lir,ilrr'fi rrrult rnai tarrliv arniotrofia atinge qi mu;chii rnembnilui inferior,,
tnurs-cbiisrlqrulari, murychii abdominali. Aini6troti'a se inso!e;te totdeauua
rlo luscieula,i;iiovidcnter incd, din perioada de Cebut.
. _ lroziu.ni aualoago pot cointeresa .si nucleii motot'i ai trunchiului cereIrllr,l, r'o:rlizind. polioenceialita superibarii cronicd, (ct oitalmoplcgie nu, l"l,ri_
.1lrogrcsir-i.), rcspectiy polioencefalita inferioari, eronicX^(plralizia
Itttllrrr,t
ii plogrusjr .i).
a
. . .). ,IniotroJia.din ,,atruJia m,usculardprogresiud,spinald, su,bacatd.
1,.r1ll:lr,Zu"rt
7i Alajounninc', /, descrisX,;i Ce Stl,te Driglincscu $i Olteanu
( ll)l-t,";),so instaleazd,destul de rapid la e,rtremitilile tiisiale ale rnembrclor
tittprlioaro, sal eventual ale membrelor inferloar:c, evoluinrl relativ rapiil
r'ii l!1)gr'()siv,ducind la un sfirqit letal prin grav sindrorn bulbar terminal,
il rlttlrrs_dc citeva luni pind,la u.n an. S-ar pi,rea (Drigincscu qi Olteanu,
l_lrlir'j
; fJuhova, 1951, citatr, de DrlgLnescu $i Olted,nu, 1915) ci,-estl} rorba
rlo o vorita,bilX poliomielitS, (ence{b,lopolioririelitX)pur5, viralil.
:1.
.Am,iotnJin sltinald, iu,fantild, (boala lui Werdnig, EofJ nztnn ) teprrzirrlii,,in realitate, una din cele mai fJecr'onteboli genetice'atecopilului
(ittt'irltrn{,ir,
dc 1]a 20 000 de na;teri, dup5,Kriiger fi-Franke, 19?4, citali
rh Itrr,rlu,1978).
r,l 'l'ipuL ,racuf' malign (Radu, 19?8)prezint5 urmittoarele caractere:
- I,l'rNlitl,1,u rricesivii nclegati de sox; - At.ingcrea ambelor sexe i l)ol)lri;li)rrr,[oprcrnoe (uneoii fetal, dar iri generallntre 3-6 iuni - md,xi
trtrrrr I a,rr)1-.Alioctarea musculaturii oste generalizatii, qi deosebit tlc
r,rrvcrii,I *-llt oarirotcr imlorl,ant al amiotrofiilor din boala lui llierdnigIlolltrrir,rrtrt:stc cointcresaiea,,:i a musculatur.ii par,avertebrale,care cair./.ril./.;i{.ilrl,.r'r.:1,
in fa!i, a copilului in pozi{ie qeziridS,,intr-o atitudilc
iIrrr:-t''
(ll,rr,du,
1978); - Evoiulia esterapidd (3*4 ani maximum);
,,IriuItir,
r\ l,i|lgrrrrril trLrrsculaturii rospiratOrii determin,i, clispnee permanenti ;i
t cu;ril{,{;iorliafra,gmaticS,,p}eoum Si infeclii intercru'ente i - Aretlexia astc
l,olrtli ;i gonoralizat;, ; - Eipotonia este masiv*, generalizatX, sirnetricit,
(r'tt rurltloplcgie, hipcrlaxitate muscuto-ligameniar[, realizind- ,,p5,purya,
rlrr rit'1ri, dozarticulatS,')- Guibert qi Guibert, L974); - Iievelatoaro
lx)lrl nr rla,$i! a, hipotonie sinti Si abdomenui bombat Si faciesul inexpresiv,
ll lr gflr'it, tlrst:hisd, (Rariu, 1978); - Paralizia flasci, este generalizatx,,
tlilttz.ii,,rilrLotriotr,rlar mai exprimatS,Ia nivelul mu$chilor gitului, ai trun"
trltiultti ryiai ri'tdiicinilor; - Iiareori se constat5,fasciculalii; - Progresiv
nrt ilfuc1,oa,zi:r,
$i mu$chii limbii, masticatorii, muschii felei, ai faringelu i,
irt,t'1,ir,nliv
picinl
,ritnugchii distali ai membrolor I * Se adaugS,cifoscoliozd,,
ir vr,t'.o([uiD5i urroorl palaplogio in flexic; - Rcaclia de degcncresccnfii,
rtrlo nrrxivit; DII(i ontc alo tip naurogon (pericarional clc reguli,) ; * Nrr
oxixtll, ttrlflrriiri do sursibilitato, sornno pira,midalc, trrlburh,ri psihico
(t'itt'rxrt'ioligolirrrrio) (llronkol, 19?il, cit&t do lia,alu, 10?t/.
lt) ll'ipu,l.,,ltlttiy'nf irrclrrrlrrclrrno l;nrirno(lin oil,zuriqi so rrilra,ll,orizoir,zil,
(iarrrstxrlp, Ili07) : -- I )rodornin&rrlitr lrr, trrolnl)l'olo
ltlirr (lirr,rlrr, 1.1)7t11
!0t
20ll
! li lulij - I,'rwr;iotr
la,(,iikr
prrrzrrlir.1rrl,dqlu1lI -. ,l.rrlbrLrii,L,ilo
sirr1,.
sfincfr.l'irrtrllitrl litu., iir.l'(li\'(1
;i rlisr.r',:i,'
t
.u,,r)It'orn.ut,Duilorri, rnalignill, Ii .a.pig evolntiyii, &fcctcazil inil,iaI $i
rrlrsiv rrrrrscula,l,uril
irrorvati5,cle nucleii motori bulbopontini. Tiebui'o
rni{i:rl..rlili.r't'l!i:r1,1de
polioencefalitii infcrioar:i $i, dineirlrelcs, cle o
?
| |lt r)r'ii(to 1r.ltrleltlc(jlcDlut,l.
tle SLA (form6 lui patrihios ) pr(,do_
. .t.;) I,'orntu TtstudultolI ncuri,tri,cii
r||Iir trr,t''x t l'ctntnin.
sn caractorjzerzS,
priu al-ingerea
de obiceia gr.rrpcI'
i,rl rrrrI i r.[| |Ir,I (. jur.rvrlc dc sciaticu] p-opliteunyLorn,cle scil I icrrl po.-ptiicu
rrlrtr'tr, sir,u:I amhelor,
,insotindu-se.de crampe _muscularein repa-uJqi h
rrr),'sfr {le all')lirea reflexului
achilian, eventual si a celui rotullan.
j
.lt) ll'ipul uaenil de BLA .ear semlalat) apaie snb 30 de ani fi realir,,orrzii,.
cu 1trcc,;rde,re
amiotro{ii proxirnale pseuclomiopaticc scapulo'_humer.r1'lr.;i/,sau
pclvi-lombarq sau-formc scapulo-peronieie
iNclsoni5i prensky,
ll|7:. (.il (i tle.Rutlu, 1978; Cioran. ICZ9). r.arc por
diticultiDi diai:
",:ca
r'|:ir ,r,r',1l&nsflrtetnsa prin prezen{a [asi.iculatiilot,)
a lrlse,atol E-\IG,;
rro(l t (,llttol Dlopstc^sr a ovoluIlot.
Q. llormu Jarnil,iald,d,eBLA lpare inlr-o proportie tle 1?o/odin totalul
,r'ir,zurikndc SLA (Haberlanalt,1964), atectinclde fapt, tn paii,Iel, celulele
t'r'r.rrrIrri, antcrior, tracturile posterioare, spino-ccrebeloasi
,si piiamidale,
{tr''.r
unelc semne ce;rebeloase,de corclon posterior qipiramidald
li
-rrrptrcin(.1
( lil,rlu,
19?8 ; Kurlancl ;i Mulder, 195b; iTaberlandt; 1964 Cibr'an,19riij.
;
d\ n'orma d,e SLA d,in cotnplerul Gtmm, ( SLA - parkinsonism *
dtvtt:ttlti ) rru ridici, probleme riiagnostice la noi in 1ari, cleiit in misura it
{r,rr lrrti),stjii,formd, are etiologie virotici, (virus leni) li in cazul unor sinrl'r.r:rrrrrr
rlr.-Sl,A.rntilni[e5i .la noi in larii iu ialrloul senriologici]LIcfrror.a
J)ot sir :rpilrit fr altc simptorneoarecum asemxnd,toare
cu cele din ,,compler.rl, ( lrrir,rn') (fenomene ext_rapiramidnle)tulburd,r.i psihice qi altel6') qi 6aro
,i.rrIllr.l in'.xdrrbilc nozologic.dar care,probabil-rcprozintiforme .,sim_
(popoviciu ,Xil?ascn, 19?9i. S_a
, ' | (' rrrrIi i,:r.' ' (yilot,ir,c Nnu_degeneratit.e)
{ r'r|$Ii11ir,1;
crr,plcvrr,lon{:r,
SLA este de 100 de ori mai marc in insulele Guam
rri l rlu,,rlrlci[ in oricc altir,regiune a lumii (Iieed qi colab.,1966),o frecvenl,i,
rrrr.lri5rrrritrlc t'arc intilnindu-se si in F,itipine si in Nour, Griinee.Ilirario
:ri.r' Lrlr. (ll,tj7) alr rrjLtl ci, rle frl'1, ..,"ornpli,xulCrm,rn'.tlcbrrloazi ll
\ rIir|r..||rirIlll(.r'u Fr lt,lco cyolufie mai leriti, semnelepiramiilale precedintl
lrrr cr'lo lrrrlllilrr.
, ,..\\..lIlt\li& ]nusculard,progresitd,Aran-.Duchenne,prccum fi Tsoralizin
4trllurrl.TtrytqresiM,
DucltctLne
se p_arecd,nu reprezintii 6ntit;!i aiisiincte, ci
r,ii,, rrrrr,,jolil,a-tctr,
acestora, in realitate roprezintd, forme al,ipice dc S.L.A.
( llurlrr, 1971J).
l)
,uLault.plue
hbrm.aLa
t,utr
atipice u,e
d,eDr_1t
B-t-4 (_(Irinuu,
(Raclu, 1978
19?9) OSte
este tmpor.tani
important
; Cioran, 19/U)
't
-ryi6;Utofan,
Hll,,lio locrrrLoscutcin plactica rreurblogici: - foima mo:roparetici, (cu
rlrrlrrrl,
rlrrlrrrl,.lr runrl
rurtrl.din
din membre,
membre, de
cleobicei
obicei dlstat;'membru
pariplegici, (tot
forma ptraplegice
(iot
; - forma
('l
0 lr { , (rlisl;nl,cvcntual intii
cu| (l
rlolrrr{,
la un singur
infirior); a foima
; rlcrr l rrrriopa,l,ioil(rolatati, $i a,nterior)I - forma cu debut brusc; _ forma
|I| l Nrlt(.Il:r1,ii
mu$culare la rlebut; - forma miaSteniformi, dC debUt,
(ctr
i t l rr,llirri(,iiu
ull;orioari de fasciculatii Ei dc amiotrofii; - founa cu tulburtiri
ptilrir,o l{, dobut (confuzionalc, dr:melr!,i incipicltii)1
incipielti) ; - forrna
forma cu sonlno
somno
ux l,rllliliuuit.lulo.
,\.,1.:!..1.
il.'Lm iotrofi tla r ad,iculonerritice
.1. (lqvn11[py4
genetale:1) Survin ln or.icrr
semiologice
lil's1,i1,.
!) A rr, rrr
urr rlcbut tlistal, mai ales la sxtlcmilil1,rlt,
r',,rr,,r':rl,
rrl,lrrlrrrrlorilli'r'irrirr.r,
it l',rl,l i lri la,tt*:r,lcsi simetrice(in poliradiculonollil,u;i ;roIilIrrIirrtr|rrrrrrrIrr
tlar qi unila,teralc,chia,t'lrcirlizlrlc.,l) l,r.r'zirrlito
t,.rlr) r;Lrrrt,sirrrel,t'ice,
, lrrrr lopogllr,ficlit dicular'5,sau troncnl&t,i,,ctt txccp(ilr,polirrirrrrrrplrlirLrr
,) li(l irNo(cscrkl tulburlri senz,itivcsubiective$i/ slr,rr
olrir,clilrr (,lt lli.r'rr]l
|,'Irrri1r'||irrradicularii, troncularX, l]rultinovriticir, $i]u l)0liltovrili(,ii. ) it,I
rrr ,r1i'lirrlc (Lilninualeasau ab0liroa reflexr:lorosltrr-t,crrrlirrotulrr.
i) Nlrrr
, lrr,rr,,ii,
o croluiio favorrr,bili,,regresivS,cu cxccpljr ]x)ljl{rvt.ilr'lur'(['rlr
rr,rrtoIrirLiiIor')
geleticc tamilialc cronico..9) So a,socil,zfl
o li,l), rlrr lr,;irrlir,
, l.rrrr.
l0) Aplorr,;rrr
I rrI,rIrrrrrrrrrr,
;i lipir.ir.!.|)Ilareori s0 insolescde fascicuLt(,ii.
, |' ,1rr;rI r'i rrr scrrsibilit*tca la, prcsiunoa rnil,solor'
trnrscrrlarrr;i lr, Ir.rlrrrIrirtlrIuI,
rL,r'ror,s(,,11) illulbur:irilcsfinctclicnc rlc ol.liceilipsosc(crr (!)irx!ptii[]1irl
rIl,rrrrrrrrLrl
radicnlarelombo-sact,a1n,
inclusiv ir,lcoozii (lo tflll). l:J) ,l,rrllrrr
r,rrrlr,vlr sorrrol,rlrii,
$ocrotrlI.iiqi tloficc sinl; ft(!(rvcni,r)
iii iltlx)t.l,tutl(f.
li. .l t'ioNfoJ
ii.lc ru,tl,icttla,rc
so pot rcounon$to prirr rrrrrril,lo:r,r.rrLr
r11s1q,'
l, r',,sctriologico: J.):\rniotrof:il,csl,o1lrc(locoqi rrkrc1,ivii,,
ll,ingir)(lrlr,.lr.lril
!) Iripsos(jc{)[t]:aoliil(]la,scicullrrcq,i librilrr,rrr.lt) AiriHlirrrlrr,
I'rrtirlrzir,{i.
ir rrll
lnr'rl,/rrilr lll,tirliziifl:tsccllltr gntpolor.llusa lal() (inclr,:llrrrlir trrxlxrcl
r',rrIrrcirri),
cllro irnllrnril, o loDoJ{r'lli()spociu,lii,,r,rldicLrLllri,",
rIrr,I,or.iIii,
lirlrlrrlrri lii, lirlrrrrr lftlii.oitrir,(lit, r'ilnnlli lir rnili rrrul{,irrrtrqrrlri
;,i crl, Iirr'rr,r,rr
rrrrtrllricsl,rrinrrrt'a,l;
4) I rlkrxolrr(,$lnlo.in}ItlilttltHr
rlo rnl,i lnlrlt{r rrjrlii,oitrj.
,r r,rrl;rrltir (| i l rri t Irri l 1,() sllu i )olito pcrrrrii;tliagrrosl,it,rrl
tlo Lrcrrlizrr,r.l
rr,
irlrrrlillii nrrlirrtlirrrr,fr) firr srrr'Ir'irrrlrr
o ltilrocxr,illrbililillogillvrrrrilil r1r
Irr,trrrIicr'l,.
li) Il lrr,zrrlrr,lrcl,r'irii
i r[ r'ilr]iir,irri|o|'poslrrlioirrrr,
l,ullrrrrjl,rilrr
rlr
,,r
rtr,trtti Iri Ii 1rr,I rr t'iNlitrtrlr,tii,
olirll, Jrosilrilili{i irr pltu rlr lor.tr,liztrro:
lt) 'l'ltllnt.
t'rttilrrsrt rzil,ivoslll)i{rrli\{rr'('l,lizcllzii
{,tizcl(!rl(! ritrlirtrli gii, r,rr,r'rt,olr,r'llrr
Iot' tltr o,illr\ Iot {r rr,r,lr,l$
it|r'hlot'it,r
r'tr,ttr
Il itt t,irt lrrtr(rt,
Irt'jrt i.rir('r,llIrt'r'rr
r r t r l f r , t r l l l z fi
l(i'l
o l tl r l tr t'r ,
l l r r l tp r ,ti i
l ,{'l t
r l i l l ttr ,,
lrr
a0$
lrzir,l,(1,
,rirrl,r'il,
r'i1,(lii,i1iIilor
rlrrrll r;rr,lr,zii,
rlrrrrrriltrfrr ptoior'{irrirr loIil,0r'iul
lrrlrrtrrl lrl rrrt'sl,otriirlicirri. l,lsl,trIrrcvorri.il,
rlc lntrirxrtlrr\r
lrilillola,lil,rtlca,
rr rIrrlllikrr', I\'lirncvttlrrrlo oklrrga,{,it:
llc lli,rLicirrikrrrkrcliltr;ca,ziiJitru(fxitcrtlrrrrzr'irr,lgiilo; b) 'Urtlbtttir,t'ilo
do scnsibilil*tc obicctivir,s(, 0&l'aotolizoilzr"t,
plirr lrilrrxrsl,ozii,l,lLcslczii,unoori 1)rin hipercstczii, cu ilspect global fi
prrrlrotfiotrill,(lo ilsorncncaou topografie speciali in bcnzi ra,diculilr'c.
'i ) ,\ pr'orr,lxrt{)tdoaunr, gi.sim trtoclificilri ale ICIi : fic de tip in{eclios lu me
rrirrgo-r'u,rliorrlil,olc
virale, luetice sau prin alte infeclii, fic tle tipul disocia( iihrl lllrtuniuo-r,itologico in compresiunlle radicularc.
(1. AtniotroJiila d,in ntonon,eurite(9i mononeuropatii de ilba'se c.,rigini)
(rltrpil (.1u,ibert
Si,Quibut, 1974):
l, |u,racl,(/rcgenerale:
r,) A riotrotia reprezintai un semn constant, alar precocitatefl, $i
irrrlxrr'la,ntra
acestia variaz5, tn func,tie dr natura leziunii I este precoco
r;i inrportuntii in sindroamele tle secliune $i de fuitalie; tardivii $i discretl
rrr sirrrllotrrulde compresiune.
lr) Arrtiotrotia se insole$te de: parez6,sau paralizie flascS,cu topo.
IlrrIi,r Iloncularil ncti; diminuarea $au abolirea reflexelor osteo-tendi.
rrorrsciri toil,oriul jneryat de nervul respecti-r; tulbur5ri de sensibilitato
iiulrirri,ivo 5i obicctivc cu topografie periferici,, do asemeneade intensitato
vrrlirr,lrilii,irr luncfie de natura leziunii I tulburi,ri trofice cutanate qi vasorrroiolii irnportante in sindromul de iritalie; L,CII,este normal.
r) I)rucrilc pot fi foarte vii, spontane ira,u proyocate d.e citlo
rrrirlr.irli,rrrrroli ou hiperesteziecutanati, $i durere la presiunea maselol
rrrrI sr,rl Iirrrr11il, trunchiurilor nenroase.
rl) ltollcxolc locale sint abolite.
o) ll,ogr'oiiiunea,qi vindecarea sint posibile, cu restaurare muscularii.
l. lllor)tL(l,ascntiol.oclicedi.feren!'iatetn J unclie d,e natllro leziunii:
it,) lli.tulnn,t.r,l.tfu secliune aompletd: - Amiotrofia este precoce, proglr.sivii,i1ilirir,t'h:cxplimati, pe tnuqchii paraliz^\i ) - Asist[m la o paralizio
rurrrr;r|rrLr'i,
crr hipo- sir,tratonio; -lieflexele osteo-tendinoasesint abolite;
li,rrl'lrrrrrl
irlio-rnusculareste. de asemenea,abolit I - Nu sint tulbur5,ri
ilir ll lrrrlrioctivo,nici alureri Ia presiunea maselor musculare , i a trunrir,rrz
r'lrirrli|rl rroLv()rs{i
slrb niyelul seclidnii; - Se constati, a,nesiiezie
superf!
r,irrlir gbbr li, I - 'I'ulbur'5,ri1e vasomotorii sint putin exprimate ; - So
lrr rul,rr,l,i,I ). Ii. l)iasivl.
It) Sinrlrom,ul,tle iritalia: - Amiotrofia este de asemenea precoce,
.r'rrprirlri
Asistim do:lr la o parezi,, cu conservareatonusului muscular;
I
lirrllrrxrrloostco-tendinoase$i cutanate sint diminuate, rareori abolito;
llr,l[rr rrl irlio-mnscular poate fi exageratI - Se constatii impon;ante
lrrllrrrllili rrrrzil,ivc subicctive: dureri vii, Bpontane,exacerbatede frig,
rlrr pllrirlrrlr rrLasclormuscularo ;i cle migchrile de elongalie; - Adesea
rrrtlrlirrrlrrrrlriporcstoziecutanat'),I * Se remarci, tulburiri trofice imporlrurlr: tkr pirrlii, ostcoarticllare qi ale Janerelor.
11 r\inlxntuL da compresittne:* Amiotrofitu estc tardivri $i mai
prr{irrirrlrrrrsi,;- |)rr,r'illizil,
poal,oii c(,rlrplol,il,
tl*r tolusul rnuscularosto
qi cttltttLill.osint clirrLitr,litl,iv ('r)llr.rolv|,t,
1 '-.ll,ofkrxclo ostft)-1,(irxlirIor,so
rrr,lo rir,u l,lxrlitoI - Liol'lc.r-rrI
irlio-tttttscttlarc$li(J(1t)tIs(tt
virL; - 'l]rtllrrryrr,r'itbiLi,
lrt
tiililo solrzil,ivo
Asislir,ttr
tt
ltipttttrsl'ozitr
strlriccl,ivo
silrl,r'rt,t'itr,bikr
I
Iilrii,i'rrlJrrrliiljtlo sottsilrilil,lr,l.l
(rrilirr rlrr,lri
rrrrrrsl,rrzirr)
li l)rtir irlilrf,,ir,,
lrlrrl0$
:( t'/
' ' .l l ro t iilr : r t t r t : t t : ulut tr lit t lt '. , it r nilt I t t 'Nlt tt tt lr ( l( ' ( plt t 'it r llr lr r )illl HllHlr ilr t l'
r r lr , l lr i r , lr r lr ol' I i t t t r r "'ti t t r r l'r r tl: t t t 1. r r . 1ipr r l' sii' lt t t lr t lt t r t t
,,,,,rr,' ,i ,,* ' t i( ii,
( llil'clr kr vr l1) ] il'
',
r
lr
i
, ,,,, i , r,' 1,rr ',ti r | , , r'IrI t i r,I rIIt t I r ( I \ 'ir I illI ir i ll{r h( l lHolr ' lll lil ;
'
(
it
r
r
r r r lr l lt lt t lt t lor : t 'l)
it
r
s'r
l'lr
s'.
'i
ir
r
.
sr
r
lt
l?l)
,rl ,rl r rl i r Allct r i 6i lir l, r '2,
1i
( ] r ilr r r r
rl , rr| rrrrrr'l , ) NI ( l ( [ |l ( kl|l{'r vil, l{)Ei r t ', I t t "r lili( 'it 'i r lt ilt |. lr 'lir - r ' ( lir lr r z t Ji
Alil(
r
r
r
i
t
t
t
r
t
ll,
Nlr
r
i
lll?l)
f i lkt ln'z
cil, r r I i t lo Als( ] lr i r ii l] ol, r '2,
trrrrr, l 1l {i l l
sr
r
t
t
lt
r ; r 'tt il lt t
r
r
t
r
r
t
i
t
t
t
:
r
i
llt
r
cvclr
t
t
'
t
t
t
r
r
i
t
r
t
r
ll,
;i
i ,,,,i t ,,l t l rlii'l'r r l,r ili,lllt 'olliilo
: t 't r r r 't r r lr t 'l
i ,l ,' ,' ,' r,' r,, 'iii, it t lo r t kr r r t t t ir lt t t t lr t i t lt 'op1, 'Ar soLi; i I nit r r z ( lll?l)
I t tlll'( l
, , | | , ,,l tr' ,liil, ' t lt r t t r igit t r r t lt r r Llt lt lli ir Llr ': Lir r r lisr 'lll'ir '. ( t r ) ll: i. llt {r ( ] lllliilt llt
l'lllr
lor
lr
lr \ r ir t '
l{r
zilllr
i
ir
t
lr
lt
.
r
r
liilo
lllill
1.,f r| r, l rrrlilir tioo t t t lii ir r t lxr t 'llt t r l, |:
( lr ,, , r r r r t r lr t t
tr ,,,,,.1,ri
rrr lr i llss ( [ o ] i1) sil,( x) lr t lr lulr t i l, t r r lio t lo or igilr o t r t t t ( t 'lt li
r r r I t '. iriII I i1ii r r lr r r
l rrr I r'r, I irr)) r Li rr git 't lsuI post cor r t llr I 1,in lr cr nc ct r , iu <'r lz't ll,
r
[
(
o lilr Hii'r l( \ r t l'r
it
t
t
lc's.
lr
i
i'slo
i ,,r," l ,i i i ' trt 'r r r ilit t 'giit cir nsr t t r hr . ',
''r.'r l'ii'
l , rr' ,,:r, rrr r ur lr t 'r r lt r ipualil, ic $i at lof iilt
9.
A III
PROBLEME
DEDIAGNOSTIC
IN AGNoZII
0.1. AGNOZIILETACTILE(astereognoziile)
Constau intr-un deficit de recunoaqterea obiectelor cu
a,irr1,,r'rrl
.pipiii,ului de c.),treun subiect (cu ochii lnchili) ate cd,rui sensil)ilil,il,tiolducrtale sint intacte.
r\ccstcl, apar in leziu,nileyasculare
_(homoragii,ramolismente,hema_
l(,rnrc),lntrrorale,traumaticc.etc.,
lobului larietal qi ate g'lrusuiui
-ale_
rrrr;l.rrrnu,r'gin:r1
(ariatactognozicia,lui
lhermittd: cimlurie Z qi iO firoa_
rrrtlrr).
',,,,
,,1 '
;'
Brncrin,r
f:'&:il':"1#.,i','jl.'
VIZUAI,I,]
9.2. AGNOZIILU
(l rrshl u in pier der ca posibilit il, t ii t lc r t t ct t r t r t it lit r lt t il ( ) l) illt iln\ lot r 'll
i r;rrl rrl rrlvct lcr ii, t le; i llolr r avr r l nt t it r t t t t it li o r nuliI icr t t 't r r r vit lt r t r l'jit lr '! lzilivr t rr'rzolirli,, irlr liacull,Ifito sa,lomirl,a,lo sittl; contlcrv:lt,tr' I\rt, fi rlr, tttrti tttttllrt
l rl rr| i :
l. A1;rrozia vizunl"r U)ntru obittcttt txrt'esputl(lo (xr(iil,i,t'iil)$ilritrri rr lrri
l \l rrrrr' l i .l i r . t olr nt lc gr avlr , r t colli bolt t r t , vi r r lt loct t ll{) f i( ,t t ioi t t t t olr it r r r l, t t ici
t : it ,t t llt t i olr it r t r l lr t t t t r r l,
)r' r' l 1rl | | |ii ,, lili t ir ilt t ' pr opt it lr ll I igt t r i, , I 't 't r zot t i, at
', |
t lolt
i, t tt nit 't lll,olt ir r ll; t t lt li, lllo t r iir t t i( 1il, t 'll( f li'11\
Irrrrtl l rr,rl i s lilt t l, it ',illl Nnlln'( ! lt ( lilzt
pr i l l rl rr pot t , ol, r r 1isil {io t lost r ist r , St t lr it xr lt t l f ixollzit ol) i( x1i'lllrI ) t ( 'zilllt t ' r l
rrrrrrri r' :isrr r '; r r ir r Fli
, c r t , t t lotizlt {iit ,t lo lt I ili, it t gt r ,t lt r I l, 1t t t , llt tolr
t, Irr'
I i lt lt r st 'lr cor
lllllli ol) i( , t 'l
t lr r t r t lt t t it t ll slt ,t ', xlt cl'li. llo( llllt r ) : l, ijl( t f oil,
i rrl , r,r.r' l r,
to il, t t l, t r l, r ollzii,
ct t lt llr r lt r r yi t , ll'r r
l rrl r. rrrrrl i ,ir r glr r t t ir r l, ii t lit , r 'iiit , r 't , slitt 'xlt r lt ilt t zlli"it t t lt r ot t t r l'i,
l rr i rl i l , rrrr , i r liLilil, cr t lil , , r it t t lr r t l" r lo t t lt ir r r r l'ttrr sl't tt t t lt , i t t li[ t 't '.
r\l l rror ir t 1r t 't t l't 't olr
t it r r lr r ii ir r r r r ; lir r iligr t t r r 'livt ',Ht r t t st t t 'ilt zli,r lt r t t lllt , r t i
r
, lir r lr i,t t r t t lil'ir r t 1, t l
r,rr rl urr,ri r, r or r sl, rt t ol ivit , r lir lr , r ir , llr : r lit r lii, ' r lir t 't r , lt , t t lit xlur
'.','ll
rhr li1q11y
vizutrl ;i rlc rrrrrll,o
Iliclt r) rlii(l(llt) ll, rIIr1rIrrl
iIii,Ii|or,i rrI r,Irrr:t rrIrIr,
Ir.ir
rr
llcr,
ll)'/7).
1li
lfrl)\!t) (11)71)i[ (]cs(1lis
utno::i.n,
tiztr.uliiuptrt:t'1tli.r:ii.,
irr r.trt: r.ltprrli
lrrl.rr rl. rlisclirrrirlrlca, obit:rl'rrlrrir:s1opistiliil,ii,dai' ccl, tlc rcr:ulolriiclo
r.rl. lrrllru|rr,1i.irr lrlto citzrrl'i,s0 tnarrifes'tr:i
o,falid,t.r:t:tt
ttoalf,r:rc
a abiic'rtlu',
.r'r'rr..r |r'la,|rrrr,zi.
lrulnlrvul ilvinrl o olrecarc irLrudiredc liolmii cu obiffhti
r q ii|,lril (1tlt'lrg^noziir,
optir::i a lui r.on n'Iayendorf). S&u, ctaci obiectrd a
l.rl rr'(ittr1r)scrrl,,
rirunelos[u este ulteriol' aplicat ;i la a,ll,eobiccte, fo:r.t,to
rlili'r'ilt (,,iirloxicai;io pt,in obiect),). Ei po1 si, nu rnai rocunoasci r.rjci
, rl.rilr.. (,t4t,,,:it
). Stu diferoxl,,le dr. r.ulor.i.irrl 1ic,,ceI,rrlr,,
.t.tt,t,tltlirn
l: , t : i
alo
s!tn b o l u l i l ttr
r l r a Ii ctr :
r,
;'r r r r
t li r r r t lr r r l r t liliz lr . r r r r ll{ r , . l r r r r l t l r , l r z r r r . l ,i r 1 . i i , l r l l r r l r y j i
l i zu a l {)
l rr' (' ? , r| l l r
| ri l l l t l rl l I
r, rt j r' , . ri r'
,:r il:r
ltll,l
| rr
r( rr , ' l ' r,
t ilIlll
| ' . I | | | ) I | | | r ) | I,, | ' rl l
,ll Ill
r'
:
l
l r'
r , r' I t I r' r' . L rrl rr.
lll
I lLll
l )r'
' : rl ,
lll
o l l l l r,
l rr , rL l ,
l l Ii \ r ' lt z ii. ( it ' : t t rti ti t tt ' i t t tt t ' t t t t tl t,I l i rl rrl l l rl l r,r' r,l r, ol l i rr,l ,ttl tri ptrrrl trrro
rl i tt trort
,,Iri . r ' r I r ' r ' r . Isrr r ) ' r l i ' .i rrrp rrI v i z rrtrl (r| ,1 i .s l .a I.,t,r,l . i rrqr.i ,i i l rrt, (I. I,c{,i l rul ,
l rr J r , r lr lr v r r l llt l ,r(!z i rrl i l rrrrrri i u rro p s i c ).
, llt . t ir r . olt li( t i s t' , rrrl r,rri l i .s l i r..p l i rr1 r,-rr
i rul ror,i bi l i i l t(r (l o i I pr.i n(Io (
.
rrrir'r
.lrirrrl,
so Ir{.?,i,tii J,.l.ir,vrrl.i (dilL }rir:inD lrrrpol,tantelor
.rllr.
r.r'o ri r 'rr
r r . , - : r r r .lr . ir rc r.rl :rl ,l r,{ .i { .t1 .;l
d i s rl r1 1 1 ql sa1,
l stl el i ncrt acei La exccul i i
rrr.r, . r lr { t ( ' : r } r r r ( .l u (,b i l ,r,_ s rrr h i ;rr.rdi m r.n r i unaI o (fi i l .,.ra ti
un atacti c
Ir'r'r 1, . H, ,iir I l, ( ' { ' r 1 .1 ' c l o s )..Ui i b o l n a v i c u s i n drom B al i nt i l i apri trd
l i gara
.. rir I irlr-rrlrrl r.c(\tcin, ci la rnijlocul ei, sau manevreazn eulitu.l in
failurle
{rr.t)llr't{irtc l')(.Ll[ in c{u'e
trebui si taie o bucatx cle caine (Krindler,
t|)? ? ) .
t t,t
i r.
al e
,l rr 1ri r' .pr ot luo indeoscbi agnozii pent r u ir nagini I igr r lr r I r r 1pr r , iLr , l) r t liI r 17r \
r..r
, r' rrozii sllllialc unilateralc,, in vleme cc l eziutrikr cr rrjsli,rti sl rrrjl r
lir.r {,rr.r j/,l
, ,r pli'r,ii,tkrrtl a,gnozie pentlu
culoli.
e.3.A(iNOZIILE
lut)tTtvt,)
( lrrprirrd urrnii,toarele formc clilicc ;
l . l l ur dit t cu, psihicii l, luLt t sau r r . r lt u*ir rt r ur lili. i. r , r t ut 1t I r . lrlt
r .r lr r r r r r r l
;' , r' rr' 1rrrzgoit t ot t io, poit , t c.r O r r r lr it t irir t l, t , nsililil, , lt r t sl. , r , lr ,r . i lr , pr r lr lr . l, r I t r lr zr r
1r;r(i rrl rrllt t 'cst c. incapllbil sil r lllir l r r , , r , it r lr ,rl r llr , I r l. r r I lr r ir . |r ( r r ,ir r . r r r r r r rrrrrlr r r
l ,' r (l r l rl 1 , o( il. r vinlc si'1,
lc id'r r lili. r '. lr r . ll, 'r r r l lr , r . ir r 'lir ''rrrrI l i r.rrr.: rt r '; r r r .r , l
' rri r,(i r
,1,:fl
)ll sor\ . ii, t rlt. r skl ir r r lr or '1, : t r(rlol,
t {ir ir r l llr I ir r l I ii lr olr ir r r , r r(l . u : r ! . , r . , , r r r .
I' r.rl l t sl l lt r t , o lr ct 'cc1lo t lc r r r t t llo oli r r lr i lr illr r or , lr il. r , r rt lr . r , r l r iur t r , lr . lr .
I l yorrrol r', lot r ur i f . it . ) si lii lt gt r ozit t , l) ( , nlt . u ljllllcio r r c\ r , r . llr , lr r r r r t lr , lr .
i ,rrr)l ri nl i ( 'u sur dil, r Lt cit t ( r . l) lt , lr i.
::. S u . lit r ililo lsilr ir , r . . sp*r . ializnt o. ': r i) Nt xlilt r lt t r / . r r alr i. . ir r r , r r lr r r , . r
.
l rri .rr rl * i r, r lili't r r r r liir ,r klr *'i ir r r r lr ir r r r l'r r : r lr . r 'r r r lisr : r r r {ir r r r i. li r r r r 'r , r . lr , ;
l tt,\,1di l (l ra snt , r r gno; iu t t t t lr xli, , ,r i rrr,:r I r. rr. i I :r I r..r r l. ir ir lr . r r lt lt ( . r r. l' t r . t r r l
-r, rrfrr,(.rri t r r : r . ir r r r r ) ( i . r ', r r sir l. r 'li r ': r r r lir r r r r ii r lr , lr l: r zir , ) r ) lir t lir ulr t r xau
;
,uttrrt i rr t' ilt t t it ii: i t trr:t 1ri rr,. i I Ir I r.II r lr , lr r l, . r iizirliir r r r t l t r r r r . illlr ir . lr r r , i r rrlz r li r lr , ,
r l rl trl r ( ( \ 1rr,t r.r,1r( r:r , lor r : r , lli r . r r lr . it r llr r 'lir .
it'10
, l ' , r l l r r : t l t - i r t.'l o t.l tl i zi r ,tt':t r l r , r 'i r ,l tr r l r r r l tr :tt i tt l tl ttl t'i t si i tti tl o ;tr l l i , l t l l i tttttl i r l 'r r o r z i l,i \'o r r ;r l i ( 'r r ,l r , |l r ', ;[t,t l |r r l r l 'l tr r vr i ,
( l l ) l i l ) ) , l tg tto zi r t l tcr tl tl t l r r r tr ti p l cg i r r tl o ttt1 Ir tl Ii i tl r r ttr 'i
lrrp;i
l ftcr l l ti r 'l i l j
, r 1 " , i l r l i l i 'r 'i l ,o : l r ) l l tr o zo g tto zi l t vo tl r r t'l i i ( ttcg r tttr l t, vcl l r tr l i i , r r ' ItcIIti 1 r II'I1 i l t) ,
,
, r l r r , l o l c;l ,o l ) r 'cz( l r l ti tl c I t l t I t t I ri t t I t i i i l i i l ttr sl tr zi t'tr ( r l r r r r r i ;r r r 'i l i ) i l t 1 r r ttl t- :r '
'r '
t'r tl r t i ttt
r
r
.
|
, , r r l l i '1 l t) :tttttzo g u r tzi l t l r l i tr l tt[) r ttr i ,r i ( l ( ! ( ( ) l r tl ]o l l l u l l ( 't) 1 ,
1,
r r r r r r l l r l r i , p l i r r l r '- o l ,ttl l r u l ttr r l tl ,r 'tr !i ci 1 r r ,( 'i ri l tl j tttr ti l ,a ,i .( i l l , ( r o tl ) r ) ti tl i r l tr r ti l
lilr.
I I rntinsomutognozrla(sintlromul lui Alton qi Babinski) apare 1a bolrrr,vii crr lrt:rrriplogiesting5,,manifestindu-se la nivelul acest'uihemicorp
: a) Nerecunoaqterea
Ii rrr lrrlrrcl,clizoilz[ prin citeva si,nrytomecard,aterfut;iae
rrirr|r'rrrrrLir.ii,
)t
1rorlo o parte a tulburXrii morbido, a paraliziei (anozognoai'e
rrrrgirrrllii, r,r'i,epirralizat I b) nerecunoaftereahemicorpului stilg sau a
propriu-zisd,) r' c) uneoli
llrlli H(lg)rl(!nl,
rl hemicorpului (asomatognozie
irslo vorlrl tlo o cornpletii indifcren!5 fa!5, de acest' hemico4r, pe care il
igrrrrlr'i,,
c[ liirrrl o ,,p:n'tc inuti]ir, a corpului)' (u"nozoLliaJorie
); d) alteori
i6i r'(xilllro$(,
rrotttlltelo, dal lo polcoll dota\satedc cotp, sau defotlrolrrrr,vii
htttnicorlrrrl,r r(:llurrgil,o
sl,u rna,iscrrr'1c)
I o) itt unolo crtzttrioi perccJlrloLtti,
sulxrtir)t),
sittt
(ilrrzirr,
l,tttilurt,
tttirtttlrtu
ttrrtti
ir,l
sl,irrgi
lttrttop tttirytilri
lrrrri
I'oltrryiitttollilrr (iltr:tii l;irtrs tzirrlJ; l) rrriri t itt'itr
itr rrrrrtrrIltrr|o
n;xrrrl,rrrrr
!'t t;
)'t'l
li MelrrhrlJr,hurrontll:.t.\ ,llrurltul
.lurthnld ul tultutolil,r rr.pr.,.zirrr.r.l
. .
. ik'(.iIl.ll.I'L|||I|\.|||IIrrr1rtrirr,I
lr'.rt.t.ptl:t
lr,rrrrtrrllr.rtltri
1x.,rlr,,irrr I rrrlriI .rr.rll,
r,ir,li,ri0rrrr,rr
-\li'r.l,ntl r.slr. I,(:Ir'|,|)IIi,
r,.lrl, <.u rrr,,i,folOgia
.ii rlirrr.rrsirrrrilr,
irlu,rr',ir.r lxr:rtc tr l)cl.(:rT.rltt
ctr i.uIirrtlmi;r,iu,isuprrsevoinlei ;i lrt.lr.se:l
r.strr
l('flr,ll rff.f{flnlr'rts;.lt) ll[rnLreb,foh-lomA
lu urirrtputu!i sintirxct,priurlr|,.
rnl,/.l|u it,ti:
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ct(.., r:urL,
.
.lrk:yuIilot, alo }idiciuilor nervoase,gangt,eur.
l)r'r||lirI (,ttouiLlt r lrlrtltbru, not an^ll,cnr,in rnod jn-icrntiterrl.p.,rr.otirr
rrrrrri.rrrr.rrrlrlulirntonli suprtiul sau fLrzionatmembrailui
Daralizat..DIcm_
rr*. I:r.1r)r'i lr,L (xislil ;i la buloarii cu secliune
compleli iau llti Inziurro
:r nrirtuvr.l sl)I|tirnl,TlrccumFi in lcziuni talamice pal,ictale(ir.,,pi,,.
t
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l i i ri , rrI innif osl, iili pnl, ologioe {r il, t 'opol' r t lit t gr r I io sl, lll'llt r l' t 't t viI t I r 'I ot ,
;,rrrr l rrl l l ut 'iu'i f ona, t or ii ] ) r o?I 'iu- ziso ( t lu r r ut isit t t r o ; i t lr t plr r t t t t t t lr t t r , r t ,
l orrr:rrrcl ol5 i n silabelor ) , f io alt t r or t ia, , lil, r r t t t l, r lollil't t l f i r ', t {lr ) r t f ltt' or 'lt t lit .
f' r' rrl l r 1r)ilt ioaccst oa s0 t ozt r l'vil,t t t t t t ur t lul gr r t t cnll t V' t li*r t t lr ii, lt t lt ult 't t l
r rrol rr, i rrl ,t '1"i,
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l . ' l ' rrI bt t r ir r ilc t lo t t nisiunt t si ( l( t l) r onut t lit r t
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I rr,', r ' r ir|r : r , r 'iri . r rll' t r,i i fo rtr:rtrt:L tltl o rtL l l l i t.
I t ) l) is I uliilt : k ti q h : s t' rl a l ,o rts c rl c o bi cci rl ui r. rl t,l i rcl c Il ,rIi i {{)I rI i (,(L
rrl r'l i r r z r ' lor ' ( c l. l rrtz i t,(l o i o l )tu c ).
t ) l)islrrliilrt 1tt:ntrtt,stttt,tlttl ),r), poitrtii rrrlnelo dn lt)lacisu.
,l ) Ilinttlulit ( utrbirL:u,na;onutd,) csto o \.iuietitc de tlislalitr ntzalii,.
l,li ric (lrflor()si,(\ ttttot' a.nomulii ale rtiLttlui pt[l(,ti|r, si\t ll&i :],rles{}i.l
u})(}r.
l)t!t.(:t stuLl|tt (,[iri.i ml0 ?(r[dtine (plr'|rlizii ale rago-spinalului pt,iir 1rLLrrrr.s,.
IrLrllrr.., r'llrli.'lllro strlr trotfc*laro intercsind
r.ag i siniLron'rt,
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ad,enltile llot 1ttorlur(1
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li. I)i:;ltttt,irr,(:ti.ofctn.icr,
) cstc o tulltullre a cmisirtnii fonc.rlelo: si, irr
(,ir,1rti Lr,rrlil, tr cuvil-rtelor iri a,nsil:nblu, in tlisfonii,.i,ulburur,rea loi.bir.ii
rf (lil,l,or(irfc [tt,.ri.1tarlce.satt, .ptnli.zii $, ttnor elenzente
.loraalorii (b1121,1,i11
rr,l prLLriuLrri, liLnbi,, l*ringe ln spcclal). in toate accsie cazuri, limljL.r,ju
I
rrrllliol csLc crlnsorvat, or.icare a,r fi intenritr"tea paraliziei. Chilr dicii
IroIr.rrr,r,rrI
trLr,mlli poa1,c cmiLe akrcit, citc\.a suneijc fi'agmcltir,tc, c1 estc
lrlr'lirct lir,p,r,bilsil inlreleagil, sii citear,sc:is&ll si, scric. ln:r,cesl,e cazur.i cs1,r.
rorlrr rlr o lirr,r.iLlizienotr.o-rnusctlarii (a rtu$.iltilor labil,li, lingu.}li. relo
qlol,ici sau ir,lutola rlintrc el). Trezilitler, poaLe li
1r:r1ril,irr.i,
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|rrlo si lultolrt.rnult ii,ll,crate,citiir,r'SLrltju,1t,,. lD r.ltzuile arinsal,e clc pa|t
lr,,i. rrilr'(ir!,ti,slr,u totllli l, ru.uschilol fonatr.ri, i-lsisttirn lit o bLrp|t.iiLixc ir,
lrrl rrrri rLurrrrloilsc Ionerne, pinri la irnposibilitatca totalil, ll, rrorbilii, rczurrrrrlrr,ll til,cr':l sun{)ti} elei:neittnrc, sau l:l o afonic comploiil, ln it;ldiul
l rrrrrl r r , lp4t ir iir iilt ir l o ,b i o -g L o s o -l .rt)i
l (, s p l rl cel l e dl ,l { r zqornotul tl ahcoj r1 , 1 . 1 1 ,, ti tn p u l c rl i j l ti ni .
| .,r' , : r r r : J , , , ' l. r :rrr.
| | is.lon I il rt so i nlil n.tst: fn .. a,) Atitigcr.i ale nervilor recuronli $i
1)neurn(l
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;i rrrr:diastinului, care anNleneazii lalilguplegii
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;
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(l rrl l rr . r . r , l, r r : s o i n s o l e s c d e .p a td l i z i e
l ro S rcri rri ! vol o pl l al o-l :t;' i ngec I
r Il i rrl ilulor r r v r ilt ; i
p o l i n c v ri te , c i ,rrcp o t c u p_ri rrrl n,
i n corLl :crtul cti ni c, ri
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fi
l:rir;rrlri rr,ririo i,lrrticLi; er) |ezinni
vl,sculitre, tuitorale) infeclio:,se
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i
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p s e ttl o b l L b a re ),
:.1.tlisiaziilo (rlisicmiile lui {kr-rsx, 19i8, sau alistorriile vorbirii) sint,
.
lrrllrrrliili rrlc rr,r'rrrouici,a,kt urorhrllilii, ale litrnrlui si a,le caclcnlei \.tlirltirii.
Itr rt0 r ; ir r r , ir , u, t t lisr i l i l l l rr s i rrrrIi n te s i n L I e l ttiti rtrl S l l S ul tl i rntte, 1l l OCi ,r,,
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special scrisu,Lcopiat. Chiat
r r r r r Ir l i
l t sl ttttr "l 'r t t i l r l .
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co tcsp r .r n r h 'l r l i i sl Ii Ii i i
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r tl tr ,)
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ttttt'l t' t'l tzttti ' l tti tt l r "r r i tr tr . r tl tl l t'ttt
r ) . l l , L :i l r tl l tto :i r r i si a ,l u :i ti .l tt
r 'i l fi o t'l l i l r i l r r l i i , sc l 'r 'r r l i zcr r z'i ir ttttl x'l r ' l i 'r 'tr tl r r ( 'l r r r r l i r l 'r r (
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l t tr l r i r tl tt
l t t t t r I i t t t I c t t I I t I r I ( si tttl to ttttl l
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l;'llili:'iiT""l';?:':y;*
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il,l';i,,iltl;;i
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t"::#l?|::,;)
,,,,,,.,i111i,1"11111,;ll-i'f"r,11,;i,"1i,;'ff;,:i*ftf
l i l ,ri l i i i ( , 1 r . t iir c o o ,,c o p i e s e i v i l i ," .
,,,,,,it;r,.i;,,i1lll,!j;#::'1il:;:i1:ii.i5:*:*"l.Tlii'till,l;1:;i.:"",l1illlll
;;i,i:i
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;:r#t:iTiililt;tilt,lx,i
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It;tiliil:iiliiiil,Iiliji;iiirir:f
:1l ;
:It /
l::illl,lll
,:,'l:l
crpriinlre,cu al1,c
cuvinti ci s'"oru,in ii"posiiriii_
ll'ill,'rL1r'rr
ru rnl.r, i,ii fon;rturi.
rni..narilecorenpLUzrjloald
].,'1.
1t:.1]..:
),:,-,rll.
fcnilu
:r.
s(,,.\l'tUnir
trr \'utbrl'' O.rlii. .inrrr.rrrrru;,.Liimiinii, pentrU a ScCipriml
rrr vorlriro scrisi. Afazia, rnotolie cuprinde 2 forme- principale:
i,fazia
rrrol,olurprlrpriu-zis?i,(alemia) qi agrafia.
.1..Ll.,fcntkt {.a;faziamotorie propriu,_zisii, (mu,tria lui ptene Marie )
lrrrrsl,ii,.il imposibiiitatea dc exlximare oralii. Este produsi,
ae feriri"i af,"
..r)11111'_i.
,,irnaginilor.t)yorbir.if:lrtioul:lte, localizat' in piciorul trontatei
,
r t t , i;r. rI i rr .tilr{l r.nnl ru I lui Bluca;. r,u roI in eLaboraredm iscililor mus_
.
{ r, ,'r' .l,)rrirl,rftrn llrnpul !orbirii :r.rticulrln.Spr" dcosebire
de muLism,
i rrll ul irro(lurnrlecolo lutr inasi\.e,boltayiiflot pronunla
ci.te,uncuvint,
o,\i1.,l)ii(ta-ta,_ti-ti,rnil-ma, da,._nuetc.). 6i fa; efo"iui, urrror_,e
p"'tru
'rr
r rrrrlr.i.:rrrL.dr'zola{i;i i'a.cihili rlio-r.anza nerou.itci
Lenttlivci -lur de
.r ri,)lr'r.lolu-rocltdoiol gl.slU.l
ila|gi. ln lULmelemai Ufuaro,boitraViipo0
r' \ lrl llrl;b
''llo r:l
.'U\ r Ulp
Ci SpUt:
. , s l i U , d a f 'n U
p0sibiLif
ititor de,crprirnare,
pinilla tulilurii,ri
:l,l.,,flli:.].1:1ll.l,i
r.\
l4r, l|ol1iJ (in(,la osle nocc_'l,t,irttilizlrcr dc lcste spenialn.
-tA;;;1;;
Din'prtnof
r.lr v1'11911lorLcticr
estc net tletorrnnti. r-i"earizareava-torilo'
cirrc\e, 'orbi.ea
rompLrre limba,jul necesiti,o
:1.]'l::'
a
',1
, lllrrUl llll
lr.Llre[[, a tensirmii corzilor vocale, gi a "oor,loo^l" Ierfectii,
,,forrnuleloi, rnotorii
lrrrr'. r'r'l r-lilringiene' caro sint proprii, adec.iiatletietliirlii-ton"m.
s,presirir (,, si/ riiL. deteriorareafoncmeloi crpr.inrl: elizi.ni, asimiliiri (ex.';;ii
,ll l,'r ii. Fnniiiruri-. pri,{rclrnluc,lc,.eslcl ctc.). orrbrririiili
l],11"'j
11,ci.
mel:1rozo(bel.rilouiu iuc dc [ribelour.npc||inzo
iilll'l
( |)||,r,rrll:
rI I "l'
r.iri ll"'l'11'i'9t,t,
rLlu( de tliblioteci,). Se mai prodrlc unelo modific5,rif6netice,
r rr : rrlrzir,lizl,r.cilunor vocale dcschise,_diiiongarea unor r,-ocale,
asurzired
r'r'|)r'{'r)rso:rlre
sonorc' o red,clie g10bal[ a varia.fiilor mel0diceaie vorbirii,
rr r,,Lt:r,lizir,r..
a, accL'ntului tonic asupra fieci'ei silabe enuntate etc., merEitld
lirrii lrr rlislorsiuni fonetice complexe. A):i,joualirre qi .,;trlr. iig3g, -i?.6ti
rrrr r.rrrril, i.i[lic aceste tulburi,ri an:rtrice qi foneiice *.,b in";;;;i
d;
..;rrrrlrr'rrrrl,',rlozinlcgrlre font.lici.'.
arupra apra.:iei buco_
1i
_!nsi"lirid
r:rr'ri|lr.,
i tr lrrt ,rr r ntlJZtrcflar.oSt0t,
Itdllut,-ri aie eSpreSiei
oi.ale.
lrr
.urlrul turb,rEr or de articrrare are afazicirormotori se situeazi
..lr)
itt ii.\ltt(.':(4l.iitc(Alajouanine ;i colab., 1939, 1964; Iloriad_Krohn,
tS+Z :
I i, )rr,z, | :r(iz). Ao(,rtrt,l touic,. ritmul, tonalitatea,,timbrul si intensitated,
r,r':rliz,.rrzrr.rrr|'lorli:r,.siru.l,rozo(lin
rorbirii. I).jn pro.oai, oe ;t,teteEvariatiiLc
l, (i l s (,,..u l l x l l trtv rtl rri , fo i n ,t. atl esoi t,vorl l i rti ;l fi i nrl ' tyni si ,
('t Il t i I ri (.| {,]r,I I I I I lL( ' (' 01| (l
, (' l i rrrb rLs l l L i rri i .
r'.) fltt,prt:iitt
tttrt. lintlttjttlrtt. t\lrtttliIirt.. I|\|| | I)|| r'I| |rIrI lo:r rrr:r,iit rlror'
iirltl'L lr, un(,f lr,lit,zirri
rroruljr irrll o lrrrlrlr{,iclr, rtrlrrrxirriolrr,lc.lrlrlrlrlrilr,
r cllrillli 1xtn,lclii-- rlrrpii,clln jt,ln llrrrirrl,il,- 1,ulir,l
suplitrrir,l,i,
slr,rrlr,rlrrti
iil ( itcva lottc,rno: stolcol,illiilo r.'ctltillc. So inlrelcgcptin stttrol,iltirtn'rlnlt
o t eductie a limbajului I'olbit, lir, o e-rpresies1,oreo1,ipir
i
crr slrr ir'1,r'ii
sr,,rrrrr
lirltic lingl'istici, ca un fel dc .Loit-motir.,pe caro Jacksor)il colIrIrIr,r'Ir,
r'rr
tttLteflen de org5. Aceasti, expresie stereotipX poato fi corrsl,il,rril,ii,
rlirr
lrrrorne,tlin cuvinte sat dintr,un fragment de frazir. Io }itr(llrrsul r.orlrl
lrilirii, afazicul i$i poate recuper& unele formule &utomalrizitt,(),
pol,
r,rr,r.rr
rlot'eni,in mod pasager, noi sterootipil. Se intilnerytclroovenl; irr lrrrrrlr,
lornncle intra.er.ebrale (temporale; Arseni, 1980).
d\ Agramutismul se manifestl prin imposibilitatea rlo I rrlilizrr lrrr'
rrttrile (modurile de a$ezaTea cuyinbclo{ in Im,zi,), cuyinl,cl0rlri logiil,rrlli,
rrrotilurile qi formele grama,tic e ale verbelor. In cltlrnl lt,gnt,rnir(i,rnllu!
irlliilnim sirnltomnl denumit ,,stihr,[neorilor", carc conslir il rrlilizrr,rr,rr
lirtlrnlui la ilfinitiv, procurn qi simptom[l ,rstilul teLqr&Jid), r,it,rc r.orrslri
irr omisiunea ile cuvinte (in special de legi,turii) rlin frazir,.
c) ParaJo;iilr, j arouna;fa,zi,ik:,tlisinteniile. Oa ;i in a{a,zirr,
sorrzolill:i,
rll iitilziir nrotorie scpol,intihrj celcmai lariate tipuri tlepm.tlittii ,,ti;jtnlrttt
rr/,r:i;. lsupra, r.irola nu mai insistiim. La acesteaso Ldlrrgii rrrrrlilrrrlo
rint.;xit, (d,isinlari.ile), care constau in aceea c5, irnbiutr,r't.:
r, :rr':r,rr.|rrr,
rr
l l lzelDr comportir, confuzii. Disintaniile, numito qi lrt il,-l{lil rrll,isr rr lr rl
.,rlslarnatismeimpresive') se diferenliazi, de aglam;ltisrno l)r'ir l,(,(\.r,r'r,
rlrrc tleosebirede agramatismul adevdrat sau exprcsil', irr r,lrrrrcslr, r'rrllrr
rl(rritil.izareaunui limbaj simplificat, in disintaxii cslo volllr rlrr o ;rir,r'rlr,r'r'
rr r-i:tloriielenentelor gramaticii si ale sintaxei, cr,l'orlrrlr, lrr,rrlilizrrlr,;r,l,,r'
rrfoorentii, la conluzii in orrlonan_ta cuvintelor'.
l) $i in afazia motorie se intilnesc p erseue
t'ii.ril.( fi inlt).1
ituliilt' ltttt
t'u 11)
|1,,
:.| t
:ll il,
l rrr:r lr , r lr r r r ulr
l u\ i l l l cl rl t i i r l l l ol gi l l rr,rrl (' i r
i i o l rl tt(' l i l rc t l .l tl r. i l l rl r,L r,tr ,rr
1 r':rz liI
lir r r lr lr , j rrll rri rr p l rrl x r ,,< o l rIIIrIr.' ' (r! i l l i ti l (' l r[c{ ,l i \ r' .
* r l o J t .rrtu ti n rt l t) i tt :
\ ' orbi l c:t H p()nti nl i i si rl -i ri ,i l r,l 'rr
' f \ lr l r . r r r r r ; l, o rr,
l , onl i !;
r o rrl o |r r r i|s lc l0t (l o rn i ti s l l s , (l i l l c o l l \ (r ' sl l ,,l .i l (rrl
I)s ul i l j | i ,ri
o l ri l rlr ' lol s l, r L r r ,in tl g i u i k rt' l l l e z c u l i tto l l rw ri u rrLttl ui ; Ll oscri cl e;-utl o tl i l tl
lrolrr:r,ri lr, rn{ri $(iori) lLriLlc siuLlligut inl,o })o u}r tabl{)lr I .- l?or-estiltit, rlr,
.rrlll lrrr:icrrl,N rrl{ji isiolioar'o (are i-a iost e-\}rrsi i - C'onstrutca tlt i.r'rtzrr
r. (lolii, l|oi sjt,rrrll:ri lmrlte c[\.inte inpuse ; - Solicitirli tlc lcperrll e ri,,
r rr(.1( f J ( ilr \ ir r 1, c; i 1 r' a z c .
'!. ilgru.l irr (x)rstil,lrio o a,11;.forDri. t1e afazie r-notorie, caic eor;siir il
Irlrrrrlrrlr.r,lrosibilitir.t,ilol unui indiyid dtl :l se cxprima c[ rjutoml sti'isu]ri.
I,lrr,rc rlrrlurc\tc ur)ol loziuni la nivehil centrului ,,imaginiior" graiirt ll{'
r orlrilii, lolrrlizat, iir piciorul circumvoluliei fuontale, a doutl din cnisfcr':r,
rl
| l]i t .
l l :''r t
lloli
;r l ,'r ':r tl r r , l :l i o ) :
i l i r ,l o l l l i i , Il Itttr IIIItt, l l tl r ':t
' 1,, l,t,itrlllt
r ', , l : i r , r l r |r r i tr r l l r .t r r r l ,'r ':tr l i t, l 1 ) r {) ) i l i ti l r r i l l l ' g r r r tt {'{}tt( tIt,ti i Ir I Ii r ItttIt,ttIt|r ' :
l tt r t|l ti tr tl r , L i i l r r l l r r l tt:ti l tr r r t |r r ttItItti i ItI l l l l tl i :l l l .i |r 'l l \ : l r l L l
' r 'r r l i
,, 1 t,,ilr.{
r r u ,i l r .{ ;.:r .
t ' J , , 1 f i i i r l r r r ,r 'li Ittl l tti i tl t' l tl l tzi tr l r r r ttti 'sl i r r i i ' ( l sl {r l l ( 'tf( fi r i tt t'i ttr r tttt l "l r 1 'l o l
o . i - j o ( 'l ( r ( fl l zl l :l r i l l r 'l
,,
r r l , o r r l I v,r t l r i i tt l i r ttl r l t, sl r i i tti
l ) o ( '? l l o l t' i l l \i i ,l l l
'
, i !
. r t t t r l i r tl r tttl r zi i ( tl r l tl tttl i l vi r tl l ;i tl o r tttr tti r 'tl i t r t,tr cs]tr il i tttttr ' r l r r :tl r tzt' )
, L ', i i r l |r i l t,t'l r l tsi i i l u l L ttttl t,ttr 1 .,i l ttrtl o i r l i o t'i l ,tr r l r l {'l r l ,{i i l ( r l r l i r r l |r r r r '1 "
L , r r l I l r r r r i r , r i 0 r r tl l t,l i z:l r r r ,si i r r sl l tl ( i l l l tl tl Ii l r l l l l tl l t l ti l l l sl l l l l n r tr ! l l l r l r l r r L l
, , r r 1 r ti t ti r tl i tr l tl r l tl i l ctr si sl tr tr L tl tl stl tttl t:t,l i zl u r r r l 'i i ,t'i i tt tttr r r l tr r 'ttr t:r l
t,
,,,, ,r' r. ,rplilii
tttt ttvo r ti i i tr i a g i ti c:t' l tti si tttl r o l i ci i , r cr l r :r l :r
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,
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\ 1 , r . r . r r ; r, ttr r ,Io |'i ttr .|,i r r i 1 r tr .r i ttIi i , o l r r 1 to g l tl l l i I l o :ttl r ' Ir t|r t,Ii :zr tIi t, ttr l , t,
| , , 'l , 1 , , L r l | t||r i 'r o r r |:r ,r i r tr r r 'r r l rr r rt rrr' t I I I r r' , ;r r 'rr l i l Ir i r r r :t I|Ji i r 'tl r l tttL tl l r r ,:t
l l '.
r l ttr
./r ) r i r , Ir r 'r tl r 'i ,,r 'r ,
r l r , , r l r r ,l r , r,, r r rI r' rr I rr I r. r' ; r | ; r
r r r r r 'i l r .r r tttr i
{ | ,I l t' l r|, ,,I | |I ; (i ) . r \ l i ,r' t.i rz tr Ii trrrl .l r ,,.i ' r,rrl rri rrrr,l ,rri rr.,' :rl rrrrrfr.l ri krr.trl r,r,.r:rrr.tt[i
r.. tr' i .rq l ,,r.t.:rsi l l ,1.l ,i )l L, l {l (i t). (.l osl ,u;:l l ;
i i (' Nl, ' r ' i. |r. . 1. r r ri l ,i i l i l i rl rrrr(,i rr,1(,\.j
rlrv Jrr Ii1rsi1,0rlo t t t r t r r r ( r ' r El. lr s r r lir , r iU,r r , it r r l, r l r r i l j , 1 , l i r , r . , l c n i t r c 1 1r l i z i t t o " ,
I
,,r
|,:r,r'Ir'IrLrIIr,;Lo cu,.;li0r11, (,ii, .,l] 1,. lrirt1,r. ,,1,.r,1,1r,r,
srr,U,li, u |'r,cul o u:oit,t,o.
l,r'irrrrgLri,
..r'c .1,c.).f.i.ii;lt si desc..zco fafl o'reneaJoX,,
up.^"i",ii'iriiii
(,1,r
iil,r'u
ril,r'll(,1,r
lri|tic la
\- alu[(]ii
alu[(]ii pc
pc lriltic
la hazard
hazardlrngmeltelc
lrngmeltelcfclei,
fclei, fir5 a line seamil,
tlS
t',:,.]l].-1.]J,l.1l,t
jlir afir.rir,ror,,rL. La fel, crnd-i se ieri) si, deseneze
o cu,xttr,
|rnislcrci
.rrislcr.i stingi,
stingi, apra,xia
apra,xiacorrstructirii
corrstructiriise.
se.manrfesti,
manlf
n'in im,osihilit,,r,r'rr,
rl, :, r'r.;uli:rir,
r.hj:'r'cr l. mri simplu ,rbir(.le $i tjgut.i tpAlr,at,,dreDlunslll,
ttrrrrrslri.r1.,i..,.r'lr..c
clc.r. ln leziuLril.t.rnist;.r,,.i.lrnpi".
tr l6r;,;;;;-;J;r;;:
r i(rr, irrl,rlrcscazlrlrai alcs dcsunelc compluxe, cvidi.ntiindu_se tulbulil,r.l
rlrr rrliutLtr,r'r_r
spatriali,a-,,cle-mentelor'-constructivc,,,
rlisproporlii qi r:l1xrr,"
1rr i gr,rjsiln)
:r,k:diversolor lenf.ute dc cunstructie,'irnposiEititato de i.r,l,
lirrrrr. rr,lrorspeclivei spalirle si, dc multc ori, neglil#ea pd,rlii stirqaiiu
Iirrrii lcsortctivel'r,olrtilc tlo dingriostic seilioJugic sint reprezunt:lte do probcle rln
.
r|l's.rr ;i d* .o'sl,rur{ic rlin cuburi,.diu belc dd chibrituri g.a.-Se solicilrl,
il;il,lirlrL)sc|larcila dir.erse obicclu, iroagini figuri. tr-,apiobele rle
urtr.
;i
,irrrr'1,i.s. snlicitii pr,cio,tur si' culstruiasci, din;hibrrturi'un triunghi, riit
pl I r';r1,,rrrrrltt4rl,ulghi eto., sii,construiascd,din cuburi un scaun, ui girrl,
, ,'rriir, ur) l rLurJsi lc_cofirpun;iun orlr d.]n pnrlile lui componeirte
tIial,,i
,irrr .r11.rr, sr-r,,kragi1
din1,r-'n 11'I Xr dc be.te-p6celc cu dhiensiuni cg.lrr,
r;rr,rrrrrl.lrrzrrrlirL plastilini. construcl,,i,r,
tridirnensionald,se testeazri'irli,
,,r] $rr.r'(.pr.odu{,,X
din buci,li rle lemn de diverse foruur
:.lli.ll:1.,t','1,1,
4{
'll
rr:lrru. rrl,,tr.t(1.
rlrlcrjte, sau sJ, transpul_rd,
o iruaginc bid nelsiorlr,lil
(r,tiilirll.lie
rr t,r!,
tridimension:r,Iir(Kreindler, 19?Z). Testul lui Abcls,tt
(rl.lr;r l(r'(1i')([lr)i,1.97?)co'st;, i' solicitarea bolnavuiui de a marca pilr.l,uu
,orrrrr :r, l,rci tig.trli goorrrotrice suprapuse.
llrrl.rrrr,vii.crr
rt,praxieconstructivi, comit urmX,toarelctilturi tle arttstr,ll
,
(rlrrlr;r
,lir..irrrllrr',t977):-a) Conturul.clcsenuluiap&re nerel'lat qi'irrt,rrr,
lr) I'rir'(ili rlt:sc'urui sint- grcgit asamblatc,-putirrtl Ii izolalc lrrt,r.rr
I
'rrIr,t,,'
r'1.
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rl,:\,.1r'l'i.".J
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; C) I)"soUUl(.it,. 11.irl
rrr:rl.r/:r.t,
rrr, rrl.r_rrrl
rI rr,r'ii;.i r.rtliuii irtrr rslul.c,riirr r,,t;riirnrti'rnicislrtt rr tl
dJ t)ctirulr rI.rrricrrtrili.rlin,r.1iuirrr,lu,ut,,,f".ui,,,i,ri
flr'l
ll .rrro'.1,'IrrII
r,i
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OfoSS (lllilli,
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ll)7'l) c,rrsl,ii,
irr i,rrrulin!,rr,
rl'Ir,,,irrI,r,ir,'t
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; ; ', ; ; i, , ; . '
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l rIl l
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i .\ (i,! ',r1l,,:]ril{
i ,i. iul
ril:rtulrriintr,o lurnintrc. ,t,
Uuiuairii,,r
[:].uL'rrr,'rliL,
1"'l r.r::lLi1,i
drl,lizbutrse si"r,
inghitii,lnrnoJrenex. ".,..f,i
l]ac:i, bol'*vil
, r rr1 ,:l
lI
) - :':'
rrr
. . , )r\:
.1;'l
l||,||
,:\'i']i
.i: t rn i:9lt'nu
mod itutolrru,l
. I)c IO: ,te rnUlLeori apr*sir bUCuf*r,i;Lll
,',rr . . rri,r,.rr,,r,',,,\l*irnl,[urnJ,tiC,I,SOCi
in:],1
a[rrzi:lmO1'o.eSi a lrri lrr(){.ir,.
r'rrr, r{"/.ra'rrr r','r:'rrr"lrinr',fior,riia e'ir.i pr+ceutrare(Dcrlv-si Lber,rrir.r.,,.
r:'r'.,; \r:1..1,)'iutltn{r
:l LUe.nt1,lc,1960: K'oind.lcr.,tgll; Ar.seni;i IJ.l,rz,
ltt0{)). P..tru rr,sr: prod*cc accaiti, apraxie, trebJie
si, exiite rlrrrrl,
,ll)l)!,,
r'lrrli
rul,! rr r,cgnrnenilterio]tii a, ariei preccntrale gi a iloua lezirrtrrr
|Ir)rrrt,lr lr) iurrlu.r)tcmrst,lrj sau in ernisfetaopusi, (Arscni,
1959. lg7g).
l;, ,\l)raKi' l.ru'chiul'i se.caracterizeazir,
prin dificulti,lile bolnavulrri
,
,.,.llc:t, rn pr1. do a q" r,irlicactin piur,tlc,, aj-loio*."n
'l{..r
si de a urirl
rl)) r,r,'\iu r:r,p'rr.
lic J5o(.iiul,i
unnori ii c,t iemnc dc lpraric a' rncmbr,lt,,r,.
lrlsl,,1rrsir,toarte g_rerde rlitelenliat dc nra\ia t""ncnii f"i
ryi Ae asincigi".
.\ p.rltr irL krziuni dc rlivcrse ulturi (_intlcosebitunori)
lr,iebrrpof"i-rii* j
lr u I l,,llt;ilk),prccum gi il bo.r,l:tlui pick (la nge 1930,
cita,t A"' X"oiriai,,ii
,
I l); ;
i.
(d{,n.risa
dc cersrrnannqi Schitdcr,t926, cit.,r,l.r
.. ,.: ltlJ|:tllrrr{|llui
/ )"s,e.
c,r
ctcrizcazir,
prin piuderr.* ini[,iariici ;i I ilrtl
q
l]1,l),ij,,,ll1l.r:
l11/
|l. t|l.r.ittt
t. A$1lel. in timpul
al.mcmbrelor
interioar"
fali Aeiol, cliiru,.
l;].,1
r,.r ,r,'.
r,,:l,.lll.rl.'tj'ir.,ra,or:r,iion)
rr ,,r's tr: rrfe p.rctroOtalc
popovir.iu
(Kleinrl_lfl,,
1977;
tr)ri; \t,,y{.r.pi ttrrrrunl 1900, citaii a" XrcinUier,'
fOi?;".
qi'Aggirlrr,
l r r 'r ,
I I r, t r I i | | i t r' (r,,ri , r l tr r r l Il l r i ,,l ;tl :r /l r r r l r ' l i p l i t o |l t. i \tr ':tl l 'i i ' Io ttl tr i ' l r l r tl r
,.rlir
r l ', r tl r tl r r i | r ';l o to r tl i zl tl l t r l r r l o zi tttti l l l r r t'tl tl ttl l tti t'l l l r tr ( i l tr l |r r l r 'l r t
, ', , , , l r t z t i l c l t,t'l 'o to i tr r r ttr l tttl l r r I I I t I t rt i t t I t,t rI ;i i tt Ittttto t i l 'r It'ttttl 'r r tr l tIr l r l r ')
i i ' . ' l r u r r ( l r i l ( l [l ) l r tr t, I1 ) l i :]) .
l l l - l l r rtr i :l
:tttttl zi t:i ( a tl ttttzi a vo e tl i i sl ttt:tvo l a l i a l tti l l r r ttse h r r r r ) r ';tl 'r
llrrittl';rrlttr
r,,
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'
ti. il,lltlt,xirl t.trlooltirLtri.;ic,i, lollllizltl,i
1xr ttttt;.ltii
'rr:r
'ii,
l{fruLOGIC
11.4.I)IA(iNOSTI0
lrr lrlruclir,ii,,:tplilxiile api:l,tde celc mil,i llullto tlti itr lt:'iurtr t'.tt(ttlttt'
, ,t ,, Lrl i i scit t , t uict t i r llm olisnelr t u, het nor r r , gii, Lct r ulor t r t Lr ') \ i it t . l. t r nt "tt l'
,,i ,r,r/r.srr r r r aiir t lilr t escinal't o. liit e( Uebr alclt r t sct t ilL ( lt t nl4lt r i ll hr int t t
, t't,1,), it\ I {d,Itrnat'i's
ne ar&nio-urebw,Ia l'1.,.
{ l rtl l
i l r' rt' l rl i t' l | | I I t | i III t i I ' Ii | | | | | | I I t I I I i I i l r'
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il)
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r,
:
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12.I.1, Prceiziri de {tr.meqi Qi alc Droblerxati*i. in:r,r.t,rrl
.rr,lril,rrlvorir abtirtla succilt problcrnctc de diienosfic doan itt std,ri.tet:attrr
lr.,a*r qi.in.alte su,spnd.d.I'i
de con$tienli, de scurtj, tlurati, ca dt, }illii
irr rrlurrifcstilrile silcepale.
I) irrruno51iu15salr cunriienti Se1nlolegcposibilifatca clea fi i.rl-r.rr.rt ,
rtrl :r,:r,v(.iri
siru a ltu crrrro;lirrliide cer&, de a sii in ruor] iust de obi(.,.i,,1,.
'-i lr.rr,r|lrr.nole
inconjurltoal.e 1dc rcalitatea inconjuldtbarcl. J pir.rrl,.
.rrr,rsl,ir4,ir,inseamnii it,nu Dti de sine (Dicfionarul lirnbii romf ne tnc,il"r,,,,,
r1,l'7).
il'rrlburdlile care survin in sfera cunoqtintei constau nu in rnoriijir,rlrr
rl,r rliloril,c gr':r,rL.,
cum.se.s1une, liinrl vorba-numai dcspre pr,czen{rrrrir,l
l r,rrrI rrI r,r.rrri rrI ri , r.r,l Lrr, l rrl l i rrri r.r.il t!l t t i r)l l Ll r. ((l l
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i'
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i tt,ItIt'tr ':t' tr r Io l r r i r r r r r r l r "r "r '
, i , , r : , , i , , , i ',i ;,';tr
i ttl r tr ttl i i ,r cl t'r 'r .r l r r tttr ttr tl r t tr r Ii 'l tl r .r
t
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.i
lo:r,nr! ( rrrI | )I | | | I LII I rrrI r ,i lulc t r ) , r u. or r tic , r lir r , lr r r l,
r l i i , , l l n r r i r r i r l r r c l r , l , i is r t l l l t , l l
,
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c lt , t lt r ir r , plr t r r t ll, r lr r r , iv lll; i r l o l t , t , s c r t c l ; o . ) .
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. .r
\ r . i t , . ) i ) r . l r r {r '*i i , t , r) i l , r r t
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; r t , ir r r r : |1, r r r i r r . I r i ; r : r r r r i I r : r . , _ r , \ . r , r . r , t .
i ';.,l ,l r
, rrttr: ttr' , ttttr' :t l tr' tl l r i ' l l ri l l r' \ l r' l l t l l r ) l l r l r l r ' 1. ;
l rrrtr,,t:i r ' r ' t , I r r'r r | ; I j
r' ' ,r' ,,;
:rl rrrrrl l ol
i '. :l tttrrl t,r
rl t |i 1t l )tt,l . ri , t,l r!:rr' r rr rrr l trrl rtrl i .l l l rrl l l l l
: i {tl
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Ilodlfic{}llo lulrr'llllot r''lt(lrth$ lrt flrt)orl (:r tlroilrl lozlunlk}r cer(llrirrkrr ltollrrosllo
tl llr{lic lll opclatorii
I n d i f u l i L t , l , l , L r, , rr
'IrrnpeIatU Ia
telot lull L,
ahicardie
bradi-
l 'l l l sul
S c i i dc rc a pr0l .trrrl 1i ,
Impollant?i
atunci
arteriald
c oul l
l rl
It0$pi l l 11i a
(iullos,tii4a
l1olenld
Tulbuleri greve in
deglutitie
l )fgl rLLi ti a
Inrportant
cnl nr
IIemillegie
Iipilepsie
Simptome de hernje
lemporali
-1
OCUm,IC.
4. Tulbur5ri neurologice,
12,L2.;i, Gradarea Si clasiJicurea comeilor
l ,l r zi ttttttl t'
r , ( 1 1 'v i r , t r ll r r t r ir ,r i |o tr ,j r r IIIII;r tr ;,.I rl r r l rrr ' , , r' r rl t r I i i i ItL , l ) l L r l ( l l l , i l 'i q l l l i i "
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o i l r r i tttr o tti l fi ctr t, fttu o ]'i i l t: vo g ( !l l t't'i vo l l l r xl ( 1 l IIl '
F,
J
rlttrttrltttttir'
r-:stc
abulit,
iii'y,t'i i it.tri,,tll,l rltrglrrfilici
,', ,,"'':rl,'i,i,,
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vt:slilittlit'til' t'rtIrti.lt'
r!
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r,olti tlo ,r,irir,r;,r,itiT
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,. ,l i i o dovi|lc ler it cor l. iugr ll, ira, globilor ocula'r 'i spr '( j ] ) r r lliil
1,,,.,l| lci} este lnedin-pontini.
l)il'l'i .i!l(!
rttqd,ul LII. Bolnalul este inconqtient, exist':i- gravo lnn'trll
I l it r lit zir r 'l'
, ,l f,o u" u"iur j'e, i ilr t ul f nf J"gr r iit i, . i, lor cabolil. t ir r r lr r t l
I
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i srt'tt
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i,i;ii',f;iiit#';i";'iiJA;ffi"'ili*-ffin;v;ryft, aop'i""u ttrrittrit'zr'l'
,lill;lll:
.,;lll,'il;li**lr;h";:;*;,tl*t';*'*rr*qLll;t'"
'lili;i.i"p#ffi;;il.
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rfi't't'.
ari
asistrtir
lost
b;A;"r,-'" ,
:l il
,L L nr r o o sorioasa
tlt
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i'ttttttrttl
iri i'rln'r'"'i'",
,,,;i;,,;,;;;i
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plt
lillizir r ' lt t i 'l'lt lt l; '
'li,,li,,il,',,,rr,:',,i
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i'ziilr
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lir ' lr t t r t it t ii',t |llr r r r r lr t t t lt l't t t t
lll ril,
1,,r' 1,rI,' I,r, 1I ir I |ir r , ii(
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t l{)
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siriqrro'r,,
l;iliilj;ii:l':i"1;".11'.lhl1!"flijll
ili.h$,J:;s,:i,;,.;:'.1.*,,','i.'
lj}*lim
r.,,,,.,..ii
picriv
;;i;;;ii;"li'i',:li;'i1i*it
i[in1til:,Hit*:
&trrcse-itnpunn'
Itrrrrol'i irrsii, ooirla doviuo
I
p'iir investigatii
riri?i
ii'li,;;:il,;lj:illi;;,:ll,;iilifl'"1cir'
.
r,r.r'r't,lrtirl
lrtitttii,it'tttrI'IIt,ttttritLit',
r,Lr
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(xrllll)., lll? l) $tlll ll'
I
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tii
ittt'ttltrrl'
tr,
tt
r,' ., ,,.it ..Ltr,,tti,It,tr''Llt
r.ii,llr rrrrrrlrr,',zrr.i(trrrrrI t i rtt ' It,ijiI tlrr trt,t.t ttttt
Hrrrll.irr
,,,,,; ,,,',ii,,iirrrrrrlrr':Ltrr.
tlivt'ts| tlrr[itriltrttrrttttrlrr
i( ltii,tirr:i,(itrsttttLitr'l
rL:r r rrztli,) sitnll{,0tltlti,olrtgilt,
(!
(,
(1.(,
.5r'lllt' (1tt'ittlttrttt'rrt';1it
.trt
t,Ltru(,i!l
liz.lr,l,i'
rti:i
r1',',,r.i coirrir,)lioato fi
'"'t"'irrrnoralir'!i
ctloln,prirLl'rrgl j i'ri lle unor tutnori ltt .r'ttltl{'irrl.tlrrttlii'
IlrPitli'r'1i rrtt
,,rr,r li'!rlr r oirient tlai;, prin mlt, staze cereLrrnlocu r-rvolLtfio
.
ttmr
intt
lt
bcmolagic
i,',' l,o1ontitl edemaio=s;i
'r'll;'
r"ijdentintna unei hemiplegii la un boln:rv colnftloJ (srr'llorl r'\t'lrrtir'
itr frrt,,:ttr';r'
r.rr,.,i ;nro tom5) reprezinti-in-generalun bot;,rilor atgutttr.ttl.
l(rr':r'trll
,, ] ,.,,'iident o aicuia" cercbrali TotuSi, in unelc sixufl'tii'irr ('rl'r'(r
I r i,rrr,r,l
vascular s-a constituit la ttistan!5,fa!5, de cd'jlonrultlii l)inrltI i(lrr|1'
r,,."'ifttcgiapoato lipsi, dar putem constaiaalliesemneneurologi.. l't(\21\lr(r!
jttsl'rrlitirr
l,rl,rit,tr,l-La unor- semno neurologice (indeosebi pirlq'1i{alg)'
I
t
mai multe posibiliti (i : ' ' tt trrt :t ;ii rr
.,' .,, :iLitent sau in tloi t,impi, suger-eazd,
procis
ocluziv bazilar, hcmatolrr (lr' 1r'tllrr'lrl
, u ri tt(latie vcutriculard',tl()
(ctt marc cdcm lii sau irl)grr"iitIt\
:,r.Ll.
cercbral
,, r,
h'".atom emisJeiic
l',1,,, ,,r|oral, cu c,rlrenareain suferinl1 ;i a enristmului optts)' l'r'r'z'tr{rr'
splo ('{rlrriil l{lrt:r
,rr',r lr,,mipl"giiinr"omplotela un paciont cate cvolu-cnzd.
ittlt't'
htrlttrt'lotrt
subdural,
:
hcmatom
expansiv
, ,, Licirineaunui Drbces
,,'
tumoale cirebraiS.(Lrseni qi colab., 1974 ; Yoicultstltt ryiNloit'rt''
',r,,),,1.
||r(;;
).
i'r':lcticaneurologicS,ne mai invali' ci, tol'deauna, i'aitrtt: tlrr rt'rt'littttrt'
rlr,r.l|,rsticljllde accid"entvascul:lr cerebral (hemor:agit,Fr,ltill,rt,t:isrrlttrttrir'),
. r, ',l,lit:l1o|irlrd,climini,m, prin cxatniniti tlr'nlo i'lirri(''r;i ||itlrr''lirri"':
l lrlrrrrlrr('
iti slll)ll'('lll)'
l raumaticecxlraduml $i subdulat (iL('uL
1,,,' trrrr, ilcle
r'l{ rl1uilrslitlitlcrrr;lirli li tttr'ltr{t"
,, ", t ,.,lo, r'rcningitclefi mcn illgoce{aUl
l Irr ,,'rnil, encr'[alopalir,hipertcnsivi si crrllLru( l)]l{'l'lr|ir'
tttltlt.tlrr ir|,lllliIt|,
hi.pcftensiniiosi,e]'ol:L1,iV
lti|r,grrt,s|iculde mcefaloptt,tie
rrtt It'tt1'tttItrt II ' tt|'rr
crt'z'
in
falil
urui
afl6,r
;
a)
n6
r, , ,r i. nl toarelor eleircnie
cstrnl'irrlii',lirr tir" tttt
i,,,,,,1,,r,si..e{fie cu hipertensiune a'terialii, a.sa-zisir'
lrrlr'lr,rrl
,t,ir.r:lrcfr.Se;Amaial6s,irrcadr"ulunuifeocromocitotrsil,llrr,rrlrlli
i
tttt'trttr,
rrl
ttlr'
i-1
lrLltorli(,
rll
,,,unla-rnoal,
unei
coarctalii
in cadrul
,,,','
, ,.lrrri,tsii'sau
al unui Satu'risrn),cu masir-r't r]1't! lr.ttsi.trlllir;i trtt ittt'rrl'
'lirodific[ri ale Il.O. (pini la maro edcrnprr,liLtt) 1. b) Ootttittttt t'rtl"
tr rli
tltr tttttllrr rtl'i ;rlttttt
cste de obicelitranzitorio I c) O'trta,trs1,t:
lrr.ofunr15,,
'r,,rr iiui
asotriit'1i :rll'tt rtrtttttrr
lr,,r,l
I il) Cefaleeaesteintensii; e) Se 1lr-tt'
"oo""i*ii
(uriu importantul etlem cerobra,l); f) J)c .bicci I rtttItrl rt,IrIIrIt I tIt'
,i,i r,,,,,.,"
'lrccetlatS,
ltt (trtrlrlltrtrittlrrttttil,
rle fenor*ene protlrottti.t
t, ,,,,l,,,ir"iaid,este
rrr'r,'r
rrnii, episoacle-deconfuzic qi obnubilare)'
de obic.i nu crccuzi, rI i I i r,rr| |,ii,t i rlirr,ifrr,
ilamoriaia subayahnoid,iand,
'r
, i, ,,. ,,,inilr"iiot *amiologicliind cel mai adcseare't'lil1,ot': s.rttttrrttt.ttitt*rrtrlrr
tu vii,rsl,t'ltri,rrrotliticili :r'Lr'lr''O (itrrlxrrlirttl'
cefalee inf,erLsit,
'rrrrr,tiri,ntc"
1
rnici tulbrrrlri d{! oonltiinli, (t || I II I| / |' ,,, I
irri,
n,'),
ret
,,1,
i f ,d^o.*gii
( '( '1, ,lt r ir r lr r r lllr '
;l;lj;i;:ii',lilji;i,iiiii,[i]""i:
'li'"il'l.ili'i;.T,J?f,$'Tl":l:iilill"lli
hipertcn;
i*i,i,
,,,,
1,.,
i1ui
fi i ffi ililrt":?H_?t,
11,,",'cu,iilr,
*"""iL:,t$1ii;i,*
b""'"r*ir"
il+ill#'i:'"('1,.11ff,,:,"';
llig':f *MJll]'l',:#i:::i"x
lli."*o*i6t)tiebuio
Iln'iltliii;i#,;,xxfti#fltii,"-1il,!:"xi.':',*':l"lfl
lilti,I1uiilj,l,j;t
'l-n:*:,#.1*:-.*lxkill#";*i**ir'llili''""1'f"'u*#;
rf#'?i
i]",*if
?ffili"L'i""{1i:iii3'Tli:fir;
l;;;;
iJ;ll,
;;;;;';';ruu;;"1;;
j1T*,'?#*1.,.fi
t,r,',il;1,5';
;x*5:i-i;"*+i"rJ::i$il.iffi*m;J"l't{l;
2. Oonxeled,in accid,entelaaasaalnre cerebra\e
jiti:ffi1"*']?:*:",*Iii*ilffi
;rllr:iitiHif#
'!1:':i,""#*ili
hemiplef#lJi/
J;''J:,?li":iflli"i:.,,1ff?;*lf,;j,tr
l::ltiti,l:.*!t:::,,_,.n"i
1i.:.,1'#1"i3;i,*",""'sf,f
ji tl ffi1""i"f;Tli
l
fifi
i
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lir:.,i:lt{*jijrlJ
i
irr v..rl.r.. cii,,,pari1,iD
unei corneh un.tind,r po^t"
porinifit"ioii
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"".1"0"
iti;;il,iitiitfil*Ji"v,lliih*11,1?"ilfiliiti*t"Ji
i""i:tt*il.i*,*"i#il
r,:liliiuis:t
r"w,,n*i,li,
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:iiiiiil',
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iT'lili;i,T.i,J,'i1f,.',",r1',Hi"d"
ifT,.fj,li1.:"iTi,T'1,#
l;llii,il,i"i,?#i*:l1l*,?gH'Hhffi1"j_".i"11"i;*ii.lr's;r"il;;;
lilcrrlrlltllii cotoJ.rralo
lrin me
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f
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unui hcrnalom posttraumitic etc..1.
imporLalrr
,'i
,,,,,r,lii,,itll,*;llili;,li,l'fil,)iLl"i'xlii
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in rr..u.s tru,itova u,,, uoir'ar"
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r l' (' t' lll(l_ r'll,/.llll,l,rt lttti
t : t t it r , l r t l t , l l l l o p t . o g t t r s i v l 'i , , i l r D r l r r r
iJ t 2
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r r i r ; 1 l l l i , r r r u l l l i t 1 . ,l l :
I t t t : t ttIL ittti'tt iI1)i ( t ( f olllilr lr ir ( r r r | lr r r ir i ir r J r .r r r i r t r t l i i , r l i r r l
si lt,zirttil.
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f-fi ti Z;
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;i
t'ttt.qitttxttt'utttt.ltt.tntiq[ ,ln,trc.henro.a,i.d,eerthrulii
.
;i in.ivctul urehro.t
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,,....
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jii, ; l i . , , .,i. , ' l ll]j , . ' j :l r.l i l 1 '.p ro ti u n dfii i.sm,vi_rr n:oi,irsi
i r i, ir np,.,r ;r n1,.
' rr, f : r r r Y r , ir liult \ ' p ) i .s l c rc !.(.l i 1 J fo 3 l ,u
i n d e osobi peutru bnmoragi r, nerc_
rrrcnr.innt.a.srrir.ii
.teconrrieni,r,'irr-"-.on,"
\upcliciatit,
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tt\
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lt
i ' rl rl l rl '
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i trr|l ri l l :r
l rl '
't ilirliri:i"?iac.lipo,lt"constituitunsenlnI)I(io{)(iotl.Jtilr.tl.ttrttttt''
,
(hemoragie,llernaton, tumollel',- . .
','r '. r'rr,rri:tilii,
(<ltrlrrt,tl'rrrt.'t'rrr lr.rrrr
umitafurAtiia TAill
,,, Srti,ilercairftnorlantrd,
c:llrl'irlii' rrrrrr:rl' i
artolii
cle
i, ,,"tiJi"i"iri'oo""' p""t"" o trombozii'
,,
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$i/ sr'u rtltfirr' IritIItrrrrI:tI
lr
(lr'ril
poitu-e-vc'1'ual-:ugut'L, Jrt'ttt.trtrirl'
',', i;';;;;;;'ititriulie*;el
I0{i7)'
Stoica'
"' , ;'ix-.*-*cmn inlelXtor frroiculcscu $i
in-pest"^?tt'l''llll
diagnostic.l
,i'lii,,oiirri-i?nii""q#a
':l'lli l'
sau microscopjci) r'r'sing' tttt i::r'rl: ' rr
r' |
' i'lcntieroa (macruscopicA
-io hernoragii' Da. lipslr'..atxrsl'o'ir rrrr I'l:r l"
.,',, f,,,- *""o"t i"d io f,,Cn
l':r 'rr
focar l:emoragic(Voiculcs"rr $l'i.ru' llrr;' ;
,. . tl"iff;;uu-i
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u
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l r{ .rrl ,r).
i i c i r r llr r llr r z ir ,ir r r rrrrrll tl r)t.l l s i \, (s o rrrru rL l rrl l irl, l sl rrl rl q l l i rti , rrl xri 1l rrri i j ,
p rctr r lr r . l, ir lr r . lr r r r l l o l rru c (o l l o s tl l l i l , rl ttl o t' i l t l trl ol rri tl l l o, ;ttror.uri i c,gl o{ ur,r,
r:r,r'I r r r I ri,r I ( ! r lit , l( : { f,i l ,l n ..l ,c l i ,z g ()l u o t(i N ,i l l i i i u l i l r' o,:r}ati 0, s0Irztr,i ,irti
ti r i .l r,,
l){)|
t |l
).
lirr rrIrt,i,oIr,r'rI
sirrl,tlili;clo r.r-lbrtrrlrlluigonctrll, p(. irrpli,t.l.Itc,
]lcurol(\lil
;,i rl. IrIIr'r,ii,lo}
r ' llsltcct tltshi,l|ltlut it t,t,tnrri-tLtui,
cu tegurn(x]i.lr\
.ii*r I.. I'(l(liIi ciurLotict:.1
- gl.bii ocul.L,ri
h.iytrtori la p:ll1:lrc - itratiilrrrr,,
(llJ Irl,irrriri),crr iuspiralie pr.'ihngiti, apoi pauz{ tt-upi,Ibare cxpii;l(,itr,
{,ilr) irrlurli) rilrrtlr,ii,rlr.o:r,ltir p:r,trzr'r
rn:],ilunE:t,(r,espirllic ascnri,niit,
o i l,
r'rr (r.rrr{l{r i,ip li.iissnnrrl);
,-- in haloni, se pcrCepclniroslrl de acetoni,;
lrilrolr'lrsiururl,t{ct il,lij,, l)uls slab si r.rWidl - hipotrrrnic,i _ nalcati; lri
'ostco-ien(Linoas[,
hipo- sau arefletiu
lrrrl.rri* rrL'srrrrlrr,r,i,;
I * nidriazii :
,
inu|rtir. d jrl'otir.irnu n)ici hemortqii h l'.O.; _ pt.nz,.lrl:i
'r.rr,'rlr:r',,1
,
,,lLrrrrzr.i
si rr,r.oll)il{rr(etnnici in urin5,1 - gliccrnia rnult cresenti,irezcr.r;rr,
rrr,lirrii
:r,lr
sciizutli.
t ) Ct)ntq tlre ricd Nste relativ usor de rccunoscut : _ antececlcnl,rr
rr|lloprrlicel - arproalc totd{ aun:t r.str. Irr.:cet1rr,1,ii
tlc Drotltoarne ca,r0
rrrrrlurrrrrrlrcezii
: oboseal5,cefalee, anorciie, glealri, v:.irs[turi, diarr:o,
(liril)rcr',n).iodozopsii
(,,,rnuqtez}uritoara,,), eclipsevi2uate (pini, la amlrr
r',,r...1,r'rrrrz,ltririi),
rnioclonii,,sitresiriri fnscicll:lre mlscuhre, ufteorl ortl
i rrlsiiI - l'rillonii,lu.c rriros a.mouitcll;
respirrr,{i:r,
r:s1,e
de in[lte ori rlr,
lrlr (rirr1'11s
Stokes; - bolnar-ul Ostc palirl, hilotelmic, cu pleoapol(l
r,rlrrrrr,l
iir,lc fi lrozinlii, sughit; - pulsul este f,,irtc binc bi,ttti Ourl
l.rr.irrrrrrr,rr,r,tclia,lil
este cr.cscut5, - cordul estc rnirii,, cu zgomote dlllr
.i lr lrlrriii.uli pcuicardiacci * la examenul nelrologic'sc cons1,atrX,
semlr{,
rrr.rrrrgitrlri,rniozir,.hiperr.eflexicosteo-ten(1inoasii,,
ilneori seinne pitatrri
,lrL, ii c x I rrlpi r:lrnidillc (inclusiv flapping tremorj ; - la exaucail F.().
,r, r.irirslrrl;iL:ncur.orci,irritilalbnminurici, cu nLorlificiri evidente vas(ilr
i;rr',',r.rrirr.srrrllll,rr
,,il stca,,',.cu cdern sau s,lazXpapilar[ cl hemoragii I
,. r,orrrirlii oliguri(i, :r,lbruninurio,azotemie ma,siv6,acicLozJ,
tl ) ('ort.tt,.ttotrnir:ti sc irst&lcazit trpta,ij I,r,un bolnav carc a prezentu,t,
, rr;r:rlrrii*rlrirl,ltc (pri1ra{ociiuni gas.iiro-intcsitinale
salr vi.r,situricentra,l.)
r,i , :i,r',,rnr t)it,r:i[1,11
rles]ridratat. Se,rllne1e
proclrornrlloSint asemxni,toitr\\
.rr r.r'1.riirr (,o riL ltr01)t.icil,
ca fi,tar.ediaglosticul difcrenlial va Ltrre scanlr,
lr, ( rl,:\ir r,lcirrcnl.ct.cr.olatoare:, bolnav tleshidratat; * TA scizLrtrl;
r,rrrlrirr,zii
i
:lzotemiei, a alcalozel qi a cloiopeniei.
l)l.ozon1:n
, ) il,ttttrr,tr:itr,ny|ioi este u,sol.de recunosou.t:- ilsoleqtc o toxicozi
'r'rrrrlrr':irlirr:r,rlorutimniil_rte:i,sa,rciniisan in crrsul nastariii _ prczirll,i,
| | r, ;rlii Ii 1r|,lli orlr!,lcI ovelatoare(r:elaiee,
v5rsi,tori, cdlme , ilbuilimrr ir,,
'r:r
lrlrr.ri,.rr.irrrrr',
oligillitr pin:"lla arulie) I -- coma debtteazf,'cu mioclonii,
lrrrr rr i rrIri rrI r.rriIII .,ir.,,.lsii l,onico,clonice(:rdescasubiriIante) qi chirrr;
r,rl rl.r rrr, Ior.:r
lo crrlclrrir,lo
(parcze,mftniiestiiri alazice etc.)"
(
itttrttt.
lu
ut
ridicir
|)
,
ltrrLirii
lroblemc cliagnosticedir,ci,_tiflomSca,rI|
rl. rr.rrrrri.rrr.Irr
.l.rrrcrri(::-- antooetlctrte
]ropatil-ro
thcp:i,titegr:il\'e1i{)xio{r
rrl rrr|r'r'irorlrc,r irtzc, nctiltlitsrrLliep:tlic), eltrnluil etilism cloniol
rrrrrilr.sliililrr,r rrltuttlt,ltrorta,r,r.r.rrlnlrcltinslcsjrll;r,tllrlrr,,N,l)atiorx,Ni(\ni(r
rrr:r.rrrlrt,suiilri(,yirsil,lri,nl{'i,'i,r,is
r.,,iirr;1i1,rr{i,.,s.rrrrr,,l,,rr(,r.i,progrosiViI,,
r'lrirrr:r'1.
r'orrlrrz'iorrirlo,
sl,iili rlrr rrqir'rrriir.
Illscicttlrrliisi sprr,srnc
rrllrsrirrrtrlr,
rrrr,,olrr',rrrvrlsiirl r lilr o;rilrr!lir,; ,\rpr.cl ,rrlI rrIIrrrrt,rrI rri r:liirrlrrlrr|rrl,ol,:
| 1r1, I 11111rI I I r' ri i. or r . irrrt.,lr'
i \l
:t It
l ,i .l ( t.t{ ,r,.
r.rr Ir' | :rr, l rr rl ri 1,.,i ,fl i i ri rl o l rr,rrrol .l rgi i
|.r,ioii(lii
(r, ir.xicllr,r(\
L 'I r I r i | | | l
t r ) ? :i |:I r l l .l i l r .,j 1 ,
r 1 ,, l r tr
i r i r I r, r ,r, I r , t rr; Li r r r tr l l r o r i
1 ,,.n l l u
r,li |ori
r l r i i , l cr I,r r r r ,:r . r { l , I l L l ,r r r .r r r r ,
Ir r r i o r 'r i r r r r l i , r .r l ,,l r Ir r r Itr r r r r r l l l
L l r l l r t t i L 'i
tl i '1 'l ( r i ,r r '
I'r ,',r
||r r ,L 'r ,
l l r ( i 'r ') r 'r r l .
1 r r l r r l . r l r ' fj ,l l .l .r r ,
' t : r . l r , r 'i r r l i . r i :r r Ii i r r l r r r r r r l r r .,r . r l r , I r l ,.l r :r ,t 1 r r 'l l i i r r r l r r r r l :r ,r ,r r l .r .:r ,l r .
r " r r '. r i L \ r i 'r r r I r 'r 'Ir i .i r i L r r :r r l . r r r ,', r l , l :r r r r i r r r l i l j r l si i ,r r i [r r r ]i i o ( r l ,:r r .r "
[ ) ( l t t t r r , L l i tt i ttl o tt,i .tr r l i r t r tr ,ttr l ,r i ,.i r l cb i L l .o i r ,zi i 1 n ]t,( l {j l r u i t1 rl ,,r r i r r l ,r .r r r l
t r l l r r r . i . i r l i g .r ;l i ve ( co l i r i r r Ir r I.r r r i r r r Ir ', vi i .si 1 .r .i , t1 i l n ,a c, c) ti l l . i t,l .r .r ,r r l r i r l ;.
\ 1 r r r 1 1 , 1 1 i 1 ,1
r :r':'i t,cr r r cu i i l ,i tl .
r ,i r l 'i r r zl i ,
i ,l l h i * L r i l i r :. si tt"o ( l r ) ._ r .i l r r ti i , r .i r
,1, lrr'. r.uur-rrl"riir sttre d0 r,oLll)s, (]orrir ail odcri.r pulmonar.,
\ i g r r u l o U \.
l U ;1 . 1 \l :r .i i n v,
Ig L i l ) .
i'l{r ltic c:i piertlerite d,euLno\\tin\d ile saurtti durafti sitri, rnlr,i r,l,,ri i/,
,.,rrt..::ri
tteurololliati,in _centrul acestot manifestlri situindu-se lr,.a.li.l,rr,1,r
l, 1rlirr.,rlil. pot./i intilnite
foarte fr.or:ent $i in diyersa]'<r
tu,lbu.rii,itl. t,ri4t tt,
, ,t:it urd, cu crxplesioneurriloglticii,ca de pikli)
sincoTteled.edivlr,str rrrrI r r i r.r
.ll
i,lisilri, carc iusE trsbnie tol,dcarua difererLliu,iirde
:
.fu,lselc tittr.t,1t,:
lrl'rlit.ii srL' sirnplc ,,leqinuri,,(Faii.re, J.9?2).-llrcbuic aco*irr,iii
,r
rr rlrrrl,art!:ir,
'r:rr.,,
,ti sincopelortagale cane,,nc conduc la o ncurologio 1rlr.itllir,.r
ct sau f[.r5, reflexe rascrltio r-aso-vagfl,Je
l,rrllicrrlari".l,
snu vagir vrr,11:u1,,,
, i rrlii.lurminologia arrglo-saxoni.,c*rc fac tlil ilcest secior hibir.rl, rrrr,ii.rr'i
,1, rr ii1,rcin1rr.cardiologic.lincurologicr'(Faivre, 19?2).Asl,icl,rlrrr.iilrl,r
, rl,i" (1,.I'il,r.si nce fibr'ulor.telntirrrlu llo rugulrri (iu lr:u|trrl rlig,.;,trr
. i rl ()r'ii-til,r.inge
Jcsplc rcJi.ru aayt,uagu,l.c
, rle pildi) sc r.olbpDbe
( llatlli.ts ) ,
r 'l:rr-i ri llr _rrrldr.cl&nfrlul dr, sinropc pl,.r"i tlin \isu, c:r {l,i
IiLl:i rlirr
' li',lll4 iru d||r tltc ad'.ro, cSfe to|lr:r tlv rrJllls DaSo.tdqnlr.
lrr 1,,:rr,,
.r' i'ii1. (razul'icstc I-orba de intcrIcn!,ia ulot tcflexc ri:[l{o_{].1,r{r1.1{,:t,t.r,i'/
rrr rl. clcctc cardio-inhibitorii. ln accstc c{r,zul,i,
corclxl rilsprrrrrl. lrr,lrilrr,r'
r rr.rri.Iio lio prin tulblriili silro z],[ricu]iare,fic jolcriotialtr (1r.irr
{,r.rrrrl,rrl
J"r( (ior)ul atlio-vcutliculrr). Iiielderile dc crrnogtinf,ir,
vagal(J),1(! irrlr',r,lrr,,
,rrlto pt1ohrgie dc grani(ii nouro-ca,rd
io,vnscu1."lr5)'(.Ir,ilivrr),It)i:jl.
I r slir'5ii. sc insistii in Lrltitrriifttri asupll i4o-rruntit(\lor
,,sincopirrrrir I,r,,,
r | )rrlr,l li grial:., 1954),ttro poi I't colscr,ittlrlr,
rrnr,iitrull or rr,fco{iLtrri
sjrl rrll,;r,
rrr
r,.rl l (,
nr ur ologir : il,
| ' i | |I (| rII'{' I t,rI rr cu r r nl, irr (lr lol: r l: i li r uI r r r 1I lr i: 'iir trp t i<, 11,
r lisol t t ( , il lr lr r Lr r , lr \ : r ,
rtr(ti 1tsi l ri .. ( lii: ilr , r r {r r ,ir r r , r r r , . , r r ') ,: r , r ir , ( ii r lr r r . r , lr r , ( , ir
( lrr r r t r , ( ii sr r r r z't . ir r
trtrrl .ti i ) 1i 11,f ir , ( r i r r r ; ir , l: r iir r . ir ': r r r ii,
,
lr
r
r
r
.
i; r l) .lr r r r . ||r r l, I i r ii
1r r r I r r r . r r : I I . r . ir r
l rrl rl l rl r.ol r r lr , r r r : r i nlr ll r , r r r r r r r pr r {r r r r . or r r lr lrlr . : r |, r , r , r 1r lir r r ( r r i,r . r r r lr ,
;It0
:t:f I
I)ia(ln,o,iott'/"d,lfot0,ttl,Jdl
ln lrrrlrrl 1rrNi1,
tr olirrrirro ttllt rnrr.
ni.ltttl,ll.t'i
n t u,ro-psi.h
i.u,l.riat,,
flirt n r. nl nt tlt' ttturrl, r pilrlttitil, li uti 0 u, tnt,porlll
0 1,(tikr,l)il.drlittol.u,l,i(
tr ntuylir'nlr'i:
l. Oritcl( ),mearopal,iorrt)
..n) (lriut ntnLnld.Soplodu outrr cir.(illlrrfl1,rr
l l(\
rprrcitlo,si ou trn,,sor)l) rr1,ililtr,r")(Alrrorrld,
1972; J?opoviciurli colrllr.,
ll)713),obsol'vindu-soirr rnrrtlicirlr,,,rIIr,r.rIrl'III)i,'t,
qcolarr'!,
sau socia,l)t(oxl)ol.
l,izr'i).Sirnularca,esto grosolruril,rlrl rrra,iadeseavizibil ,,volunta,ri,tt,lir,l'i,
lrtlltnt'ii,rivasomotorii (in slxtcia,lla fa!ir,), firi rnitlriazi, Id,rI tulbrrr'fiti
Ilill()toliene, fLrX somns piramitl:r,loeta. b) Cripelepitiatice pot rca,lizl,fi(!
lrsorrdo-comeletargice, dar cu absenla tulburXrilor nourovogetnl,ivu, r'rr
, cosdo tezistenfi ia tentativele de ,,trezire, t $i cu ,,impresiott dc vigilol rl il ,
'r
lir! crize pseutlo-convulsiyo,dar care nu comportd, nici citlole br,rrlllfi,
rrici apnee, nici clonii, nici stortor, nici hebetudine postoiticl.
So nlr,i
lo,
lrrrte nota ur tremor palpebral qi circumstante emolionale docla,nqa,rr
r\ Criza afeatiad,banald,,.omare a unui $oc emotiv, poate comporlrL llltol{r
pot preto la erori tliagnostice : stupoare, hebetuclino, il,gi1rlio
'.lolnente care
psihomotorie dezordonatS, rlar totul clerulindu-se pe un registru do torr,rnil,
rji {1o anxietate.
2. Criaele m,atebol,ice:a) Criaele kigtogl,icenicese manifost?t do obicrl
rlupi un efort, la un inttlrval mai lung clupX,alimentalie $i sint pr.o(1(xllrl,(l
rhr tlanspiralii $i ale o sonzatie de foame bruscd qi violentd,, Dsrulilroil lrl
porlte fi similard cu cea a crizelor epileptice, chiar cu prezenla do furrr|lrrr
1riltrrridale. Efectuarea unoi glicemii trangeazd diagnosticul. b) Oritt'lrt
xpnsmofilice, Experienia ciinicS a diverqilor autori (Arnoulal, J.0?2) rii l
ruiu,strS,
din ultimii ani (tr'Xg5ri,gangi colab., 1971 ; Popoviciu qi r:olirlr.,
ltJ70, 1.972, 19?8) aratd, cH,acests erize spasmofilice $int alostul (lo I'l,r
vrt il,rbile crize ,,tetanice" prin tulburare primiiivi, a rnctabolisrrrrrlrri
.rrlcic. De multe ori este vorba cle crize de agitaiie anxioasd, cu pal;ril,rr,l,ii,
rrr irnpresia de ,,moarte iminentE tt, cu tendinie lipotimico llsol,il,rr rlo
rrr,nzalii de rd,cile gi clo furnicituri, dured $i amorleli in oxtrornit,i,fi rii
l;r rrivelul buzelor, precum $i de contracturt in membre. Amintirlr oil, nrrrrlrr
{ r'izo spasrnolilice pot imbri,ca aspecte ale crize pitiatico, iar alt,olo pol,
lrrru:r,specteclinico aproape tipice de ,,absenfett,sau chiar do qnvrrlsii
lonico sau tonico-clonice epileptice. I)oar prezenla spasmului clt.rlll
1,,rrlu,linainte, in timpul criZei iau postcritid precrirr, ryi aspocl,{rlo.ltiri( I
(rk'scd,rci,rilc d.e unde lento asculite hipersincrone gi/ sau clo undo lorrl,rr
rrirrrrsoidale
induse cle hiperpnee; absenla modificd,rilor do tilr opilolrl,io
lrr, st;imularea foto-carclidzolicS, qi la activS,rile cu Mdgimido) 'puf t,r,it,,irr'
rlirgnosticul in fa,r'oarea spasmofilioi, oventual diagnosticul do slxr,rrrurfilirr
:rvrcilr,t5.c-u epilepsie (I'A,gArE
$an $i colab., 1971 ; Popoviciu fi c(,lub.,
l r)?0,1972, 1978),
.12.1.3.2.2.Iotusurile de saurtd, duratd, Al[,turi do ictusul apolloot,io,
,r,lr r{,r'ui rnanifcstd,ri pot 1iiile lungi tluratf,,, so pot obsorva la unii vtscu,
lrriJ i{}lilr$uri$curto, atkrsoartpotatc, caro survin do multo ofi cu oqlzill
rrrroiilohinrbii,rirlo pozi{io in spaliu, dor unoori chiar Iu ropaus (Arrroull,
lll72 i.llopovicirr ryi.I.)ascrr,
1{)71}).
So paro citrln &ooctocinzuriogl,ovot'lu do
o l,nlbuto,to d0 iriga,llg oorobmlfi,, produ*Itr prin hiloto:nsiurri t,ol tivo, rot{"
rrlr.obrtloty[nzito]'ii Ii/ snrrint;olrniln)r]1r(l
;xrrl,ivpt'in it tufioianl,ouilrIrrIrr,|rolii
(rIr,1,1
rlo l,rorrrlxrzolx!rlir o l)r! slnl,orrrrr'l
oaroti(li0,n).lfupil, n<ttrtllio
t.l,rr,rrrrri
irrltonlln(l(ort (lltrr!1, (lo ollr!\,1,noctrtrdo1rlrr11,
ln oil,ovn rrrlrrll,rr)rll,lnltr
irrttji,tlr' olrirltrittrtclr.rrtir,ilit.rturrttIrtIt.rrIrrI"icr,:
lll1riu.r,,
1r1q:1r51,1,7i1,
J,iu.(,/.(,
rlr:rrrrrrlrr
l,rtllrtrr:ifiltfllzi(Nl{)1,o
, 1 1 r r i r l r l l L r l , , I r i | ,r , r r , r r I r|
,
r t t i l r t l o I I r I i rL Ir ( r cr r l r tr r r i .
I ll,( ] .
llo li
lr , ) lr , l, , r ' o r ii : r l i l l i o s c l c r r r z t i
; lr) irontltor,;i.
I'!l
, r r l r r l :r t( . r 'l l r l l ,r 't i r :r tt i l o r r r l r ,r
i r r l i r r l t rl l i : r i l 1rrr 1i : r Iti 1 r ,,ri r .tr l i t:r ;
tL l i r o t i tr r tl l r {l r ; l l ,i l ,.r ,l l r l i r r r r
(u ri t rl t r r r lr oir ir : r , ir r ll rr,| r).,\r.r,| i o rti rrrl rl ,,rr(' t:r, rl rroi .i cl | }i frrl r.fi ,rl rrti rrrIl o
rrrri o l rr r lr r ,lr ollr . r ilir ' 1 ir' 1 ri Ir,IrIi l Ii ,l )l i l (i l ti .i l l l l l o l l r.rrr.l i i ,r,l r,;i
Jrl i rr(,t)l l (,\l l l
l t rr 1r1rrrrr:r1rr. rl i t r r til i i IrrrttI]o Ittr,.
l . |ir t t l) t lt : , , , , ' U ..,u ,t,'
l .i.. , 1 r' rr.irz
r i i , ((i i l i l r.rLl i .rrrrl z,l l ti ti ) i .i , l rrr.1,.1q1,;
;L rr.rr1 r r r I rr,l.r ' . r ' ir J irri i rl u l l i rIi
o s l o a k i rl )1 { ))i i rnr}li v I l l o si rrrrrpo, rl ..rr
rrIi . * Irr I is I i. i r l, llii (i i l ,l r l )r' o (]{ rJ rti
(l o l 0 % d o a,l :or(,i l ,' rir.' u' rl i o-vi ,scrrl rr,rrr
I rL l r' l i lt r . r ' iqir r . r r s i ttl u rp .l 0 r' , l l o c i r, i ri i u U l s i ]tcopol ol , (i i u,di i l fi l osl ,(, l .l ,
rl .rrrrrr ' r r i' r ' lr r ii, I iir rrl r,r' b l r, { l o o fi rl l )n } l ,r' o h em-' di nami oi i cl e grrvi l rr,r.
l i o -' p ,rrz i r c n l rl i L c ri r,r
.i rl r.rrlii r r r . ilrliili rr,)_
,^ ' i n rl cl 1i crnscci nt i .' i rn.r Ii :rIrr,
,r ,Ir'i .r' . r , i' r ' r r I I r , I r I.|i: i r;b ) l i c o ttrl b rr| ru o d e ri trn , uttri l rtcl rl rl l a, trn gl l rl rl r,
i rr, Ii .rr' iI r r I r r . lr r lili' il, I r) fi e ri s i mp l i l l r' i b r' .;ir:c :l cl cbi trdni , c:r,ro
D { ),rl t,
r1( rn r)r r t r ' r r r r r i r nr rl l o l ro c :1 rri s r' n cr'
. ro g rn s N i cr l l rccstol si ncopc { r:l ,ri l i rr.r,
l rl r, Io I r I r , r r , r r r r glt
r I r r' , o x i s ti n tl l i s c ti l rrL rtr' !;isrLl
i
ti te.
r," linrttlrtIa. rl.in t:u.rsuI r:tt tliopltiilor
rr) lrr .r./aro:c {{0rli&i sinoop:t :u.q ciu'itotoro prtognoixoDice: sullirrrr
L II(| ( i || iI r ir ir r or r i. s [ l i tf0 r' 1 ,u ri l o r,e s 1 ;cto l a l l i i , i l u r etl td 1:Z mi n te si l i l sr,rtr.
,,'..r'rrl
,.1,ilt1rlifrrr.rnr',rle\i prczerrl:r, a,oestiola,nu elimini iiilglroi t,irrrrl
(t;rl ',r'rr.iil,
t , r ' ir1r 1 lllil) .
(i rl t1 :l\.a i ' d i n , p t' e c rrtn
]Jammarst0n l C i tal i rt,,
(lrll',{'rl{r'''lz, l9?ti) N,ur.r'llta,l, e:isloD{a rlrror Di
tulJ:urH,ri premoniiorii, r.rr,r.,,
l',.r'rrrii.lrr.rlrlr,r'rrlui sit-fi , rprcgiitea$o['r {10 multe ori iXclerea: clisltrrr,rr
Ir orilr,sir ii, plo,siruro i,olr-ucicil,senzir,fie hitllJir, tle ,,glmbe de vat5,,, ovr.rr
lrrrrl o. r r.r'il,l,lrilr"r.
itizii, r1e
lngor'. St. r(lttitr,.il ,, pibuqire {r, T.A., ptils f ili
l,,r'rr. (,11.'s('il,irn pci,r.tptibil). a,sur.zi'eil zgomotelor cardiace, arleiea s.llrr
.1,_,1i,rI i rrri rrrrr,t r'r, s Ln {ii\lriu ilia ttil{hri sistolic. Dupi, Trendgre (cilrrl,
,r, {:i r,,' ,
,1
r r l. r ' r r r t r . lir;? t. s i rr..u l ):ltl " o fo i , -rrl r i rru i o :b% di n" sl enozr,t,.
: ,r.i ir r', r'rr r.is. dc t.o:lr|c subil.i si r.r, p.oEnostic ulter.iur reZervat (mour,l,r
rrr rrrr,r lil ir r r lr r r r r ls d o :' -4
a n i d u p i t p l i m a si ncop;).
lt) Itt, ttti.tot"tttr.l le,u trotnboz& u,u,riculo,rd,(afec{iune rari,), tuiburilr ill
r. 1r'rrlrr. r,cl rrl,i rilr'sou,r,u ocazii:l schitnlllililor de pozi!:ie : crti, digpnoi(,il,
, rri r)zi l , ( lr llt llli s i c t.c rr{ ,u a ls i n t:o p i r,.
, ) lrr h i1t.r'tlerLs
iunea 7tulm,onari1,,pierderiie de cuno;tinli
sinl 1rulil
I cl rr.rlr ( ( lilgc r r lit r .rrl ,z ,1 .9 7 2 ), Ii i n d l l l o re rl a te- de cl i spl cc qi consti i ,,i i ,,
l,,r:,r, r (1,irrii,lrr,, ll*ntrri, d u.e'e llrrginrrir,sril.ln cadr-ul hip'ertensiurr ilrrr.
l rrrl rrl rrr:rr . , rrrr.lot. spcci:ll-i) o',rr1u, hipcltcrrsiunea puhnondrX primil,ivir,
rrr .rr|r' I ir r r ur I r r r I us in t m a i tl c rv e l tc . l i r s rh i n rl r , hi pcrtensi uni l e -securrtl ,u,,,
rr.r'r,| || ! I ir ) I ) iI I ii dr lri u d i te s rn l c o n g c n i trl l . &r d t si ncol c tl oar i n 2/o rl i rr
, i l l r i r fiir l, ir S r , . 1) l ' .. , i u l rl c G i l l n .n l u a n l z , l C 72).rl\. ltt i tt*rtlioientu. coronq,ri(Lr1.d,
t)ot Bit so producii si,ii,ri sincopalc, rlrr,r.
1 rr i ' l a rc fl rl trti o c a rd i c ,p o a,tc sul reni , i n faza a,rtrrl ,i 1,
l rrrrr rrllr r r r r r i, ; t , t r is r n ..
lr ltrrtrt rlr Ilrrr.,vgrrl;ro sinCgpli, :ltlCSea,mOltit]ri" lllt,I, Aoeeaisil,radu1r,,r,ri
,l rrrr':i r ; ir r . olr r l: ' i,1x [ 1 l ,tll i i 1 r| o rl u s i i ,d e c l l rtz e d i l 0]' i i i e: 1,ul btrr.nL,e
dc l i l ,rrr,
r',.l l r,r r : r t ir r lr s r r r r r . rl u 1 rs . l i 0 c u n o i l q to , tb p i l d ri , gt,i tvi t,at,ci t,1,ul l tut.i i ,r,i l ,ri
(1 ,' Ii l n r ( lir ) ir r I t t r r l, i rL s l c l i l l
i n b l o c ru i l o ll t,r' i o-venl ;I,i (tr
l :Lfo. I)unrr.t]l t,
:| | r|| I I t I j i, i I I t t rt tI t t trt I 1t t I d cttlttrr',rit,t,ii
l{jftr)Z(ri I)olt1,ol)fovotjlI o sincol)it,ro1lcXil,.
Irr i rrri rrI i r. i rrrrI l r, r , oir l rl n .i l n ri ' t,r' r' o rti i ri l i c c rtrr,l rr i i r
,,l l ngoru I si trr,,ol ti tl r).l )l
||IiI I| | I r\| |t III ! lr it t l, r t t t t r ts t,trl o l tt,r' i tl trtrl r' l o ;rrrl ri l ,r' rl i rtIIr| rIi o1rItIi i IrIi st' l l {rrrri | r,.
ll" |;i tt,ln'lt tlil turlt"ttl l,tt,lhuriitilrt rle ri.l,n utnlit,r:
r\ r r r c ilr r r r rr rrrri rrl l i rI r' rrI, rrrrn rrJ rl l i r.r' rrl rr l r l oi :rl l i rr r l rrIl i rrrrI:r,r,
l rrrrr,l ri
L tttttIr'It ' t I Ir r r r t r lt r t t tArl
t l l tttrtl { l o l i trs . I' t i tr r.rl i trrl r' rr' ,rrr'Iroi IIr' rrrrrrIti rIo
l rrr' { ,l rIi
,l l ri
l l tttti ttol rtgi c;,r t r , it t r l , 'r iir , r lr l, r , 1, ii l, i rLl l , rr) rr l i r l l : t ilr t t lr r r lilr r r ( ( lilt 1r 't r
J,r' ;rI l z, l l tt:l ).
lit t sit t r lr ot r rt l \ r lr r r r r ; 1i, r l\ 'r r I ( r l) l( r zir r lii ; l, l'11, ( lilr l( ) lr r lr r l
I' i i tttrtt1rt'It1|
( lr r t I r r r ir
, rrzttti l ot sl rtrl ilLlo r lo \ \ r t r r r '( ll( ; ll
, r i t ) r : , ili, {lill st r t lir {, iiit , lt t i
(
l(
j
ilr
'
lr
r
'it
jr it li I t L
lt
li's
llt t i, t llili
(l 1l ;l J). ,r\l )rtr tlc ol) i( 'i'i r lr llr r r \ r r 'r l: r r lr l l0
:rrrl ccctl cri to c{. ! Tdit t f t )f i : lI I I r,rt rrLI ( ,|| | (i . illli, llt or r lcliuic r lt ljr t , zli it t I t t t t r '{t r '
l iliilile r t 'pcr cr lt r ir t r Lii: r st t l't : t
rl rf 1,i pu1tl e asislolie, 1r r I rt t t t t r ii r lr r p r tr '1, iciraa
, ir r,Lrl:r,!iciocrobralo. lJll{rii s1.ol)ul cludiac tluieazi ci{ cr;ll stttttLtltrr ltprtttr
,lorrr o st&te dc slil,biciuno, itLso!it,il,do pftlo:lrc) alneloli, ;ri tLlllrrrlili, tlr'
rrrrlcre. :\sislolia r1e pesle .10 secnnde produce piet tlcr'cll c1n1(rltiltl('i,.(1ll
, irr,rtozir,turgescenla i'enelor jugulale, Ii"rirea qi suler{icjllizir r' rt, r'l'slrirrl
l i(fi (pin:l li. npneir) 1i convulsil tonico-olonice (tr1-a1'ne,11)0i I ( 'olIrt't itt ,
rl ri l i ).
dc lii,m, ''je descritl:
ln cadrul 1tll-rlriu'ilol
1) I'ulbtu i'rile (le co duc(re, ca'ie sini celc rrrtli Jritrc cunoscttttr trtttzr'
rI0 sincopelor :
(rLlar. De obicei, pic,rdelea ile cuirorllilt{ii t'rlt'
Blocltl etri.o-t)etLtri
^)
qi imprevizibilir,. '\Itrll, rlrai r:ll oa estc dccl:rn;atir, in-tirtLltttl tttrrrr
'rlNrtrtllnir,
'
\'
Sc-;tie cir, daci' blr.tcttl '\
,,iirrt, ca, Oe pilrti, mictiune:t slrn defccalia.
t ir lir : r
,,,rrrfl et se i tiagnost ichcazf r r . ur ' ( ii3. j; ; ) , l, loculile
- pr t r r isI ir r t r
(le L L1lrof
\
't'in1ii'diu blt.rctrriltr'\
l,rrbleme di{icile t1e diagnostic. PiFrllt'rcir,
/t
( ) lloo' 1. &t iit *, ' tti . s (' r' ' .,r' l r.ri ' i /,' rz i r,
rr.i , rLI I r.|' | |rr,r) (l r, r:r l rr,.l rt,5il l ' l trn,v,
rt, l trr , i : r lilr r r ii r'r rrr I rIr' I r. 1 ' r' i rr rrl rl i l rrl i ,,i ,tu .i l l l i rl i l
'
.
;,i ,, rrrr,.i l ri :r,,l i cl rrrl l i
i rr, l i t tttr t,i l ttt l tt,
"\tl r'tt t { \ P t l t lt ! t t i i l )N ltl ttl i \' . ,{ r.r,s i 0 1 r!t,r .t,i l rr.trl ,:t,lrl
rrl l rr,l 1r ' l lr ' r r.l r r . ll- rri rr.r[a ' i rr. t' rrr.rl L i rr{ i r,,c i t'.
l ri rri r,i rr apr:l i r, rrr,rrr* tri r,tl rr
,.i |,IrI , I ( ' I I I I I I ) I r I r cL'lt)rc trrrs i s l ,o l j c(p l i rr p 1 r,r,1 1 r)i rr,),sl i i r.rsr.:ri
p1i
t 1 tl i i i rruft,ni l
l r'ri r;r c rlr ir r ' lt r lr . . r .:r i rt s l rrr0 t rl l r I i 1, ,.
!, !l\tr,l,lnu
ii,rilp de ?raitabili,t lt'.. I,rjrrilc ltcslclr, trit,rrl,ioniun fiiblill,!ln
trtrl l i rr r lllli, r lr c iu e i c o rrs c c l i u !ri i trrc rl i l tl estu ol ri l el t,' c i t,cul tl ;ori o.
i )o
, I,, ,l,,lrrr'r|lr,\'1'
i',,1,il,
iceI)ol..rii
pot.silsu
seinsot,ensci,
rrl,,o{o0,s.i
rt9t,i,,"ac"i
dr'1rir.r'dr.ri
,t,,c.*;,rliir,iii,
rh:
urro;rirr[.11,
:1.',i]1.
' l' rro
l]
'l :]:]
l1]l.il
i]:l :,iil,,lru.it,^
,i I r'iu'r'
.\rrr)l)('r(!
i\rr!)r)cirt
sl
srrti
.i,l'r' irrr ltitl
c r'rl lr. SUp"A
rrhicrrr'<iiilo
supra-ventriculili'e
I onlr,ir.u]rr|e
(J3oriver"b,
. FittLlirt,,
Firruiu,,
lllotrvCrcl
h ibr il r{i.,a,r:ri.ulll.ri lllr,xistitiL I irr ulltirna va.ictu,1e,'sincopapbato
surl
lr, ,slir;itLrl,rtrustrlui,,pr.iripa,Llzir,
auriculari, post_tifirifdliej.SiiiL,
'r'ri
rrr/ , r'rLr lr(.llcUl()rNc,
i;r stlLirnb,tahicardiile
ile vontriculalc,
prin riscurllo
vontricula'c,prin
l o l rl r los olt il, o,
rri, -l
ru)
lr pr:r'turbiililc
_10 setunde,tulllu.
hcrnodinarrrice
l)u liulDtl rlo llclnodin&nice
cu druati,
cu
tlurati, de
Ae bl-iO
llrlil r, .i'.rr
cirrrrrl.1,t',iit
lll,tx,iit trn
tr. osle
osle de
de obicei
obicci losinll;jtii
.tsinriitii de
tle bolnav,
hotnav, perioaciafiirrd
ptlrr st,ttrtit.
( f ala. rr;ag5,
d;
sl rrrl,ir,.(iol
tul i- holt
holnsrar-nl
, r . ' r r l resim
r es inr tbe
o o
n stare
.r1e
t^
UeJtnrr-ult,
,,rb,u,,-sau
- x . 1 r - ^ - , . o efemot{r
s"rr,zrr,(it^
rle
i.tv'ior", cr_i,re-i
pemrit evitare"acXa6i.iiin cazul in cftr,(l
",,vitl
,lr)l,|1rrcrL
Lcnlodiritnli(.i lI liude Si se prciungeaSCH.
-seeunde,
b)
pcllutbirile
Lr.
hernodinamice ae 1O-ZO
manitestlrilo
. ,
;,r|lI
O pal oAr,. b.ruiati a fetei, VOrtil.
,lrrirt ltrlr.lrsr.,l,ulnurut [|r'Czerrlind
t.r'i.opr rfc .r \ oJlJirii $i I acr iv iln lji mo tori i, d u pir cari: inai viOtji
I'r r\ r11.ir,irsr.rr
rijr ttrlli ilol,rv ttatc:t.
corstituic
,rstarende rdu
r: 9*p-"9!!oto^nq,r1rm?Fsauprccectate
uneorido ctonii girrr"ruririii",
lpl
(CorIariu,
| 97.1.;
gi
.i
.llt tclritrrlr,irr LitrrIrrllirrcolroisirrrlrlosrrr,rtlrrgrrrrdolont(!, I) iIiI I i II |,I(I
(l(!iIlul.i'i,
tiiiBiIl(,r"r,IIir,
xrrlr|lr,r
(1lt
ol1,lr,l,rr,
.l
sirrrtsoirllr,lli,,o Irr!ov(!l)1,i1,
il0 it.
r,/rr
((|rrfrU'i]t].ll)71.; (l(irlal'irlryi l,,1r,vic'irr,u)?tl Wt,brrr, lt)?J). lrr sirrrr,lrl
(lr)rn(lo lcrrto sirr1,
.rrrIrrlsiIr'i,lrrrlirut.ilo
rnai Jrirrgi6i siirl irrtrurrrpiorlo irn
Ilrr.l'r'irL
rrilrrrr{'irr
lIplo '1loo0rnplr.t,(,:rrl1.
c(u{.NI,uur[o
sl]lr,s]lllrllri
loiric. ,,t<rcsl,
lil.l {ir rlrrrclrz'ii'
rrilcla,sccundoqi cstc urrrr:r,tdc lcirlllr,r'i{irlrr}(|j'loli{'l11o,
.rr|. o Il,rrr rIlzii, lrr0grosir', pinii h rcculrc}a}t,llurrr-rir.iirri rronrrrrl,l\rsti
r1r'iii(rllt cx isl;i,ilrxrrna,liillDG.
(.lrr,sl,rr,rr1;
. (I950) . a . doscris sirtolpi], nrrcturnir,a hiperl.agotorjicilor Si
rr.r,r,r,iLirI.it,
ili lir|crr'(;ioriia,ocstciade- opile+sia rnodei;i,. Aiestr: sincolNr
\r,,o \ ir,gir,l(,
sirrl l:lyoriz:11,c
in oursul nopl.ii, de ridicarea in tirto,.talijin
I.rirlc rrrrvoiir,
rlo ir,.rLriru,la vagotorricii constitnlionali irL faza ch hipor,rr'ot,ulnr"l.Asocierca acestor diterili factori (staliunc l,ertic:Lli,
'rr,g.i.rrirr
rrr
lrili'l lr, ln srrbicci,prcalabil culcat $i cu tonus vascuiar r:eclus,afer,r,nlo
r irrrrrr':rJrr
ctrrl;r'ipcl,crJ)rovalen1,[nocturlX a reactiviti,lii vagald) oxpljcll
.'r'rr,vil:rlorr
il,cosl,olsirrcopeqi asociereafreclenti a nra,iifeBtSrilorcoiyul_
riVrr Iirlifi1, u.ol)lonM, tliagnosticului diferenlial cn epilepsia rnorfoici-r,,
'l'oIrr1i, lrr.ozon{,:r,
tloar a tnei contmclii tonic6 in opistAtoius (pl.cccdlr1,rj,
rrrr uIrIrt'i rkrlr r10 1*2 sccuso muscnlare gcnel;lizate, ilar'-Iiciorl:r,1ri,
irrrrolilii,rlo o 1'rr,z[c]onicii ritmicii propriu-zisi), precesiuneacidorii ;i rr,
dc c5,tle o stare de riiu gencral cu gre!.uri, paltiilr.o
;riclrlolii .orlLory1,inloi
,,i tr':r,rrslrir':r1irr
r!lrund,nli!, a-llscotIr
ncmoolorEEG de epilppsi;. 1,r.ecur,r
si
rxrinpro$iunc .a globilor oc[lftTi pozitivi,, etimind, Olignosticril
1rroIrII..rlo
rlrr rrpilrrpsiolnorleicd, qi obiectiveazi, hipeivagotodia (Gastaut,'i9I0).
l)orli.s-1,orczu-t tri sincop-ayaso-vagald, reprezint[ u ri,spnns teusio_
.
r.lrrIr'rriror
}r {).lt,l{r()sirne
psihici,,cercctiri ale rioastre(Corfariu $i l,opor.icirr,
l!r?.ll; ( iorInlitr, I97-8)au arltat c5,existir,o irnportanti participarti cardiol
rrrlriliil,oirnl
.(1i11.38), carc oste capabila prin ea ilsh,-;i sb, declanriezco
rrrr,rrio cottll'i,|,il"t.
l'onl,ru rlocllnqarea unei sincope, respeoi;iv pentru leprodueerea irt
.
lrIr()r'ltl,rt:..1,
nroocsllhlisinco_pal,se.utilizeazi, conprcsiunea oculari, compr\)_
rrirrrrur, rJilrusulr.ricr,roljidian qi rnanevra Valsalva f Corfariir. l9?t.
I lr78; ( lrrl'ariu Si Popoviciu:,19?1.;Gastaut, 1950; Gasta,ritqi cola,ti.,f ObOi
( lirrrlrr.ri,
1_956;
YercclJctto,
1960 j \ycber, 19 Z2)..Oompresiun{t;
6i ^(h,$1,lr,ut,
olrrlir,riitrr fu,rxr
tirnp de 10-15 secunrle,etecbuindu-seconcomitent o inrollirrl,nrlr ;xrligrtfici, (EEG, ECG, pneunfograrnd,,eventual $i pletismogra.
nrii,). l\,llrnovla, o$to pozitiyi dac}, aceasta antreneazl, nauli cardi;,rr?.i
rlrr 5.,I l:lu rnai nultI
_ririrea,. ftec\.enlei cardiace cu c6t pulilr 50o/o;
rrrrrrilcll;flri1r'o.siucopale (prc-ictale), sventual chiar o siircopn
1vb)i
lirzlrltoto poziti.l'e cI valoare
,
_diagnosticr,au ob{,iDut Gastaut (1950)
i1 (.il, 1,rnr'1,4i
colab. (19-lir6),
Vcrcellctto (19ti0), Corfariu (1971, 19?S) fi
l Irr'l'rrlil ;ri l'oqovicin (1971).r,s, uncle djn cazurilc noastre, pe lingi nlrrd(rrlrrobiqrlril,odo opriro cardiac5(la 4? 0/odin cazuri) am obsbr-vatgibloruri
rrrrrrrrr,lrirrkr ,,ltr lanltt, lil intervale iie 2-3 secunde.La cazurile obsorvtlo
lrri. ((lorj:)l'iu,-19?1, 1978; (,trrJariu qi Popoviciu, 19i.t) nu arn putul;
'l('
1'rrrrrrirr.rrvidonftr prin acuastL.probii riispunsuri ,,corrrphtetr itrU(i, <nr
lrl l.trri rlo.rrnilokl-nto scpu,r0.bi
rlr:1x.r'itr.r,tlLr
tk' tl, ]rrrlsjr.t,luutr.ici-r,,
il,Dil,
iflntt
I r'.rri[t(,i!lVorcollt:1,10
t)1,)(i ,,irrtiorri1rl0.lr,)t
.11{}60),ei rloir} r.its1rrrrrsrrri
(frrtlottt'i
rlo uttrlo.lontti,.lrillll,olllle,
sirrcrtrrr',siriruirJru.,ri,rllru'|,sirLrrsoirlrr,lii).
(l atl,iul't6iorlitb. (ll]5(i) ltu lu'i,tir,l.ii, r'rlrrtsiit ulxrl,r'rx,rrc.lrr,l.g'ri1r...Irp1r,
lirrt'I,onlo rltri,rrntritlr,lli,
rlc rlrrlrr,l,ll
:mliri1,ol,i
: rur llloc rrlrrrlillotirro.lliriirl
J30
ECG - f 81r'mtn.
1tY,:^\*.\
44-',4-/,-4"Nr"-.^-,v4,,'"--,\A^/,+"^
VA . C
t-
-+,,rt\
"q^rnvl-t"
rA^
\^!1414^,{12\4/*!1/4/"^4^%
PD .D
Yry.^"*{i&a'
"
}.@q..!,,\V/
aaa^^'\&{/'{a,,a
*'\'arv
iii
:l .i l
ECG
r-e@.-i!/t^"\*f
4@,t4-,\-1.4J
T.r'' 150/80
Jv+4
-^.-4r'4,.\"44.l'
urrr"^rrtr.l.r-^.Ap*.^^r.r^^.^i"
irig. 39. Inregistrare poligrafic! tn titnpul compresieisiDusuluicarotidiaD
dr:ept.le bolnavul L-'\., 47 de ani De mai multi ani prezinte rare c ze
(2-3 pe an) de picrdelc a cuDoqtiniei, declansate de tuse (de obicel),
dar ti de rls. Esie mare fumdtor $i are o brcnqilti cronicd. Proba (k:
compresiea globilor oculari a fost negativd. Se poate lemarca laptul ctr
la compresia siriusului carotidian drept apare o pronunlatd bradicnrdie (cu 16 bitii/min lali de valoarea initiall). Concohitent s a produs
o scidere a T.A. de ]a 150/80 la 85/40 mmHg, cu revenire la valorilc
initiale dupi 22 secuntle, L:r manevra Valsalva, scddrea tensional{
{usese si mai mare (ta 10 seculde dupi lnceperea acesieia), iar dupf
itrsu1314sn4nqvrei, s-a evidentiat o rcaclie hipertonic{, cu cre$tefl alc
'1.A. pini le 170/B0. Ileicsc o hiperscnsibilitatc a sinusului carotidian
dc Lip crrdioinhibi Lor$i t ensiodepresorfi o reactie hipertensiv{ exagcralI
(lup[ tcminarea manevrei Valsalvs (dupi Corfdair.l, i971' Corturiu
Fi I'opauiciLl,19'176i Popooiciu$i doldr., 1978).
I t'lr,ttrrull,icl'i,-
: l:l:l
'r''lr-/i-
1i-\^^^,}r&&@^/qq^-1*w
-/^\_-'^\/--\,--l_-\,^/\_
T.A E5/ 1A
tle
aentriLalia
este mai rareori intilniti,. Aparo indoo, .l1l...Nin!\1,?
..'.\r,r
tr! t,'rI|t,rInLrc ^lt,ipu
z0 -40 rle ani,.cu-tulburhri Iuncl,ionalegaitl,o_intcsl,i.: .r,/ ir,lr .i mlb-.r,.:,sculare. tractorii d6clanganfi sint'totcleadna de naturr"r,
:r.rrllr.rintl_osimptomalologiepreacceiualLmai lunga (3*l rni_
;,,,i,lri.ri,
|lrr,(.),,r'irr':tl'I.(:t'rza,l,i
prin^palfi1,a1ii,sl,arcde rd,u, transpiratii ieci, senzatii
rI|,,,,1)rrrIrr,
lclci, usctciuneagurii, incetogarca,
, cong0sl,l&
vederii, furni. ir.r.'r'rl| *'rr)rtotr in exlrmititi, prccum
!i respira(ii frecvcnte. Aecosrrl
rlo.lrirrrkl.o rucuno$tintei este de scurtd,duiath
iZO secl, in ti-prl U"oiii
lr,rl.rr;r'rrl
r..rrriirt'riscito cd,-vedc,
dar cd,nu poatc rlsprilrde.Acestemanir'.. :r.fr ..Illr, l,l.orlusoprrrr htpervenlilltia pulmonard (wayne, l96t).
-\*-\---_\-7---\
IT A $A/80 Plussla/min.
r r ,r ItIi n o tti t,tr t, tti tItt1 i r r tr r i r 'Itr 'i H l t,l l l ttl ,r !l i ( 'i .
:t:t:t
(' l rl { ' H c l ,l u if l: 'i . ior r lli,r r r r lol t r r r 1r olir r , r rirI r r lr r r llt r r r slr r r rlriu
, r . r r sl,Hir
r . i r lopr r ,plir r
i tcl ,i tLtrir,rllrlio ir rlrilr ilol ir .
PNEUMO COMPRESIUNE.4
SINUSULUI CARA|IqAN DREPf
.^\.-/2\
ECG
TA, 120/75
-l+\
JlqtuW
Pius51/min.
u a. - 4.
F D. - C. D.
l 5 A rV
^e,\^4^^ryu4,^^\/r/q.^^'/lJ,1lA/(\4r'^l-ar-t^^1^A/!^d^"a.-y1^
P D,- T,D.
^^.^4
Vu^,ve-
PS. - tS.
Ii0. lr, Inrcgistiare I)oli$afici tn timpul compresiei sinusului carolidiu drept lli bolnavul A. I., 3? de ani, alg. crizc sincopale orto_
statice. Boln4Yul prezinli erizc sincopdc tnatinale la trccerca din
ciino- ln ortostatism. TA. ln clinostatism era de 120/?0 nmHg'
irr in orl,ostatism de 90/60 nmHg. Comprcsia globilor oculari a
{ost negalivi. ln schiarb, (jomprtsi.rsinusuluicaroLidiandrept se
voalc ci produce o scidere a tmului caldiac cll 12 ]ritdtlmiDut, crr
o cliscretl scitlere a T.A. (de l^ 1201'15la 11/75)' Manevla Yalselva
a proalus o masivi scidero tctlsionali dc la 120/75 la 75145mmHg
1s71 ei -PopoDictu$i
((rupi alorlariu, tn t,
""Il:i"i:.qisP|apa'icilt'
lr
'i
ilI
L:.
tl t
,rttti l uItt.
V{l r f ( r i l l {I
i t t t t 'g i t l t t r r l t , s i t t o r r l tto l i tl i l t,ttl t : :tI|' tr ''I'Ir Ir r ' 1 r r 'r i r r r JItL i l r "..{.1 1 ) l l i l xl zi i ( l r r l
lrllill
l
{}i
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i
(
i
\l
i
r
l
l
i
l
i
l
l
r
',
r
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l
r
"tl
r
'
t r t l i , i r t r t t o t i t , r ,tvi Il t,l r , r tl ttr ,tttt'
: lllr lr '
'
rrti tl t' cj trrl so it |lclit l' I t lt \ r 'lr lit t ' l' r ': r ilr iz: r 't l'itsllllt
idic'tt'r' I'lrcilrrr.rt
si'tr'
tl' s ernn'ele obier:ltt;t'trlt lti1"rn llrLlirila!ii
' "urot
cal(11ido lrL
r
digitrli
pr
iir
crrirrplo'irnca
prttct
icii
se
,,i,n-"*rliiOiaoi
',,if"riil'
"unei
oN,r'(liruu'"
sr._utinic poljgr:lliu('1r,1.ri.
r,ii.li.iliei,
..i
itl i rl ri g1r1r.rt'lI
'rmi'iril.
respiniorii
r,irrsirirale.
Si cerebl'ale.Itroitaxea sino-ca'ro1
'""liiiii"
,, ,itl.o'ri
iolicita,rea ixdiyidrhi de a-1i llsiurna cllpul i]rlrl).i.
lrrir'r'('
lrl
dfirl)t
are
car
,', ,J.
-arilorsi comlr'csiuncacarotidci llimitiYe'
j ,,, "tt"ii*
;'
ldier i'rnrti nrlltl salr mai pulin colnplclj rI'li'tr'1tt''
fr-ria
('rr(losr
Lipott'tsiuno:l,
rc:i'c!ii
antlt'nellzi
r l|l'zt's-Rueft, 1953), care
.prin
ir'
rrrtz-iLli
* 1]rorlxci. Prohl itrvot.:] rlc hipcrtlnsiLureendosin-uzdi-t' lrrrtlr'
luiY:tl'ir'lt;'
p
pr'rba
irr
I9L7)sau
,,Iri: o-'-- ".."ui 0,'t'rsr.' (Ntinvi.jllc.
$'Jfii:1"Jt
fi J:,{:Ti:{,1:"','[,i
i"%"*{ri;
,,,,f;i*#i",'0,,),2ufii$Jl:t"$
t'olfariu. 19?8):
1\'] I i.pul aag*L tatt c{ 'dto'1'nllibilor' fnci' ]a <lel:utul excitilrii' rlsifliirtr
upoi chiar la o oprile cardiaci timp de 10 stttttttk''
l.Lo;tu;e';'e;;'i"iui,
,"^r,ia la frecrcnla i'o'mali' lllectrocardiogra'Ir. it'r'it'llt
;ll,i,i;;;
i"
r
""t:i""
,.iL'bradicaltlia s datdrefte urui b16caj sino-atrial sru. atrio-vtll1.r'i(iull
prevu]f
rr{r'nl('
r\ tlopinizarca pralabilX sau ld inistraJca de adrtrrlini'
rulbrirnri. Ar iitra in ioc u:r rnocanism bulbar (nfinvieille, 195?)'
consl,S,intr-o hipotensiune altoriitlil irKl(l
b\ fitrut lttnsio-d,epresor
'Oe
t:l,rc s-ar d*tot'a unei va'sodilatafii g(trcrirl('t
r,rm"irtri
"ud.i"utjdi",
ta
adrenalidi li o. sht inflrenlate d(*r1r'.1)itrrl
i
cdazii,
i"-"it.
t95?l Corfari[ [i ?opovicili, 19?2). Ar inira in joo iirl rrrl
-o"itn*tl',
ifriin i";lfc,
uiecanism bnlbal (Minf ieille' 1957).
c\ Iivut c??rr&l cor($Iulde tablourilor de hipelTefleci'ivil it'il sitttt
j cattlirttr':i srttr
modif ic5-r'
,:'rut idian'I (are nu |.c ilso!r'sf de rprct'inl-ri)c
rrt
dr,, rt.ioooi. ..i carc nu .ilt in{luenlafddo atropilri sa,tt adrr'tur'litr'r'
'l
trti.
I.t
(Minvieillc,
19571.
,l,i,rcrvarcaiino-crr.titljanil Iijnr.le{icrce
-A.r'rtili
r,rfebrali, n fosi individurlizati' inci de lTeiss $i Raker (1933), rlltrti tltr
t1'flris. UaDrs si Weiss (193T,cita1i de Corfariu $i Popoviciu' l1)?!), trrttro
i
,,,
iof'Jti rLou)itreiini .1in caiu,r.ile4e hiperreflectivitatc situr.r,rrtrrl
".i realizeazi' aceaJttd,
forlllri, tleqi llilvicille (19i7) Fi Corl lirl {11)il)
rlir,ni,
llr ai.[tat cE,,de fapt, este Tot.bacle ccle mai multc uri r.lc folrru, rrrirlrr,\ liji autori ilaSeurl, in cadrul formel'r cerebrale Sindroanl(trf tl.r' lt ilrt't
j,4ifrtrrtttl ('rt'('ir' li
r,,liectivitatei, a cirot simptomatologieesto nervoasi,
rrrutriicst.it
ilo obi(cl i\ e de Laz*.
Mjnvieille (195?) a individralizat mai multc Jomt' ;
tlc rlittti
cetebraLePxrr(i(rara) ^secaracterizoazilpr,in rr'trrtrsc
a,) U'anneLe
li lL
llJtlrl((
lLlsoulinl',
t|rtalc a s15rii tlc cort:lticnl,ii,piolderoa, totLusriitti
()pjl(rllLio,
sli,ltitrittttrr,
alrf
$0.l',iriii
ti,
d0
r,tirrvulsii
zl_L,rrot.au'icu lar'(',.hiu'
rk' lllitts ttctrlot'ivlr'1
lt(j(1(rs('
, tliurr1ro1'Ii tr'1rt'
do yt'drrtir,il(l('s{'it,
ti]ibrLlir,ri
(,iir1)i
.lliIXrt''tt{r\
i(litur,I)lill
rirrrrsrrtrri
$i }rrirr rltr.l.
,tiisc *i f1,lr, l)1.(,si'r'r,,
prrrrl l s'Il i rtrrl t,t , llr t git r r ,t ,ll, t lr r I 'r lt l: i l) t ilr r llllt t it r ihLlilt l r lr '. ll'( lili lli( t 'l llli( 1
I i t ' \ ' i I | |tI I i ||'| (I r l t lr '( llr r
i l \l i rrvi rri l | ,, l l )b'l) , I lr lit t t |lr l lt |t slr 't r r r r xsr \ |r 'l'
'
i ( Nir r r i|illr , , llllr 'i) , ir r I lr u t r ot t lt r r l olir t lt t t Dlr t gir ',t r t or lt
i ' l l ,)(i rl rr ti I rrl rilr , |)io
l roi rti rr| ' vi rN (l ol lt 'l llr l{'lt t ',
:t:l i
: t : t {i
../Itu
r-d-rr
Iltlri,rrrrtr
l ilt r , r l, t , t , n. lt x r l ; i, r r ,lilt t r . l, u i ( t t . t , d i r t . s , , l . t t s i r t r t r l ,
, ltt
ltt,tl,
I J):.rlllir
Ir. l'r.Z;r r llr t , . l' r l. r lit r r r . , . : , , . , r , , iir r r l l l i i , t , {l , t i . r , r l r r r., r rr - I i , . I I t . | ( , . 1
:,t I i,r'ir rlirr\'l.iir.,,1, r ir , . : r
r . r , r r lr r lr r i . i f r r lt r r i r . : i r i l . r., . ; r i r : . r , , r, i i . l r r l . i l l i , r
"
| | l1, .,r | .lr zi|r' :rlr. . it r ir r lr r i , . : r r , r t ir lilr t r
1dr . r L , . r t : r r , , . l ;r , r r . , t , . 2 i , . : i ) . r t , r . . r l l r l r i r
\ lir i i"rlr,, (l|,:,t)' r ir L' iiur L' - s u1t r os iv ii lr , iupll
s i i r . 0 {) 1 ) ( ! 1 0 1
s l r n ) . {j l r r 1 ) 1i r l i ( 'r ( \ ,
I )lrlr r ''.'\l.t1 it, Ir':r g . il' , t r l. CO t liiiiir t t lir , Si p t , i i t . l i l X , r , l ] , t r , : I f 'r , t r i l r , f i r r r r i l , r l
ri;iriliiiffii
;]
I'jiili
:r';'trll*[rtf;
i;li,
*rsi11i.rtih,**;lx|rl:
;)'ffii;-i,p"l#ii;t$tru**l,:";lf
t"';iy:;t,ltiil'li'f,Lllr;.liiit
|
, r.i, iri' ir,c{-.ltip de r.iispunsEEG ; c} Al treilna tip: rrrodifici.r,iIr
1,1,r!.
'ri, tr'
r'.r',t,s'rt
m&i plu'utrfr,tc, l,raducindu_scprin rdriii ale trils.rrLrr.
rrirlrt,,rlii rol:rtr.,.1.952;
.tIinvieillc,1957).Astfel, limp de citeva scclulllr
jci. r,poi scadr.ampliturlinea,iar -drLpi
lr:r.;,'.rlrr|l :'r:rrrrrdil
5_10 gccrrlrrlrr
:r'r' r' riJr.rlr'ii.ur,ll'\'ollrrle(to t0 ci'ri/scc si undc rtate, mai cvitlerrt,orrrr
lr;lirtrril', I'ttrtrirLl
.
d:lr cu o ur.olru,prcdominanln de prr,r,f.i,ru
.lrifu.lr.rulr..
., rlt.. t'r r'\(,r1.;[1
, /\,...il,, rrrlu]ente Sint la inCcpUtdin bAnda l,cl,a1rr.||rrl
ir1r.r'itt.sofi rr)rl,itn[1], odat5 cu crcDtereaamplitudinii. realizinil'rrrirl.
rlrrlirrrlrr I,r'rrri, sirrrrs,idal5,.Oda,tricu-e,pa.ilil u-ndclorlente, bolnavut i4l
lrrr,r'rl.r',,11ir..1f,,,putind _l)l,eze'tas,i _citevaconvulsii. Unrielc 1e.1,. lrit,
l(,_ -l() s'' {'nd'', tlar' uneoxi chiar 1-2 minute. ccl mai arrrrrsarr
r'|r'r'$rrlir
,r.r:{;r,,' r'r.Lr,{io
ct.'r'lugitiu intre ri,rirea ttaseelor EEG qi br:ldioar.rllrr,
tl:r,r
diacii nu depiqe;te 6 secuntle,lr,rr,oeulEEG nu srrlirrii
1lrr,rrzu,
'r'rr1r.r'Lrr
lir,rir,tri, rlL]. du,cii a,julgc ia 10-1b secuntle,apar modificii,ri EE(i, crxru
.rr .r'r'ii' rulrrl u'rroxi.i ccrcbralo *,uzate dc abseuJasistolei ventricirluftr,
rl, li :rr,lrirr.r.rr csr, singuta t,auzri,
lMinrl.illo, j9j7), jntrucit cor.r.r,trlli
:rl, ltti.l,ltrg,,l.ii r,r'lrrb.(19j4) a'r rqtrrrrtti, rnoclifjciri
-E-DGin :llrar,rr1rr,
,,r'rr';r.r lJnr.rlr(,ilnrlll
;:r,ll hilrotcnsiuni ar.teriale.Aceste constati,r,i altrnf,$
' \r.ltr,llt,ir, lot. lbLlrrourlollralti. purc, aliluri d0 formo intricate, irr rr lrr
.r,;r,l|,rrtlu, irrllrrr'r{:"r,
r',,r't,bta,li,
diro.ctd,la, 1i.r,r,tOrii
cardi:r,rrsau 1jonsiorrrr,l.
'I r'olrtl"irrll,irrvudrrt:lr,ptulcir,p_o.Ill)Gnuscpuuileviclenij,
manilcxl,i,fl
,,1,,.1,r'ir','
clilr.Ii,it.. irr lirtrlrrrl p.ob.ktr dc .xcii:r,1li.sirLo-oar6tidiarrii(.Nllrr,
rr'.rllr'.,l^l)fi.7
i |!')|.Ii,iir|,lU7l, l.9Zlii Liorlariu ryi l:bpoviciu, 19?2). illllor
ir|,,|r(r('||rt l,r'r,trir'
iiri Ir:r'Irirliir
prirllr!0 pi0r'rLrr.0
rLl eotrril,icrrl,ii,
crt rnirycr'l,r'l
rlrrI'iIll lrrl,o|.lr,l,isrrurLrr'qi
orr cil,trvllclolrii,rrtr sc i rrrrrgis
l,rr1r,zir,
rlrlgil,itrrrln
l.rrl. rri rrr..Il,i,r'rl .ii,.rir I'ir'|i-rrrrrI.
(Cor.fa,rirr
ryi ltrl,ovicirr, I1)?2),l)rrrrl
tt,tr,tt,ll,lr,
lr,lxrrrr(li,
rr IcrrIr,o-rrIiIrirrii,
r'sirr 1,ollt,lrlilirr.ilrii,
rlrr it,lrstrrrlit,
rlirr |rrl,ilt
trlrl 1i rlr,,,lillltr.lr" irlrrir,rrlrr
1;rrrrrIrolrIIr,.
:J;Il
,"I
:'.i'lJ't't;lii;lill'ii
\T:f".li::'tJ-ru"""t*ti?;','""*"#iJff
l,i}lrf
,;il"r"''
,$11i;,**-;;*it*[:41"*6]t":1l3"Tlill'"',
t'ffli11uf#k*t44"-#.:*ili'lt"'*g_si::!"i
.
ce
i;t*m' "*llx",*ril;ll ;lT$H"{:ii#"T
.ti*a'liksopio,,r,
*l"*fl1*"#*
*;*flX.*:\s{.l*$*f*1yi*tl*:"*d
"il?xtl;'de-hipcrr
u-.*::,igm*1;)f
;*?;,:"tntmm*t*iif
it*,T:".ii#,","'*##i*i-*l?H#4il1:
,,I';iffi;l;r*t""on5ria"""i'iii"$""\1]#i:lllrsriJii:3i!,?lH"
-",,*gm'ttif
'ii,1::r:?T,ff
:,ff*1ii:ifii.g1*,.t11i""t*','f;:gf
il*iil,l;ll;l
i#tltril;,
T:rj:i:rdf#"r"*rT{#:ni#"*;#"J
ll llil;;i
Ji,ri;:iirilllti,i*lt#"lii,''i:
m
:li:'I;:;llt"i:l'.i;l
;'ru;:l
ililikn""l'Jl*"j,l*,.ff;?"*:pl*"-tf;:li,ll:""l,nl*'i,'il
al ciirnii;ii etc').
jl:,k#::L,$ffi
;d:::*il'i"i*lii:ilkij?{,*r
*:fi,lliil;fii
;;ll;;ill;'
ji
:;
I
:iit
t
hlr**llunHitr
J;*ft
i{1,
':l"""th
icurtii,starecrcluscrit'I,.$:.ii1$"".:i;''ff1',i:1,%:t-ilL[llili,,
irii"i""1 .ir""rr"A ;;"tt;p'ii"i;;il.
|o rrH
Iii
Si*ptoro'atotrgiapost:}ccosua,lii
''tr-o
dulatii
onitt'
pind, la 24 de ore)' e
delir (Passouant gi Minvieille, 1954)'
""
cruneori*i:Si;i"tt?l,t'J:ff?r-li#iH:Il
faptui
serelateazs,
:il]'lliillil:
,ii:rHitff
f'"iL:f
i'.:titgp"ryt41*itrf
t*l
kilil[il,lif
lillll' ;iiiiiilli,*lii':ffi
Iti;iii,li:ln,lrl
i;iifl}liiii
i,1:
ilii]
,ilil;;,;ill,lit;
ll,,,llilil:;;,l,,li,ij,,lli
l*!:,,lii;,jllilr,i;,i'ill"llilll,,
,;l;ii;,1;lt,,i,i,li;1.;l,l:ill1
,
,
;;;ii,,i.i:
i,
;lilllili:i,l;ll
i:lfl
:r30
a i{X!4^,4^,\^.&-^^.^.4ae@
FM-V/\
"."".,,
{*:S***@
"Y-:-'":,;:*'
PD.-TO
tl
p r tl i r tr tl i ti
i n r l i ttp r ":t
l r ) 1 1 ) ( l fi
cl L l l l l ( r q i sl l 'i l i l ( r
tr zttl l 'l
. D U l l i i , c t t t t r i l l tl i l l i L l :r l :r l .r 'l l l 'l l r r l '
( l l i l ]g l l t) s
p
o
l
1
1
'l
tl
l
l
(
i
l
l
(
[i
$
P(
'xl
'i
u
l
)
|\i
l
,ttl
i
l
r
i
r
,r
'i
i
o
I X ) l i g f a f i o o t l ) l l i i 1 ,i 1 ,
1 r :r r :r r .Ittti t{1
i i . -r i l
'1 i tIi I.tr :tr 1 i :r I :r l si tr .,1 ' I.r ''
t,utiiir
n u r l l r 'l i r l r '"1 'i * t i i I I t' ! t I ; r' I i i
;;l tttti t:t\
t:t.t, stttd ti r t
. \ '. - i , , r " q i i t , A i i k
'
(ort'r'r'irt, 19?1, 1978; (.lollir'r'rll
(Gast*ut, 1t)"56i Oilcfia,ulL qi 51oic.t,, lutj;;
cr
tztt.tt
tl
j
l
r
l
r
'
3
u
o
/o
g
a
si
l
Vo t"t l l ctto ( 1 9 6 0 / 3
l C 7 :.j i . l ) o r t
.iFrno"iaiu,
Fffi--..,.^ A \
\/1 n n f\A nnA A r
^ vv
v v^ l/ v
F.u Gvv !4 v v v v \/v w -'\/v
@Va{Url^t*r^r,r.
l l tl r l tr l
t '| . 1 . : ; - : J , l . t "
Ir
I iItt,l, uc(Je:t!o1 5I IIr:tt1trr
" l
?t1*\t'$^^&4!t'{ry&+@
./.it. :{.9. I cflistmrc lolisralici
(compresiunea sinusului earoLiCian dupi
|ilx'ryDce) Ii bolnr\,ut C.ll., 48 dc ani. Dg, cr.izc sincopate p n hipclreflecli\'il.ntc sinocar.otjdian:I. Pentlu cr.izcle de pierdorc a euno$tintrei, deti IirA
collvuisii lo i(!)-clonicc ti lir;r njci o simptonratologie preacces[a]d, a lost
r.lidrctr)t:1 drelt epileptjci. lll clinica noastri loate invesligaljilc
clinice
\ i t , r r , l i l l i c e t i n r l .iv UEG .i I' F :b ) cr r fo .t n cg rti vc. C ompi restun,a gtt,l r j l o r o c u l r l i a i o st lr e g a tivi. In sch in jtJ p t llg u r a ie r edc cum_conl prcsrunca
sir rsului curolidiAn sting (dupi hiperpnee) produce rrn bloc siu;atrial cu
( l r r r N l i r d c I s r c nn d e , In so lit d c u n b u fcu d e u n d e lente
bi l ateral e, si ncrol l e
similflre s-au produs 9i prin comptesiunea sinusrlui
ii ni )rilrict, llodiliciri
rirolidiln
d r c p l . lla n cr r a Va lsh h :a a lo st. Dcg a tiYi (dupd L'ortori u, 1971,
( h r l a r i u$ i ? o p o Diciu , tg ? l si p o lo r i.iu
$i col ab.,Tgj B ),
r l t : l| l.
: l ll)
./141
,l:llli,i',.rfl,.,l,r''r.rlrLtirir,
r'r.rr1lrr,
biilirilrrcrrr,rlrrlui,
rllpri,t,ir,rrr
ljl'j;j',,1:.
;rr.tlirr.t.rrl
rrjrljrir'rllIr, rr(.N|rrrrrlr'lrr
lr.rtlr'.
tl.r,rrllrr,lizlr,ir,,
r,ru.citylt,lrsi, ssrr,rlii,'.irr
lrrrpli.
l . )N pi .l ,t1 t : : .r iu.
't p'. zir r lii, r r , I r ,((t r I I r ( ) : |,
r , r r , , : r , r '.silcopoLl s. lxr t . , , f r r r r r lll
.
:rrl l sea. l :)str' ctr r io; 1r r , llr r l lr r r lir r ir r . slo: J00 ( t ( r bolnai. i invcii, iga! ; i r lr r r r oi,
,,lt ruTcllc lurmd rto iil]l.,)J)r't (l.oitr il,lr'o)iirMtiv 5o/o au {ost indlrrrrrat,i
crr
rl rr,g)l ostl cuI cor ent . t lc. sjur . upi, r est - ul all f ust djl}, Sno. 1ica,i:1l, r f lbr r la1or .lr?l
,l j \' r' rrcl e.sorri cji polir . ) iline, dr cpt cpilr . pl jcj, ceet ic culjnor ( li
; i , . r r r r r i, , l, .
,'l,surla!l a1e lui.Gastaut qi Broughton (19?Z) si ale lui \-v-ayne
(11)(il).
343
,illll
-tl(,
;;:";;:;'i.'lt; '- iegirinilorr,Lcrioitr'(', llp Ftlil).\ ili lIllA, !t,"llllll]];il1
(1inc Ldlul ill:r(lllllll
l'
.r ((,Lrl)..ltitU)'
-iiocirr: c{'put, cunllllrdil,cll urrdt.Lr llli
a.l actslur g.ir'lo{l"rIr.ute .stc rlilt'til'
.;" ,;;;;il ,I,tr
i."t,, t ilo :r,pari1i,:
,r, t ,.rzu l'sin uu pci
ac es f e anoD] ; r lii l: l. l( l
lpJ l l n t t
i l r l l r i u r r t g l i i l . l r '( '& : l i ) l r l r r r l l
I A
IE'.
(TULIIUIIARI
PSIHOOROANICE
TULBURARI
OIIGANI(;)
CUSUBSTRAT
DE CONSTIINTA
T
trt'rtsilttlt,fii
itt l,rrrtrcltittl
otrtrrbtill(trotrrii),sirrii rrNlrtpttt'tilllli',tllltri,Itzitlttttlt,
(''rlrlll/i', il,ili
rlrrlrsrrpll,
tnozottco{illulttilit,sl[olittcif ittglttlllt'sottttrttltrll(ii,'
Irr,{irr1rr l,rrIbulrit'ilolrrlr{ialr dc cot16tiicrL{,ii.
ilo slts-l)l(tlArlrsl; pundr do votlcro nu trste coloctr dtxlattrctl1,ullrur'ilt
liorrrlo sirrt lulllulrili t1o conql,iin!:iI osi,o a'dovai'ratcit itt utrttltr <litztlt'i
(riolnrr()lonirir)
cxistir,6i o cornpontlnti' rninirnii do tulburl,trl tltl cott;i'iclt{,ii,,
fiintl insi, tulburarca de conry1;iinlrri,
rn:r,jolir,
Irrrr'|,ici1rir,r'ul,
Arrrsto sintlroarnc sint foarte elocvente in lcziunilc traurnatioe cr'ruii(l
(|r('olirliccgrirvc or,rc sc Iemit. Cind bolnavul iesc din comL, leziuuilc siltl,
irr cnrislirrele cerebrale pinii in regiunea mezotlienccfalici''
I )u,<fr,
loziunea din intreg creierul este pini, ileasupra capi,tului rostral
rrl Llrrnchiului corobral per;iapetluctal duce la instalarea unui muti$ur
lkirrrrtic sau h, sindromul de d.ezaterentarc.
I)l,cii leziunca r5,nline cantonati, in emisferele cerebrs,Iepini l:r zona
rrrczorIienccfalioS,
apare,,staroa yegetativ5,".
I)rcL lcziunile de intensitate variati, sinii cantonate in emisferolo
r,r'r'ollale, inclusiv nucleii bazali dau sindromul cliencefalic.
G, I)acii, Icziunea este in totalitatea, cortexului' in general provoacil
o rl'ru'e tle agitalie, cu iusomnie, confuzie agitat5, sau anxioasS,rpdn fa,ptuI
lri, iul,rca,gaactivitate rdmine sub controlul nucleilor bazali Dial trunchiultti
,lolollral,
;\dcseori, in diferite afecliuni, procese infeclioase' procese itrlocuitoaro
rlo spu,fiu, traumatisme cranio-cerebrale etc., leziunile inte,reseazd,toal,tJ
cclr t,roi ctaje ale encefalului - cortex, nuclei bazali, tr"unchi cerebral 1ap{;rarrr du"cela realizarea unor sindro'ame combina,tA lsiniiromui apalic),
l)rrcori, intr-un sindrom pot fi implicate tliferite etaje separat (hiperkinezio
r,rr Iogorcc, rigiditate decerebrati,).
I),r1,orii,i,legii biologice, structurile anatomice cit qi funcliile cerebralo
loh rrrir,inoi sii-t lezato p{i}Aqle Si cel mai uqor (cortoxul qi vorbirea); lrr
,,rrzrkr t'cYcnire (tlc la trunchi spre cortex) ele iqi revin ultimele, persistin(l
irrcii,rrrr 1,imp dupf revenirea integralS a celorlalte funclii (surdomutitattl'
rirrllornul vogelativ prefrontal tiescris tie Ttinnis).
ItiNliitrrr][r,i ios aceste sindroatne
Sindrotmclc generate de lcziuni Ia iliverso niveluri ale creierului
/1. l,czi[ni situats in partea supcri{)r,r'ir,a trunchiului cerebral
ll. l/{!z.iunisiLtla'hc
in nuclcii bazali
Ii
t;:
t;
lf:
rlrrrrr,rr r[rlu,l,ir,
J l. liigirlil,rr,l,rrrr,
lf. Ililxrlkirltzic ol Irgotrrrr
lIJ.l. SINDIIOAMII
I)A1'I{I)I' I,,IIZII]NII.,TI
DIN PARTIJA
SUPIIRIOAITT
A TIIUNCIIIULUCEREBRAL
f#fjdjs?i','"',g;l#,i,|Uq*'ih"""?,1,,:'^1';"""J
it$li;
;llil"';#l?'"1""J"?Iit:#;,t*$it*f":ih
r,',',flt
+j+1:;-*e*aH##tH*.;q",XT
Jl,iiij
g:*#ri"*i}!"'','ffi:ffi;iq'*w
ill"{*l"
It'"t'T"'*vniyll:l1lt*tirtlxktti+
yil,}*:_Tf*}:rd:F:diiFirml
llH*l"{ifl
:ffi:*i"",Tffi
iffst$i
iJ"tii*#l'?*1",1?J**T]]H',1n
Ilutismul akinetic se cr
;';ii1;,;'
ffH:lli;;ffi*#'1#x"""t"ff
ri?"J
l'"*"-ii:{{J:t:*i13ft';';;1
f;i;"!l"q.'":t.rH*idih*r,"r'*l
i',fi*{i;"##"";;r;;:f#1,"jt#*fitl*i:,":j:t
t3l;llJ#d"f#rr:f
:d{i{Fii}-lilih'tii-i"""""
lttliH"txt'.'ji.T#iiil",iljtril?i:'.*,?
'iJill;iif!it?,1!![i:l'i"
firi'{ft
*;1
f
rr"ffi+e$*t}"m;at{[1
f*{ilfr;;grig+;:;;f4';:{'fl
};;if
iiji'}:b'dr'"arii
H,:t{il:#if,iir**irH"Jid,r
-t1ff
ir1
lrLr{11*r[t'iil1i1,fl1
,liri"l*ioiii*
ili'.liillll,ll,lll:l'llliii:tl,,"ii,,ll,f,:l,i;llllli,ll
i;liik,w:ilii:li;$*li*llT
:t4(l
.)1,
F
(l(rill(x)llijli{rl11il'
rkr;tilxrlrrrt'vii
sil'llil(r(l(1llr(rlr('i',
illll)t'(lsilr
rji rrlllliHllrlllltol,(lrrfil'
qi trol.
(Ort,itrrs
rkr
a'llii
ll',
rrort,sl
irrtttilil';i
I'irrrltrit
pctlrtl''crtttill,iottfi.
iirrl,
1f}(is; $dn)i'i, iii (r)1. .ll)(i5 Ifrlyattrl - lltttrrt,T,tl
I
ll).1l; lll{i!; Skrr1l,01,y,
l,ir,(clriirr
do lit, thitxrzirt ir(lovit,r'ir
liissirl l..irrol., l1)(i{))(,slo cit oxislit,vit,rir[1,ii
1r:rlrrlizicitr sottsulor(lirlr,r al otrvinliului) ;i rmrtisn (sart tloilt l,Ionitr)IItri
hipolsolnnio situ obnLbiir Lrrlbrrlanrolalil tle corr;liinlii, (sau doar u$oa'r'ii,
lrrrr,) pi rri, la,o sirnpli'l apatie generalizati, cu reactivitat'c bun:i h exoita,lrli.
{ l(ilrx;lirilc rroa,slrfa
iln mai ari-rtat c5,,de ceic mai multo ori, dupai,o 1u ir,
lrrlrr,lrrl'qi I{cmpcr qi liomanul (196?), XIA (in folma clasici rlesclisil,rltr
t lr,ilrrs si trol. t.i+t) rcprezintil un sindrom tle ocluzic a al'terei bazilare in
por(irtttir sa rnijlocil.sl,u joasi. la care unoori se pot asociz'tulburili rt"
atinginrl
i,orr1iiin1,L(prin" leziunea ialoi,ei pontine qi/ sau .mezencefb,lice,
(l t' i rr' Lr1.1r . , 1. . llt i l) . lr r I ir , z. ilr 'r lilr r , r l. . i ( l'I ii, r lt i r r r r r ll. siPliir r r r r r i
ri tttt.l tttri Ii r,l rr r lr I r vii c sr r ; ) I r t vio( , r r ir .,o, r 'r , gr ,I ,r , li r l'it t l, r 'it sor , Lr r r , r , iiilrr t r r r l0
lr r r l
Itrttl t: sttpl i nr r lllr , lr slr , r rr , lr ilr r r r r r lilr r r : r lllr , rrrrrrrI Ir I i I i I .i I I ri Irr ir r sr i,lir sl ir r r r r lii
t i zrl r,l i , a,rrr lilivi silr r nooicclll, r vr ,
' l opogr' : r , t ia1i inlinr kt r it r r Lt
, zir r nilol nu llr r pr r lr r l,licr r r r r r l i{r r r lir r csir r lr ilill
.
rl t rol :l ti vel o put ino la, zur i st ldial, c. Au hisi, r lt , st r lisc clt ar r r i cu r r r lir r r o
I.zittIri neocolticale. So cilea,zii cazuri crr lozirrrii t,rt..nsit'ir srrlr..r.i i.irlr,,
rllrr cu crulat'oa structurilor. trunchiului cetr:ltlll si
inr,crs
rrr lr,:rinrri
rlc lrunchi sau cu r:xtinse zone isr.hcrrtice tut iii,Lile s;r,u srrlxurr,l,it.rr,lr,.
13.2.SINDROAME
DATEDE LEZIUNIIN NUCLEIIBAZALI
s RAA ) .
Sindromul diencefalic
Se earacterizeazX prin tulburS,r'i rle constiintf cle intensit:r,l,o r.:rlirrl,ji,
ci.n'econsl,au intr-o sta,re de apai,ie, lolpoare, obnubilaro, soIIll(t (,1{i'i,
'il Ipoirre-Rcspirr(ia e\te de !ip Cheyne-stbkescau t'espirrlir,.rr Iit r rr.*,,ri
I r1'ttrgulat,",
rnllerullt uncorr de pauze scurte, pupile mici, rtrilr,tivrrlll, lU
r nrr;.lellexul cilio-spjntl este conservat, miqci,rile reflexe rlo gl0lriloI
{r'uralr ln plan orlzontal slnt con$ervate,insi, uneori rnotilitate r,r:lltrrii
rxrular5 rrerticall este.IimitatS sau abo]it;, (comprimarea rcgiulii
l)t.ol,(r,
fale) ; existS, reflex oculocefalogir (in lezidnile'de ironticrtii rIitrrr|r,IrrIo
rrrczencefalici), deriere ronjugatd, a capului qi ochilor, ten0rnt,lrrrIrlrr
,.r.nr dc prpu$i,'. rinooli der it,re Ienti ti porsistenti a glolrilrrl rx,ul:rlr.
So noteazi, semne de suferinta, pir*midal5 ditatcrali, (I3::r,blnsltihilrr,l('r.rr,l
).
Ibt fi evidenliate o rci,istenjii, ^muscularii, tle l,ip paiitor,fu
rrrr r,,ll,Ji
.\i
,1,.ftpucarefortatA.;iD abscnla unui deticit rnoloi ri.eqtclnorliii{,riIip,rt Ii
l,ihter:!le. Pot erista diskinezii. Tulburi,rile vegetative sint abscrrtr,.
.par(,iall
a t,ir$l,l rl
._Sttpoar_ea.**" *oilnoi&1" reprezinti, u p,ig_rdere
sit'ilor la solicil,5rile mediului inconjurilor, iii starea-tle colt$liitrlii r)Hlrt
rrtectati, r.ra,i rnult sau mai pulin. precurn d,ratii,denumjlile iu;_rirr,rrt,io
rirte. pacientul prezinti o stare de somnolenli, mai mat,e sa,urnti rrrir.ir,
elrr lr
'.)ic aln sau ..hlat,.uncori. cpontan (dupn gl,a(lulslrrlrrlji) rr. l|r.
z' rl' . l urbe:lo, (lA riispulrsuriader.rat. compl"ie,lncornpl,.tridinl tiurli\ r.,
(,,,r'ece a}e ne\-orc, mill]rnci, singur sau rlacd,i se di, sL rniirrirr<:o
I rlr.rrrrr
l|r'rroil.loule tlr'sr.lridc
ochii, str (eara Si.$i fa(,i ncccsili{ile, rrrrr.rrIi
rrri;r.:r,
r. rrll(. Sponlrn. cbtrr potte urubla; [ulcqiile vi[lt,lcrjlt Lrlrrrr,.
Sr.r,lrtlr,.t,.
rizprtzi, printr-o. mai iltensi, cr.g;t-glqa plairurilor slzoriale, cilrt arrr rlrr,pl
r|rrrrt: o recepl,ieintilziai,i, qi inadecYatd,o lentoal,esi o tllfi<:trl1,|ltrr rlr,s
ii.-ttririi 1rror..esalot
tsociatire, Bolnrr ul c.tr. lpllir, r,iitrrrtrrlr.r,rr
irrlirzrclr.
l:r itrlrr,biri. pr'in rri.punsuri vagi. apluxirnriir,,, irroirrpl,.tr.
rlr, ,,,,1r.
1i,
r,rrairnulte ori, lipsite de sens.
-lltpori (,s1e,\ornn;leut, tlr'zurirrnill,;i corr
Itz,. Evocaro:, ar'nczi(ii so efc(.tucazir,rliii,.il, rr't,rrri liirrrl irtrlrrisilrilri.
llr'lrrrr,vnl
cst c..lI;r11i1tsih
iu ;i.lnitdikinetic, sc or.iirrrl,cl,zL
ilifioil si irrr,'rrr1rIr,|,
tr {l}t(ill .i .li'ri irrlir'rrrrrIii
si irtr.s:r.lcrlr.sIr.r,lr',lr'itr *r P,.r,.,,r:rrri.
l,rt int,ila,{,ii
rrritilc;x,lrrlir!i lllti'rrli
irlr,lrfir.,lrolrlrvrrlir,r,rli.trri.zcrrla,
riurirrrllllr
rii
t'iirliI:r'|r'.
Il.lh'rrtl rlr.r.lilrit l:r rrrrLr.rriir{*r,.si
l,r'(\rizi.
r',rlloxrtl.o|rr.irrr
;rittl lttcz,r'tttr,.lirlrrrrvrrj lrr lrrrir,lrr
IrIi rrIrrrr|,Ir,, illl r,litr,l,i,r,ll Irrrrr:(iorrr,ir,zii,
rlr,..rtbirrrri
ttottrtrr,l,l.llu;Jgati);t
r\sls rrllriytr,lslrli,
(11 (,oglir,Vigilr\, llr,rrrr.rr
rrliliz:ll,tl. ilrtirrr.iiI'r,rrrrr.r,zi.
plr.it,trlrrl \,rl,lr, lr\ 4i trrr
l)rr,r,tr,
ltr,
'lt
'illDrtrrrlr,
(t4lr
,{il
it4rl
l,\lliI ' ilI iil(lll,l.l:.j,iIl(x)lltlit lt lqt . llt I t t ll, ilt l' r I lt r . iit ' iilllr t t t t ll t t t . i I r . l i t t I i t t r . r r r . l 'r , t r | 1 . '
s i t lt l ( l' s i ll|r t r ll l . . '
, . 1r. rt r l.t (l ..1:r1 1'r"' llillz i\ . ' .
grll(lir:
llttttii {rlltlttl tltl s r t nt t t r llet t ll- l ; lt t lr r r lr ' lllr ' r ' r l r ' l r l 'r l l l l l l l l l i
s . r r r r r 'l " r r l : i '
:
t
r
I
.
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I
r
t
't
I
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'
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r
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it
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':
r
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rlr'{l:r ' lr r l
Jriiti,,,l,','
' i' l
rr'trlf(11('il1rr
, slc tlatir,t1c troitrtcrosltrclplrr'lirrJii
,,1,rr,,f,ii,i':,.,
r,i,, 1,,'ip,,,'tr'.,
r)iscotrlil rtti,Prr'(i"lt1rl(lN(loilI (r:i'(lilr
i'"1,ctnotLcr':r'til,
sotrtttttlllrrl,rt
l,rr,z,rtli:
,,ii',,i ii, ,,irr,l qi {ra'ticlpir, pulin la oxciiat,iilu tlitr tt.rcrlittlitto.ttjulitlut.
St:rr.r.: r l|t t , , r . ; r O ni,.i ,. F o l l l (. d C fi n i r' :' ,i ttl o l r i dtZol i | Ji l i i ro Icntl tt' ror1t:t
t ,' :r,,ti l i i ,' ,' 2 i ,.s i r' .r s r i rl .rr' rr' l .nusttl l l i uf.r' l i ' r,,l i i .i ut.rr' l
i i ,,i ,i . , . , , , . i, , r i"
"
,
r
ir'liltlcttiiri
;i ruptiof. Stalcr tltr
ii',iiiiirl*liri,"lt,.i" sc,[t6.c:l ilifilr,tirli,
oLr r) dirrinuaic ir'
srnzorjirle
ilur
prrlgul
:t,
craqierri
intro
i,f,i,ili" ,r"*in
groutabe 'li.ctr
ilu
oarecare
rr,rsilrilit,ir,lilol rlc leccDtrie (care s6 rdalizeazi
.'""''.1'i;1;ll.ilj;'hi
bolnav'l
,''ai a":'certrltit'i,'
!i'trLl lr osteo somnolerrti'
('cLl Lin(1}ri
|';\||.1|onIi|''Ier.iinir'."-laloIogi..ibincrIofinit:r.l'cz''].''r'ldin:rq,.!{'iotc}
in
,1,, ,ririiiL..tffiii neurologice'dc tii polinerritic cu manitostilri psihicc'
dt'zorientarca'
confabulalin'
clr'r tltttrtitlit, &mnezia antcrogradJ,
"'i
lJrrrliul lcziunilor dominantc este mezencefalo-dicncetaUc'
iu: marea
lrr cliolottic, factoml dominant esto toxioo-metabolict
o
rrtiutrlilltt:
otinlogico
sttrvitr,intt
t'onrlit,ii
Alt.
,,,,ul,,llir,,t"','r'-7"r.Lrrjlor'
ii,, l,iil,,ri ri rt"i-tl,r riaturi, turno'al;i (tt*roL i tle uutJei brz2r1i,rnetastazc'
t.r l,,,r,rrikra,rno),infectrioasil,, l'asculatit' slu t'r'atn af ic;"
sitttlrtrtttttl
t l i r i {n t t t 'i r t r
Sirrrll0 rrrrrl lili i\ / ( ' f ilu( ' ) . lt 1} r t , , t t r t l, i : r l r l : r l i i s . u r l l t ''z i L l t t i
l l i l ' {'o i l r l l l
l
t
l
l
(
l t i 1 'r x 'r r t r r l 't t
I ri I l t,1' r' t rt I t rr lt'tttltltI'lllt l , 1i lit r c r r ' ' t illr I ir r ' ( gilr t s r t l
' :tliilii tlr' cott(
}
r
r
r
:
t
l
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t
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r
(
{
lt
'
1 '
lrti A rtrtrtritr, rrtirtlilc r t t l lr ' t r r igt llllillr t ) ;
:lti0
prin docorlicarc
( l r't'l l i l
l r j l t.r ,ti l .r , r ,r i l r r H o tr r ,r ,l r l i r
;i l ' I
A rnnoziikr posttrnutnll,irttl
(jotrsfil;ttic urtttl tlinl,rc oelo rnai cornunofcnornone alc ctcoltlor ttiturrlrlictr rurrr'lrrille- iltit lt:cento cit si tardive --- indifotcnt de inl,onsitltcit
I r';r,rt
rnlll,isrntt
Itri.
Amuttzia posxlraurnaticii propriu.zisd
\rnrurzia posttlaumatic; propriu-zlsi (APT) este tlefinit5, ca perioada
rio r,rnnezic dun5, revcnirea bolnavului la un anumit nir-el tle conDtiin-ti',
clrirlr inoil, perturbati, sau la un nivel normal, in care persisti, nurnai
rkrlli0ilul amnezic.
I)ulatja amn0zici }osttraumatice este in diroct raport cu graYitatca
Irrziunilor traumatice cerebrale .:i exist[' o relatie directii intre durata
ru,rrurcziciposl,iraumatice',ql virsta bolnalrului traumatizat.
,\prrocierea amnoziilor posttraumatice nu se 1loate. face {leriit rotrosrlupii ce bolnavul gi-a redobintlit un suficient nivel de_conftien!5.
lxxrtiv,
'
Exisbii, pertulbarea memoriei recente' chiat in condilii de completii,
rorr,bilitare aparentd, a nivelului de congtien!5,, Si nu a1 legfturi, nici c_u
glrr,vils,tea, I6ziunilor core.br&lernici cu virsta ori cu leziunile celebrale
ploorcisbente.Nt ar exista dificultS,li in reamintirea vechilor engrame
inrrcsticc. Bolnavul este in md,sur5,si,-qi rezolve problemele vielii cle fiecare
iri, (lal este invalitlat in achizilia unor cunostinle noi.
S[Jrs1;ratul moriologic, lezionaI, al amneziilor posttraumatice paro
si, f ic in arilie hipoca,mpice ale lobilor temporali'
Amnezia retfogradi (AR) este detiniti, ca imposibilitatea de a reme'
rrrola, ta,pti] sau idei din perioatla imediat precedenti tmumatismuiu'i'
( k)rldiliia-cste c:] in momentul traumatismnlui oreieful sii, fi fost &lelt qi
irr conrlitii functionale norma.le.
I)o regul5, AIl, cste tle foa,rte scrrrti' ahratil (tle ciieva -secunale,citeva
rrLirrrLi,c,
mai lar dc citeva ore). l)urata AR este in prirnul rinil in laport
r:rr u,ruploatea ii ou grayitatea leziunilor serebraltl traumatice.
llxistii, cazuri ile AR <le foarte lungi durati, - citeva' luni sau chiar
ci{,ilu,ir,rri.In aoestecazuri sint implicate pert[rblri gral-e qi ieziuni intinse
ir sl,r'uctulilo rinencefalice (Russell' 1976).
?
grtspittgotrrrlrtillrIrr,1tdolttrlit lii plin lroz(rlll,il,
rllurf(xllrl)r'inlirl,t'tttrcltiul
rr.l'lrrr
rrlui tltt Drrrttr:tinsiltlttr:tlii.
irr cunclu)ic, tablloul urrui bolnav cu logorec ryi hipcrl<inezi.ociittr
rrlrrriitorul : pacicntul prezinti, o dolinfi sau un irnpuls irezistibil ;i aproalxr
rorrl,irrnrr spi'e acfiune, miqcare ,sivorbire cu : a) logoreer.cre$terca fluxuhLi
irtcrr,liv(tahipsihic) $i a si$temi ui itleativ (tahifemie)' cind leziunile corl,i, rrlrr rru sint prea mati ; b) latenli, hiperroactiYfi (hiperprosexic) Di reflex
rl,, oli,'ntlre prornpt; c) latcn!5, foarte micd in ri,spuusuri I d) incircare
:r,frxrt,ivi,atiocvatS,aitualiilor e) hipermnezie, cu exagerare, el'oci,rilor7 caro
rlrv irLtrrrnultuoase,intempestivo qi rapido ; f) sim! cxitic ascul,it; g) coerr,nl,r iii ].rttrfunzimea gindirii pot fi pistrate' dar de cele mai multe ori
r-1r1,rk,tri iorate, fapt Cate depinde de leziunea cerebraH, $i tie fenomenul
rlr, hipcrtensiune intracrania,nl, in cazul proceselor e{pansil'e; hipermlezi,, (cu r.xagcraroa cvocS,r'i1or,care deYin tnmultuoascr intempestive qi
r'.r,lriil,.),cxagelareil atcnliei, u reflexului de orienl;are, logoreea, mobilitate
siini, critic ascu-tit,somn foarte pulin (2--3 nre din 24)r jud.ecatd
,.rrrr,.r',r,tri,
;ri lr iunamcnt- nortn:tle sau deteriorate dupX gratlul ;i localizarea leziuni.i
{ir)ttrl)raLc,
it5,l
l l ,''fr i .r -
Arscnl
C , , Op r cscr t
l - * I) u r cr t:d .Fi .i o p d l o l o g i ecl i n tcdsi l r tl d m e r r l ,Ii d . Acu ( 1 .l l .S,l l .l
llucrrrcltl, ll)(i7.
( ; , Si D r l o n cN o l l
\1 ,.- I>a l o b l i a D ( tl n o - n l kl l r tl n r [0 .Ii a l r yi ( r l d , l i r l , I\1 r ,.,
Arscof
(lk:nlil, Iltlcu.otlI, I{lli8,
( : . , O!r I
c'' 1 ., [!n r r l BI$
Arrfnl
,\1 -, - /) /l r l r |r l i ]l r i .i , l tl l l Sfl ,,l ', l 1 2 .
305
(,Ir.r,r'll
.-|l l _
1 ., \l :' r ' lr ir ,
\1 .
t) ltttthdnui rt, t1|ri i t,. /,,:j
l ) t ) | , s ( r , t., t\t :r | ,.t s lx ]t.
t) llu lttr,tnl i t, tl l r;l t t,. /,, .^l ti 1t u1)t.
l\ll'(tsisIt.
Nfu f( ' 1 ., I,sitr i;r t., N| [r .,x.hi r., l t)?t), /.j , t|!t .:j :i 9,
l,0lr,z
t\I. 1 ..
h tth u ttir i ) r isccr or tq | lu tit)t::.,:i tr,l i tt
ttt tr:i tuti t.
|\Ltl ti tr,
l, l ( 1 .A c a ( 1 . l l . S . l t . , Ilr ( .u r ( sli, t9 ? 1 "
( : . . ( j o D s t a ntin cs( :u
A f rc lri
]\l . I._ Ncr ir o l.,
j t;,
P si hi l rt., N eurochi r., l gi 1,
ll) j j - l t { ) .
( 1 . , ( ; o n s L u n t i n e scll
, \ rs rn;
A,l,- ^ Hip e
e n siu ea ttacrani arLd, E d..A .ced. II.S ,R _,
I lr ( u r . { t t i , 1 9 7 2 .
Ars c ui
O., Oprcscu
\*
I' ? a u m a lo lo g ie cr a n io - c ercbrel d, Itd. fkdi cal d, E ucurcl ti ,
M2,
(1., ,tlarotsis
/ \ rs rni
lI.- Ro v.
r .o [m . Ne u r o ]., 19?8, tr, 359_362.
, \ rs f
i ( 1 . , C o n s t a n l i n cscr 1
A. l.J lla r e tsislI.,
S tauci u]I.,
V oi rescu
7.., Itrocescle cxpLotsiDc ifitrdcrutliencr \'ol. L, Ecl. Acacl. tt.S.R., Bucurcsti, 1$?3.
.It
C . , C o n s L a n t i r o \. i c i Al., p a n o za
G l .\._
tl unati smel e ue ebrc-med.u_
' \ rs rui
tut?. si ltl. tLcrDilor, Iad, IIcdicali,
Bucnrc$ti, 10?3.
, \ rs t lri
C . , C o n s t a n l i n e so u
A.t,, Co n sta n tin o vi ci
A ., (]hi f
esc!
M.,
Nl 1 r r e t s i s
lI.I) o cr sc e xp a n sir le itr lr e t! a n icn e , vol . II, Ij d. A cxd. R .S ,R ., B ucufcsti. 1974.
.\ f s c I li(1 . ,
Ioncsou
S., Ir ie tr a r u
N., Ilie scu
D . _ N cul ol ., psi hi at., N enroctri r.,
10 7 4 , t r , 3 8 5 - 3 8 8.
j U ., Din d itii
, \ rs oni
O., Golu
psj hi at., N eurochi r.,
T - ., Alcxia n u
D ._N curoi .,
1$ 1 t , , 2 1 , 2 4 1 - 2 5 : t .
.\ rs c ni
C . , C o n s L a n t i n e scu
Al. I., M a r e isis
l I._
S mi ol ogi errcurcchi rLrrgi col d,
\ 1, . , . 11r i i . .
r\ | l. e, i ( : . ,
AI I r. rrI O - .
\fsi
ni ( 1 . ,
Art(lu||
I l . , t) r , l r o r 't., l ,,r t,,'vt'
tl l L
i ,.r r |'t., Ih r tr r t., N .r r r o i .h tr ..,l 1 t/1 ,, / r ,,,
Ii l ' i '1 .
Atglrn
ff.
l str l i ti u l t r i t.ttl 'ttt'tt ttttl th ,th ,t
r r r i tn r tn :t.
l r r : L . I'o p 0
'ti tl t 1 [i n
( f h . I'r ' r l cl t|l ,l l |
viIirl,
r r t t. t'r ' ! ( , Il o l i l t n t$ t1 fu trff: ,l ,r u k n i tt si r l ,, tl
DcrtI:lrIo
ltu.i[t$, lltliL. .Jrnrlrrfi, l{}1. llrtl{,, t,t', llil) -l8lj.
Avirdo
1 ) . tr I., Avi r {l o
l ) .M . ,l r , .;\r r r r .r '..t. l ,t) ysi o t,,1 $ It, Jr j r , !0 t .U 0 $ .
..t. N ,.u r o t) tr vsi o t.,
llailoy
1 , . , BIcm e r
L
1 $ :t8 , l , .to 5 - - .tr 1 2 .
llancaud
J., Ta l a i r a ( h
.I. - l l ( fv. N d r r o p sych . In L , 1 0 6 5 , J.? ,4 l t3 - 1 0 0 _
Iiannister
R .- L a n ccl , 1 0 7 1 , u , 1 ? 5 - - 1 7 0 .
IJarbeau
sgndtuneof lreteditarulaleonselptosiscn.}dtJsphagia
in l;rnch (: rtttltt.
In: It.^.*The
K u h n, Prc|ressine maskelilgstrophle,mgolonie, mllasthcnic, Springrr V,,r.tllt,
Berlin, 1966, pp. 102-109,
Ilecker
P.E,* Iratamiotoniacongenila(Eulenbery),Fortschr. allg. klin. IluDllur,1,,Ilrl ,
Badd III, Georg Thieme, Stuttgart, 1970, pp, 1-1A1.
i J c c u S T . , Ln l t4 cs
E., Fr i n cr r
I. - N e u r o l .,p si h i a t,,N e u l o ch i r ,,1 9 1 2 , 1 7 , l t:,! Ii t.'.
Ilehrmann
G., C r r o l l
.1 .D ., .l a r Io ta
J, B.j ]Ia tth c\ys
W.B.- D r .l l h r , l $ 0 1 t,
99,663-678.
Ilein
E. S.-Languege and Speech, 1958, l, 23:]-2b,1,
Bein
E. S. .'-..Comunicar.rla,,Simpozionql astrprd afazici", Bucure$ti, 1960.
Ilenard
H . , [Ie r kl e n
F.P.- C .R .
So c, Bi o l ., 1 9 4 0 , 1 8 4 , 1 7 3 ,4 7 5 .
Dender
M . B., Fu r l o w
L .T.- Ar ch .
N e u r o t. Psych i a L ,,1 9 .tr bd, J, 1 0 b - L ? 0 .
p ,J. a n d tsr u yl l
Bcncler
I l . l l . - r i so r d e r s o f e g em o D e m e n l s.
( i . \\.,
In l Vi n ke n
Ilandbook of clitrical nearcIogg,
1, Nodh-tlouand publ. Co., Anstu,(|!Ilr, tl|il,
'tol.
pp.571-630.
Ecrgman
P. S.*Arch.
Nourol. Psychiat., 1957, ZS, 568-b8.t.
Bcrner
S . Jr .- AcL a m e d . sca [d .r 1 9 5 2 , ]4 .3 , 3 3 6 - 3 4 2 .
tsest T.-Aroh.
PsychiAt. Nervenkr., 1952, 188,571-521.
Bickerstalf
E. R ,- L a n ce t, 1 9 5 1 , 1 , 1 5 - 1 7 .
llickerstaf
I E.R .- R e v.
N e u r o l ., 1 9 6 4 , .r 7 r , 5 8 2 - 5 8 8 .
llickJord
R. c. - Elcchocnceph.clin. Neurophysiol,,1952, 1,27b*282.
R i c k f o r d R.c., Wh e a l a n
J,L ., Kta ss
D , W., C o r b i n
K.B,I.r n s. Ar r ,,r .
Neurol. Ass., 1956, 8r, 100-102.
Elack
L . F , Eya tt
R .E.- Am e r .
R e v. R e sp . D i s., 1 9 7 1 , Ir j , 6 4 1 - 6 5 0 .
Dlank
K . N . , Vi ck
A,N ., Sch u l m a n
S.- Acta
N e u r o p a th , 1 9 ? 5 , JJ, l :) T .l l ,( ,,
Blumenthal
FI., M i l l e r
C . - Ar ch , N e u r o l ., 1 9 6 9 , 2 0 ,3 6 2 * 3 6 1 .
Bofrorsiclt
A., Bi o d y
J,A.- N e w
En g l . J. N Ie d .,1 9 ,7 32, sg , 1 O,1 7 * 1 Ofi ,
B o dechtel
G.* DidgnoslicdiffArcncieldesnaladicsrLeurologi.laes,
Ed. Doin |jt.01,,,ttrrbr.
1965.
Bogae.t
v a n L ., M a r ti n
L ., M a r i i n
J.- Acta
N cu r o l . p sych i a t, Itr :t{., l l ) l i t,,
d5, 845-872.
Bohnert
8 ., Sti th r
M ,- Ar ch , Psych i a t,N e r ve n kr,. 1 9 7 7 ,2 2 4 , 1 1 - 2 t,
Borrduelle
M .- R e v.
Pr a t. ( Pa r i s) , 1 9 6 5 , l j , 3 9 1 1 - 8 9 2 4 .
Bonduelle
M .- R e v.
N e u r o l ., 1 9 6 8 , 1 1 9 , 3 l - 4 6 .
Bonduelle
( i ,* .- .1 . N { r ,t.
M ., Bo u yg o e s
P., l l sco u r o l l e
R ., L o r r n e tu
Sci., 1968, d, 315-332.
Bonduelle
M ., Bo u yg u e s
7 8 , 8 2 7 - 8 3 !,
[Jonnet
Af
I]., Pirof
I J ., Po p o viciu
t lilll
L ., Du lIu
E ,S trud. C crc, N curol ., 1g69,
/ l, . 1 9 - 5 f ' .
p silia t., Nm r ochi r., 1969, rl ,2l 5_2tt.
Al ,lirrn
Il., I)opoviciu
I..*Ne r r o t.,
n ir A ix n I ] . - ( k u r r n d p p l? clictl, Dd . Dr o il, Clu j- Na p o ca, 1074.
P . -t{cv.
BonvallcL
| 11ir.
P,, L o r m e a u
G., I( e l l e r
J.- p r o sso
M 1 :r 1 .,
t1 l /r ) ,
Oto - l r e L r r o - o p h t.r1l .,
057, 19, 65*80.
I,., IIi cl ) o l
C "* C . tt. So c, U to t. ( l ,xr i s) , t0 5 :t, 1 /? ,
M ,, I) r !l l
,l l tt:l ,t tl !l tr tr \r |tttt
llo t l,z U, l,
r l { r r l f l ll .';.l l , l l r r l :r .
't( tttr
lt
p r o ct:sttt
|,tt,u n si n (i r r ft.tn tt/r r , Ir t, AIa
: i {;
: l lr '/
,rd
I J , ' I r' ,
t U . I . , S ir f I l ) It
r(fti,,1r{)1,
( .$ r : u ' 1 .
.llu iltu r n n
n c t i cru i o [,(i tl r,
(1 ., IJ!r}b lz c t
llor{ liD
S. , l) c r oues nd
C. , V a n A m c r o n g c l t
P.., -llrv.
Ncurol., 1!67, l/r, 80-95.
(i.; PCp ir
I lou(lin
B. , Vc r naDt
J . S. , G aut ie r
IJ,, Goudrou
IL-Itov,
Ncurol., 1971, 124, 90-92.
I! r rf I c y W. G. - llisorders of petipheral nerrc.s,Black\rell Scientilie PublicatioDs, Ltd.,
0xlord-London, 19?4.
It) irin \V.R.* Brain ,
7941",6a, $- e2: 24{ * 272.
llrrin
I-., Croft
P, 8. , W ilk ins on
M . - Bla i n , 1 9 6 5 , E r , 4 7 9 - 4 9 8 .
llrait
I{., Fah n
S . , Sc hwar t z
G . - Neur olo g y ,1 9 7 3 , 2 , t , 9 9 $ - 1 0 0 2 .
I Jrion
Neu! ol. , 1 9 6 7 , l l t , 3 8 3 - 4 0 0 .
S., De Hecondo
J . D. * Rev .
lrlody
A. , Sc ot t
R. M . - Neu r o l o g y , 1 9 7 1 , t I , 5 2 8 - 5 3 6 ,
J.A., I-liran o
llrown
.1.W., Colcman
R. F.-BuU. Los AngclesNeurol- Soc,, 1966, J_I,21-34.
l) r o w n J, W. -.4phasia, aprukla and. agnosia, Charles Thomas, Spri'gfictd (In.), 19?2.
Ilrow nell
8., Op penheim er
D. R. , 1_I ughe s J . T , - - J .
Neulol. Neurosurg,
l,sychiat., 19?0, J.', 338-357,
lf r u e t rn a rI M. E.- Post$ad. [{ed., 1974, 36, 779-*125.
f f nrian
H., Burn s
C. - Am c r .
J , O pht hal. , 79$ 1 , 6 3 , 2 2 - 2 4 .
Oairns
I],, Old f ie ld
R. C. , Penny bac k er
J. B . , Wh i t e r i d g e
D.* Brair,
1941. 61. 2i3*290.
O rr i r n s 11.* Brain, 1952, 75, 10$*146.
(::tmbier
J., Bscou r olle
R. , M as s on
I l. , Le c h e v a l i e r
B-- Rev, 1\-eurol.,
1060, 1r.1,139-154,
(l: rDrpbe Il
A.:[[. G.- Riv .
Pat . Ner v . lledt . , 1965, s 8 , 2 1 1 *2 1 7 .
(: : r r d: r ! lL , Milcu tiu
V. , Vuia
O . - Ac t a Neu r o l . B e l g . , 1 9 6 6 ,d d , 7 1 9 - ? 3 1 .
(l ,rr richa el8 ,A.,
Dix M . R. , Hallpik e
C. S. - B ! i t . M e d , B u l l . , 1 9 5 6 , 7 9 ,1 4 6 152.
(j rrstaig ne
P,, Bu g A. , Es c our olle
R. , t r {a s s o n M . *R e v . N e u r o l . , 1 9 6 2 ,
108,351-3ti2.
(;N st aign c
P,, Bu ge 4. , Es c our olle
R. - Re v .
O t o - l e u r o - o p h t a l . ,1 9 6 5 , 3 ? ,
321-328.
(jrst rigne
R. , B r u n e t P . ,
P., Camb ie r J . , Es c onr olle
Guilleminault
Ne!rol., 19?O, 122, 313--320.
0.*Rev.
(: ! rst nigne
J , , Es c our olle
R. , B r u n e t
P., Cam bler
P,-J.
Neurol. Ssi.,
lfir, ft, 725--135.
(: ast.ign e
R. , A u g u l t i n
P., L ap iar c
D. , Es c our olle
P., De Recondo
. I.D., Matin ex
Lage
G . J . , Villa11uev a
Eusa
J.A.-Rev.
Neulol..
rf)71. lr1. 454*466
(jrst cigne
D. , Far deau
I l. , Do! d a l n
P. La pla ne
C,, Autrct
A. Ilirt
Ncurol., 1372, 12d, 81*96.
L,-Rev.
(ln$' l. horDc
T.E., D ix M . n. , Hallpik e
C. S. , g o o d
J.D.-Brit.
lIed. BuU,,
1IitE. 12. 137*142.
ycslr"
(lr\dt hor n e
J . D. , Spen c e r F l a ! r 'i s o n
T.E,, Dix t r { ,R. , I I ood
M,bular sllndrotnesand.Dettigo.Dtffctenlial aliagnosisbetweencenlral aftd petipleral inDoluemcnr.ln:Vinken
P.J. rnd Bluyn
G.W. (Eds.),.Ilatd.tooltof clinial ncwologl,
'vol.2, Nodlr llolland Publ, Comp., Amsterdam, 1969, pp. 358*301.
t)lt',zalo
(iillcllianu
G.*.Actr
l.- Eleclroenccfalografi.q
G,, Stoica
Dd. Mcdlc,\ll,
$i elcct]onliografid,
Ihrcuicsti. 1$65,
(l Ir x Dr b o l $ W. 11.* Arir(I, Practico, 1955, 6, 84-89,
Cht,rol)$ ki
Jttrl
, 1,1iJ , 2 . J 0 - 3 1 8 .
.1.-.- Arch. Nnr r ol. I , s y c hi1r l. 1$l,
{i l tl A l ol l
l l tri :],,ri .
I' i .,
l ti l
/\r{ l orri or
l l l (i .
l ' ..1,
ll,
||,l ,,r
M. l l .
( l i o | . | r ,l r s i c h l r L .N r l l f r '| n 1 , , l l ) ( i {t , , r t ,
lrLt rt . l lt,. lrlnizlo
11 S. , llr r ,
I r lllli
A.
7l l 7.ll{,
l)tf)rrs
\', S., Iicrr
A. - ( , o qh ! r . / n. opr(, lhNr l0s'l l r o n l l r sl l r b l i s h c r . S p r . i i g l i f l ( l( l l l - ) ,
l0i)lt.
l)rr:ourt
J---,ll(:rir s oiguis , G as t on Doin et Ct o , P a r i s , 1 9 2 7 ,
(Iesaffectians
f )l.i iri ll( .1.- Si-illaioloUie
dd syrf{ilncTrerrear,lt:rsson et Cte, Faris, 1{)14.
l) r'l ir )u n I c .I.- Gez. Ntd. Flarce, 1979, 8d, 1651*1651.
l)r' l:ry
,1., L hcrnritte
F. - Enc y c lop6dicm 6d. - ch i r . ,1 9 6 3 ,1 7 0 1 9A 1 0 ,. 1 ,1 - 1 0 .
l)t lry
.I., Lh crmittc
11,- ' Enc y c lopodie m 6d. - c h i r . ,1 t 6 3 , 1 7 0 1 94 3 1 . 1 , 1 - 4 .
l)f lry .l.,
Lh crr)rittc
f , , Enc y c lopediem d- c hi r . , 1 9 6 3 , 1 7 0 1 9A a o , 4 , 1 - . 4 ,
I )rr). DL
\v.O., I{cc ht s c half
en A. , c ulev ic h
c.* Ncuriogy" 1Stj6, 16,
I lt._33.
f )e l)aris
\I- - Glo s s ophar ungeal
(Eds,),
r r c ur algia.I n: P. J . V i n k e n ,
C.\\. Bruyn
Ilundlrool; of clitical neurologp,\o1,5, Notth-IIollaud Publ. Co,, Amslcrdam, t968, pp.
35 0.3 61 .
l)r' \ic
M., Bou ch cr
N. , I la\ ' ear
lI . - J .
iled . L y o n , 1 9 8 6 ,5 A v r i l , 5 3 7 - 5 4 7 .
l)cvic
Il., Aima rd
P. , 1I ic hc let
F", M as q r i n
M . O . *R e v .
neurol.r 1967,
11 6,4 67 -17 1.
l) i r nr o n d S. - Postgrad. Med,, 1974, 56, 69*73.
l)i| lr{ uro
S., Scho t land
D. L. , Boni} la
E., Lee C.-P,, Cambetti
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Ilo wlan cl I- P.-Arch.
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f)inritriu
0. R. \I. - Neurol., Psihiat., NeuroIlir., 1972, 11, 29-39I) i\ )I. R.J IIallp ike
C, S. - I t oc . Roy . Soc .M ed . , 1 9 5 2 , 4 5 , 3 4 1 - 3 5 4 .
f) ix n I. R., Ilxrrison
lI . J . G . , Le$is
N c u r o l , S c i . , 7 C 7 1 ,X 3 , 2 3 2 - 2 5 6 ,
P. D, - J .
l)o(iinot
B.-ADr.
M ed. Nanc y , 1$72, t J , 987- 9 9 4 .
f)i N chrr,1,1 D.4., Bank er
B, G . - Ar c h. N. ur o l . , 1 9 6 1 , 5 , '1 7 *9 3 .
f )rrf chnrcn
D. A. - A. r c h, Ner r ol. , 1968, 18, 654- 6 1 4 .
l,r' N chma n
D. A., \ Vet z el
N. , \ v as s c r m an
II., Naito
trI.-Arch, Ncurol.,
19 60 ,21 , 1 ?0 -.18 3,
f)rrchman
plus: a classificalionof the dis.rder$associated
D, A. - Op,il,taLmoplegia
uilfu
proor.ssi?e
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f)f il! l{ ne scu St,, Dr igines c u
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lid. Ac.d. R.P.n., Bucure$ti, 1962.
l)rrit{ I ncscu
St., Dum a D. , Popov ic iu
L, , T u r c u
T., Driglnese
u N",
l!o tot
Tr,, $ c r baD
l{ . , Pops c u
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D.-Rev. roum. Neurol.,
lli{ii), rl, 50-58.
l)ril 4in cscu
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L. , Vuia
L , * N c u r o l - , P s i h i a t . ,N c u r o e h i l . ,
01 St r oia
l)u
1I!'A, 1, 1'l-24.
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V, V.,
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P.,
Vu ia
1 6 9 - 1 7 J.
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V, V"
l)", I'flIilifln
I ' N l h l u l . , N c r r f t x ' h i r., l0 ( il) , l) , J, 4 0 :> - 4 1 1 .
Po p o vic i rr
J.:., Y r|I!r
L., IJoros
Tr,--Slr
O., li u I y
I. *- i.-rrrrol.,
l i ,r,r
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I)ul nt
D ., P N pi l i l [
\' .!.,
]1., P opov i (:i
t,- ,N c (r.r,t., I\ ri rt.,
i i i rbax
N crroc i l i r., 1905, tr, 3.10 :ti )l J
D nma
D ., P s pi ti ar
I-., S (r r' brrr
\' . V ., l ,opov i c i u
l I.--c tl l .i ut
l l r{ i ,, t1||,],,
J7,409_418.
D trn1a
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\:. V ., ;erban
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(i r1r.l . N ,.r|],t.
I-.* S tu(t.
1965, I r,4S 9-515.
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\.ol. I\', C. V. \losblr Company, St. Louisr 19tr0, pp. 3651--3652,
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Ilkbom
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Ol i va r i r s
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\r ., Po p o vi ci u
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E . , Sch w a r tz
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G.*An!!.
Fsvarel-.Benazet
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A. U.Thtomboses
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Figdr5f
B,! Po p o vi l i u
a n M ., D u l d u
8 ., AFg i a n
L . - }l e v. M cd . ( T,{. M u ',r ,}) ,
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Fdgdrbf
L . - M a n i l e sti i r i sp a sm o l i l i tc.In : L . I,o p o r tr r r l
a n M ., p o p o \;i ci l r
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I.crIaro
Fischer
Fische
A., .Icr vi s
G. A.* Ar cI.
N cu r o l . Psi ch i i t.,7 9 4 4 , t2 ,4 4 tl - - .1 U i t,
t r{.- N e v
l tn g l , J. [tcd ., 1 9 5 6 , 9 5 r , 5 7 - 6 5 .
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G o n y e a il. F. . -l\r.rh. N(,uj.ot.,1!74, J/, 168-1?j.
G o o d \ '" i n
R . Ir ,, I) o scr
C , l I.J.A.II.A., 1 9 6 3 , l d r , 2 5 3 - 2 5 9 .
( ; , , I ta g e I., Pe r r i e !
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G r e e D \ \ '. R ., l l a e ke tt
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Greer
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Guillain
C ., M o l l a r e t
G u i l l e m i n a u lt
C ., \ti l so Il
R . A., 1 ) e In e n t \\r . C .- Ar cL . N e n r .o l(. ( ]tr i c.) ,l !r ,t.
21, 255-_261.
Guyton
A. C.*.Strucf&re dnd tdnctiorrof lhe neNoussysfem,\V. B. SaundcrsCo., I'l,it ,t, t
pbia, 1g?2.
Ilaberlandt
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Ilagerrau
( i r ,.
I.- Pa th o l o l i ed e sn e r tscr u n i cn $l n : L e m i e !r e ,\.,
Lenorrnalrr
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I- ,
:r \ 1 r ,,.
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Itallpike
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Ilarrin1an
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H .- Br a i n , 1 9 6 g , 9 1 , 4 0 1 - - 4 1 8 .
Ilarrington
R , B,, Fl o l l e n h o r st
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N r u r o l ., l txi r ,.
15,29--34.
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s R .- L a ca ci ti p sl l ch i q u eIl,a sso n e t C l c, p o r l s, tti ;t.
II6caen
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Il .- Pd tl to l o g i cd u l a n g a g c.l .,.|p h a si e ,L n r o u n sr .l h r t\,
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Hilton
G . F., H o yt
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Ilinterbuchner
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N e w Yo r k l ca d . \Icd ,, 1 9 7 4 , ,r , b 8 9 - - $ 0 r ,
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N o o r o l . ( ( :h t,..) ,
L967, 16,357*3$5.
Ilishikawa
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2 ..- Ii tr .tr o t.r l
crltr. cliD. Nr.rrrophlxlol,,10f,5,,8, 487-.i92,
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A l .s c rri
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\.
4..
,l r,l
Ir,,,1
l l rl )tl ,
1, t2tI
12\).
(i ol l c w ac rt
l .,atLerre
!i .0.,
A ., Il erenIars
.1. ts ., S l al l o
Z.N c rrr-oh11y ,
1970, rr, $82-990,
l ,azorfl rcs
G.-Le
s gs l i me n$oeur c c nl ral , l l as s on et C i c , P rri s , 1967.
(i .*
l ,azortl l cs
P al hol og!|, c l as s i ti c al i a and c l i ni .al as pc c ts af uas c ul ar di s trts ol l l t,
spi nal co rd. Tn: l ' . J . \ri rk ert
and G, W . B ruy n
(E ds .), Il andbool i ol .l i ri .r' l
neurol ogy , !ol , l :, \:as c l ar di s eas es of the nc ry ous s y s tc m, P art II,
l l ,' l |,!rl
^_orl h
P ubl . C o mp., A ns terdam, 1C 72, pp. 492 506.
l, e a c lr \V. - J. Laryng., 1962, 16, 114-790.
Lccs
f.,
Li v ers edge
I-. A .B rai n, 1962, 3r, 701-710.
l -eLoczk],
T.-A c l a
Mol phol . A c ad. S c i . H uni j ., 1353, 4, 301-408.
(l ardi ov as c , D i s ., 1964, 31, 4A 9--41.1.
f,en .gre
L- Frogr.
Le11no\-IJuchthaI
L.E.,
K abat
E . A ,, $roi f
A .,
B ez erA .E .-J .
253-270.
llic
L c {r n P. D ., Il o .w i l z
1s9-772.
N . H ., R o b i n so n
F.* Yr l c
J. Bi o l . M {i ( l ., l l }1 ,:1 , .,.
A . , S tr n r Il o i !|
l . - I'o l i n ? u r i tcl c,l ,l d . N {cd i cl l l , l l ( l u r r fti , 1 0 6 1 1 .
A . , N l ,r l r ) o r r r r r r 1 ,. .l r r :l
{y/i r S? si u t't( n n tl i t Sr 4 i ti l i tl ( , ti i \I( ; |
l i t i o h n n tl i l ti h t, I'l Il 'I N ,l '|1 , Il l 7 l ,. ? .2 t1 .
[itli||,
lInrk1urrl
!r.r,
l l ,,
|i .,, i r i .l l , r '
( ) . r .1 ,. l ,!|I
l l . 1 ,.
A.
!tt'tr .)
/!N ,
: l5
L , , nic k k inen
P. *
c t a Ncu r o l . s c a n d . , 1 9 7 4 , 5 0 , 6 9 0 - - 1 1 8 .
N lko$holn in(]
li, r Nik os holainen
J . , Sc lm i
A,4,., Ilaloncn
I r . 1 j . *Act:r Ncurol. sctrrd., 1975, ,'J, 3lliJ-,346; l]47-364.
N lshl' .{oki
N l$hll{ nk;
Nlrltrrrrllo
S.--Ard r .
Norrir
f , . l l .. l i ,r 'l xr ,t
t. I
t\tr l ,r t) , ttttt l t|.ttt!r :|, Ii t\r tu ( Jtt) tr<tn tu .ttr ) /) l tii ttttr
r
.t,l
! ( l t t . r tr r j i l tttn tt,t tl t. tl t,., ti ,,,,,, !,!t l ,l r i r tt0 , N r ,\1 \'( ,r l i , 1 l ]fi l .
N o r t 'i s
l f . fl .,
i n l ,.r r ,.r r r \ \\ tt, tr :,r |l l r ( t
tt. O,- ",1 l |tu .l i ,h o r .]t
tu |ttt\r n i t,
dtrrirt)1ntn|$^ 1rttutrIrrttittttu tt'tltrrtttt rt!tt oth.r
turn al molot.nt)t|a ./jsd.".. /r: r.
I I . N o r t'i r ,
1 ,. t. ti I Ir ,,r ,t ( ti l s.) ,,U o k) rn e u r o nd i sc( l stt.l tl tsc/r cko tu j t o tl tt,t]tr
'r
k arol $tlttosi:tturf rthttut r/isrr/Ifrr,,(lrtrDo arl.t Stratton, Ncv \ork, 191;1.
Oblu
N . , l l r r su
l \1 ...N l 'n r o t. l ,si l ti n t. N cu r o ch i r ., 1 9 6 9 , 1 1 , 1 0 1 _ _ 1 1 0 .
Olson
\ V . , N a sh vi
o '1 .,, ti n g e l w - It., N a l sh
c. O., L :tr n n u 0 l r f r t( .
.\reh. Neurol,, 1t72, Zt;, 1S3._,211.
Oprescu
L , Io n e scr
I.* L l r ye n l e l e
l n n e u r o ch i r u r g i e n e l r r cl o g i eItd
, . N r ( ti cr l i , l tl
curelti, 196A.
Ortiz
d e Za r a te
J. C ., tr {a r Isso
A.* Eu r o p , N cl r r o l ., 1 g T0 ,J, ]_ ,_ I2 .
O t h e r .6..- Acta Opirthalmol., 1S6?, lr, 371-3?3.
O t t K . I L , Ka se S,, O j e m a n n
It. C ., IIo h r
J. I'. - Ar ctr . N o u o l ., 1 i l 7 .l ,.r r , tti tl
11i7.
Paillas
J , E.* R cv.
N e u r o l ., 1 9 6 0 , Jr 2 , 1 8 2 .
Pampigl
ion e G.* Eleclricatactirrilljoflje brain in somegeneticalllJ
dct?.l,1ir(trrutr)t,t,til
l ) o l i cd i se a se s,
In :Il . Va n D u i j Il ,
D . N . J. D o n ke r ,
A.C . Vtl n Itu t.tf r ,,l
(Eds.), C&rrerl conceplsin clinical neutuphgsiologr, N. V. Druktierij .l.rjo, ,t tr(. r|jr,,
19'ti.
Pascu
I " , P o p o vi ci u
P a s e u I . , C o n sta tl ti n
45-48.
L ., Bo a n ti
I.- R e \,. M e .t. ( Tg . N l r u ct) , 1 9 7 1 ;,...1 r:,i
,,,i .I
I{. D ., p o p o vi ci u
L ,- R e \.. tr Ie d ,( Tg . r u r r .ff) , l 1 ) ,,,
Pasik
P . , I ,a si k
T., Be n d cr
M . B.- Tr a n s. Am cr . l l e r l r o l . Ass,,tg 0 0 , r .l , i tl l t ]|i .
Passouant
P., N l i n vi e i l l e
J.- R e v.
N e u r o l ., 1 9 5 3 , s8 ,3 6 i ) 3 7 o .
Passouant
P., M i n vi e i l l c
J.- R cv,
N e u r o 1 .,Ig E4 , 9 A, 1 l A- h :.
Passouant
P,- Ol fa cti o n e t r h i n e n ci p i w l e ,1 e r Sym p o si o nXta d i te r a n n a .nsu r . I,,,,l ,,r r t,
CrasseeL Canncs,3-5 Juin 1962,La Francc et sesIrarhrms,1002,pp, ,rll- .l:,1)_
Passorlant
P., Sch w a b
R . S., Oa .i i l h a c.I.,
Ba l d yM o u l r l r ,cr
,.\'.
[1 _
Nellrot., 1964, llL 415-126,
Passorlant
P., C a d i l h a c
J., Ba Id y- M o u l i n i cr
i I.- _ R cv. N o r r r o l .,l l l ti ,,, ///i ,
585-,620.
Passouant
P., p o p o vi ci u
L ,, Ve l o h
C ., I] a 1 d y_ l l o u I i n i c r l !t.
Itr .\.
Neulol., 1968, 118, 431-447.
Pauly
N0 rr' [ rt n
1 l | . ( | r , | , , I1I (.n , t [ 1 t ,
.|,
,iti
i\tnt
tj,,,l,
t r| l .
| | )] ,
10,/.
3{t(l
ltfi?
I' i r I ir'l(l
\\'.
,\'( l' . ) , J r lr l' t . l' ! \ ( lr ir l. , 11J : 111,
ir ' , l l i ) i l : l / l .
l' r' rr lic l(l
\\r., Sr|llbr
li. , ( : it r r ir r i
r\.
. ,. N c r r r o l ) l r l s i r ) 1l.l ,l i ] 1 ] ,: : , : i " ) . ) . t \ '1 .
I ii l{l \\r., .l r s t r r I I I .
f' r
I it ) il. t s lt anl lht l t u : ! i o n u lt t l t r t ) t no l t l I h I t 'I t h a i ,
'l
Liltl(, ltfo\!n un d ( i) m p. , lJ os t oD,l0l, l.
ll, rlicld
1, . - - ^Spr c cat
, r {i ( n ( t r l l i v . I \ . c s s ,l , o r ) {l o n ,
w., ltol)rr Ls
i ldbt ain Dt r c h a i s n l s {)
I1 |tlt.
I',.f (lrf lo|l (i. - -lilndc(nalo1liqu?tl\ thakj'll$ dc l'honu/r .tdullt tI de sa udsculrr'is(Ilioir
(i"/rjrir'11?,
l'h'(c, P:rri!, 1960.
(;.-ltrv .
I' cirlro rolr
Nc ur ol. , 19?6, 132, t 0\ l- : 12 4 .
l' lrilco\
I). V., S(! 11: r r s S. I - . , Panr plelt
I t ., B c i g h t o n
P.-Brain,
X97j1,
../(, J09-316.
( l h. - ' I ' oulous e r n d d . , 1 9 5 3 , f , 5 6 $ - 5 8 1 .
l' lroqu rs
.J., Oriz os - Rr eI l
l' lll (hin o
lr., Orivolli
G . , Vog- hi ] I . - { . - Ac ta
N e u r o c h i r . ,1 g 'i 5 , 3 L 2 A 1 2 2 1 .
llrl lt)F( irrno 0 ,-Ilcs .
illr bl. As s . 1c nt . ner v . Dis . , 1 9 6 7 , / 1 5 , 3 5 1 - 1 2 3 .
I' ol)cscu
Il. i\., Io an \ r . - . llif r z r d,
lld, Uc dic : il i r ,B u c l r c l t i , 1 9 ? 7 .
l' oprsou
tL , R!{lr
( E d . ) , P a l r ? . , g tu
lf . - - I ' olinlio. ilc le.ln: I i. R. d u
an i t d l i i m a l o t i i ,
lld. Mcdic{rli, Brcrir'$Li, 1978, p}. 3tt7-113.
lropo!jciLr
1,.- CLrceltuiosuptu Dalo|ii utlat dalc Liothimi.e ti eleclroencelalogrufi.e
tn
tlecliunile DascnLarc
ccrebrale,Tczi de doctorat, IMF. Breur9ti, 19{i5.
l' op(, ! iciu
L ., Alg j) lar !
D. , Sc r ' llan
J t . - - S t t r d . C e r c e t .N e u r o l , , 1 9 6 6 , l r ,
'211t-237.
| ' op(, ! i(l
iu L ,, -.\rginLar r
I ) , - - Rev . M od. ( ' I ' 9 .I t u r e $ ) j l ! L 'l , 1 3 , 7 0 - 1 1 .
I' opol
ir ju L., 1 \S! ijan
B. - Re1- . - \ - r ur ol. , 1$6 7 , 1 1 1 , 1 a l 2 - 7 3 '7 l' opo.,'icir
I-., Gre c u
I r . - St ud. O elc et .Neur ol . , 1 9 6 " 11, 2 , 4 2 9 4 1 1 .
lf ot )oviciu
1 ,., Af gian 8' L^z . Ar I - . , P: 1l: r d e C . , S z a b 6 L . - S l u d . C e r c c t .
1.908, 1r, 39-'16.
^-eurul.r
llopoYiciu
L., Afg ian
C c r c c t .N e u r o l , , 1 9 6 8 ,
I } . , Sz alr . l I . , Rado l I . - S l u d .
1.7, 15.J-77/1.
l' opovi0 iu
L ., Atg ian
ed. ( Tg. M u r e f ) , 7 9 6 8 , 2 , 1 2 2 - 1 2 5 .
t s . * Rev .
l' r)po\ 'ic ju I-., A;gian
l] . - - ] ] ev . l{ ed. ( ' f g. M u r e s ) , 1 9 6 8 , l r , 2 0 - . 2 4 .
l' ot)o\ ' iciu L., Pa s c r
I . , AFgian
8, , Lr z dr
L., Becu$
a l '. , D u l i u
E.Slird. Cdcct. Ne rol., 1$69, 11, 111-426.
l' ol)ovicir
L ., Aig iar
n. , Duliu
E. - \ eu. ol ,
P s i h i a t . , N o n l o c h i r . ) 1 9 6 9 , l y ',
1i]1..,135.
l' r)pov ioir
L., .{Fgian
lrr)po\.iciu
L., BecuS
/r,3 90 .-39 4.
i' r, t )oviein
L ., .{tg ian
I' r)J)o!iciu
31):t.
J-., P::l s c u
l' ol)oviciu
I-,, Atg ian
| | .1, 2t)G-2tj'1 ,
tsopo\:i ci r
L,, l l i rc k
L.C ol l c l uz i i fi IntbLrmi bi nl el o{ l ol oti c c .ID :C ous fi i l Lri ftI ti rLn!,,
.otund.ii ,,.f-onros{ialica lteftcbraki lil pri.ti.a
uedicald", Tg. Muref, 20 rl]ni l1);'(;.
P opovi ci u
L., P as c u
I., ,)i po$
C ,, C orJ ari rL
O., LA z trr
L,, A S i ti :r
r l t..
B e c u t ' I. - W s hi ng rnd S l c epi D g, 1970, l , 89-101.
P opoIi ci
l l L., P as c o
I. - h ; S i mpoz i onul ,,l c htl l ;"Ldl i l rr pal ol al l i d oas (ul urd rrhtl ttt ,
S oral fl, 1077, 1-21,
IropoY i ci r
L. (s ub red.)-
i U dti fes l ti ri paroti s l i c e utebrtl e tl tepi [rt][i tc , t,i l - [l ,rti (,' t]r,
B ucurr$1i , 19?8.
P opo\,i ci u
1,. (s ub rc d.)-- t' i s al , ed. D ac i a, 0l uj -N apoc n, l 97i j ,
(1. fi S rt.c k
P opo\i ci u
L., l J ec x t
T., D rl i u
L., $i pof
Maf t.r--(i rrl rrl ,r/r,
l ( sl ud i ul .l i nfu s i el ec ranl i ogral i c ul putu\l i ol atni i [ot, C onr. S rs i unc r N rri rl :r r ti t.
Tg. l l ure$ a S oc . S L. l l c di c al e, 2:] apri i i c 1978.
vi ci u
T,.- J n: { i . A rs eni
(l i d.), al ' rattl Lde neurc l ogi c , v ol , I, l i rt. } ti (l i (rl rl ,
I,rl
rcsti , 1 970.
P opoti ci n
L., I):rs r|1
l .I' ri ux i pi i general e de l Lrapi e naw ol oti c ti , l rrrO.,\rr,
rr r
(l d.), ' !ral dL.l e x euob7i e, \' oi . \' ' ., Ii d, l i l rdi c al i , I]rour.c s ti , 1079,pp.25:t
l ,ti r).
P oFo
tr,., P as c u
l .-' Iul burbi l e
de c an;ti i nl d c l i tt l c z i utti te s i s l t:ttrl ui t,ttl tl ,l r
bu:i l ar. 1o. L.P opo\.i c i u,
Gtt. P c ndofunda
(s ul ) (rl .), /,,,/,/
S i I. P as c l l
l a7i tr uos c ul ari i d !i s l c rntdui D ertc bto-bu.i l ar, Lr.l . .l uui nrc a, Ia;i , 1!?9 l )p. 2:ti t :l tti .
Fopoyi ci u
f,. (s ub red.)- S dnl i ol ogi a neutul ogi c ti , Li togul i l r Il l l .. l g. N l or(t, l l r/1r.
i ci r
P opo\
1,., B c c ut
T., W ai ts rk
P ., D ul
Me(l . (' l d. \l |r,,,r.
i { u D .-l trt.
P opovi ci u
11, , Pir os , I J - - I lc v .
l u c d . ( T g . I ! u l e i ) , 1 9 6 9 ,J i , , 1 1 - , 1 8 ,
' f . , Liz Lr
L. , Sz abd L . *R e v . M c d .
( T g . I l u r e *, 1 9 6 $ ,
8. , Sz ab6
I . , Af gt an
L. , Rado
l l . *R c v .
8, , S i p o F C ,-
8. , F: lgiir t r f
19t9,:5,32.* .3s .
popo\.i ci rt
L., P i s c u
'trdtal de neurobgie,
N o u o l . , 1 9 6 9 ,1 e 1 , 3 2 6 *
R e v . N e ! r o l . , 1 9 6 9 ,1 2 1 , 3 8 O -
an ] I . , D u l i u
E,-Rev.
Ncurol., 1070
f' { , pr)viciu
I.., S tam : r t oiu
1. * Ropor l ld a X, I - a S e s i a r aE E G , E X I G t t N e a r o t i t i o Io!)ie clinicll, Tg. trlur'e$,9-10 oct. 1970, pp. 43-5B.
l)opoviciu
I-,, Prs c u
1. , At gir n
trr. Al{d . l}a lh., 1971, , , 603* 606.
8, , $ipo$
C,, Moldovcanu
I'o L1rr
,L
.t. l ,rrry |l $)|. Otol ., 11)7:1,l l (i , ul J l tl 1l 2.
. /' ri ri /r/ri ,, l ,:{ 1. ;\rc (l i (.l l i , l } |l i ror(.i l i , l 97l j .
l | \' ,
I,ro(l csr
\i r \' .
l 'fi tc'l
fl ., f' r' I,
Il l rrl tou\\' l i l t,l rtl i (
I)t i l ri c d, l i l .
1111,;t .
M . *A r c h ,
lropovici
1 ,", lgit D
I . , Sz ib6
I-I t , , Pas c u
Sonnul nornwl $i pak)lo|ia,
Iid. Ilrdicr)lt, llu(Lll(sti. 1972.
l' olrrlv l(,iI|
L ,, I)xs( : u I . , , , Sipot ( 1, , I . : ' r z ir
1 , , , A $ {i t | | |
I],. Nlol(l ovc0ru
,11,. Nerfl,l,, |rilrirLl., Nrur'ochlr., 107!, /7, 3:ll-!-.31{i.
:I
l 'r'ol r
|'I
l 0)
4.. l !|||r,.,r,
.l ;t i ,
.1. L
/\11l r. S ui \v
\r,urri .
N (r' r,r' l ri r.
i \l f,l j rl l i .
l l l |(. r,)l l .
:t( l
n, i;. \\r"
lir:r ,J.-- llt ) il! ls u iu llt t lt ! t u! : t uliD. . iix r a {r r .15r.' : 1 '. . 1 . \ '| I l i (
" ' nr(
1l I rl y Il (lnls.), Ildndbool,ol tli lk:ul nalrclog!1,\rll. J5, lils{:\ior',r\rnslfrdrni. 11174,
:\2t 372l iirrl rlvi( :i
Fl. * I ' r ' c s s c m dd. , 1913, J 8,5 7 3 .
/\., I-ascu
ll r {l u lI.- . l,doloUie utlihlii motorii, Ed. X{edica)i,Bucuregtj, 1977,
llr(f u 11. - IJalolotliaunitdlii lnolotii, Ed. Medicxu, Bucure$Li,1978.
(s b red.), I-tutal cle ncarolaoir,
Ltrrlu ll..- -lJatolot
i4 rleutumusculurd.In: C..r\rseni
\'1,1.\r, Itd. Xlediqali, Bucureiti, 19?9, pp. 17S-208.
l lli
8., Jolly
S. S.- J .
I Ddian if ed. As s . , 1971, 57 , 3 1 5 - 3 1 3 .
l l:rvrr lI.-Acta
Nru rol. s c and. ,1967, 4. 1,Supp] . 30, 1 - 6 . 1 .
I t.ch ts ch alfe n
A., D c m en t 1\ : .- - Rc s .Publ. As s . m e r r '. m e n t , D i s . , 1 9 5 r - ,l ; , 1 3 E - .
.108.
l lr' (f 1l D., Pla to
L. T . - - - A m e r . J , E p i d e n . , 1 9 6 6 , 8 , 9 ,
C., ! liz an
T. , I ( r r land
5 t-?3.
li ( l s rt nr S. - Il.rcdopaIhiLt alecticopo4jneurilifornis : Phlllunic ucid sloragcdhcuse( litfsun's
dist4:ic) with parliaular referc1celo lherapeulicotul pdthogcneticaspcts.Tr : D, B. T o w e r
(Iid.),'lhe D c r \ro r s sy sl e rn, vol.:, Ralcn Press,New York, 19?5,pp,22$-234"
llis(:r
lt.Pr,dliquen.u|ologiq e, vol. I, 1I, trlassonet Cie, lreris, 1952.
I tr)l)( rts A. H., Ba '1f or t h
J . - Nc nr ology ,1968 , 1 8 , 6 4 5 - 6 5 2 .
l l,){ rr
R. A. - M & I l i p a e $ a n i a l n e r D ep d l s i r s . I n i
,1 ., BiIlc
J. alld Vigour oux
(Dds.),Ilanlbook of cLinicalneuolagu,'tol. 2,
I,. J. Vi)rken
and G. \v. Bruyn
i,ocalizalion in clinical neulology, palt I, Norlh-Uolla;rel Publ. Co., Amsterdetn, 1969,
pp.8 6-1 06 .
l i(' lLrrlcr f'., lsch Ij,, I s eh- Tr eus s ar d
C. , Nor t h
J . - R e 1 '. N e u r o l . ,1 9 7 1 ,l ? J ,
2:t0-2.1G.
l l (' son
K,, Lo eb 1 1,, Sino
I . , Ram int oola
1I., Cunnar
R. - Circulationr
1$51, l.?, 836--8.1{.
l i 0scnberg
D. , Lov elac e
R. , R o $ l a n d
L.-Areh. Ncruol,"
R,, Scho t land
1068 , r9 ,36 2-3 ?6 .
Ii,) s l( r r .t.- Prcsso lled., 1930, ,:li, 5lO-591.
l l oss ,^.., I-ipsch vitz
lled., 1970,
D. , Aus t in. I . ,
Sm it h. I .
Jr.-NewEngl.J.
230,313-376.
ll rr (' li . r C. \V. mer. .J. Ophthal., 1960, t/, 1293-129B.
i i rl)e ID r rrl fI. D., fen t a
L, T. - Alc l! , O t olar y ng.( C h i c . ) ,1 9 6 6 , 3 1 , l $ 2 - 2 9 6 .
irr'lfs(:n\regcI
R. * ,\ulloi,lusk.lliiftmuntci, Vl:B Gcorg.'flrirme, Leipzig, 1860.
: r (: ir s o11$o gcr R.- {:linical locoliselional otulomolor(listurbunces,
In : P. J. \'inken
lln(l G.\{. Bruyrl
(Eds.),Handbaakol clitricalncuNloglJ,\.o1,?, North-Ilolland Pub1.
(b., Amsterdam, 11)09,pp. 286-357.
lr,r I l( s ,1. G., fi r I o i O.- .I.A.II.A., 19i5, 2J1, 69-'12,
S l gol O., Oltea 11 r
L, Cez ar
I . - St ud. Cer c ot .N e u r o l . , 1 9 5 0 ,7 , 2 2 3 2 4 2 .
lil|((,f
O.- ricr.ct(?!t, Itd. r\cad. n,S.n., Bucurciti, 1960.
l r rl ltrr O., llore s
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